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WEB-based GEne SeT AnaLysis Toolkit |
| Translating gene lists into biological insights... | |
| Database:biological process       Name:cellular respiration       ID:GO:0045333 | ||||||
|---|---|---|---|---|---|---|
| C=159; O=100; E=9.74; R=10.27; rawP=1.93e-81; adjP=5.33e-78 | ||||||
| Index | UserID | Value | Gene Symbol | Gene Name | EntrezGene | Ensembl |
| 1  | ENSG00000151366 | NA | NDUFC2 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa | 4718 | ENSG00000151366 |
| 2  | ENSG00000128609 | NA | NDUFA5 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa | 4698 | ENSG00000128609 |
| 3  | ENSG00000165264 | NA | NDUFB6 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa | 4712 | ENSG00000165264 |
| 4  | ENSG00000163541 | NA | SUCLG1 | succinate-CoA ligase, alpha subunit | 8802 | ENSG00000163541 |
| 5  | ENSG00000156467 | NA | UQCRB | ubiquinol-cytochrome c reductase binding protein | 7381 | ENSG00000156467 |
| 6  | ENSG00000146701 | NA | MDH2 | malate dehydrogenase 2, NAD (mitochondrial) | 4191 | ENSG00000146701 |
| 7  | ENSG00000184076 | NA | UQCR10 | ubiquinol-cytochrome c reductase, complex III subunit X | 29796 | ENSG00000184076 |
| 8  | ENSG00000136521 | NA | NDUFB5 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa | 4711 | ENSG00000136521 |
| 9  | ENSG00000004779 | NA | NDUFAB1 | NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa | 4706 | ENSG00000004779 |
| 10  | ENSG00000169020 | NA | ATP5I | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E | 521 | ENSG00000169020 |
| 11  | ENSG00000182054 | NA | IDH2 | isocitrate dehydrogenase 2 (NADP+), mitochondrial | 3418 | ENSG00000182054 |
| 12  | ENSG00000147123 | NA | NDUFB11 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa | 54539 | ENSG00000147123 |
| 13  | ENSG00000154723 | NA | ATP5J | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 | 522 | ENSG00000154723 |
| 14  | ENSG00000006695 | NA | COX10 | COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) | 1352 | ENSG00000006695 |
| 15  | ENSG00000073578 | NA | SDHA | succinate dehydrogenase complex, subunit A, flavoprotein (Fp) | 6389 | ENSG00000073578 |
| 16  | ENSG00000119013 | NA | NDUFB3 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa | 4709 | ENSG00000119013 |
| 17  | ENSG00000169021 | NA | UQCRFS1 | ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 | 7386 | ENSG00000169021 |
| 18  | ENSG00000062485 | NA | CS | citrate synthase | 1431 | ENSG00000062485 |
| 19  | ENSG00000140740 | NA | UQCRC2 | ubiquinol-cytochrome c reductase core protein II | 7385 | ENSG00000140740 |
| 20  | ENSG00000166136 | NA | NDUFB8 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa | 4714 | ENSG00000166136 |
| 21  | ENSG00000140374 | NA | ETFA | electron-transfer-flavoprotein, alpha polypeptide | 2108 | ENSG00000140374 |
| 22  | ENSG00000172340 | NA | SUCLG2 | succinate-CoA ligase, GDP-forming, beta subunit | 8801 | ENSG00000172340 |
| 23  | ENSG00000147684 | NA | NDUFB9 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa | 4715 | ENSG00000147684 |
| 24  | ENSG00000160194 | NA | NDUFV3 | NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa | 4731 | ENSG00000160194 |
| 25  | ENSG00000184983 | NA | NDUFA6 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa | 4700 | ENSG00000184983 |
| 26  | ENSG00000130414 | NA | NDUFA10 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa | 4705 | ENSG00000130414 |
| 27  | ENSG00000091140 | NA | DLD | dihydrolipoamide dehydrogenase | 1738 | ENSG00000091140 |
| 28  | ENSG00000165060 | NA | FXN | frataxin | 2395 | ENSG00000165060 |
| 29  | ENSG00000158864 | NA | NDUFS2 | NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) | 4720 | ENSG00000158864 |
| 30  | ENSG00000139180 | NA | NDUFA9 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa | 4704 | ENSG00000139180 |
| 31  | ENSG00000127184 | NA | COX7C | cytochrome c oxidase subunit VIIc | 1350 | ENSG00000127184 |
| 32  | ENSG00000109390 | NA | NDUFC1 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa | 4717 | ENSG00000109390 |
| 33  | ENSG00000164405 | NA | UQCRQ | ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa | 27089 | ENSG00000164405 |
| 34  | ENSG00000091483 | NA | FH | fumarate hydratase | 2271 | ENSG00000091483 |
| 35  | ENSG00000122729 | NA | ACO1 | aconitase 1, soluble | 48 | ENSG00000122729 |
| 36  | ENSG00000124172 | NA | ATP5E | ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit | 514 | ENSG00000124172 |
| 37  | ENSG00000183648 | NA | NDUFB1 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa | 4707 | ENSG00000183648 |
| 38  | ENSG00000142082 | NA | SIRT3 | sirtuin 3 | 23410 | ENSG00000142082 |
| 39  | ENSG00000119689 | NA | DLST | dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex) | 1743 | ENSG00000119689 |
| 40  | ENSG00000168291 | NA | PDHB | pyruvate dehydrogenase (lipoamide) beta | 5162 | ENSG00000168291 |
| 41  | ENSG00000099624 | NA | ATP5D | ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit | 513 | ENSG00000099624 |
| 42  | ENSG00000204370 | NA | SDHD | succinate dehydrogenase complex, subunit D, integral membrane protein | 6392 | ENSG00000204370 |
| 43  | ENSG00000116459 | NA | ATP5F1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 | 515 | ENSG00000116459 |
| 44  | ENSG00000100412 | NA | ACO2 | aconitase 2, mitochondrial | 50 | ENSG00000100412 |
| 45  | ENSG00000138399 | NA | FASTKD1 | FAST kinase domains 1 | 79675 | ENSG00000138399 |
| 46  | ENSG00000112992 | NA | NNT | nicotinamide nucleotide transhydrogenase | 23530 | ENSG00000112992 |
| 47  | ENSG00000125356 | NA | NDUFA1 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa | 4694 | ENSG00000125356 |
| 48  | ENSG00000215251 | NA | FASTKD5 | FAST kinase domains 5 | 60493 | ENSG00000215251 |
| 49  | ENSG00000213619 | NA | NDUFS3 | NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) | 4722 | ENSG00000213619 |
| 50  | ENSG00000178741 | NA | COX5A | cytochrome c oxidase subunit Va | 9377 | ENSG00000178741 |
| 51  | ENSG00000173660 | NA | UQCRH | ubiquinol-cytochrome c reductase hinge protein | 7388 | ENSG00000173660 |
| 52  | ENSG00000099795 | NA | NDUFB7 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa | 4713 | ENSG00000099795 |
| 53  | ENSG00000119421 | NA | NDUFA8 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa | 4702 | ENSG00000119421 |
| 54  | ENSG00000126267 | NA | COX6B1 | cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) | 1340 | ENSG00000126267 |
| 55  | ENSG00000135940 | NA | COX5B | cytochrome c oxidase subunit Vb | 1329 | ENSG00000135940 |
| 56  | ENSG00000023228 | NA | NDUFS1 | NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) | 4719 | ENSG00000023228 |
| 57  | ENSG00000143252 | NA | SDHC | succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa | 6391 | ENSG00000143252 |
| 58  | ENSG00000151376 | NA | ME3 | malic enzyme 3, NADP(+)-dependent, mitochondrial | 10873 | ENSG00000151376 |
| 59  | ENSG00000145494 | NA | NDUFS6 | NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) | 4726 | ENSG00000145494 |
| 60  | ENSG00000115840 | NA | SLC25A12 | solute carrier family 25 (aspartate/glutamate carrier), member 12 | 8604 | ENSG00000115840 |
| 61  | ENSG00000131143 | NA | COX4I1 | cytochrome c oxidase subunit IV isoform 1 | 1327 | ENSG00000131143 |
| 62  | ENSG00000189043 | NA | NDUFA4 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa | 4697 | ENSG00000189043 |
| 63  | ENSG00000172115 | NA | CYCS | cytochrome c, somatic | 54205 | ENSG00000172115 |
| 64  | ENSG00000110955 | NA | ATP5B | ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide | 506 | ENSG00000110955 |
| 65  | ENSG00000164919 | NA | COX6C | cytochrome c oxidase subunit VIc | 1345 | ENSG00000164919 |
| 66  | ENSG00000105379 | NA | ETFB | electron-transfer-flavoprotein, beta polypeptide | 2109 | ENSG00000105379 |
| 67  | ENSG00000115286 | NA | NDUFS7 | NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) | 374291 | ENSG00000115286 |
| 68  | ENSG00000164258 | NA | NDUFS4 | NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) | 4724 | ENSG00000164258 |
| 69  | ENSG00000167792 | NA | NDUFV1 | NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa | 4723 | ENSG00000167792 |
| 70  | ENSG00000131495 | NA | NDUFA2 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa | 4695 | ENSG00000131495 |
| 71  | ENSG00000065518 | NA | NDUFB4 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa | 4710 | ENSG00000065518 |
| 72  | ENSG00000155463 | NA | OXA1L | oxidase (cytochrome c) assembly 1-like | 5018 | ENSG00000155463 |
| 73  | ENSG00000167863 | NA | ATP5H | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d | 10476 | ENSG00000167863 |
| 74  | ENSG00000090266 | NA | NDUFB2 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa | 4708 | ENSG00000090266 |
| 75  | ENSG00000110717 | NA | NDUFS8 | NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) | 4728 | ENSG00000110717 |
| 76  | ENSG00000127540 | NA | UQCR11 | ubiquinol-cytochrome c reductase, complex III subunit XI | 10975 | ENSG00000127540 |
| 77  | ENSG00000131174 | NA | COX7B | cytochrome c oxidase subunit VIIb | 1349 | ENSG00000131174 |
| 78  | ENSG00000179091 | NA | CYC1 | cytochrome c-1 | 1537 | ENSG00000179091 |
| 79  | ENSG00000184752 | NA | NDUFA12 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 | 55967 | ENSG00000184752 |
| 80  | ENSG00000170906 | NA | NDUFA3 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa | 4696 | ENSG00000170906 |
| 81  | ENSG00000159199 | NA | ATP5G1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) | 516 | ENSG00000159199 |
| 82  | ENSG00000136143 | NA | SUCLA2 | succinate-CoA ligase, ADP-forming, beta subunit | 8803 | ENSG00000136143 |
| 83  | ENSG00000167283 | NA | ATP5L | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G | 10632 | ENSG00000167283 |
| 84  | ENSG00000067829 | NA | IDH3G | isocitrate dehydrogenase 3 (NAD+) gamma | 3421 | ENSG00000067829 |
| 85  | ENSG00000136270 | NA | TBRG4 | transforming growth factor beta regulator 4 | 9238 | ENSG00000136270 |
| 86  | ENSG00000010256 | NA | UQCRC1 | ubiquinol-cytochrome c reductase core protein I | 7384 | ENSG00000010256 |
| 87  | ENSG00000137806 | NA | NDUFAF1 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 | 51103 | ENSG00000137806 |
| 88  | ENSG00000241468 | NA | ATP5J2 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 | 9551 | ENSG00000241468 |
| 89  | ENSG00000140990 | NA | NDUFB10 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa | 4716 | ENSG00000140990 |
| 90  | ENSG00000117118 | NA | SDHB | succinate dehydrogenase complex, subunit B, iron sulfur (Ip) | 6390 | ENSG00000117118 |
| 91  | ENSG00000171503 | NA | ETFDH | electron-transferring-flavoprotein dehydrogenase | 2110 | ENSG00000171503 |
| 92  | ENSG00000165629 | NA | ATP5C1 | ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 | 509 | ENSG00000165629 |
| 93  | ENSG00000115944 | NA | COX7A2L | cytochrome c oxidase subunit VIIa polypeptide 2 like | 9167 | ENSG00000115944 |
| 94  | ENSG00000176340 | NA | COX8A | cytochrome c oxidase subunit VIIIA (ubiquitous) | 1351 | ENSG00000176340 |
| 95  | ENSG00000148290 | NA | SURF1 | surfeit 1 | 6834 | ENSG00000148290 |
| 96  | ENSG00000014641 | NA | MDH1 | malate dehydrogenase 1, NAD (soluble) | 4190 | ENSG00000014641 |
| 97  | ENSG00000168653 | NA | NDUFS5 | NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) | 4725 | ENSG00000168653 |
| 98  | ENSG00000152234 | NA | ATP5A1 | ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle | 498 | ENSG00000152234 |
| 99  | ENSG00000101365 | NA | IDH3B | isocitrate dehydrogenase 3 (NAD+) beta | 3420 | ENSG00000101365 |
| 100  | ENSG00000241837 | NA | ATP5O | ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit | 539 | ENSG00000241837 |
| Database:biological process       Name:respiratory electron transport chain       ID:GO:0022904 | ||||||
|---|---|---|---|---|---|---|
| C=110; O=77; E=6.74; R=11.43; rawP=3.24e-68; adjP=4.47e-65 | ||||||
| Index | UserID | Value | Gene Symbol | Gene Name | EntrezGene | Ensembl |
| 1  | ENSG00000151366 | NA | NDUFC2 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa | 4718 | ENSG00000151366 |
| 2  | ENSG00000128609 | NA | NDUFA5 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa | 4698 | ENSG00000128609 |
| 3  | ENSG00000165264 | NA | NDUFB6 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa | 4712 | ENSG00000165264 |
| 4  | ENSG00000156467 | NA | UQCRB | ubiquinol-cytochrome c reductase binding protein | 7381 | ENSG00000156467 |
| 5  | ENSG00000184076 | NA | UQCR10 | ubiquinol-cytochrome c reductase, complex III subunit X | 29796 | ENSG00000184076 |
| 6  | ENSG00000136521 | NA | NDUFB5 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa | 4711 | ENSG00000136521 |
| 7  | ENSG00000004779 | NA | NDUFAB1 | NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa | 4706 | ENSG00000004779 |
| 8  | ENSG00000169020 | NA | ATP5I | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E | 521 | ENSG00000169020 |
| 9  | ENSG00000147123 | NA | NDUFB11 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa | 54539 | ENSG00000147123 |
| 10  | ENSG00000154723 | NA | ATP5J | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 | 522 | ENSG00000154723 |
| 11  | ENSG00000006695 | NA | COX10 | COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) | 1352 | ENSG00000006695 |
| 12  | ENSG00000073578 | NA | SDHA | succinate dehydrogenase complex, subunit A, flavoprotein (Fp) | 6389 | ENSG00000073578 |
| 13  | ENSG00000119013 | NA | NDUFB3 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa | 4709 | ENSG00000119013 |
| 14  | ENSG00000169021 | NA | UQCRFS1 | ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 | 7386 | ENSG00000169021 |
| 15  | ENSG00000140740 | NA | UQCRC2 | ubiquinol-cytochrome c reductase core protein II | 7385 | ENSG00000140740 |
| 16  | ENSG00000166136 | NA | NDUFB8 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa | 4714 | ENSG00000166136 |
| 17  | ENSG00000140374 | NA | ETFA | electron-transfer-flavoprotein, alpha polypeptide | 2108 | ENSG00000140374 |
| 18  | ENSG00000147684 | NA | NDUFB9 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa | 4715 | ENSG00000147684 |
| 19  | ENSG00000160194 | NA | NDUFV3 | NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa | 4731 | ENSG00000160194 |
| 20  | ENSG00000184983 | NA | NDUFA6 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa | 4700 | ENSG00000184983 |
| 21  | ENSG00000130414 | NA | NDUFA10 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa | 4705 | ENSG00000130414 |
| 22  | ENSG00000091140 | NA | DLD | dihydrolipoamide dehydrogenase | 1738 | ENSG00000091140 |
| 23  | ENSG00000158864 | NA | NDUFS2 | NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) | 4720 | ENSG00000158864 |
| 24  | ENSG00000139180 | NA | NDUFA9 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa | 4704 | ENSG00000139180 |
| 25  | ENSG00000127184 | NA | COX7C | cytochrome c oxidase subunit VIIc | 1350 | ENSG00000127184 |
| 26  | ENSG00000109390 | NA | NDUFC1 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa | 4717 | ENSG00000109390 |
| 27  | ENSG00000164405 | NA | UQCRQ | ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa | 27089 | ENSG00000164405 |
| 28  | ENSG00000124172 | NA | ATP5E | ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit | 514 | ENSG00000124172 |
| 29  | ENSG00000183648 | NA | NDUFB1 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa | 4707 | ENSG00000183648 |
| 30  | ENSG00000204370 | NA | SDHD | succinate dehydrogenase complex, subunit D, integral membrane protein | 6392 | ENSG00000204370 |
| 31  | ENSG00000116459 | NA | ATP5F1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 | 515 | ENSG00000116459 |
| 32  | ENSG00000099624 | NA | ATP5D | ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit | 513 | ENSG00000099624 |
| 33  | ENSG00000125356 | NA | NDUFA1 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa | 4694 | ENSG00000125356 |
| 34  | ENSG00000213619 | NA | NDUFS3 | NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) | 4722 | ENSG00000213619 |
| 35  | ENSG00000178741 | NA | COX5A | cytochrome c oxidase subunit Va | 9377 | ENSG00000178741 |
| 36  | ENSG00000173660 | NA | UQCRH | ubiquinol-cytochrome c reductase hinge protein | 7388 | ENSG00000173660 |
| 37  | ENSG00000099795 | NA | NDUFB7 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa | 4713 | ENSG00000099795 |
| 38  | ENSG00000119421 | NA | NDUFA8 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa | 4702 | ENSG00000119421 |
| 39  | ENSG00000126267 | NA | COX6B1 | cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) | 1340 | ENSG00000126267 |
| 40  | ENSG00000135940 | NA | COX5B | cytochrome c oxidase subunit Vb | 1329 | ENSG00000135940 |
| 41  | ENSG00000023228 | NA | NDUFS1 | NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) | 4719 | ENSG00000023228 |
| 42  | ENSG00000143252 | NA | SDHC | succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa | 6391 | ENSG00000143252 |
| 43  | ENSG00000145494 | NA | NDUFS6 | NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) | 4726 | ENSG00000145494 |
| 44  | ENSG00000115840 | NA | SLC25A12 | solute carrier family 25 (aspartate/glutamate carrier), member 12 | 8604 | ENSG00000115840 |
| 45  | ENSG00000131143 | NA | COX4I1 | cytochrome c oxidase subunit IV isoform 1 | 1327 | ENSG00000131143 |
| 46  | ENSG00000189043 | NA | NDUFA4 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa | 4697 | ENSG00000189043 |
| 47  | ENSG00000172115 | NA | CYCS | cytochrome c, somatic | 54205 | ENSG00000172115 |
| 48  | ENSG00000110955 | NA | ATP5B | ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide | 506 | ENSG00000110955 |
| 49  | ENSG00000164919 | NA | COX6C | cytochrome c oxidase subunit VIc | 1345 | ENSG00000164919 |
| 50  | ENSG00000115286 | NA | NDUFS7 | NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) | 374291 | ENSG00000115286 |
| 51  | ENSG00000105379 | NA | ETFB | electron-transfer-flavoprotein, beta polypeptide | 2109 | ENSG00000105379 |
| 52  | ENSG00000164258 | NA | NDUFS4 | NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) | 4724 | ENSG00000164258 |
| 53  | ENSG00000167792 | NA | NDUFV1 | NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa | 4723 | ENSG00000167792 |
| 54  | ENSG00000131495 | NA | NDUFA2 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa | 4695 | ENSG00000131495 |
| 55  | ENSG00000065518 | NA | NDUFB4 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa | 4710 | ENSG00000065518 |
| 56  | ENSG00000167863 | NA | ATP5H | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d | 10476 | ENSG00000167863 |
| 57  | ENSG00000090266 | NA | NDUFB2 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa | 4708 | ENSG00000090266 |
| 58  | ENSG00000110717 | NA | NDUFS8 | NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) | 4728 | ENSG00000110717 |
| 59  | ENSG00000131174 | NA | COX7B | cytochrome c oxidase subunit VIIb | 1349 | ENSG00000131174 |
| 60  | ENSG00000127540 | NA | UQCR11 | ubiquinol-cytochrome c reductase, complex III subunit XI | 10975 | ENSG00000127540 |
| 61  | ENSG00000179091 | NA | CYC1 | cytochrome c-1 | 1537 | ENSG00000179091 |
| 62  | ENSG00000184752 | NA | NDUFA12 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 | 55967 | ENSG00000184752 |
| 63  | ENSG00000170906 | NA | NDUFA3 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa | 4696 | ENSG00000170906 |
| 64  | ENSG00000159199 | NA | ATP5G1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) | 516 | ENSG00000159199 |
| 65  | ENSG00000167283 | NA | ATP5L | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G | 10632 | ENSG00000167283 |
| 66  | ENSG00000010256 | NA | UQCRC1 | ubiquinol-cytochrome c reductase core protein I | 7384 | ENSG00000010256 |
| 67  | ENSG00000137806 | NA | NDUFAF1 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 | 51103 | ENSG00000137806 |
| 68  | ENSG00000241468 | NA | ATP5J2 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 | 9551 | ENSG00000241468 |
| 69  | ENSG00000140990 | NA | NDUFB10 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa | 4716 | ENSG00000140990 |
| 70  | ENSG00000117118 | NA | SDHB | succinate dehydrogenase complex, subunit B, iron sulfur (Ip) | 6390 | ENSG00000117118 |
| 71  | ENSG00000171503 | NA | ETFDH | electron-transferring-flavoprotein dehydrogenase | 2110 | ENSG00000171503 |
| 72  | ENSG00000165629 | NA | ATP5C1 | ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 | 509 | ENSG00000165629 |
| 73  | ENSG00000115944 | NA | COX7A2L | cytochrome c oxidase subunit VIIa polypeptide 2 like | 9167 | ENSG00000115944 |
| 74  | ENSG00000176340 | NA | COX8A | cytochrome c oxidase subunit VIIIA (ubiquitous) | 1351 | ENSG00000176340 |
| 75  | ENSG00000152234 | NA | ATP5A1 | ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle | 498 | ENSG00000152234 |
| 76  | ENSG00000168653 | NA | NDUFS5 | NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) | 4725 | ENSG00000168653 |
| 77  | ENSG00000241837 | NA | ATP5O | ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit | 539 | ENSG00000241837 |
| Database:biological process       Name:electron transport chain       ID:GO:0022900 | ||||||
|---|---|---|---|---|---|---|
| C=148; O=81; E=9.06; R=8.94; rawP=4.48e-59; adjP=4.12e-56 | ||||||
| Index | UserID | Value | Gene Symbol | Gene Name | EntrezGene | Ensembl |
| 1  | ENSG00000151366 | NA | NDUFC2 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa | 4718 | ENSG00000151366 |
| 2  | ENSG00000128609 | NA | NDUFA5 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa | 4698 | ENSG00000128609 |
| 3  | ENSG00000165264 | NA | NDUFB6 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa | 4712 | ENSG00000165264 |
| 4  | ENSG00000156467 | NA | UQCRB | ubiquinol-cytochrome c reductase binding protein | 7381 | ENSG00000156467 |
| 5  | ENSG00000184076 | NA | UQCR10 | ubiquinol-cytochrome c reductase, complex III subunit X | 29796 | ENSG00000184076 |
| 6  | ENSG00000136521 | NA | NDUFB5 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa | 4711 | ENSG00000136521 |
| 7  | ENSG00000004779 | NA | NDUFAB1 | NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa | 4706 | ENSG00000004779 |
| 8  | ENSG00000169020 | NA | ATP5I | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E | 521 | ENSG00000169020 |
| 9  | ENSG00000147123 | NA | NDUFB11 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa | 54539 | ENSG00000147123 |
| 10  | ENSG00000154723 | NA | ATP5J | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 | 522 | ENSG00000154723 |
| 11  | ENSG00000006695 | NA | COX10 | COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) | 1352 | ENSG00000006695 |
| 12  | ENSG00000073578 | NA | SDHA | succinate dehydrogenase complex, subunit A, flavoprotein (Fp) | 6389 | ENSG00000073578 |
| 13  | ENSG00000137714 | NA | FDX1 | ferredoxin 1 | 2230 | ENSG00000137714 |
| 14  | ENSG00000119013 | NA | NDUFB3 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa | 4709 | ENSG00000119013 |
| 15  | ENSG00000169021 | NA | UQCRFS1 | ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 | 7386 | ENSG00000169021 |
| 16  | ENSG00000140740 | NA | UQCRC2 | ubiquinol-cytochrome c reductase core protein II | 7385 | ENSG00000140740 |
| 17  | ENSG00000166136 | NA | NDUFB8 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa | 4714 | ENSG00000166136 |
| 18  | ENSG00000140374 | NA | ETFA | electron-transfer-flavoprotein, alpha polypeptide | 2108 | ENSG00000140374 |
| 19  | ENSG00000147684 | NA | NDUFB9 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa | 4715 | ENSG00000147684 |
| 20  | ENSG00000160194 | NA | NDUFV3 | NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa | 4731 | ENSG00000160194 |
| 21  | ENSG00000184983 | NA | NDUFA6 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa | 4700 | ENSG00000184983 |
| 22  | ENSG00000130414 | NA | NDUFA10 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa | 4705 | ENSG00000130414 |
| 23  | ENSG00000091140 | NA | DLD | dihydrolipoamide dehydrogenase | 1738 | ENSG00000091140 |
| 24  | ENSG00000158864 | NA | NDUFS2 | NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) | 4720 | ENSG00000158864 |
| 25  | ENSG00000139180 | NA | NDUFA9 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa | 4704 | ENSG00000139180 |
| 26  | ENSG00000127184 | NA | COX7C | cytochrome c oxidase subunit VIIc | 1350 | ENSG00000127184 |
| 27  | ENSG00000109390 | NA | NDUFC1 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa | 4717 | ENSG00000109390 |
| 28  | ENSG00000164405 | NA | UQCRQ | ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa | 27089 | ENSG00000164405 |
| 29  | ENSG00000124172 | NA | ATP5E | ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit | 514 | ENSG00000124172 |
| 30  | ENSG00000183648 | NA | NDUFB1 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa | 4707 | ENSG00000183648 |
| 31  | ENSG00000204370 | NA | SDHD | succinate dehydrogenase complex, subunit D, integral membrane protein | 6392 | ENSG00000204370 |
| 32  | ENSG00000116459 | NA | ATP5F1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 | 515 | ENSG00000116459 |
| 33  | ENSG00000099624 | NA | ATP5D | ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit | 513 | ENSG00000099624 |
| 34  | ENSG00000125356 | NA | NDUFA1 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa | 4694 | ENSG00000125356 |
| 35  | ENSG00000213619 | NA | NDUFS3 | NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) | 4722 | ENSG00000213619 |
| 36  | ENSG00000178741 | NA | COX5A | cytochrome c oxidase subunit Va | 9377 | ENSG00000178741 |
| 37  | ENSG00000173660 | NA | UQCRH | ubiquinol-cytochrome c reductase hinge protein | 7388 | ENSG00000173660 |
| 38  | ENSG00000099795 | NA | NDUFB7 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa | 4713 | ENSG00000099795 |
| 39  | ENSG00000119421 | NA | NDUFA8 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa | 4702 | ENSG00000119421 |
| 40  | ENSG00000100348 | NA | TXN2 | thioredoxin 2 | 25828 | ENSG00000100348 |
| 41  | ENSG00000126267 | NA | COX6B1 | cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) | 1340 | ENSG00000126267 |
| 42  | ENSG00000135940 | NA | COX5B | cytochrome c oxidase subunit Vb | 1329 | ENSG00000135940 |
| 43  | ENSG00000023228 | NA | NDUFS1 | NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) | 4719 | ENSG00000023228 |
| 44  | ENSG00000143252 | NA | SDHC | succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa | 6391 | ENSG00000143252 |
| 45  | ENSG00000145494 | NA | NDUFS6 | NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) | 4726 | ENSG00000145494 |
| 46  | ENSG00000115840 | NA | SLC25A12 | solute carrier family 25 (aspartate/glutamate carrier), member 12 | 8604 | ENSG00000115840 |
| 47  | ENSG00000131143 | NA | COX4I1 | cytochrome c oxidase subunit IV isoform 1 | 1327 | ENSG00000131143 |
| 48  | ENSG00000189043 | NA | NDUFA4 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa | 4697 | ENSG00000189043 |
| 49  | ENSG00000172115 | NA | CYCS | cytochrome c, somatic | 54205 | ENSG00000172115 |
| 50  | ENSG00000110955 | NA | ATP5B | ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide | 506 | ENSG00000110955 |
| 51  | ENSG00000164919 | NA | COX6C | cytochrome c oxidase subunit VIc | 1345 | ENSG00000164919 |
| 52  | ENSG00000105379 | NA | ETFB | electron-transfer-flavoprotein, beta polypeptide | 2109 | ENSG00000105379 |
| 53  | ENSG00000115286 | NA | NDUFS7 | NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) | 374291 | ENSG00000115286 |
| 54  | ENSG00000164258 | NA | NDUFS4 | NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) | 4724 | ENSG00000164258 |
| 55  | ENSG00000167792 | NA | NDUFV1 | NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa | 4723 | ENSG00000167792 |
| 56  | ENSG00000131495 | NA | NDUFA2 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa | 4695 | ENSG00000131495 |
| 57  | ENSG00000065518 | NA | NDUFB4 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa | 4710 | ENSG00000065518 |
| 58  | ENSG00000167863 | NA | ATP5H | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d | 10476 | ENSG00000167863 |
| 59  | ENSG00000090266 | NA | NDUFB2 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa | 4708 | ENSG00000090266 |
| 60  | ENSG00000110717 | NA | NDUFS8 | NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) | 4728 | ENSG00000110717 |
| 61  | ENSG00000131174 | NA | COX7B | cytochrome c oxidase subunit VIIb | 1349 | ENSG00000131174 |
| 62  | ENSG00000127540 | NA | UQCR11 | ubiquinol-cytochrome c reductase, complex III subunit XI | 10975 | ENSG00000127540 |
| 63  | ENSG00000179091 | NA | CYC1 | cytochrome c-1 | 1537 | ENSG00000179091 |
| 64  | ENSG00000184752 | NA | NDUFA12 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 | 55967 | ENSG00000184752 |
| 65  | ENSG00000170906 | NA | NDUFA3 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa | 4696 | ENSG00000170906 |
| 66  | ENSG00000091164 | NA | TXNL1 | thioredoxin-like 1 | 9352 | ENSG00000091164 |
| 67  | ENSG00000159199 | NA | ATP5G1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) | 516 | ENSG00000159199 |
| 68  | ENSG00000167283 | NA | ATP5L | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G | 10632 | ENSG00000167283 |
| 69  | ENSG00000010256 | NA | UQCRC1 | ubiquinol-cytochrome c reductase core protein I | 7384 | ENSG00000010256 |
| 70  | ENSG00000137806 | NA | NDUFAF1 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 | 51103 | ENSG00000137806 |
| 71  | ENSG00000241468 | NA | ATP5J2 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 | 9551 | ENSG00000241468 |
| 72  | ENSG00000103018 | NA | CYB5B | cytochrome b5 type B (outer mitochondrial membrane) | 80777 | ENSG00000103018 |
| 73  | ENSG00000140990 | NA | NDUFB10 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa | 4716 | ENSG00000140990 |
| 74  | ENSG00000117118 | NA | SDHB | succinate dehydrogenase complex, subunit B, iron sulfur (Ip) | 6390 | ENSG00000117118 |
| 75  | ENSG00000171503 | NA | ETFDH | electron-transferring-flavoprotein dehydrogenase | 2110 | ENSG00000171503 |
| 76  | ENSG00000165629 | NA | ATP5C1 | ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 | 509 | ENSG00000165629 |
| 77  | ENSG00000115944 | NA | COX7A2L | cytochrome c oxidase subunit VIIa polypeptide 2 like | 9167 | ENSG00000115944 |
| 78  | ENSG00000176340 | NA | COX8A | cytochrome c oxidase subunit VIIIA (ubiquitous) | 1351 | ENSG00000176340 |
| 79  | ENSG00000152234 | NA | ATP5A1 | ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle | 498 | ENSG00000152234 |
| 80  | ENSG00000168653 | NA | NDUFS5 | NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) | 4725 | ENSG00000168653 |
| 81  | ENSG00000241837 | NA | ATP5O | ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit | 539 | ENSG00000241837 |
| Database:biological process       Name:generation of precursor metabolites and energy       ID:GO:0006091 | ||||||
|---|---|---|---|---|---|---|
| C=451; O=134; E=27.62; R=4.85; rawP=3.19e-57; adjP=2.20e-54 | ||||||
| Index | UserID | Value | Gene Symbol | Gene Name | EntrezGene | Ensembl |
| 1  | ENSG00000165264 | NA | NDUFB6 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa | 4712 | ENSG00000165264 |
| 2  | ENSG00000156467 | NA | UQCRB | ubiquinol-cytochrome c reductase binding protein | 7381 | ENSG00000156467 |
| 3  | ENSG00000184076 | NA | UQCR10 | ubiquinol-cytochrome c reductase, complex III subunit X | 29796 | ENSG00000184076 |
| 4  | ENSG00000161281 | NA | COX7A1 | cytochrome c oxidase subunit VIIa polypeptide 1 (muscle) | 1346 | ENSG00000161281 |
| 5  | ENSG00000075415 | NA | SLC25A3 | solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 3 | 5250 | ENSG00000075415 |
| 6  | ENSG00000156885 | NA | COX6A2 | cytochrome c oxidase subunit VIa polypeptide 2 | 1339 | ENSG00000156885 |
| 7  | ENSG00000154723 | NA | ATP5J | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 | 522 | ENSG00000154723 |
| 8  | ENSG00000006695 | NA | COX10 | COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) | 1352 | ENSG00000006695 |
| 9  | ENSG00000140740 | NA | UQCRC2 | ubiquinol-cytochrome c reductase core protein II | 7385 | ENSG00000140740 |
| 10  | ENSG00000166136 | NA | NDUFB8 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa | 4714 | ENSG00000166136 |
| 11  | ENSG00000140374 | NA | ETFA | electron-transfer-flavoprotein, alpha polypeptide | 2108 | ENSG00000140374 |
| 12  | ENSG00000172340 | NA | SUCLG2 | succinate-CoA ligase, GDP-forming, beta subunit | 8801 | ENSG00000172340 |
| 13  | ENSG00000147684 | NA | NDUFB9 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa | 4715 | ENSG00000147684 |
| 14  | ENSG00000160194 | NA | NDUFV3 | NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa | 4731 | ENSG00000160194 |
| 15  | ENSG00000184983 | NA | NDUFA6 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa | 4700 | ENSG00000184983 |
| 16  | ENSG00000130414 | NA | NDUFA10 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa | 4705 | ENSG00000130414 |
| 17  | ENSG00000091140 | NA | DLD | dihydrolipoamide dehydrogenase | 1738 | ENSG00000091140 |
| 18  | ENSG00000165060 | NA | FXN | frataxin | 2395 | ENSG00000165060 |
| 19  | ENSG00000158864 | NA | NDUFS2 | NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) | 4720 | ENSG00000158864 |
| 20  | ENSG00000131828 | NA | PDHA1 | pyruvate dehydrogenase (lipoamide) alpha 1 | 5160 | ENSG00000131828 |
| 21  | ENSG00000109390 | NA | NDUFC1 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa | 4717 | ENSG00000109390 |
| 22  | ENSG00000176533 | NA | GNG7 | guanine nucleotide binding protein (G protein), gamma 7 | 2788 | ENSG00000176533 |
| 23  | ENSG00000091483 | NA | FH | fumarate hydratase | 2271 | ENSG00000091483 |
| 24  | ENSG00000181929 | NA | PRKAG1 | protein kinase, AMP-activated, gamma 1 non-catalytic subunit | 5571 | ENSG00000181929 |
| 25  | ENSG00000101440 | NA | ASIP | agouti signaling protein | 434 | ENSG00000101440 |
| 26  | ENSG00000119689 | NA | DLST | dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex) | 1743 | ENSG00000119689 |
| 27  | ENSG00000142082 | NA | SIRT3 | sirtuin 3 | 23410 | ENSG00000142082 |
| 28  | ENSG00000168291 | NA | PDHB | pyruvate dehydrogenase (lipoamide) beta | 5162 | ENSG00000168291 |
| 29  | ENSG00000116459 | NA | ATP5F1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 | 515 | ENSG00000116459 |
| 30  | ENSG00000138399 | NA | FASTKD1 | FAST kinase domains 1 | 79675 | ENSG00000138399 |
| 31  | ENSG00000151729 | NA | SLC25A4 | solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4 | 291 | ENSG00000151729 |
| 32  | ENSG00000112992 | NA | NNT | nicotinamide nucleotide transhydrogenase | 23530 | ENSG00000112992 |
| 33  | ENSG00000149925 | NA | ALDOA | aldolase A, fructose-bisphosphate | 226 | ENSG00000149925 |
| 34  | ENSG00000215251 | NA | FASTKD5 | FAST kinase domains 5 | 60493 | ENSG00000215251 |
| 35  | ENSG00000213619 | NA | NDUFS3 | NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) | 4722 | ENSG00000213619 |
| 36  | ENSG00000178741 | NA | COX5A | cytochrome c oxidase subunit Va | 9377 | ENSG00000178741 |
| 37  | ENSG00000173660 | NA | UQCRH | ubiquinol-cytochrome c reductase hinge protein | 7388 | ENSG00000173660 |
| 38  | ENSG00000133028 | NA | SCO1 | SCO cytochrome oxidase deficient homolog 1 (yeast) | 6341 | ENSG00000133028 |
| 39  | ENSG00000087250 | NA | MT3 | metallothionein 3 | 4504 | ENSG00000087250 |
| 40  | ENSG00000119421 | NA | NDUFA8 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa | 4702 | ENSG00000119421 |
| 41  | ENSG00000100348 | NA | TXN2 | thioredoxin 2 | 25828 | ENSG00000100348 |
| 42  | ENSG00000126267 | NA | COX6B1 | cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) | 1340 | ENSG00000126267 |
| 43  | ENSG00000135940 | NA | COX5B | cytochrome c oxidase subunit Vb | 1329 | ENSG00000135940 |
| 44  | ENSG00000145494 | NA | NDUFS6 | NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) | 4726 | ENSG00000145494 |
| 45  | ENSG00000172115 | NA | CYCS | cytochrome c, somatic | 54205 | ENSG00000172115 |
| 46  | ENSG00000189043 | NA | NDUFA4 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa | 4697 | ENSG00000189043 |
| 47  | ENSG00000131143 | NA | COX4I1 | cytochrome c oxidase subunit IV isoform 1 | 1327 | ENSG00000131143 |
| 48  | ENSG00000164919 | NA | COX6C | cytochrome c oxidase subunit VIc | 1345 | ENSG00000164919 |
| 49  | ENSG00000105379 | NA | ETFB | electron-transfer-flavoprotein, beta polypeptide | 2109 | ENSG00000105379 |
| 50  | ENSG00000115286 | NA | NDUFS7 | NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) | 374291 | ENSG00000115286 |
| 51  | ENSG00000164258 | NA | NDUFS4 | NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) | 4724 | ENSG00000164258 |
| 52  | ENSG00000155463 | NA | OXA1L | oxidase (cytochrome c) assembly 1-like | 5018 | ENSG00000155463 |
| 53  | ENSG00000167863 | NA | ATP5H | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d | 10476 | ENSG00000167863 |
| 54  | ENSG00000090266 | NA | NDUFB2 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa | 4708 | ENSG00000090266 |
| 55  | ENSG00000108515 | NA | ENO3 | enolase 3 (beta, muscle) | 2027 | ENSG00000108515 |
| 56  | ENSG00000179091 | NA | CYC1 | cytochrome c-1 | 1537 | ENSG00000179091 |
| 57  | ENSG00000127540 | NA | UQCR11 | ubiquinol-cytochrome c reductase, complex III subunit XI | 10975 | ENSG00000127540 |
| 58  | ENSG00000184752 | NA | NDUFA12 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 | 55967 | ENSG00000184752 |
| 59  | ENSG00000159199 | NA | ATP5G1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) | 516 | ENSG00000159199 |
| 60  | ENSG00000136143 | NA | SUCLA2 | succinate-CoA ligase, ADP-forming, beta subunit | 8803 | ENSG00000136143 |
| 61  | ENSG00000172331 | NA | BPGM | 2,3-bisphosphoglycerate mutase | 669 | ENSG00000172331 |
| 62  | ENSG00000067829 | NA | IDH3G | isocitrate dehydrogenase 3 (NAD+) gamma | 3421 | ENSG00000067829 |
| 63  | ENSG00000067225 | NA | PKM | pyruvate kinase, muscle | 5315 | ENSG00000067225 |
| 64  | ENSG00000103018 | NA | CYB5B | cytochrome b5 type B (outer mitochondrial membrane) | 80777 | ENSG00000103018 |
| 65  | ENSG00000140990 | NA | NDUFB10 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa | 4716 | ENSG00000140990 |
| 66  | ENSG00000066926 | NA | FECH | ferrochelatase | 2235 | ENSG00000066926 |
| 67  | ENSG00000087460 | NA | GNAS | GNAS complex locus | 2778 | ENSG00000087460 |
| 68  | ENSG00000138495 | NA | COX17 | COX17 cytochrome c oxidase assembly homolog (S. cerevisiae) | 10063 | ENSG00000138495 |
| 69  | ENSG00000117118 | NA | SDHB | succinate dehydrogenase complex, subunit B, iron sulfur (Ip) | 6390 | ENSG00000117118 |
| 70  | ENSG00000165629 | NA | ATP5C1 | ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 | 509 | ENSG00000165629 |
| 71  | ENSG00000115944 | NA | COX7A2L | cytochrome c oxidase subunit VIIa polypeptide 2 like | 9167 | ENSG00000115944 |
| 72  | ENSG00000148290 | NA | SURF1 | surfeit 1 | 6834 | ENSG00000148290 |
| 73  | ENSG00000014641 | NA | MDH1 | malate dehydrogenase 1, NAD (soluble) | 4190 | ENSG00000014641 |
| 74  | ENSG00000105220 | NA | GPI | glucose-6-phosphate isomerase | 2821 | ENSG00000105220 |
| 75  | ENSG00000152234 | NA | ATP5A1 | ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle | 498 | ENSG00000152234 |
| 76  | ENSG00000146729 | NA | GBAS | glioblastoma amplified sequence | 2631 | ENSG00000146729 |
| 77  | ENSG00000072778 | NA | ACADVL | acyl-CoA dehydrogenase, very long chain | 37 | ENSG00000072778 |
| 78  | ENSG00000128609 | NA | NDUFA5 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa | 4698 | ENSG00000128609 |
| 79  | ENSG00000151366 | NA | NDUFC2 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa | 4718 | ENSG00000151366 |
| 80  | ENSG00000163541 | NA | SUCLG1 | succinate-CoA ligase, alpha subunit | 8802 | ENSG00000163541 |
| 81  | ENSG00000146701 | NA | MDH2 | malate dehydrogenase 2, NAD (mitochondrial) | 4191 | ENSG00000146701 |
| 82  | ENSG00000136521 | NA | NDUFB5 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa | 4711 | ENSG00000136521 |
| 83  | ENSG00000182054 | NA | IDH2 | isocitrate dehydrogenase 2 (NADP+), mitochondrial | 3418 | ENSG00000182054 |
| 84  | ENSG00000169020 | NA | ATP5I | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E | 521 | ENSG00000169020 |
| 85  | ENSG00000004779 | NA | NDUFAB1 | NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa | 4706 | ENSG00000004779 |
| 86  | ENSG00000147123 | NA | NDUFB11 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa | 54539 | ENSG00000147123 |
| 87  | ENSG00000073578 | NA | SDHA | succinate dehydrogenase complex, subunit A, flavoprotein (Fp) | 6389 | ENSG00000073578 |
| 88  | ENSG00000137714 | NA | FDX1 | ferredoxin 1 | 2230 | ENSG00000137714 |
| 89  | ENSG00000119013 | NA | NDUFB3 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa | 4709 | ENSG00000119013 |
| 90  | ENSG00000169021 | NA | UQCRFS1 | ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 | 7386 | ENSG00000169021 |
| 91  | ENSG00000062485 | NA | CS | citrate synthase | 1431 | ENSG00000062485 |
| 92  | ENSG00000174021 | NA | GNG5 | guanine nucleotide binding protein (G protein), gamma 5 | 2787 | ENSG00000174021 |
| 93  | ENSG00000139180 | NA | NDUFA9 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa | 4704 | ENSG00000139180 |
| 94  | ENSG00000111640 | NA | GAPDH | glyceraldehyde-3-phosphate dehydrogenase | 2597 | ENSG00000111640 |
| 95  | ENSG00000127184 | NA | COX7C | cytochrome c oxidase subunit VIIc | 1350 | ENSG00000127184 |
| 96  | ENSG00000123836 | NA | PFKFB2 | 6-phosphofructo-2-kinase/fructose-2,6-biphosphatase 2 | 5208 | ENSG00000123836 |
| 97  | ENSG00000164405 | NA | UQCRQ | ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa | 27089 | ENSG00000164405 |
| 98  | ENSG00000122729 | NA | ACO1 | aconitase 1, soluble | 48 | ENSG00000122729 |
| 99  | ENSG00000124172 | NA | ATP5E | ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit | 514 | ENSG00000124172 |
| 100  | ENSG00000183648 | NA | NDUFB1 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa | 4707 | ENSG00000183648 |
| 101  | ENSG00000204370 | NA | SDHD | succinate dehydrogenase complex, subunit D, integral membrane protein | 6392 | ENSG00000204370 |
| 102  | ENSG00000099624 | NA | ATP5D | ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit | 513 | ENSG00000099624 |
| 103  | ENSG00000100412 | NA | ACO2 | aconitase 2, mitochondrial | 50 | ENSG00000100412 |
| 104  | ENSG00000125356 | NA | NDUFA1 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa | 4694 | ENSG00000125356 |
| 105  | ENSG00000099795 | NA | NDUFB7 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa | 4713 | ENSG00000099795 |
| 106  | ENSG00000143437 | NA | ARNT | aryl hydrocarbon receptor nuclear translocator | 405 | ENSG00000143437 |
| 107  | ENSG00000111669 | NA | TPI1 | triosephosphate isomerase 1 | 7167 | ENSG00000111669 |
| 108  | ENSG00000023228 | NA | NDUFS1 | NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) | 4719 | ENSG00000023228 |
| 109  | ENSG00000143252 | NA | SDHC | succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa | 6391 | ENSG00000143252 |
| 110  | ENSG00000151376 | NA | ME3 | malic enzyme 3, NADP(+)-dependent, mitochondrial | 10873 | ENSG00000151376 |
| 111  | ENSG00000115840 | NA | SLC25A12 | solute carrier family 25 (aspartate/glutamate carrier), member 12 | 8604 | ENSG00000115840 |
| 112  | ENSG00000250479 | NA | CHCHD10 | coiled-coil-helix-coiled-coil-helix domain containing 10 | 400916 | ENSG00000250479 |
| 113  | ENSG00000110955 | NA | ATP5B | ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide | 506 | ENSG00000110955 |
| 114  | ENSG00000173281 | NA | PPP1R3B | protein phosphatase 1, regulatory subunit 3B | 79660 | ENSG00000173281 |
| 115  | ENSG00000167792 | NA | NDUFV1 | NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa | 4723 | ENSG00000167792 |
| 116  | ENSG00000131495 | NA | NDUFA2 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa | 4695 | ENSG00000131495 |
| 117  | ENSG00000065518 | NA | NDUFB4 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa | 4710 | ENSG00000065518 |
| 118  | ENSG00000110717 | NA | NDUFS8 | NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) | 4728 | ENSG00000110717 |
| 119  | ENSG00000131174 | NA | COX7B | cytochrome c oxidase subunit VIIb | 1349 | ENSG00000131174 |
| 120  | ENSG00000170906 | NA | NDUFA3 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa | 4696 | ENSG00000170906 |
| 121  | ENSG00000150594 | NA | ADRA2A | adrenoceptor alpha 2A | 150 | ENSG00000150594 |
| 122  | ENSG00000111716 | NA | LDHB | lactate dehydrogenase B | 3945 | ENSG00000111716 |
| 123  | ENSG00000091164 | NA | TXNL1 | thioredoxin-like 1 | 9352 | ENSG00000091164 |
| 124  | ENSG00000167283 | NA | ATP5L | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G | 10632 | ENSG00000167283 |
| 125  | ENSG00000136270 | NA | TBRG4 | transforming growth factor beta regulator 4 | 9238 | ENSG00000136270 |
| 126  | ENSG00000010256 | NA | UQCRC1 | ubiquinol-cytochrome c reductase core protein I | 7384 | ENSG00000010256 |
| 127  | ENSG00000137806 | NA | NDUFAF1 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 | 51103 | ENSG00000137806 |
| 128  | ENSG00000241468 | NA | ATP5J2 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 | 9551 | ENSG00000241468 |
| 129  | ENSG00000171503 | NA | ETFDH | electron-transferring-flavoprotein dehydrogenase | 2110 | ENSG00000171503 |
| 130  | ENSG00000161533 | NA | ACOX1 | acyl-CoA oxidase 1, palmitoyl | 51 | ENSG00000161533 |
| 131  | ENSG00000176340 | NA | COX8A | cytochrome c oxidase subunit VIIIA (ubiquitous) | 1351 | ENSG00000176340 |
| 132  | ENSG00000168653 | NA | NDUFS5 | NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) | 4725 | ENSG00000168653 |
| 133  | ENSG00000101365 | NA | IDH3B | isocitrate dehydrogenase 3 (NAD+) beta | 3420 | ENSG00000101365 |
| 134  | ENSG00000241837 | NA | ATP5O | ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit | 539 | ENSG00000241837 |
| Database:biological process       Name:oxidation-reduction process       ID:GO:0055114 | ||||||
|---|---|---|---|---|---|---|
| C=558; O=147; E=34.17; R=4.30; rawP=1.92e-55; adjP=1.06e-52 | ||||||
| Index | UserID | Value | Gene Symbol | Gene Name | EntrezGene | Ensembl |
| 1  | ENSG00000165264 | NA | NDUFB6 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa | 4712 | ENSG00000165264 |
| 2  | ENSG00000156467 | NA | UQCRB | ubiquinol-cytochrome c reductase binding protein | 7381 | ENSG00000156467 |
| 3  | ENSG00000184076 | NA | UQCR10 | ubiquinol-cytochrome c reductase, complex III subunit X | 29796 | ENSG00000184076 |
| 4  | ENSG00000154723 | NA | ATP5J | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 | 522 | ENSG00000154723 |
| 5  | ENSG00000006695 | NA | COX10 | COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) | 1352 | ENSG00000006695 |
| 6  | ENSG00000167969 | NA | ECI1 | enoyl-CoA delta isomerase 1 | 1632 | ENSG00000167969 |
| 7  | ENSG00000139531 | NA | SUOX | sulfite oxidase | 6821 | ENSG00000139531 |
| 8  | ENSG00000140740 | NA | UQCRC2 | ubiquinol-cytochrome c reductase core protein II | 7385 | ENSG00000140740 |
| 9  | ENSG00000166136 | NA | NDUFB8 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa | 4714 | ENSG00000166136 |
| 10  | ENSG00000140374 | NA | ETFA | electron-transfer-flavoprotein, alpha polypeptide | 2108 | ENSG00000140374 |
| 11  | ENSG00000172340 | NA | SUCLG2 | succinate-CoA ligase, GDP-forming, beta subunit | 8801 | ENSG00000172340 |
| 12  | ENSG00000147684 | NA | NDUFB9 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa | 4715 | ENSG00000147684 |
| 13  | ENSG00000160194 | NA | NDUFV3 | NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa | 4731 | ENSG00000160194 |
| 14  | ENSG00000184983 | NA | NDUFA6 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa | 4700 | ENSG00000184983 |
| 15  | ENSG00000130414 | NA | NDUFA10 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa | 4705 | ENSG00000130414 |
| 16  | ENSG00000091140 | NA | DLD | dihydrolipoamide dehydrogenase | 1738 | ENSG00000091140 |
| 17  | ENSG00000165060 | NA | FXN | frataxin | 2395 | ENSG00000165060 |
| 18  | ENSG00000158864 | NA | NDUFS2 | NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) | 4720 | ENSG00000158864 |
| 19  | ENSG00000122971 | NA | ACADS | acyl-CoA dehydrogenase, C-2 to C-3 short chain | 35 | ENSG00000122971 |
| 20  | ENSG00000109390 | NA | NDUFC1 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa | 4717 | ENSG00000109390 |
| 21  | ENSG00000176533 | NA | GNG7 | guanine nucleotide binding protein (G protein), gamma 7 | 2788 | ENSG00000176533 |
| 22  | ENSG00000091483 | NA | FH | fumarate hydratase | 2271 | ENSG00000091483 |
| 23  | ENSG00000181929 | NA | PRKAG1 | protein kinase, AMP-activated, gamma 1 non-catalytic subunit | 5571 | ENSG00000181929 |
| 24  | ENSG00000119689 | NA | DLST | dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex) | 1743 | ENSG00000119689 |
| 25  | ENSG00000142082 | NA | SIRT3 | sirtuin 3 | 23410 | ENSG00000142082 |
| 26  | ENSG00000168291 | NA | PDHB | pyruvate dehydrogenase (lipoamide) beta | 5162 | ENSG00000168291 |
| 27  | ENSG00000116459 | NA | ATP5F1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 | 515 | ENSG00000116459 |
| 28  | ENSG00000138399 | NA | FASTKD1 | FAST kinase domains 1 | 79675 | ENSG00000138399 |
| 29  | ENSG00000151729 | NA | SLC25A4 | solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4 | 291 | ENSG00000151729 |
| 30  | ENSG00000112992 | NA | NNT | nicotinamide nucleotide transhydrogenase | 23530 | ENSG00000112992 |
| 31  | ENSG00000126432 | NA | PRDX5 | peroxiredoxin 5 | 25824 | ENSG00000126432 |
| 32  | ENSG00000215251 | NA | FASTKD5 | FAST kinase domains 5 | 60493 | ENSG00000215251 |
| 33  | ENSG00000213619 | NA | NDUFS3 | NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) | 4722 | ENSG00000213619 |
| 34  | ENSG00000178741 | NA | COX5A | cytochrome c oxidase subunit Va | 9377 | ENSG00000178741 |
| 35  | ENSG00000173660 | NA | UQCRH | ubiquinol-cytochrome c reductase hinge protein | 7388 | ENSG00000173660 |
| 36  | ENSG00000087250 | NA | MT3 | metallothionein 3 | 4504 | ENSG00000087250 |
| 37  | ENSG00000119421 | NA | NDUFA8 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa | 4702 | ENSG00000119421 |
| 38  | ENSG00000100348 | NA | TXN2 | thioredoxin 2 | 25828 | ENSG00000100348 |
| 39  | ENSG00000126267 | NA | COX6B1 | cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) | 1340 | ENSG00000126267 |
| 40  | ENSG00000135940 | NA | COX5B | cytochrome c oxidase subunit Vb | 1329 | ENSG00000135940 |
| 41  | ENSG00000113790 | NA | EHHADH | enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase | 1962 | ENSG00000113790 |
| 42  | ENSG00000145494 | NA | NDUFS6 | NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) | 4726 | ENSG00000145494 |
| 43  | ENSG00000172115 | NA | CYCS | cytochrome c, somatic | 54205 | ENSG00000172115 |
| 44  | ENSG00000189043 | NA | NDUFA4 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa | 4697 | ENSG00000189043 |
| 45  | ENSG00000131143 | NA | COX4I1 | cytochrome c oxidase subunit IV isoform 1 | 1327 | ENSG00000131143 |
| 46  | ENSG00000164919 | NA | COX6C | cytochrome c oxidase subunit VIc | 1345 | ENSG00000164919 |
| 47  | ENSG00000105379 | NA | ETFB | electron-transfer-flavoprotein, beta polypeptide | 2109 | ENSG00000105379 |
| 48  | ENSG00000115286 | NA | NDUFS7 | NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) | 374291 | ENSG00000115286 |
| 49  | ENSG00000164258 | NA | NDUFS4 | NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) | 4724 | ENSG00000164258 |
| 50  | ENSG00000155463 | NA | OXA1L | oxidase (cytochrome c) assembly 1-like | 5018 | ENSG00000155463 |
| 51  | ENSG00000167863 | NA | ATP5H | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d | 10476 | ENSG00000167863 |
| 52  | ENSG00000090266 | NA | NDUFB2 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa | 4708 | ENSG00000090266 |
| 53  | ENSG00000179091 | NA | CYC1 | cytochrome c-1 | 1537 | ENSG00000179091 |
| 54  | ENSG00000127540 | NA | UQCR11 | ubiquinol-cytochrome c reductase, complex III subunit XI | 10975 | ENSG00000127540 |
| 55  | ENSG00000184752 | NA | NDUFA12 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 | 55967 | ENSG00000184752 |
| 56  | ENSG00000159199 | NA | ATP5G1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) | 516 | ENSG00000159199 |
| 57  | ENSG00000136143 | NA | SUCLA2 | succinate-CoA ligase, ADP-forming, beta subunit | 8803 | ENSG00000136143 |
| 58  | ENSG00000003137 | NA | CYP26B1 | cytochrome P450, family 26, subfamily B, polypeptide 1 | 56603 | ENSG00000003137 |
| 59  | ENSG00000175198 | NA | PCCA | propionyl CoA carboxylase, alpha polypeptide | 5095 | ENSG00000175198 |
| 60  | ENSG00000067829 | NA | IDH3G | isocitrate dehydrogenase 3 (NAD+) gamma | 3421 | ENSG00000067829 |
| 61  | ENSG00000082146 | NA | STRADB | STE20-related kinase adaptor beta | 55437 | ENSG00000082146 |
| 62  | ENSG00000116171 | NA | SCP2 | sterol carrier protein 2 | 6342 | ENSG00000116171 |
| 63  | ENSG00000103018 | NA | CYB5B | cytochrome b5 type B (outer mitochondrial membrane) | 80777 | ENSG00000103018 |
| 64  | ENSG00000140990 | NA | NDUFB10 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa | 4716 | ENSG00000140990 |
| 65  | ENSG00000157326 | NA | DHRS4 | dehydrogenase/reductase (SDR family) member 4 | 10901 | ENSG00000157326 |
| 66  | ENSG00000135297 | NA | MTO1 | mitochondrial translation optimization 1 homolog (S. cerevisiae) | 25821 | ENSG00000135297 |
| 67  | ENSG00000087460 | NA | GNAS | GNAS complex locus | 2778 | ENSG00000087460 |
| 68  | ENSG00000117118 | NA | SDHB | succinate dehydrogenase complex, subunit B, iron sulfur (Ip) | 6390 | ENSG00000117118 |
| 69  | ENSG00000165629 | NA | ATP5C1 | ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 | 509 | ENSG00000165629 |
| 70  | ENSG00000115944 | NA | COX7A2L | cytochrome c oxidase subunit VIIa polypeptide 2 like | 9167 | ENSG00000115944 |
| 71  | ENSG00000148290 | NA | SURF1 | surfeit 1 | 6834 | ENSG00000148290 |
| 72  | ENSG00000014641 | NA | MDH1 | malate dehydrogenase 1, NAD (soluble) | 4190 | ENSG00000014641 |
| 73  | ENSG00000152234 | NA | ATP5A1 | ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle | 498 | ENSG00000152234 |
| 74  | ENSG00000072778 | NA | ACADVL | acyl-CoA dehydrogenase, very long chain | 37 | ENSG00000072778 |
| 75  | ENSG00000154930 | NA | ACSS1 | acyl-CoA synthetase short-chain family member 1 | 84532 | ENSG00000154930 |
| 76  | ENSG00000128609 | NA | NDUFA5 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa | 4698 | ENSG00000128609 |
| 77  | ENSG00000151366 | NA | NDUFC2 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa | 4718 | ENSG00000151366 |
| 78  | ENSG00000163541 | NA | SUCLG1 | succinate-CoA ligase, alpha subunit | 8802 | ENSG00000163541 |
| 79  | ENSG00000146701 | NA | MDH2 | malate dehydrogenase 2, NAD (mitochondrial) | 4191 | ENSG00000146701 |
| 80  | ENSG00000136521 | NA | NDUFB5 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa | 4711 | ENSG00000136521 |
| 81  | ENSG00000182054 | NA | IDH2 | isocitrate dehydrogenase 2 (NADP+), mitochondrial | 3418 | ENSG00000182054 |
| 82  | ENSG00000169020 | NA | ATP5I | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E | 521 | ENSG00000169020 |
| 83  | ENSG00000004779 | NA | NDUFAB1 | NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa | 4706 | ENSG00000004779 |
| 84  | ENSG00000004961 | NA | HCCS | holocytochrome c synthase | 3052 | ENSG00000004961 |
| 85  | ENSG00000147123 | NA | NDUFB11 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa | 54539 | ENSG00000147123 |
| 86  | ENSG00000073578 | NA | SDHA | succinate dehydrogenase complex, subunit A, flavoprotein (Fp) | 6389 | ENSG00000073578 |
| 87  | ENSG00000137714 | NA | FDX1 | ferredoxin 1 | 2230 | ENSG00000137714 |
| 88  | ENSG00000119013 | NA | NDUFB3 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa | 4709 | ENSG00000119013 |
| 89  | ENSG00000169021 | NA | UQCRFS1 | ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 | 7386 | ENSG00000169021 |
| 90  | ENSG00000104325 | NA | DECR1 | 2,4-dienoyl CoA reductase 1, mitochondrial | 1666 | ENSG00000104325 |
| 91  | ENSG00000062485 | NA | CS | citrate synthase | 1431 | ENSG00000062485 |
| 92  | ENSG00000122691 | NA | TWIST1 | twist homolog 1 (Drosophila) | 7291 | ENSG00000122691 |
| 93  | ENSG00000174021 | NA | GNG5 | guanine nucleotide binding protein (G protein), gamma 5 | 2787 | ENSG00000174021 |
| 94  | ENSG00000167468 | NA | GPX4 | glutathione peroxidase 4 | 2879 | ENSG00000167468 |
| 95  | ENSG00000124370 | NA | MCEE | methylmalonyl CoA epimerase | 84693 | ENSG00000124370 |
| 96  | ENSG00000139180 | NA | NDUFA9 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa | 4704 | ENSG00000139180 |
| 97  | ENSG00000127184 | NA | COX7C | cytochrome c oxidase subunit VIIc | 1350 | ENSG00000127184 |
| 98  | ENSG00000164405 | NA | UQCRQ | ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa | 27089 | ENSG00000164405 |
| 99  | ENSG00000122729 | NA | ACO1 | aconitase 1, soluble | 48 | ENSG00000122729 |
| 100  | ENSG00000124172 | NA | ATP5E | ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit | 514 | ENSG00000124172 |
| 101  | ENSG00000183648 | NA | NDUFB1 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa | 4707 | ENSG00000183648 |
| 102  | ENSG00000204370 | NA | SDHD | succinate dehydrogenase complex, subunit D, integral membrane protein | 6392 | ENSG00000204370 |
| 103  | ENSG00000099624 | NA | ATP5D | ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit | 513 | ENSG00000099624 |
| 104  | ENSG00000137106 | NA | GRHPR | glyoxylate reductase/hydroxypyruvate reductase | 9380 | ENSG00000137106 |
| 105  | ENSG00000100412 | NA | ACO2 | aconitase 2, mitochondrial | 50 | ENSG00000100412 |
| 106  | ENSG00000169738 | NA | DCXR | dicarbonyl/L-xylulose reductase | 51181 | ENSG00000169738 |
| 107  | ENSG00000160211 | NA | G6PD | glucose-6-phosphate dehydrogenase | 2539 | ENSG00000160211 |
| 108  | ENSG00000125356 | NA | NDUFA1 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa | 4694 | ENSG00000125356 |
| 109  | ENSG00000100601 | NA | ALKBH1 | alkB, alkylation repair homolog 1 (E. coli) | 8846 | ENSG00000100601 |
| 110  | ENSG00000099795 | NA | NDUFB7 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa | 4713 | ENSG00000099795 |
| 111  | ENSG00000111669 | NA | TPI1 | triosephosphate isomerase 1 | 7167 | ENSG00000111669 |
| 112  | ENSG00000153574 | NA | RPIA | ribose 5-phosphate isomerase A | 22934 | ENSG00000153574 |
| 113  | ENSG00000023228 | NA | NDUFS1 | NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) | 4719 | ENSG00000023228 |
| 114  | ENSG00000143252 | NA | SDHC | succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa | 6391 | ENSG00000143252 |
| 115  | ENSG00000151376 | NA | ME3 | malic enzyme 3, NADP(+)-dependent, mitochondrial | 10873 | ENSG00000151376 |
| 116  | ENSG00000115840 | NA | SLC25A12 | solute carrier family 25 (aspartate/glutamate carrier), member 12 | 8604 | ENSG00000115840 |
| 117  | ENSG00000110955 | NA | ATP5B | ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide | 506 | ENSG00000110955 |
| 118  | ENSG00000060971 | NA | ACAA1 | acetyl-CoA acyltransferase 1 | 30 | ENSG00000060971 |
| 119  | ENSG00000197894 | NA | ADH5 | alcohol dehydrogenase 5 (class III), chi polypeptide | 128 | ENSG00000197894 |
| 120  | ENSG00000173281 | NA | PPP1R3B | protein phosphatase 1, regulatory subunit 3B | 79660 | ENSG00000173281 |
| 121  | ENSG00000112357 | NA | PEX7 | peroxisomal biogenesis factor 7 | 5191 | ENSG00000112357 |
| 122  | ENSG00000167792 | NA | NDUFV1 | NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa | 4723 | ENSG00000167792 |
| 123  | ENSG00000131495 | NA | NDUFA2 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa | 4695 | ENSG00000131495 |
| 124  | ENSG00000065518 | NA | NDUFB4 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa | 4710 | ENSG00000065518 |
| 125  | ENSG00000095321 | NA | CRAT | carnitine O-acetyltransferase | 1384 | ENSG00000095321 |
| 126  | ENSG00000110717 | NA | NDUFS8 | NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) | 4728 | ENSG00000110717 |
| 127  | ENSG00000197580 | NA | BCO2 | beta-carotene oxygenase 2 | 83875 | ENSG00000197580 |
| 128  | ENSG00000131174 | NA | COX7B | cytochrome c oxidase subunit VIIb | 1349 | ENSG00000131174 |
| 129  | ENSG00000170906 | NA | NDUFA3 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa | 4696 | ENSG00000170906 |
| 130  | ENSG00000150594 | NA | ADRA2A | adrenoceptor alpha 2A | 150 | ENSG00000150594 |
| 131  | ENSG00000091164 | NA | TXNL1 | thioredoxin-like 1 | 9352 | ENSG00000091164 |
| 132  | ENSG00000167283 | NA | ATP5L | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G | 10632 | ENSG00000167283 |
| 133  | ENSG00000114054 | NA | PCCB | propionyl CoA carboxylase, beta polypeptide | 5096 | ENSG00000114054 |
| 134  | ENSG00000111275 | NA | ALDH2 | aldehyde dehydrogenase 2 family (mitochondrial) | 217 | ENSG00000111275 |
| 135  | ENSG00000127884 | NA | ECHS1 | enoyl CoA hydratase, short chain, 1, mitochondrial | 1892 | ENSG00000127884 |
| 136  | ENSG00000136270 | NA | TBRG4 | transforming growth factor beta regulator 4 | 9238 | ENSG00000136270 |
| 137  | ENSG00000010256 | NA | UQCRC1 | ubiquinol-cytochrome c reductase core protein I | 7384 | ENSG00000010256 |
| 138  | ENSG00000137806 | NA | NDUFAF1 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 | 51103 | ENSG00000137806 |
| 139  | ENSG00000241468 | NA | ATP5J2 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 | 9551 | ENSG00000241468 |
| 140  | ENSG00000104823 | NA | ECH1 | enoyl CoA hydratase 1, peroxisomal | 1891 | ENSG00000104823 |
| 141  | ENSG00000171503 | NA | ETFDH | electron-transferring-flavoprotein dehydrogenase | 2110 | ENSG00000171503 |
| 142  | ENSG00000138796 | NA | HADH | hydroxyacyl-CoA dehydrogenase | 3033 | ENSG00000138796 |
| 143  | ENSG00000161533 | NA | ACOX1 | acyl-CoA oxidase 1, palmitoyl | 51 | ENSG00000161533 |
| 144  | ENSG00000176340 | NA | COX8A | cytochrome c oxidase subunit VIIIA (ubiquitous) | 1351 | ENSG00000176340 |
| 145  | ENSG00000168653 | NA | NDUFS5 | NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) | 4725 | ENSG00000168653 |
| 146  | ENSG00000101365 | NA | IDH3B | isocitrate dehydrogenase 3 (NAD+) beta | 3420 | ENSG00000101365 |
| 147  | ENSG00000241837 | NA | ATP5O | ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit | 539 | ENSG00000241837 |
| Database:biological process       Name:energy derivation by oxidation of organic compounds       ID:GO:0015980 | ||||||
|---|---|---|---|---|---|---|
| C=329; O=108; E=20.15; R=5.36; rawP=1.05e-50; adjP=4.83e-48 | ||||||
| Index | UserID | Value | Gene Symbol | Gene Name | EntrezGene | Ensembl |
| 1  | ENSG00000151366 | NA | NDUFC2 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa | 4718 | ENSG00000151366 |
| 2  | ENSG00000128609 | NA | NDUFA5 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa | 4698 | ENSG00000128609 |
| 3  | ENSG00000165264 | NA | NDUFB6 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa | 4712 | ENSG00000165264 |
| 4  | ENSG00000163541 | NA | SUCLG1 | succinate-CoA ligase, alpha subunit | 8802 | ENSG00000163541 |
| 5  | ENSG00000156467 | NA | UQCRB | ubiquinol-cytochrome c reductase binding protein | 7381 | ENSG00000156467 |
| 6  | ENSG00000146701 | NA | MDH2 | malate dehydrogenase 2, NAD (mitochondrial) | 4191 | ENSG00000146701 |
| 7  | ENSG00000184076 | NA | UQCR10 | ubiquinol-cytochrome c reductase, complex III subunit X | 29796 | ENSG00000184076 |
| 8  | ENSG00000136521 | NA | NDUFB5 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa | 4711 | ENSG00000136521 |
| 9  | ENSG00000004779 | NA | NDUFAB1 | NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa | 4706 | ENSG00000004779 |
| 10  | ENSG00000169020 | NA | ATP5I | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E | 521 | ENSG00000169020 |
| 11  | ENSG00000182054 | NA | IDH2 | isocitrate dehydrogenase 2 (NADP+), mitochondrial | 3418 | ENSG00000182054 |
| 12  | ENSG00000147123 | NA | NDUFB11 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa | 54539 | ENSG00000147123 |
| 13  | ENSG00000154723 | NA | ATP5J | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 | 522 | ENSG00000154723 |
| 14  | ENSG00000006695 | NA | COX10 | COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) | 1352 | ENSG00000006695 |
| 15  | ENSG00000073578 | NA | SDHA | succinate dehydrogenase complex, subunit A, flavoprotein (Fp) | 6389 | ENSG00000073578 |
| 16  | ENSG00000119013 | NA | NDUFB3 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa | 4709 | ENSG00000119013 |
| 17  | ENSG00000169021 | NA | UQCRFS1 | ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 | 7386 | ENSG00000169021 |
| 18  | ENSG00000062485 | NA | CS | citrate synthase | 1431 | ENSG00000062485 |
| 19  | ENSG00000140740 | NA | UQCRC2 | ubiquinol-cytochrome c reductase core protein II | 7385 | ENSG00000140740 |
| 20  | ENSG00000166136 | NA | NDUFB8 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa | 4714 | ENSG00000166136 |
| 21  | ENSG00000140374 | NA | ETFA | electron-transfer-flavoprotein, alpha polypeptide | 2108 | ENSG00000140374 |
| 22  | ENSG00000172340 | NA | SUCLG2 | succinate-CoA ligase, GDP-forming, beta subunit | 8801 | ENSG00000172340 |
| 23  | ENSG00000147684 | NA | NDUFB9 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa | 4715 | ENSG00000147684 |
| 24  | ENSG00000160194 | NA | NDUFV3 | NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa | 4731 | ENSG00000160194 |
| 25  | ENSG00000184983 | NA | NDUFA6 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa | 4700 | ENSG00000184983 |
| 26  | ENSG00000130414 | NA | NDUFA10 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa | 4705 | ENSG00000130414 |
| 27  | ENSG00000091140 | NA | DLD | dihydrolipoamide dehydrogenase | 1738 | ENSG00000091140 |
| 28  | ENSG00000165060 | NA | FXN | frataxin | 2395 | ENSG00000165060 |
| 29  | ENSG00000174021 | NA | GNG5 | guanine nucleotide binding protein (G protein), gamma 5 | 2787 | ENSG00000174021 |
| 30  | ENSG00000158864 | NA | NDUFS2 | NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) | 4720 | ENSG00000158864 |
| 31  | ENSG00000139180 | NA | NDUFA9 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa | 4704 | ENSG00000139180 |
| 32  | ENSG00000127184 | NA | COX7C | cytochrome c oxidase subunit VIIc | 1350 | ENSG00000127184 |
| 33  | ENSG00000109390 | NA | NDUFC1 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa | 4717 | ENSG00000109390 |
| 34  | ENSG00000164405 | NA | UQCRQ | ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa | 27089 | ENSG00000164405 |
| 35  | ENSG00000176533 | NA | GNG7 | guanine nucleotide binding protein (G protein), gamma 7 | 2788 | ENSG00000176533 |
| 36  | ENSG00000091483 | NA | FH | fumarate hydratase | 2271 | ENSG00000091483 |
| 37  | ENSG00000122729 | NA | ACO1 | aconitase 1, soluble | 48 | ENSG00000122729 |
| 38  | ENSG00000124172 | NA | ATP5E | ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit | 514 | ENSG00000124172 |
| 39  | ENSG00000183648 | NA | NDUFB1 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa | 4707 | ENSG00000183648 |
| 40  | ENSG00000142082 | NA | SIRT3 | sirtuin 3 | 23410 | ENSG00000142082 |
| 41  | ENSG00000119689 | NA | DLST | dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex) | 1743 | ENSG00000119689 |
| 42  | ENSG00000168291 | NA | PDHB | pyruvate dehydrogenase (lipoamide) beta | 5162 | ENSG00000168291 |
| 43  | ENSG00000099624 | NA | ATP5D | ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit | 513 | ENSG00000099624 |
| 44  | ENSG00000204370 | NA | SDHD | succinate dehydrogenase complex, subunit D, integral membrane protein | 6392 | ENSG00000204370 |
| 45  | ENSG00000116459 | NA | ATP5F1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 | 515 | ENSG00000116459 |
| 46  | ENSG00000100412 | NA | ACO2 | aconitase 2, mitochondrial | 50 | ENSG00000100412 |
| 47  | ENSG00000138399 | NA | FASTKD1 | FAST kinase domains 1 | 79675 | ENSG00000138399 |
| 48  | ENSG00000151729 | NA | SLC25A4 | solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4 | 291 | ENSG00000151729 |
| 49  | ENSG00000112992 | NA | NNT | nicotinamide nucleotide transhydrogenase | 23530 | ENSG00000112992 |
| 50  | ENSG00000125356 | NA | NDUFA1 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa | 4694 | ENSG00000125356 |
| 51  | ENSG00000215251 | NA | FASTKD5 | FAST kinase domains 5 | 60493 | ENSG00000215251 |
| 52  | ENSG00000213619 | NA | NDUFS3 | NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) | 4722 | ENSG00000213619 |
| 53  | ENSG00000178741 | NA | COX5A | cytochrome c oxidase subunit Va | 9377 | ENSG00000178741 |
| 54  | ENSG00000173660 | NA | UQCRH | ubiquinol-cytochrome c reductase hinge protein | 7388 | ENSG00000173660 |
| 55  | ENSG00000087250 | NA | MT3 | metallothionein 3 | 4504 | ENSG00000087250 |
| 56  | ENSG00000099795 | NA | NDUFB7 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa | 4713 | ENSG00000099795 |
| 57  | ENSG00000119421 | NA | NDUFA8 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa | 4702 | ENSG00000119421 |
| 58  | ENSG00000126267 | NA | COX6B1 | cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) | 1340 | ENSG00000126267 |
| 59  | ENSG00000135940 | NA | COX5B | cytochrome c oxidase subunit Vb | 1329 | ENSG00000135940 |
| 60  | ENSG00000023228 | NA | NDUFS1 | NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) | 4719 | ENSG00000023228 |
| 61  | ENSG00000143252 | NA | SDHC | succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa | 6391 | ENSG00000143252 |
| 62  | ENSG00000151376 | NA | ME3 | malic enzyme 3, NADP(+)-dependent, mitochondrial | 10873 | ENSG00000151376 |
| 63  | ENSG00000145494 | NA | NDUFS6 | NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) | 4726 | ENSG00000145494 |
| 64  | ENSG00000115840 | NA | SLC25A12 | solute carrier family 25 (aspartate/glutamate carrier), member 12 | 8604 | ENSG00000115840 |
| 65  | ENSG00000131143 | NA | COX4I1 | cytochrome c oxidase subunit IV isoform 1 | 1327 | ENSG00000131143 |
| 66  | ENSG00000189043 | NA | NDUFA4 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa | 4697 | ENSG00000189043 |
| 67  | ENSG00000172115 | NA | CYCS | cytochrome c, somatic | 54205 | ENSG00000172115 |
| 68  | ENSG00000110955 | NA | ATP5B | ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide | 506 | ENSG00000110955 |
| 69  | ENSG00000164919 | NA | COX6C | cytochrome c oxidase subunit VIc | 1345 | ENSG00000164919 |
| 70  | ENSG00000105379 | NA | ETFB | electron-transfer-flavoprotein, beta polypeptide | 2109 | ENSG00000105379 |
| 71  | ENSG00000115286 | NA | NDUFS7 | NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) | 374291 | ENSG00000115286 |
| 72  | ENSG00000164258 | NA | NDUFS4 | NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) | 4724 | ENSG00000164258 |
| 73  | ENSG00000173281 | NA | PPP1R3B | protein phosphatase 1, regulatory subunit 3B | 79660 | ENSG00000173281 |
| 74  | ENSG00000167792 | NA | NDUFV1 | NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa | 4723 | ENSG00000167792 |
| 75  | ENSG00000131495 | NA | NDUFA2 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa | 4695 | ENSG00000131495 |
| 76  | ENSG00000065518 | NA | NDUFB4 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa | 4710 | ENSG00000065518 |
| 77  | ENSG00000155463 | NA | OXA1L | oxidase (cytochrome c) assembly 1-like | 5018 | ENSG00000155463 |
| 78  | ENSG00000167863 | NA | ATP5H | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d | 10476 | ENSG00000167863 |
| 79  | ENSG00000090266 | NA | NDUFB2 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa | 4708 | ENSG00000090266 |
| 80  | ENSG00000110717 | NA | NDUFS8 | NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) | 4728 | ENSG00000110717 |
| 81  | ENSG00000127540 | NA | UQCR11 | ubiquinol-cytochrome c reductase, complex III subunit XI | 10975 | ENSG00000127540 |
| 82  | ENSG00000131174 | NA | COX7B | cytochrome c oxidase subunit VIIb | 1349 | ENSG00000131174 |
| 83  | ENSG00000179091 | NA | CYC1 | cytochrome c-1 | 1537 | ENSG00000179091 |
| 84  | ENSG00000170906 | NA | NDUFA3 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa | 4696 | ENSG00000170906 |
| 85  | ENSG00000184752 | NA | NDUFA12 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 | 55967 | ENSG00000184752 |
| 86  | ENSG00000150594 | NA | ADRA2A | adrenoceptor alpha 2A | 150 | ENSG00000150594 |
| 87  | ENSG00000159199 | NA | ATP5G1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) | 516 | ENSG00000159199 |
| 88  | ENSG00000136143 | NA | SUCLA2 | succinate-CoA ligase, ADP-forming, beta subunit | 8803 | ENSG00000136143 |
| 89  | ENSG00000167283 | NA | ATP5L | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G | 10632 | ENSG00000167283 |
| 90  | ENSG00000067829 | NA | IDH3G | isocitrate dehydrogenase 3 (NAD+) gamma | 3421 | ENSG00000067829 |
| 91  | ENSG00000136270 | NA | TBRG4 | transforming growth factor beta regulator 4 | 9238 | ENSG00000136270 |
| 92  | ENSG00000010256 | NA | UQCRC1 | ubiquinol-cytochrome c reductase core protein I | 7384 | ENSG00000010256 |
| 93  | ENSG00000137806 | NA | NDUFAF1 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 | 51103 | ENSG00000137806 |
| 94  | ENSG00000241468 | NA | ATP5J2 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 | 9551 | ENSG00000241468 |
| 95  | ENSG00000140990 | NA | NDUFB10 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa | 4716 | ENSG00000140990 |
| 96  | ENSG00000087460 | NA | GNAS | GNAS complex locus | 2778 | ENSG00000087460 |
| 97  | ENSG00000117118 | NA | SDHB | succinate dehydrogenase complex, subunit B, iron sulfur (Ip) | 6390 | ENSG00000117118 |
| 98  | ENSG00000171503 | NA | ETFDH | electron-transferring-flavoprotein dehydrogenase | 2110 | ENSG00000171503 |
| 99  | ENSG00000165629 | NA | ATP5C1 | ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 | 509 | ENSG00000165629 |
| 100  | ENSG00000115944 | NA | COX7A2L | cytochrome c oxidase subunit VIIa polypeptide 2 like | 9167 | ENSG00000115944 |
| 101  | ENSG00000176340 | NA | COX8A | cytochrome c oxidase subunit VIIIA (ubiquitous) | 1351 | ENSG00000176340 |
| 102  | ENSG00000148290 | NA | SURF1 | surfeit 1 | 6834 | ENSG00000148290 |
| 103  | ENSG00000014641 | NA | MDH1 | malate dehydrogenase 1, NAD (soluble) | 4190 | ENSG00000014641 |
| 104  | ENSG00000168653 | NA | NDUFS5 | NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) | 4725 | ENSG00000168653 |
| 105  | ENSG00000152234 | NA | ATP5A1 | ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle | 498 | ENSG00000152234 |
| 106  | ENSG00000101365 | NA | IDH3B | isocitrate dehydrogenase 3 (NAD+) beta | 3420 | ENSG00000101365 |
| 107  | ENSG00000072778 | NA | ACADVL | acyl-CoA dehydrogenase, very long chain | 37 | ENSG00000072778 |
| 108  | ENSG00000241837 | NA | ATP5O | ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit | 539 | ENSG00000241837 |
| Database:biological process       Name:oxidative phosphorylation       ID:GO:0006119 | ||||||
|---|---|---|---|---|---|---|
| C=69; O=47; E=4.23; R=11.12; rawP=5.01e-41; adjP=1.98e-38 | ||||||
| Index | UserID | Value | Gene Symbol | Gene Name | EntrezGene | Ensembl |
| 1  | ENSG00000151366 | NA | NDUFC2 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa | 4718 | ENSG00000151366 |
| 2  | ENSG00000128609 | NA | NDUFA5 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa | 4698 | ENSG00000128609 |
| 3  | ENSG00000023228 | NA | NDUFS1 | NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) | 4719 | ENSG00000023228 |
| 4  | ENSG00000165264 | NA | NDUFB6 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa | 4712 | ENSG00000165264 |
| 5  | ENSG00000156467 | NA | UQCRB | ubiquinol-cytochrome c reductase binding protein | 7381 | ENSG00000156467 |
| 6  | ENSG00000184076 | NA | UQCR10 | ubiquinol-cytochrome c reductase, complex III subunit X | 29796 | ENSG00000184076 |
| 7  | ENSG00000145494 | NA | NDUFS6 | NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) | 4726 | ENSG00000145494 |
| 8  | ENSG00000136521 | NA | NDUFB5 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa | 4711 | ENSG00000136521 |
| 9  | ENSG00000250479 | NA | CHCHD10 | coiled-coil-helix-coiled-coil-helix domain containing 10 | 400916 | ENSG00000250479 |
| 10  | ENSG00000004779 | NA | NDUFAB1 | NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa | 4706 | ENSG00000004779 |
| 11  | ENSG00000189043 | NA | NDUFA4 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa | 4697 | ENSG00000189043 |
| 12  | ENSG00000006695 | NA | COX10 | COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) | 1352 | ENSG00000006695 |
| 13  | ENSG00000115286 | NA | NDUFS7 | NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) | 374291 | ENSG00000115286 |
| 14  | ENSG00000164258 | NA | NDUFS4 | NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) | 4724 | ENSG00000164258 |
| 15  | ENSG00000119013 | NA | NDUFB3 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa | 4709 | ENSG00000119013 |
| 16  | ENSG00000167792 | NA | NDUFV1 | NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa | 4723 | ENSG00000167792 |
| 17  | ENSG00000131495 | NA | NDUFA2 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa | 4695 | ENSG00000131495 |
| 18  | ENSG00000065518 | NA | NDUFB4 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa | 4710 | ENSG00000065518 |
| 19  | ENSG00000090266 | NA | NDUFB2 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa | 4708 | ENSG00000090266 |
| 20  | ENSG00000140740 | NA | UQCRC2 | ubiquinol-cytochrome c reductase core protein II | 7385 | ENSG00000140740 |
| 21  | ENSG00000166136 | NA | NDUFB8 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa | 4714 | ENSG00000166136 |
| 22  | ENSG00000110717 | NA | NDUFS8 | NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) | 4728 | ENSG00000110717 |
| 23  | ENSG00000147684 | NA | NDUFB9 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa | 4715 | ENSG00000147684 |
| 24  | ENSG00000160194 | NA | NDUFV3 | NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa | 4731 | ENSG00000160194 |
| 25  | ENSG00000184983 | NA | NDUFA6 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa | 4700 | ENSG00000184983 |
| 26  | ENSG00000170906 | NA | NDUFA3 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa | 4696 | ENSG00000170906 |
| 27  | ENSG00000130414 | NA | NDUFA10 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa | 4705 | ENSG00000130414 |
| 28  | ENSG00000091140 | NA | DLD | dihydrolipoamide dehydrogenase | 1738 | ENSG00000091140 |
| 29  | ENSG00000165060 | NA | FXN | frataxin | 2395 | ENSG00000165060 |
| 30  | ENSG00000158864 | NA | NDUFS2 | NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) | 4720 | ENSG00000158864 |
| 31  | ENSG00000139180 | NA | NDUFA9 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa | 4704 | ENSG00000139180 |
| 32  | ENSG00000109390 | NA | NDUFC1 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa | 4717 | ENSG00000109390 |
| 33  | ENSG00000010256 | NA | UQCRC1 | ubiquinol-cytochrome c reductase core protein I | 7384 | ENSG00000010256 |
| 34  | ENSG00000137806 | NA | NDUFAF1 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 | 51103 | ENSG00000137806 |
| 35  | ENSG00000183648 | NA | NDUFB1 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa | 4707 | ENSG00000183648 |
| 36  | ENSG00000140990 | NA | NDUFB10 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa | 4716 | ENSG00000140990 |
| 37  | ENSG00000204370 | NA | SDHD | succinate dehydrogenase complex, subunit D, integral membrane protein | 6392 | ENSG00000204370 |
| 38  | ENSG00000099624 | NA | ATP5D | ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit | 513 | ENSG00000099624 |
| 39  | ENSG00000165629 | NA | ATP5C1 | ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 | 509 | ENSG00000165629 |
| 40  | ENSG00000125356 | NA | NDUFA1 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa | 4694 | ENSG00000125356 |
| 41  | ENSG00000148290 | NA | SURF1 | surfeit 1 | 6834 | ENSG00000148290 |
| 42  | ENSG00000213619 | NA | NDUFS3 | NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) | 4722 | ENSG00000213619 |
| 43  | ENSG00000173660 | NA | UQCRH | ubiquinol-cytochrome c reductase hinge protein | 7388 | ENSG00000173660 |
| 44  | ENSG00000168653 | NA | NDUFS5 | NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) | 4725 | ENSG00000168653 |
| 45  | ENSG00000099795 | NA | NDUFB7 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa | 4713 | ENSG00000099795 |
| 46  | ENSG00000146729 | NA | GBAS | glioblastoma amplified sequence | 2631 | ENSG00000146729 |
| 47  | ENSG00000119421 | NA | NDUFA8 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa | 4702 | ENSG00000119421 |
| Database:biological process       Name:mitochondrial ATP synthesis coupled electron transport       ID:GO:0042775 | ||||||
|---|---|---|---|---|---|---|
| C=58; O=40; E=3.55; R=11.26; rawP=2.06e-35; adjP=5.69e-33 | ||||||
| Index | UserID | Value | Gene Symbol | Gene Name | EntrezGene | Ensembl |
| 1  | ENSG00000151366 | NA | NDUFC2 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa | 4718 | ENSG00000151366 |
| 2  | ENSG00000128609 | NA | NDUFA5 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa | 4698 | ENSG00000128609 |
| 3  | ENSG00000023228 | NA | NDUFS1 | NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) | 4719 | ENSG00000023228 |
| 4  | ENSG00000165264 | NA | NDUFB6 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa | 4712 | ENSG00000165264 |
| 5  | ENSG00000156467 | NA | UQCRB | ubiquinol-cytochrome c reductase binding protein | 7381 | ENSG00000156467 |
| 6  | ENSG00000184076 | NA | UQCR10 | ubiquinol-cytochrome c reductase, complex III subunit X | 29796 | ENSG00000184076 |
| 7  | ENSG00000145494 | NA | NDUFS6 | NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) | 4726 | ENSG00000145494 |
| 8  | ENSG00000136521 | NA | NDUFB5 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa | 4711 | ENSG00000136521 |
| 9  | ENSG00000004779 | NA | NDUFAB1 | NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa | 4706 | ENSG00000004779 |
| 10  | ENSG00000189043 | NA | NDUFA4 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa | 4697 | ENSG00000189043 |
| 11  | ENSG00000006695 | NA | COX10 | COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) | 1352 | ENSG00000006695 |
| 12  | ENSG00000115286 | NA | NDUFS7 | NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) | 374291 | ENSG00000115286 |
| 13  | ENSG00000164258 | NA | NDUFS4 | NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) | 4724 | ENSG00000164258 |
| 14  | ENSG00000119013 | NA | NDUFB3 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa | 4709 | ENSG00000119013 |
| 15  | ENSG00000167792 | NA | NDUFV1 | NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa | 4723 | ENSG00000167792 |
| 16  | ENSG00000131495 | NA | NDUFA2 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa | 4695 | ENSG00000131495 |
| 17  | ENSG00000065518 | NA | NDUFB4 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa | 4710 | ENSG00000065518 |
| 18  | ENSG00000090266 | NA | NDUFB2 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa | 4708 | ENSG00000090266 |
| 19  | ENSG00000166136 | NA | NDUFB8 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa | 4714 | ENSG00000166136 |
| 20  | ENSG00000110717 | NA | NDUFS8 | NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) | 4728 | ENSG00000110717 |
| 21  | ENSG00000147684 | NA | NDUFB9 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa | 4715 | ENSG00000147684 |
| 22  | ENSG00000160194 | NA | NDUFV3 | NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa | 4731 | ENSG00000160194 |
| 23  | ENSG00000184983 | NA | NDUFA6 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa | 4700 | ENSG00000184983 |
| 24  | ENSG00000170906 | NA | NDUFA3 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa | 4696 | ENSG00000170906 |
| 25  | ENSG00000091140 | NA | DLD | dihydrolipoamide dehydrogenase | 1738 | ENSG00000091140 |
| 26  | ENSG00000130414 | NA | NDUFA10 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa | 4705 | ENSG00000130414 |
| 27  | ENSG00000158864 | NA | NDUFS2 | NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) | 4720 | ENSG00000158864 |
| 28  | ENSG00000139180 | NA | NDUFA9 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa | 4704 | ENSG00000139180 |
| 29  | ENSG00000109390 | NA | NDUFC1 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa | 4717 | ENSG00000109390 |
| 30  | ENSG00000010256 | NA | UQCRC1 | ubiquinol-cytochrome c reductase core protein I | 7384 | ENSG00000010256 |
| 31  | ENSG00000137806 | NA | NDUFAF1 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 | 51103 | ENSG00000137806 |
| 32  | ENSG00000183648 | NA | NDUFB1 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa | 4707 | ENSG00000183648 |
| 33  | ENSG00000140990 | NA | NDUFB10 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa | 4716 | ENSG00000140990 |
| 34  | ENSG00000204370 | NA | SDHD | succinate dehydrogenase complex, subunit D, integral membrane protein | 6392 | ENSG00000204370 |
| 35  | ENSG00000125356 | NA | NDUFA1 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa | 4694 | ENSG00000125356 |
| 36  | ENSG00000213619 | NA | NDUFS3 | NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) | 4722 | ENSG00000213619 |
| 37  | ENSG00000173660 | NA | UQCRH | ubiquinol-cytochrome c reductase hinge protein | 7388 | ENSG00000173660 |
| 38  | ENSG00000168653 | NA | NDUFS5 | NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) | 4725 | ENSG00000168653 |
| 39  | ENSG00000099795 | NA | NDUFB7 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa | 4713 | ENSG00000099795 |
| 40  | ENSG00000119421 | NA | NDUFA8 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa | 4702 | ENSG00000119421 |
| Database:biological process       Name:ATP synthesis coupled electron transport       ID:GO:0042773 | ||||||
|---|---|---|---|---|---|---|
| C=58; O=40; E=3.55; R=11.26; rawP=2.06e-35; adjP=5.69e-33 | ||||||
| Index | UserID | Value | Gene Symbol | Gene Name | EntrezGene | Ensembl |
| 1  | ENSG00000151366 | NA | NDUFC2 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa | 4718 | ENSG00000151366 |
| 2  | ENSG00000128609 | NA | NDUFA5 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa | 4698 | ENSG00000128609 |
| 3  | ENSG00000023228 | NA | NDUFS1 | NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) | 4719 | ENSG00000023228 |
| 4  | ENSG00000165264 | NA | NDUFB6 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa | 4712 | ENSG00000165264 |
| 5  | ENSG00000156467 | NA | UQCRB | ubiquinol-cytochrome c reductase binding protein | 7381 | ENSG00000156467 |
| 6  | ENSG00000184076 | NA | UQCR10 | ubiquinol-cytochrome c reductase, complex III subunit X | 29796 | ENSG00000184076 |
| 7  | ENSG00000145494 | NA | NDUFS6 | NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) | 4726 | ENSG00000145494 |
| 8  | ENSG00000136521 | NA | NDUFB5 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa | 4711 | ENSG00000136521 |
| 9  | ENSG00000004779 | NA | NDUFAB1 | NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa | 4706 | ENSG00000004779 |
| 10  | ENSG00000189043 | NA | NDUFA4 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa | 4697 | ENSG00000189043 |
| 11  | ENSG00000006695 | NA | COX10 | COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) | 1352 | ENSG00000006695 |
| 12  | ENSG00000115286 | NA | NDUFS7 | NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) | 374291 | ENSG00000115286 |
| 13  | ENSG00000164258 | NA | NDUFS4 | NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) | 4724 | ENSG00000164258 |
| 14  | ENSG00000119013 | NA | NDUFB3 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa | 4709 | ENSG00000119013 |
| 15  | ENSG00000167792 | NA | NDUFV1 | NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa | 4723 | ENSG00000167792 |
| 16  | ENSG00000131495 | NA | NDUFA2 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa | 4695 | ENSG00000131495 |
| 17  | ENSG00000065518 | NA | NDUFB4 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa | 4710 | ENSG00000065518 |
| 18  | ENSG00000090266 | NA | NDUFB2 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa | 4708 | ENSG00000090266 |
| 19  | ENSG00000166136 | NA | NDUFB8 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa | 4714 | ENSG00000166136 |
| 20  | ENSG00000110717 | NA | NDUFS8 | NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) | 4728 | ENSG00000110717 |
| 21  | ENSG00000147684 | NA | NDUFB9 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa | 4715 | ENSG00000147684 |
| 22  | ENSG00000160194 | NA | NDUFV3 | NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa | 4731 | ENSG00000160194 |
| 23  | ENSG00000184983 | NA | NDUFA6 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa | 4700 | ENSG00000184983 |
| 24  | ENSG00000170906 | NA | NDUFA3 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa | 4696 | ENSG00000170906 |
| 25  | ENSG00000091140 | NA | DLD | dihydrolipoamide dehydrogenase | 1738 | ENSG00000091140 |
| 26  | ENSG00000130414 | NA | NDUFA10 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa | 4705 | ENSG00000130414 |
| 27  | ENSG00000158864 | NA | NDUFS2 | NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) | 4720 | ENSG00000158864 |
| 28  | ENSG00000139180 | NA | NDUFA9 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa | 4704 | ENSG00000139180 |
| 29  | ENSG00000109390 | NA | NDUFC1 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa | 4717 | ENSG00000109390 |
| 30  | ENSG00000010256 | NA | UQCRC1 | ubiquinol-cytochrome c reductase core protein I | 7384 | ENSG00000010256 |
| 31  | ENSG00000137806 | NA | NDUFAF1 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 | 51103 | ENSG00000137806 |
| 32  | ENSG00000183648 | NA | NDUFB1 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa | 4707 | ENSG00000183648 |
| 33  | ENSG00000140990 | NA | NDUFB10 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa | 4716 | ENSG00000140990 |
| 34  | ENSG00000204370 | NA | SDHD | succinate dehydrogenase complex, subunit D, integral membrane protein | 6392 | ENSG00000204370 |
| 35  | ENSG00000125356 | NA | NDUFA1 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa | 4694 | ENSG00000125356 |
| 36  | ENSG00000213619 | NA | NDUFS3 | NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) | 4722 | ENSG00000213619 |
| 37  | ENSG00000173660 | NA | UQCRH | ubiquinol-cytochrome c reductase hinge protein | 7388 | ENSG00000173660 |
| 38  | ENSG00000168653 | NA | NDUFS5 | NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) | 4725 | ENSG00000168653 |
| 39  | ENSG00000099795 | NA | NDUFB7 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa | 4713 | ENSG00000099795 |
| 40  | ENSG00000119421 | NA | NDUFA8 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa | 4702 | ENSG00000119421 |
| Database:biological process       Name:small molecule metabolic process       ID:GO:0044281 | ||||||
|---|---|---|---|---|---|---|
| C=2515; O=302; E=154.03; R=1.96; rawP=1.91e-35; adjP=5.69e-33 | ||||||
| Index | UserID | Value | Gene Symbol | Gene Name | EntrezGene | Ensembl |
| 1  | ENSG00000168803 | NA | ADAL | adenosine deaminase-like | 161823 | ENSG00000168803 |
| 2  | ENSG00000165264 | NA | NDUFB6 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa | 4712 | ENSG00000165264 |
| 3  | ENSG00000148672 | NA | GLUD1 | glutamate dehydrogenase 1 | 2746 | ENSG00000148672 |
| 4  | ENSG00000169375 | NA | SIN3A | SIN3 transcription regulator homolog A (yeast) | 25942 | ENSG00000169375 |
| 5  | ENSG00000164172 | NA | MOCS2 | molybdenum cofactor synthesis 2 | 4338 | ENSG00000164172 |
| 6  | ENSG00000239264 | NA | TXNDC5 | thioredoxin domain containing 5 (endoplasmic reticulum) | 81567 | ENSG00000239264 |
| 7  | ENSG00000135390 | NA | ATP5G2 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C2 (subunit 9) | 517 | ENSG00000135390 |
| 8  | ENSG00000166136 | NA | NDUFB8 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa | 4714 | ENSG00000166136 |
| 9  | ENSG00000116353 | NA | MECR | mitochondrial trans-2-enoyl-CoA reductase | 51102 | ENSG00000116353 |
| 10  | ENSG00000172340 | NA | SUCLG2 | succinate-CoA ligase, GDP-forming, beta subunit | 8801 | ENSG00000172340 |
| 11  | ENSG00000151093 | NA | OXSM | 3-oxoacyl-ACP synthase, mitochondrial | 54995 | ENSG00000151093 |
| 12  | ENSG00000130414 | NA | NDUFA10 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa | 4705 | ENSG00000130414 |
| 13  | ENSG00000091140 | NA | DLD | dihydrolipoamide dehydrogenase | 1738 | ENSG00000091140 |
| 14  | ENSG00000131828 | NA | PDHA1 | pyruvate dehydrogenase (lipoamide) alpha 1 | 5160 | ENSG00000131828 |
| 15  | ENSG00000122971 | NA | ACADS | acyl-CoA dehydrogenase, C-2 to C-3 short chain | 35 | ENSG00000122971 |
| 16  | ENSG00000103356 | NA | EARS2 | glutamyl-tRNA synthetase 2, mitochondrial (putative) | 124454 | ENSG00000103356 |
| 17  | ENSG00000109390 | NA | NDUFC1 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa | 4717 | ENSG00000109390 |
| 18  | ENSG00000176533 | NA | GNG7 | guanine nucleotide binding protein (G protein), gamma 7 | 2788 | ENSG00000176533 |
| 19  | ENSG00000091483 | NA | FH | fumarate hydratase | 2271 | ENSG00000091483 |
| 20  | ENSG00000203797 | NA | DDO | D-aspartate oxidase | 8528 | ENSG00000203797 |
| 21  | ENSG00000123384 | NA | LRP1 | low density lipoprotein receptor-related protein 1 | 4035 | ENSG00000123384 |
| 22  | ENSG00000135218 | NA | CD36 | CD36 molecule (thrombospondin receptor) | 948 | ENSG00000135218 |
| 23  | ENSG00000127838 | NA | PNKD | paroxysmal nonkinesigenic dyskinesia | 25953 | ENSG00000127838 |
| 24  | ENSG00000119537 | NA | KDSR | 3-ketodihydrosphingosine reductase | 2531 | ENSG00000119537 |
| 25  | ENSG00000151729 | NA | SLC25A4 | solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4 | 291 | ENSG00000151729 |
| 26  | ENSG00000185627 | NA | PSMD13 | proteasome (prosome, macropain) 26S subunit, non-ATPase, 13 | 5719 | ENSG00000185627 |
| 27  | ENSG00000119383 | NA | PPP2R4 | protein phosphatase 2A activator, regulatory subunit 4 | 5524 | ENSG00000119383 |
| 28  | ENSG00000126432 | NA | PRDX5 | peroxiredoxin 5 | 25824 | ENSG00000126432 |
| 29  | ENSG00000149925 | NA | ALDOA | aldolase A, fructose-bisphosphate | 226 | ENSG00000149925 |
| 30  | ENSG00000023330 | NA | ALAS1 | aminolevulinate, delta-, synthase 1 | 211 | ENSG00000023330 |
| 31  | ENSG00000178741 | NA | COX5A | cytochrome c oxidase subunit Va | 9377 | ENSG00000178741 |
| 32  | ENSG00000213619 | NA | NDUFS3 | NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) | 4722 | ENSG00000213619 |
| 33  | ENSG00000173660 | NA | UQCRH | ubiquinol-cytochrome c reductase hinge protein | 7388 | ENSG00000173660 |
| 34  | ENSG00000100348 | NA | TXN2 | thioredoxin 2 | 25828 | ENSG00000100348 |
| 35  | ENSG00000140876 | NA | NUDT7 | nudix (nucleoside diphosphate linked moiety X)-type motif 7 | 283927 | ENSG00000140876 |
| 36  | ENSG00000114854 | NA | TNNC1 | troponin C type 1 (slow) | 7134 | ENSG00000114854 |
| 37  | ENSG00000135940 | NA | COX5B | cytochrome c oxidase subunit Vb | 1329 | ENSG00000135940 |
| 38  | ENSG00000129991 | NA | TNNI3 | troponin I type 3 (cardiac) | 7137 | ENSG00000129991 |
| 39  | ENSG00000113790 | NA | EHHADH | enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase | 1962 | ENSG00000113790 |
| 40  | ENSG00000172115 | NA | CYCS | cytochrome c, somatic | 54205 | ENSG00000172115 |
| 41  | ENSG00000189043 | NA | NDUFA4 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa | 4697 | ENSG00000189043 |
| 42  | ENSG00000123739 | NA | PLA2G12A | phospholipase A2, group XIIA | 81579 | ENSG00000123739 |
| 43  | ENSG00000164919 | NA | COX6C | cytochrome c oxidase subunit VIc | 1345 | ENSG00000164919 |
| 44  | ENSG00000185100 | NA | ADSSL1 | adenylosuccinate synthase like 1 | 122622 | ENSG00000185100 |
| 45  | ENSG00000115286 | NA | NDUFS7 | NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) | 374291 | ENSG00000115286 |
| 46  | ENSG00000139131 | NA | YARS2 | tyrosyl-tRNA synthetase 2, mitochondrial | 51067 | ENSG00000139131 |
| 47  | ENSG00000164258 | NA | NDUFS4 | NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) | 4724 | ENSG00000164258 |
| 48  | ENSG00000155463 | NA | OXA1L | oxidase (cytochrome c) assembly 1-like | 5018 | ENSG00000155463 |
| 49  | ENSG00000167863 | NA | ATP5H | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d | 10476 | ENSG00000167863 |
| 50  | ENSG00000137077 | NA | CCL21 | chemokine (C-C motif) ligand 21 | 6366 | ENSG00000137077 |
| 51  | ENSG00000130203 | NA | APOE | apolipoprotein E | 348 | ENSG00000130203 |
| 52  | ENSG00000179091 | NA | CYC1 | cytochrome c-1 | 1537 | ENSG00000179091 |
| 53  | ENSG00000166165 | NA | CKB | creatine kinase, brain | 1152 | ENSG00000166165 |
| 54  | ENSG00000127540 | NA | UQCR11 | ubiquinol-cytochrome c reductase, complex III subunit XI | 10975 | ENSG00000127540 |
| 55  | ENSG00000184752 | NA | NDUFA12 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 | 55967 | ENSG00000184752 |
| 56  | ENSG00000132423 | NA | COQ3 | coenzyme Q3 homolog, methyltransferase (S. cerevisiae) | 51805 | ENSG00000132423 |
| 57  | ENSG00000131844 | NA | MCCC2 | methylcrotonoyl-CoA carboxylase 2 (beta) | 64087 | ENSG00000131844 |
| 58  | ENSG00000134905 | NA | CARS2 | cysteinyl-tRNA synthetase 2, mitochondrial (putative) | 79587 | ENSG00000134905 |
| 59  | ENSG00000204228 | NA | HSD17B8 | hydroxysteroid (17-beta) dehydrogenase 8 | 7923 | ENSG00000204228 |
| 60  | ENSG00000197283 | NA | SYNGAP1 | synaptic Ras GTPase activating protein 1 | 8831 | ENSG00000197283 |
| 61  | ENSG00000175198 | NA | PCCA | propionyl CoA carboxylase, alpha polypeptide | 5095 | ENSG00000175198 |
| 62  | ENSG00000067829 | NA | IDH3G | isocitrate dehydrogenase 3 (NAD+) gamma | 3421 | ENSG00000067829 |
| 63  | ENSG00000129187 | NA | DCTD | dCMP deaminase | 1635 | ENSG00000129187 |
| 64  | ENSG00000067225 | NA | PKM | pyruvate kinase, muscle | 5315 | ENSG00000067225 |
| 65  | ENSG00000140990 | NA | NDUFB10 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa | 4716 | ENSG00000140990 |
| 66  | ENSG00000157326 | NA | DHRS4 | dehydrogenase/reductase (SDR family) member 4 | 10901 | ENSG00000157326 |
| 67  | ENSG00000135297 | NA | MTO1 | mitochondrial translation optimization 1 homolog (S. cerevisiae) | 25821 | ENSG00000135297 |
| 68  | ENSG00000247626 | NA | MARS2 | methionyl-tRNA synthetase 2, mitochondrial | 92935 | ENSG00000247626 |
| 69  | ENSG00000167363 | NA | FN3K | fructosamine 3 kinase | 64122 | ENSG00000167363 |
| 70  | ENSG00000165629 | NA | ATP5C1 | ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 | 509 | ENSG00000165629 |
| 71  | ENSG00000116906 | NA | GNPAT | glyceronephosphate O-acyltransferase | 8443 | ENSG00000116906 |
| 72  | ENSG00000148290 | NA | SURF1 | surfeit 1 | 6834 | ENSG00000148290 |
| 73  | ENSG00000014641 | NA | MDH1 | malate dehydrogenase 1, NAD (soluble) | 4190 | ENSG00000014641 |
| 74  | ENSG00000105220 | NA | GPI | glucose-6-phosphate isomerase | 2821 | ENSG00000105220 |
| 75  | ENSG00000133315 | NA | MACROD1 | MACRO domain containing 1 | 28992 | ENSG00000133315 |
| 76  | ENSG00000072778 | NA | ACADVL | acyl-CoA dehydrogenase, very long chain | 37 | ENSG00000072778 |
| 77  | ENSG00000172893 | NA | DHCR7 | 7-dehydrocholesterol reductase | 1717 | ENSG00000172893 |
| 78  | ENSG00000154930 | NA | ACSS1 | acyl-CoA synthetase short-chain family member 1 | 84532 | ENSG00000154930 |
| 79  | ENSG00000108774 | NA | RAB5C | RAB5C, member RAS oncogene family | 5878 | ENSG00000108774 |
| 80  | ENSG00000196636 | NA | ACN9 | ACN9 homolog (S. cerevisiae) | 57001 | ENSG00000196636 |
| 81  | ENSG00000139410 | NA | SDSL | serine dehydratase-like | 113675 | ENSG00000139410 |
| 82  | ENSG00000059691 | NA | PET112 | PET112 homolog (yeast) | 5188 | ENSG00000059691 |
| 83  | ENSG00000112981 | NA | NME5 | NME/NM23 family member 5 | 8382 | ENSG00000112981 |
| 84  | ENSG00000126088 | NA | UROD | uroporphyrinogen decarboxylase | 7389 | ENSG00000126088 |
| 85  | ENSG00000138430 | NA | OLA1 | Obg-like ATPase 1 | 29789 | ENSG00000138430 |
| 86  | ENSG00000136521 | NA | NDUFB5 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa | 4711 | ENSG00000136521 |
| 87  | ENSG00000004779 | NA | NDUFAB1 | NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa | 4706 | ENSG00000004779 |
| 88  | ENSG00000169020 | NA | ATP5I | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E | 521 | ENSG00000169020 |
| 89  | ENSG00000182054 | NA | IDH2 | isocitrate dehydrogenase 2 (NADP+), mitochondrial | 3418 | ENSG00000182054 |
| 90  | ENSG00000120253 | NA | NUP43 | nucleoporin 43kDa | 348995 | ENSG00000120253 |
| 91  | ENSG00000085871 | NA | MGST2 | microsomal glutathione S-transferase 2 | 4258 | ENSG00000085871 |
| 92  | ENSG00000172954 | NA | LCLAT1 | lysocardiolipin acyltransferase 1 | 253558 | ENSG00000172954 |
| 93  | ENSG00000073578 | NA | SDHA | succinate dehydrogenase complex, subunit A, flavoprotein (Fp) | 6389 | ENSG00000073578 |
| 94  | ENSG00000119013 | NA | NDUFB3 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa | 4709 | ENSG00000119013 |
| 95  | ENSG00000104325 | NA | DECR1 | 2,4-dienoyl CoA reductase 1, mitochondrial | 1666 | ENSG00000104325 |
| 96  | ENSG00000144827 | NA | ABHD10 | abhydrolase domain containing 10 | 55347 | ENSG00000144827 |
| 97  | ENSG00000173786 | NA | CNP | 2',3'-cyclic nucleotide 3' phosphodiesterase | 1267 | ENSG00000173786 |
| 98  | ENSG00000139180 | NA | NDUFA9 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa | 4704 | ENSG00000139180 |
| 99  | ENSG00000127184 | NA | COX7C | cytochrome c oxidase subunit VIIc | 1350 | ENSG00000127184 |
| 100  | ENSG00000111640 | NA | GAPDH | glyceraldehyde-3-phosphate dehydrogenase | 2597 | ENSG00000111640 |
| 101  | ENSG00000123836 | NA | PFKFB2 | 6-phosphofructo-2-kinase/fructose-2,6-biphosphatase 2 | 5208 | ENSG00000123836 |
| 102  | ENSG00000130208 | NA | APOC1 | apolipoprotein C-I | 341 | ENSG00000130208 |
| 103  | ENSG00000120265 | NA | PCMT1 | protein-L-isoaspartate (D-aspartate) O-methyltransferase | 5110 | ENSG00000120265 |
| 104  | ENSG00000204370 | NA | SDHD | succinate dehydrogenase complex, subunit D, integral membrane protein | 6392 | ENSG00000204370 |
| 105  | ENSG00000137106 | NA | GRHPR | glyoxylate reductase/hydroxypyruvate reductase | 9380 | ENSG00000137106 |
| 106  | ENSG00000169738 | NA | DCXR | dicarbonyl/L-xylulose reductase | 51181 | ENSG00000169738 |
| 107  | ENSG00000160211 | NA | G6PD | glucose-6-phosphate dehydrogenase | 2539 | ENSG00000160211 |
| 108  | ENSG00000138777 | NA | PPA2 | pyrophosphatase (inorganic) 2 | 27068 | ENSG00000138777 |
| 109  | ENSG00000117280 | NA | RAB7L1 | RAB7, member RAS oncogene family-like 1 | 8934 | ENSG00000117280 |
| 110  | ENSG00000111669 | NA | TPI1 | triosephosphate isomerase 1 | 7167 | ENSG00000111669 |
| 111  | ENSG00000138823 | NA | MTTP | microsomal triglyceride transfer protein | 4547 | ENSG00000138823 |
| 112  | ENSG00000023228 | NA | NDUFS1 | NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) | 4719 | ENSG00000023228 |
| 113  | ENSG00000100116 | NA | GCAT | glycine C-acetyltransferase | 23464 | ENSG00000100116 |
| 114  | ENSG00000143252 | NA | SDHC | succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa | 6391 | ENSG00000143252 |
| 115  | ENSG00000151376 | NA | ME3 | malic enzyme 3, NADP(+)-dependent, mitochondrial | 10873 | ENSG00000151376 |
| 116  | ENSG00000145982 | NA | FARS2 | phenylalanyl-tRNA synthetase 2, mitochondrial | 10667 | ENSG00000145982 |
| 117  | ENSG00000115840 | NA | SLC25A12 | solute carrier family 25 (aspartate/glutamate carrier), member 12 | 8604 | ENSG00000115840 |
| 118  | ENSG00000121897 | NA | LIAS | lipoic acid synthetase | 11019 | ENSG00000121897 |
| 119  | ENSG00000110955 | NA | ATP5B | ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide | 506 | ENSG00000110955 |
| 120  | ENSG00000147155 | NA | EBP | emopamil binding protein (sterol isomerase) | 10682 | ENSG00000147155 |
| 121  | ENSG00000179958 | NA | DCTPP1 | dCTP pyrophosphatase 1 | 79077 | ENSG00000179958 |
| 122  | ENSG00000131495 | NA | NDUFA2 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa | 4695 | ENSG00000131495 |
| 123  | ENSG00000083720 | NA | OXCT1 | 3-oxoacid CoA transferase 1 | 5019 | ENSG00000083720 |
| 124  | ENSG00000065518 | NA | NDUFB4 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa | 4710 | ENSG00000065518 |
| 125  | ENSG00000095321 | NA | CRAT | carnitine O-acetyltransferase | 1384 | ENSG00000095321 |
| 126  | ENSG00000159445 | NA | THEM4 | thioesterase superfamily member 4 | 117145 | ENSG00000159445 |
| 127  | ENSG00000120992 | NA | LYPLA1 | lysophospholipase I | 10434 | ENSG00000120992 |
| 128  | ENSG00000198721 | NA | ECI2 | enoyl-CoA delta isomerase 2 | 10455 | ENSG00000198721 |
| 129  | ENSG00000112855 | NA | HARS2 | histidyl-tRNA synthetase 2, mitochondrial | 23438 | ENSG00000112855 |
| 130  | ENSG00000197580 | NA | BCO2 | beta-carotene oxygenase 2 | 83875 | ENSG00000197580 |
| 131  | ENSG00000131174 | NA | COX7B | cytochrome c oxidase subunit VIIb | 1349 | ENSG00000131174 |
| 132  | ENSG00000147853 | NA | AK3 | adenylate kinase 3 | 50808 | ENSG00000147853 |
| 133  | ENSG00000170906 | NA | NDUFA3 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa | 4696 | ENSG00000170906 |
| 134  | ENSG00000205309 | NA | NT5M | 5',3'-nucleotidase, mitochondrial | 56953 | ENSG00000205309 |
| 135  | ENSG00000106305 | NA | AIMP2 | aminoacyl tRNA synthetase complex-interacting multifunctional protein 2 | 7965 | ENSG00000106305 |
| 136  | ENSG00000160808 | NA | MYL3 | myosin, light chain 3, alkali; ventricular, skeletal, slow | 4634 | ENSG00000160808 |
| 137  | ENSG00000142507 | NA | PSMB6 | proteasome (prosome, macropain) subunit, beta type, 6 | 5694 | ENSG00000142507 |
| 138  | ENSG00000111716 | NA | LDHB | lactate dehydrogenase B | 3945 | ENSG00000111716 |
| 139  | ENSG00000108439 | NA | PNPO | pyridoxamine 5'-phosphate oxidase | 55163 | ENSG00000108439 |
| 140  | ENSG00000114054 | NA | PCCB | propionyl CoA carboxylase, beta polypeptide | 5096 | ENSG00000114054 |
| 141  | ENSG00000167283 | NA | ATP5L | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G | 10632 | ENSG00000167283 |
| 142  | ENSG00000111275 | NA | ALDH2 | aldehyde dehydrogenase 2 family (mitochondrial) | 217 | ENSG00000111275 |
| 143  | ENSG00000136928 | NA | GABBR2 | gamma-aminobutyric acid (GABA) B receptor, 2 | 9568 | ENSG00000136928 |
| 144  | ENSG00000078401 | NA | EDN1 | endothelin 1 | 1906 | ENSG00000078401 |
| 145  | ENSG00000010256 | NA | UQCRC1 | ubiquinol-cytochrome c reductase core protein I | 7384 | ENSG00000010256 |
| 146  | ENSG00000104823 | NA | ECH1 | enoyl CoA hydratase 1, peroxisomal | 1891 | ENSG00000104823 |
| 147  | ENSG00000171503 | NA | ETFDH | electron-transferring-flavoprotein dehydrogenase | 2110 | ENSG00000171503 |
| 148  | ENSG00000138796 | NA | HADH | hydroxyacyl-CoA dehydrogenase | 3033 | ENSG00000138796 |
| 149  | ENSG00000154518 | NA | ATP5G3 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C3 (subunit 9) | 518 | ENSG00000154518 |
| 150  | ENSG00000088682 | NA | COQ9 | coenzyme Q9 homolog (S. cerevisiae) | 57017 | ENSG00000088682 |
| 151  | ENSG00000161533 | NA | ACOX1 | acyl-CoA oxidase 1, palmitoyl | 51 | ENSG00000161533 |
| 152  | ENSG00000168653 | NA | NDUFS5 | NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) | 4725 | ENSG00000168653 |
| 153  | ENSG00000156110 | NA | ADK | adenosine kinase | 132 | ENSG00000156110 |
| 154  | ENSG00000087299 | NA | L2HGDH | L-2-hydroxyglutarate dehydrogenase | 79944 | ENSG00000087299 |
| 155  | ENSG00000163864 | NA | NMNAT3 | nicotinamide nucleotide adenylyltransferase 3 | 349565 | ENSG00000163864 |
| 156  | ENSG00000156467 | NA | UQCRB | ubiquinol-cytochrome c reductase binding protein | 7381 | ENSG00000156467 |
| 157  | ENSG00000103316 | NA | CRYM | crystallin, mu | 1428 | ENSG00000103316 |
| 158  | ENSG00000184076 | NA | UQCR10 | ubiquinol-cytochrome c reductase, complex III subunit X | 29796 | ENSG00000184076 |
| 159  | ENSG00000078070 | NA | MCCC1 | methylcrotonoyl-CoA carboxylase 1 (alpha) | 56922 | ENSG00000078070 |
| 160  | ENSG00000115884 | NA | SDC1 | syndecan 1 | 6382 | ENSG00000115884 |
| 161  | ENSG00000154723 | NA | ATP5J | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 | 522 | ENSG00000154723 |
| 162  | ENSG00000167969 | NA | ECI1 | enoyl-CoA delta isomerase 1 | 1632 | ENSG00000167969 |
| 163  | ENSG00000105552 | NA | BCAT2 | branched chain amino-acid transaminase 2, mitochondrial | 587 | ENSG00000105552 |
| 164  | ENSG00000006606 | NA | CCL26 | chemokine (C-C motif) ligand 26 | 10344 | ENSG00000006606 |
| 165  | ENSG00000139531 | NA | SUOX | sulfite oxidase | 6821 | ENSG00000139531 |
| 166  | ENSG00000125166 | NA | GOT2 | glutamic-oxaloacetic transaminase 2, mitochondrial (aspartate aminotransferase 2) | 2806 | ENSG00000125166 |
| 167  | ENSG00000140374 | NA | ETFA | electron-transfer-flavoprotein, alpha polypeptide | 2108 | ENSG00000140374 |
| 168  | ENSG00000140740 | NA | UQCRC2 | ubiquinol-cytochrome c reductase core protein II | 7385 | ENSG00000140740 |
| 169  | ENSG00000114378 | NA | HYAL1 | hyaluronoglucosaminidase 1 | 3373 | ENSG00000114378 |
| 170  | ENSG00000160194 | NA | NDUFV3 | NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa | 4731 | ENSG00000160194 |
| 171  | ENSG00000147684 | NA | NDUFB9 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa | 4715 | ENSG00000147684 |
| 172  | ENSG00000184983 | NA | NDUFA6 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa | 4700 | ENSG00000184983 |
| 173  | ENSG00000158864 | NA | NDUFS2 | NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) | 4720 | ENSG00000158864 |
| 174  | ENSG00000079691 | NA | LRRC16A | leucine rich repeat containing 16A | 55604 | ENSG00000079691 |
| 175  | ENSG00000155749 | NA | ALS2CR12 | amyotrophic lateral sclerosis 2 (juvenile) chromosome region, candidate 12 | 130540 | ENSG00000155749 |
| 176  | ENSG00000142168 | NA | SOD1 | superoxide dismutase 1, soluble | 6647 | ENSG00000142168 |
| 177  | ENSG00000000419 | NA | DPM1 | dolichyl-phosphate mannosyltransferase polypeptide 1, catalytic subunit | 8813 | ENSG00000000419 |
| 178  | ENSG00000181929 | NA | PRKAG1 | protein kinase, AMP-activated, gamma 1 non-catalytic subunit | 5571 | ENSG00000181929 |
| 179  | ENSG00000076043 | NA | REXO2 | REX2, RNA exonuclease 2 homolog (S. cerevisiae) | 25996 | ENSG00000076043 |
| 180  | ENSG00000120254 | NA | MTHFD1L | methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 1-like | 25902 | ENSG00000120254 |
| 181  | ENSG00000147813 | NA | NAPRT1 | nicotinate phosphoribosyltransferase domain containing 1 | 93100 | ENSG00000147813 |
| 182  | ENSG00000119689 | NA | DLST | dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex) | 1743 | ENSG00000119689 |
| 183  | ENSG00000168291 | NA | PDHB | pyruvate dehydrogenase (lipoamide) beta | 5162 | ENSG00000168291 |
| 184  | ENSG00000156049 | NA | GNA14 | guanine nucleotide binding protein (G protein), alpha 14 | 9630 | ENSG00000156049 |
| 185  | ENSG00000116459 | NA | ATP5F1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 | 515 | ENSG00000116459 |
| 186  | ENSG00000105499 | NA | PLA2G4C | phospholipase A2, group IVC (cytosolic, calcium-independent) | 8605 | ENSG00000105499 |
| 187  | ENSG00000119328 | NA | FAM206A | family with sequence similarity 206, member A | 54942 | ENSG00000119328 |
| 188  | ENSG00000112992 | NA | NNT | nicotinamide nucleotide transhydrogenase | 23530 | ENSG00000112992 |
| 189  | ENSG00000067704 | NA | IARS2 | isoleucyl-tRNA synthetase 2, mitochondrial | 55699 | ENSG00000067704 |
| 190  | ENSG00000130348 | NA | QRSL1 | glutaminyl-tRNA synthase (glutamine-hydrolyzing)-like 1 | 55278 | ENSG00000130348 |
| 191  | ENSG00000087250 | NA | MT3 | metallothionein 3 | 4504 | ENSG00000087250 |
| 192  | ENSG00000170502 | NA | NUDT9 | nudix (nucleoside diphosphate linked moiety X)-type motif 9 | 53343 | ENSG00000170502 |
| 193  | ENSG00000119421 | NA | NDUFA8 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa | 4702 | ENSG00000119421 |
| 194  | ENSG00000244005 | NA | NFS1 | NFS1 nitrogen fixation 1 homolog (S. cerevisiae) | 9054 | ENSG00000244005 |
| 195  | ENSG00000104879 | NA | CKM | creatine kinase, muscle | 1158 | ENSG00000104879 |
| 196  | ENSG00000126267 | NA | COX6B1 | cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) | 1340 | ENSG00000126267 |
| 197  | ENSG00000121769 | NA | FABP3 | fatty acid binding protein 3, muscle and heart (mammary-derived growth inhibitor) | 2170 | ENSG00000121769 |
| 198  | ENSG00000100804 | NA | PSMB5 | proteasome (prosome, macropain) subunit, beta type, 5 | 5693 | ENSG00000100804 |
| 199  | ENSG00000145494 | NA | NDUFS6 | NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) | 4726 | ENSG00000145494 |
| 200  | ENSG00000072506 | NA | HSD17B10 | hydroxysteroid (17-beta) dehydrogenase 10 | 3028 | ENSG00000072506 |
| 201  | ENSG00000131143 | NA | COX4I1 | cytochrome c oxidase subunit IV isoform 1 | 1327 | ENSG00000131143 |
| 202  | ENSG00000142546 | NA | NOSIP | nitric oxide synthase interacting protein | 51070 | ENSG00000142546 |
| 203  | ENSG00000105379 | NA | ETFB | electron-transfer-flavoprotein, beta polypeptide | 2109 | ENSG00000105379 |
| 204  | ENSG00000108515 | NA | ENO3 | enolase 3 (beta, muscle) | 2027 | ENSG00000108515 |
| 205  | ENSG00000090266 | NA | NDUFB2 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa | 4708 | ENSG00000090266 |
| 206  | ENSG00000105649 | NA | RAB3A | RAB3A, member RAS oncogene family | 5864 | ENSG00000105649 |
| 207  | ENSG00000047249 | NA | ATP6V1H | ATPase, H+ transporting, lysosomal 50/57kDa, V1 subunit H | 51606 | ENSG00000047249 |
| 208  | ENSG00000151498 | NA | ACAD8 | acyl-CoA dehydrogenase family, member 8 | 27034 | ENSG00000151498 |
| 209  | ENSG00000136143 | NA | SUCLA2 | succinate-CoA ligase, ADP-forming, beta subunit | 8803 | ENSG00000136143 |
| 210  | ENSG00000003137 | NA | CYP26B1 | cytochrome P450, family 26, subfamily B, polypeptide 1 | 56603 | ENSG00000003137 |
| 211  | ENSG00000159199 | NA | ATP5G1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) | 516 | ENSG00000159199 |
| 212  | ENSG00000173614 | NA | NMNAT1 | nicotinamide nucleotide adenylyltransferase 1 | 64802 | ENSG00000173614 |
| 213  | ENSG00000082146 | NA | STRADB | STE20-related kinase adaptor beta | 55437 | ENSG00000082146 |
| 214  | ENSG00000116171 | NA | SCP2 | sterol carrier protein 2 | 6342 | ENSG00000116171 |
| 215  | ENSG00000129084 | NA | PSMA1 | proteasome (prosome, macropain) subunit, alpha type, 1 | 5682 | ENSG00000256206 ENSG00000129084 |
| 216  | ENSG00000143374 | NA | TARS2 | threonyl-tRNA synthetase 2, mitochondrial (putative) | 80222 | ENSG00000143374 |
| 217  | ENSG00000013275 | NA | PSMC4 | proteasome (prosome, macropain) 26S subunit, ATPase, 4 | 5704 | ENSG00000013275 |
| 218  | ENSG00000117118 | NA | SDHB | succinate dehydrogenase complex, subunit B, iron sulfur (Ip) | 6390 | ENSG00000117118 |
| 219  | ENSG00000087460 | NA | GNAS | GNAS complex locus | 2778 | ENSG00000087460 |
| 220  | ENSG00000066926 | NA | FECH | ferrochelatase | 2235 | ENSG00000066926 |
| 221  | ENSG00000168827 | NA | GFM1 | G elongation factor, mitochondrial 1 | 85476 | ENSG00000168827 |
| 222  | ENSG00000115944 | NA | COX7A2L | cytochrome c oxidase subunit VIIa polypeptide 2 like | 9167 | ENSG00000115944 |
| 223  | ENSG00000166228 | NA | PCBD1 | pterin-4 alpha-carbinolamine dehydratase/dimerization cofactor of hepatocyte nuclear factor 1 alpha | 5092 | ENSG00000166228 |
| 224  | ENSG00000100294 | NA | MCAT | malonyl CoA:ACP acyltransferase (mitochondrial) | 27349 | ENSG00000100294 |
| 225  | ENSG00000112667 | NA | C6orf108 | chromosome 6 open reading frame 108 | 10591 | ENSG00000112667 |
| 226  | ENSG00000164022 | NA | AIMP1 | aminoacyl tRNA synthetase complex-interacting multifunctional protein 1 | 9255 | ENSG00000164022 |
| 227  | ENSG00000152234 | NA | ATP5A1 | ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle | 498 | ENSG00000152234 |
| 228  | ENSG00000146729 | NA | GBAS | glioblastoma amplified sequence | 2631 | ENSG00000146729 |
| 229  | ENSG00000164494 | NA | PDSS2 | prenyl (decaprenyl) diphosphate synthase, subunit 2 | 57107 | ENSG00000164494 |
| 230  | ENSG00000132763 | NA | MMACHC | methylmalonic aciduria (cobalamin deficiency) cblC type, with homocystinuria | 25974 | ENSG00000132763 |
| 231  | ENSG00000151366 | NA | NDUFC2 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa | 4718 | ENSG00000151366 |
| 232  | ENSG00000128609 | NA | NDUFA5 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa | 4698 | ENSG00000128609 |
| 233  | ENSG00000178802 | NA | MPI | mannose phosphate isomerase | 4351 | ENSG00000178802 |
| 234  | ENSG00000163541 | NA | SUCLG1 | succinate-CoA ligase, alpha subunit | 8802 | ENSG00000163541 |
| 235  | ENSG00000146701 | NA | MDH2 | malate dehydrogenase 2, NAD (mitochondrial) | 4191 | ENSG00000146701 |
| 236  | ENSG00000131730 | NA | CKMT2 | creatine kinase, mitochondrial 2 (sarcomeric) | 1160 | ENSG00000131730 |
| 237  | ENSG00000147123 | NA | NDUFB11 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa | 54539 | ENSG00000147123 |
| 238  | ENSG00000137714 | NA | FDX1 | ferredoxin 1 | 2230 | ENSG00000137714 |
| 239  | ENSG00000169021 | NA | UQCRFS1 | ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 | 7386 | ENSG00000169021 |
| 240  | ENSG00000115652 | NA | UXS1 | UDP-glucuronate decarboxylase 1 | 80146 | ENSG00000115652 |
| 241  | ENSG00000145439 | NA | CBR4 | carbonyl reductase 4 | 84869 | ENSG00000145439 |
| 242  | ENSG00000157881 | NA | PANK4 | pantothenate kinase 4 | 55229 | ENSG00000157881 |
| 243  | ENSG00000170231 | NA | FABP6 | fatty acid binding protein 6, ileal | 2172 | ENSG00000170231 |
| 244  | ENSG00000197943 | NA | PLCG2 | phospholipase C, gamma 2 (phosphatidylinositol-specific) | 5336 | ENSG00000197943 |
| 245  | ENSG00000062485 | NA | CS | citrate synthase | 1431 | ENSG00000062485 |
| 246  | ENSG00000122691 | NA | TWIST1 | twist homolog 1 (Drosophila) | 7291 | ENSG00000122691 |
| 247  | ENSG00000120053 | NA | GOT1 | glutamic-oxaloacetic transaminase 1, soluble (aspartate aminotransferase 1) | 2805 | ENSG00000120053 |
| 248  | ENSG00000189283 | NA | FHIT | fragile histidine triad | 2272 | ENSG00000189283 |
| 249  | ENSG00000174021 | NA | GNG5 | guanine nucleotide binding protein (G protein), gamma 5 | 2787 | ENSG00000174021 |
| 250  | ENSG00000139428 | NA | MMAB | methylmalonic aciduria (cobalamin deficiency) cblB type | 326625 | ENSG00000139428 |
| 251  | ENSG00000185973 | NA | TMLHE | trimethyllysine hydroxylase, epsilon | 55217 | ENSG00000185973 |
| 252  | ENSG00000196562 | NA | SULF2 | sulfatase 2 | 55959 | ENSG00000196562 |
| 253  | ENSG00000137513 | NA | NARS2 | asparaginyl-tRNA synthetase 2, mitochondrial (putative) | 79731 | ENSG00000137513 |
| 254  | ENSG00000124370 | NA | MCEE | methylmalonyl CoA epimerase | 84693 | ENSG00000124370 |
| 255  | ENSG00000164405 | NA | UQCRQ | ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa | 27089 | ENSG00000164405 |
| 256  | ENSG00000136930 | NA | PSMB7 | proteasome (prosome, macropain) subunit, beta type, 7 | 5695 | ENSG00000136930 |
| 257  | ENSG00000122729 | NA | ACO1 | aconitase 1, soluble | 48 | ENSG00000122729 |
| 258  | ENSG00000173085 | NA | COQ2 | coenzyme Q2 homolog, prenyltransferase (yeast) | 27235 | ENSG00000173085 |
| 259  | ENSG00000124767 | NA | GLO1 | glyoxalase I | 2739 | ENSG00000124767 |
| 260  | ENSG00000124172 | NA | ATP5E | ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit | 514 | ENSG00000124172 |
| 261  | ENSG00000183648 | NA | NDUFB1 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa | 4707 | ENSG00000183648 |
| 262  | ENSG00000110435 | NA | PDHX | pyruvate dehydrogenase complex, component X | 8050 | ENSG00000110435 |
| 263  | ENSG00000099624 | NA | ATP5D | ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit | 513 | ENSG00000099624 |
| 264  | ENSG00000100412 | NA | ACO2 | aconitase 2, mitochondrial | 50 | ENSG00000100412 |
| 265  | ENSG00000125356 | NA | NDUFA1 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa | 4694 | ENSG00000125356 |
| 266  | ENSG00000108528 | NA | SLC25A11 | solute carrier family 25 (mitochondrial carrier; oxoglutarate carrier), member 11 | 8402 | ENSG00000108528 |
| 267  | ENSG00000119673 | NA | ACOT2 | acyl-CoA thioesterase 2 | 10965 | ENSG00000119673 |
| 268  | ENSG00000163636 | NA | PSMD6 | proteasome (prosome, macropain) 26S subunit, non-ATPase, 6 | 9861 | ENSG00000163636 |
| 269  | ENSG00000137574 | NA | TGS1 | trimethylguanosine synthase 1 | 96764 | ENSG00000137574 |
| 270  | ENSG00000099795 | NA | NDUFB7 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa | 4713 | ENSG00000099795 |
| 271  | ENSG00000153574 | NA | RPIA | ribose 5-phosphate isomerase A | 22934 | ENSG00000153574 |
| 272  | ENSG00000103507 | NA | BCKDK | branched chain ketoacid dehydrogenase kinase | 10295 | ENSG00000103507 |
| 273  | ENSG00000148090 | NA | AUH | AU RNA binding protein/enoyl-CoA hydratase | 549 | ENSG00000148090 |
| 274  | ENSG00000090013 | NA | BLVRB | biliverdin reductase B (flavin reductase (NADPH)) | 645 | ENSG00000090013 |
| 275  | ENSG00000172270 | NA | BSG | basigin (Ok blood group) | 682 | ENSG00000172270 |
| 276  | ENSG00000250479 | NA | CHCHD10 | coiled-coil-helix-coiled-coil-helix domain containing 10 | 400916 | ENSG00000250479 |
| 277  | ENSG00000111817 | NA | DSE | dermatan sulfate epimerase | 29940 | ENSG00000111817 |
| 278  | ENSG00000060971 | NA | ACAA1 | acetyl-CoA acyltransferase 1 | 30 | ENSG00000060971 |
| 279  | ENSG00000150867 | NA | PIP4K2A | phosphatidylinositol-5-phosphate 4-kinase, type II, alpha | 5305 | ENSG00000150867 |
| 280  | ENSG00000164347 | NA | GFM2 | G elongation factor, mitochondrial 2 | 84340 | ENSG00000164347 |
| 281  | ENSG00000119723 | NA | COQ6 | coenzyme Q6 homolog, monooxygenase (S. cerevisiae) | 51004 | ENSG00000119723 |
| 282  | ENSG00000197894 | NA | ADH5 | alcohol dehydrogenase 5 (class III), chi polypeptide | 128 | ENSG00000197894 |
| 283  | ENSG00000112357 | NA | PEX7 | peroxisomal biogenesis factor 7 | 5191 | ENSG00000112357 |
| 284  | ENSG00000197448 | NA | GSTK1 | glutathione S-transferase kappa 1 | 373156 | ENSG00000197448 |
| 285  | ENSG00000167792 | NA | NDUFV1 | NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa | 4723 | ENSG00000167792 |
| 286  | ENSG00000117594 | NA | HSD11B1 | hydroxysteroid (11-beta) dehydrogenase 1 | 3290 | ENSG00000117594 |
| 287  | ENSG00000110717 | NA | NDUFS8 | NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) | 4728 | ENSG00000110717 |
| 288  | ENSG00000165609 | NA | NUDT5 | nudix (nucleoside diphosphate linked moiety X)-type motif 5 | 11164 | ENSG00000165609 |
| 289  | ENSG00000197535 | NA | MYO5A | myosin VA (heavy chain 12, myoxin) | 4644 | ENSG00000197535 |
| 290  | ENSG00000150594 | NA | ADRA2A | adrenoceptor alpha 2A | 150 | ENSG00000150594 |
| 291  | ENSG00000091164 | NA | TXNL1 | thioredoxin-like 1 | 9352 | ENSG00000091164 |
| 292  | ENSG00000198467 | NA | TPM2 | tropomyosin 2 (beta) | 7169 | ENSG00000198467 |
| 293  | ENSG00000159377 | NA | PSMB4 | proteasome (prosome, macropain) subunit, beta type, 4 | 5692 | ENSG00000159377 |
| 294  | ENSG00000127884 | NA | ECHS1 | enoyl CoA hydratase, short chain, 1, mitochondrial | 1892 | ENSG00000127884 |
| 295  | ENSG00000241468 | NA | ATP5J2 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 | 9551 | ENSG00000241468 |
| 296  | ENSG00000213420 | NA | GPC2 | glypican 2 | 221914 | ENSG00000213420 |
| 297  | ENSG00000176340 | NA | COX8A | cytochrome c oxidase subunit VIIIA (ubiquitous) | 1351 | ENSG00000176340 |
| 298  | ENSG00000170266 | NA | GLB1 | galactosidase, beta 1 | 2720 | ENSG00000170266 |
| 299  | ENSG00000101365 | NA | IDH3B | isocitrate dehydrogenase 3 (NAD+) beta | 3420 | ENSG00000101365 |
| 300  | ENSG00000173409 | NA | ARV1 | ARV1 homolog (S. cerevisiae) | 64801 | ENSG00000173409 |
| 301  | ENSG00000241837 | NA | ATP5O | ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit | 539 | ENSG00000241837 |
| 302  | ENSG00000140905 | NA | GCSH | glycine cleavage system protein H (aminomethyl carrier) | 2653 | ENSG00000140905 |
| Database:molecular function       Name:oxidoreductase activity       ID:GO:0016491 | ||||||
|---|---|---|---|---|---|---|
| C=711; O=144; E=42.80; R=3.36; rawP=2.98e-40; adjP=1.75e-37 | ||||||
| Index | UserID | Value | Gene Symbol | Gene Name | EntrezGene | Ensembl |
| 1  | ENSG00000087299 | NA | L2HGDH | L-2-hydroxyglutarate dehydrogenase | 79944 | ENSG00000087299 |
| 2  | ENSG00000187630 | NA | DHRS4L2 | dehydrogenase/reductase (SDR family) member 4 like 2 | 317749 | ENSG00000187630 |
| 3  | ENSG00000165264 | NA | NDUFB6 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa | 4712 | ENSG00000165264 |
| 4  | ENSG00000103316 | NA | CRYM | crystallin, mu | 1428 | ENSG00000103316 |
| 5  | ENSG00000156467 | NA | UQCRB | ubiquinol-cytochrome c reductase binding protein | 7381 | ENSG00000156467 |
| 6  | ENSG00000184076 | NA | UQCR10 | ubiquinol-cytochrome c reductase, complex III subunit X | 29796 | ENSG00000184076 |
| 7  | ENSG00000161281 | NA | COX7A1 | cytochrome c oxidase subunit VIIa polypeptide 1 (muscle) | 1346 | ENSG00000161281 |
| 8  | ENSG00000148672 | NA | GLUD1 | glutamate dehydrogenase 1 | 2746 | ENSG00000148672 |
| 9  | ENSG00000156885 | NA | COX6A2 | cytochrome c oxidase subunit VIa polypeptide 2 | 1339 | ENSG00000156885 |
| 10  | ENSG00000006695 | NA | COX10 | COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) | 1352 | ENSG00000006695 |
| 11  | ENSG00000169084 | NA | DHRSX | dehydrogenase/reductase (SDR family) X-linked | 207063 | ENSG00000169084 |
| 12  | ENSG00000116288 | NA | PARK7 | parkinson protein 7 | 11315 | ENSG00000116288 |
| 13  | ENSG00000128203 | NA | ASPHD2 | aspartate beta-hydroxylase domain containing 2 | 57168 | ENSG00000128203 |
| 14  | ENSG00000239264 | NA | TXNDC5 | thioredoxin domain containing 5 (endoplasmic reticulum) | 81567 | ENSG00000239264 |
| 15  | ENSG00000139531 | NA | SUOX | sulfite oxidase | 6821 | ENSG00000139531 |
| 16  | ENSG00000166136 | NA | NDUFB8 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa | 4714 | ENSG00000166136 |
| 17  | ENSG00000140374 | NA | ETFA | electron-transfer-flavoprotein, alpha polypeptide | 2108 | ENSG00000140374 |
| 18  | ENSG00000116353 | NA | MECR | mitochondrial trans-2-enoyl-CoA reductase | 51102 | ENSG00000116353 |
| 19  | ENSG00000147684 | NA | NDUFB9 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa | 4715 | ENSG00000147684 |
| 20  | ENSG00000160194 | NA | NDUFV3 | NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa | 4731 | ENSG00000160194 |
| 21  | ENSG00000184983 | NA | NDUFA6 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa | 4700 | ENSG00000184983 |
| 22  | ENSG00000130414 | NA | NDUFA10 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa | 4705 | ENSG00000130414 |
| 23  | ENSG00000091140 | NA | DLD | dihydrolipoamide dehydrogenase | 1738 | ENSG00000091140 |
| 24  | ENSG00000165060 | NA | FXN | frataxin | 2395 | ENSG00000165060 |
| 25  | ENSG00000158864 | NA | NDUFS2 | NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) | 4720 | ENSG00000158864 |
| 26  | ENSG00000131828 | NA | PDHA1 | pyruvate dehydrogenase (lipoamide) alpha 1 | 5160 | ENSG00000131828 |
| 27  | ENSG00000122971 | NA | ACADS | acyl-CoA dehydrogenase, C-2 to C-3 short chain | 35 | ENSG00000122971 |
| 28  | ENSG00000142168 | NA | SOD1 | superoxide dismutase 1, soluble | 6647 | ENSG00000142168 |
| 29  | ENSG00000109390 | NA | NDUFC1 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa | 4717 | ENSG00000109390 |
| 30  | ENSG00000182512 | NA | GLRX5 | glutaredoxin 5 | 51218 | ENSG00000182512 |
| 31  | ENSG00000203797 | NA | DDO | D-aspartate oxidase | 8528 | ENSG00000203797 |
| 32  | ENSG00000103160 | NA | HSDL1 | hydroxysteroid dehydrogenase like 1 | 83693 | ENSG00000103160 |
| 33  | ENSG00000120254 | NA | MTHFD1L | methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 1-like | 25902 | ENSG00000120254 |
| 34  | ENSG00000110074 | NA | FOXRED1 | FAD-dependent oxidoreductase domain containing 1 | 55572 | ENSG00000110074 |
| 35  | ENSG00000168291 | NA | PDHB | pyruvate dehydrogenase (lipoamide) beta | 5162 | ENSG00000168291 |
| 36  | ENSG00000148334 | NA | PTGES2 | prostaglandin E synthase 2 | 80142 | ENSG00000148334 |
| 37  | ENSG00000119537 | NA | KDSR | 3-ketodihydrosphingosine reductase | 2531 | ENSG00000119537 |
| 38  | ENSG00000112992 | NA | NNT | nicotinamide nucleotide transhydrogenase | 23530 | ENSG00000112992 |
| 39  | ENSG00000126432 | NA | PRDX5 | peroxiredoxin 5 | 25824 | ENSG00000126432 |
| 40  | ENSG00000178741 | NA | COX5A | cytochrome c oxidase subunit Va | 9377 | ENSG00000178741 |
| 41  | ENSG00000213619 | NA | NDUFS3 | NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) | 4722 | ENSG00000213619 |
| 42  | ENSG00000173660 | NA | UQCRH | ubiquinol-cytochrome c reductase hinge protein | 7388 | ENSG00000173660 |
| 43  | ENSG00000119421 | NA | NDUFA8 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa | 4702 | ENSG00000119421 |
| 44  | ENSG00000100348 | NA | TXN2 | thioredoxin 2 | 25828 | ENSG00000100348 |
| 45  | ENSG00000130347 | NA | RTN4IP1 | reticulon 4 interacting protein 1 | 84816 | ENSG00000130347 |
| 46  | ENSG00000126267 | NA | COX6B1 | cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) | 1340 | ENSG00000126267 |
| 47  | ENSG00000135940 | NA | COX5B | cytochrome c oxidase subunit Vb | 1329 | ENSG00000135940 |
| 48  | ENSG00000154814 | NA | OXNAD1 | oxidoreductase NAD-binding domain containing 1 | 92106 | ENSG00000154814 |
| 49  | ENSG00000113790 | NA | EHHADH | enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase | 1962 | ENSG00000113790 |
| 50  | ENSG00000148450 | NA | MSRB2 | methionine sulfoxide reductase B2 | 22921 | ENSG00000148450 |
| 51  | ENSG00000145494 | NA | NDUFS6 | NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) | 4726 | ENSG00000145494 |
| 52  | ENSG00000156709 | NA | AIFM1 | apoptosis-inducing factor, mitochondrion-associated, 1 | 9131 | ENSG00000156709 |
| 53  | ENSG00000072506 | NA | HSD17B10 | hydroxysteroid (17-beta) dehydrogenase 10 | 3028 | ENSG00000072506 |
| 54  | ENSG00000189043 | NA | NDUFA4 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa | 4697 | ENSG00000189043 |
| 55  | ENSG00000131143 | NA | COX4I1 | cytochrome c oxidase subunit IV isoform 1 | 1327 | ENSG00000131143 |
| 56  | ENSG00000164919 | NA | COX6C | cytochrome c oxidase subunit VIc | 1345 | ENSG00000164919 |
| 57  | ENSG00000136444 | NA | RSAD1 | radical S-adenosyl methionine domain containing 1 | 55316 | ENSG00000136444 |
| 58  | ENSG00000115286 | NA | NDUFS7 | NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) | 374291 | ENSG00000115286 |
| 59  | ENSG00000164258 | NA | NDUFS4 | NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) | 4724 | ENSG00000164258 |
| 60  | ENSG00000132570 | NA | PCBD2 | pterin-4 alpha-carbinolamine dehydratase/dimerization cofactor of hepatocyte nuclear factor 1 alpha (TCF1) 2 | 84105 | ENSG00000132570 |
| 61  | ENSG00000090266 | NA | NDUFB2 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa | 4708 | ENSG00000090266 |
| 62  | ENSG00000184860 | NA | SDR42E1 | short chain dehydrogenase/reductase family 42E, member 1 | 93517 | ENSG00000184860 |
| 63  | ENSG00000127540 | NA | UQCR11 | ubiquinol-cytochrome c reductase, complex III subunit XI | 10975 | ENSG00000127540 |
| 64  | ENSG00000151498 | NA | ACAD8 | acyl-CoA dehydrogenase family, member 8 | 27034 | ENSG00000151498 |
| 65  | ENSG00000184752 | NA | NDUFA12 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 | 55967 | ENSG00000184752 |
| 66  | ENSG00000003137 | NA | CYP26B1 | cytochrome P450, family 26, subfamily B, polypeptide 1 | 56603 | ENSG00000003137 |
| 67  | ENSG00000204228 | NA | HSD17B8 | hydroxysteroid (17-beta) dehydrogenase 8 | 7923 | ENSG00000204228 |
| 68  | ENSG00000067829 | NA | IDH3G | isocitrate dehydrogenase 3 (NAD+) gamma | 3421 | ENSG00000067829 |
| 69  | ENSG00000130159 | NA | ECSIT | ECSIT homolog (Drosophila) | 51295 | ENSG00000130159 |
| 70  | ENSG00000167815 | NA | PRDX2 | peroxiredoxin 2 | 7001 | ENSG00000167815 |
| 71  | ENSG00000166816 | NA | LDHD | lactate dehydrogenase D | 197257 | ENSG00000166816 |
| 72  | ENSG00000140990 | NA | NDUFB10 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa | 4716 | ENSG00000140990 |
| 73  | ENSG00000157326 | NA | DHRS4 | dehydrogenase/reductase (SDR family) member 4 | 10901 | ENSG00000157326 |
| 74  | ENSG00000117118 | NA | SDHB | succinate dehydrogenase complex, subunit B, iron sulfur (Ip) | 6390 | ENSG00000117118 |
| 75  | ENSG00000143653 | NA | SCCPDH | saccharopine dehydrogenase (putative) | 51097 | ENSG00000143653 |
| 76  | ENSG00000149380 | NA | P4HA3 | prolyl 4-hydroxylase, alpha polypeptide III | 283208 | ENSG00000149380 |
| 77  | ENSG00000115944 | NA | COX7A2L | cytochrome c oxidase subunit VIIa polypeptide 2 like | 9167 | ENSG00000115944 |
| 78  | ENSG00000166228 | NA | PCBD1 | pterin-4 alpha-carbinolamine dehydratase/dimerization cofactor of hepatocyte nuclear factor 1 alpha | 5092 | ENSG00000166228 |
| 79  | ENSG00000148290 | NA | SURF1 | surfeit 1 | 6834 | ENSG00000148290 |
| 80  | ENSG00000014641 | NA | MDH1 | malate dehydrogenase 1, NAD (soluble) | 4190 | ENSG00000014641 |
| 81  | ENSG00000072778 | NA | ACADVL | acyl-CoA dehydrogenase, very long chain | 37 | ENSG00000072778 |
| 82  | ENSG00000172893 | NA | DHCR7 | 7-dehydrocholesterol reductase | 1717 | ENSG00000172893 |
| 83  | ENSG00000125652 | NA | ALKBH7 | alkB, alkylation repair homolog 7 (E. coli) | 84266 | ENSG00000125652 |
| 84  | ENSG00000128609 | NA | NDUFA5 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa | 4698 | ENSG00000128609 |
| 85  | ENSG00000151366 | NA | NDUFC2 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa | 4718 | ENSG00000151366 |
| 86  | ENSG00000146701 | NA | MDH2 | malate dehydrogenase 2, NAD (mitochondrial) | 4191 | ENSG00000146701 |
| 87  | ENSG00000136521 | NA | NDUFB5 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa | 4711 | ENSG00000136521 |
| 88  | ENSG00000182054 | NA | IDH2 | isocitrate dehydrogenase 2 (NADP+), mitochondrial | 3418 | ENSG00000182054 |
| 89  | ENSG00000004779 | NA | NDUFAB1 | NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa | 4706 | ENSG00000004779 |
| 90  | ENSG00000085871 | NA | MGST2 | microsomal glutathione S-transferase 2 | 4258 | ENSG00000085871 |
| 91  | ENSG00000073578 | NA | SDHA | succinate dehydrogenase complex, subunit A, flavoprotein (Fp) | 6389 | ENSG00000073578 |
| 92  | ENSG00000137714 | NA | FDX1 | ferredoxin 1 | 2230 | ENSG00000137714 |
| 93  | ENSG00000119013 | NA | NDUFB3 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa | 4709 | ENSG00000119013 |
| 94  | ENSG00000169021 | NA | UQCRFS1 | ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 | 7386 | ENSG00000169021 |
| 95  | ENSG00000104325 | NA | DECR1 | 2,4-dienoyl CoA reductase 1, mitochondrial | 1666 | ENSG00000104325 |
| 96  | ENSG00000145439 | NA | CBR4 | carbonyl reductase 4 | 84869 | ENSG00000145439 |
| 97  | ENSG00000160439 | NA | RDH13 | retinol dehydrogenase 13 (all-trans/9-cis) | 112724 | ENSG00000160439 |
| 98  | ENSG00000185973 | NA | TMLHE | trimethyllysine hydroxylase, epsilon | 55217 | ENSG00000185973 |
| 99  | ENSG00000167468 | NA | GPX4 | glutathione peroxidase 4 | 2879 | ENSG00000167468 |
| 100  | ENSG00000139180 | NA | NDUFA9 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa | 4704 | ENSG00000139180 |
| 101  | ENSG00000111640 | NA | GAPDH | glyceraldehyde-3-phosphate dehydrogenase | 2597 | ENSG00000111640 |
| 102  | ENSG00000127184 | NA | COX7C | cytochrome c oxidase subunit VIIc | 1350 | ENSG00000127184 |
| 103  | ENSG00000164405 | NA | UQCRQ | ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa | 27089 | ENSG00000164405 |
| 104  | ENSG00000183648 | NA | NDUFB1 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa | 4707 | ENSG00000183648 |
| 105  | ENSG00000204370 | NA | SDHD | succinate dehydrogenase complex, subunit D, integral membrane protein | 6392 | ENSG00000204370 |
| 106  | ENSG00000137106 | NA | GRHPR | glyoxylate reductase/hydroxypyruvate reductase | 9380 | ENSG00000137106 |
| 107  | ENSG00000169738 | NA | DCXR | dicarbonyl/L-xylulose reductase | 51181 | ENSG00000169738 |
| 108  | ENSG00000111271 | NA | ACAD10 | acyl-CoA dehydrogenase family, member 10 | 80724 | ENSG00000111271 |
| 109  | ENSG00000160211 | NA | G6PD | glucose-6-phosphate dehydrogenase | 2539 | ENSG00000160211 |
| 110  | ENSG00000125356 | NA | NDUFA1 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa | 4694 | ENSG00000125356 |
| 111  | ENSG00000100601 | NA | ALKBH1 | alkB, alkylation repair homolog 1 (E. coli) | 8846 | ENSG00000100601 |
| 112  | ENSG00000099795 | NA | NDUFB7 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa | 4713 | ENSG00000099795 |
| 113  | ENSG00000023228 | NA | NDUFS1 | NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) | 4719 | ENSG00000023228 |
| 114  | ENSG00000143252 | NA | SDHC | succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa | 6391 | ENSG00000143252 |
| 115  | ENSG00000151376 | NA | ME3 | malic enzyme 3, NADP(+)-dependent, mitochondrial | 10873 | ENSG00000151376 |
| 116  | ENSG00000090013 | NA | BLVRB | biliverdin reductase B (flavin reductase (NADPH)) | 645 | ENSG00000090013 |
| 117  | ENSG00000060971 | NA | ACAA1 | acetyl-CoA acyltransferase 1 | 30 | ENSG00000060971 |
| 118  | ENSG00000119723 | NA | COQ6 | coenzyme Q6 homolog, monooxygenase (S. cerevisiae) | 51004 | ENSG00000119723 |
| 119  | ENSG00000112695 | NA | COX7A2 | cytochrome c oxidase subunit VIIa polypeptide 2 (liver) | 1347 | ENSG00000112695 |
| 120  | ENSG00000198736 | NA | MSRB1 | methionine sulfoxide reductase B1 | 51734 | ENSG00000198736 |
| 121  | ENSG00000197894 | NA | ADH5 | alcohol dehydrogenase 5 (class III), chi polypeptide | 128 | ENSG00000197894 |
| 122  | ENSG00000197448 | NA | GSTK1 | glutathione S-transferase kappa 1 | 373156 | ENSG00000197448 |
| 123  | ENSG00000167792 | NA | NDUFV1 | NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa | 4723 | ENSG00000167792 |
| 124  | ENSG00000131495 | NA | NDUFA2 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa | 4695 | ENSG00000131495 |
| 125  | ENSG00000065518 | NA | NDUFB4 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa | 4710 | ENSG00000065518 |
| 126  | ENSG00000117594 | NA | HSD11B1 | hydroxysteroid (11-beta) dehydrogenase 1 | 3290 | ENSG00000117594 |
| 127  | ENSG00000110717 | NA | NDUFS8 | NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) | 4728 | ENSG00000110717 |
| 128  | ENSG00000197580 | NA | BCO2 | beta-carotene oxygenase 2 | 83875 | ENSG00000197580 |
| 129  | ENSG00000131174 | NA | COX7B | cytochrome c oxidase subunit VIIb | 1349 | ENSG00000131174 |
| 130  | ENSG00000170906 | NA | NDUFA3 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa | 4696 | ENSG00000170906 |
| 131  | ENSG00000184719 | NA | RNLS | renalase, FAD-dependent amine oxidase | 55328 | ENSG00000184719 |
| 132  | ENSG00000111716 | NA | LDHB | lactate dehydrogenase B | 3945 | ENSG00000111716 |
| 133  | ENSG00000091164 | NA | TXNL1 | thioredoxin-like 1 | 9352 | ENSG00000091164 |
| 134  | ENSG00000108439 | NA | PNPO | pyridoxamine 5'-phosphate oxidase | 55163 | ENSG00000108439 |
| 135  | ENSG00000111275 | NA | ALDH2 | aldehyde dehydrogenase 2 family (mitochondrial) | 217 | ENSG00000111275 |
| 136  | ENSG00000117139 | NA | KDM5B | lysine (K)-specific demethylase 5B | 10765 | ENSG00000117139 |
| 137  | ENSG00000010256 | NA | UQCRC1 | ubiquinol-cytochrome c reductase core protein I | 7384 | ENSG00000010256 |
| 138  | ENSG00000171503 | NA | ETFDH | electron-transferring-flavoprotein dehydrogenase | 2110 | ENSG00000171503 |
| 139  | ENSG00000138796 | NA | HADH | hydroxyacyl-CoA dehydrogenase | 3033 | ENSG00000138796 |
| 140  | ENSG00000165672 | NA | PRDX3 | peroxiredoxin 3 | 10935 | ENSG00000165672 |
| 141  | ENSG00000161533 | NA | ACOX1 | acyl-CoA oxidase 1, palmitoyl | 51 | ENSG00000161533 |
| 142  | ENSG00000176340 | NA | COX8A | cytochrome c oxidase subunit VIIIA (ubiquitous) | 1351 | ENSG00000176340 |
| 143  | ENSG00000168653 | NA | NDUFS5 | NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) | 4725 | ENSG00000168653 |
| 144  | ENSG00000101365 | NA | IDH3B | isocitrate dehydrogenase 3 (NAD+) beta | 3420 | ENSG00000101365 |
| Database:molecular function       Name:NADH dehydrogenase (ubiquinone) activity       ID:GO:0008137 | ||||||
|---|---|---|---|---|---|---|
| C=44; O=33; E=2.65; R=12.46; rawP=1.24e-31; adjP=1.82e-29 | ||||||
| Index | UserID | Value | Gene Symbol | Gene Name | EntrezGene | Ensembl |
| 1  | ENSG00000151366 | NA | NDUFC2 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa | 4718 | ENSG00000151366 |
| 2  | ENSG00000128609 | NA | NDUFA5 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa | 4698 | ENSG00000128609 |
| 3  | ENSG00000023228 | NA | NDUFS1 | NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) | 4719 | ENSG00000023228 |
| 4  | ENSG00000165264 | NA | NDUFB6 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa | 4712 | ENSG00000165264 |
| 5  | ENSG00000145494 | NA | NDUFS6 | NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) | 4726 | ENSG00000145494 |
| 6  | ENSG00000136521 | NA | NDUFB5 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa | 4711 | ENSG00000136521 |
| 7  | ENSG00000004779 | NA | NDUFAB1 | NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa | 4706 | ENSG00000004779 |
| 8  | ENSG00000189043 | NA | NDUFA4 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa | 4697 | ENSG00000189043 |
| 9  | ENSG00000115286 | NA | NDUFS7 | NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) | 374291 | ENSG00000115286 |
| 10  | ENSG00000164258 | NA | NDUFS4 | NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) | 4724 | ENSG00000164258 |
| 11  | ENSG00000119013 | NA | NDUFB3 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa | 4709 | ENSG00000119013 |
| 12  | ENSG00000167792 | NA | NDUFV1 | NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa | 4723 | ENSG00000167792 |
| 13  | ENSG00000131495 | NA | NDUFA2 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa | 4695 | ENSG00000131495 |
| 14  | ENSG00000065518 | NA | NDUFB4 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa | 4710 | ENSG00000065518 |
| 15  | ENSG00000090266 | NA | NDUFB2 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa | 4708 | ENSG00000090266 |
| 16  | ENSG00000166136 | NA | NDUFB8 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa | 4714 | ENSG00000166136 |
| 17  | ENSG00000110717 | NA | NDUFS8 | NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) | 4728 | ENSG00000110717 |
| 18  | ENSG00000147684 | NA | NDUFB9 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa | 4715 | ENSG00000147684 |
| 19  | ENSG00000160194 | NA | NDUFV3 | NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa | 4731 | ENSG00000160194 |
| 20  | ENSG00000184983 | NA | NDUFA6 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa | 4700 | ENSG00000184983 |
| 21  | ENSG00000170906 | NA | NDUFA3 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa | 4696 | ENSG00000170906 |
| 22  | ENSG00000184752 | NA | NDUFA12 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 | 55967 | ENSG00000184752 |
| 23  | ENSG00000130414 | NA | NDUFA10 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa | 4705 | ENSG00000130414 |
| 24  | ENSG00000158864 | NA | NDUFS2 | NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) | 4720 | ENSG00000158864 |
| 25  | ENSG00000139180 | NA | NDUFA9 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa | 4704 | ENSG00000139180 |
| 26  | ENSG00000109390 | NA | NDUFC1 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa | 4717 | ENSG00000109390 |
| 27  | ENSG00000183648 | NA | NDUFB1 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa | 4707 | ENSG00000183648 |
| 28  | ENSG00000140990 | NA | NDUFB10 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa | 4716 | ENSG00000140990 |
| 29  | ENSG00000125356 | NA | NDUFA1 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa | 4694 | ENSG00000125356 |
| 30  | ENSG00000213619 | NA | NDUFS3 | NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) | 4722 | ENSG00000213619 |
| 31  | ENSG00000168653 | NA | NDUFS5 | NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) | 4725 | ENSG00000168653 |
| 32  | ENSG00000119421 | NA | NDUFA8 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa | 4702 | ENSG00000119421 |
| 33  | ENSG00000099795 | NA | NDUFB7 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa | 4713 | ENSG00000099795 |
| Database:molecular function       Name:NADH dehydrogenase activity       ID:GO:0003954 | ||||||
|---|---|---|---|---|---|---|
| C=44; O=33; E=2.65; R=12.46; rawP=1.24e-31; adjP=1.82e-29 | ||||||
| Index | UserID | Value | Gene Symbol | Gene Name | EntrezGene | Ensembl |
| 1  | ENSG00000151366 | NA | NDUFC2 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa | 4718 | ENSG00000151366 |
| 2  | ENSG00000128609 | NA | NDUFA5 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa | 4698 | ENSG00000128609 |
| 3  | ENSG00000023228 | NA | NDUFS1 | NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) | 4719 | ENSG00000023228 |
| 4  | ENSG00000165264 | NA | NDUFB6 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa | 4712 | ENSG00000165264 |
| 5  | ENSG00000145494 | NA | NDUFS6 | NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) | 4726 | ENSG00000145494 |
| 6  | ENSG00000136521 | NA | NDUFB5 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa | 4711 | ENSG00000136521 |
| 7  | ENSG00000004779 | NA | NDUFAB1 | NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa | 4706 | ENSG00000004779 |
| 8  | ENSG00000189043 | NA | NDUFA4 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa | 4697 | ENSG00000189043 |
| 9  | ENSG00000115286 | NA | NDUFS7 | NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) | 374291 | ENSG00000115286 |
| 10  | ENSG00000164258 | NA | NDUFS4 | NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) | 4724 | ENSG00000164258 |
| 11  | ENSG00000119013 | NA | NDUFB3 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa | 4709 | ENSG00000119013 |
| 12  | ENSG00000167792 | NA | NDUFV1 | NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa | 4723 | ENSG00000167792 |
| 13  | ENSG00000131495 | NA | NDUFA2 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa | 4695 | ENSG00000131495 |
| 14  | ENSG00000065518 | NA | NDUFB4 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa | 4710 | ENSG00000065518 |
| 15  | ENSG00000090266 | NA | NDUFB2 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa | 4708 | ENSG00000090266 |
| 16  | ENSG00000166136 | NA | NDUFB8 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa | 4714 | ENSG00000166136 |
| 17  | ENSG00000110717 | NA | NDUFS8 | NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) | 4728 | ENSG00000110717 |
| 18  | ENSG00000147684 | NA | NDUFB9 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa | 4715 | ENSG00000147684 |
| 19  | ENSG00000160194 | NA | NDUFV3 | NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa | 4731 | ENSG00000160194 |
| 20  | ENSG00000184983 | NA | NDUFA6 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa | 4700 | ENSG00000184983 |
| 21  | ENSG00000170906 | NA | NDUFA3 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa | 4696 | ENSG00000170906 |
| 22  | ENSG00000184752 | NA | NDUFA12 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 | 55967 | ENSG00000184752 |
| 23  | ENSG00000130414 | NA | NDUFA10 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa | 4705 | ENSG00000130414 |
| 24  | ENSG00000158864 | NA | NDUFS2 | NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) | 4720 | ENSG00000158864 |
| 25  | ENSG00000139180 | NA | NDUFA9 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa | 4704 | ENSG00000139180 |
| 26  | ENSG00000109390 | NA | NDUFC1 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa | 4717 | ENSG00000109390 |
| 27  | ENSG00000183648 | NA | NDUFB1 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa | 4707 | ENSG00000183648 |
| 28  | ENSG00000140990 | NA | NDUFB10 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa | 4716 | ENSG00000140990 |
| 29  | ENSG00000125356 | NA | NDUFA1 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa | 4694 | ENSG00000125356 |
| 30  | ENSG00000213619 | NA | NDUFS3 | NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) | 4722 | ENSG00000213619 |
| 31  | ENSG00000168653 | NA | NDUFS5 | NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) | 4725 | ENSG00000168653 |
| 32  | ENSG00000119421 | NA | NDUFA8 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa | 4702 | ENSG00000119421 |
| 33  | ENSG00000099795 | NA | NDUFB7 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa | 4713 | ENSG00000099795 |
| Database:molecular function       Name:NADH dehydrogenase (quinone) activity       ID:GO:0050136 | ||||||
|---|---|---|---|---|---|---|
| C=44; O=33; E=2.65; R=12.46; rawP=1.24e-31; adjP=1.82e-29 | ||||||
| Index | UserID | Value | Gene Symbol | Gene Name | EntrezGene | Ensembl |
| 1  | ENSG00000151366 | NA | NDUFC2 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa | 4718 | ENSG00000151366 |
| 2  | ENSG00000128609 | NA | NDUFA5 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa | 4698 | ENSG00000128609 |
| 3  | ENSG00000023228 | NA | NDUFS1 | NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) | 4719 | ENSG00000023228 |
| 4  | ENSG00000165264 | NA | NDUFB6 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa | 4712 | ENSG00000165264 |
| 5  | ENSG00000145494 | NA | NDUFS6 | NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) | 4726 | ENSG00000145494 |
| 6  | ENSG00000136521 | NA | NDUFB5 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa | 4711 | ENSG00000136521 |
| 7  | ENSG00000004779 | NA | NDUFAB1 | NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa | 4706 | ENSG00000004779 |
| 8  | ENSG00000189043 | NA | NDUFA4 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa | 4697 | ENSG00000189043 |
| 9  | ENSG00000115286 | NA | NDUFS7 | NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) | 374291 | ENSG00000115286 |
| 10  | ENSG00000164258 | NA | NDUFS4 | NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) | 4724 | ENSG00000164258 |
| 11  | ENSG00000119013 | NA | NDUFB3 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa | 4709 | ENSG00000119013 |
| 12  | ENSG00000167792 | NA | NDUFV1 | NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa | 4723 | ENSG00000167792 |
| 13  | ENSG00000131495 | NA | NDUFA2 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa | 4695 | ENSG00000131495 |
| 14  | ENSG00000065518 | NA | NDUFB4 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa | 4710 | ENSG00000065518 |
| 15  | ENSG00000090266 | NA | NDUFB2 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa | 4708 | ENSG00000090266 |
| 16  | ENSG00000166136 | NA | NDUFB8 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa | 4714 | ENSG00000166136 |
| 17  | ENSG00000110717 | NA | NDUFS8 | NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) | 4728 | ENSG00000110717 |
| 18  | ENSG00000147684 | NA | NDUFB9 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa | 4715 | ENSG00000147684 |
| 19  | ENSG00000160194 | NA | NDUFV3 | NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa | 4731 | ENSG00000160194 |
| 20  | ENSG00000184983 | NA | NDUFA6 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa | 4700 | ENSG00000184983 |
| 21  | ENSG00000170906 | NA | NDUFA3 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa | 4696 | ENSG00000170906 |
| 22  | ENSG00000184752 | NA | NDUFA12 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 | 55967 | ENSG00000184752 |
| 23  | ENSG00000130414 | NA | NDUFA10 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa | 4705 | ENSG00000130414 |
| 24  | ENSG00000158864 | NA | NDUFS2 | NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) | 4720 | ENSG00000158864 |
| 25  | ENSG00000139180 | NA | NDUFA9 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa | 4704 | ENSG00000139180 |
| 26  | ENSG00000109390 | NA | NDUFC1 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa | 4717 | ENSG00000109390 |
| 27  | ENSG00000183648 | NA | NDUFB1 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa | 4707 | ENSG00000183648 |
| 28  | ENSG00000140990 | NA | NDUFB10 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa | 4716 | ENSG00000140990 |
| 29  | ENSG00000125356 | NA | NDUFA1 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa | 4694 | ENSG00000125356 |
| 30  | ENSG00000213619 | NA | NDUFS3 | NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) | 4722 | ENSG00000213619 |
| 31  | ENSG00000168653 | NA | NDUFS5 | NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) | 4725 | ENSG00000168653 |
| 32  | ENSG00000119421 | NA | NDUFA8 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa | 4702 | ENSG00000119421 |
| 33  | ENSG00000099795 | NA | NDUFB7 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa | 4713 | ENSG00000099795 |
| Database:molecular function       Name:oxidoreductase activity, acting on NADH or NADPH, quinone or similar compound as acceptor       ID:GO:0016655 | ||||||
|---|---|---|---|---|---|---|
| C=58; O=36; E=3.49; R=10.31; rawP=9.45e-30; adjP=1.11e-27 | ||||||
| Index | UserID | Value | Gene Symbol | Gene Name | EntrezGene | Ensembl |
| 1  | ENSG00000151366 | NA | NDUFC2 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa | 4718 | ENSG00000151366 |
| 2  | ENSG00000128609 | NA | NDUFA5 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa | 4698 | ENSG00000128609 |
| 3  | ENSG00000023228 | NA | NDUFS1 | NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) | 4719 | ENSG00000023228 |
| 4  | ENSG00000165264 | NA | NDUFB6 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa | 4712 | ENSG00000165264 |
| 5  | ENSG00000145494 | NA | NDUFS6 | NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) | 4726 | ENSG00000145494 |
| 6  | ENSG00000136521 | NA | NDUFB5 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa | 4711 | ENSG00000136521 |
| 7  | ENSG00000004779 | NA | NDUFAB1 | NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa | 4706 | ENSG00000004779 |
| 8  | ENSG00000189043 | NA | NDUFA4 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa | 4697 | ENSG00000189043 |
| 9  | ENSG00000115286 | NA | NDUFS7 | NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) | 374291 | ENSG00000115286 |
| 10  | ENSG00000164258 | NA | NDUFS4 | NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) | 4724 | ENSG00000164258 |
| 11  | ENSG00000119013 | NA | NDUFB3 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa | 4709 | ENSG00000119013 |
| 12  | ENSG00000167792 | NA | NDUFV1 | NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa | 4723 | ENSG00000167792 |
| 13  | ENSG00000131495 | NA | NDUFA2 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa | 4695 | ENSG00000131495 |
| 14  | ENSG00000065518 | NA | NDUFB4 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa | 4710 | ENSG00000065518 |
| 15  | ENSG00000145439 | NA | CBR4 | carbonyl reductase 4 | 84869 | ENSG00000145439 |
| 16  | ENSG00000090266 | NA | NDUFB2 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa | 4708 | ENSG00000090266 |
| 17  | ENSG00000166136 | NA | NDUFB8 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa | 4714 | ENSG00000166136 |
| 18  | ENSG00000110717 | NA | NDUFS8 | NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) | 4728 | ENSG00000110717 |
| 19  | ENSG00000147684 | NA | NDUFB9 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa | 4715 | ENSG00000147684 |
| 20  | ENSG00000160194 | NA | NDUFV3 | NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa | 4731 | ENSG00000160194 |
| 21  | ENSG00000184983 | NA | NDUFA6 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa | 4700 | ENSG00000184983 |
| 22  | ENSG00000170906 | NA | NDUFA3 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa | 4696 | ENSG00000170906 |
| 23  | ENSG00000184752 | NA | NDUFA12 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 | 55967 | ENSG00000184752 |
| 24  | ENSG00000130414 | NA | NDUFA10 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa | 4705 | ENSG00000130414 |
| 25  | ENSG00000158864 | NA | NDUFS2 | NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) | 4720 | ENSG00000158864 |
| 26  | ENSG00000139180 | NA | NDUFA9 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa | 4704 | ENSG00000139180 |
| 27  | ENSG00000109390 | NA | NDUFC1 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa | 4717 | ENSG00000109390 |
| 28  | ENSG00000183648 | NA | NDUFB1 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa | 4707 | ENSG00000183648 |
| 29  | ENSG00000157326 | NA | DHRS4 | dehydrogenase/reductase (SDR family) member 4 | 10901 | ENSG00000157326 |
| 30  | ENSG00000140990 | NA | NDUFB10 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa | 4716 | ENSG00000140990 |
| 31  | ENSG00000169738 | NA | DCXR | dicarbonyl/L-xylulose reductase | 51181 | ENSG00000169738 |
| 32  | ENSG00000125356 | NA | NDUFA1 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa | 4694 | ENSG00000125356 |
| 33  | ENSG00000213619 | NA | NDUFS3 | NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) | 4722 | ENSG00000213619 |
| 34  | ENSG00000168653 | NA | NDUFS5 | NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) | 4725 | ENSG00000168653 |
| 35  | ENSG00000099795 | NA | NDUFB7 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa | 4713 | ENSG00000099795 |
| 36  | ENSG00000119421 | NA | NDUFA8 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa | 4702 | ENSG00000119421 |
| Database:molecular function       Name:catalytic activity       ID:GO:0003824 | ||||||
|---|---|---|---|---|---|---|
| C=5371; O=478; E=323.30; R=1.48; rawP=3.58e-27; adjP=3.50e-25 | ||||||
| Index | UserID | Value | Gene Symbol | Gene Name | EntrezGene | Ensembl |
| 1  | ENSG00000070501 | NA | POLB | polymerase (DNA directed), beta | 5423 | ENSG00000070501 |
| 2  | ENSG00000187630 | NA | DHRS4L2 | dehydrogenase/reductase (SDR family) member 4 like 2 | 317749 | ENSG00000187630 |
| 3  | ENSG00000038295 | NA | TLL1 | tolloid-like 1 | 7092 | ENSG00000038295 |
| 4  | ENSG00000168803 | NA | ADAL | adenosine deaminase-like | 161823 | ENSG00000168803 |
| 5  | ENSG00000165264 | NA | NDUFB6 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa | 4712 | ENSG00000165264 |
| 6  | ENSG00000161281 | NA | COX7A1 | cytochrome c oxidase subunit VIIa polypeptide 1 (muscle) | 1346 | ENSG00000161281 |
| 7  | ENSG00000167862 | NA | ICT1 | immature colon carcinoma transcript 1 | 3396 | ENSG00000167862 |
| 8  | ENSG00000067596 | NA | DHX8 | DEAH (Asp-Glu-Ala-His) box polypeptide 8 | 1659 | ENSG00000067596 |
| 9  | ENSG00000148672 | NA | GLUD1 | glutamate dehydrogenase 1 | 2746 | ENSG00000148672 |
| 10  | ENSG00000147592 | NA | LACTB2 | lactamase, beta 2 | 51110 | ENSG00000147592 |
| 11  | ENSG00000164172 | NA | MOCS2 | molybdenum cofactor synthesis 2 | 4338 | ENSG00000164172 |
| 12  | ENSG00000116288 | NA | PARK7 | parkinson protein 7 | 11315 | ENSG00000116288 |
| 13  | ENSG00000128203 | NA | ASPHD2 | aspartate beta-hydroxylase domain containing 2 | 57168 | ENSG00000128203 |
| 14  | ENSG00000239264 | NA | TXNDC5 | thioredoxin domain containing 5 (endoplasmic reticulum) | 81567 | ENSG00000239264 |
| 15  | ENSG00000134109 | NA | EDEM1 | ER degradation enhancer, mannosidase alpha-like 1 | 9695 | ENSG00000134109 |
| 16  | ENSG00000166136 | NA | NDUFB8 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa | 4714 | ENSG00000166136 |
| 17  | ENSG00000116353 | NA | MECR | mitochondrial trans-2-enoyl-CoA reductase | 51102 | ENSG00000116353 |
| 18  | ENSG00000003509 | NA | C2orf56 | chromosome 2 open reading frame 56 | 55471 | ENSG00000003509 |
| 19  | ENSG00000172340 | NA | SUCLG2 | succinate-CoA ligase, GDP-forming, beta subunit | 8801 | ENSG00000172340 |
| 20  | ENSG00000151093 | NA | OXSM | 3-oxoacyl-ACP synthase, mitochondrial | 54995 | ENSG00000151093 |
| 21  | ENSG00000130414 | NA | NDUFA10 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa | 4705 | ENSG00000130414 |
| 22  | ENSG00000091140 | NA | DLD | dihydrolipoamide dehydrogenase | 1738 | ENSG00000091140 |
| 23  | ENSG00000165060 | NA | FXN | frataxin | 2395 | ENSG00000165060 |
| 24  | ENSG00000079387 | NA | SENP1 | SUMO1/sentrin specific peptidase 1 | 29843 | ENSG00000079387 |
| 25  | ENSG00000131828 | NA | PDHA1 | pyruvate dehydrogenase (lipoamide) alpha 1 | 5160 | ENSG00000131828 |
| 26  | ENSG00000122971 | NA | ACADS | acyl-CoA dehydrogenase, C-2 to C-3 short chain | 35 | ENSG00000122971 |
| 27  | ENSG00000012061 | NA | ERCC1 | excision repair cross-complementing rodent repair deficiency, complementation group 1 (includes overlapping antisense sequence) | 2067 | ENSG00000012061 |
| 28  | ENSG00000103356 | NA | EARS2 | glutamyl-tRNA synthetase 2, mitochondrial (putative) | 124454 | ENSG00000103356 |
| 29  | ENSG00000109390 | NA | NDUFC1 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa | 4717 | ENSG00000109390 |
| 30  | ENSG00000182512 | NA | GLRX5 | glutaredoxin 5 | 51218 | ENSG00000182512 |
| 31  | ENSG00000103642 | NA | LACTB | lactamase, beta | 114294 | ENSG00000103642 |
| 32  | ENSG00000091483 | NA | FH | fumarate hydratase | 2271 | ENSG00000091483 |
| 33  | ENSG00000203797 | NA | DDO | D-aspartate oxidase | 8528 | ENSG00000203797 |
| 34  | ENSG00000103160 | NA | HSDL1 | hydroxysteroid dehydrogenase like 1 | 83693 | ENSG00000103160 |
| 35  | ENSG00000109586 | NA | GALNT7 | UDP-N-acetyl-alpha-D-galactosamine:polypeptide N-acetylgalactosaminyltransferase 7 (GalNAc-T7) | 51809 | ENSG00000109586 |
| 36  | ENSG00000110074 | NA | FOXRED1 | FAD-dependent oxidoreductase domain containing 1 | 55572 | ENSG00000110074 |
| 37  | ENSG00000142082 | NA | SIRT3 | sirtuin 3 | 23410 | ENSG00000142082 |
| 38  | ENSG00000127838 | NA | PNKD | paroxysmal nonkinesigenic dyskinesia | 25953 | ENSG00000127838 |
| 39  | ENSG00000168228 | NA | ZCCHC4 | zinc finger, CCHC domain containing 4 | 29063 | ENSG00000168228 |
| 40  | ENSG00000148334 | NA | PTGES2 | prostaglandin E synthase 2 | 80142 | ENSG00000148334 |
| 41  | ENSG00000119537 | NA | KDSR | 3-ketodihydrosphingosine reductase | 2531 | ENSG00000119537 |
| 42  | ENSG00000167112 | NA | TRUB2 | TruB pseudouridine (psi) synthase homolog 2 (E. coli) | 26995 | ENSG00000167112 |
| 43  | ENSG00000169189 | NA | NSMCE1 | non-SMC element 1 homolog (S. cerevisiae) | 197370 | ENSG00000169189 |
| 44  | ENSG00000119383 | NA | PPP2R4 | protein phosphatase 2A activator, regulatory subunit 4 | 5524 | ENSG00000119383 |
| 45  | ENSG00000149925 | NA | ALDOA | aldolase A, fructose-bisphosphate | 226 | ENSG00000149925 |
| 46  | ENSG00000126432 | NA | PRDX5 | peroxiredoxin 5 | 25824 | ENSG00000126432 |
| 47  | ENSG00000023330 | NA | ALAS1 | aminolevulinate, delta-, synthase 1 | 211 | ENSG00000023330 |
| 48  | ENSG00000213619 | NA | NDUFS3 | NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) | 4722 | ENSG00000213619 |
| 49  | ENSG00000178741 | NA | COX5A | cytochrome c oxidase subunit Va | 9377 | ENSG00000178741 |
| 50  | ENSG00000173660 | NA | UQCRH | ubiquinol-cytochrome c reductase hinge protein | 7388 | ENSG00000173660 |
| 51  | ENSG00000176490 | NA | DIRAS1 | DIRAS family, GTP-binding RAS-like 1 | 148252 | ENSG00000176490 |
| 52  | ENSG00000105135 | NA | ILVBL | ilvB (bacterial acetolactate synthase)-like | 10994 | ENSG00000105135 |
| 53  | ENSG00000100348 | NA | TXN2 | thioredoxin 2 | 25828 | ENSG00000100348 |
| 54  | ENSG00000140876 | NA | NUDT7 | nudix (nucleoside diphosphate linked moiety X)-type motif 7 | 283927 | ENSG00000140876 |
| 55  | ENSG00000101181 | NA | GTPBP5 | GTP binding protein 5 (putative) | 26164 | ENSG00000101181 |
| 56  | ENSG00000135940 | NA | COX5B | cytochrome c oxidase subunit Vb | 1329 | ENSG00000135940 |
| 57  | ENSG00000135900 | NA | MRPL44 | mitochondrial ribosomal protein L44 | 65080 | ENSG00000135900 |
| 58  | ENSG00000029639 | NA | TFB1M | transcription factor B1, mitochondrial | 51106 | ENSG00000029639 |
| 59  | ENSG00000113790 | NA | EHHADH | enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase | 1962 | ENSG00000113790 |
| 60  | ENSG00000162851 | NA | TFB2M | transcription factor B2, mitochondrial | 64216 | ENSG00000162851 |
| 61  | ENSG00000203705 | NA | TATDN3 | TatD DNase domain containing 3 | 128387 | ENSG00000203705 |
| 62  | ENSG00000156709 | NA | AIFM1 | apoptosis-inducing factor, mitochondrion-associated, 1 | 9131 | ENSG00000156709 |
| 63  | ENSG00000172115 | NA | CYCS | cytochrome c, somatic | 54205 | ENSG00000172115 |
| 64  | ENSG00000179085 | NA | DPM3 | dolichyl-phosphate mannosyltransferase polypeptide 3 | 54344 | ENSG00000179085 |
| 65  | ENSG00000189043 | NA | NDUFA4 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa | 4697 | ENSG00000189043 |
| 66  | ENSG00000123739 | NA | PLA2G12A | phospholipase A2, group XIIA | 81579 | ENSG00000123739 |
| 67  | ENSG00000164919 | NA | COX6C | cytochrome c oxidase subunit VIc | 1345 | ENSG00000164919 |
| 68  | ENSG00000185100 | NA | ADSSL1 | adenylosuccinate synthase like 1 | 122622 | ENSG00000185100 |
| 69  | ENSG00000196465 | NA | MYL6B | myosin, light chain 6B, alkali, smooth muscle and non-muscle | 140465 | ENSG00000196465 |
| 70  | ENSG00000115286 | NA | NDUFS7 | NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) | 374291 | ENSG00000115286 |
| 71  | ENSG00000139131 | NA | YARS2 | tyrosyl-tRNA synthetase 2, mitochondrial | 51067 | ENSG00000139131 |
| 72  | ENSG00000117543 | NA | DPH5 | DPH5 homolog (S. cerevisiae) | 51611 | ENSG00000117543 |
| 73  | ENSG00000164258 | NA | NDUFS4 | NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) | 4724 | ENSG00000164258 |
| 74  | ENSG00000132570 | NA | PCBD2 | pterin-4 alpha-carbinolamine dehydratase/dimerization cofactor of hepatocyte nuclear factor 1 alpha (TCF1) 2 | 84105 | ENSG00000132570 |
| 75  | ENSG00000156170 | NA | NDUFAF6 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 | 137682 | ENSG00000156170 |
| 76  | ENSG00000167863 | NA | ATP5H | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d | 10476 | ENSG00000167863 |
| 77  | ENSG00000166165 | NA | CKB | creatine kinase, brain | 1152 | ENSG00000166165 |
| 78  | ENSG00000127540 | NA | UQCR11 | ubiquinol-cytochrome c reductase, complex III subunit XI | 10975 | ENSG00000127540 |
| 79  | ENSG00000184752 | NA | NDUFA12 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 | 55967 | ENSG00000184752 |
| 80  | ENSG00000132423 | NA | COQ3 | coenzyme Q3 homolog, methyltransferase (S. cerevisiae) | 51805 | ENSG00000132423 |
| 81  | ENSG00000148335 | NA | NTMT1 | N-terminal Xaa-Pro-Lys N-methyltransferase 1 | 28989 | ENSG00000148335 |
| 82  | ENSG00000171861 | NA | RNMTL1 | RNA methyltransferase like 1 | 55178 | ENSG00000171861 |
| 83  | ENSG00000131844 | NA | MCCC2 | methylcrotonoyl-CoA carboxylase 2 (beta) | 64087 | ENSG00000131844 |
| 84  | ENSG00000134905 | NA | CARS2 | cysteinyl-tRNA synthetase 2, mitochondrial (putative) | 79587 | ENSG00000134905 |
| 85  | ENSG00000006282 | NA | SPATA20 | spermatogenesis associated 20 | 64847 | ENSG00000006282 |
| 86  | ENSG00000105819 | NA | PMPCB | peptidase (mitochondrial processing) beta | 9512 | ENSG00000105819 |
| 87  | ENSG00000182810 | NA | DDX28 | DEAD (Asp-Glu-Ala-Asp) box polypeptide 28 | 55794 | ENSG00000182810 |
| 88  | ENSG00000204228 | NA | HSD17B8 | hydroxysteroid (17-beta) dehydrogenase 8 | 7923 | ENSG00000204228 |
| 89  | ENSG00000149743 | NA | TRPT1 | tRNA phosphotransferase 1 | 83707 | ENSG00000149743 |
| 90  | ENSG00000175198 | NA | PCCA | propionyl CoA carboxylase, alpha polypeptide | 5095 | ENSG00000175198 |
| 91  | ENSG00000067829 | NA | IDH3G | isocitrate dehydrogenase 3 (NAD+) gamma | 3421 | ENSG00000067829 |
| 92  | ENSG00000129187 | NA | DCTD | dCMP deaminase | 1635 | ENSG00000129187 |
| 93  | ENSG00000067225 | NA | PKM | pyruvate kinase, muscle | 5315 | ENSG00000067225 |
| 94  | ENSG00000140990 | NA | NDUFB10 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa | 4716 | ENSG00000140990 |
| 95  | ENSG00000157326 | NA | DHRS4 | dehydrogenase/reductase (SDR family) member 4 | 10901 | ENSG00000157326 |
| 96  | ENSG00000144182 | NA | LIPT1 | lipoyltransferase 1 | 51601 | ENSG00000144182 |
| 97  | ENSG00000102996 | NA | MMP15 | matrix metallopeptidase 15 (membrane-inserted) | 4324 | ENSG00000102996 |
| 98  | ENSG00000247626 | NA | MARS2 | methionyl-tRNA synthetase 2, mitochondrial | 92935 | ENSG00000247626 |
| 99  | ENSG00000006530 | NA | AGK | acylglycerol kinase | 55750 | ENSG00000006530 |
| 100  | ENSG00000184207 | NA | PGP | phosphoglycolate phosphatase | 283871 | ENSG00000184207 |
| 101  | ENSG00000005075 | NA | POLR2J | polymerase (RNA) II (DNA directed) polypeptide J, 13.3kDa | 5439 | ENSG00000005075 |
| 102  | ENSG00000167363 | NA | FN3K | fructosamine 3 kinase | 64122 | ENSG00000167363 |
| 103  | ENSG00000165629 | NA | ATP5C1 | ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 | 509 | ENSG00000165629 |
| 104  | ENSG00000143653 | NA | SCCPDH | saccharopine dehydrogenase (putative) | 51097 | ENSG00000143653 |
| 105  | ENSG00000116906 | NA | GNPAT | glyceronephosphate O-acyltransferase | 8443 | ENSG00000116906 |
| 106  | ENSG00000148290 | NA | SURF1 | surfeit 1 | 6834 | ENSG00000148290 |
| 107  | ENSG00000198522 | NA | GPN1 | GPN-loop GTPase 1 | 11321 | ENSG00000198522 |
| 108  | ENSG00000117266 | NA | CDK18 | cyclin-dependent kinase 18 | 5129 | ENSG00000117266 |
| 109  | ENSG00000170634 | NA | ACYP2 | acylphosphatase 2, muscle type | 98 | ENSG00000170634 |
| 110  | ENSG00000014641 | NA | MDH1 | malate dehydrogenase 1, NAD (soluble) | 4190 | ENSG00000014641 |
| 111  | ENSG00000105220 | NA | GPI | glucose-6-phosphate isomerase | 2821 | ENSG00000105220 |
| 112  | ENSG00000133315 | NA | MACROD1 | MACRO domain containing 1 | 28992 | ENSG00000133315 |
| 113  | ENSG00000072778 | NA | ACADVL | acyl-CoA dehydrogenase, very long chain | 37 | ENSG00000072778 |
| 114  | ENSG00000172893 | NA | DHCR7 | 7-dehydrocholesterol reductase | 1717 | ENSG00000172893 |
| 115  | ENSG00000154930 | NA | ACSS1 | acyl-CoA synthetase short-chain family member 1 | 84532 | ENSG00000154930 |
| 116  | ENSG00000108774 | NA | RAB5C | RAB5C, member RAS oncogene family | 5878 | ENSG00000108774 |
| 117  | ENSG00000125652 | NA | ALKBH7 | alkB, alkylation repair homolog 7 (E. coli) | 84266 | ENSG00000125652 |
| 118  | ENSG00000054148 | NA | PHPT1 | phosphohistidine phosphatase 1 | 29085 | ENSG00000054148 |
| 119  | ENSG00000084731 | NA | KIF3C | kinesin family member 3C | 3797 | ENSG00000084731 |
| 120  | ENSG00000139410 | NA | SDSL | serine dehydratase-like | 113675 | ENSG00000139410 |
| 121  | ENSG00000059691 | NA | PET112 | PET112 homolog (yeast) | 5188 | ENSG00000059691 |
| 122  | ENSG00000112981 | NA | NME5 | NME/NM23 family member 5 | 8382 | ENSG00000112981 |
| 123  | ENSG00000126088 | NA | UROD | uroporphyrinogen decarboxylase | 7389 | ENSG00000126088 |
| 124  | ENSG00000168060 | NA | NAALADL1 | N-acetylated alpha-linked acidic dipeptidase-like 1 | 10004 | ENSG00000168060 |
| 125  | ENSG00000138430 | NA | OLA1 | Obg-like ATPase 1 | 29789 | ENSG00000138430 |
| 126  | ENSG00000136521 | NA | NDUFB5 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa | 4711 | ENSG00000136521 |
| 127  | ENSG00000004779 | NA | NDUFAB1 | NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa | 4706 | ENSG00000004779 |
| 128  | ENSG00000169020 | NA | ATP5I | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E | 521 | ENSG00000169020 |
| 129  | ENSG00000182054 | NA | IDH2 | isocitrate dehydrogenase 2 (NADP+), mitochondrial | 3418 | ENSG00000182054 |
| 130  | ENSG00000114021 | NA | NIT2 | nitrilase family, member 2 | 56954 | ENSG00000114021 |
| 131  | ENSG00000167272 | NA | POP5 | processing of precursor 5, ribonuclease P/MRP subunit (S. cerevisiae) | 51367 | ENSG00000167272 |
| 132  | ENSG00000085871 | NA | MGST2 | microsomal glutathione S-transferase 2 | 4258 | ENSG00000085871 |
| 133  | ENSG00000004961 | NA | HCCS | holocytochrome c synthase | 3052 | ENSG00000004961 |
| 134  | ENSG00000172954 | NA | LCLAT1 | lysocardiolipin acyltransferase 1 | 253558 | ENSG00000172954 |
| 135  | ENSG00000073578 | NA | SDHA | succinate dehydrogenase complex, subunit A, flavoprotein (Fp) | 6389 | ENSG00000073578 |
| 136  | ENSG00000119013 | NA | NDUFB3 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa | 4709 | ENSG00000119013 |
| 137  | ENSG00000213965 | NA | NUDT19 | nudix (nucleoside diphosphate linked moiety X)-type motif 19 | 390916 | ENSG00000213965 |
| 138  | ENSG00000104325 | NA | DECR1 | 2,4-dienoyl CoA reductase 1, mitochondrial | 1666 | ENSG00000104325 |
| 139  | ENSG00000259494 | NA | MRPL46 | mitochondrial ribosomal protein L46 | 26589 | ENSG00000259494 |
| 140  | ENSG00000077348 | NA | EXOSC5 | exosome component 5 | 56915 | ENSG00000077348 |
| 141  | ENSG00000144827 | NA | ABHD10 | abhydrolase domain containing 10 | 55347 | ENSG00000144827 |
| 142  | ENSG00000006757 | NA | PNPLA4 | patatin-like phospholipase domain containing 4 | 8228 | ENSG00000006757 |
| 143  | ENSG00000072401 | NA | UBE2D1 | ubiquitin-conjugating enzyme E2D 1 | 7321 | ENSG00000072401 |
| 144  | ENSG00000173786 | NA | CNP | 2',3'-cyclic nucleotide 3' phosphodiesterase | 1267 | ENSG00000173786 |
| 145  | ENSG00000171130 | NA | ATP6V0E2 | ATPase, H+ transporting V0 subunit e2 | 155066 | ENSG00000171130 |
| 146  | ENSG00000159593 | NA | NAE1 | NEDD8 activating enzyme E1 subunit 1 | 8883 | ENSG00000159593 |
| 147  | ENSG00000167468 | NA | GPX4 | glutathione peroxidase 4 | 2879 | ENSG00000167468 |
| 148  | ENSG00000139180 | NA | NDUFA9 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa | 4704 | ENSG00000139180 |
| 149  | ENSG00000127184 | NA | COX7C | cytochrome c oxidase subunit VIIc | 1350 | ENSG00000127184 |
| 150  | ENSG00000111640 | NA | GAPDH | glyceraldehyde-3-phosphate dehydrogenase | 2597 | ENSG00000111640 |
| 151  | ENSG00000177700 | NA | POLR2L | polymerase (RNA) II (DNA directed) polypeptide L, 7.6kDa | 5441 | ENSG00000177700 |
| 152  | ENSG00000123836 | NA | PFKFB2 | 6-phosphofructo-2-kinase/fructose-2,6-biphosphatase 2 | 5208 | ENSG00000123836 |
| 153  | ENSG00000085760 | NA | MTIF2 | mitochondrial translational initiation factor 2 | 4528 | ENSG00000085760 |
| 154  | ENSG00000120265 | NA | PCMT1 | protein-L-isoaspartate (D-aspartate) O-methyltransferase | 5110 | ENSG00000120265 |
| 155  | ENSG00000109911 | NA | ELP4 | elongator acetyltransferase complex subunit 4 | 26610 | ENSG00000109911 |
| 156  | ENSG00000156239 | NA | N6AMT1 | N-6 adenine-specific DNA methyltransferase 1 (putative) | 29104 | ENSG00000156239 |
| 157  | ENSG00000156958 | NA | GALK2 | galactokinase 2 | 2585 | ENSG00000156958 |
| 158  | ENSG00000136159 | NA | NUDT15 | nudix (nucleoside diphosphate linked moiety X)-type motif 15 | 55270 | ENSG00000136159 |
| 159  | ENSG00000100442 | NA | FKBP3 | FK506 binding protein 3, 25kDa | 2287 | ENSG00000100442 |
| 160  | ENSG00000172878 | NA | METAP1D | methionyl aminopeptidase type 1D (mitochondrial) | 254042 | ENSG00000172878 |
| 161  | ENSG00000204370 | NA | SDHD | succinate dehydrogenase complex, subunit D, integral membrane protein | 6392 | ENSG00000204370 |
| 162  | ENSG00000196704 | NA | AMZ2 | archaelysin family metallopeptidase 2 | 51321 | ENSG00000196704 |
| 163  | ENSG00000108384 | NA | RAD51C | RAD51 homolog C (S. cerevisiae) | 5889 | ENSG00000108384 |
| 164  | ENSG00000137106 | NA | GRHPR | glyoxylate reductase/hydroxypyruvate reductase | 9380 | ENSG00000137106 |
| 165  | ENSG00000111271 | NA | ACAD10 | acyl-CoA dehydrogenase family, member 10 | 80724 | ENSG00000111271 |
| 166  | ENSG00000169738 | NA | DCXR | dicarbonyl/L-xylulose reductase | 51181 | ENSG00000169738 |
| 167  | ENSG00000027001 | NA | MIPEP | mitochondrial intermediate peptidase | 4285 | ENSG00000027001 |
| 168  | ENSG00000160211 | NA | G6PD | glucose-6-phosphate dehydrogenase | 2539 | ENSG00000160211 |
| 169  | ENSG00000138777 | NA | PPA2 | pyrophosphatase (inorganic) 2 | 27068 | ENSG00000138777 |
| 170  | ENSG00000143727 | NA | ACP1 | acid phosphatase 1, soluble | 52 | ENSG00000143727 |
| 171  | ENSG00000100601 | NA | ALKBH1 | alkB, alkylation repair homolog 1 (E. coli) | 8846 | ENSG00000100601 |
| 172  | ENSG00000117280 | NA | RAB7L1 | RAB7, member RAS oncogene family-like 1 | 8934 | ENSG00000117280 |
| 173  | ENSG00000115042 | NA | FAHD2A | fumarylacetoacetate hydrolase domain containing 2A | 51011 | ENSG00000115042 |
| 174  | ENSG00000066583 | NA | ISOC1 | isochorismatase domain containing 1 | 51015 | ENSG00000066583 |
| 175  | ENSG00000111669 | NA | TPI1 | triosephosphate isomerase 1 | 7167 | ENSG00000111669 |
| 176  | ENSG00000023228 | NA | NDUFS1 | NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) | 4719 | ENSG00000023228 |
| 177  | ENSG00000184788 | NA | SATL1 | spermidine/spermine N1-acetyl transferase-like 1 | 340562 | ENSG00000184788 |
| 178  | ENSG00000139160 | NA | METTL20 | methyltransferase like 20 | 254013 | ENSG00000139160 |
| 179  | ENSG00000143252 | NA | SDHC | succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa | 6391 | ENSG00000143252 |
| 180  | ENSG00000100116 | NA | GCAT | glycine C-acetyltransferase | 23464 | ENSG00000100116 |
| 181  | ENSG00000186318 | NA | BACE1 | beta-site APP-cleaving enzyme 1 | 23621 | ENSG00000265969 ENSG00000186318 |
| 182  | ENSG00000151376 | NA | ME3 | malic enzyme 3, NADP(+)-dependent, mitochondrial | 10873 | ENSG00000151376 |
| 183  | ENSG00000145982 | NA | FARS2 | phenylalanyl-tRNA synthetase 2, mitochondrial | 10667 | ENSG00000145982 |
| 184  | ENSG00000121897 | NA | LIAS | lipoic acid synthetase | 11019 | ENSG00000121897 |
| 185  | ENSG00000110955 | NA | ATP5B | ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide | 506 | ENSG00000110955 |
| 186  | ENSG00000151883 | NA | PARP8 | poly (ADP-ribose) polymerase family, member 8 | 79668 | ENSG00000151883 |
| 187  | ENSG00000197122 | NA | SRC | v-src sarcoma (Schmidt-Ruppin A-2) viral oncogene homolog (avian) | 6714 | ENSG00000197122 |
| 188  | ENSG00000112695 | NA | COX7A2 | cytochrome c oxidase subunit VIIa polypeptide 2 (liver) | 1347 | ENSG00000112695 |
| 189  | ENSG00000147155 | NA | EBP | emopamil binding protein (sterol isomerase) | 10682 | ENSG00000147155 |
| 190  | ENSG00000198373 | NA | WWP2 | WW domain containing E3 ubiquitin protein ligase 2 | 11060 | ENSG00000198373 |
| 191  | ENSG00000198736 | NA | MSRB1 | methionine sulfoxide reductase B1 | 51734 | ENSG00000198736 |
| 192  | ENSG00000179958 | NA | DCTPP1 | dCTP pyrophosphatase 1 | 79077 | ENSG00000179958 |
| 193  | ENSG00000131495 | NA | NDUFA2 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa | 4695 | ENSG00000131495 |
| 194  | ENSG00000083720 | NA | OXCT1 | 3-oxoacid CoA transferase 1 | 5019 | ENSG00000083720 |
| 195  | ENSG00000065518 | NA | NDUFB4 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa | 4710 | ENSG00000065518 |
| 196  | ENSG00000095321 | NA | CRAT | carnitine O-acetyltransferase | 1384 | ENSG00000095321 |
| 197  | ENSG00000185808 | NA | PIGP | phosphatidylinositol glycan anchor biosynthesis, class P | 51227 | ENSG00000185808 |
| 198  | ENSG00000159445 | NA | THEM4 | thioesterase superfamily member 4 | 117145 | ENSG00000159445 |
| 199  | ENSG00000165688 | NA | PMPCA | peptidase (mitochondrial processing) alpha | 23203 | ENSG00000165688 |
| 200  | ENSG00000120992 | NA | LYPLA1 | lysophospholipase I | 10434 | ENSG00000120992 |
| 201  | ENSG00000198721 | NA | ECI2 | enoyl-CoA delta isomerase 2 | 10455 | ENSG00000198721 |
| 202  | ENSG00000112855 | NA | HARS2 | histidyl-tRNA synthetase 2, mitochondrial | 23438 | ENSG00000112855 |
| 203  | ENSG00000197580 | NA | BCO2 | beta-carotene oxygenase 2 | 83875 | ENSG00000197580 |
| 204  | ENSG00000147853 | NA | AK3 | adenylate kinase 3 | 50808 | ENSG00000147853 |
| 205  | ENSG00000131174 | NA | COX7B | cytochrome c oxidase subunit VIIb | 1349 | ENSG00000131174 |
| 206  | ENSG00000147364 | NA | FBXO25 | F-box protein 25 | 26260 | ENSG00000147364 |
| 207  | ENSG00000170906 | NA | NDUFA3 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa | 4696 | ENSG00000170906 |
| 208  | ENSG00000205309 | NA | NT5M | 5',3'-nucleotidase, mitochondrial | 56953 | ENSG00000205309 |
| 209  | ENSG00000136247 | NA | ZDHHC4 | zinc finger, DHHC-type containing 4 | 55146 | ENSG00000136247 |
| 210  | ENSG00000112304 | NA | ACOT13 | acyl-CoA thioesterase 13 | 55856 | ENSG00000112304 |
| 211  | ENSG00000160808 | NA | MYL3 | myosin, light chain 3, alkali; ventricular, skeletal, slow | 4634 | ENSG00000160808 |
| 212  | ENSG00000142507 | NA | PSMB6 | proteasome (prosome, macropain) subunit, beta type, 6 | 5694 | ENSG00000142507 |
| 213  | ENSG00000111716 | NA | LDHB | lactate dehydrogenase B | 3945 | ENSG00000111716 |
| 214  | ENSG00000108439 | NA | PNPO | pyridoxamine 5'-phosphate oxidase | 55163 | ENSG00000108439 |
| 215  | ENSG00000114054 | NA | PCCB | propionyl CoA carboxylase, beta polypeptide | 5096 | ENSG00000114054 |
| 216  | ENSG00000167283 | NA | ATP5L | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G | 10632 | ENSG00000167283 |
| 217  | ENSG00000111275 | NA | ALDH2 | aldehyde dehydrogenase 2 family (mitochondrial) | 217 | ENSG00000111275 |
| 218  | ENSG00000167799 | NA | NUDT8 | nudix (nucleoside diphosphate linked moiety X)-type motif 8 | 254552 | ENSG00000167799 |
| 219  | ENSG00000169071 | NA | ROR2 | receptor tyrosine kinase-like orphan receptor 2 | 4920 | ENSG00000169071 |
| 220  | ENSG00000134452 | NA | FBXO18 | F-box protein, helicase, 18 | 84893 | ENSG00000134452 |
| 221  | ENSG00000136270 | NA | TBRG4 | transforming growth factor beta regulator 4 | 9238 | ENSG00000136270 |
| 222  | ENSG00000131269 | NA | ABCB7 | ATP-binding cassette, sub-family B (MDR/TAP), member 7 | 22 | ENSG00000131269 |
| 223  | ENSG00000010256 | NA | UQCRC1 | ubiquinol-cytochrome c reductase core protein I | 7384 | ENSG00000010256 |
| 224  | ENSG00000104823 | NA | ECH1 | enoyl CoA hydratase 1, peroxisomal | 1891 | ENSG00000104823 |
| 225  | ENSG00000101391 | NA | CDK5RAP1 | CDK5 regulatory subunit associated protein 1 | 51654 | ENSG00000101391 |
| 226  | ENSG00000197912 | NA | SPG7 | spastic paraplegia 7 (pure and complicated autosomal recessive) | 6687 | ENSG00000197912 |
| 227  | ENSG00000171503 | NA | ETFDH | electron-transferring-flavoprotein dehydrogenase | 2110 | ENSG00000171503 |
| 228  | ENSG00000167065 | NA | DUSP18 | dual specificity phosphatase 18 | 150290 | ENSG00000167065 |
| 229  | ENSG00000138796 | NA | HADH | hydroxyacyl-CoA dehydrogenase | 3033 | ENSG00000138796 |
| 230  | ENSG00000099804 | NA | CDC34 | cell division cycle 34 homolog (S. cerevisiae) | 997 | ENSG00000099804 |
| 231  | ENSG00000141965 | NA | FEM1A | fem-1 homolog a (C. elegans) | 55527 | ENSG00000141965 |
| 232  | ENSG00000165672 | NA | PRDX3 | peroxiredoxin 3 | 10935 | ENSG00000165672 |
| 233  | ENSG00000227345 | NA | PARG | poly (ADP-ribose) glycohydrolase | 8505 | ENSG00000227345 |
| 234  | ENSG00000163521 | NA | GLB1L | galactosidase, beta 1-like | 79411 | ENSG00000163521 |
| 235  | ENSG00000161533 | NA | ACOX1 | acyl-CoA oxidase 1, palmitoyl | 51 | ENSG00000161533 |
| 236  | ENSG00000107317 | NA | PTGDS | prostaglandin D2 synthase 21kDa (brain) | 5730 | ENSG00000107317 |
| 237  | ENSG00000163382 | NA | APOA1BP | apolipoprotein A-I binding protein | 128240 | ENSG00000163382 |
| 238  | ENSG00000154237 | NA | LRRK1 | leucine-rich repeat kinase 1 | 79705 | ENSG00000154237 |
| 239  | ENSG00000168653 | NA | NDUFS5 | NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) | 4725 | ENSG00000168653 |
| 240  | ENSG00000247077 | NA | PGAM5 | phosphoglycerate mutase family member 5 | 192111 | ENSG00000247077 |
| 241  | ENSG00000156110 | NA | ADK | adenosine kinase | 132 | ENSG00000156110 |
| 242  | ENSG00000149761 | NA | NUDT22 | nudix (nucleoside diphosphate linked moiety X)-type motif 22 | 84304 | ENSG00000149761 |
| 243  | ENSG00000087299 | NA | L2HGDH | L-2-hydroxyglutarate dehydrogenase | 79944 | ENSG00000087299 |
| 244  | ENSG00000184903 | NA | IMMP2L | IMP2 inner mitochondrial membrane peptidase-like (S. cerevisiae) | 83943 | ENSG00000184903 |
| 245  | ENSG00000163864 | NA | NMNAT3 | nicotinamide nucleotide adenylyltransferase 3 | 349565 | ENSG00000163864 |
| 246  | ENSG00000103316 | NA | CRYM | crystallin, mu | 1428 | ENSG00000103316 |
| 247  | ENSG00000161204 | NA | ABCF3 | ATP-binding cassette, sub-family F (GCN20), member 3 | 55324 | ENSG00000161204 |
| 248  | ENSG00000197586 | NA | ENTPD6 | ectonucleoside triphosphate diphosphohydrolase 6 (putative) | 955 | ENSG00000197586 |
| 249  | ENSG00000156467 | NA | UQCRB | ubiquinol-cytochrome c reductase binding protein | 7381 | ENSG00000156467 |
| 250  | ENSG00000100142 | NA | POLR2F | polymerase (RNA) II (DNA directed) polypeptide F | 5435 | ENSG00000100142 |
| 251  | ENSG00000184076 | NA | UQCR10 | ubiquinol-cytochrome c reductase, complex III subunit X | 29796 | ENSG00000184076 |
| 252  | ENSG00000078070 | NA | MCCC1 | methylcrotonoyl-CoA carboxylase 1 (alpha) | 56922 | ENSG00000078070 |
| 253  | ENSG00000184489 | NA | PTP4A3 | protein tyrosine phosphatase type IVA, member 3 | 11156 | ENSG00000184489 |
| 254  | ENSG00000068903 | NA | SIRT2 | sirtuin 2 | 22933 | ENSG00000068903 |
| 255  | ENSG00000166133 | NA | RPUSD2 | RNA pseudouridylate synthase domain containing 2 | 27079 | ENSG00000166133 |
| 256  | ENSG00000156885 | NA | COX6A2 | cytochrome c oxidase subunit VIa polypeptide 2 | 1339 | ENSG00000156885 |
| 257  | ENSG00000154723 | NA | ATP5J | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 | 522 | ENSG00000154723 |
| 258  | ENSG00000169084 | NA | DHRSX | dehydrogenase/reductase (SDR family) X-linked | 207063 | ENSG00000169084 |
| 259  | ENSG00000006695 | NA | COX10 | COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) | 1352 | ENSG00000006695 |
| 260  | ENSG00000167969 | NA | ECI1 | enoyl-CoA delta isomerase 1 | 1632 | ENSG00000167969 |
| 261  | ENSG00000105552 | NA | BCAT2 | branched chain amino-acid transaminase 2, mitochondrial | 587 | ENSG00000105552 |
| 262  | ENSG00000153531 | NA | ADPRHL1 | ADP-ribosylhydrolase like 1 | 113622 | ENSG00000153531 |
| 263  | ENSG00000139531 | NA | SUOX | sulfite oxidase | 6821 | ENSG00000139531 |
| 264  | ENSG00000106066 | NA | CPVL | carboxypeptidase, vitellogenic-like | 54504 | ENSG00000106066 |
| 265  | ENSG00000125166 | NA | GOT2 | glutamic-oxaloacetic transaminase 2, mitochondrial (aspartate aminotransferase 2) | 2806 | ENSG00000125166 |
| 266  | ENSG00000141552 | NA | ANAPC11 | anaphase promoting complex subunit 11 | 51529 | ENSG00000141552 |
| 267  | ENSG00000172336 | NA | POP7 | processing of precursor 7, ribonuclease P/MRP subunit (S. cerevisiae) | 10248 | ENSG00000172336 |
| 268  | ENSG00000140740 | NA | UQCRC2 | ubiquinol-cytochrome c reductase core protein II | 7385 | ENSG00000140740 |
| 269  | ENSG00000140374 | NA | ETFA | electron-transfer-flavoprotein, alpha polypeptide | 2108 | ENSG00000140374 |
| 270  | ENSG00000114378 | NA | HYAL1 | hyaluronoglucosaminidase 1 | 3373 | ENSG00000114378 |
| 271  | ENSG00000147684 | NA | NDUFB9 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa | 4715 | ENSG00000147684 |
| 272  | ENSG00000160194 | NA | NDUFV3 | NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa | 4731 | ENSG00000160194 |
| 273  | ENSG00000184983 | NA | NDUFA6 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa | 4700 | ENSG00000184983 |
| 274  | ENSG00000102309 | NA | PIN4 | protein (peptidylprolyl cis/trans isomerase) NIMA-interacting, 4 (parvulin) | 5303 | ENSG00000102309 |
| 275  | ENSG00000158864 | NA | NDUFS2 | NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) | 4720 | ENSG00000158864 |
| 276  | ENSG00000105197 | NA | TIMM50 | translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae) | 92609 | ENSG00000105197 |
| 277  | ENSG00000142168 | NA | SOD1 | superoxide dismutase 1, soluble | 6647 | ENSG00000142168 |
| 278  | ENSG00000168101 | NA | NUDT16L1 | nudix (nucleoside diphosphate linked moiety X)-type motif 16-like 1 | 84309 | ENSG00000168101 |
| 279  | ENSG00000000419 | NA | DPM1 | dolichyl-phosphate mannosyltransferase polypeptide 1, catalytic subunit | 8813 | ENSG00000000419 |
| 280  | ENSG00000181929 | NA | PRKAG1 | protein kinase, AMP-activated, gamma 1 non-catalytic subunit | 5571 | ENSG00000181929 |
| 281  | ENSG00000076043 | NA | REXO2 | REX2, RNA exonuclease 2 homolog (S. cerevisiae) | 25996 | ENSG00000076043 |
| 282  | ENSG00000120254 | NA | MTHFD1L | methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 1-like | 25902 | ENSG00000120254 |
| 283  | ENSG00000069998 | NA | CECR5 | cat eye syndrome chromosome region, candidate 5 | 27440 | ENSG00000069998 |
| 284  | ENSG00000147813 | NA | NAPRT1 | nicotinate phosphoribosyltransferase domain containing 1 | 93100 | ENSG00000147813 |
| 285  | ENSG00000119689 | NA | DLST | dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex) | 1743 | ENSG00000119689 |
| 286  | ENSG00000184924 | NA | PTRHD1 | peptidyl-tRNA hydrolase domain containing 1 | 391356 | ENSG00000184924 |
| 287  | ENSG00000168291 | NA | PDHB | pyruvate dehydrogenase (lipoamide) beta | 5162 | ENSG00000168291 |
| 288  | ENSG00000156502 | NA | SUPV3L1 | suppressor of var1, 3-like 1 (S. cerevisiae) | 6832 | ENSG00000156502 |
| 289  | ENSG00000156049 | NA | GNA14 | guanine nucleotide binding protein (G protein), alpha 14 | 9630 | ENSG00000156049 |
| 290  | ENSG00000162849 | NA | KIF26B | kinesin family member 26B | 55083 | ENSG00000162849 |
| 291  | ENSG00000116459 | NA | ATP5F1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 | 515 | ENSG00000116459 |
| 292  | ENSG00000105499 | NA | PLA2G4C | phospholipase A2, group IVC (cytosolic, calcium-independent) | 8605 | ENSG00000105499 |
| 293  | ENSG00000138399 | NA | FASTKD1 | FAST kinase domains 1 | 79675 | ENSG00000138399 |
| 294  | ENSG00000112992 | NA | NNT | nicotinamide nucleotide transhydrogenase | 23530 | ENSG00000112992 |
| 295  | ENSG00000107951 | NA | MTPAP | mitochondrial poly(A) polymerase | 55149 | ENSG00000107951 |
| 296  | ENSG00000067704 | NA | IARS2 | isoleucyl-tRNA synthetase 2, mitochondrial | 55699 | ENSG00000067704 |
| 297  | ENSG00000215251 | NA | FASTKD5 | FAST kinase domains 5 | 60493 | ENSG00000215251 |
| 298  | ENSG00000183785 | NA | TUBA8 | tubulin, alpha 8 | 51807 | ENSG00000183785 |
| 299  | ENSG00000182185 | NA | RAD51B | RAD51 homolog B (S. cerevisiae) | 5890 | ENSG00000182185 |
| 300  | ENSG00000130348 | NA | QRSL1 | glutaminyl-tRNA synthase (glutamine-hydrolyzing)-like 1 | 55278 | ENSG00000130348 |
| 301  | ENSG00000183765 | NA | CHEK2 | checkpoint kinase 2 | 11200 | ENSG00000183765 |
| 302  | ENSG00000148950 | NA | IMMP1L | IMP1 inner mitochondrial membrane peptidase-like (S. cerevisiae) | 196294 | ENSG00000148950 |
| 303  | ENSG00000119421 | NA | NDUFA8 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa | 4702 | ENSG00000119421 |
| 304  | ENSG00000170502 | NA | NUDT9 | nudix (nucleoside diphosphate linked moiety X)-type motif 9 | 53343 | ENSG00000170502 |
| 305  | ENSG00000130347 | NA | RTN4IP1 | reticulon 4 interacting protein 1 | 84816 | ENSG00000130347 |
| 306  | ENSG00000244005 | NA | NFS1 | NFS1 nitrogen fixation 1 homolog (S. cerevisiae) | 9054 | ENSG00000244005 |
| 307  | ENSG00000126267 | NA | COX6B1 | cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) | 1340 | ENSG00000126267 |
| 308  | ENSG00000104879 | NA | CKM | creatine kinase, muscle | 1158 | ENSG00000104879 |
| 309  | ENSG00000166192 | NA | SENP8 | SUMO/sentrin specific peptidase family member 8 | 123228 | ENSG00000166192 |
| 310  | ENSG00000154814 | NA | OXNAD1 | oxidoreductase NAD-binding domain containing 1 | 92106 | ENSG00000154814 |
| 311  | ENSG00000076003 | NA | MCM6 | minichromosome maintenance complex component 6 | 4175 | ENSG00000076003 |
| 312  | ENSG00000100804 | NA | PSMB5 | proteasome (prosome, macropain) subunit, beta type, 5 | 5693 | ENSG00000100804 |
| 313  | ENSG00000134330 | NA | IAH1 | isoamyl acetate-hydrolyzing esterase 1 homolog (S. cerevisiae) | 285148 | ENSG00000134330 |
| 314  | ENSG00000148450 | NA | MSRB2 | methionine sulfoxide reductase B2 | 22921 | ENSG00000148450 |
| 315  | ENSG00000145494 | NA | NDUFS6 | NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) | 4726 | ENSG00000145494 |
| 316  | ENSG00000163687 | NA | DNASE1L3 | deoxyribonuclease I-like 3 | 1776 | ENSG00000163687 |
| 317  | ENSG00000072506 | NA | HSD17B10 | hydroxysteroid (17-beta) dehydrogenase 10 | 3028 | ENSG00000072506 |
| 318  | ENSG00000131143 | NA | COX4I1 | cytochrome c oxidase subunit IV isoform 1 | 1327 | ENSG00000131143 |
| 319  | ENSG00000196236 | NA | XPNPEP3 | X-prolyl aminopeptidase (aminopeptidase P) 3, putative | 63929 | ENSG00000196236 |
| 320  | ENSG00000136444 | NA | RSAD1 | radical S-adenosyl methionine domain containing 1 | 55316 | ENSG00000136444 |
| 321  | ENSG00000197885 | NA | NKIRAS1 | NFKB inhibitor interacting Ras-like 1 | 28512 | ENSG00000197885 |
| 322  | ENSG00000090266 | NA | NDUFB2 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa | 4708 | ENSG00000090266 |
| 323  | ENSG00000108515 | NA | ENO3 | enolase 3 (beta, muscle) | 2027 | ENSG00000108515 |
| 324  | ENSG00000213995 | NA | CARKD | carbohydrate kinase domain containing | 55739 | ENSG00000213995 |
| 325  | ENSG00000105649 | NA | RAB3A | RAB3A, member RAS oncogene family | 5864 | ENSG00000105649 |
| 326  | ENSG00000184860 | NA | SDR42E1 | short chain dehydrogenase/reductase family 42E, member 1 | 93517 | ENSG00000184860 |
| 327  | ENSG00000151498 | NA | ACAD8 | acyl-CoA dehydrogenase family, member 8 | 27034 | ENSG00000151498 |
| 328  | ENSG00000047249 | NA | ATP6V1H | ATPase, H+ transporting, lysosomal 50/57kDa, V1 subunit H | 51606 | ENSG00000047249 |
| 329  | ENSG00000136143 | NA | SUCLA2 | succinate-CoA ligase, ADP-forming, beta subunit | 8803 | ENSG00000136143 |
| 330  | ENSG00000003137 | NA | CYP26B1 | cytochrome P450, family 26, subfamily B, polypeptide 1 | 56603 | ENSG00000003137 |
| 331  | ENSG00000135778 | NA | NTPCR | nucleoside-triphosphatase, cancer-related | 84284 | ENSG00000135778 |
| 332  | ENSG00000105258 | NA | POLR2I | polymerase (RNA) II (DNA directed) polypeptide I, 14.5kDa | 5438 | ENSG00000105258 |
| 333  | ENSG00000166855 | NA | CLPX | ClpX caseinolytic peptidase X homolog (E. coli) | 10845 | ENSG00000166855 |
| 334  | ENSG00000110931 | NA | CAMKK2 | calcium/calmodulin-dependent protein kinase kinase 2, beta | 10645 | ENSG00000110931 |
| 335  | ENSG00000173614 | NA | NMNAT1 | nicotinamide nucleotide adenylyltransferase 1 | 64802 | ENSG00000173614 |
| 336  | ENSG00000172331 | NA | BPGM | 2,3-bisphosphoglycerate mutase | 669 | ENSG00000172331 |
| 337  | ENSG00000166321 | NA | NUDT13 | nudix (nucleoside diphosphate linked moiety X)-type motif 13 | 25961 | ENSG00000166321 |
| 338  | ENSG00000130159 | NA | ECSIT | ECSIT homolog (Drosophila) | 51295 | ENSG00000130159 |
| 339  | ENSG00000171763 | NA | SPATA5L1 | spermatogenesis associated 5-like 1 | 79029 | ENSG00000171763 |
| 340  | ENSG00000074582 | NA | BCS1L | BCS1-like (S. cerevisiae) | 617 | ENSG00000074582 |
| 341  | ENSG00000129084 | NA | PSMA1 | proteasome (prosome, macropain) subunit, alpha type, 1 | 5682 | ENSG00000256206 ENSG00000129084 |
| 342  | ENSG00000082146 | NA | STRADB | STE20-related kinase adaptor beta | 55437 | ENSG00000082146 |
| 343  | ENSG00000116171 | NA | SCP2 | sterol carrier protein 2 | 6342 | ENSG00000116171 |
| 344  | ENSG00000103274 | NA | NUBP1 | nucleotide binding protein 1 | 4682 | ENSG00000103274 |
| 345  | ENSG00000167815 | NA | PRDX2 | peroxiredoxin 2 | 7001 | ENSG00000167815 |
| 346  | ENSG00000166816 | NA | LDHD | lactate dehydrogenase D | 197257 | ENSG00000166816 |
| 347  | ENSG00000143374 | NA | TARS2 | threonyl-tRNA synthetase 2, mitochondrial (putative) | 80222 | ENSG00000143374 |
| 348  | ENSG00000013275 | NA | PSMC4 | proteasome (prosome, macropain) 26S subunit, ATPase, 4 | 5704 | ENSG00000013275 |
| 349  | ENSG00000066926 | NA | FECH | ferrochelatase | 2235 | ENSG00000066926 |
| 350  | ENSG00000087460 | NA | GNAS | GNAS complex locus | 2778 | ENSG00000087460 |
| 351  | ENSG00000117118 | NA | SDHB | succinate dehydrogenase complex, subunit B, iron sulfur (Ip) | 6390 | ENSG00000117118 |
| 352  | ENSG00000168827 | NA | GFM1 | G elongation factor, mitochondrial 1 | 85476 | ENSG00000168827 |
| 353  | ENSG00000143641 | NA | GALNT2 | UDP-N-acetyl-alpha-D-galactosamine:polypeptide N-acetylgalactosaminyltransferase 2 (GalNAc-T2) | 2590 | ENSG00000143641 |
| 354  | ENSG00000142149 | NA | HUNK | hormonally up-regulated Neu-associated kinase | 30811 | ENSG00000142149 |
| 355  | ENSG00000149380 | NA | P4HA3 | prolyl 4-hydroxylase, alpha polypeptide III | 283208 | ENSG00000149380 |
| 356  | ENSG00000115944 | NA | COX7A2L | cytochrome c oxidase subunit VIIa polypeptide 2 like | 9167 | ENSG00000115944 |
| 357  | ENSG00000166228 | NA | PCBD1 | pterin-4 alpha-carbinolamine dehydratase/dimerization cofactor of hepatocyte nuclear factor 1 alpha | 5092 | ENSG00000166228 |
| 358  | ENSG00000137225 | NA | CAPN11 | calpain 11 | 11131 | ENSG00000137225 |
| 359  | ENSG00000100294 | NA | MCAT | malonyl CoA:ACP acyltransferase (mitochondrial) | 27349 | ENSG00000100294 |
| 360  | ENSG00000112667 | NA | C6orf108 | chromosome 6 open reading frame 108 | 10591 | ENSG00000112667 |
| 361  | ENSG00000197150 | NA | ABCB8 | ATP-binding cassette, sub-family B (MDR/TAP), member 8 | 11194 | ENSG00000197150 |
| 362  | ENSG00000152234 | NA | ATP5A1 | ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle | 498 | ENSG00000152234 |
| 363  | ENSG00000164494 | NA | PDSS2 | prenyl (decaprenyl) diphosphate synthase, subunit 2 | 57107 | ENSG00000164494 |
| 364  | ENSG00000151366 | NA | NDUFC2 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa | 4718 | ENSG00000151366 |
| 365  | ENSG00000178802 | NA | MPI | mannose phosphate isomerase | 4351 | ENSG00000178802 |
| 366  | ENSG00000128609 | NA | NDUFA5 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa | 4698 | ENSG00000128609 |
| 367  | ENSG00000163541 | NA | SUCLG1 | succinate-CoA ligase, alpha subunit | 8802 | ENSG00000163541 |
| 368  | ENSG00000090432 | NA | MUL1 | mitochondrial E3 ubiquitin protein ligase 1 | 79594 | ENSG00000090432 |
| 369  | ENSG00000146701 | NA | MDH2 | malate dehydrogenase 2, NAD (mitochondrial) | 4191 | ENSG00000146701 |
| 370  | ENSG00000103489 | NA | XYLT1 | xylosyltransferase I | 64131 | ENSG00000103489 |
| 371  | ENSG00000172350 | NA | ABCG4 | ATP-binding cassette, sub-family G (WHITE), member 4 | 64137 | ENSG00000172350 |
| 372  | ENSG00000131730 | NA | CKMT2 | creatine kinase, mitochondrial 2 (sarcomeric) | 1160 | ENSG00000131730 |
| 373  | ENSG00000137714 | NA | FDX1 | ferredoxin 1 | 2230 | ENSG00000137714 |
| 374  | ENSG00000169021 | NA | UQCRFS1 | ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 | 7386 | ENSG00000169021 |
| 375  | ENSG00000115652 | NA | UXS1 | UDP-glucuronate decarboxylase 1 | 80146 | ENSG00000115652 |
| 376  | ENSG00000132541 | NA | HRSP12 | heat-responsive protein 12 | 10247 | ENSG00000132541 |
| 377  | ENSG00000124523 | NA | SIRT5 | sirtuin 5 | 23408 | ENSG00000124523 |
| 378  | ENSG00000145439 | NA | CBR4 | carbonyl reductase 4 | 84869 | ENSG00000145439 |
| 379  | ENSG00000160446 | NA | ZDHHC12 | zinc finger, DHHC-type containing 12 | 84885 | ENSG00000160446 |
| 380  | ENSG00000157881 | NA | PANK4 | pantothenate kinase 4 | 55229 | ENSG00000157881 |
| 381  | ENSG00000197943 | NA | PLCG2 | phospholipase C, gamma 2 (phosphatidylinositol-specific) | 5336 | ENSG00000197943 |
| 382  | ENSG00000144199 | NA | FAHD2B | fumarylacetoacetate hydrolase domain containing 2B | 151313 | ENSG00000144199 |
| 383  | ENSG00000062485 | NA | CS | citrate synthase | 1431 | ENSG00000062485 |
| 384  | ENSG00000160439 | NA | RDH13 | retinol dehydrogenase 13 (all-trans/9-cis) | 112724 | ENSG00000160439 |
| 385  | ENSG00000175193 | NA | PARL | presenilin associated, rhomboid-like | 55486 | ENSG00000175193 |
| 386  | ENSG00000120053 | NA | GOT1 | glutamic-oxaloacetic transaminase 1, soluble (aspartate aminotransferase 1) | 2805 | ENSG00000120053 |
| 387  | ENSG00000149328 | NA | GLB1L2 | galactosidase, beta 1-like 2 | 89944 | ENSG00000149328 |
| 388  | ENSG00000189283 | NA | FHIT | fragile histidine triad | 2272 | ENSG00000189283 |
| 389  | ENSG00000174021 | NA | GNG5 | guanine nucleotide binding protein (G protein), gamma 5 | 2787 | ENSG00000174021 |
| 390  | ENSG00000139428 | NA | MMAB | methylmalonic aciduria (cobalamin deficiency) cblB type | 326625 | ENSG00000139428 |
| 391  | ENSG00000100246 | NA | DNAL4 | dynein, axonemal, light chain 4 | 10126 | ENSG00000100246 |
| 392  | ENSG00000070808 | NA | CAMK2A | calcium/calmodulin-dependent protein kinase II alpha | 815 | ENSG00000070808 |
| 393  | ENSG00000185973 | NA | TMLHE | trimethyllysine hydroxylase, epsilon | 55217 | ENSG00000185973 |
| 394  | ENSG00000196562 | NA | SULF2 | sulfatase 2 | 55959 | ENSG00000196562 |
| 395  | ENSG00000137513 | NA | NARS2 | asparaginyl-tRNA synthetase 2, mitochondrial (putative) | 79731 | ENSG00000137513 |
| 396  | ENSG00000124370 | NA | MCEE | methylmalonyl CoA epimerase | 84693 | ENSG00000124370 |
| 397  | ENSG00000162600 | NA | OMA1 | OMA1 zinc metallopeptidase homolog (S. cerevisiae) | 115209 | ENSG00000162600 |
| 398  | ENSG00000108179 | NA | PPIF | peptidylprolyl isomerase F | 10105 | ENSG00000108179 |
| 399  | ENSG00000137133 | NA | HINT2 | histidine triad nucleotide binding protein 2 | 84681 | ENSG00000137133 |
| 400  | ENSG00000164405 | NA | UQCRQ | ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa | 27089 | ENSG00000164405 |
| 401  | ENSG00000136930 | NA | PSMB7 | proteasome (prosome, macropain) subunit, beta type, 7 | 5695 | ENSG00000136930 |
| 402  | ENSG00000122729 | NA | ACO1 | aconitase 1, soluble | 48 | ENSG00000122729 |
| 403  | ENSG00000173085 | NA | COQ2 | coenzyme Q2 homolog, prenyltransferase (yeast) | 27235 | ENSG00000173085 |
| 404  | ENSG00000124767 | NA | GLO1 | glyoxalase I | 2739 | ENSG00000124767 |
| 405  | ENSG00000124172 | NA | ATP5E | ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit | 514 | ENSG00000124172 |
| 406  | ENSG00000183648 | NA | NDUFB1 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa | 4707 | ENSG00000183648 |
| 407  | ENSG00000110435 | NA | PDHX | pyruvate dehydrogenase complex, component X | 8050 | ENSG00000110435 |
| 408  | ENSG00000099624 | NA | ATP5D | ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit | 513 | ENSG00000099624 |
| 409  | ENSG00000107954 | NA | NEURL | neuralized homolog (Drosophila) | 9148 | ENSG00000107954 |
| 410  | ENSG00000100412 | NA | ACO2 | aconitase 2, mitochondrial | 50 | ENSG00000100412 |
| 411  | ENSG00000185621 | NA | LMLN | leishmanolysin-like (metallopeptidase M8 family) | 89782 | ENSG00000185621 |
| 412  | ENSG00000175792 | NA | RUVBL1 | RuvB-like 1 (E. coli) | 8607 | ENSG00000175792 |
| 413  | ENSG00000121022 | NA | COPS5 | COP9 constitutive photomorphogenic homolog subunit 5 (Arabidopsis) | 10987 | ENSG00000121022 |
| 414  | ENSG00000164896 | NA | FASTK | Fas-activated serine/threonine kinase | 10922 | ENSG00000164896 |
| 415  | ENSG00000112655 | NA | PTK7 | PTK7 protein tyrosine kinase 7 | 5754 | ENSG00000112655 |
| 416  | ENSG00000125356 | NA | NDUFA1 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa | 4694 | ENSG00000125356 |
| 417  | ENSG00000129282 | NA | MRM1 | mitochondrial rRNA methyltransferase 1 homolog (S. cerevisiae) | 79922 | ENSG00000129282 |
| 418  | ENSG00000124641 | NA | MED20 | mediator complex subunit 20 | 9477 | ENSG00000124641 |
| 419  | ENSG00000119673 | NA | ACOT2 | acyl-CoA thioesterase 2 | 10965 | ENSG00000119673 |
| 420  | ENSG00000163636 | NA | PSMD6 | proteasome (prosome, macropain) 26S subunit, non-ATPase, 6 | 9861 | ENSG00000163636 |
| 421  | ENSG00000070785 | NA | EIF2B3 | eukaryotic translation initiation factor 2B, subunit 3 gamma, 58kDa | 8891 | ENSG00000070785 |
| 422  | ENSG00000137574 | NA | TGS1 | trimethylguanosine synthase 1 | 96764 | ENSG00000137574 |
| 423  | ENSG00000099795 | NA | NDUFB7 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa | 4713 | ENSG00000099795 |
| 424  | ENSG00000180185 | NA | FAHD1 | fumarylacetoacetate hydrolase domain containing 1 | 81889 | ENSG00000180185 |
| 425  | ENSG00000175470 | NA | PPP2R2D | protein phosphatase 2, regulatory subunit B, delta | 55844 | ENSG00000175470 |
| 426  | ENSG00000044459 | NA | CNTLN | centlein, centrosomal protein | 54875 | ENSG00000044459 |
| 427  | ENSG00000153574 | NA | RPIA | ribose 5-phosphate isomerase A | 22934 | ENSG00000153574 |
| 428  | ENSG00000101350 | NA | KIF3B | kinesin family member 3B | 9371 | ENSG00000101350 |
| 429  | ENSG00000103507 | NA | BCKDK | branched chain ketoacid dehydrogenase kinase | 10295 | ENSG00000103507 |
| 430  | ENSG00000148090 | NA | AUH | AU RNA binding protein/enoyl-CoA hydratase | 549 | ENSG00000148090 |
| 431  | ENSG00000137171 | NA | KLC4 | kinesin light chain 4 | 89953 | ENSG00000137171 |
| 432  | ENSG00000090013 | NA | BLVRB | biliverdin reductase B (flavin reductase (NADPH)) | 645 | ENSG00000090013 |
| 433  | ENSG00000167136 | NA | ENDOG | endonuclease G | 2021 | ENSG00000167136 |
| 434  | ENSG00000123427 | NA | METTL21B | methyltransferase like 21B | 25895 | ENSG00000123427 |
| 435  | ENSG00000111817 | NA | DSE | dermatan sulfate epimerase | 29940 | ENSG00000111817 |
| 436  | ENSG00000060971 | NA | ACAA1 | acetyl-CoA acyltransferase 1 | 30 | ENSG00000060971 |
| 437  | ENSG00000150867 | NA | PIP4K2A | phosphatidylinositol-5-phosphate 4-kinase, type II, alpha | 5305 | ENSG00000150867 |
| 438  | ENSG00000164347 | NA | GFM2 | G elongation factor, mitochondrial 2 | 84340 | ENSG00000164347 |
| 439  | ENSG00000111906 | NA | HDDC2 | HD domain containing 2 | 51020 | ENSG00000111906 |
| 440  | ENSG00000119723 | NA | COQ6 | coenzyme Q6 homolog, monooxygenase (S. cerevisiae) | 51004 | ENSG00000119723 |
| 441  | ENSG00000138175 | NA | ARL3 | ADP-ribosylation factor-like 3 | 403 | ENSG00000138175 |
| 442  | ENSG00000197894 | NA | ADH5 | alcohol dehydrogenase 5 (class III), chi polypeptide | 128 | ENSG00000197894 |
| 443  | ENSG00000197448 | NA | GSTK1 | glutathione S-transferase kappa 1 | 373156 | ENSG00000197448 |
| 444  | ENSG00000167792 | NA | NDUFV1 | NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa | 4723 | ENSG00000167792 |
| 445  | ENSG00000117594 | NA | HSD11B1 | hydroxysteroid (11-beta) dehydrogenase 1 | 3290 | ENSG00000117594 |
| 446  | ENSG00000188342 | NA | GTF2F2 | general transcription factor IIF, polypeptide 2, 30kDa | 2963 | ENSG00000188342 |
| 447  | ENSG00000110717 | NA | NDUFS8 | NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) | 4728 | ENSG00000110717 |
| 448  | ENSG00000165609 | NA | NUDT5 | nudix (nucleoside diphosphate linked moiety X)-type motif 5 | 11164 | ENSG00000165609 |
| 449  | ENSG00000197535 | NA | MYO5A | myosin VA (heavy chain 12, myoxin) | 4644 | ENSG00000197535 |
| 450  | ENSG00000204308 | NA | RNF5 | ring finger protein 5, E3 ubiquitin protein ligase | 6048 | ENSG00000204308 |
| 451  | ENSG00000184719 | NA | RNLS | renalase, FAD-dependent amine oxidase | 55328 | ENSG00000184719 |
| 452  | ENSG00000137996 | NA | RTCA | RNA 3'-terminal phosphate cyclase | 8634 | ENSG00000137996 |
| 453  | ENSG00000091164 | NA | TXNL1 | thioredoxin-like 1 | 9352 | ENSG00000091164 |
| 454  | ENSG00000184508 | NA | HDDC3 | HD domain containing 3 | 374659 | ENSG00000184508 |
| 455  | ENSG00000036672 | NA | USP2 | ubiquitin specific peptidase 2 | 9099 | ENSG00000036672 |
| 456  | ENSG00000117139 | NA | KDM5B | lysine (K)-specific demethylase 5B | 10765 | ENSG00000117139 |
| 457  | ENSG00000159377 | NA | PSMB4 | proteasome (prosome, macropain) subunit, beta type, 4 | 5692 | ENSG00000159377 |
| 458  | ENSG00000100034 | NA | PPM1F | protein phosphatase, Mg2+/Mn2+ dependent, 1F | 9647 | ENSG00000100034 |
| 459  | ENSG00000138382 | NA | METTL5 | methyltransferase like 5 | 29081 | ENSG00000138382 |
| 460  | ENSG00000178952 | NA | TUFM | Tu translation elongation factor, mitochondrial | 7284 | ENSG00000178952 |
| 461  | ENSG00000177302 | NA | TOP3A | topoisomerase (DNA) III alpha | 7156 | ENSG00000177302 |
| 462  | ENSG00000127884 | NA | ECHS1 | enoyl CoA hydratase, short chain, 1, mitochondrial | 1892 | ENSG00000127884 |
| 463  | ENSG00000198796 | NA | ALPK2 | alpha-kinase 2 | 115701 | ENSG00000198796 |
| 464  | ENSG00000126247 | NA | CAPNS1 | calpain, small subunit 1 | 826 | ENSG00000126247 |
| 465  | ENSG00000241468 | NA | ATP5J2 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 | 9551 | ENSG00000241468 |
| 466  | ENSG00000170430 | NA | MGMT | O-6-methylguanine-DNA methyltransferase | 4255 | ENSG00000170430 |
| 467  | ENSG00000140470 | NA | ADAMTS17 | ADAM metallopeptidase with thrombospondin type 1 motif, 17 | 170691 | ENSG00000140470 |
| 468  | ENSG00000013563 | NA | DNASE1L1 | deoxyribonuclease I-like 1 | 1774 | ENSG00000013563 |
| 469  | ENSG00000117151 | NA | CTBS | chitobiase, di-N-acetyl- | 1486 | ENSG00000117151 |
| 470  | ENSG00000176340 | NA | COX8A | cytochrome c oxidase subunit VIIIA (ubiquitous) | 1351 | ENSG00000176340 |
| 471  | ENSG00000170266 | NA | GLB1 | galactosidase, beta 1 | 2720 | ENSG00000170266 |
| 472  | ENSG00000101247 | NA | NDUFAF5 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 5 | 79133 | ENSG00000101247 |
| 473  | ENSG00000101365 | NA | IDH3B | isocitrate dehydrogenase 3 (NAD+) beta | 3420 | ENSG00000101365 |
| 474  | ENSG00000241837 | NA | ATP5O | ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit | 539 | ENSG00000241837 |
| 475  | ENSG00000141504 | NA | SAT2 | spermidine/spermine N1-acetyltransferase family member 2 | 112483 | ENSG00000141504 |
| 476  | ENSG00000140905 | NA | GCSH | glycine cleavage system protein H (aminomethyl carrier) | 2653 | ENSG00000140905 |
| 477  | ENSG00000158793 | NA | NIT1 | nitrilase 1 | 4817 | ENSG00000158793 |
| 478  | ENSG00000182909 | NA | LENG9 | leukocyte receptor cluster (LRC) member 9 | 94059 | ENSG00000182909 |
| Database:molecular function       Name:oxidoreductase activity, acting on NADH or NADPH       ID:GO:0016651 | ||||||
|---|---|---|---|---|---|---|
| C=94; O=41; E=5.66; R=7.25; rawP=1.38e-25; adjP=1.16e-23 | ||||||
| Index | UserID | Value | Gene Symbol | Gene Name | EntrezGene | Ensembl |
| 1  | ENSG00000151366 | NA | NDUFC2 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa | 4718 | ENSG00000151366 |
| 2  | ENSG00000128609 | NA | NDUFA5 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa | 4698 | ENSG00000128609 |
| 3  | ENSG00000023228 | NA | NDUFS1 | NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) | 4719 | ENSG00000023228 |
| 4  | ENSG00000165264 | NA | NDUFB6 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa | 4712 | ENSG00000165264 |
| 5  | ENSG00000145494 | NA | NDUFS6 | NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) | 4726 | ENSG00000145494 |
| 6  | ENSG00000136521 | NA | NDUFB5 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa | 4711 | ENSG00000136521 |
| 7  | ENSG00000004779 | NA | NDUFAB1 | NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa | 4706 | ENSG00000004779 |
| 8  | ENSG00000189043 | NA | NDUFA4 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa | 4697 | ENSG00000189043 |
| 9  | ENSG00000115286 | NA | NDUFS7 | NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) | 374291 | ENSG00000115286 |
| 10  | ENSG00000164258 | NA | NDUFS4 | NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) | 4724 | ENSG00000164258 |
| 11  | ENSG00000119013 | NA | NDUFB3 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa | 4709 | ENSG00000119013 |
| 12  | ENSG00000104325 | NA | DECR1 | 2,4-dienoyl CoA reductase 1, mitochondrial | 1666 | ENSG00000104325 |
| 13  | ENSG00000167792 | NA | NDUFV1 | NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa | 4723 | ENSG00000167792 |
| 14  | ENSG00000131495 | NA | NDUFA2 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa | 4695 | ENSG00000131495 |
| 15  | ENSG00000065518 | NA | NDUFB4 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa | 4710 | ENSG00000065518 |
| 16  | ENSG00000145439 | NA | CBR4 | carbonyl reductase 4 | 84869 | ENSG00000145439 |
| 17  | ENSG00000090266 | NA | NDUFB2 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa | 4708 | ENSG00000090266 |
| 18  | ENSG00000166136 | NA | NDUFB8 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa | 4714 | ENSG00000166136 |
| 19  | ENSG00000110717 | NA | NDUFS8 | NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) | 4728 | ENSG00000110717 |
| 20  | ENSG00000147684 | NA | NDUFB9 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa | 4715 | ENSG00000147684 |
| 21  | ENSG00000160194 | NA | NDUFV3 | NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa | 4731 | ENSG00000160194 |
| 22  | ENSG00000184983 | NA | NDUFA6 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa | 4700 | ENSG00000184983 |
| 23  | ENSG00000170906 | NA | NDUFA3 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa | 4696 | ENSG00000170906 |
| 24  | ENSG00000184752 | NA | NDUFA12 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 | 55967 | ENSG00000184752 |
| 25  | ENSG00000091140 | NA | DLD | dihydrolipoamide dehydrogenase | 1738 | ENSG00000091140 |
| 26  | ENSG00000130414 | NA | NDUFA10 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa | 4705 | ENSG00000130414 |
| 27  | ENSG00000158864 | NA | NDUFS2 | NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) | 4720 | ENSG00000158864 |
| 28  | ENSG00000139180 | NA | NDUFA9 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa | 4704 | ENSG00000139180 |
| 29  | ENSG00000109390 | NA | NDUFC1 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa | 4717 | ENSG00000109390 |
| 30  | ENSG00000130159 | NA | ECSIT | ECSIT homolog (Drosophila) | 51295 | ENSG00000130159 |
| 31  | ENSG00000183648 | NA | NDUFB1 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa | 4707 | ENSG00000183648 |
| 32  | ENSG00000157326 | NA | DHRS4 | dehydrogenase/reductase (SDR family) member 4 | 10901 | ENSG00000157326 |
| 33  | ENSG00000140990 | NA | NDUFB10 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa | 4716 | ENSG00000140990 |
| 34  | ENSG00000169738 | NA | DCXR | dicarbonyl/L-xylulose reductase | 51181 | ENSG00000169738 |
| 35  | ENSG00000165672 | NA | PRDX3 | peroxiredoxin 3 | 10935 | ENSG00000165672 |
| 36  | ENSG00000112992 | NA | NNT | nicotinamide nucleotide transhydrogenase | 23530 | ENSG00000112992 |
| 37  | ENSG00000125356 | NA | NDUFA1 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa | 4694 | ENSG00000125356 |
| 38  | ENSG00000213619 | NA | NDUFS3 | NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) | 4722 | ENSG00000213619 |
| 39  | ENSG00000168653 | NA | NDUFS5 | NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) | 4725 | ENSG00000168653 |
| 40  | ENSG00000099795 | NA | NDUFB7 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa | 4713 | ENSG00000099795 |
| 41  | ENSG00000119421 | NA | NDUFA8 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa | 4702 | ENSG00000119421 |
| Database:molecular function       Name:hydrogen ion transmembrane transporter activity       ID:GO:0015078 | ||||||
|---|---|---|---|---|---|---|
| C=101; O=40; E=6.08; R=6.58; rawP=4.48e-23; adjP=3.28e-21 | ||||||
| Index | UserID | Value | Gene Symbol | Gene Name | EntrezGene | Ensembl |
| 1  | ENSG00000135940 | NA | COX5B | cytochrome c oxidase subunit Vb | 1329 | ENSG00000135940 |
| 2  | ENSG00000156467 | NA | UQCRB | ubiquinol-cytochrome c reductase binding protein | 7381 | ENSG00000156467 |
| 3  | ENSG00000184076 | NA | UQCR10 | ubiquinol-cytochrome c reductase, complex III subunit X | 29796 | ENSG00000184076 |
| 4  | ENSG00000161281 | NA | COX7A1 | cytochrome c oxidase subunit VIIa polypeptide 1 (muscle) | 1346 | ENSG00000161281 |
| 5  | ENSG00000169020 | NA | ATP5I | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E | 521 | ENSG00000169020 |
| 6  | ENSG00000189043 | NA | NDUFA4 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa | 4697 | ENSG00000189043 |
| 7  | ENSG00000131143 | NA | COX4I1 | cytochrome c oxidase subunit IV isoform 1 | 1327 | ENSG00000131143 |
| 8  | ENSG00000110955 | NA | ATP5B | ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide | 506 | ENSG00000110955 |
| 9  | ENSG00000164038 | NA | SLC9B2 | solute carrier family 9, subfamily B (NHA2, cation proton antiporter 2), member 2 | 133308 | ENSG00000164038 |
| 10  | ENSG00000156885 | NA | COX6A2 | cytochrome c oxidase subunit VIa polypeptide 2 | 1339 | ENSG00000156885 |
| 11  | ENSG00000164919 | NA | COX6C | cytochrome c oxidase subunit VIc | 1345 | ENSG00000164919 |
| 12  | ENSG00000154723 | NA | ATP5J | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 | 522 | ENSG00000154723 |
| 13  | ENSG00000006695 | NA | COX10 | COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) | 1352 | ENSG00000006695 |
| 14  | ENSG00000112695 | NA | COX7A2 | cytochrome c oxidase subunit VIIa polypeptide 2 (liver) | 1347 | ENSG00000112695 |
| 15  | ENSG00000169021 | NA | UQCRFS1 | ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 | 7386 | ENSG00000169021 |
| 16  | ENSG00000135390 | NA | ATP5G2 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C2 (subunit 9) | 517 | ENSG00000135390 |
| 17  | ENSG00000167863 | NA | ATP5H | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d | 10476 | ENSG00000167863 |
| 18  | ENSG00000127540 | NA | UQCR11 | ubiquinol-cytochrome c reductase, complex III subunit XI | 10975 | ENSG00000127540 |
| 19  | ENSG00000131174 | NA | COX7B | cytochrome c oxidase subunit VIIb | 1349 | ENSG00000131174 |
| 20  | ENSG00000047249 | NA | ATP6V1H | ATPase, H+ transporting, lysosomal 50/57kDa, V1 subunit H | 51606 | ENSG00000047249 |
| 21  | ENSG00000171130 | NA | ATP6V0E2 | ATPase, H+ transporting V0 subunit e2 | 155066 | ENSG00000171130 |
| 22  | ENSG00000159199 | NA | ATP5G1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) | 516 | ENSG00000159199 |
| 23  | ENSG00000167283 | NA | ATP5L | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G | 10632 | ENSG00000167283 |
| 24  | ENSG00000127184 | NA | COX7C | cytochrome c oxidase subunit VIIc | 1350 | ENSG00000127184 |
| 25  | ENSG00000164405 | NA | UQCRQ | ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa | 27089 | ENSG00000164405 |
| 26  | ENSG00000010256 | NA | UQCRC1 | ubiquinol-cytochrome c reductase core protein I | 7384 | ENSG00000010256 |
| 27  | ENSG00000124172 | NA | ATP5E | ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit | 514 | ENSG00000124172 |
| 28  | ENSG00000116459 | NA | ATP5F1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 | 515 | ENSG00000116459 |
| 29  | ENSG00000099624 | NA | ATP5D | ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit | 513 | ENSG00000099624 |
| 30  | ENSG00000154518 | NA | ATP5G3 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C3 (subunit 9) | 518 | ENSG00000154518 |
| 31  | ENSG00000165629 | NA | ATP5C1 | ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 | 509 | ENSG00000165629 |
| 32  | ENSG00000112992 | NA | NNT | nicotinamide nucleotide transhydrogenase | 23530 | ENSG00000112992 |
| 33  | ENSG00000115944 | NA | COX7A2L | cytochrome c oxidase subunit VIIa polypeptide 2 like | 9167 | ENSG00000115944 |
| 34  | ENSG00000176340 | NA | COX8A | cytochrome c oxidase subunit VIIIA (ubiquitous) | 1351 | ENSG00000176340 |
| 35  | ENSG00000148290 | NA | SURF1 | surfeit 1 | 6834 | ENSG00000148290 |
| 36  | ENSG00000178741 | NA | COX5A | cytochrome c oxidase subunit Va | 9377 | ENSG00000178741 |
| 37  | ENSG00000173660 | NA | UQCRH | ubiquinol-cytochrome c reductase hinge protein | 7388 | ENSG00000173660 |
| 38  | ENSG00000152234 | NA | ATP5A1 | ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle | 498 | ENSG00000152234 |
| 39  | ENSG00000241837 | NA | ATP5O | ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit | 539 | ENSG00000241837 |
| 40  | ENSG00000126267 | NA | COX6B1 | cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) | 1340 | ENSG00000126267 |
| Database:molecular function       Name:structural constituent of ribosome       ID:GO:0003735 | ||||||
|---|---|---|---|---|---|---|
| C=157; O=48; E=9.45; R=5.08; rawP=9.72e-22; adjP=6.33e-20 | ||||||
| Index | UserID | Value | Gene Symbol | Gene Name | EntrezGene | Ensembl |
| 1  | ENSG00000135972 | NA | MRPS9 | mitochondrial ribosomal protein S9 | 64965 | ENSG00000135972 |
| 2  | ENSG00000239789 | NA | MRPS17 | mitochondrial ribosomal protein S17 | 51373 | ENSG00000239789 |
| 3  | ENSG00000143436 | NA | MRPL9 | mitochondrial ribosomal protein L9 | 65005 | ENSG00000143436 |
| 4  | ENSG00000198015 | NA | MRPL42 | mitochondrial ribosomal protein L42 | 28977 | ENSG00000198015 |
| 5  | ENSG00000122140 | NA | MRPS2 | mitochondrial ribosomal protein S2 | 51116 | ENSG00000122140 |
| 6  | ENSG00000116898 | NA | MRPS15 | mitochondrial ribosomal protein S15 | 64960 | ENSG00000116898 |
| 7  | ENSG00000082515 | NA | MRPL22 | mitochondrial ribosomal protein L22 | 29093 | ENSG00000082515 |
| 8  | ENSG00000115364 | NA | MRPL19 | mitochondrial ribosomal protein L19 | 9801 | ENSG00000115364 |
| 9  | ENSG00000181991 | NA | MRPS11 | mitochondrial ribosomal protein S11 | 64963 | ENSG00000181991 |
| 10  | ENSG00000112996 | NA | MRPS30 | mitochondrial ribosomal protein S30 | 10884 | ENSG00000112996 |
| 11  | ENSG00000175110 | NA | MRPS22 | mitochondrial ribosomal protein S22 | 56945 | ENSG00000175110 |
| 12  | ENSG00000102738 | NA | MRPS31 | mitochondrial ribosomal protein S31 | 10240 | ENSG00000102738 |
| 13  | ENSG00000130312 | NA | MRPL34 | mitochondrial ribosomal protein L34 | 64981 | ENSG00000130312 |
| 14  | ENSG00000163319 | NA | MRPS18C | mitochondrial ribosomal protein S18C | 51023 | ENSG00000163319 |
| 15  | ENSG00000182154 | NA | MRPL41 | mitochondrial ribosomal protein L41 | 64975 | ENSG00000182154 |
| 16  | ENSG00000175581 | NA | MRPL48 | mitochondrial ribosomal protein L48 | 51642 | ENSG00000175581 |
| 17  | ENSG00000174547 | NA | MRPL11 | mitochondrial ribosomal protein L11 | 65003 | ENSG00000174547 |
| 18  | ENSG00000197345 | NA | MRPL21 | mitochondrial ribosomal protein L21 | 219927 | ENSG00000197345 |
| 19  | ENSG00000137547 | NA | MRPL15 | mitochondrial ribosomal protein L15 | 29088 | ENSG00000137547 |
| 20  | ENSG00000173141 | NA | MRP63 | mitochondrial ribosomal protein 63 | 78988 | ENSG00000173141 |
| 21  | ENSG00000116221 | NA | MRPL37 | mitochondrial ribosomal protein L37 | 51253 | ENSG00000116221 |
| 22  | ENSG00000090263 | NA | MRPS33 | mitochondrial ribosomal protein S33 | 51650 | ENSG00000090263 |
| 23  | ENSG00000111639 | NA | MRPL51 | mitochondrial ribosomal protein L51 | 51258 | ENSG00000111639 |
| 24  | ENSG00000143314 | NA | MRPL24 | mitochondrial ribosomal protein L24 | 79590 | ENSG00000143314 |
| 25  | ENSG00000055950 | NA | MRPL43 | mitochondrial ribosomal protein L43 | 84545 | ENSG00000055950 |
| 26  | ENSG00000262814 | NA | MRPL12 | mitochondrial ribosomal protein L12 | 6182 | ENSG00000262814 |
| 27  | ENSG00000048544 | NA | MRPS10 | mitochondrial ribosomal protein S10 | 55173 | ENSG00000048544 |
| 28  | ENSG00000166902 | NA | MRPL16 | mitochondrial ribosomal protein L16 | 54948 | ENSG00000166902 |
| 29  | ENSG00000096080 | NA | MRPS18A | mitochondrial ribosomal protein S18A | 55168 | ENSG00000096080 |
| 30  | ENSG00000172590 | NA | MRPL52 | mitochondrial ribosomal protein L52 | 122704 | ENSG00000172590 |
| 31  | ENSG00000134056 | NA | MRPS36 | mitochondrial ribosomal protein S36 | 92259 | ENSG00000134056 |
| 32  | ENSG00000120333 | NA | MRPS14 | mitochondrial ribosomal protein S14 | 63931 | ENSG00000120333 |
| 33  | ENSG00000204568 | NA | MRPS18B | mitochondrial ribosomal protein S18B | 28973 | ENSG00000204568 |
| 34  | ENSG00000132313 | NA | MRPL35 | mitochondrial ribosomal protein L35 | 51318 | ENSG00000132313 |
| 35  | ENSG00000125445 | NA | MRPS7 | mitochondrial ribosomal protein S7 | 51081 | ENSG00000125445 |
| 36  | ENSG00000187145 | NA | MRPS21 | mitochondrial ribosomal protein S21 | 54460 | ENSG00000187145 |
| 37  | ENSG00000105364 | NA | MRPL4 | mitochondrial ribosomal protein L4 | 51073 | ENSG00000105364 |
| 38  | ENSG00000086504 | NA | MRPL28 | mitochondrial ribosomal protein L28 | 10573 | ENSG00000086504 |
| 39  | ENSG00000112651 | NA | MRPL2 | mitochondrial ribosomal protein L2 | 51069 | ENSG00000112651 |
| 40  | ENSG00000162910 | NA | MRPL55 | mitochondrial ribosomal protein L55 | 128308 | ENSG00000162910 |
| 41  | ENSG00000181610 | NA | MRPS23 | mitochondrial ribosomal protein S23 | 51649 | ENSG00000181610 |
| 42  | ENSG00000243147 | NA | MRPL33 | mitochondrial ribosomal protein L33 | 9553 | ENSG00000243147 |
| 43  | ENSG00000144029 | NA | MRPS5 | mitochondrial ribosomal protein S5 | 64969 | ENSG00000144029 |
| 44  | ENSG00000169288 | NA | MRPL1 | mitochondrial ribosomal protein L1 | 65008 | ENSG00000169288 |
| 45  | ENSG00000172172 | NA | MRPL13 | mitochondrial ribosomal protein L13 | 28998 | ENSG00000172172 |
| 46  | ENSG00000182180 | NA | MRPS16 | mitochondrial ribosomal protein S16 | 51021 | ENSG00000182180 |
| 47  | ENSG00000136522 | NA | MRPL47 | mitochondrial ribosomal protein L47 | 57129 | ENSG00000136522 |
| 48  | ENSG00000214026 | NA | MRPL23 | mitochondrial ribosomal protein L23 | 6150 | ENSG00000214026 |
| Database:molecular function       Name:cofactor binding       ID:GO:0048037 | ||||||
|---|---|---|---|---|---|---|
| C=262; O=54; E=15.77; R=3.42; rawP=8.09e-16; adjP=4.74e-14 | ||||||
| Index | UserID | Value | Gene Symbol | Gene Name | EntrezGene | Ensembl |
| 1  | ENSG00000139410 | NA | SDSL | serine dehydratase-like | 113675 | ENSG00000139410 |
| 2  | ENSG00000113790 | NA | EHHADH | enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase | 1962 | ENSG00000113790 |
| 3  | ENSG00000163541 | NA | SUCLG1 | succinate-CoA ligase, alpha subunit | 8802 | ENSG00000163541 |
| 4  | ENSG00000103316 | NA | CRYM | crystallin, mu | 1428 | ENSG00000103316 |
| 5  | ENSG00000100116 | NA | GCAT | glycine C-acetyltransferase | 23464 | ENSG00000100116 |
| 6  | ENSG00000151376 | NA | ME3 | malic enzyme 3, NADP(+)-dependent, mitochondrial | 10873 | ENSG00000151376 |
| 7  | ENSG00000072506 | NA | HSD17B10 | hydroxysteroid (17-beta) dehydrogenase 10 | 3028 | ENSG00000072506 |
| 8  | ENSG00000156709 | NA | AIFM1 | apoptosis-inducing factor, mitochondrion-associated, 1 | 9131 | ENSG00000156709 |
| 9  | ENSG00000004779 | NA | NDUFAB1 | NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa | 4706 | ENSG00000004779 |
| 10  | ENSG00000182054 | NA | IDH2 | isocitrate dehydrogenase 2 (NADP+), mitochondrial | 3418 | ENSG00000182054 |
| 11  | ENSG00000148672 | NA | GLUD1 | glutamate dehydrogenase 1 | 2746 | ENSG00000148672 |
| 12  | ENSG00000068903 | NA | SIRT2 | sirtuin 2 | 22933 | ENSG00000068903 |
| 13  | ENSG00000073578 | NA | SDHA | succinate dehydrogenase complex, subunit A, flavoprotein (Fp) | 6389 | ENSG00000073578 |
| 14  | ENSG00000115286 | NA | NDUFS7 | NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) | 374291 | ENSG00000115286 |
| 15  | ENSG00000119723 | NA | COQ6 | coenzyme Q6 homolog, monooxygenase (S. cerevisiae) | 51004 | ENSG00000119723 |
| 16  | ENSG00000115652 | NA | UXS1 | UDP-glucuronate decarboxylase 1 | 80146 | ENSG00000115652 |
| 17  | ENSG00000104325 | NA | DECR1 | 2,4-dienoyl CoA reductase 1, mitochondrial | 1666 | ENSG00000104325 |
| 18  | ENSG00000167792 | NA | NDUFV1 | NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa | 4723 | ENSG00000167792 |
| 19  | ENSG00000139531 | NA | SUOX | sulfite oxidase | 6821 | ENSG00000139531 |
| 20  | ENSG00000125166 | NA | GOT2 | glutamic-oxaloacetic transaminase 2, mitochondrial (aspartate aminotransferase 2) | 2806 | ENSG00000125166 |
| 21  | ENSG00000124523 | NA | SIRT5 | sirtuin 5 | 23408 | ENSG00000124523 |
| 22  | ENSG00000145439 | NA | CBR4 | carbonyl reductase 4 | 84869 | ENSG00000145439 |
| 23  | ENSG00000140374 | NA | ETFA | electron-transfer-flavoprotein, alpha polypeptide | 2108 | ENSG00000140374 |
| 24  | ENSG00000198721 | NA | ECI2 | enoyl-CoA delta isomerase 2 | 10455 | ENSG00000198721 |
| 25  | ENSG00000120053 | NA | GOT1 | glutamic-oxaloacetic transaminase 1, soluble (aspartate aminotransferase 1) | 2805 | ENSG00000120053 |
| 26  | ENSG00000151498 | NA | ACAD8 | acyl-CoA dehydrogenase family, member 8 | 27034 | ENSG00000151498 |
| 27  | ENSG00000091140 | NA | DLD | dihydrolipoamide dehydrogenase | 1738 | ENSG00000091140 |
| 28  | ENSG00000158864 | NA | NDUFS2 | NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) | 4720 | ENSG00000158864 |
| 29  | ENSG00000111716 | NA | LDHB | lactate dehydrogenase B | 3945 | ENSG00000111716 |
| 30  | ENSG00000108439 | NA | PNPO | pyridoxamine 5'-phosphate oxidase | 55163 | ENSG00000108439 |
| 31  | ENSG00000139180 | NA | NDUFA9 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa | 4704 | ENSG00000139180 |
| 32  | ENSG00000122971 | NA | ACADS | acyl-CoA dehydrogenase, C-2 to C-3 short chain | 35 | ENSG00000122971 |
| 33  | ENSG00000111640 | NA | GAPDH | glyceraldehyde-3-phosphate dehydrogenase | 2597 | ENSG00000111640 |
| 34  | ENSG00000067829 | NA | IDH3G | isocitrate dehydrogenase 3 (NAD+) gamma | 3421 | ENSG00000067829 |
| 35  | ENSG00000203797 | NA | DDO | D-aspartate oxidase | 8528 | ENSG00000203797 |
| 36  | ENSG00000116171 | NA | SCP2 | sterol carrier protein 2 | 6342 | ENSG00000116171 |
| 37  | ENSG00000142082 | NA | SIRT3 | sirtuin 3 | 23410 | ENSG00000142082 |
| 38  | ENSG00000166816 | NA | LDHD | lactate dehydrogenase D | 197257 | ENSG00000166816 |
| 39  | ENSG00000135297 | NA | MTO1 | mitochondrial translation optimization 1 homolog (S. cerevisiae) | 25821 | ENSG00000135297 |
| 40  | ENSG00000204370 | NA | SDHD | succinate dehydrogenase complex, subunit D, integral membrane protein | 6392 | ENSG00000204370 |
| 41  | ENSG00000117118 | NA | SDHB | succinate dehydrogenase complex, subunit B, iron sulfur (Ip) | 6390 | ENSG00000117118 |
| 42  | ENSG00000171503 | NA | ETFDH | electron-transferring-flavoprotein dehydrogenase | 2110 | ENSG00000171503 |
| 43  | ENSG00000137106 | NA | GRHPR | glyoxylate reductase/hydroxypyruvate reductase | 9380 | ENSG00000137106 |
| 44  | ENSG00000138796 | NA | HADH | hydroxyacyl-CoA dehydrogenase | 3033 | ENSG00000138796 |
| 45  | ENSG00000111271 | NA | ACAD10 | acyl-CoA dehydrogenase family, member 10 | 80724 | ENSG00000111271 |
| 46  | ENSG00000160211 | NA | G6PD | glucose-6-phosphate dehydrogenase | 2539 | ENSG00000160211 |
| 47  | ENSG00000161533 | NA | ACOX1 | acyl-CoA oxidase 1, palmitoyl | 51 | ENSG00000161533 |
| 48  | ENSG00000112992 | NA | NNT | nicotinamide nucleotide transhydrogenase | 23530 | ENSG00000112992 |
| 49  | ENSG00000155368 | NA | DBI | diazepam binding inhibitor (GABA receptor modulator, acyl-CoA binding protein) | 1622 | ENSG00000155368 |
| 50  | ENSG00000023330 | NA | ALAS1 | aminolevulinate, delta-, synthase 1 | 211 | ENSG00000023330 |
| 51  | ENSG00000105135 | NA | ILVBL | ilvB (bacterial acetolactate synthase)-like | 10994 | ENSG00000105135 |
| 52  | ENSG00000101365 | NA | IDH3B | isocitrate dehydrogenase 3 (NAD+) beta | 3420 | ENSG00000101365 |
| 53  | ENSG00000072778 | NA | ACADVL | acyl-CoA dehydrogenase, very long chain | 37 | ENSG00000072778 |
| 54  | ENSG00000244005 | NA | NFS1 | NFS1 nitrogen fixation 1 homolog (S. cerevisiae) | 9054 | ENSG00000244005 |
| Database:cellular component       Name:mitochondrion       ID:GO:0005739 | ||||||
|---|---|---|---|---|---|---|
| C=1525; O=468; E=92.56; R=5.06; rawP=4.24e-232; adjP=1.68e-229 | ||||||
| Index | UserID | Value | Gene Symbol | Gene Name | EntrezGene | Ensembl |
| 1  | ENSG00000143575 | NA | HAX1 | HCLS1 associated protein X-1 | 10456 | ENSG00000143575 |
| 2  | ENSG00000165264 | NA | NDUFB6 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa | 4712 | ENSG00000165264 |
| 3  | ENSG00000109846 | NA | CRYAB | crystallin, alpha B | 1410 | ENSG00000109846 |
| 4  | ENSG00000116898 | NA | MRPS15 | mitochondrial ribosomal protein S15 | 64960 | ENSG00000116898 |
| 5  | ENSG00000161281 | NA | COX7A1 | cytochrome c oxidase subunit VIIa polypeptide 1 (muscle) | 1346 | ENSG00000161281 |
| 6  | ENSG00000167862 | NA | ICT1 | immature colon carcinoma transcript 1 | 3396 | ENSG00000167862 |
| 7  | ENSG00000148672 | NA | GLUD1 | glutamate dehydrogenase 1 | 2746 | ENSG00000148672 |
| 8  | ENSG00000147592 | NA | LACTB2 | lactamase, beta 2 | 51110 | ENSG00000147592 |
| 9  | ENSG00000116288 | NA | PARK7 | parkinson protein 7 | 11315 | ENSG00000116288 |
| 10  | ENSG00000135390 | NA | ATP5G2 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C2 (subunit 9) | 517 | ENSG00000135390 |
| 11  | ENSG00000177370 | NA | TIMM22 | translocase of inner mitochondrial membrane 22 homolog (yeast) | 29928 | ENSG00000177370 |
| 12  | ENSG00000003509 | NA | C2orf56 | chromosome 2 open reading frame 56 | 55471 | ENSG00000003509 |
| 13  | ENSG00000166136 | NA | NDUFB8 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa | 4714 | ENSG00000166136 |
| 14  | ENSG00000116353 | NA | MECR | mitochondrial trans-2-enoyl-CoA reductase | 51102 | ENSG00000116353 |
| 15  | ENSG00000172340 | NA | SUCLG2 | succinate-CoA ligase, GDP-forming, beta subunit | 8801 | ENSG00000172340 |
| 16  | ENSG00000151093 | NA | OXSM | 3-oxoacyl-ACP synthase, mitochondrial | 54995 | ENSG00000151093 |
| 17  | ENSG00000205707 | NA | LYRM5 | LYR motif containing 5 | 144363 | ENSG00000205707 |
| 18  | ENSG00000091140 | NA | DLD | dihydrolipoamide dehydrogenase | 1738 | ENSG00000091140 |
| 19  | ENSG00000130414 | NA | NDUFA10 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa | 4705 | ENSG00000130414 |
| 20  | ENSG00000165060 | NA | FXN | frataxin | 2395 | ENSG00000165060 |
| 21  | ENSG00000007923 | NA | DNAJC11 | DnaJ (Hsp40) homolog, subfamily C, member 11 | 55735 | ENSG00000007923 |
| 22  | ENSG00000173141 | NA | MRP63 | mitochondrial ribosomal protein 63 | 78988 | ENSG00000173141 |
| 23  | ENSG00000131828 | NA | PDHA1 | pyruvate dehydrogenase (lipoamide) alpha 1 | 5160 | ENSG00000131828 |
| 24  | ENSG00000122971 | NA | ACADS | acyl-CoA dehydrogenase, C-2 to C-3 short chain | 35 | ENSG00000122971 |
| 25  | ENSG00000103356 | NA | EARS2 | glutamyl-tRNA synthetase 2, mitochondrial (putative) | 124454 | ENSG00000103356 |
| 26  | ENSG00000109390 | NA | NDUFC1 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa | 4717 | ENSG00000109390 |
| 27  | ENSG00000182512 | NA | GLRX5 | glutaredoxin 5 | 51218 | ENSG00000182512 |
| 28  | ENSG00000091483 | NA | FH | fumarate hydratase | 2271 | ENSG00000091483 |
| 29  | ENSG00000143314 | NA | MRPL24 | mitochondrial ribosomal protein L24 | 79590 | ENSG00000143314 |
| 30  | ENSG00000103160 | NA | HSDL1 | hydroxysteroid dehydrogenase like 1 | 83693 | ENSG00000103160 |
| 31  | ENSG00000055950 | NA | MRPL43 | mitochondrial ribosomal protein L43 | 84545 | ENSG00000055950 |
| 32  | ENSG00000103642 | NA | LACTB | lactamase, beta | 114294 | ENSG00000103642 |
| 33  | ENSG00000110074 | NA | FOXRED1 | FAD-dependent oxidoreductase domain containing 1 | 55572 | ENSG00000110074 |
| 34  | ENSG00000135070 | NA | ISCA1 | iron-sulfur cluster assembly 1 homolog (S. cerevisiae) | 81689 | ENSG00000135070 |
| 35  | ENSG00000142082 | NA | SIRT3 | sirtuin 3 | 23410 | ENSG00000142082 |
| 36  | ENSG00000127838 | NA | PNKD | paroxysmal nonkinesigenic dyskinesia | 25953 | ENSG00000127838 |
| 37  | ENSG00000204568 | NA | MRPS18B | mitochondrial ribosomal protein S18B | 28973 | ENSG00000204568 |
| 38  | ENSG00000148334 | NA | PTGES2 | prostaglandin E synthase 2 | 80142 | ENSG00000148334 |
| 39  | ENSG00000174374 | NA | WBSCR16 | Williams-Beuren syndrome chromosome region 16 | 81554 | ENSG00000174374 |
| 40  | ENSG00000165283 | NA | STOML2 | stomatin (EPB72)-like 2 | 30968 | ENSG00000165283 |
| 41  | ENSG00000164466 | NA | SFXN1 | sideroflexin 1 | 94081 | ENSG00000164466 |
| 42  | ENSG00000151729 | NA | SLC25A4 | solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4 | 291 | ENSG00000151729 |
| 43  | ENSG00000178057 | NA | NDUFAF3 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 3 | 25915 | ENSG00000178057 |
| 44  | ENSG00000126432 | NA | PRDX5 | peroxiredoxin 5 | 25824 | ENSG00000126432 |
| 45  | ENSG00000023330 | NA | ALAS1 | aminolevulinate, delta-, synthase 1 | 211 | ENSG00000023330 |
| 46  | ENSG00000183172 | NA | C22orf32 | chromosome 22 open reading frame 32 | 91689 | ENSG00000183172 |
| 47  | ENSG00000213619 | NA | NDUFS3 | NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) | 4722 | ENSG00000213619 |
| 48  | ENSG00000109180 | NA | OCIAD1 | OCIA domain containing 1 | 54940 | ENSG00000109180 |
| 49  | ENSG00000178741 | NA | COX5A | cytochrome c oxidase subunit Va | 9377 | ENSG00000178741 |
| 50  | ENSG00000173660 | NA | UQCRH | ubiquinol-cytochrome c reductase hinge protein | 7388 | ENSG00000173660 |
| 51  | ENSG00000214253 | NA | FIS1 | fission 1 (mitochondrial outer membrane) homolog (S. cerevisiae) | 51024 | ENSG00000214253 |
| 52  | ENSG00000147586 | NA | MRPS28 | mitochondrial ribosomal protein S28 | 28957 | ENSG00000147586 |
| 53  | ENSG00000133028 | NA | SCO1 | SCO cytochrome oxidase deficient homolog 1 (yeast) | 6341 | ENSG00000133028 |
| 54  | ENSG00000169288 | NA | MRPL1 | mitochondrial ribosomal protein L1 | 65008 | ENSG00000169288 |
| 55  | ENSG00000100348 | NA | TXN2 | thioredoxin 2 | 25828 | ENSG00000100348 |
| 56  | ENSG00000160221 | NA | C21orf33 | chromosome 21 open reading frame 33 | 8209 | ENSG00000160221 |
| 57  | ENSG00000101181 | NA | GTPBP5 | GTP binding protein 5 (putative) | 26164 | ENSG00000101181 |
| 58  | ENSG00000109919 | NA | MTCH2 | mitochondrial carrier 2 | 23788 | ENSG00000109919 |
| 59  | ENSG00000135940 | NA | COX5B | cytochrome c oxidase subunit Vb | 1329 | ENSG00000135940 |
| 60  | ENSG00000029639 | NA | TFB1M | transcription factor B1, mitochondrial | 51106 | ENSG00000029639 |
| 61  | ENSG00000135900 | NA | MRPL44 | mitochondrial ribosomal protein L44 | 65080 | ENSG00000135900 |
| 62  | ENSG00000143436 | NA | MRPL9 | mitochondrial ribosomal protein L9 | 65005 | ENSG00000143436 |
| 63  | ENSG00000239789 | NA | MRPS17 | mitochondrial ribosomal protein S17 | 51373 | ENSG00000239789 |
| 64  | ENSG00000113790 | NA | EHHADH | enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase | 1962 | ENSG00000113790 |
| 65  | ENSG00000162851 | NA | TFB2M | transcription factor B2, mitochondrial | 64216 | ENSG00000162851 |
| 66  | ENSG00000122140 | NA | MRPS2 | mitochondrial ribosomal protein S2 | 51116 | ENSG00000122140 |
| 67  | ENSG00000156709 | NA | AIFM1 | apoptosis-inducing factor, mitochondrion-associated, 1 | 9131 | ENSG00000156709 |
| 68  | ENSG00000082515 | NA | MRPL22 | mitochondrial ribosomal protein L22 | 29093 | ENSG00000082515 |
| 69  | ENSG00000189043 | NA | NDUFA4 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa | 4697 | ENSG00000189043 |
| 70  | ENSG00000172115 | NA | CYCS | cytochrome c, somatic | 54205 | ENSG00000172115 |
| 71  | ENSG00000176894 | NA | PXMP2 | peroxisomal membrane protein 2, 22kDa | 5827 | ENSG00000176894 |
| 72  | ENSG00000035141 | NA | FAM136A | family with sequence similarity 136, member A | 84908 | ENSG00000035141 |
| 73  | ENSG00000164919 | NA | COX6C | cytochrome c oxidase subunit VIc | 1345 | ENSG00000164919 |
| 74  | ENSG00000139131 | NA | YARS2 | tyrosyl-tRNA synthetase 2, mitochondrial | 51067 | ENSG00000139131 |
| 75  | ENSG00000115286 | NA | NDUFS7 | NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) | 374291 | ENSG00000115286 |
| 76  | ENSG00000164258 | NA | NDUFS4 | NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) | 4724 | ENSG00000164258 |
| 77  | ENSG00000132570 | NA | PCBD2 | pterin-4 alpha-carbinolamine dehydratase/dimerization cofactor of hepatocyte nuclear factor 1 alpha (TCF1) 2 | 84105 | ENSG00000132570 |
| 78  | ENSG00000156170 | NA | NDUFAF6 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 | 137682 | ENSG00000156170 |
| 79  | ENSG00000155463 | NA | OXA1L | oxidase (cytochrome c) assembly 1-like | 5018 | ENSG00000155463 |
| 80  | ENSG00000167863 | NA | ATP5H | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d | 10476 | ENSG00000167863 |
| 81  | ENSG00000163319 | NA | MRPS18C | mitochondrial ribosomal protein S18C | 51023 | ENSG00000163319 |
| 82  | ENSG00000166165 | NA | CKB | creatine kinase, brain | 1152 | ENSG00000166165 |
| 83  | ENSG00000179091 | NA | CYC1 | cytochrome c-1 | 1537 | ENSG00000179091 |
| 84  | ENSG00000185608 | NA | MRPL40 | mitochondrial ribosomal protein L40 | 64976 | ENSG00000185608 |
| 85  | ENSG00000127540 | NA | UQCR11 | ubiquinol-cytochrome c reductase, complex III subunit XI | 10975 | ENSG00000127540 |
| 86  | ENSG00000197345 | NA | MRPL21 | mitochondrial ribosomal protein L21 | 219927 | ENSG00000197345 |
| 87  | ENSG00000184752 | NA | NDUFA12 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 | 55967 | ENSG00000184752 |
| 88  | ENSG00000132423 | NA | COQ3 | coenzyme Q3 homolog, methyltransferase (S. cerevisiae) | 51805 | ENSG00000132423 |
| 89  | ENSG00000171861 | NA | RNMTL1 | RNA methyltransferase like 1 | 55178 | ENSG00000171861 |
| 90  | ENSG00000156411 | NA | C14orf2 | chromosome 14 open reading frame 2 | 9556 | ENSG00000156411 |
| 91  | ENSG00000131844 | NA | MCCC2 | methylcrotonoyl-CoA carboxylase 2 (beta) | 64087 | ENSG00000131844 |
| 92  | ENSG00000134905 | NA | CARS2 | cysteinyl-tRNA synthetase 2, mitochondrial (putative) | 79587 | ENSG00000134905 |
| 93  | ENSG00000182810 | NA | DDX28 | DEAD (Asp-Glu-Ala-Asp) box polypeptide 28 | 55794 | ENSG00000182810 |
| 94  | ENSG00000105819 | NA | PMPCB | peptidase (mitochondrial processing) beta | 9512 | ENSG00000105819 |
| 95  | ENSG00000150779 | NA | TIMM8B | translocase of inner mitochondrial membrane 8 homolog B (yeast) | 26521 | ENSG00000150779 |
| 96  | ENSG00000204228 | NA | HSD17B8 | hydroxysteroid (17-beta) dehydrogenase 8 | 7923 | ENSG00000204228 |
| 97  | ENSG00000196683 | NA | TOMM7 | translocase of outer mitochondrial membrane 7 homolog (yeast) | 54543 | ENSG00000196683 |
| 98  | ENSG00000179152 | NA | TCAIM | T cell activation inhibitor, mitochondrial | 285343 | ENSG00000179152 |
| 99  | ENSG00000175198 | NA | PCCA | propionyl CoA carboxylase, alpha polypeptide | 5095 | ENSG00000175198 |
| 100  | ENSG00000067829 | NA | IDH3G | isocitrate dehydrogenase 3 (NAD+) gamma | 3421 | ENSG00000067829 |
| 101  | ENSG00000166902 | NA | MRPL16 | mitochondrial ribosomal protein L16 | 54948 | ENSG00000166902 |
| 102  | ENSG00000067225 | NA | PKM | pyruvate kinase, muscle | 5315 | ENSG00000067225 |
| 103  | ENSG00000114023 | NA | FAM162A | family with sequence similarity 162, member A | 26355 | ENSG00000114023 |
| 104  | ENSG00000157326 | NA | DHRS4 | dehydrogenase/reductase (SDR family) member 4 | 10901 | ENSG00000157326 |
| 105  | ENSG00000140990 | NA | NDUFB10 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa | 4716 | ENSG00000140990 |
| 106  | ENSG00000135297 | NA | MTO1 | mitochondrial translation optimization 1 homolog (S. cerevisiae) | 25821 | ENSG00000135297 |
| 107  | ENSG00000144182 | NA | LIPT1 | lipoyltransferase 1 | 51601 | ENSG00000144182 |
| 108  | ENSG00000198523 | NA | PLN | phospholamban | 5350 | ENSG00000198523 |
| 109  | ENSG00000006530 | NA | AGK | acylglycerol kinase | 55750 | ENSG00000006530 |
| 110  | ENSG00000120662 | NA | MTRF1 | mitochondrial translational release factor 1 | 9617 | ENSG00000120662 |
| 111  | ENSG00000247626 | NA | MARS2 | methionyl-tRNA synthetase 2, mitochondrial | 92935 | ENSG00000247626 |
| 112  | ENSG00000126602 | NA | TRAP1 | TNF receptor-associated protein 1 | 10131 | ENSG00000126602 |
| 113  | ENSG00000243147 | NA | MRPL33 | mitochondrial ribosomal protein L33 | 9553 | ENSG00000243147 |
| 114  | ENSG00000165629 | NA | ATP5C1 | ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 | 509 | ENSG00000165629 |
| 115  | ENSG00000224877 | NA | C17orf89 | chromosome 17 open reading frame 89 | 284184 | ENSG00000224877 |
| 116  | ENSG00000143653 | NA | SCCPDH | saccharopine dehydrogenase (putative) | 51097 | ENSG00000143653 |
| 117  | ENSG00000116906 | NA | GNPAT | glyceronephosphate O-acyltransferase | 8443 | ENSG00000116906 |
| 118  | ENSG00000123545 | NA | NDUFAF4 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 4 | 29078 | ENSG00000123545 |
| 119  | ENSG00000148290 | NA | SURF1 | surfeit 1 | 6834 | ENSG00000148290 |
| 120  | ENSG00000170634 | NA | ACYP2 | acylphosphatase 2, muscle type | 98 | ENSG00000170634 |
| 121  | ENSG00000133315 | NA | MACROD1 | MACRO domain containing 1 | 28992 | ENSG00000133315 |
| 122  | ENSG00000072778 | NA | ACADVL | acyl-CoA dehydrogenase, very long chain | 37 | ENSG00000072778 |
| 123  | ENSG00000154930 | NA | ACSS1 | acyl-CoA synthetase short-chain family member 1 | 84532 | ENSG00000154930 |
| 124  | ENSG00000125652 | NA | ALKBH7 | alkB, alkylation repair homolog 7 (E. coli) | 84266 | ENSG00000125652 |
| 125  | ENSG00000049883 | NA | PTCD2 | pentatricopeptide repeat domain 2 | 79810 | ENSG00000049883 |
| 126  | ENSG00000196636 | NA | ACN9 | ACN9 homolog (S. cerevisiae) | 57001 | ENSG00000196636 |
| 127  | ENSG00000139410 | NA | SDSL | serine dehydratase-like | 113675 | ENSG00000139410 |
| 128  | ENSG00000059691 | NA | PET112 | PET112 homolog (yeast) | 5188 | ENSG00000059691 |
| 129  | ENSG00000160124 | NA | CCDC58 | coiled-coil domain containing 58 | 131076 | ENSG00000160124 |
| 130  | ENSG00000125995 | NA | ROMO1 | reactive oxygen species modulator 1 | 140823 | ENSG00000125995 |
| 131  | ENSG00000136521 | NA | NDUFB5 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa | 4711 | ENSG00000136521 |
| 132  | ENSG00000169020 | NA | ATP5I | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E | 521 | ENSG00000169020 |
| 133  | ENSG00000114021 | NA | NIT2 | nitrilase family, member 2 | 56954 | ENSG00000114021 |
| 134  | ENSG00000004779 | NA | NDUFAB1 | NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa | 4706 | ENSG00000004779 |
| 135  | ENSG00000182054 | NA | IDH2 | isocitrate dehydrogenase 2 (NADP+), mitochondrial | 3418 | ENSG00000182054 |
| 136  | ENSG00000168958 | NA | MFF | mitochondrial fission factor | 56947 | ENSG00000168958 |
| 137  | ENSG00000004961 | NA | HCCS | holocytochrome c synthase | 3052 | ENSG00000004961 |
| 138  | ENSG00000165898 | NA | ISCA2 | iron-sulfur cluster assembly 2 homolog (S. cerevisiae) | 122961 | ENSG00000165898 |
| 139  | ENSG00000073578 | NA | SDHA | succinate dehydrogenase complex, subunit A, flavoprotein (Fp) | 6389 | ENSG00000073578 |
| 140  | ENSG00000119013 | NA | NDUFB3 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa | 4709 | ENSG00000119013 |
| 141  | ENSG00000151413 | NA | NUBPL | nucleotide binding protein-like | 80224 | ENSG00000151413 |
| 142  | ENSG00000213965 | NA | NUDT19 | nudix (nucleoside diphosphate linked moiety X)-type motif 19 | 390916 | ENSG00000213965 |
| 143  | ENSG00000104325 | NA | DECR1 | 2,4-dienoyl CoA reductase 1, mitochondrial | 1666 | ENSG00000104325 |
| 144  | ENSG00000132463 | NA | GRSF1 | G-rich RNA sequence binding factor 1 | 2926 | ENSG00000132463 |
| 145  | ENSG00000259494 | NA | MRPL46 | mitochondrial ribosomal protein L46 | 26589 | ENSG00000259494 |
| 146  | ENSG00000113048 | NA | MRPS27 | mitochondrial ribosomal protein S27 | 23107 | ENSG00000113048 |
| 147  | ENSG00000165487 | NA | EFHA1 | EF-hand domain family, member A1 | 221154 | ENSG00000165487 |
| 148  | ENSG00000078668 | NA | VDAC3 | voltage-dependent anion channel 3 | 7419 | ENSG00000078668 |
| 149  | ENSG00000182154 | NA | MRPL41 | mitochondrial ribosomal protein L41 | 64975 | ENSG00000182154 |
| 150  | ENSG00000144827 | NA | ABHD10 | abhydrolase domain containing 10 | 55347 | ENSG00000144827 |
| 151  | ENSG00000167468 | NA | GPX4 | glutathione peroxidase 4 | 2879 | ENSG00000167468 |
| 152  | ENSG00000139180 | NA | NDUFA9 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa | 4704 | ENSG00000139180 |
| 153  | ENSG00000127184 | NA | COX7C | cytochrome c oxidase subunit VIIc | 1350 | ENSG00000127184 |
| 154  | ENSG00000085760 | NA | MTIF2 | mitochondrial translational initiation factor 2 | 4528 | ENSG00000085760 |
| 155  | ENSG00000165637 | NA | VDAC2 | voltage-dependent anion channel 2 | 7417 | ENSG00000165637 |
| 156  | ENSG00000187118 | NA | CMC1 | COX assembly mitochondrial protein 1 homolog (S. cerevisiae) | 152100 | ENSG00000187118 |
| 157  | ENSG00000172878 | NA | METAP1D | methionyl aminopeptidase type 1D (mitochondrial) | 254042 | ENSG00000172878 |
| 158  | ENSG00000204370 | NA | SDHD | succinate dehydrogenase complex, subunit D, integral membrane protein | 6392 | ENSG00000204370 |
| 159  | ENSG00000106554 | NA | CHCHD3 | coiled-coil-helix-coiled-coil-helix domain containing 3 | 54927 | ENSG00000106554 |
| 160  | ENSG00000086504 | NA | MRPL28 | mitochondrial ribosomal protein L28 | 10573 | ENSG00000086504 |
| 161  | ENSG00000108384 | NA | RAD51C | RAD51 homolog C (S. cerevisiae) | 5889 | ENSG00000108384 |
| 162  | ENSG00000162910 | NA | MRPL55 | mitochondrial ribosomal protein L55 | 128308 | ENSG00000162910 |
| 163  | ENSG00000130349 | NA | C6orf203 | chromosome 6 open reading frame 203 | 51250 | ENSG00000130349 |
| 164  | ENSG00000027001 | NA | MIPEP | mitochondrial intermediate peptidase | 4285 | ENSG00000027001 |
| 165  | ENSG00000111271 | NA | ACAD10 | acyl-CoA dehydrogenase family, member 10 | 80724 | ENSG00000111271 |
| 166  | ENSG00000103423 | NA | DNAJA3 | DnaJ (Hsp40) homolog, subfamily A, member 3 | 9093 | ENSG00000103423 |
| 167  | ENSG00000138777 | NA | PPA2 | pyrophosphatase (inorganic) 2 | 27068 | ENSG00000138777 |
| 168  | ENSG00000100601 | NA | ALKBH1 | alkB, alkylation repair homolog 1 (E. coli) | 8846 | ENSG00000100601 |
| 169  | ENSG00000182180 | NA | MRPS16 | mitochondrial ribosomal protein S16 | 51021 | ENSG00000182180 |
| 170  | ENSG00000174032 | NA | SLC25A30 | solute carrier family 25, member 30 | 253512 | ENSG00000174032 |
| 171  | ENSG00000136522 | NA | MRPL47 | mitochondrial ribosomal protein L47 | 57129 | ENSG00000136522 |
| 172  | ENSG00000175756 | NA | AURKAIP1 | aurora kinase A interacting protein 1 | 54998 | ENSG00000175756 |
| 173  | ENSG00000135972 | NA | MRPS9 | mitochondrial ribosomal protein S9 | 64965 | ENSG00000135972 |
| 174  | ENSG00000023228 | NA | NDUFS1 | NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) | 4719 | ENSG00000023228 |
| 175  | ENSG00000143252 | NA | SDHC | succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa | 6391 | ENSG00000143252 |
| 176  | ENSG00000100116 | NA | GCAT | glycine C-acetyltransferase | 23464 | ENSG00000100116 |
| 177  | ENSG00000151376 | NA | ME3 | malic enzyme 3, NADP(+)-dependent, mitochondrial | 10873 | ENSG00000151376 |
| 178  | ENSG00000165775 | NA | FUNDC2 | FUN14 domain containing 2 | 65991 | ENSG00000165775 |
| 179  | ENSG00000182606 | NA | TRAK1 | trafficking protein, kinesin binding 1 | 22906 | ENSG00000182606 |
| 180  | ENSG00000115840 | NA | SLC25A12 | solute carrier family 25 (aspartate/glutamate carrier), member 12 | 8604 | ENSG00000115840 |
| 181  | ENSG00000145982 | NA | FARS2 | phenylalanyl-tRNA synthetase 2, mitochondrial | 10667 | ENSG00000145982 |
| 182  | ENSG00000121897 | NA | LIAS | lipoic acid synthetase | 11019 | ENSG00000121897 |
| 183  | ENSG00000110955 | NA | ATP5B | ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide | 506 | ENSG00000110955 |
| 184  | ENSG00000197122 | NA | SRC | v-src sarcoma (Schmidt-Ruppin A-2) viral oncogene homolog (avian) | 6714 | ENSG00000197122 |
| 185  | ENSG00000112695 | NA | COX7A2 | cytochrome c oxidase subunit VIIa polypeptide 2 (liver) | 1347 | ENSG00000112695 |
| 186  | ENSG00000083720 | NA | OXCT1 | 3-oxoacid CoA transferase 1 | 5019 | ENSG00000083720 |
| 187  | ENSG00000131495 | NA | NDUFA2 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa | 4695 | ENSG00000131495 |
| 188  | ENSG00000065518 | NA | NDUFB4 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa | 4710 | ENSG00000065518 |
| 189  | ENSG00000095321 | NA | CRAT | carnitine O-acetyltransferase | 1384 | ENSG00000095321 |
| 190  | ENSG00000159445 | NA | THEM4 | thioesterase superfamily member 4 | 117145 | ENSG00000159445 |
| 191  | ENSG00000165688 | NA | PMPCA | peptidase (mitochondrial processing) alpha | 23203 | ENSG00000165688 |
| 192  | ENSG00000120992 | NA | LYPLA1 | lysophospholipase I | 10434 | ENSG00000120992 |
| 193  | ENSG00000198721 | NA | ECI2 | enoyl-CoA delta isomerase 2 | 10455 | ENSG00000198721 |
| 194  | ENSG00000183617 | NA | MRPL54 | mitochondrial ribosomal protein L54 | 116541 | ENSG00000183617 |
| 195  | ENSG00000112855 | NA | HARS2 | histidyl-tRNA synthetase 2, mitochondrial | 23438 | ENSG00000112855 |
| 196  | ENSG00000197580 | NA | BCO2 | beta-carotene oxygenase 2 | 83875 | ENSG00000197580 |
| 197  | ENSG00000147853 | NA | AK3 | adenylate kinase 3 | 50808 | ENSG00000147853 |
| 198  | ENSG00000131174 | NA | COX7B | cytochrome c oxidase subunit VIIb | 1349 | ENSG00000131174 |
| 199  | ENSG00000119705 | NA | SLIRP | SRA stem-loop interacting RNA binding protein | 81892 | ENSG00000119705 |
| 200  | ENSG00000205309 | NA | NT5M | 5',3'-nucleotidase, mitochondrial | 56953 | ENSG00000205309 |
| 201  | ENSG00000170906 | NA | NDUFA3 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa | 4696 | ENSG00000170906 |
| 202  | ENSG00000128654 | NA | MTX2 | metaxin 2 | 10651 | ENSG00000128654 |
| 203  | ENSG00000111716 | NA | LDHB | lactate dehydrogenase B | 3945 | ENSG00000111716 |
| 204  | ENSG00000112304 | NA | ACOT13 | acyl-CoA thioesterase 13 | 55856 | ENSG00000112304 |
| 205  | ENSG00000167283 | NA | ATP5L | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G | 10632 | ENSG00000167283 |
| 206  | ENSG00000114054 | NA | PCCB | propionyl CoA carboxylase, beta polypeptide | 5096 | ENSG00000114054 |
| 207  | ENSG00000069509 | NA | FUNDC1 | FUN14 domain containing 1 | 139341 | ENSG00000069509 |
| 208  | ENSG00000167799 | NA | NUDT8 | nudix (nucleoside diphosphate linked moiety X)-type motif 8 | 254552 | ENSG00000167799 |
| 209  | ENSG00000111275 | NA | ALDH2 | aldehyde dehydrogenase 2 family (mitochondrial) | 217 | ENSG00000111275 |
| 210  | ENSG00000171202 | NA | TMEM126A | transmembrane protein 126A | 84233 | ENSG00000171202 |
| 211  | ENSG00000124532 | NA | MRS2 | MRS2 magnesium homeostasis factor homolog (S. cerevisiae) | 57380 | ENSG00000124532 |
| 212  | ENSG00000136270 | NA | TBRG4 | transforming growth factor beta regulator 4 | 9238 | ENSG00000136270 |
| 213  | ENSG00000048544 | NA | MRPS10 | mitochondrial ribosomal protein S10 | 55173 | ENSG00000048544 |
| 214  | ENSG00000051620 | NA | HEBP2 | heme binding protein 2 | 23593 | ENSG00000051620 |
| 215  | ENSG00000131269 | NA | ABCB7 | ATP-binding cassette, sub-family B (MDR/TAP), member 7 | 22 | ENSG00000131269 |
| 216  | ENSG00000010256 | NA | UQCRC1 | ubiquinol-cytochrome c reductase core protein I | 7384 | ENSG00000010256 |
| 217  | ENSG00000137806 | NA | NDUFAF1 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 | 51103 | ENSG00000137806 |
| 218  | ENSG00000104823 | NA | ECH1 | enoyl CoA hydratase 1, peroxisomal | 1891 | ENSG00000104823 |
| 219  | ENSG00000197912 | NA | SPG7 | spastic paraplegia 7 (pure and complicated autosomal recessive) | 6687 | ENSG00000197912 |
| 220  | ENSG00000171503 | NA | ETFDH | electron-transferring-flavoprotein dehydrogenase | 2110 | ENSG00000171503 |
| 221  | ENSG00000138796 | NA | HADH | hydroxyacyl-CoA dehydrogenase | 3033 | ENSG00000138796 |
| 222  | ENSG00000165672 | NA | PRDX3 | peroxiredoxin 3 | 10935 | ENSG00000165672 |
| 223  | ENSG00000154518 | NA | ATP5G3 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C3 (subunit 9) | 518 | ENSG00000154518 |
| 224  | ENSG00000101132 | NA | PFDN4 | prefoldin subunit 4 | 5203 | ENSG00000101132 |
| 225  | ENSG00000088682 | NA | COQ9 | coenzyme Q9 homolog (S. cerevisiae) | 57017 | ENSG00000088682 |
| 226  | ENSG00000161533 | NA | ACOX1 | acyl-CoA oxidase 1, palmitoyl | 51 | ENSG00000161533 |
| 227  | ENSG00000075303 | NA | SLC25A40 | solute carrier family 25, member 40 | 55972 | ENSG00000075303 |
| 228  | ENSG00000155368 | NA | DBI | diazepam binding inhibitor (GABA receptor modulator, acyl-CoA binding protein) | 1622 | ENSG00000155368 |
| 229  | ENSG00000163382 | NA | APOA1BP | apolipoprotein A-I binding protein | 128240 | ENSG00000163382 |
| 230  | ENSG00000126768 | NA | TIMM17B | translocase of inner mitochondrial membrane 17 homolog B (yeast) | 10245 | ENSG00000126768 |
| 231  | ENSG00000154237 | NA | LRRK1 | leucine-rich repeat kinase 1 | 79705 | ENSG00000154237 |
| 232  | ENSG00000168653 | NA | NDUFS5 | NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) | 4725 | ENSG00000168653 |
| 233  | ENSG00000247077 | NA | PGAM5 | phosphoglycerate mutase family member 5 | 192111 | ENSG00000247077 |
| 234  | ENSG00000101019 | NA | UQCC | ubiquinol-cytochrome c reductase complex chaperone | 55245 | ENSG00000101019 |
| 235  | ENSG00000184903 | NA | IMMP2L | IMP2 inner mitochondrial membrane peptidase-like (S. cerevisiae) | 83943 | ENSG00000184903 |
| 236  | ENSG00000087299 | NA | L2HGDH | L-2-hydroxyglutarate dehydrogenase | 79944 | ENSG00000087299 |
| 237  | ENSG00000163864 | NA | NMNAT3 | nicotinamide nucleotide adenylyltransferase 3 | 349565 | ENSG00000163864 |
| 238  | ENSG00000136463 | NA | TACO1 | translational activator of mitochondrially encoded cytochrome c oxidase I | 51204 | ENSG00000136463 |
| 239  | ENSG00000156467 | NA | UQCRB | ubiquinol-cytochrome c reductase binding protein | 7381 | ENSG00000156467 |
| 240  | ENSG00000103316 | NA | CRYM | crystallin, mu | 1428 | ENSG00000103316 |
| 241  | ENSG00000184076 | NA | UQCR10 | ubiquinol-cytochrome c reductase, complex III subunit X | 29796 | ENSG00000184076 |
| 242  | ENSG00000123297 | NA | TSFM | Ts translation elongation factor, mitochondrial | 10102 | ENSG00000123297 |
| 243  | ENSG00000078070 | NA | MCCC1 | methylcrotonoyl-CoA carboxylase 1 (alpha) | 56922 | ENSG00000078070 |
| 244  | ENSG00000075415 | NA | SLC25A3 | solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 3 | 5250 | ENSG00000075415 |
| 245  | ENSG00000156885 | NA | COX6A2 | cytochrome c oxidase subunit VIa polypeptide 2 | 1339 | ENSG00000156885 |
| 246  | ENSG00000006695 | NA | COX10 | COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) | 1352 | ENSG00000006695 |
| 247  | ENSG00000154723 | NA | ATP5J | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 | 522 | ENSG00000154723 |
| 248  | ENSG00000133983 | NA | COX16 | COX16 cytochrome c oxidase assembly homolog (S. cerevisiae) | 51241 | ENSG00000133983 |
| 249  | ENSG00000167969 | NA | ECI1 | enoyl-CoA delta isomerase 1 | 1632 | ENSG00000167969 |
| 250  | ENSG00000115364 | NA | MRPL19 | mitochondrial ribosomal protein L19 | 9801 | ENSG00000115364 |
| 251  | ENSG00000123472 | NA | ATPAF1 | ATP synthase mitochondrial F1 complex assembly factor 1 | 64756 | ENSG00000123472 |
| 252  | ENSG00000105552 | NA | BCAT2 | branched chain amino-acid transaminase 2, mitochondrial | 587 | ENSG00000105552 |
| 253  | ENSG00000112996 | NA | MRPS30 | mitochondrial ribosomal protein S30 | 10884 | ENSG00000112996 |
| 254  | ENSG00000139531 | NA | SUOX | sulfite oxidase | 6821 | ENSG00000139531 |
| 255  | ENSG00000100347 | NA | SAMM50 | sorting and assembly machinery component 50 homolog (S. cerevisiae) | 25813 | ENSG00000100347 |
| 256  | ENSG00000125166 | NA | GOT2 | glutamic-oxaloacetic transaminase 2, mitochondrial (aspartate aminotransferase 2) | 2806 | ENSG00000125166 |
| 257  | ENSG00000161558 | NA | TMEM143 | transmembrane protein 143 | 55260 | ENSG00000161558 |
| 258  | ENSG00000140374 | NA | ETFA | electron-transfer-flavoprotein, alpha polypeptide | 2108 | ENSG00000140374 |
| 259  | ENSG00000140740 | NA | UQCRC2 | ubiquinol-cytochrome c reductase core protein II | 7385 | ENSG00000140740 |
| 260  | ENSG00000160194 | NA | NDUFV3 | NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa | 4731 | ENSG00000160194 |
| 261  | ENSG00000147684 | NA | NDUFB9 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa | 4715 | ENSG00000147684 |
| 262  | ENSG00000169599 | NA | NFU1 | NFU1 iron-sulfur cluster scaffold homolog (S. cerevisiae) | 27247 | ENSG00000169599 |
| 263  | ENSG00000184983 | NA | NDUFA6 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa | 4700 | ENSG00000184983 |
| 264  | ENSG00000102309 | NA | PIN4 | protein (peptidylprolyl cis/trans isomerase) NIMA-interacting, 4 (parvulin) | 5303 | ENSG00000102309 |
| 265  | ENSG00000163626 | NA | COX18 | COX18 cytochrome c oxidase assembly homolog (S. cerevisiae) | 285521 | ENSG00000163626 |
| 266  | ENSG00000158864 | NA | NDUFS2 | NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) | 4720 | ENSG00000158864 |
| 267  | ENSG00000173436 | NA | MINOS1 | mitochondrial inner membrane organizing system 1 | 440574 | ENSG00000173436 |
| 268  | ENSG00000105197 | NA | TIMM50 | translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae) | 92609 | ENSG00000105197 |
| 269  | ENSG00000135537 | NA | LACE1 | lactation elevated 1 | 246269 | ENSG00000135537 |
| 270  | ENSG00000116221 | NA | MRPL37 | mitochondrial ribosomal protein L37 | 51253 | ENSG00000116221 |
| 271  | ENSG00000142168 | NA | SOD1 | superoxide dismutase 1, soluble | 6647 | ENSG00000142168 |
| 272  | ENSG00000109519 | NA | GRPEL1 | GrpE-like 1, mitochondrial (E. coli) | 80273 | ENSG00000109519 |
| 273  | ENSG00000262814 | NA | MRPL12 | mitochondrial ribosomal protein L12 | 6182 | ENSG00000262814 |
| 274  | ENSG00000076043 | NA | REXO2 | REX2, RNA exonuclease 2 homolog (S. cerevisiae) | 25996 | ENSG00000076043 |
| 275  | ENSG00000096080 | NA | MRPS18A | mitochondrial ribosomal protein S18A | 55168 | ENSG00000096080 |
| 276  | ENSG00000069998 | NA | CECR5 | cat eye syndrome chromosome region, candidate 5 | 27440 | ENSG00000069998 |
| 277  | ENSG00000120254 | NA | MTHFD1L | methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 1-like | 25902 | ENSG00000120254 |
| 278  | ENSG00000134056 | NA | MRPS36 | mitochondrial ribosomal protein S36 | 92259 | ENSG00000134056 |
| 279  | ENSG00000119689 | NA | DLST | dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex) | 1743 | ENSG00000119689 |
| 280  | ENSG00000168291 | NA | PDHB | pyruvate dehydrogenase (lipoamide) beta | 5162 | ENSG00000168291 |
| 281  | ENSG00000156502 | NA | SUPV3L1 | suppressor of var1, 3-like 1 (S. cerevisiae) | 6832 | ENSG00000156502 |
| 282  | ENSG00000060762 | NA | MPC1 | mitochondrial pyruvate carrier 1 | 51660 | ENSG00000060762 |
| 283  | ENSG00000116459 | NA | ATP5F1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 | 515 | ENSG00000116459 |
| 284  | ENSG00000104980 | NA | TIMM44 | translocase of inner mitochondrial membrane 44 homolog (yeast) | 10469 | ENSG00000104980 |
| 285  | ENSG00000187145 | NA | MRPS21 | mitochondrial ribosomal protein S21 | 54460 | ENSG00000187145 |
| 286  | ENSG00000099800 | NA | TIMM13 | translocase of inner mitochondrial membrane 13 homolog (yeast) | 26517 | ENSG00000099800 |
| 287  | ENSG00000138399 | NA | FASTKD1 | FAST kinase domains 1 | 79675 | ENSG00000138399 |
| 288  | ENSG00000107951 | NA | MTPAP | mitochondrial poly(A) polymerase | 55149 | ENSG00000107951 |
| 289  | ENSG00000112992 | NA | NNT | nicotinamide nucleotide transhydrogenase | 23530 | ENSG00000112992 |
| 290  | ENSG00000067704 | NA | IARS2 | isoleucyl-tRNA synthetase 2, mitochondrial | 55699 | ENSG00000067704 |
| 291  | ENSG00000215251 | NA | FASTKD5 | FAST kinase domains 5 | 60493 | ENSG00000215251 |
| 292  | ENSG00000130348 | NA | QRSL1 | glutaminyl-tRNA synthase (glutamine-hydrolyzing)-like 1 | 55278 | ENSG00000130348 |
| 293  | ENSG00000148950 | NA | IMMP1L | IMP1 inner mitochondrial membrane peptidase-like (S. cerevisiae) | 196294 | ENSG00000148950 |
| 294  | ENSG00000119421 | NA | NDUFA8 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa | 4702 | ENSG00000119421 |
| 295  | ENSG00000170502 | NA | NUDT9 | nudix (nucleoside diphosphate linked moiety X)-type motif 9 | 53343 | ENSG00000170502 |
| 296  | ENSG00000137288 | NA | MNF1 | mitochondrial nucleoid factor 1 | 84300 | ENSG00000137288 |
| 297  | ENSG00000130347 | NA | RTN4IP1 | reticulon 4 interacting protein 1 | 84816 | ENSG00000130347 |
| 298  | ENSG00000172172 | NA | MRPL13 | mitochondrial ribosomal protein L13 | 28998 | ENSG00000172172 |
| 299  | ENSG00000244005 | NA | NFS1 | NFS1 nitrogen fixation 1 homolog (S. cerevisiae) | 9054 | ENSG00000244005 |
| 300  | ENSG00000126267 | NA | COX6B1 | cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) | 1340 | ENSG00000126267 |
| 301  | ENSG00000154814 | NA | OXNAD1 | oxidoreductase NAD-binding domain containing 1 | 92106 | ENSG00000154814 |
| 302  | ENSG00000103121 | NA | CMC2 | COX assembly mitochondrial protein 2 homolog (S. cerevisiae) | 56942 | ENSG00000103121 |
| 303  | ENSG00000148450 | NA | MSRB2 | methionine sulfoxide reductase B2 | 22921 | ENSG00000148450 |
| 304  | ENSG00000170791 | NA | CHCHD7 | coiled-coil-helix-coiled-coil-helix domain containing 7 | 79145 | ENSG00000170791 |
| 305  | ENSG00000215021 | NA | PHB2 | prohibitin 2 | 11331 | ENSG00000215021 |
| 306  | ENSG00000145494 | NA | NDUFS6 | NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) | 4726 | ENSG00000145494 |
| 307  | ENSG00000167085 | NA | PHB | prohibitin | 5245 | ENSG00000167085 |
| 308  | ENSG00000072506 | NA | HSD17B10 | hydroxysteroid (17-beta) dehydrogenase 10 | 3028 | ENSG00000072506 |
| 309  | ENSG00000106153 | NA | CHCHD2 | coiled-coil-helix-coiled-coil-helix domain containing 2 | 51142 | ENSG00000106153 |
| 310  | ENSG00000131143 | NA | COX4I1 | cytochrome c oxidase subunit IV isoform 1 | 1327 | ENSG00000131143 |
| 311  | ENSG00000196236 | NA | XPNPEP3 | X-prolyl aminopeptidase (aminopeptidase P) 3, putative | 63929 | ENSG00000196236 |
| 312  | ENSG00000136444 | NA | RSAD1 | radical S-adenosyl methionine domain containing 1 | 55316 | ENSG00000136444 |
| 313  | ENSG00000108561 | NA | C1QBP | complement component 1, q subcomponent binding protein | 708 | ENSG00000108561 |
| 314  | ENSG00000105379 | NA | ETFB | electron-transfer-flavoprotein, beta polypeptide | 2109 | ENSG00000105379 |
| 315  | ENSG00000213995 | NA | CARKD | carbohydrate kinase domain containing | 55739 | ENSG00000213995 |
| 316  | ENSG00000090266 | NA | NDUFB2 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa | 4708 | ENSG00000090266 |
| 317  | ENSG00000230055 | NA | CISD3 | CDGSH iron sulfur domain 3 | 284106 | ENSG00000230055 |
| 318  | ENSG00000175581 | NA | MRPL48 | mitochondrial ribosomal protein L48 | 51642 | ENSG00000175581 |
| 319  | ENSG00000151498 | NA | ACAD8 | acyl-CoA dehydrogenase family, member 8 | 27034 | ENSG00000151498 |
| 320  | ENSG00000156928 | NA | MALSU1 | mitochondrial assembly of ribosomal large subunit 1 | 115416 | ENSG00000156928 |
| 321  | ENSG00000136143 | NA | SUCLA2 | succinate-CoA ligase, ADP-forming, beta subunit | 8803 | ENSG00000136143 |
| 322  | ENSG00000159199 | NA | ATP5G1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) | 516 | ENSG00000159199 |
| 323  | ENSG00000166855 | NA | CLPX | ClpX caseinolytic peptidase X homolog (E. coli) | 10845 | ENSG00000166855 |
| 324  | ENSG00000090263 | NA | MRPS33 | mitochondrial ribosomal protein S33 | 51650 | ENSG00000090263 |
| 325  | ENSG00000155906 | NA | RMND1 | required for meiotic nuclear division 1 homolog (S. cerevisiae) | 55005 | ENSG00000155906 |
| 326  | ENSG00000166321 | NA | NUDT13 | nudix (nucleoside diphosphate linked moiety X)-type motif 13 | 25961 | ENSG00000166321 |
| 327  | ENSG00000130159 | NA | ECSIT | ECSIT homolog (Drosophila) | 51295 | ENSG00000130159 |
| 328  | ENSG00000074582 | NA | BCS1L | BCS1-like (S. cerevisiae) | 617 | ENSG00000074582 |
| 329  | ENSG00000122033 | NA | MTIF3 | mitochondrial translational initiation factor 3 | 219402 | ENSG00000122033 |
| 330  | ENSG00000116171 | NA | SCP2 | sterol carrier protein 2 | 6342 | ENSG00000116171 |
| 331  | ENSG00000104412 | NA | EMC2 | ER membrane protein complex subunit 2 | 9694 | ENSG00000104412 |
| 332  | ENSG00000114383 | NA | TUSC2 | tumor suppressor candidate 2 | 11334 | ENSG00000114383 |
| 333  | ENSG00000172590 | NA | MRPL52 | mitochondrial ribosomal protein L52 | 122704 | ENSG00000172590 |
| 334  | ENSG00000140009 | NA | ESR2 | estrogen receptor 2 (ER beta) | 2100 | ENSG00000140009 |
| 335  | ENSG00000103018 | NA | CYB5B | cytochrome b5 type B (outer mitochondrial membrane) | 80777 | ENSG00000103018 |
| 336  | ENSG00000174917 | NA | C19orf70 | chromosome 19 open reading frame 70 | 125988 | ENSG00000174917 |
| 337  | ENSG00000166816 | NA | LDHD | lactate dehydrogenase D | 197257 | ENSG00000166816 |
| 338  | ENSG00000143374 | NA | TARS2 | threonyl-tRNA synthetase 2, mitochondrial (putative) | 80222 | ENSG00000143374 |
| 339  | ENSG00000013275 | NA | PSMC4 | proteasome (prosome, macropain) 26S subunit, ATPase, 4 | 5704 | ENSG00000013275 |
| 340  | ENSG00000132313 | NA | MRPL35 | mitochondrial ribosomal protein L35 | 51318 | ENSG00000132313 |
| 341  | ENSG00000066926 | NA | FECH | ferrochelatase | 2235 | ENSG00000066926 |
| 342  | ENSG00000131779 | NA | PEX11B | peroxisomal biogenesis factor 11 beta | 8799 | ENSG00000131779 |
| 343  | ENSG00000138495 | NA | COX17 | COX17 cytochrome c oxidase assembly homolog (S. cerevisiae) | 10063 | ENSG00000138495 |
| 344  | ENSG00000117118 | NA | SDHB | succinate dehydrogenase complex, subunit B, iron sulfur (Ip) | 6390 | ENSG00000117118 |
| 345  | ENSG00000171953 | NA | ATPAF2 | ATP synthase mitochondrial F1 complex assembly factor 2 | 91647 | ENSG00000171953 |
| 346  | ENSG00000168827 | NA | GFM1 | G elongation factor, mitochondrial 1 | 85476 | ENSG00000168827 |
| 347  | ENSG00000135469 | NA | COQ10A | coenzyme Q10 homolog A (S. cerevisiae) | 93058 | ENSG00000135469 |
| 348  | ENSG00000177427 | NA | SMCR7 | Smith-Magenis syndrome chromosome region, candidate 7 | 125170 | ENSG00000177427 |
| 349  | ENSG00000115944 | NA | COX7A2L | cytochrome c oxidase subunit VIIa polypeptide 2 like | 9167 | ENSG00000115944 |
| 350  | ENSG00000039560 | NA | RAI14 | retinoic acid induced 14 | 26064 | ENSG00000039560 |
| 351  | ENSG00000100294 | NA | MCAT | malonyl CoA:ACP acyltransferase (mitochondrial) | 27349 | ENSG00000100294 |
| 352  | ENSG00000197150 | NA | ABCB8 | ATP-binding cassette, sub-family B (MDR/TAP), member 8 | 11194 | ENSG00000197150 |
| 353  | ENSG00000152234 | NA | ATP5A1 | ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle | 498 | ENSG00000152234 |
| 354  | ENSG00000146729 | NA | GBAS | glioblastoma amplified sequence | 2631 | ENSG00000146729 |
| 355  | ENSG00000164494 | NA | PDSS2 | prenyl (decaprenyl) diphosphate synthase, subunit 2 | 57107 | ENSG00000164494 |
| 356  | ENSG00000132763 | NA | MMACHC | methylmalonic aciduria (cobalamin deficiency) cblC type, with homocystinuria | 25974 | ENSG00000132763 |
| 357  | ENSG00000128609 | NA | NDUFA5 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa | 4698 | ENSG00000128609 |
| 358  | ENSG00000151366 | NA | NDUFC2 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa | 4718 | ENSG00000151366 |
| 359  | ENSG00000132305 | NA | IMMT | inner membrane protein, mitochondrial | 10989 | ENSG00000132305 |
| 360  | ENSG00000163541 | NA | SUCLG1 | succinate-CoA ligase, alpha subunit | 8802 | ENSG00000163541 |
| 361  | ENSG00000090432 | NA | MUL1 | mitochondrial E3 ubiquitin protein ligase 1 | 79594 | ENSG00000090432 |
| 362  | ENSG00000165678 | NA | GHITM | growth hormone inducible transmembrane protein | 27069 | ENSG00000165678 |
| 363  | ENSG00000154719 | NA | MRPL39 | mitochondrial ribosomal protein L39 | 54148 | ENSG00000154719 |
| 364  | ENSG00000146701 | NA | MDH2 | malate dehydrogenase 2, NAD (mitochondrial) | 4191 | ENSG00000146701 |
| 365  | ENSG00000173915 | NA | USMG5 | up-regulated during skeletal muscle growth 5 homolog (mouse) | 84833 | ENSG00000173915 |
| 366  | ENSG00000131730 | NA | CKMT2 | creatine kinase, mitochondrial 2 (sarcomeric) | 1160 | ENSG00000131730 |
| 367  | ENSG00000158882 | NA | TOMM40L | translocase of outer mitochondrial membrane 40 homolog (yeast)-like | 84134 | ENSG00000158882 |
| 368  | ENSG00000164038 | NA | SLC9B2 | solute carrier family 9, subfamily B (NHA2, cation proton antiporter 2), member 2 | 133308 | ENSG00000164038 |
| 369  | ENSG00000147123 | NA | NDUFB11 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa | 54539 | ENSG00000147123 |
| 370  | ENSG00000137714 | NA | FDX1 | ferredoxin 1 | 2230 | ENSG00000137714 |
| 371  | ENSG00000169021 | NA | UQCRFS1 | ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 | 7386 | ENSG00000169021 |
| 372  | ENSG00000115652 | NA | UXS1 | UDP-glucuronate decarboxylase 1 | 80146 | ENSG00000115652 |
| 373  | ENSG00000136897 | NA | MRPL50 | mitochondrial ribosomal protein L50 | 54534 | ENSG00000136897 |
| 374  | ENSG00000132541 | NA | HRSP12 | heat-responsive protein 12 | 10247 | ENSG00000132541 |
| 375  | ENSG00000124523 | NA | SIRT5 | sirtuin 5 | 23408 | ENSG00000124523 |
| 376  | ENSG00000102738 | NA | MRPS31 | mitochondrial ribosomal protein S31 | 10240 | ENSG00000102738 |
| 377  | ENSG00000178449 | NA | COX14 | COX14 cytochrome c oxidase assembly homolog (S. cerevisiae) | 84987 | ENSG00000178449 |
| 378  | ENSG00000145439 | NA | CBR4 | carbonyl reductase 4 | 84869 | ENSG00000145439 |
| 379  | ENSG00000130312 | NA | MRPL34 | mitochondrial ribosomal protein L34 | 64981 | ENSG00000130312 |
| 380  | ENSG00000132300 | NA | PTCD3 | pentatricopeptide repeat domain 3 | 55037 | ENSG00000132300 |
| 381  | ENSG00000062485 | NA | CS | citrate synthase | 1431 | ENSG00000062485 |
| 382  | ENSG00000175193 | NA | PARL | presenilin associated, rhomboid-like | 55486 | ENSG00000175193 |
| 383  | ENSG00000111843 | NA | TMEM14C | transmembrane protein 14C | 51522 | ENSG00000111843 |
| 384  | ENSG00000139428 | NA | MMAB | methylmalonic aciduria (cobalamin deficiency) cblB type | 326625 | ENSG00000139428 |
| 385  | ENSG00000185973 | NA | TMLHE | trimethyllysine hydroxylase, epsilon | 55217 | ENSG00000185973 |
| 386  | ENSG00000124370 | NA | MCEE | methylmalonyl CoA epimerase | 84693 | ENSG00000124370 |
| 387  | ENSG00000162600 | NA | OMA1 | OMA1 zinc metallopeptidase homolog (S. cerevisiae) | 115209 | ENSG00000162600 |
| 388  | ENSG00000108179 | NA | PPIF | peptidylprolyl isomerase F | 10105 | ENSG00000108179 |
| 389  | ENSG00000137513 | NA | NARS2 | asparaginyl-tRNA synthetase 2, mitochondrial (putative) | 79731 | ENSG00000137513 |
| 390  | ENSG00000137133 | NA | HINT2 | histidine triad nucleotide binding protein 2 | 84681 | ENSG00000137133 |
| 391  | ENSG00000111639 | NA | MRPL51 | mitochondrial ribosomal protein L51 | 51258 | ENSG00000111639 |
| 392  | ENSG00000164405 | NA | UQCRQ | ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa | 27089 | ENSG00000164405 |
| 393  | ENSG00000168569 | NA | TMEM223 | transmembrane protein 223 | 79064 | ENSG00000168569 |
| 394  | ENSG00000122729 | NA | ACO1 | aconitase 1, soluble | 48 | ENSG00000122729 |
| 395  | ENSG00000173085 | NA | COQ2 | coenzyme Q2 homolog, prenyltransferase (yeast) | 27235 | ENSG00000173085 |
| 396  | ENSG00000148187 | NA | MRRF | mitochondrial ribosome recycling factor | 92399 | ENSG00000148187 |
| 397  | ENSG00000061794 | NA | MRPS35 | mitochondrial ribosomal protein S35 | 60488 | ENSG00000061794 |
| 398  | ENSG00000124172 | NA | ATP5E | ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit | 514 | ENSG00000124172 |
| 399  | ENSG00000183648 | NA | NDUFB1 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa | 4707 | ENSG00000183648 |
| 400  | ENSG00000132591 | NA | ERAL1 | Era G-protein-like 1 (E. coli) | 26284 | ENSG00000132591 |
| 401  | ENSG00000205981 | NA | DNAJC19 | DnaJ (Hsp40) homolog, subfamily C, member 19 | 131118 | ENSG00000205981 |
| 402  | ENSG00000213585 | NA | VDAC1 | voltage-dependent anion channel 1 | 7416 | ENSG00000213585 |
| 403  | ENSG00000120333 | NA | MRPS14 | mitochondrial ribosomal protein S14 | 63931 | ENSG00000120333 |
| 404  | ENSG00000110435 | NA | PDHX | pyruvate dehydrogenase complex, component X | 8050 | ENSG00000110435 |
| 405  | ENSG00000184857 | NA | TMEM186 | transmembrane protein 186 | 25880 | ENSG00000184857 |
| 406  | ENSG00000099624 | NA | ATP5D | ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit | 513 | ENSG00000099624 |
| 407  | ENSG00000100412 | NA | ACO2 | aconitase 2, mitochondrial | 50 | ENSG00000100412 |
| 408  | ENSG00000112651 | NA | MRPL2 | mitochondrial ribosomal protein L2 | 51069 | ENSG00000112651 |
| 409  | ENSG00000132676 | NA | DAP3 | death associated protein 3 | 7818 | ENSG00000132676 |
| 410  | ENSG00000164051 | NA | CCDC51 | coiled-coil domain containing 51 | 79714 | ENSG00000164051 |
| 411  | ENSG00000181610 | NA | MRPS23 | mitochondrial ribosomal protein S23 | 51649 | ENSG00000181610 |
| 412  | ENSG00000213563 | NA | C8orf82 | chromosome 8 open reading frame 82 | 414919 | ENSG00000213563 |
| 413  | ENSG00000172586 | NA | CHCHD1 | coiled-coil-helix-coiled-coil-helix domain containing 1 | 118487 | ENSG00000172586 |
| 414  | ENSG00000164896 | NA | FASTK | Fas-activated serine/threonine kinase | 10922 | ENSG00000164896 |
| 415  | ENSG00000125356 | NA | NDUFA1 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa | 4694 | ENSG00000125356 |
| 416  | ENSG00000107020 | NA | PLGRKT | plasminogen receptor, C-terminal lysine transmembrane protein | 55848 | ENSG00000107020 |
| 417  | ENSG00000108528 | NA | SLC25A11 | solute carrier family 25 (mitochondrial carrier; oxoglutarate carrier), member 11 | 8402 | ENSG00000108528 |
| 418  | ENSG00000129282 | NA | MRM1 | mitochondrial rRNA methyltransferase 1 homolog (S. cerevisiae) | 79922 | ENSG00000129282 |
| 419  | ENSG00000119673 | NA | ACOT2 | acyl-CoA thioesterase 2 | 10965 | ENSG00000119673 |
| 420  | ENSG00000176422 | NA | SPRYD4 | SPRY domain containing 4 | 283377 | ENSG00000176422 |
| 421  | ENSG00000099795 | NA | NDUFB7 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa | 4713 | ENSG00000099795 |
| 422  | ENSG00000180185 | NA | FAHD1 | fumarylacetoacetate hydrolase domain containing 1 | 81889 | ENSG00000180185 |
| 423  | ENSG00000044459 | NA | CNTLN | centlein, centrosomal protein | 54875 | ENSG00000044459 |
| 424  | ENSG00000103507 | NA | BCKDK | branched chain ketoacid dehydrogenase kinase | 10295 | ENSG00000103507 |
| 425  | ENSG00000148090 | NA | AUH | AU RNA binding protein/enoyl-CoA hydratase | 549 | ENSG00000148090 |
| 426  | ENSG00000198015 | NA | MRPL42 | mitochondrial ribosomal protein L42 | 28977 | ENSG00000198015 |
| 427  | ENSG00000127989 | NA | MTERF | mitochondrial transcription termination factor | 7978 | ENSG00000127989 |
| 428  | ENSG00000125901 | NA | MRPS26 | mitochondrial ribosomal protein S26 | 64949 | ENSG00000125901 |
| 429  | ENSG00000167136 | NA | ENDOG | endonuclease G | 2021 | ENSG00000167136 |
| 430  | ENSG00000075336 | NA | TIMM21 | translocase of inner mitochondrial membrane 21 homolog (yeast) | 29090 | ENSG00000075336 |
| 431  | ENSG00000133943 | NA | C14orf159 | chromosome 14 open reading frame 159 | 80017 | ENSG00000133943 |
| 432  | ENSG00000172270 | NA | BSG | basigin (Ok blood group) | 682 | ENSG00000172270 |
| 433  | ENSG00000250479 | NA | CHCHD10 | coiled-coil-helix-coiled-coil-helix domain containing 10 | 400916 | ENSG00000250479 |
| 434  | ENSG00000074071 | NA | MRPS34 | mitochondrial ribosomal protein S34 | 65993 | ENSG00000074071 |
| 435  | ENSG00000164347 | NA | GFM2 | G elongation factor, mitochondrial 2 | 84340 | ENSG00000164347 |
| 436  | ENSG00000111906 | NA | HDDC2 | HD domain containing 2 | 51020 | ENSG00000111906 |
| 437  | ENSG00000119723 | NA | COQ6 | coenzyme Q6 homolog, monooxygenase (S. cerevisiae) | 51004 | ENSG00000119723 |
| 438  | ENSG00000181991 | NA | MRPS11 | mitochondrial ribosomal protein S11 | 64963 | ENSG00000181991 |
| 439  | ENSG00000197894 | NA | ADH5 | alcohol dehydrogenase 5 (class III), chi polypeptide | 128 | ENSG00000197894 |
| 440  | ENSG00000175110 | NA | MRPS22 | mitochondrial ribosomal protein S22 | 56945 | ENSG00000175110 |
| 441  | ENSG00000197448 | NA | GSTK1 | glutathione S-transferase kappa 1 | 373156 | ENSG00000197448 |
| 442  | ENSG00000167792 | NA | NDUFV1 | NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa | 4723 | ENSG00000167792 |
| 443  | ENSG00000110717 | NA | NDUFS8 | NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) | 4728 | ENSG00000110717 |
| 444  | ENSG00000174547 | NA | MRPL11 | mitochondrial ribosomal protein L11 | 65003 | ENSG00000174547 |
| 445  | ENSG00000137547 | NA | MRPL15 | mitochondrial ribosomal protein L15 | 29088 | ENSG00000137547 |
| 446  | ENSG00000204308 | NA | RNF5 | ring finger protein 5, E3 ubiquitin protein ligase | 6048 | ENSG00000204308 |
| 447  | ENSG00000162972 | NA | C2orf47 | chromosome 2 open reading frame 47 | 79568 | ENSG00000162972 |
| 448  | ENSG00000183978 | NA | COA3 | cytochrome C oxidase assembly factor 3 | 28958 | ENSG00000183978 |
| 449  | ENSG00000121361 | NA | KCNJ8 | potassium inwardly-rectifying channel, subfamily J, member 8 | 3764 | ENSG00000121361 |
| 450  | ENSG00000113845 | NA | TIMMDC1 | translocase of inner mitochondrial membrane domain containing 1 | 51300 | ENSG00000113845 |
| 451  | ENSG00000127884 | NA | ECHS1 | enoyl CoA hydratase, short chain, 1, mitochondrial | 1892 | ENSG00000127884 |
| 452  | ENSG00000178952 | NA | TUFM | Tu translation elongation factor, mitochondrial | 7284 | ENSG00000178952 |
| 453  | ENSG00000241468 | NA | ATP5J2 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 | 9551 | ENSG00000241468 |
| 454  | ENSG00000168273 | NA | C3orf78 | chromosome 3 open reading frame 78 | 440957 | ENSG00000168273 |
| 455  | ENSG00000125445 | NA | MRPS7 | mitochondrial ribosomal protein S7 | 51081 | ENSG00000125445 |
| 456  | ENSG00000105364 | NA | MRPL4 | mitochondrial ribosomal protein L4 | 51073 | ENSG00000105364 |
| 457  | ENSG00000143158 | NA | MPC2 | mitochondrial pyruvate carrier 2 | 25874 | ENSG00000143158 |
| 458  | ENSG00000113013 | NA | HSPA9 | heat shock 70kDa protein 9 (mortalin) | 3313 | ENSG00000113013 |
| 459  | ENSG00000110011 | NA | DNAJC4 | DnaJ (Hsp40) homolog, subfamily C, member 4 | 3338 | ENSG00000110011 |
| 460  | ENSG00000176340 | NA | COX8A | cytochrome c oxidase subunit VIIIA (ubiquitous) | 1351 | ENSG00000176340 |
| 461  | ENSG00000144029 | NA | MRPS5 | mitochondrial ribosomal protein S5 | 64969 | ENSG00000144029 |
| 462  | ENSG00000101247 | NA | NDUFAF5 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 5 | 79133 | ENSG00000101247 |
| 463  | ENSG00000050393 | NA | CCDC90A | coiled-coil domain containing 90A | 63933 | ENSG00000050393 |
| 464  | ENSG00000101365 | NA | IDH3B | isocitrate dehydrogenase 3 (NAD+) beta | 3420 | ENSG00000101365 |
| 465  | ENSG00000241837 | NA | ATP5O | ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit | 539 | ENSG00000241837 |
| 466  | ENSG00000140905 | NA | GCSH | glycine cleavage system protein H (aminomethyl carrier) | 2653 | ENSG00000140905 |
| 467  | ENSG00000214026 | NA | MRPL23 | mitochondrial ribosomal protein L23 | 6150 | ENSG00000214026 |
| 468  | ENSG00000158793 | NA | NIT1 | nitrilase 1 | 4817 | ENSG00000158793 |
| Database:cellular component       Name:mitochondrial part       ID:GO:0044429 | ||||||
|---|---|---|---|---|---|---|
| C=744; O=281; E=45.16; R=6.22; rawP=1.45e-156; adjP=2.87e-154 | ||||||
| Index | UserID | Value | Gene Symbol | Gene Name | EntrezGene | Ensembl |
| 1  | ENSG00000165264 | NA | NDUFB6 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa | 4712 | ENSG00000165264 |
| 2  | ENSG00000116898 | NA | MRPS15 | mitochondrial ribosomal protein S15 | 64960 | ENSG00000116898 |
| 3  | ENSG00000161281 | NA | COX7A1 | cytochrome c oxidase subunit VIIa polypeptide 1 (muscle) | 1346 | ENSG00000161281 |
| 4  | ENSG00000167862 | NA | ICT1 | immature colon carcinoma transcript 1 | 3396 | ENSG00000167862 |
| 5  | ENSG00000148672 | NA | GLUD1 | glutamate dehydrogenase 1 | 2746 | ENSG00000148672 |
| 6  | ENSG00000135390 | NA | ATP5G2 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C2 (subunit 9) | 517 | ENSG00000135390 |
| 7  | ENSG00000177370 | NA | TIMM22 | translocase of inner mitochondrial membrane 22 homolog (yeast) | 29928 | ENSG00000177370 |
| 8  | ENSG00000166136 | NA | NDUFB8 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa | 4714 | ENSG00000166136 |
| 9  | ENSG00000172340 | NA | SUCLG2 | succinate-CoA ligase, GDP-forming, beta subunit | 8801 | ENSG00000172340 |
| 10  | ENSG00000091140 | NA | DLD | dihydrolipoamide dehydrogenase | 1738 | ENSG00000091140 |
| 11  | ENSG00000130414 | NA | NDUFA10 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa | 4705 | ENSG00000130414 |
| 12  | ENSG00000165060 | NA | FXN | frataxin | 2395 | ENSG00000165060 |
| 13  | ENSG00000007923 | NA | DNAJC11 | DnaJ (Hsp40) homolog, subfamily C, member 11 | 55735 | ENSG00000007923 |
| 14  | ENSG00000173141 | NA | MRP63 | mitochondrial ribosomal protein 63 | 78988 | ENSG00000173141 |
| 15  | ENSG00000131828 | NA | PDHA1 | pyruvate dehydrogenase (lipoamide) alpha 1 | 5160 | ENSG00000131828 |
| 16  | ENSG00000122971 | NA | ACADS | acyl-CoA dehydrogenase, C-2 to C-3 short chain | 35 | ENSG00000122971 |
| 17  | ENSG00000103356 | NA | EARS2 | glutamyl-tRNA synthetase 2, mitochondrial (putative) | 124454 | ENSG00000103356 |
| 18  | ENSG00000109390 | NA | NDUFC1 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa | 4717 | ENSG00000109390 |
| 19  | ENSG00000091483 | NA | FH | fumarate hydratase | 2271 | ENSG00000091483 |
| 20  | ENSG00000055950 | NA | MRPL43 | mitochondrial ribosomal protein L43 | 84545 | ENSG00000055950 |
| 21  | ENSG00000142082 | NA | SIRT3 | sirtuin 3 | 23410 | ENSG00000142082 |
| 22  | ENSG00000204568 | NA | MRPS18B | mitochondrial ribosomal protein S18B | 28973 | ENSG00000204568 |
| 23  | ENSG00000165283 | NA | STOML2 | stomatin (EPB72)-like 2 | 30968 | ENSG00000165283 |
| 24  | ENSG00000164466 | NA | SFXN1 | sideroflexin 1 | 94081 | ENSG00000164466 |
| 25  | ENSG00000151729 | NA | SLC25A4 | solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4 | 291 | ENSG00000151729 |
| 26  | ENSG00000178057 | NA | NDUFAF3 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 3 | 25915 | ENSG00000178057 |
| 27  | ENSG00000023330 | NA | ALAS1 | aminolevulinate, delta-, synthase 1 | 211 | ENSG00000023330 |
| 28  | ENSG00000213619 | NA | NDUFS3 | NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) | 4722 | ENSG00000213619 |
| 29  | ENSG00000178741 | NA | COX5A | cytochrome c oxidase subunit Va | 9377 | ENSG00000178741 |
| 30  | ENSG00000173660 | NA | UQCRH | ubiquinol-cytochrome c reductase hinge protein | 7388 | ENSG00000173660 |
| 31  | ENSG00000214253 | NA | FIS1 | fission 1 (mitochondrial outer membrane) homolog (S. cerevisiae) | 51024 | ENSG00000214253 |
| 32  | ENSG00000147586 | NA | MRPS28 | mitochondrial ribosomal protein S28 | 28957 | ENSG00000147586 |
| 33  | ENSG00000133028 | NA | SCO1 | SCO cytochrome oxidase deficient homolog 1 (yeast) | 6341 | ENSG00000133028 |
| 34  | ENSG00000109919 | NA | MTCH2 | mitochondrial carrier 2 | 23788 | ENSG00000109919 |
| 35  | ENSG00000135940 | NA | COX5B | cytochrome c oxidase subunit Vb | 1329 | ENSG00000135940 |
| 36  | ENSG00000029639 | NA | TFB1M | transcription factor B1, mitochondrial | 51106 | ENSG00000029639 |
| 37  | ENSG00000143436 | NA | MRPL9 | mitochondrial ribosomal protein L9 | 65005 | ENSG00000143436 |
| 38  | ENSG00000239789 | NA | MRPS17 | mitochondrial ribosomal protein S17 | 51373 | ENSG00000239789 |
| 39  | ENSG00000162851 | NA | TFB2M | transcription factor B2, mitochondrial | 64216 | ENSG00000162851 |
| 40  | ENSG00000156709 | NA | AIFM1 | apoptosis-inducing factor, mitochondrion-associated, 1 | 9131 | ENSG00000156709 |
| 41  | ENSG00000189043 | NA | NDUFA4 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa | 4697 | ENSG00000189043 |
| 42  | ENSG00000172115 | NA | CYCS | cytochrome c, somatic | 54205 | ENSG00000172115 |
| 43  | ENSG00000164919 | NA | COX6C | cytochrome c oxidase subunit VIc | 1345 | ENSG00000164919 |
| 44  | ENSG00000139131 | NA | YARS2 | tyrosyl-tRNA synthetase 2, mitochondrial | 51067 | ENSG00000139131 |
| 45  | ENSG00000115286 | NA | NDUFS7 | NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) | 374291 | ENSG00000115286 |
| 46  | ENSG00000164258 | NA | NDUFS4 | NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) | 4724 | ENSG00000164258 |
| 47  | ENSG00000156170 | NA | NDUFAF6 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 | 137682 | ENSG00000156170 |
| 48  | ENSG00000155463 | NA | OXA1L | oxidase (cytochrome c) assembly 1-like | 5018 | ENSG00000155463 |
| 49  | ENSG00000167863 | NA | ATP5H | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d | 10476 | ENSG00000167863 |
| 50  | ENSG00000163319 | NA | MRPS18C | mitochondrial ribosomal protein S18C | 51023 | ENSG00000163319 |
| 51  | ENSG00000179091 | NA | CYC1 | cytochrome c-1 | 1537 | ENSG00000179091 |
| 52  | ENSG00000185608 | NA | MRPL40 | mitochondrial ribosomal protein L40 | 64976 | ENSG00000185608 |
| 53  | ENSG00000127540 | NA | UQCR11 | ubiquinol-cytochrome c reductase, complex III subunit XI | 10975 | ENSG00000127540 |
| 54  | ENSG00000184752 | NA | NDUFA12 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 | 55967 | ENSG00000184752 |
| 55  | ENSG00000132423 | NA | COQ3 | coenzyme Q3 homolog, methyltransferase (S. cerevisiae) | 51805 | ENSG00000132423 |
| 56  | ENSG00000156411 | NA | C14orf2 | chromosome 14 open reading frame 2 | 9556 | ENSG00000156411 |
| 57  | ENSG00000131844 | NA | MCCC2 | methylcrotonoyl-CoA carboxylase 2 (beta) | 64087 | ENSG00000131844 |
| 58  | ENSG00000134905 | NA | CARS2 | cysteinyl-tRNA synthetase 2, mitochondrial (putative) | 79587 | ENSG00000134905 |
| 59  | ENSG00000182810 | NA | DDX28 | DEAD (Asp-Glu-Ala-Asp) box polypeptide 28 | 55794 | ENSG00000182810 |
| 60  | ENSG00000105819 | NA | PMPCB | peptidase (mitochondrial processing) beta | 9512 | ENSG00000105819 |
| 61  | ENSG00000150779 | NA | TIMM8B | translocase of inner mitochondrial membrane 8 homolog B (yeast) | 26521 | ENSG00000150779 |
| 62  | ENSG00000204228 | NA | HSD17B8 | hydroxysteroid (17-beta) dehydrogenase 8 | 7923 | ENSG00000204228 |
| 63  | ENSG00000196683 | NA | TOMM7 | translocase of outer mitochondrial membrane 7 homolog (yeast) | 54543 | ENSG00000196683 |
| 64  | ENSG00000175198 | NA | PCCA | propionyl CoA carboxylase, alpha polypeptide | 5095 | ENSG00000175198 |
| 65  | ENSG00000067829 | NA | IDH3G | isocitrate dehydrogenase 3 (NAD+) gamma | 3421 | ENSG00000067829 |
| 66  | ENSG00000140990 | NA | NDUFB10 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa | 4716 | ENSG00000140990 |
| 67  | ENSG00000198523 | NA | PLN | phospholamban | 5350 | ENSG00000198523 |
| 68  | ENSG00000006530 | NA | AGK | acylglycerol kinase | 55750 | ENSG00000006530 |
| 69  | ENSG00000247626 | NA | MARS2 | methionyl-tRNA synthetase 2, mitochondrial | 92935 | ENSG00000247626 |
| 70  | ENSG00000165629 | NA | ATP5C1 | ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 | 509 | ENSG00000165629 |
| 71  | ENSG00000123545 | NA | NDUFAF4 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 4 | 29078 | ENSG00000123545 |
| 72  | ENSG00000148290 | NA | SURF1 | surfeit 1 | 6834 | ENSG00000148290 |
| 73  | ENSG00000072778 | NA | ACADVL | acyl-CoA dehydrogenase, very long chain | 37 | ENSG00000072778 |
| 74  | ENSG00000154930 | NA | ACSS1 | acyl-CoA synthetase short-chain family member 1 | 84532 | ENSG00000154930 |
| 75  | ENSG00000196636 | NA | ACN9 | ACN9 homolog (S. cerevisiae) | 57001 | ENSG00000196636 |
| 76  | ENSG00000125995 | NA | ROMO1 | reactive oxygen species modulator 1 | 140823 | ENSG00000125995 |
| 77  | ENSG00000136521 | NA | NDUFB5 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa | 4711 | ENSG00000136521 |
| 78  | ENSG00000169020 | NA | ATP5I | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E | 521 | ENSG00000169020 |
| 79  | ENSG00000182054 | NA | IDH2 | isocitrate dehydrogenase 2 (NADP+), mitochondrial | 3418 | ENSG00000182054 |
| 80  | ENSG00000004779 | NA | NDUFAB1 | NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa | 4706 | ENSG00000004779 |
| 81  | ENSG00000168958 | NA | MFF | mitochondrial fission factor | 56947 | ENSG00000168958 |
| 82  | ENSG00000004961 | NA | HCCS | holocytochrome c synthase | 3052 | ENSG00000004961 |
| 83  | ENSG00000073578 | NA | SDHA | succinate dehydrogenase complex, subunit A, flavoprotein (Fp) | 6389 | ENSG00000073578 |
| 84  | ENSG00000119013 | NA | NDUFB3 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa | 4709 | ENSG00000119013 |
| 85  | ENSG00000104325 | NA | DECR1 | 2,4-dienoyl CoA reductase 1, mitochondrial | 1666 | ENSG00000104325 |
| 86  | ENSG00000078668 | NA | VDAC3 | voltage-dependent anion channel 3 | 7419 | ENSG00000078668 |
| 87  | ENSG00000182154 | NA | MRPL41 | mitochondrial ribosomal protein L41 | 64975 | ENSG00000182154 |
| 88  | ENSG00000139180 | NA | NDUFA9 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa | 4704 | ENSG00000139180 |
| 89  | ENSG00000127184 | NA | COX7C | cytochrome c oxidase subunit VIIc | 1350 | ENSG00000127184 |
| 90  | ENSG00000165637 | NA | VDAC2 | voltage-dependent anion channel 2 | 7417 | ENSG00000165637 |
| 91  | ENSG00000204370 | NA | SDHD | succinate dehydrogenase complex, subunit D, integral membrane protein | 6392 | ENSG00000204370 |
| 92  | ENSG00000106554 | NA | CHCHD3 | coiled-coil-helix-coiled-coil-helix domain containing 3 | 54927 | ENSG00000106554 |
| 93  | ENSG00000086504 | NA | MRPL28 | mitochondrial ribosomal protein L28 | 10573 | ENSG00000086504 |
| 94  | ENSG00000162910 | NA | MRPL55 | mitochondrial ribosomal protein L55 | 128308 | ENSG00000162910 |
| 95  | ENSG00000027001 | NA | MIPEP | mitochondrial intermediate peptidase | 4285 | ENSG00000027001 |
| 96  | ENSG00000103423 | NA | DNAJA3 | DnaJ (Hsp40) homolog, subfamily A, member 3 | 9093 | ENSG00000103423 |
| 97  | ENSG00000138777 | NA | PPA2 | pyrophosphatase (inorganic) 2 | 27068 | ENSG00000138777 |
| 98  | ENSG00000182180 | NA | MRPS16 | mitochondrial ribosomal protein S16 | 51021 | ENSG00000182180 |
| 99  | ENSG00000174032 | NA | SLC25A30 | solute carrier family 25, member 30 | 253512 | ENSG00000174032 |
| 100  | ENSG00000136522 | NA | MRPL47 | mitochondrial ribosomal protein L47 | 57129 | ENSG00000136522 |
| 101  | ENSG00000135972 | NA | MRPS9 | mitochondrial ribosomal protein S9 | 64965 | ENSG00000135972 |
| 102  | ENSG00000023228 | NA | NDUFS1 | NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) | 4719 | ENSG00000023228 |
| 103  | ENSG00000143252 | NA | SDHC | succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa | 6391 | ENSG00000143252 |
| 104  | ENSG00000151376 | NA | ME3 | malic enzyme 3, NADP(+)-dependent, mitochondrial | 10873 | ENSG00000151376 |
| 105  | ENSG00000115840 | NA | SLC25A12 | solute carrier family 25 (aspartate/glutamate carrier), member 12 | 8604 | ENSG00000115840 |
| 106  | ENSG00000145982 | NA | FARS2 | phenylalanyl-tRNA synthetase 2, mitochondrial | 10667 | ENSG00000145982 |
| 107  | ENSG00000110955 | NA | ATP5B | ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide | 506 | ENSG00000110955 |
| 108  | ENSG00000197122 | NA | SRC | v-src sarcoma (Schmidt-Ruppin A-2) viral oncogene homolog (avian) | 6714 | ENSG00000197122 |
| 109  | ENSG00000112695 | NA | COX7A2 | cytochrome c oxidase subunit VIIa polypeptide 2 (liver) | 1347 | ENSG00000112695 |
| 110  | ENSG00000083720 | NA | OXCT1 | 3-oxoacid CoA transferase 1 | 5019 | ENSG00000083720 |
| 111  | ENSG00000131495 | NA | NDUFA2 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa | 4695 | ENSG00000131495 |
| 112  | ENSG00000065518 | NA | NDUFB4 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa | 4710 | ENSG00000065518 |
| 113  | ENSG00000095321 | NA | CRAT | carnitine O-acetyltransferase | 1384 | ENSG00000095321 |
| 114  | ENSG00000165688 | NA | PMPCA | peptidase (mitochondrial processing) alpha | 23203 | ENSG00000165688 |
| 115  | ENSG00000112855 | NA | HARS2 | histidyl-tRNA synthetase 2, mitochondrial | 23438 | ENSG00000112855 |
| 116  | ENSG00000147853 | NA | AK3 | adenylate kinase 3 | 50808 | ENSG00000147853 |
| 117  | ENSG00000131174 | NA | COX7B | cytochrome c oxidase subunit VIIb | 1349 | ENSG00000131174 |
| 118  | ENSG00000205309 | NA | NT5M | 5',3'-nucleotidase, mitochondrial | 56953 | ENSG00000205309 |
| 119  | ENSG00000170906 | NA | NDUFA3 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa | 4696 | ENSG00000170906 |
| 120  | ENSG00000128654 | NA | MTX2 | metaxin 2 | 10651 | ENSG00000128654 |
| 121  | ENSG00000167283 | NA | ATP5L | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G | 10632 | ENSG00000167283 |
| 122  | ENSG00000114054 | NA | PCCB | propionyl CoA carboxylase, beta polypeptide | 5096 | ENSG00000114054 |
| 123  | ENSG00000069509 | NA | FUNDC1 | FUN14 domain containing 1 | 139341 | ENSG00000069509 |
| 124  | ENSG00000111275 | NA | ALDH2 | aldehyde dehydrogenase 2 family (mitochondrial) | 217 | ENSG00000111275 |
| 125  | ENSG00000124532 | NA | MRS2 | MRS2 magnesium homeostasis factor homolog (S. cerevisiae) | 57380 | ENSG00000124532 |
| 126  | ENSG00000131269 | NA | ABCB7 | ATP-binding cassette, sub-family B (MDR/TAP), member 7 | 22 | ENSG00000131269 |
| 127  | ENSG00000010256 | NA | UQCRC1 | ubiquinol-cytochrome c reductase core protein I | 7384 | ENSG00000010256 |
| 128  | ENSG00000137806 | NA | NDUFAF1 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 | 51103 | ENSG00000137806 |
| 129  | ENSG00000197912 | NA | SPG7 | spastic paraplegia 7 (pure and complicated autosomal recessive) | 6687 | ENSG00000197912 |
| 130  | ENSG00000171503 | NA | ETFDH | electron-transferring-flavoprotein dehydrogenase | 2110 | ENSG00000171503 |
| 131  | ENSG00000138796 | NA | HADH | hydroxyacyl-CoA dehydrogenase | 3033 | ENSG00000138796 |
| 132  | ENSG00000154518 | NA | ATP5G3 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C3 (subunit 9) | 518 | ENSG00000154518 |
| 133  | ENSG00000075303 | NA | SLC25A40 | solute carrier family 25, member 40 | 55972 | ENSG00000075303 |
| 134  | ENSG00000126768 | NA | TIMM17B | translocase of inner mitochondrial membrane 17 homolog B (yeast) | 10245 | ENSG00000126768 |
| 135  | ENSG00000168653 | NA | NDUFS5 | NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) | 4725 | ENSG00000168653 |
| 136  | ENSG00000247077 | NA | PGAM5 | phosphoglycerate mutase family member 5 | 192111 | ENSG00000247077 |
| 137  | ENSG00000184903 | NA | IMMP2L | IMP2 inner mitochondrial membrane peptidase-like (S. cerevisiae) | 83943 | ENSG00000184903 |
| 138  | ENSG00000087299 | NA | L2HGDH | L-2-hydroxyglutarate dehydrogenase | 79944 | ENSG00000087299 |
| 139  | ENSG00000156467 | NA | UQCRB | ubiquinol-cytochrome c reductase binding protein | 7381 | ENSG00000156467 |
| 140  | ENSG00000184076 | NA | UQCR10 | ubiquinol-cytochrome c reductase, complex III subunit X | 29796 | ENSG00000184076 |
| 141  | ENSG00000078070 | NA | MCCC1 | methylcrotonoyl-CoA carboxylase 1 (alpha) | 56922 | ENSG00000078070 |
| 142  | ENSG00000075415 | NA | SLC25A3 | solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 3 | 5250 | ENSG00000075415 |
| 143  | ENSG00000156885 | NA | COX6A2 | cytochrome c oxidase subunit VIa polypeptide 2 | 1339 | ENSG00000156885 |
| 144  | ENSG00000154723 | NA | ATP5J | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 | 522 | ENSG00000154723 |
| 145  | ENSG00000133983 | NA | COX16 | COX16 cytochrome c oxidase assembly homolog (S. cerevisiae) | 51241 | ENSG00000133983 |
| 146  | ENSG00000006695 | NA | COX10 | COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) | 1352 | ENSG00000006695 |
| 147  | ENSG00000167969 | NA | ECI1 | enoyl-CoA delta isomerase 1 | 1632 | ENSG00000167969 |
| 148  | ENSG00000105552 | NA | BCAT2 | branched chain amino-acid transaminase 2, mitochondrial | 587 | ENSG00000105552 |
| 149  | ENSG00000139531 | NA | SUOX | sulfite oxidase | 6821 | ENSG00000139531 |
| 150  | ENSG00000100347 | NA | SAMM50 | sorting and assembly machinery component 50 homolog (S. cerevisiae) | 25813 | ENSG00000100347 |
| 151  | ENSG00000125166 | NA | GOT2 | glutamic-oxaloacetic transaminase 2, mitochondrial (aspartate aminotransferase 2) | 2806 | ENSG00000125166 |
| 152  | ENSG00000140374 | NA | ETFA | electron-transfer-flavoprotein, alpha polypeptide | 2108 | ENSG00000140374 |
| 153  | ENSG00000140740 | NA | UQCRC2 | ubiquinol-cytochrome c reductase core protein II | 7385 | ENSG00000140740 |
| 154  | ENSG00000147684 | NA | NDUFB9 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa | 4715 | ENSG00000147684 |
| 155  | ENSG00000160194 | NA | NDUFV3 | NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa | 4731 | ENSG00000160194 |
| 156  | ENSG00000184983 | NA | NDUFA6 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa | 4700 | ENSG00000184983 |
| 157  | ENSG00000102309 | NA | PIN4 | protein (peptidylprolyl cis/trans isomerase) NIMA-interacting, 4 (parvulin) | 5303 | ENSG00000102309 |
| 158  | ENSG00000158864 | NA | NDUFS2 | NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) | 4720 | ENSG00000158864 |
| 159  | ENSG00000163626 | NA | COX18 | COX18 cytochrome c oxidase assembly homolog (S. cerevisiae) | 285521 | ENSG00000163626 |
| 160  | ENSG00000173436 | NA | MINOS1 | mitochondrial inner membrane organizing system 1 | 440574 | ENSG00000173436 |
| 161  | ENSG00000105197 | NA | TIMM50 | translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae) | 92609 | ENSG00000105197 |
| 162  | ENSG00000116221 | NA | MRPL37 | mitochondrial ribosomal protein L37 | 51253 | ENSG00000116221 |
| 163  | ENSG00000142168 | NA | SOD1 | superoxide dismutase 1, soluble | 6647 | ENSG00000142168 |
| 164  | ENSG00000109519 | NA | GRPEL1 | GrpE-like 1, mitochondrial (E. coli) | 80273 | ENSG00000109519 |
| 165  | ENSG00000262814 | NA | MRPL12 | mitochondrial ribosomal protein L12 | 6182 | ENSG00000262814 |
| 166  | ENSG00000096080 | NA | MRPS18A | mitochondrial ribosomal protein S18A | 55168 | ENSG00000096080 |
| 167  | ENSG00000119689 | NA | DLST | dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex) | 1743 | ENSG00000119689 |
| 168  | ENSG00000134056 | NA | MRPS36 | mitochondrial ribosomal protein S36 | 92259 | ENSG00000134056 |
| 169  | ENSG00000156502 | NA | SUPV3L1 | suppressor of var1, 3-like 1 (S. cerevisiae) | 6832 | ENSG00000156502 |
| 170  | ENSG00000168291 | NA | PDHB | pyruvate dehydrogenase (lipoamide) beta | 5162 | ENSG00000168291 |
| 171  | ENSG00000060762 | NA | MPC1 | mitochondrial pyruvate carrier 1 | 51660 | ENSG00000060762 |
| 172  | ENSG00000116459 | NA | ATP5F1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 | 515 | ENSG00000116459 |
| 173  | ENSG00000104980 | NA | TIMM44 | translocase of inner mitochondrial membrane 44 homolog (yeast) | 10469 | ENSG00000104980 |
| 174  | ENSG00000187145 | NA | MRPS21 | mitochondrial ribosomal protein S21 | 54460 | ENSG00000187145 |
| 175  | ENSG00000099800 | NA | TIMM13 | translocase of inner mitochondrial membrane 13 homolog (yeast) | 26517 | ENSG00000099800 |
| 176  | ENSG00000112992 | NA | NNT | nicotinamide nucleotide transhydrogenase | 23530 | ENSG00000112992 |
| 177  | ENSG00000067704 | NA | IARS2 | isoleucyl-tRNA synthetase 2, mitochondrial | 55699 | ENSG00000067704 |
| 178  | ENSG00000148950 | NA | IMMP1L | IMP1 inner mitochondrial membrane peptidase-like (S. cerevisiae) | 196294 | ENSG00000148950 |
| 179  | ENSG00000137288 | NA | MNF1 | mitochondrial nucleoid factor 1 | 84300 | ENSG00000137288 |
| 180  | ENSG00000172172 | NA | MRPL13 | mitochondrial ribosomal protein L13 | 28998 | ENSG00000172172 |
| 181  | ENSG00000119421 | NA | NDUFA8 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa | 4702 | ENSG00000119421 |
| 182  | ENSG00000244005 | NA | NFS1 | NFS1 nitrogen fixation 1 homolog (S. cerevisiae) | 9054 | ENSG00000244005 |
| 183  | ENSG00000126267 | NA | COX6B1 | cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) | 1340 | ENSG00000126267 |
| 184  | ENSG00000215021 | NA | PHB2 | prohibitin 2 | 11331 | ENSG00000215021 |
| 185  | ENSG00000167085 | NA | PHB | prohibitin | 5245 | ENSG00000167085 |
| 186  | ENSG00000145494 | NA | NDUFS6 | NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) | 4726 | ENSG00000145494 |
| 187  | ENSG00000072506 | NA | HSD17B10 | hydroxysteroid (17-beta) dehydrogenase 10 | 3028 | ENSG00000072506 |
| 188  | ENSG00000131143 | NA | COX4I1 | cytochrome c oxidase subunit IV isoform 1 | 1327 | ENSG00000131143 |
| 189  | ENSG00000108561 | NA | C1QBP | complement component 1, q subcomponent binding protein | 708 | ENSG00000108561 |
| 190  | ENSG00000105379 | NA | ETFB | electron-transfer-flavoprotein, beta polypeptide | 2109 | ENSG00000105379 |
| 191  | ENSG00000090266 | NA | NDUFB2 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa | 4708 | ENSG00000090266 |
| 192  | ENSG00000175581 | NA | MRPL48 | mitochondrial ribosomal protein L48 | 51642 | ENSG00000175581 |
| 193  | ENSG00000151498 | NA | ACAD8 | acyl-CoA dehydrogenase family, member 8 | 27034 | ENSG00000151498 |
| 194  | ENSG00000156928 | NA | MALSU1 | mitochondrial assembly of ribosomal large subunit 1 | 115416 | ENSG00000156928 |
| 195  | ENSG00000159199 | NA | ATP5G1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) | 516 | ENSG00000159199 |
| 196  | ENSG00000136143 | NA | SUCLA2 | succinate-CoA ligase, ADP-forming, beta subunit | 8803 | ENSG00000136143 |
| 197  | ENSG00000090263 | NA | MRPS33 | mitochondrial ribosomal protein S33 | 51650 | ENSG00000090263 |
| 198  | ENSG00000166855 | NA | CLPX | ClpX caseinolytic peptidase X homolog (E. coli) | 10845 | ENSG00000166855 |
| 199  | ENSG00000074582 | NA | BCS1L | BCS1-like (S. cerevisiae) | 617 | ENSG00000074582 |
| 200  | ENSG00000172590 | NA | MRPL52 | mitochondrial ribosomal protein L52 | 122704 | ENSG00000172590 |
| 201  | ENSG00000103018 | NA | CYB5B | cytochrome b5 type B (outer mitochondrial membrane) | 80777 | ENSG00000103018 |
| 202  | ENSG00000143374 | NA | TARS2 | threonyl-tRNA synthetase 2, mitochondrial (putative) | 80222 | ENSG00000143374 |
| 203  | ENSG00000166816 | NA | LDHD | lactate dehydrogenase D | 197257 | ENSG00000166816 |
| 204  | ENSG00000132313 | NA | MRPL35 | mitochondrial ribosomal protein L35 | 51318 | ENSG00000132313 |
| 205  | ENSG00000066926 | NA | FECH | ferrochelatase | 2235 | ENSG00000066926 |
| 206  | ENSG00000117118 | NA | SDHB | succinate dehydrogenase complex, subunit B, iron sulfur (Ip) | 6390 | ENSG00000117118 |
| 207  | ENSG00000138495 | NA | COX17 | COX17 cytochrome c oxidase assembly homolog (S. cerevisiae) | 10063 | ENSG00000138495 |
| 208  | ENSG00000135469 | NA | COQ10A | coenzyme Q10 homolog A (S. cerevisiae) | 93058 | ENSG00000135469 |
| 209  | ENSG00000177427 | NA | SMCR7 | Smith-Magenis syndrome chromosome region, candidate 7 | 125170 | ENSG00000177427 |
| 210  | ENSG00000115944 | NA | COX7A2L | cytochrome c oxidase subunit VIIa polypeptide 2 like | 9167 | ENSG00000115944 |
| 211  | ENSG00000197150 | NA | ABCB8 | ATP-binding cassette, sub-family B (MDR/TAP), member 8 | 11194 | ENSG00000197150 |
| 212  | ENSG00000152234 | NA | ATP5A1 | ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle | 498 | ENSG00000152234 |
| 213  | ENSG00000151366 | NA | NDUFC2 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa | 4718 | ENSG00000151366 |
| 214  | ENSG00000128609 | NA | NDUFA5 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa | 4698 | ENSG00000128609 |
| 215  | ENSG00000132305 | NA | IMMT | inner membrane protein, mitochondrial | 10989 | ENSG00000132305 |
| 216  | ENSG00000163541 | NA | SUCLG1 | succinate-CoA ligase, alpha subunit | 8802 | ENSG00000163541 |
| 217  | ENSG00000090432 | NA | MUL1 | mitochondrial E3 ubiquitin protein ligase 1 | 79594 | ENSG00000090432 |
| 218  | ENSG00000146701 | NA | MDH2 | malate dehydrogenase 2, NAD (mitochondrial) | 4191 | ENSG00000146701 |
| 219  | ENSG00000154719 | NA | MRPL39 | mitochondrial ribosomal protein L39 | 54148 | ENSG00000154719 |
| 220  | ENSG00000165678 | NA | GHITM | growth hormone inducible transmembrane protein | 27069 | ENSG00000165678 |
| 221  | ENSG00000173915 | NA | USMG5 | up-regulated during skeletal muscle growth 5 homolog (mouse) | 84833 | ENSG00000173915 |
| 222  | ENSG00000158882 | NA | TOMM40L | translocase of outer mitochondrial membrane 40 homolog (yeast)-like | 84134 | ENSG00000158882 |
| 223  | ENSG00000131730 | NA | CKMT2 | creatine kinase, mitochondrial 2 (sarcomeric) | 1160 | ENSG00000131730 |
| 224  | ENSG00000164038 | NA | SLC9B2 | solute carrier family 9, subfamily B (NHA2, cation proton antiporter 2), member 2 | 133308 | ENSG00000164038 |
| 225  | ENSG00000147123 | NA | NDUFB11 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa | 54539 | ENSG00000147123 |
| 226  | ENSG00000137714 | NA | FDX1 | ferredoxin 1 | 2230 | ENSG00000137714 |
| 227  | ENSG00000169021 | NA | UQCRFS1 | ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 | 7386 | ENSG00000169021 |
| 228  | ENSG00000178449 | NA | COX14 | COX14 cytochrome c oxidase assembly homolog (S. cerevisiae) | 84987 | ENSG00000178449 |
| 229  | ENSG00000102738 | NA | MRPS31 | mitochondrial ribosomal protein S31 | 10240 | ENSG00000102738 |
| 230  | ENSG00000124523 | NA | SIRT5 | sirtuin 5 | 23408 | ENSG00000124523 |
| 231  | ENSG00000145439 | NA | CBR4 | carbonyl reductase 4 | 84869 | ENSG00000145439 |
| 232  | ENSG00000062485 | NA | CS | citrate synthase | 1431 | ENSG00000062485 |
| 233  | ENSG00000130312 | NA | MRPL34 | mitochondrial ribosomal protein L34 | 64981 | ENSG00000130312 |
| 234  | ENSG00000175193 | NA | PARL | presenilin associated, rhomboid-like | 55486 | ENSG00000175193 |
| 235  | ENSG00000111843 | NA | TMEM14C | transmembrane protein 14C | 51522 | ENSG00000111843 |
| 236  | ENSG00000185973 | NA | TMLHE | trimethyllysine hydroxylase, epsilon | 55217 | ENSG00000185973 |
| 237  | ENSG00000124370 | NA | MCEE | methylmalonyl CoA epimerase | 84693 | ENSG00000124370 |
| 238  | ENSG00000137513 | NA | NARS2 | asparaginyl-tRNA synthetase 2, mitochondrial (putative) | 79731 | ENSG00000137513 |
| 239  | ENSG00000108179 | NA | PPIF | peptidylprolyl isomerase F | 10105 | ENSG00000108179 |
| 240  | ENSG00000162600 | NA | OMA1 | OMA1 zinc metallopeptidase homolog (S. cerevisiae) | 115209 | ENSG00000162600 |
| 241  | ENSG00000111639 | NA | MRPL51 | mitochondrial ribosomal protein L51 | 51258 | ENSG00000111639 |
| 242  | ENSG00000164405 | NA | UQCRQ | ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa | 27089 | ENSG00000164405 |
| 243  | ENSG00000173085 | NA | COQ2 | coenzyme Q2 homolog, prenyltransferase (yeast) | 27235 | ENSG00000173085 |
| 244  | ENSG00000061794 | NA | MRPS35 | mitochondrial ribosomal protein S35 | 60488 | ENSG00000061794 |
| 245  | ENSG00000124172 | NA | ATP5E | ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit | 514 | ENSG00000124172 |
| 246  | ENSG00000183648 | NA | NDUFB1 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa | 4707 | ENSG00000183648 |
| 247  | ENSG00000132591 | NA | ERAL1 | Era G-protein-like 1 (E. coli) | 26284 | ENSG00000132591 |
| 248  | ENSG00000205981 | NA | DNAJC19 | DnaJ (Hsp40) homolog, subfamily C, member 19 | 131118 | ENSG00000205981 |
| 249  | ENSG00000213585 | NA | VDAC1 | voltage-dependent anion channel 1 | 7416 | ENSG00000213585 |
| 250  | ENSG00000120333 | NA | MRPS14 | mitochondrial ribosomal protein S14 | 63931 | ENSG00000120333 |
| 251  | ENSG00000110435 | NA | PDHX | pyruvate dehydrogenase complex, component X | 8050 | ENSG00000110435 |
| 252  | ENSG00000099624 | NA | ATP5D | ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit | 513 | ENSG00000099624 |
| 253  | ENSG00000100412 | NA | ACO2 | aconitase 2, mitochondrial | 50 | ENSG00000100412 |
| 254  | ENSG00000132676 | NA | DAP3 | death associated protein 3 | 7818 | ENSG00000132676 |
| 255  | ENSG00000125356 | NA | NDUFA1 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa | 4694 | ENSG00000125356 |
| 256  | ENSG00000108528 | NA | SLC25A11 | solute carrier family 25 (mitochondrial carrier; oxoglutarate carrier), member 11 | 8402 | ENSG00000108528 |
| 257  | ENSG00000099795 | NA | NDUFB7 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa | 4713 | ENSG00000099795 |
| 258  | ENSG00000103507 | NA | BCKDK | branched chain ketoacid dehydrogenase kinase | 10295 | ENSG00000103507 |
| 259  | ENSG00000148090 | NA | AUH | AU RNA binding protein/enoyl-CoA hydratase | 549 | ENSG00000148090 |
| 260  | ENSG00000198015 | NA | MRPL42 | mitochondrial ribosomal protein L42 | 28977 | ENSG00000198015 |
| 261  | ENSG00000127989 | NA | MTERF | mitochondrial transcription termination factor | 7978 | ENSG00000127989 |
| 262  | ENSG00000125901 | NA | MRPS26 | mitochondrial ribosomal protein S26 | 64949 | ENSG00000125901 |
| 263  | ENSG00000075336 | NA | TIMM21 | translocase of inner mitochondrial membrane 21 homolog (yeast) | 29090 | ENSG00000075336 |
| 264  | ENSG00000181991 | NA | MRPS11 | mitochondrial ribosomal protein S11 | 64963 | ENSG00000181991 |
| 265  | ENSG00000175110 | NA | MRPS22 | mitochondrial ribosomal protein S22 | 56945 | ENSG00000175110 |
| 266  | ENSG00000197448 | NA | GSTK1 | glutathione S-transferase kappa 1 | 373156 | ENSG00000197448 |
| 267  | ENSG00000167792 | NA | NDUFV1 | NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa | 4723 | ENSG00000167792 |
| 268  | ENSG00000110717 | NA | NDUFS8 | NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) | 4728 | ENSG00000110717 |
| 269  | ENSG00000174547 | NA | MRPL11 | mitochondrial ribosomal protein L11 | 65003 | ENSG00000174547 |
| 270  | ENSG00000204308 | NA | RNF5 | ring finger protein 5, E3 ubiquitin protein ligase | 6048 | ENSG00000204308 |
| 271  | ENSG00000183978 | NA | COA3 | cytochrome C oxidase assembly factor 3 | 28958 | ENSG00000183978 |
| 272  | ENSG00000178952 | NA | TUFM | Tu translation elongation factor, mitochondrial | 7284 | ENSG00000178952 |
| 273  | ENSG00000127884 | NA | ECHS1 | enoyl CoA hydratase, short chain, 1, mitochondrial | 1892 | ENSG00000127884 |
| 274  | ENSG00000241468 | NA | ATP5J2 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 | 9551 | ENSG00000241468 |
| 275  | ENSG00000113013 | NA | HSPA9 | heat shock 70kDa protein 9 (mortalin) | 3313 | ENSG00000113013 |
| 276  | ENSG00000143158 | NA | MPC2 | mitochondrial pyruvate carrier 2 | 25874 | ENSG00000143158 |
| 277  | ENSG00000176340 | NA | COX8A | cytochrome c oxidase subunit VIIIA (ubiquitous) | 1351 | ENSG00000176340 |
| 278  | ENSG00000101247 | NA | NDUFAF5 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 5 | 79133 | ENSG00000101247 |
| 279  | ENSG00000101365 | NA | IDH3B | isocitrate dehydrogenase 3 (NAD+) beta | 3420 | ENSG00000101365 |
| 280  | ENSG00000241837 | NA | ATP5O | ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit | 539 | ENSG00000241837 |
| 281  | ENSG00000214026 | NA | MRPL23 | mitochondrial ribosomal protein L23 | 6150 | ENSG00000214026 |
| Database:cellular component       Name:mitochondrial inner membrane       ID:GO:0005743 | ||||||
|---|---|---|---|---|---|---|
| C=354; O=151; E=21.49; R=7.03; rawP=2.20e-90; adjP=2.90e-88 | ||||||
| Index | UserID | Value | Gene Symbol | Gene Name | EntrezGene | Ensembl |
| 1  | ENSG00000087299 | NA | L2HGDH | L-2-hydroxyglutarate dehydrogenase | 79944 | ENSG00000087299 |
| 2  | ENSG00000184903 | NA | IMMP2L | IMP2 inner mitochondrial membrane peptidase-like (S. cerevisiae) | 83943 | ENSG00000184903 |
| 3  | ENSG00000165264 | NA | NDUFB6 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa | 4712 | ENSG00000165264 |
| 4  | ENSG00000156467 | NA | UQCRB | ubiquinol-cytochrome c reductase binding protein | 7381 | ENSG00000156467 |
| 5  | ENSG00000161281 | NA | COX7A1 | cytochrome c oxidase subunit VIIa polypeptide 1 (muscle) | 1346 | ENSG00000161281 |
| 6  | ENSG00000184076 | NA | UQCR10 | ubiquinol-cytochrome c reductase, complex III subunit X | 29796 | ENSG00000184076 |
| 7  | ENSG00000078070 | NA | MCCC1 | methylcrotonoyl-CoA carboxylase 1 (alpha) | 56922 | ENSG00000078070 |
| 8  | ENSG00000075415 | NA | SLC25A3 | solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 3 | 5250 | ENSG00000075415 |
| 9  | ENSG00000156885 | NA | COX6A2 | cytochrome c oxidase subunit VIa polypeptide 2 | 1339 | ENSG00000156885 |
| 10  | ENSG00000154723 | NA | ATP5J | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 | 522 | ENSG00000154723 |
| 11  | ENSG00000167969 | NA | ECI1 | enoyl-CoA delta isomerase 1 | 1632 | ENSG00000167969 |
| 12  | ENSG00000125166 | NA | GOT2 | glutamic-oxaloacetic transaminase 2, mitochondrial (aspartate aminotransferase 2) | 2806 | ENSG00000125166 |
| 13  | ENSG00000100347 | NA | SAMM50 | sorting and assembly machinery component 50 homolog (S. cerevisiae) | 25813 | ENSG00000100347 |
| 14  | ENSG00000135390 | NA | ATP5G2 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C2 (subunit 9) | 517 | ENSG00000135390 |
| 15  | ENSG00000177370 | NA | TIMM22 | translocase of inner mitochondrial membrane 22 homolog (yeast) | 29928 | ENSG00000177370 |
| 16  | ENSG00000140740 | NA | UQCRC2 | ubiquinol-cytochrome c reductase core protein II | 7385 | ENSG00000140740 |
| 17  | ENSG00000166136 | NA | NDUFB8 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa | 4714 | ENSG00000166136 |
| 18  | ENSG00000160194 | NA | NDUFV3 | NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa | 4731 | ENSG00000160194 |
| 19  | ENSG00000147684 | NA | NDUFB9 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa | 4715 | ENSG00000147684 |
| 20  | ENSG00000184983 | NA | NDUFA6 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa | 4700 | ENSG00000184983 |
| 21  | ENSG00000130414 | NA | NDUFA10 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa | 4705 | ENSG00000130414 |
| 22  | ENSG00000163626 | NA | COX18 | COX18 cytochrome c oxidase assembly homolog (S. cerevisiae) | 285521 | ENSG00000163626 |
| 23  | ENSG00000158864 | NA | NDUFS2 | NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) | 4720 | ENSG00000158864 |
| 24  | ENSG00000007923 | NA | DNAJC11 | DnaJ (Hsp40) homolog, subfamily C, member 11 | 55735 | ENSG00000007923 |
| 25  | ENSG00000173436 | NA | MINOS1 | mitochondrial inner membrane organizing system 1 | 440574 | ENSG00000173436 |
| 26  | ENSG00000105197 | NA | TIMM50 | translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae) | 92609 | ENSG00000105197 |
| 27  | ENSG00000109390 | NA | NDUFC1 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa | 4717 | ENSG00000109390 |
| 28  | ENSG00000060762 | NA | MPC1 | mitochondrial pyruvate carrier 1 | 51660 | ENSG00000060762 |
| 29  | ENSG00000165283 | NA | STOML2 | stomatin (EPB72)-like 2 | 30968 | ENSG00000165283 |
| 30  | ENSG00000104980 | NA | TIMM44 | translocase of inner mitochondrial membrane 44 homolog (yeast) | 10469 | ENSG00000104980 |
| 31  | ENSG00000116459 | NA | ATP5F1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 | 515 | ENSG00000116459 |
| 32  | ENSG00000164466 | NA | SFXN1 | sideroflexin 1 | 94081 | ENSG00000164466 |
| 33  | ENSG00000099800 | NA | TIMM13 | translocase of inner mitochondrial membrane 13 homolog (yeast) | 26517 | ENSG00000099800 |
| 34  | ENSG00000151729 | NA | SLC25A4 | solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4 | 291 | ENSG00000151729 |
| 35  | ENSG00000178057 | NA | NDUFAF3 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 3 | 25915 | ENSG00000178057 |
| 36  | ENSG00000112992 | NA | NNT | nicotinamide nucleotide transhydrogenase | 23530 | ENSG00000112992 |
| 37  | ENSG00000213619 | NA | NDUFS3 | NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) | 4722 | ENSG00000213619 |
| 38  | ENSG00000178741 | NA | COX5A | cytochrome c oxidase subunit Va | 9377 | ENSG00000178741 |
| 39  | ENSG00000173660 | NA | UQCRH | ubiquinol-cytochrome c reductase hinge protein | 7388 | ENSG00000173660 |
| 40  | ENSG00000133028 | NA | SCO1 | SCO cytochrome oxidase deficient homolog 1 (yeast) | 6341 | ENSG00000133028 |
| 41  | ENSG00000148950 | NA | IMMP1L | IMP1 inner mitochondrial membrane peptidase-like (S. cerevisiae) | 196294 | ENSG00000148950 |
| 42  | ENSG00000119421 | NA | NDUFA8 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa | 4702 | ENSG00000119421 |
| 43  | ENSG00000126267 | NA | COX6B1 | cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) | 1340 | ENSG00000126267 |
| 44  | ENSG00000109919 | NA | MTCH2 | mitochondrial carrier 2 | 23788 | ENSG00000109919 |
| 45  | ENSG00000135940 | NA | COX5B | cytochrome c oxidase subunit Vb | 1329 | ENSG00000135940 |
| 46  | ENSG00000215021 | NA | PHB2 | prohibitin 2 | 11331 | ENSG00000215021 |
| 47  | ENSG00000145494 | NA | NDUFS6 | NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) | 4726 | ENSG00000145494 |
| 48  | ENSG00000167085 | NA | PHB | prohibitin | 5245 | ENSG00000167085 |
| 49  | ENSG00000072506 | NA | HSD17B10 | hydroxysteroid (17-beta) dehydrogenase 10 | 3028 | ENSG00000072506 |
| 50  | ENSG00000156709 | NA | AIFM1 | apoptosis-inducing factor, mitochondrion-associated, 1 | 9131 | ENSG00000156709 |
| 51  | ENSG00000189043 | NA | NDUFA4 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa | 4697 | ENSG00000189043 |
| 52  | ENSG00000131143 | NA | COX4I1 | cytochrome c oxidase subunit IV isoform 1 | 1327 | ENSG00000131143 |
| 53  | ENSG00000172115 | NA | CYCS | cytochrome c, somatic | 54205 | ENSG00000172115 |
| 54  | ENSG00000164919 | NA | COX6C | cytochrome c oxidase subunit VIc | 1345 | ENSG00000164919 |
| 55  | ENSG00000115286 | NA | NDUFS7 | NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) | 374291 | ENSG00000115286 |
| 56  | ENSG00000164258 | NA | NDUFS4 | NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) | 4724 | ENSG00000164258 |
| 57  | ENSG00000156170 | NA | NDUFAF6 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 | 137682 | ENSG00000156170 |
| 58  | ENSG00000155463 | NA | OXA1L | oxidase (cytochrome c) assembly 1-like | 5018 | ENSG00000155463 |
| 59  | ENSG00000167863 | NA | ATP5H | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d | 10476 | ENSG00000167863 |
| 60  | ENSG00000090266 | NA | NDUFB2 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa | 4708 | ENSG00000090266 |
| 61  | ENSG00000127540 | NA | UQCR11 | ubiquinol-cytochrome c reductase, complex III subunit XI | 10975 | ENSG00000127540 |
| 62  | ENSG00000179091 | NA | CYC1 | cytochrome c-1 | 1537 | ENSG00000179091 |
| 63  | ENSG00000184752 | NA | NDUFA12 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 | 55967 | ENSG00000184752 |
| 64  | ENSG00000156411 | NA | C14orf2 | chromosome 14 open reading frame 2 | 9556 | ENSG00000156411 |
| 65  | ENSG00000131844 | NA | MCCC2 | methylcrotonoyl-CoA carboxylase 2 (beta) | 64087 | ENSG00000131844 |
| 66  | ENSG00000159199 | NA | ATP5G1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) | 516 | ENSG00000159199 |
| 67  | ENSG00000105819 | NA | PMPCB | peptidase (mitochondrial processing) beta | 9512 | ENSG00000105819 |
| 68  | ENSG00000150779 | NA | TIMM8B | translocase of inner mitochondrial membrane 8 homolog B (yeast) | 26521 | ENSG00000150779 |
| 69  | ENSG00000166855 | NA | CLPX | ClpX caseinolytic peptidase X homolog (E. coli) | 10845 | ENSG00000166855 |
| 70  | ENSG00000074582 | NA | BCS1L | BCS1-like (S. cerevisiae) | 617 | ENSG00000074582 |
| 71  | ENSG00000103018 | NA | CYB5B | cytochrome b5 type B (outer mitochondrial membrane) | 80777 | ENSG00000103018 |
| 72  | ENSG00000166816 | NA | LDHD | lactate dehydrogenase D | 197257 | ENSG00000166816 |
| 73  | ENSG00000140990 | NA | NDUFB10 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa | 4716 | ENSG00000140990 |
| 74  | ENSG00000066926 | NA | FECH | ferrochelatase | 2235 | ENSG00000066926 |
| 75  | ENSG00000117118 | NA | SDHB | succinate dehydrogenase complex, subunit B, iron sulfur (Ip) | 6390 | ENSG00000117118 |
| 76  | ENSG00000135469 | NA | COQ10A | coenzyme Q10 homolog A (S. cerevisiae) | 93058 | ENSG00000135469 |
| 77  | ENSG00000165629 | NA | ATP5C1 | ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 | 509 | ENSG00000165629 |
| 78  | ENSG00000115944 | NA | COX7A2L | cytochrome c oxidase subunit VIIa polypeptide 2 like | 9167 | ENSG00000115944 |
| 79  | ENSG00000148290 | NA | SURF1 | surfeit 1 | 6834 | ENSG00000148290 |
| 80  | ENSG00000197150 | NA | ABCB8 | ATP-binding cassette, sub-family B (MDR/TAP), member 8 | 11194 | ENSG00000197150 |
| 81  | ENSG00000152234 | NA | ATP5A1 | ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle | 498 | ENSG00000152234 |
| 82  | ENSG00000072778 | NA | ACADVL | acyl-CoA dehydrogenase, very long chain | 37 | ENSG00000072778 |
| 83  | ENSG00000151366 | NA | NDUFC2 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa | 4718 | ENSG00000151366 |
| 84  | ENSG00000128609 | NA | NDUFA5 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa | 4698 | ENSG00000128609 |
| 85  | ENSG00000132305 | NA | IMMT | inner membrane protein, mitochondrial | 10989 | ENSG00000132305 |
| 86  | ENSG00000163541 | NA | SUCLG1 | succinate-CoA ligase, alpha subunit | 8802 | ENSG00000163541 |
| 87  | ENSG00000146701 | NA | MDH2 | malate dehydrogenase 2, NAD (mitochondrial) | 4191 | ENSG00000146701 |
| 88  | ENSG00000165678 | NA | GHITM | growth hormone inducible transmembrane protein | 27069 | ENSG00000165678 |
| 89  | ENSG00000125995 | NA | ROMO1 | reactive oxygen species modulator 1 | 140823 | ENSG00000125995 |
| 90  | ENSG00000136521 | NA | NDUFB5 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa | 4711 | ENSG00000136521 |
| 91  | ENSG00000173915 | NA | USMG5 | up-regulated during skeletal muscle growth 5 homolog (mouse) | 84833 | ENSG00000173915 |
| 92  | ENSG00000182054 | NA | IDH2 | isocitrate dehydrogenase 2 (NADP+), mitochondrial | 3418 | ENSG00000182054 |
| 93  | ENSG00000004779 | NA | NDUFAB1 | NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa | 4706 | ENSG00000004779 |
| 94  | ENSG00000131730 | NA | CKMT2 | creatine kinase, mitochondrial 2 (sarcomeric) | 1160 | ENSG00000131730 |
| 95  | ENSG00000169020 | NA | ATP5I | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E | 521 | ENSG00000169020 |
| 96  | ENSG00000004961 | NA | HCCS | holocytochrome c synthase | 3052 | ENSG00000004961 |
| 97  | ENSG00000147123 | NA | NDUFB11 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa | 54539 | ENSG00000147123 |
| 98  | ENSG00000073578 | NA | SDHA | succinate dehydrogenase complex, subunit A, flavoprotein (Fp) | 6389 | ENSG00000073578 |
| 99  | ENSG00000137714 | NA | FDX1 | ferredoxin 1 | 2230 | ENSG00000137714 |
| 100  | ENSG00000119013 | NA | NDUFB3 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa | 4709 | ENSG00000119013 |
| 101  | ENSG00000169021 | NA | UQCRFS1 | ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 | 7386 | ENSG00000169021 |
| 102  | ENSG00000175193 | NA | PARL | presenilin associated, rhomboid-like | 55486 | ENSG00000175193 |
| 103  | ENSG00000108179 | NA | PPIF | peptidylprolyl isomerase F | 10105 | ENSG00000108179 |
| 104  | ENSG00000139180 | NA | NDUFA9 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa | 4704 | ENSG00000139180 |
| 105  | ENSG00000162600 | NA | OMA1 | OMA1 zinc metallopeptidase homolog (S. cerevisiae) | 115209 | ENSG00000162600 |
| 106  | ENSG00000127184 | NA | COX7C | cytochrome c oxidase subunit VIIc | 1350 | ENSG00000127184 |
| 107  | ENSG00000164405 | NA | UQCRQ | ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa | 27089 | ENSG00000164405 |
| 108  | ENSG00000165637 | NA | VDAC2 | voltage-dependent anion channel 2 | 7417 | ENSG00000165637 |
| 109  | ENSG00000124172 | NA | ATP5E | ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit | 514 | ENSG00000124172 |
| 110  | ENSG00000183648 | NA | NDUFB1 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa | 4707 | ENSG00000183648 |
| 111  | ENSG00000132591 | NA | ERAL1 | Era G-protein-like 1 (E. coli) | 26284 | ENSG00000132591 |
| 112  | ENSG00000205981 | NA | DNAJC19 | DnaJ (Hsp40) homolog, subfamily C, member 19 | 131118 | ENSG00000205981 |
| 113  | ENSG00000213585 | NA | VDAC1 | voltage-dependent anion channel 1 | 7416 | ENSG00000213585 |
| 114  | ENSG00000204370 | NA | SDHD | succinate dehydrogenase complex, subunit D, integral membrane protein | 6392 | ENSG00000204370 |
| 115  | ENSG00000099624 | NA | ATP5D | ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit | 513 | ENSG00000099624 |
| 116  | ENSG00000106554 | NA | CHCHD3 | coiled-coil-helix-coiled-coil-helix domain containing 3 | 54927 | ENSG00000106554 |
| 117  | ENSG00000125356 | NA | NDUFA1 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa | 4694 | ENSG00000125356 |
| 118  | ENSG00000108528 | NA | SLC25A11 | solute carrier family 25 (mitochondrial carrier; oxoglutarate carrier), member 11 | 8402 | ENSG00000108528 |
| 119  | ENSG00000099795 | NA | NDUFB7 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa | 4713 | ENSG00000099795 |
| 120  | ENSG00000174032 | NA | SLC25A30 | solute carrier family 25, member 30 | 253512 | ENSG00000174032 |
| 121  | ENSG00000023228 | NA | NDUFS1 | NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) | 4719 | ENSG00000023228 |
| 122  | ENSG00000143252 | NA | SDHC | succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa | 6391 | ENSG00000143252 |
| 123  | ENSG00000115840 | NA | SLC25A12 | solute carrier family 25 (aspartate/glutamate carrier), member 12 | 8604 | ENSG00000115840 |
| 124  | ENSG00000110955 | NA | ATP5B | ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide | 506 | ENSG00000110955 |
| 125  | ENSG00000197122 | NA | SRC | v-src sarcoma (Schmidt-Ruppin A-2) viral oncogene homolog (avian) | 6714 | ENSG00000197122 |
| 126  | ENSG00000112695 | NA | COX7A2 | cytochrome c oxidase subunit VIIa polypeptide 2 (liver) | 1347 | ENSG00000112695 |
| 127  | ENSG00000197448 | NA | GSTK1 | glutathione S-transferase kappa 1 | 373156 | ENSG00000197448 |
| 128  | ENSG00000167792 | NA | NDUFV1 | NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa | 4723 | ENSG00000167792 |
| 129  | ENSG00000131495 | NA | NDUFA2 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa | 4695 | ENSG00000131495 |
| 130  | ENSG00000065518 | NA | NDUFB4 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa | 4710 | ENSG00000065518 |
| 131  | ENSG00000095321 | NA | CRAT | carnitine O-acetyltransferase | 1384 | ENSG00000095321 |
| 132  | ENSG00000165688 | NA | PMPCA | peptidase (mitochondrial processing) alpha | 23203 | ENSG00000165688 |
| 133  | ENSG00000110717 | NA | NDUFS8 | NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) | 4728 | ENSG00000110717 |
| 134  | ENSG00000131174 | NA | COX7B | cytochrome c oxidase subunit VIIb | 1349 | ENSG00000131174 |
| 135  | ENSG00000170906 | NA | NDUFA3 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa | 4696 | ENSG00000170906 |
| 136  | ENSG00000167283 | NA | ATP5L | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G | 10632 | ENSG00000167283 |
| 137  | ENSG00000124532 | NA | MRS2 | MRS2 magnesium homeostasis factor homolog (S. cerevisiae) | 57380 | ENSG00000124532 |
| 138  | ENSG00000131269 | NA | ABCB7 | ATP-binding cassette, sub-family B (MDR/TAP), member 7 | 22 | ENSG00000131269 |
| 139  | ENSG00000010256 | NA | UQCRC1 | ubiquinol-cytochrome c reductase core protein I | 7384 | ENSG00000010256 |
| 140  | ENSG00000137806 | NA | NDUFAF1 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 | 51103 | ENSG00000137806 |
| 141  | ENSG00000241468 | NA | ATP5J2 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 | 9551 | ENSG00000241468 |
| 142  | ENSG00000171503 | NA | ETFDH | electron-transferring-flavoprotein dehydrogenase | 2110 | ENSG00000171503 |
| 143  | ENSG00000143158 | NA | MPC2 | mitochondrial pyruvate carrier 2 | 25874 | ENSG00000143158 |
| 144  | ENSG00000138796 | NA | HADH | hydroxyacyl-CoA dehydrogenase | 3033 | ENSG00000138796 |
| 145  | ENSG00000154518 | NA | ATP5G3 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C3 (subunit 9) | 518 | ENSG00000154518 |
| 146  | ENSG00000075303 | NA | SLC25A40 | solute carrier family 25, member 40 | 55972 | ENSG00000075303 |
| 147  | ENSG00000176340 | NA | COX8A | cytochrome c oxidase subunit VIIIA (ubiquitous) | 1351 | ENSG00000176340 |
| 148  | ENSG00000101247 | NA | NDUFAF5 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 5 | 79133 | ENSG00000101247 |
| 149  | ENSG00000168653 | NA | NDUFS5 | NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) | 4725 | ENSG00000168653 |
| 150  | ENSG00000126768 | NA | TIMM17B | translocase of inner mitochondrial membrane 17 homolog B (yeast) | 10245 | ENSG00000126768 |
| 151  | ENSG00000241837 | NA | ATP5O | ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit | 539 | ENSG00000241837 |
| Database:cellular component       Name:mitochondrial matrix       ID:GO:0005759 | ||||||
|---|---|---|---|---|---|---|
| C=278; O=135; E=16.87; R=8.00; rawP=8.25e-90; adjP=8.17e-88 | ||||||
| Index | UserID | Value | Gene Symbol | Gene Name | EntrezGene | Ensembl |
| 1  | ENSG00000116898 | NA | MRPS15 | mitochondrial ribosomal protein S15 | 64960 | ENSG00000116898 |
| 2  | ENSG00000167862 | NA | ICT1 | immature colon carcinoma transcript 1 | 3396 | ENSG00000167862 |
| 3  | ENSG00000078070 | NA | MCCC1 | methylcrotonoyl-CoA carboxylase 1 (alpha) | 56922 | ENSG00000078070 |
| 4  | ENSG00000148672 | NA | GLUD1 | glutamate dehydrogenase 1 | 2746 | ENSG00000148672 |
| 5  | ENSG00000167969 | NA | ECI1 | enoyl-CoA delta isomerase 1 | 1632 | ENSG00000167969 |
| 6  | ENSG00000105552 | NA | BCAT2 | branched chain amino-acid transaminase 2, mitochondrial | 587 | ENSG00000105552 |
| 7  | ENSG00000139531 | NA | SUOX | sulfite oxidase | 6821 | ENSG00000139531 |
| 8  | ENSG00000125166 | NA | GOT2 | glutamic-oxaloacetic transaminase 2, mitochondrial (aspartate aminotransferase 2) | 2806 | ENSG00000125166 |
| 9  | ENSG00000140374 | NA | ETFA | electron-transfer-flavoprotein, alpha polypeptide | 2108 | ENSG00000140374 |
| 10  | ENSG00000172340 | NA | SUCLG2 | succinate-CoA ligase, GDP-forming, beta subunit | 8801 | ENSG00000172340 |
| 11  | ENSG00000091140 | NA | DLD | dihydrolipoamide dehydrogenase | 1738 | ENSG00000091140 |
| 12  | ENSG00000130414 | NA | NDUFA10 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa | 4705 | ENSG00000130414 |
| 13  | ENSG00000102309 | NA | PIN4 | protein (peptidylprolyl cis/trans isomerase) NIMA-interacting, 4 (parvulin) | 5303 | ENSG00000102309 |
| 14  | ENSG00000165060 | NA | FXN | frataxin | 2395 | ENSG00000165060 |
| 15  | ENSG00000173141 | NA | MRP63 | mitochondrial ribosomal protein 63 | 78988 | ENSG00000173141 |
| 16  | ENSG00000116221 | NA | MRPL37 | mitochondrial ribosomal protein L37 | 51253 | ENSG00000116221 |
| 17  | ENSG00000131828 | NA | PDHA1 | pyruvate dehydrogenase (lipoamide) alpha 1 | 5160 | ENSG00000131828 |
| 18  | ENSG00000122971 | NA | ACADS | acyl-CoA dehydrogenase, C-2 to C-3 short chain | 35 | ENSG00000122971 |
| 19  | ENSG00000142168 | NA | SOD1 | superoxide dismutase 1, soluble | 6647 | ENSG00000142168 |
| 20  | ENSG00000103356 | NA | EARS2 | glutamyl-tRNA synthetase 2, mitochondrial (putative) | 124454 | ENSG00000103356 |
| 21  | ENSG00000109519 | NA | GRPEL1 | GrpE-like 1, mitochondrial (E. coli) | 80273 | ENSG00000109519 |
| 22  | ENSG00000091483 | NA | FH | fumarate hydratase | 2271 | ENSG00000091483 |
| 23  | ENSG00000262814 | NA | MRPL12 | mitochondrial ribosomal protein L12 | 6182 | ENSG00000262814 |
| 24  | ENSG00000055950 | NA | MRPL43 | mitochondrial ribosomal protein L43 | 84545 | ENSG00000055950 |
| 25  | ENSG00000096080 | NA | MRPS18A | mitochondrial ribosomal protein S18A | 55168 | ENSG00000096080 |
| 26  | ENSG00000134056 | NA | MRPS36 | mitochondrial ribosomal protein S36 | 92259 | ENSG00000134056 |
| 27  | ENSG00000142082 | NA | SIRT3 | sirtuin 3 | 23410 | ENSG00000142082 |
| 28  | ENSG00000119689 | NA | DLST | dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex) | 1743 | ENSG00000119689 |
| 29  | ENSG00000204568 | NA | MRPS18B | mitochondrial ribosomal protein S18B | 28973 | ENSG00000204568 |
| 30  | ENSG00000168291 | NA | PDHB | pyruvate dehydrogenase (lipoamide) beta | 5162 | ENSG00000168291 |
| 31  | ENSG00000156502 | NA | SUPV3L1 | suppressor of var1, 3-like 1 (S. cerevisiae) | 6832 | ENSG00000156502 |
| 32  | ENSG00000104980 | NA | TIMM44 | translocase of inner mitochondrial membrane 44 homolog (yeast) | 10469 | ENSG00000104980 |
| 33  | ENSG00000116459 | NA | ATP5F1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 | 515 | ENSG00000116459 |
| 34  | ENSG00000187145 | NA | MRPS21 | mitochondrial ribosomal protein S21 | 54460 | ENSG00000187145 |
| 35  | ENSG00000067704 | NA | IARS2 | isoleucyl-tRNA synthetase 2, mitochondrial | 55699 | ENSG00000067704 |
| 36  | ENSG00000023330 | NA | ALAS1 | aminolevulinate, delta-, synthase 1 | 211 | ENSG00000023330 |
| 37  | ENSG00000147586 | NA | MRPS28 | mitochondrial ribosomal protein S28 | 28957 | ENSG00000147586 |
| 38  | ENSG00000172172 | NA | MRPL13 | mitochondrial ribosomal protein L13 | 28998 | ENSG00000172172 |
| 39  | ENSG00000137288 | NA | MNF1 | mitochondrial nucleoid factor 1 | 84300 | ENSG00000137288 |
| 40  | ENSG00000244005 | NA | NFS1 | NFS1 nitrogen fixation 1 homolog (S. cerevisiae) | 9054 | ENSG00000244005 |
| 41  | ENSG00000029639 | NA | TFB1M | transcription factor B1, mitochondrial | 51106 | ENSG00000029639 |
| 42  | ENSG00000143436 | NA | MRPL9 | mitochondrial ribosomal protein L9 | 65005 | ENSG00000143436 |
| 43  | ENSG00000239789 | NA | MRPS17 | mitochondrial ribosomal protein S17 | 51373 | ENSG00000239789 |
| 44  | ENSG00000162851 | NA | TFB2M | transcription factor B2, mitochondrial | 64216 | ENSG00000162851 |
| 45  | ENSG00000072506 | NA | HSD17B10 | hydroxysteroid (17-beta) dehydrogenase 10 | 3028 | ENSG00000072506 |
| 46  | ENSG00000108561 | NA | C1QBP | complement component 1, q subcomponent binding protein | 708 | ENSG00000108561 |
| 47  | ENSG00000105379 | NA | ETFB | electron-transfer-flavoprotein, beta polypeptide | 2109 | ENSG00000105379 |
| 48  | ENSG00000139131 | NA | YARS2 | tyrosyl-tRNA synthetase 2, mitochondrial | 51067 | ENSG00000139131 |
| 49  | ENSG00000163319 | NA | MRPS18C | mitochondrial ribosomal protein S18C | 51023 | ENSG00000163319 |
| 50  | ENSG00000175581 | NA | MRPL48 | mitochondrial ribosomal protein L48 | 51642 | ENSG00000175581 |
| 51  | ENSG00000185608 | NA | MRPL40 | mitochondrial ribosomal protein L40 | 64976 | ENSG00000185608 |
| 52  | ENSG00000151498 | NA | ACAD8 | acyl-CoA dehydrogenase family, member 8 | 27034 | ENSG00000151498 |
| 53  | ENSG00000132423 | NA | COQ3 | coenzyme Q3 homolog, methyltransferase (S. cerevisiae) | 51805 | ENSG00000132423 |
| 54  | ENSG00000131844 | NA | MCCC2 | methylcrotonoyl-CoA carboxylase 2 (beta) | 64087 | ENSG00000131844 |
| 55  | ENSG00000134905 | NA | CARS2 | cysteinyl-tRNA synthetase 2, mitochondrial (putative) | 79587 | ENSG00000134905 |
| 56  | ENSG00000156928 | NA | MALSU1 | mitochondrial assembly of ribosomal large subunit 1 | 115416 | ENSG00000156928 |
| 57  | ENSG00000136143 | NA | SUCLA2 | succinate-CoA ligase, ADP-forming, beta subunit | 8803 | ENSG00000136143 |
| 58  | ENSG00000182810 | NA | DDX28 | DEAD (Asp-Glu-Ala-Asp) box polypeptide 28 | 55794 | ENSG00000182810 |
| 59  | ENSG00000105819 | NA | PMPCB | peptidase (mitochondrial processing) beta | 9512 | ENSG00000105819 |
| 60  | ENSG00000166855 | NA | CLPX | ClpX caseinolytic peptidase X homolog (E. coli) | 10845 | ENSG00000166855 |
| 61  | ENSG00000090263 | NA | MRPS33 | mitochondrial ribosomal protein S33 | 51650 | ENSG00000090263 |
| 62  | ENSG00000204228 | NA | HSD17B8 | hydroxysteroid (17-beta) dehydrogenase 8 | 7923 | ENSG00000204228 |
| 63  | ENSG00000175198 | NA | PCCA | propionyl CoA carboxylase, alpha polypeptide | 5095 | ENSG00000175198 |
| 64  | ENSG00000067829 | NA | IDH3G | isocitrate dehydrogenase 3 (NAD+) gamma | 3421 | ENSG00000067829 |
| 65  | ENSG00000172590 | NA | MRPL52 | mitochondrial ribosomal protein L52 | 122704 | ENSG00000172590 |
| 66  | ENSG00000143374 | NA | TARS2 | threonyl-tRNA synthetase 2, mitochondrial (putative) | 80222 | ENSG00000143374 |
| 67  | ENSG00000132313 | NA | MRPL35 | mitochondrial ribosomal protein L35 | 51318 | ENSG00000132313 |
| 68  | ENSG00000066926 | NA | FECH | ferrochelatase | 2235 | ENSG00000066926 |
| 69  | ENSG00000247626 | NA | MARS2 | methionyl-tRNA synthetase 2, mitochondrial | 92935 | ENSG00000247626 |
| 70  | ENSG00000165629 | NA | ATP5C1 | ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 | 509 | ENSG00000165629 |
| 71  | ENSG00000152234 | NA | ATP5A1 | ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle | 498 | ENSG00000152234 |
| 72  | ENSG00000072778 | NA | ACADVL | acyl-CoA dehydrogenase, very long chain | 37 | ENSG00000072778 |
| 73  | ENSG00000154930 | NA | ACSS1 | acyl-CoA synthetase short-chain family member 1 | 84532 | ENSG00000154930 |
| 74  | ENSG00000163541 | NA | SUCLG1 | succinate-CoA ligase, alpha subunit | 8802 | ENSG00000163541 |
| 75  | ENSG00000146701 | NA | MDH2 | malate dehydrogenase 2, NAD (mitochondrial) | 4191 | ENSG00000146701 |
| 76  | ENSG00000154719 | NA | MRPL39 | mitochondrial ribosomal protein L39 | 54148 | ENSG00000154719 |
| 77  | ENSG00000182054 | NA | IDH2 | isocitrate dehydrogenase 2 (NADP+), mitochondrial | 3418 | ENSG00000182054 |
| 78  | ENSG00000004779 | NA | NDUFAB1 | NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa | 4706 | ENSG00000004779 |
| 79  | ENSG00000137714 | NA | FDX1 | ferredoxin 1 | 2230 | ENSG00000137714 |
| 80  | ENSG00000104325 | NA | DECR1 | 2,4-dienoyl CoA reductase 1, mitochondrial | 1666 | ENSG00000104325 |
| 81  | ENSG00000102738 | NA | MRPS31 | mitochondrial ribosomal protein S31 | 10240 | ENSG00000102738 |
| 82  | ENSG00000124523 | NA | SIRT5 | sirtuin 5 | 23408 | ENSG00000124523 |
| 83  | ENSG00000145439 | NA | CBR4 | carbonyl reductase 4 | 84869 | ENSG00000145439 |
| 84  | ENSG00000062485 | NA | CS | citrate synthase | 1431 | ENSG00000062485 |
| 85  | ENSG00000130312 | NA | MRPL34 | mitochondrial ribosomal protein L34 | 64981 | ENSG00000130312 |
| 86  | ENSG00000182154 | NA | MRPL41 | mitochondrial ribosomal protein L41 | 64975 | ENSG00000182154 |
| 87  | ENSG00000185973 | NA | TMLHE | trimethyllysine hydroxylase, epsilon | 55217 | ENSG00000185973 |
| 88  | ENSG00000108179 | NA | PPIF | peptidylprolyl isomerase F | 10105 | ENSG00000108179 |
| 89  | ENSG00000139180 | NA | NDUFA9 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa | 4704 | ENSG00000139180 |
| 90  | ENSG00000137513 | NA | NARS2 | asparaginyl-tRNA synthetase 2, mitochondrial (putative) | 79731 | ENSG00000137513 |
| 91  | ENSG00000124370 | NA | MCEE | methylmalonyl CoA epimerase | 84693 | ENSG00000124370 |
| 92  | ENSG00000111639 | NA | MRPL51 | mitochondrial ribosomal protein L51 | 51258 | ENSG00000111639 |
| 93  | ENSG00000165637 | NA | VDAC2 | voltage-dependent anion channel 2 | 7417 | ENSG00000165637 |
| 94  | ENSG00000061794 | NA | MRPS35 | mitochondrial ribosomal protein S35 | 60488 | ENSG00000061794 |
| 95  | ENSG00000124172 | NA | ATP5E | ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit | 514 | ENSG00000124172 |
| 96  | ENSG00000132591 | NA | ERAL1 | Era G-protein-like 1 (E. coli) | 26284 | ENSG00000132591 |
| 97  | ENSG00000213585 | NA | VDAC1 | voltage-dependent anion channel 1 | 7416 | ENSG00000213585 |
| 98  | ENSG00000120333 | NA | MRPS14 | mitochondrial ribosomal protein S14 | 63931 | ENSG00000120333 |
| 99  | ENSG00000110435 | NA | PDHX | pyruvate dehydrogenase complex, component X | 8050 | ENSG00000110435 |
| 100  | ENSG00000099624 | NA | ATP5D | ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit | 513 | ENSG00000099624 |
| 101  | ENSG00000100412 | NA | ACO2 | aconitase 2, mitochondrial | 50 | ENSG00000100412 |
| 102  | ENSG00000086504 | NA | MRPL28 | mitochondrial ribosomal protein L28 | 10573 | ENSG00000086504 |
| 103  | ENSG00000132676 | NA | DAP3 | death associated protein 3 | 7818 | ENSG00000132676 |
| 104  | ENSG00000162910 | NA | MRPL55 | mitochondrial ribosomal protein L55 | 128308 | ENSG00000162910 |
| 105  | ENSG00000027001 | NA | MIPEP | mitochondrial intermediate peptidase | 4285 | ENSG00000027001 |
| 106  | ENSG00000103423 | NA | DNAJA3 | DnaJ (Hsp40) homolog, subfamily A, member 3 | 9093 | ENSG00000103423 |
| 107  | ENSG00000138777 | NA | PPA2 | pyrophosphatase (inorganic) 2 | 27068 | ENSG00000138777 |
| 108  | ENSG00000182180 | NA | MRPS16 | mitochondrial ribosomal protein S16 | 51021 | ENSG00000182180 |
| 109  | ENSG00000136522 | NA | MRPL47 | mitochondrial ribosomal protein L47 | 57129 | ENSG00000136522 |
| 110  | ENSG00000135972 | NA | MRPS9 | mitochondrial ribosomal protein S9 | 64965 | ENSG00000135972 |
| 111  | ENSG00000103507 | NA | BCKDK | branched chain ketoacid dehydrogenase kinase | 10295 | ENSG00000103507 |
| 112  | ENSG00000148090 | NA | AUH | AU RNA binding protein/enoyl-CoA hydratase | 549 | ENSG00000148090 |
| 113  | ENSG00000198015 | NA | MRPL42 | mitochondrial ribosomal protein L42 | 28977 | ENSG00000198015 |
| 114  | ENSG00000127989 | NA | MTERF | mitochondrial transcription termination factor | 7978 | ENSG00000127989 |
| 115  | ENSG00000151376 | NA | ME3 | malic enzyme 3, NADP(+)-dependent, mitochondrial | 10873 | ENSG00000151376 |
| 116  | ENSG00000125901 | NA | MRPS26 | mitochondrial ribosomal protein S26 | 64949 | ENSG00000125901 |
| 117  | ENSG00000145982 | NA | FARS2 | phenylalanyl-tRNA synthetase 2, mitochondrial | 10667 | ENSG00000145982 |
| 118  | ENSG00000110955 | NA | ATP5B | ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide | 506 | ENSG00000110955 |
| 119  | ENSG00000181991 | NA | MRPS11 | mitochondrial ribosomal protein S11 | 64963 | ENSG00000181991 |
| 120  | ENSG00000175110 | NA | MRPS22 | mitochondrial ribosomal protein S22 | 56945 | ENSG00000175110 |
| 121  | ENSG00000083720 | NA | OXCT1 | 3-oxoacid CoA transferase 1 | 5019 | ENSG00000083720 |
| 122  | ENSG00000165688 | NA | PMPCA | peptidase (mitochondrial processing) alpha | 23203 | ENSG00000165688 |
| 123  | ENSG00000112855 | NA | HARS2 | histidyl-tRNA synthetase 2, mitochondrial | 23438 | ENSG00000112855 |
| 124  | ENSG00000147853 | NA | AK3 | adenylate kinase 3 | 50808 | ENSG00000147853 |
| 125  | ENSG00000174547 | NA | MRPL11 | mitochondrial ribosomal protein L11 | 65003 | ENSG00000174547 |
| 126  | ENSG00000205309 | NA | NT5M | 5',3'-nucleotidase, mitochondrial | 56953 | ENSG00000205309 |
| 127  | ENSG00000114054 | NA | PCCB | propionyl CoA carboxylase, beta polypeptide | 5096 | ENSG00000114054 |
| 128  | ENSG00000111275 | NA | ALDH2 | aldehyde dehydrogenase 2 family (mitochondrial) | 217 | ENSG00000111275 |
| 129  | ENSG00000178952 | NA | TUFM | Tu translation elongation factor, mitochondrial | 7284 | ENSG00000178952 |
| 130  | ENSG00000127884 | NA | ECHS1 | enoyl CoA hydratase, short chain, 1, mitochondrial | 1892 | ENSG00000127884 |
| 131  | ENSG00000171503 | NA | ETFDH | electron-transferring-flavoprotein dehydrogenase | 2110 | ENSG00000171503 |
| 132  | ENSG00000113013 | NA | HSPA9 | heat shock 70kDa protein 9 (mortalin) | 3313 | ENSG00000113013 |
| 133  | ENSG00000138796 | NA | HADH | hydroxyacyl-CoA dehydrogenase | 3033 | ENSG00000138796 |
| 134  | ENSG00000101365 | NA | IDH3B | isocitrate dehydrogenase 3 (NAD+) beta | 3420 | ENSG00000101365 |
| 135  | ENSG00000214026 | NA | MRPL23 | mitochondrial ribosomal protein L23 | 6150 | ENSG00000214026 |
| Database:cellular component       Name:mitochondrial envelope       ID:GO:0005740 | ||||||
|---|---|---|---|---|---|---|
| C=530; O=179; E=32.17; R=5.56; rawP=1.89e-87; adjP=1.50e-85 | ||||||
| Index | UserID | Value | Gene Symbol | Gene Name | EntrezGene | Ensembl |
| 1  | ENSG00000087299 | NA | L2HGDH | L-2-hydroxyglutarate dehydrogenase | 79944 | ENSG00000087299 |
| 2  | ENSG00000184903 | NA | IMMP2L | IMP2 inner mitochondrial membrane peptidase-like (S. cerevisiae) | 83943 | ENSG00000184903 |
| 3  | ENSG00000165264 | NA | NDUFB6 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa | 4712 | ENSG00000165264 |
| 4  | ENSG00000156467 | NA | UQCRB | ubiquinol-cytochrome c reductase binding protein | 7381 | ENSG00000156467 |
| 5  | ENSG00000161281 | NA | COX7A1 | cytochrome c oxidase subunit VIIa polypeptide 1 (muscle) | 1346 | ENSG00000161281 |
| 6  | ENSG00000184076 | NA | UQCR10 | ubiquinol-cytochrome c reductase, complex III subunit X | 29796 | ENSG00000184076 |
| 7  | ENSG00000078070 | NA | MCCC1 | methylcrotonoyl-CoA carboxylase 1 (alpha) | 56922 | ENSG00000078070 |
| 8  | ENSG00000075415 | NA | SLC25A3 | solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 3 | 5250 | ENSG00000075415 |
| 9  | ENSG00000156885 | NA | COX6A2 | cytochrome c oxidase subunit VIa polypeptide 2 | 1339 | ENSG00000156885 |
| 10  | ENSG00000006695 | NA | COX10 | COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) | 1352 | ENSG00000006695 |
| 11  | ENSG00000133983 | NA | COX16 | COX16 cytochrome c oxidase assembly homolog (S. cerevisiae) | 51241 | ENSG00000133983 |
| 12  | ENSG00000154723 | NA | ATP5J | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 | 522 | ENSG00000154723 |
| 13  | ENSG00000167969 | NA | ECI1 | enoyl-CoA delta isomerase 1 | 1632 | ENSG00000167969 |
| 14  | ENSG00000139531 | NA | SUOX | sulfite oxidase | 6821 | ENSG00000139531 |
| 15  | ENSG00000125166 | NA | GOT2 | glutamic-oxaloacetic transaminase 2, mitochondrial (aspartate aminotransferase 2) | 2806 | ENSG00000125166 |
| 16  | ENSG00000100347 | NA | SAMM50 | sorting and assembly machinery component 50 homolog (S. cerevisiae) | 25813 | ENSG00000100347 |
| 17  | ENSG00000135390 | NA | ATP5G2 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C2 (subunit 9) | 517 | ENSG00000135390 |
| 18  | ENSG00000177370 | NA | TIMM22 | translocase of inner mitochondrial membrane 22 homolog (yeast) | 29928 | ENSG00000177370 |
| 19  | ENSG00000140740 | NA | UQCRC2 | ubiquinol-cytochrome c reductase core protein II | 7385 | ENSG00000140740 |
| 20  | ENSG00000166136 | NA | NDUFB8 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa | 4714 | ENSG00000166136 |
| 21  | ENSG00000160194 | NA | NDUFV3 | NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa | 4731 | ENSG00000160194 |
| 22  | ENSG00000147684 | NA | NDUFB9 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa | 4715 | ENSG00000147684 |
| 23  | ENSG00000184983 | NA | NDUFA6 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa | 4700 | ENSG00000184983 |
| 24  | ENSG00000130414 | NA | NDUFA10 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa | 4705 | ENSG00000130414 |
| 25  | ENSG00000163626 | NA | COX18 | COX18 cytochrome c oxidase assembly homolog (S. cerevisiae) | 285521 | ENSG00000163626 |
| 26  | ENSG00000158864 | NA | NDUFS2 | NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) | 4720 | ENSG00000158864 |
| 27  | ENSG00000007923 | NA | DNAJC11 | DnaJ (Hsp40) homolog, subfamily C, member 11 | 55735 | ENSG00000007923 |
| 28  | ENSG00000173436 | NA | MINOS1 | mitochondrial inner membrane organizing system 1 | 440574 | ENSG00000173436 |
| 29  | ENSG00000105197 | NA | TIMM50 | translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae) | 92609 | ENSG00000105197 |
| 30  | ENSG00000109390 | NA | NDUFC1 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa | 4717 | ENSG00000109390 |
| 31  | ENSG00000060762 | NA | MPC1 | mitochondrial pyruvate carrier 1 | 51660 | ENSG00000060762 |
| 32  | ENSG00000165283 | NA | STOML2 | stomatin (EPB72)-like 2 | 30968 | ENSG00000165283 |
| 33  | ENSG00000104980 | NA | TIMM44 | translocase of inner mitochondrial membrane 44 homolog (yeast) | 10469 | ENSG00000104980 |
| 34  | ENSG00000116459 | NA | ATP5F1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 | 515 | ENSG00000116459 |
| 35  | ENSG00000164466 | NA | SFXN1 | sideroflexin 1 | 94081 | ENSG00000164466 |
| 36  | ENSG00000099800 | NA | TIMM13 | translocase of inner mitochondrial membrane 13 homolog (yeast) | 26517 | ENSG00000099800 |
| 37  | ENSG00000151729 | NA | SLC25A4 | solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4 | 291 | ENSG00000151729 |
| 38  | ENSG00000178057 | NA | NDUFAF3 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 3 | 25915 | ENSG00000178057 |
| 39  | ENSG00000112992 | NA | NNT | nicotinamide nucleotide transhydrogenase | 23530 | ENSG00000112992 |
| 40  | ENSG00000213619 | NA | NDUFS3 | NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) | 4722 | ENSG00000213619 |
| 41  | ENSG00000178741 | NA | COX5A | cytochrome c oxidase subunit Va | 9377 | ENSG00000178741 |
| 42  | ENSG00000173660 | NA | UQCRH | ubiquinol-cytochrome c reductase hinge protein | 7388 | ENSG00000173660 |
| 43  | ENSG00000214253 | NA | FIS1 | fission 1 (mitochondrial outer membrane) homolog (S. cerevisiae) | 51024 | ENSG00000214253 |
| 44  | ENSG00000133028 | NA | SCO1 | SCO cytochrome oxidase deficient homolog 1 (yeast) | 6341 | ENSG00000133028 |
| 45  | ENSG00000148950 | NA | IMMP1L | IMP1 inner mitochondrial membrane peptidase-like (S. cerevisiae) | 196294 | ENSG00000148950 |
| 46  | ENSG00000119421 | NA | NDUFA8 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa | 4702 | ENSG00000119421 |
| 47  | ENSG00000126267 | NA | COX6B1 | cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) | 1340 | ENSG00000126267 |
| 48  | ENSG00000109919 | NA | MTCH2 | mitochondrial carrier 2 | 23788 | ENSG00000109919 |
| 49  | ENSG00000135940 | NA | COX5B | cytochrome c oxidase subunit Vb | 1329 | ENSG00000135940 |
| 50  | ENSG00000215021 | NA | PHB2 | prohibitin 2 | 11331 | ENSG00000215021 |
| 51  | ENSG00000145494 | NA | NDUFS6 | NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) | 4726 | ENSG00000145494 |
| 52  | ENSG00000167085 | NA | PHB | prohibitin | 5245 | ENSG00000167085 |
| 53  | ENSG00000072506 | NA | HSD17B10 | hydroxysteroid (17-beta) dehydrogenase 10 | 3028 | ENSG00000072506 |
| 54  | ENSG00000156709 | NA | AIFM1 | apoptosis-inducing factor, mitochondrion-associated, 1 | 9131 | ENSG00000156709 |
| 55  | ENSG00000189043 | NA | NDUFA4 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa | 4697 | ENSG00000189043 |
| 56  | ENSG00000131143 | NA | COX4I1 | cytochrome c oxidase subunit IV isoform 1 | 1327 | ENSG00000131143 |
| 57  | ENSG00000172115 | NA | CYCS | cytochrome c, somatic | 54205 | ENSG00000172115 |
| 58  | ENSG00000164919 | NA | COX6C | cytochrome c oxidase subunit VIc | 1345 | ENSG00000164919 |
| 59  | ENSG00000115286 | NA | NDUFS7 | NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) | 374291 | ENSG00000115286 |
| 60  | ENSG00000164258 | NA | NDUFS4 | NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) | 4724 | ENSG00000164258 |
| 61  | ENSG00000156170 | NA | NDUFAF6 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 | 137682 | ENSG00000156170 |
| 62  | ENSG00000155463 | NA | OXA1L | oxidase (cytochrome c) assembly 1-like | 5018 | ENSG00000155463 |
| 63  | ENSG00000167863 | NA | ATP5H | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d | 10476 | ENSG00000167863 |
| 64  | ENSG00000090266 | NA | NDUFB2 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa | 4708 | ENSG00000090266 |
| 65  | ENSG00000127540 | NA | UQCR11 | ubiquinol-cytochrome c reductase, complex III subunit XI | 10975 | ENSG00000127540 |
| 66  | ENSG00000179091 | NA | CYC1 | cytochrome c-1 | 1537 | ENSG00000179091 |
| 67  | ENSG00000184752 | NA | NDUFA12 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 | 55967 | ENSG00000184752 |
| 68  | ENSG00000156411 | NA | C14orf2 | chromosome 14 open reading frame 2 | 9556 | ENSG00000156411 |
| 69  | ENSG00000131844 | NA | MCCC2 | methylcrotonoyl-CoA carboxylase 2 (beta) | 64087 | ENSG00000131844 |
| 70  | ENSG00000159199 | NA | ATP5G1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) | 516 | ENSG00000159199 |
| 71  | ENSG00000105819 | NA | PMPCB | peptidase (mitochondrial processing) beta | 9512 | ENSG00000105819 |
| 72  | ENSG00000150779 | NA | TIMM8B | translocase of inner mitochondrial membrane 8 homolog B (yeast) | 26521 | ENSG00000150779 |
| 73  | ENSG00000166855 | NA | CLPX | ClpX caseinolytic peptidase X homolog (E. coli) | 10845 | ENSG00000166855 |
| 74  | ENSG00000204228 | NA | HSD17B8 | hydroxysteroid (17-beta) dehydrogenase 8 | 7923 | ENSG00000204228 |
| 75  | ENSG00000196683 | NA | TOMM7 | translocase of outer mitochondrial membrane 7 homolog (yeast) | 54543 | ENSG00000196683 |
| 76  | ENSG00000074582 | NA | BCS1L | BCS1-like (S. cerevisiae) | 617 | ENSG00000074582 |
| 77  | ENSG00000103018 | NA | CYB5B | cytochrome b5 type B (outer mitochondrial membrane) | 80777 | ENSG00000103018 |
| 78  | ENSG00000166816 | NA | LDHD | lactate dehydrogenase D | 197257 | ENSG00000166816 |
| 79  | ENSG00000140990 | NA | NDUFB10 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa | 4716 | ENSG00000140990 |
| 80  | ENSG00000066926 | NA | FECH | ferrochelatase | 2235 | ENSG00000066926 |
| 81  | ENSG00000117118 | NA | SDHB | succinate dehydrogenase complex, subunit B, iron sulfur (Ip) | 6390 | ENSG00000117118 |
| 82  | ENSG00000138495 | NA | COX17 | COX17 cytochrome c oxidase assembly homolog (S. cerevisiae) | 10063 | ENSG00000138495 |
| 83  | ENSG00000198523 | NA | PLN | phospholamban | 5350 | ENSG00000198523 |
| 84  | ENSG00000006530 | NA | AGK | acylglycerol kinase | 55750 | ENSG00000006530 |
| 85  | ENSG00000135469 | NA | COQ10A | coenzyme Q10 homolog A (S. cerevisiae) | 93058 | ENSG00000135469 |
| 86  | ENSG00000177427 | NA | SMCR7 | Smith-Magenis syndrome chromosome region, candidate 7 | 125170 | ENSG00000177427 |
| 87  | ENSG00000165629 | NA | ATP5C1 | ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 | 509 | ENSG00000165629 |
| 88  | ENSG00000115944 | NA | COX7A2L | cytochrome c oxidase subunit VIIa polypeptide 2 like | 9167 | ENSG00000115944 |
| 89  | ENSG00000123545 | NA | NDUFAF4 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 4 | 29078 | ENSG00000123545 |
| 90  | ENSG00000148290 | NA | SURF1 | surfeit 1 | 6834 | ENSG00000148290 |
| 91  | ENSG00000197150 | NA | ABCB8 | ATP-binding cassette, sub-family B (MDR/TAP), member 8 | 11194 | ENSG00000197150 |
| 92  | ENSG00000152234 | NA | ATP5A1 | ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle | 498 | ENSG00000152234 |
| 93  | ENSG00000072778 | NA | ACADVL | acyl-CoA dehydrogenase, very long chain | 37 | ENSG00000072778 |
| 94  | ENSG00000151366 | NA | NDUFC2 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa | 4718 | ENSG00000151366 |
| 95  | ENSG00000196636 | NA | ACN9 | ACN9 homolog (S. cerevisiae) | 57001 | ENSG00000196636 |
| 96  | ENSG00000128609 | NA | NDUFA5 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa | 4698 | ENSG00000128609 |
| 97  | ENSG00000132305 | NA | IMMT | inner membrane protein, mitochondrial | 10989 | ENSG00000132305 |
| 98  | ENSG00000163541 | NA | SUCLG1 | succinate-CoA ligase, alpha subunit | 8802 | ENSG00000163541 |
| 99  | ENSG00000090432 | NA | MUL1 | mitochondrial E3 ubiquitin protein ligase 1 | 79594 | ENSG00000090432 |
| 100  | ENSG00000146701 | NA | MDH2 | malate dehydrogenase 2, NAD (mitochondrial) | 4191 | ENSG00000146701 |
| 101  | ENSG00000165678 | NA | GHITM | growth hormone inducible transmembrane protein | 27069 | ENSG00000165678 |
| 102  | ENSG00000125995 | NA | ROMO1 | reactive oxygen species modulator 1 | 140823 | ENSG00000125995 |
| 103  | ENSG00000136521 | NA | NDUFB5 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa | 4711 | ENSG00000136521 |
| 104  | ENSG00000173915 | NA | USMG5 | up-regulated during skeletal muscle growth 5 homolog (mouse) | 84833 | ENSG00000173915 |
| 105  | ENSG00000169020 | NA | ATP5I | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E | 521 | ENSG00000169020 |
| 106  | ENSG00000158882 | NA | TOMM40L | translocase of outer mitochondrial membrane 40 homolog (yeast)-like | 84134 | ENSG00000158882 |
| 107  | ENSG00000182054 | NA | IDH2 | isocitrate dehydrogenase 2 (NADP+), mitochondrial | 3418 | ENSG00000182054 |
| 108  | ENSG00000004779 | NA | NDUFAB1 | NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa | 4706 | ENSG00000004779 |
| 109  | ENSG00000131730 | NA | CKMT2 | creatine kinase, mitochondrial 2 (sarcomeric) | 1160 | ENSG00000131730 |
| 110  | ENSG00000168958 | NA | MFF | mitochondrial fission factor | 56947 | ENSG00000168958 |
| 111  | ENSG00000164038 | NA | SLC9B2 | solute carrier family 9, subfamily B (NHA2, cation proton antiporter 2), member 2 | 133308 | ENSG00000164038 |
| 112  | ENSG00000004961 | NA | HCCS | holocytochrome c synthase | 3052 | ENSG00000004961 |
| 113  | ENSG00000147123 | NA | NDUFB11 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa | 54539 | ENSG00000147123 |
| 114  | ENSG00000073578 | NA | SDHA | succinate dehydrogenase complex, subunit A, flavoprotein (Fp) | 6389 | ENSG00000073578 |
| 115  | ENSG00000137714 | NA | FDX1 | ferredoxin 1 | 2230 | ENSG00000137714 |
| 116  | ENSG00000119013 | NA | NDUFB3 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa | 4709 | ENSG00000119013 |
| 117  | ENSG00000169021 | NA | UQCRFS1 | ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 | 7386 | ENSG00000169021 |
| 118  | ENSG00000178449 | NA | COX14 | COX14 cytochrome c oxidase assembly homolog (S. cerevisiae) | 84987 | ENSG00000178449 |
| 119  | ENSG00000124523 | NA | SIRT5 | sirtuin 5 | 23408 | ENSG00000124523 |
| 120  | ENSG00000175193 | NA | PARL | presenilin associated, rhomboid-like | 55486 | ENSG00000175193 |
| 121  | ENSG00000078668 | NA | VDAC3 | voltage-dependent anion channel 3 | 7419 | ENSG00000078668 |
| 122  | ENSG00000111843 | NA | TMEM14C | transmembrane protein 14C | 51522 | ENSG00000111843 |
| 123  | ENSG00000139180 | NA | NDUFA9 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa | 4704 | ENSG00000139180 |
| 124  | ENSG00000108179 | NA | PPIF | peptidylprolyl isomerase F | 10105 | ENSG00000108179 |
| 125  | ENSG00000162600 | NA | OMA1 | OMA1 zinc metallopeptidase homolog (S. cerevisiae) | 115209 | ENSG00000162600 |
| 126  | ENSG00000127184 | NA | COX7C | cytochrome c oxidase subunit VIIc | 1350 | ENSG00000127184 |
| 127  | ENSG00000164405 | NA | UQCRQ | ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa | 27089 | ENSG00000164405 |
| 128  | ENSG00000165637 | NA | VDAC2 | voltage-dependent anion channel 2 | 7417 | ENSG00000165637 |
| 129  | ENSG00000173085 | NA | COQ2 | coenzyme Q2 homolog, prenyltransferase (yeast) | 27235 | ENSG00000173085 |
| 130  | ENSG00000124172 | NA | ATP5E | ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit | 514 | ENSG00000124172 |
| 131  | ENSG00000183648 | NA | NDUFB1 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa | 4707 | ENSG00000183648 |
| 132  | ENSG00000213585 | NA | VDAC1 | voltage-dependent anion channel 1 | 7416 | ENSG00000213585 |
| 133  | ENSG00000205981 | NA | DNAJC19 | DnaJ (Hsp40) homolog, subfamily C, member 19 | 131118 | ENSG00000205981 |
| 134  | ENSG00000132591 | NA | ERAL1 | Era G-protein-like 1 (E. coli) | 26284 | ENSG00000132591 |
| 135  | ENSG00000204370 | NA | SDHD | succinate dehydrogenase complex, subunit D, integral membrane protein | 6392 | ENSG00000204370 |
| 136  | ENSG00000099624 | NA | ATP5D | ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit | 513 | ENSG00000099624 |
| 137  | ENSG00000106554 | NA | CHCHD3 | coiled-coil-helix-coiled-coil-helix domain containing 3 | 54927 | ENSG00000106554 |
| 138  | ENSG00000125356 | NA | NDUFA1 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa | 4694 | ENSG00000125356 |
| 139  | ENSG00000108528 | NA | SLC25A11 | solute carrier family 25 (mitochondrial carrier; oxoglutarate carrier), member 11 | 8402 | ENSG00000108528 |
| 140  | ENSG00000099795 | NA | NDUFB7 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa | 4713 | ENSG00000099795 |
| 141  | ENSG00000174032 | NA | SLC25A30 | solute carrier family 25, member 30 | 253512 | ENSG00000174032 |
| 142  | ENSG00000023228 | NA | NDUFS1 | NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) | 4719 | ENSG00000023228 |
| 143  | ENSG00000143252 | NA | SDHC | succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa | 6391 | ENSG00000143252 |
| 144  | ENSG00000075336 | NA | TIMM21 | translocase of inner mitochondrial membrane 21 homolog (yeast) | 29090 | ENSG00000075336 |
| 145  | ENSG00000115840 | NA | SLC25A12 | solute carrier family 25 (aspartate/glutamate carrier), member 12 | 8604 | ENSG00000115840 |
| 146  | ENSG00000110955 | NA | ATP5B | ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide | 506 | ENSG00000110955 |
| 147  | ENSG00000197122 | NA | SRC | v-src sarcoma (Schmidt-Ruppin A-2) viral oncogene homolog (avian) | 6714 | ENSG00000197122 |
| 148  | ENSG00000112695 | NA | COX7A2 | cytochrome c oxidase subunit VIIa polypeptide 2 (liver) | 1347 | ENSG00000112695 |
| 149  | ENSG00000197448 | NA | GSTK1 | glutathione S-transferase kappa 1 | 373156 | ENSG00000197448 |
| 150  | ENSG00000167792 | NA | NDUFV1 | NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa | 4723 | ENSG00000167792 |
| 151  | ENSG00000131495 | NA | NDUFA2 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa | 4695 | ENSG00000131495 |
| 152  | ENSG00000065518 | NA | NDUFB4 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa | 4710 | ENSG00000065518 |
| 153  | ENSG00000095321 | NA | CRAT | carnitine O-acetyltransferase | 1384 | ENSG00000095321 |
| 154  | ENSG00000165688 | NA | PMPCA | peptidase (mitochondrial processing) alpha | 23203 | ENSG00000165688 |
| 155  | ENSG00000110717 | NA | NDUFS8 | NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) | 4728 | ENSG00000110717 |
| 156  | ENSG00000131174 | NA | COX7B | cytochrome c oxidase subunit VIIb | 1349 | ENSG00000131174 |
| 157  | ENSG00000170906 | NA | NDUFA3 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa | 4696 | ENSG00000170906 |
| 158  | ENSG00000128654 | NA | MTX2 | metaxin 2 | 10651 | ENSG00000128654 |
| 159  | ENSG00000204308 | NA | RNF5 | ring finger protein 5, E3 ubiquitin protein ligase | 6048 | ENSG00000204308 |
| 160  | ENSG00000167283 | NA | ATP5L | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G | 10632 | ENSG00000167283 |
| 161  | ENSG00000069509 | NA | FUNDC1 | FUN14 domain containing 1 | 139341 | ENSG00000069509 |
| 162  | ENSG00000183978 | NA | COA3 | cytochrome C oxidase assembly factor 3 | 28958 | ENSG00000183978 |
| 163  | ENSG00000124532 | NA | MRS2 | MRS2 magnesium homeostasis factor homolog (S. cerevisiae) | 57380 | ENSG00000124532 |
| 164  | ENSG00000131269 | NA | ABCB7 | ATP-binding cassette, sub-family B (MDR/TAP), member 7 | 22 | ENSG00000131269 |
| 165  | ENSG00000010256 | NA | UQCRC1 | ubiquinol-cytochrome c reductase core protein I | 7384 | ENSG00000010256 |
| 166  | ENSG00000137806 | NA | NDUFAF1 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 | 51103 | ENSG00000137806 |
| 167  | ENSG00000241468 | NA | ATP5J2 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 | 9551 | ENSG00000241468 |
| 168  | ENSG00000197912 | NA | SPG7 | spastic paraplegia 7 (pure and complicated autosomal recessive) | 6687 | ENSG00000197912 |
| 169  | ENSG00000171503 | NA | ETFDH | electron-transferring-flavoprotein dehydrogenase | 2110 | ENSG00000171503 |
| 170  | ENSG00000143158 | NA | MPC2 | mitochondrial pyruvate carrier 2 | 25874 | ENSG00000143158 |
| 171  | ENSG00000138796 | NA | HADH | hydroxyacyl-CoA dehydrogenase | 3033 | ENSG00000138796 |
| 172  | ENSG00000154518 | NA | ATP5G3 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C3 (subunit 9) | 518 | ENSG00000154518 |
| 173  | ENSG00000075303 | NA | SLC25A40 | solute carrier family 25, member 40 | 55972 | ENSG00000075303 |
| 174  | ENSG00000176340 | NA | COX8A | cytochrome c oxidase subunit VIIIA (ubiquitous) | 1351 | ENSG00000176340 |
| 175  | ENSG00000101247 | NA | NDUFAF5 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 5 | 79133 | ENSG00000101247 |
| 176  | ENSG00000168653 | NA | NDUFS5 | NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) | 4725 | ENSG00000168653 |
| 177  | ENSG00000126768 | NA | TIMM17B | translocase of inner mitochondrial membrane 17 homolog B (yeast) | 10245 | ENSG00000126768 |
| 178  | ENSG00000247077 | NA | PGAM5 | phosphoglycerate mutase family member 5 | 192111 | ENSG00000247077 |
| 179  | ENSG00000241837 | NA | ATP5O | ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit | 539 | ENSG00000241837 |
| Database:cellular component       Name:organelle inner membrane       ID:GO:0019866 | ||||||
|---|---|---|---|---|---|---|
| C=384; O=153; E=23.31; R=6.56; rawP=2.25e-86; adjP=1.48e-84 | ||||||
| Index | UserID | Value | Gene Symbol | Gene Name | EntrezGene | Ensembl |
| 1  | ENSG00000164828 | NA | SUN1 | Sad1 and UNC84 domain containing 1 | 23353 | ENSG00000164828 |
| 2  | ENSG00000087299 | NA | L2HGDH | L-2-hydroxyglutarate dehydrogenase | 79944 | ENSG00000087299 |
| 3  | ENSG00000184903 | NA | IMMP2L | IMP2 inner mitochondrial membrane peptidase-like (S. cerevisiae) | 83943 | ENSG00000184903 |
| 4  | ENSG00000165264 | NA | NDUFB6 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa | 4712 | ENSG00000165264 |
| 5  | ENSG00000156467 | NA | UQCRB | ubiquinol-cytochrome c reductase binding protein | 7381 | ENSG00000156467 |
| 6  | ENSG00000161281 | NA | COX7A1 | cytochrome c oxidase subunit VIIa polypeptide 1 (muscle) | 1346 | ENSG00000161281 |
| 7  | ENSG00000184076 | NA | UQCR10 | ubiquinol-cytochrome c reductase, complex III subunit X | 29796 | ENSG00000184076 |
| 8  | ENSG00000078070 | NA | MCCC1 | methylcrotonoyl-CoA carboxylase 1 (alpha) | 56922 | ENSG00000078070 |
| 9  | ENSG00000075415 | NA | SLC25A3 | solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 3 | 5250 | ENSG00000075415 |
| 10  | ENSG00000156885 | NA | COX6A2 | cytochrome c oxidase subunit VIa polypeptide 2 | 1339 | ENSG00000156885 |
| 11  | ENSG00000154723 | NA | ATP5J | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 | 522 | ENSG00000154723 |
| 12  | ENSG00000167969 | NA | ECI1 | enoyl-CoA delta isomerase 1 | 1632 | ENSG00000167969 |
| 13  | ENSG00000125166 | NA | GOT2 | glutamic-oxaloacetic transaminase 2, mitochondrial (aspartate aminotransferase 2) | 2806 | ENSG00000125166 |
| 14  | ENSG00000100347 | NA | SAMM50 | sorting and assembly machinery component 50 homolog (S. cerevisiae) | 25813 | ENSG00000100347 |
| 15  | ENSG00000135390 | NA | ATP5G2 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C2 (subunit 9) | 517 | ENSG00000135390 |
| 16  | ENSG00000177370 | NA | TIMM22 | translocase of inner mitochondrial membrane 22 homolog (yeast) | 29928 | ENSG00000177370 |
| 17  | ENSG00000140740 | NA | UQCRC2 | ubiquinol-cytochrome c reductase core protein II | 7385 | ENSG00000140740 |
| 18  | ENSG00000166136 | NA | NDUFB8 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa | 4714 | ENSG00000166136 |
| 19  | ENSG00000160194 | NA | NDUFV3 | NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa | 4731 | ENSG00000160194 |
| 20  | ENSG00000147684 | NA | NDUFB9 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa | 4715 | ENSG00000147684 |
| 21  | ENSG00000184983 | NA | NDUFA6 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa | 4700 | ENSG00000184983 |
| 22  | ENSG00000130414 | NA | NDUFA10 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa | 4705 | ENSG00000130414 |
| 23  | ENSG00000163626 | NA | COX18 | COX18 cytochrome c oxidase assembly homolog (S. cerevisiae) | 285521 | ENSG00000163626 |
| 24  | ENSG00000158864 | NA | NDUFS2 | NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) | 4720 | ENSG00000158864 |
| 25  | ENSG00000007923 | NA | DNAJC11 | DnaJ (Hsp40) homolog, subfamily C, member 11 | 55735 | ENSG00000007923 |
| 26  | ENSG00000173436 | NA | MINOS1 | mitochondrial inner membrane organizing system 1 | 440574 | ENSG00000173436 |
| 27  | ENSG00000105197 | NA | TIMM50 | translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae) | 92609 | ENSG00000105197 |
| 28  | ENSG00000109390 | NA | NDUFC1 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa | 4717 | ENSG00000109390 |
| 29  | ENSG00000060762 | NA | MPC1 | mitochondrial pyruvate carrier 1 | 51660 | ENSG00000060762 |
| 30  | ENSG00000165283 | NA | STOML2 | stomatin (EPB72)-like 2 | 30968 | ENSG00000165283 |
| 31  | ENSG00000104980 | NA | TIMM44 | translocase of inner mitochondrial membrane 44 homolog (yeast) | 10469 | ENSG00000104980 |
| 32  | ENSG00000116459 | NA | ATP5F1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 | 515 | ENSG00000116459 |
| 33  | ENSG00000164466 | NA | SFXN1 | sideroflexin 1 | 94081 | ENSG00000164466 |
| 34  | ENSG00000099800 | NA | TIMM13 | translocase of inner mitochondrial membrane 13 homolog (yeast) | 26517 | ENSG00000099800 |
| 35  | ENSG00000151729 | NA | SLC25A4 | solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4 | 291 | ENSG00000151729 |
| 36  | ENSG00000178057 | NA | NDUFAF3 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 3 | 25915 | ENSG00000178057 |
| 37  | ENSG00000112992 | NA | NNT | nicotinamide nucleotide transhydrogenase | 23530 | ENSG00000112992 |
| 38  | ENSG00000213619 | NA | NDUFS3 | NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) | 4722 | ENSG00000213619 |
| 39  | ENSG00000178741 | NA | COX5A | cytochrome c oxidase subunit Va | 9377 | ENSG00000178741 |
| 40  | ENSG00000173660 | NA | UQCRH | ubiquinol-cytochrome c reductase hinge protein | 7388 | ENSG00000173660 |
| 41  | ENSG00000133028 | NA | SCO1 | SCO cytochrome oxidase deficient homolog 1 (yeast) | 6341 | ENSG00000133028 |
| 42  | ENSG00000148950 | NA | IMMP1L | IMP1 inner mitochondrial membrane peptidase-like (S. cerevisiae) | 196294 | ENSG00000148950 |
| 43  | ENSG00000119421 | NA | NDUFA8 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa | 4702 | ENSG00000119421 |
| 44  | ENSG00000126267 | NA | COX6B1 | cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) | 1340 | ENSG00000126267 |
| 45  | ENSG00000109919 | NA | MTCH2 | mitochondrial carrier 2 | 23788 | ENSG00000109919 |
| 46  | ENSG00000135940 | NA | COX5B | cytochrome c oxidase subunit Vb | 1329 | ENSG00000135940 |
| 47  | ENSG00000215021 | NA | PHB2 | prohibitin 2 | 11331 | ENSG00000215021 |
| 48  | ENSG00000145494 | NA | NDUFS6 | NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) | 4726 | ENSG00000145494 |
| 49  | ENSG00000167085 | NA | PHB | prohibitin | 5245 | ENSG00000167085 |
| 50  | ENSG00000072506 | NA | HSD17B10 | hydroxysteroid (17-beta) dehydrogenase 10 | 3028 | ENSG00000072506 |
| 51  | ENSG00000156709 | NA | AIFM1 | apoptosis-inducing factor, mitochondrion-associated, 1 | 9131 | ENSG00000156709 |
| 52  | ENSG00000189043 | NA | NDUFA4 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa | 4697 | ENSG00000189043 |
| 53  | ENSG00000131143 | NA | COX4I1 | cytochrome c oxidase subunit IV isoform 1 | 1327 | ENSG00000131143 |
| 54  | ENSG00000172115 | NA | CYCS | cytochrome c, somatic | 54205 | ENSG00000172115 |
| 55  | ENSG00000164919 | NA | COX6C | cytochrome c oxidase subunit VIc | 1345 | ENSG00000164919 |
| 56  | ENSG00000115286 | NA | NDUFS7 | NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) | 374291 | ENSG00000115286 |
| 57  | ENSG00000164258 | NA | NDUFS4 | NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) | 4724 | ENSG00000164258 |
| 58  | ENSG00000156170 | NA | NDUFAF6 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 | 137682 | ENSG00000156170 |
| 59  | ENSG00000155463 | NA | OXA1L | oxidase (cytochrome c) assembly 1-like | 5018 | ENSG00000155463 |
| 60  | ENSG00000167863 | NA | ATP5H | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d | 10476 | ENSG00000167863 |
| 61  | ENSG00000090266 | NA | NDUFB2 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa | 4708 | ENSG00000090266 |
| 62  | ENSG00000127540 | NA | UQCR11 | ubiquinol-cytochrome c reductase, complex III subunit XI | 10975 | ENSG00000127540 |
| 63  | ENSG00000179091 | NA | CYC1 | cytochrome c-1 | 1537 | ENSG00000179091 |
| 64  | ENSG00000184752 | NA | NDUFA12 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 | 55967 | ENSG00000184752 |
| 65  | ENSG00000156411 | NA | C14orf2 | chromosome 14 open reading frame 2 | 9556 | ENSG00000156411 |
| 66  | ENSG00000131844 | NA | MCCC2 | methylcrotonoyl-CoA carboxylase 2 (beta) | 64087 | ENSG00000131844 |
| 67  | ENSG00000159199 | NA | ATP5G1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) | 516 | ENSG00000159199 |
| 68  | ENSG00000105819 | NA | PMPCB | peptidase (mitochondrial processing) beta | 9512 | ENSG00000105819 |
| 69  | ENSG00000150779 | NA | TIMM8B | translocase of inner mitochondrial membrane 8 homolog B (yeast) | 26521 | ENSG00000150779 |
| 70  | ENSG00000166855 | NA | CLPX | ClpX caseinolytic peptidase X homolog (E. coli) | 10845 | ENSG00000166855 |
| 71  | ENSG00000074582 | NA | BCS1L | BCS1-like (S. cerevisiae) | 617 | ENSG00000074582 |
| 72  | ENSG00000103018 | NA | CYB5B | cytochrome b5 type B (outer mitochondrial membrane) | 80777 | ENSG00000103018 |
| 73  | ENSG00000166816 | NA | LDHD | lactate dehydrogenase D | 197257 | ENSG00000166816 |
| 74  | ENSG00000140990 | NA | NDUFB10 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa | 4716 | ENSG00000140990 |
| 75  | ENSG00000066926 | NA | FECH | ferrochelatase | 2235 | ENSG00000066926 |
| 76  | ENSG00000117118 | NA | SDHB | succinate dehydrogenase complex, subunit B, iron sulfur (Ip) | 6390 | ENSG00000117118 |
| 77  | ENSG00000135469 | NA | COQ10A | coenzyme Q10 homolog A (S. cerevisiae) | 93058 | ENSG00000135469 |
| 78  | ENSG00000165629 | NA | ATP5C1 | ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 | 509 | ENSG00000165629 |
| 79  | ENSG00000115944 | NA | COX7A2L | cytochrome c oxidase subunit VIIa polypeptide 2 like | 9167 | ENSG00000115944 |
| 80  | ENSG00000148290 | NA | SURF1 | surfeit 1 | 6834 | ENSG00000148290 |
| 81  | ENSG00000197150 | NA | ABCB8 | ATP-binding cassette, sub-family B (MDR/TAP), member 8 | 11194 | ENSG00000197150 |
| 82  | ENSG00000152234 | NA | ATP5A1 | ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle | 498 | ENSG00000152234 |
| 83  | ENSG00000072778 | NA | ACADVL | acyl-CoA dehydrogenase, very long chain | 37 | ENSG00000072778 |
| 84  | ENSG00000151366 | NA | NDUFC2 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa | 4718 | ENSG00000151366 |
| 85  | ENSG00000128609 | NA | NDUFA5 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa | 4698 | ENSG00000128609 |
| 86  | ENSG00000132305 | NA | IMMT | inner membrane protein, mitochondrial | 10989 | ENSG00000132305 |
| 87  | ENSG00000163541 | NA | SUCLG1 | succinate-CoA ligase, alpha subunit | 8802 | ENSG00000163541 |
| 88  | ENSG00000146701 | NA | MDH2 | malate dehydrogenase 2, NAD (mitochondrial) | 4191 | ENSG00000146701 |
| 89  | ENSG00000165678 | NA | GHITM | growth hormone inducible transmembrane protein | 27069 | ENSG00000165678 |
| 90  | ENSG00000125995 | NA | ROMO1 | reactive oxygen species modulator 1 | 140823 | ENSG00000125995 |
| 91  | ENSG00000136521 | NA | NDUFB5 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa | 4711 | ENSG00000136521 |
| 92  | ENSG00000173915 | NA | USMG5 | up-regulated during skeletal muscle growth 5 homolog (mouse) | 84833 | ENSG00000173915 |
| 93  | ENSG00000182054 | NA | IDH2 | isocitrate dehydrogenase 2 (NADP+), mitochondrial | 3418 | ENSG00000182054 |
| 94  | ENSG00000004779 | NA | NDUFAB1 | NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa | 4706 | ENSG00000004779 |
| 95  | ENSG00000131730 | NA | CKMT2 | creatine kinase, mitochondrial 2 (sarcomeric) | 1160 | ENSG00000131730 |
| 96  | ENSG00000169020 | NA | ATP5I | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E | 521 | ENSG00000169020 |
| 97  | ENSG00000004961 | NA | HCCS | holocytochrome c synthase | 3052 | ENSG00000004961 |
| 98  | ENSG00000147123 | NA | NDUFB11 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa | 54539 | ENSG00000147123 |
| 99  | ENSG00000073578 | NA | SDHA | succinate dehydrogenase complex, subunit A, flavoprotein (Fp) | 6389 | ENSG00000073578 |
| 100  | ENSG00000137714 | NA | FDX1 | ferredoxin 1 | 2230 | ENSG00000137714 |
| 101  | ENSG00000119013 | NA | NDUFB3 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa | 4709 | ENSG00000119013 |
| 102  | ENSG00000169021 | NA | UQCRFS1 | ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 | 7386 | ENSG00000169021 |
| 103  | ENSG00000175193 | NA | PARL | presenilin associated, rhomboid-like | 55486 | ENSG00000175193 |
| 104  | ENSG00000108179 | NA | PPIF | peptidylprolyl isomerase F | 10105 | ENSG00000108179 |
| 105  | ENSG00000139180 | NA | NDUFA9 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa | 4704 | ENSG00000139180 |
| 106  | ENSG00000162600 | NA | OMA1 | OMA1 zinc metallopeptidase homolog (S. cerevisiae) | 115209 | ENSG00000162600 |
| 107  | ENSG00000127184 | NA | COX7C | cytochrome c oxidase subunit VIIc | 1350 | ENSG00000127184 |
| 108  | ENSG00000164405 | NA | UQCRQ | ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa | 27089 | ENSG00000164405 |
| 109  | ENSG00000165637 | NA | VDAC2 | voltage-dependent anion channel 2 | 7417 | ENSG00000165637 |
| 110  | ENSG00000124172 | NA | ATP5E | ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit | 514 | ENSG00000124172 |
| 111  | ENSG00000183648 | NA | NDUFB1 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa | 4707 | ENSG00000183648 |
| 112  | ENSG00000132591 | NA | ERAL1 | Era G-protein-like 1 (E. coli) | 26284 | ENSG00000132591 |
| 113  | ENSG00000205981 | NA | DNAJC19 | DnaJ (Hsp40) homolog, subfamily C, member 19 | 131118 | ENSG00000205981 |
| 114  | ENSG00000213585 | NA | VDAC1 | voltage-dependent anion channel 1 | 7416 | ENSG00000213585 |
| 115  | ENSG00000204370 | NA | SDHD | succinate dehydrogenase complex, subunit D, integral membrane protein | 6392 | ENSG00000204370 |
| 116  | ENSG00000099624 | NA | ATP5D | ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit | 513 | ENSG00000099624 |
| 117  | ENSG00000106554 | NA | CHCHD3 | coiled-coil-helix-coiled-coil-helix domain containing 3 | 54927 | ENSG00000106554 |
| 118  | ENSG00000166949 | NA | SMAD3 | SMAD family member 3 | 4088 | ENSG00000166949 |
| 119  | ENSG00000125356 | NA | NDUFA1 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa | 4694 | ENSG00000125356 |
| 120  | ENSG00000108528 | NA | SLC25A11 | solute carrier family 25 (mitochondrial carrier; oxoglutarate carrier), member 11 | 8402 | ENSG00000108528 |
| 121  | ENSG00000099795 | NA | NDUFB7 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa | 4713 | ENSG00000099795 |
| 122  | ENSG00000174032 | NA | SLC25A30 | solute carrier family 25, member 30 | 253512 | ENSG00000174032 |
| 123  | ENSG00000023228 | NA | NDUFS1 | NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) | 4719 | ENSG00000023228 |
| 124  | ENSG00000143252 | NA | SDHC | succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa | 6391 | ENSG00000143252 |
| 125  | ENSG00000115840 | NA | SLC25A12 | solute carrier family 25 (aspartate/glutamate carrier), member 12 | 8604 | ENSG00000115840 |
| 126  | ENSG00000110955 | NA | ATP5B | ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide | 506 | ENSG00000110955 |
| 127  | ENSG00000197122 | NA | SRC | v-src sarcoma (Schmidt-Ruppin A-2) viral oncogene homolog (avian) | 6714 | ENSG00000197122 |
| 128  | ENSG00000112695 | NA | COX7A2 | cytochrome c oxidase subunit VIIa polypeptide 2 (liver) | 1347 | ENSG00000112695 |
| 129  | ENSG00000197448 | NA | GSTK1 | glutathione S-transferase kappa 1 | 373156 | ENSG00000197448 |
| 130  | ENSG00000167792 | NA | NDUFV1 | NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa | 4723 | ENSG00000167792 |
| 131  | ENSG00000131495 | NA | NDUFA2 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa | 4695 | ENSG00000131495 |
| 132  | ENSG00000065518 | NA | NDUFB4 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa | 4710 | ENSG00000065518 |
| 133  | ENSG00000095321 | NA | CRAT | carnitine O-acetyltransferase | 1384 | ENSG00000095321 |
| 134  | ENSG00000165688 | NA | PMPCA | peptidase (mitochondrial processing) alpha | 23203 | ENSG00000165688 |
| 135  | ENSG00000110717 | NA | NDUFS8 | NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) | 4728 | ENSG00000110717 |
| 136  | ENSG00000131174 | NA | COX7B | cytochrome c oxidase subunit VIIb | 1349 | ENSG00000131174 |
| 137  | ENSG00000170906 | NA | NDUFA3 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa | 4696 | ENSG00000170906 |
| 138  | ENSG00000167283 | NA | ATP5L | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G | 10632 | ENSG00000167283 |
| 139  | ENSG00000124532 | NA | MRS2 | MRS2 magnesium homeostasis factor homolog (S. cerevisiae) | 57380 | ENSG00000124532 |
| 140  | ENSG00000131269 | NA | ABCB7 | ATP-binding cassette, sub-family B (MDR/TAP), member 7 | 22 | ENSG00000131269 |
| 141  | ENSG00000010256 | NA | UQCRC1 | ubiquinol-cytochrome c reductase core protein I | 7384 | ENSG00000010256 |
| 142  | ENSG00000137806 | NA | NDUFAF1 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 | 51103 | ENSG00000137806 |
| 143  | ENSG00000241468 | NA | ATP5J2 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 | 9551 | ENSG00000241468 |
| 144  | ENSG00000171503 | NA | ETFDH | electron-transferring-flavoprotein dehydrogenase | 2110 | ENSG00000171503 |
| 145  | ENSG00000143158 | NA | MPC2 | mitochondrial pyruvate carrier 2 | 25874 | ENSG00000143158 |
| 146  | ENSG00000138796 | NA | HADH | hydroxyacyl-CoA dehydrogenase | 3033 | ENSG00000138796 |
| 147  | ENSG00000154518 | NA | ATP5G3 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C3 (subunit 9) | 518 | ENSG00000154518 |
| 148  | ENSG00000075303 | NA | SLC25A40 | solute carrier family 25, member 40 | 55972 | ENSG00000075303 |
| 149  | ENSG00000176340 | NA | COX8A | cytochrome c oxidase subunit VIIIA (ubiquitous) | 1351 | ENSG00000176340 |
| 150  | ENSG00000101247 | NA | NDUFAF5 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 5 | 79133 | ENSG00000101247 |
| 151  | ENSG00000168653 | NA | NDUFS5 | NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) | 4725 | ENSG00000168653 |
| 152  | ENSG00000126768 | NA | TIMM17B | translocase of inner mitochondrial membrane 17 homolog B (yeast) | 10245 | ENSG00000126768 |
| 153  | ENSG00000241837 | NA | ATP5O | ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit | 539 | ENSG00000241837 |
| Database:cellular component       Name:mitochondrial membrane       ID:GO:0031966 | ||||||
|---|---|---|---|---|---|---|
| C=508; O=174; E=30.83; R=5.64; rawP=4.88e-86; adjP=2.76e-84 | ||||||
| Index | UserID | Value | Gene Symbol | Gene Name | EntrezGene | Ensembl |
| 1  | ENSG00000087299 | NA | L2HGDH | L-2-hydroxyglutarate dehydrogenase | 79944 | ENSG00000087299 |
| 2  | ENSG00000184903 | NA | IMMP2L | IMP2 inner mitochondrial membrane peptidase-like (S. cerevisiae) | 83943 | ENSG00000184903 |
| 3  | ENSG00000165264 | NA | NDUFB6 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa | 4712 | ENSG00000165264 |
| 4  | ENSG00000156467 | NA | UQCRB | ubiquinol-cytochrome c reductase binding protein | 7381 | ENSG00000156467 |
| 5  | ENSG00000161281 | NA | COX7A1 | cytochrome c oxidase subunit VIIa polypeptide 1 (muscle) | 1346 | ENSG00000161281 |
| 6  | ENSG00000184076 | NA | UQCR10 | ubiquinol-cytochrome c reductase, complex III subunit X | 29796 | ENSG00000184076 |
| 7  | ENSG00000078070 | NA | MCCC1 | methylcrotonoyl-CoA carboxylase 1 (alpha) | 56922 | ENSG00000078070 |
| 8  | ENSG00000075415 | NA | SLC25A3 | solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 3 | 5250 | ENSG00000075415 |
| 9  | ENSG00000156885 | NA | COX6A2 | cytochrome c oxidase subunit VIa polypeptide 2 | 1339 | ENSG00000156885 |
| 10  | ENSG00000006695 | NA | COX10 | COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) | 1352 | ENSG00000006695 |
| 11  | ENSG00000133983 | NA | COX16 | COX16 cytochrome c oxidase assembly homolog (S. cerevisiae) | 51241 | ENSG00000133983 |
| 12  | ENSG00000154723 | NA | ATP5J | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 | 522 | ENSG00000154723 |
| 13  | ENSG00000167969 | NA | ECI1 | enoyl-CoA delta isomerase 1 | 1632 | ENSG00000167969 |
| 14  | ENSG00000125166 | NA | GOT2 | glutamic-oxaloacetic transaminase 2, mitochondrial (aspartate aminotransferase 2) | 2806 | ENSG00000125166 |
| 15  | ENSG00000100347 | NA | SAMM50 | sorting and assembly machinery component 50 homolog (S. cerevisiae) | 25813 | ENSG00000100347 |
| 16  | ENSG00000135390 | NA | ATP5G2 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C2 (subunit 9) | 517 | ENSG00000135390 |
| 17  | ENSG00000177370 | NA | TIMM22 | translocase of inner mitochondrial membrane 22 homolog (yeast) | 29928 | ENSG00000177370 |
| 18  | ENSG00000140740 | NA | UQCRC2 | ubiquinol-cytochrome c reductase core protein II | 7385 | ENSG00000140740 |
| 19  | ENSG00000166136 | NA | NDUFB8 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa | 4714 | ENSG00000166136 |
| 20  | ENSG00000160194 | NA | NDUFV3 | NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa | 4731 | ENSG00000160194 |
| 21  | ENSG00000147684 | NA | NDUFB9 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa | 4715 | ENSG00000147684 |
| 22  | ENSG00000184983 | NA | NDUFA6 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa | 4700 | ENSG00000184983 |
| 23  | ENSG00000130414 | NA | NDUFA10 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa | 4705 | ENSG00000130414 |
| 24  | ENSG00000163626 | NA | COX18 | COX18 cytochrome c oxidase assembly homolog (S. cerevisiae) | 285521 | ENSG00000163626 |
| 25  | ENSG00000158864 | NA | NDUFS2 | NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) | 4720 | ENSG00000158864 |
| 26  | ENSG00000007923 | NA | DNAJC11 | DnaJ (Hsp40) homolog, subfamily C, member 11 | 55735 | ENSG00000007923 |
| 27  | ENSG00000173436 | NA | MINOS1 | mitochondrial inner membrane organizing system 1 | 440574 | ENSG00000173436 |
| 28  | ENSG00000105197 | NA | TIMM50 | translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae) | 92609 | ENSG00000105197 |
| 29  | ENSG00000109390 | NA | NDUFC1 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa | 4717 | ENSG00000109390 |
| 30  | ENSG00000060762 | NA | MPC1 | mitochondrial pyruvate carrier 1 | 51660 | ENSG00000060762 |
| 31  | ENSG00000165283 | NA | STOML2 | stomatin (EPB72)-like 2 | 30968 | ENSG00000165283 |
| 32  | ENSG00000104980 | NA | TIMM44 | translocase of inner mitochondrial membrane 44 homolog (yeast) | 10469 | ENSG00000104980 |
| 33  | ENSG00000116459 | NA | ATP5F1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 | 515 | ENSG00000116459 |
| 34  | ENSG00000164466 | NA | SFXN1 | sideroflexin 1 | 94081 | ENSG00000164466 |
| 35  | ENSG00000099800 | NA | TIMM13 | translocase of inner mitochondrial membrane 13 homolog (yeast) | 26517 | ENSG00000099800 |
| 36  | ENSG00000151729 | NA | SLC25A4 | solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4 | 291 | ENSG00000151729 |
| 37  | ENSG00000178057 | NA | NDUFAF3 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 3 | 25915 | ENSG00000178057 |
| 38  | ENSG00000112992 | NA | NNT | nicotinamide nucleotide transhydrogenase | 23530 | ENSG00000112992 |
| 39  | ENSG00000213619 | NA | NDUFS3 | NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) | 4722 | ENSG00000213619 |
| 40  | ENSG00000178741 | NA | COX5A | cytochrome c oxidase subunit Va | 9377 | ENSG00000178741 |
| 41  | ENSG00000173660 | NA | UQCRH | ubiquinol-cytochrome c reductase hinge protein | 7388 | ENSG00000173660 |
| 42  | ENSG00000214253 | NA | FIS1 | fission 1 (mitochondrial outer membrane) homolog (S. cerevisiae) | 51024 | ENSG00000214253 |
| 43  | ENSG00000133028 | NA | SCO1 | SCO cytochrome oxidase deficient homolog 1 (yeast) | 6341 | ENSG00000133028 |
| 44  | ENSG00000148950 | NA | IMMP1L | IMP1 inner mitochondrial membrane peptidase-like (S. cerevisiae) | 196294 | ENSG00000148950 |
| 45  | ENSG00000119421 | NA | NDUFA8 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa | 4702 | ENSG00000119421 |
| 46  | ENSG00000126267 | NA | COX6B1 | cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) | 1340 | ENSG00000126267 |
| 47  | ENSG00000109919 | NA | MTCH2 | mitochondrial carrier 2 | 23788 | ENSG00000109919 |
| 48  | ENSG00000135940 | NA | COX5B | cytochrome c oxidase subunit Vb | 1329 | ENSG00000135940 |
| 49  | ENSG00000215021 | NA | PHB2 | prohibitin 2 | 11331 | ENSG00000215021 |
| 50  | ENSG00000145494 | NA | NDUFS6 | NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) | 4726 | ENSG00000145494 |
| 51  | ENSG00000167085 | NA | PHB | prohibitin | 5245 | ENSG00000167085 |
| 52  | ENSG00000072506 | NA | HSD17B10 | hydroxysteroid (17-beta) dehydrogenase 10 | 3028 | ENSG00000072506 |
| 53  | ENSG00000156709 | NA | AIFM1 | apoptosis-inducing factor, mitochondrion-associated, 1 | 9131 | ENSG00000156709 |
| 54  | ENSG00000189043 | NA | NDUFA4 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa | 4697 | ENSG00000189043 |
| 55  | ENSG00000131143 | NA | COX4I1 | cytochrome c oxidase subunit IV isoform 1 | 1327 | ENSG00000131143 |
| 56  | ENSG00000172115 | NA | CYCS | cytochrome c, somatic | 54205 | ENSG00000172115 |
| 57  | ENSG00000164919 | NA | COX6C | cytochrome c oxidase subunit VIc | 1345 | ENSG00000164919 |
| 58  | ENSG00000115286 | NA | NDUFS7 | NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) | 374291 | ENSG00000115286 |
| 59  | ENSG00000164258 | NA | NDUFS4 | NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) | 4724 | ENSG00000164258 |
| 60  | ENSG00000156170 | NA | NDUFAF6 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 | 137682 | ENSG00000156170 |
| 61  | ENSG00000155463 | NA | OXA1L | oxidase (cytochrome c) assembly 1-like | 5018 | ENSG00000155463 |
| 62  | ENSG00000167863 | NA | ATP5H | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d | 10476 | ENSG00000167863 |
| 63  | ENSG00000090266 | NA | NDUFB2 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa | 4708 | ENSG00000090266 |
| 64  | ENSG00000127540 | NA | UQCR11 | ubiquinol-cytochrome c reductase, complex III subunit XI | 10975 | ENSG00000127540 |
| 65  | ENSG00000179091 | NA | CYC1 | cytochrome c-1 | 1537 | ENSG00000179091 |
| 66  | ENSG00000184752 | NA | NDUFA12 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 | 55967 | ENSG00000184752 |
| 67  | ENSG00000156411 | NA | C14orf2 | chromosome 14 open reading frame 2 | 9556 | ENSG00000156411 |
| 68  | ENSG00000131844 | NA | MCCC2 | methylcrotonoyl-CoA carboxylase 2 (beta) | 64087 | ENSG00000131844 |
| 69  | ENSG00000159199 | NA | ATP5G1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) | 516 | ENSG00000159199 |
| 70  | ENSG00000105819 | NA | PMPCB | peptidase (mitochondrial processing) beta | 9512 | ENSG00000105819 |
| 71  | ENSG00000150779 | NA | TIMM8B | translocase of inner mitochondrial membrane 8 homolog B (yeast) | 26521 | ENSG00000150779 |
| 72  | ENSG00000166855 | NA | CLPX | ClpX caseinolytic peptidase X homolog (E. coli) | 10845 | ENSG00000166855 |
| 73  | ENSG00000196683 | NA | TOMM7 | translocase of outer mitochondrial membrane 7 homolog (yeast) | 54543 | ENSG00000196683 |
| 74  | ENSG00000074582 | NA | BCS1L | BCS1-like (S. cerevisiae) | 617 | ENSG00000074582 |
| 75  | ENSG00000103018 | NA | CYB5B | cytochrome b5 type B (outer mitochondrial membrane) | 80777 | ENSG00000103018 |
| 76  | ENSG00000166816 | NA | LDHD | lactate dehydrogenase D | 197257 | ENSG00000166816 |
| 77  | ENSG00000140990 | NA | NDUFB10 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa | 4716 | ENSG00000140990 |
| 78  | ENSG00000066926 | NA | FECH | ferrochelatase | 2235 | ENSG00000066926 |
| 79  | ENSG00000117118 | NA | SDHB | succinate dehydrogenase complex, subunit B, iron sulfur (Ip) | 6390 | ENSG00000117118 |
| 80  | ENSG00000198523 | NA | PLN | phospholamban | 5350 | ENSG00000198523 |
| 81  | ENSG00000006530 | NA | AGK | acylglycerol kinase | 55750 | ENSG00000006530 |
| 82  | ENSG00000135469 | NA | COQ10A | coenzyme Q10 homolog A (S. cerevisiae) | 93058 | ENSG00000135469 |
| 83  | ENSG00000177427 | NA | SMCR7 | Smith-Magenis syndrome chromosome region, candidate 7 | 125170 | ENSG00000177427 |
| 84  | ENSG00000165629 | NA | ATP5C1 | ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 | 509 | ENSG00000165629 |
| 85  | ENSG00000115944 | NA | COX7A2L | cytochrome c oxidase subunit VIIa polypeptide 2 like | 9167 | ENSG00000115944 |
| 86  | ENSG00000123545 | NA | NDUFAF4 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 4 | 29078 | ENSG00000123545 |
| 87  | ENSG00000148290 | NA | SURF1 | surfeit 1 | 6834 | ENSG00000148290 |
| 88  | ENSG00000197150 | NA | ABCB8 | ATP-binding cassette, sub-family B (MDR/TAP), member 8 | 11194 | ENSG00000197150 |
| 89  | ENSG00000152234 | NA | ATP5A1 | ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle | 498 | ENSG00000152234 |
| 90  | ENSG00000072778 | NA | ACADVL | acyl-CoA dehydrogenase, very long chain | 37 | ENSG00000072778 |
| 91  | ENSG00000151366 | NA | NDUFC2 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa | 4718 | ENSG00000151366 |
| 92  | ENSG00000128609 | NA | NDUFA5 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa | 4698 | ENSG00000128609 |
| 93  | ENSG00000132305 | NA | IMMT | inner membrane protein, mitochondrial | 10989 | ENSG00000132305 |
| 94  | ENSG00000163541 | NA | SUCLG1 | succinate-CoA ligase, alpha subunit | 8802 | ENSG00000163541 |
| 95  | ENSG00000090432 | NA | MUL1 | mitochondrial E3 ubiquitin protein ligase 1 | 79594 | ENSG00000090432 |
| 96  | ENSG00000146701 | NA | MDH2 | malate dehydrogenase 2, NAD (mitochondrial) | 4191 | ENSG00000146701 |
| 97  | ENSG00000165678 | NA | GHITM | growth hormone inducible transmembrane protein | 27069 | ENSG00000165678 |
| 98  | ENSG00000125995 | NA | ROMO1 | reactive oxygen species modulator 1 | 140823 | ENSG00000125995 |
| 99  | ENSG00000136521 | NA | NDUFB5 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa | 4711 | ENSG00000136521 |
| 100  | ENSG00000173915 | NA | USMG5 | up-regulated during skeletal muscle growth 5 homolog (mouse) | 84833 | ENSG00000173915 |
| 101  | ENSG00000169020 | NA | ATP5I | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E | 521 | ENSG00000169020 |
| 102  | ENSG00000158882 | NA | TOMM40L | translocase of outer mitochondrial membrane 40 homolog (yeast)-like | 84134 | ENSG00000158882 |
| 103  | ENSG00000182054 | NA | IDH2 | isocitrate dehydrogenase 2 (NADP+), mitochondrial | 3418 | ENSG00000182054 |
| 104  | ENSG00000004779 | NA | NDUFAB1 | NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa | 4706 | ENSG00000004779 |
| 105  | ENSG00000131730 | NA | CKMT2 | creatine kinase, mitochondrial 2 (sarcomeric) | 1160 | ENSG00000131730 |
| 106  | ENSG00000168958 | NA | MFF | mitochondrial fission factor | 56947 | ENSG00000168958 |
| 107  | ENSG00000164038 | NA | SLC9B2 | solute carrier family 9, subfamily B (NHA2, cation proton antiporter 2), member 2 | 133308 | ENSG00000164038 |
| 108  | ENSG00000004961 | NA | HCCS | holocytochrome c synthase | 3052 | ENSG00000004961 |
| 109  | ENSG00000147123 | NA | NDUFB11 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa | 54539 | ENSG00000147123 |
| 110  | ENSG00000073578 | NA | SDHA | succinate dehydrogenase complex, subunit A, flavoprotein (Fp) | 6389 | ENSG00000073578 |
| 111  | ENSG00000137714 | NA | FDX1 | ferredoxin 1 | 2230 | ENSG00000137714 |
| 112  | ENSG00000119013 | NA | NDUFB3 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa | 4709 | ENSG00000119013 |
| 113  | ENSG00000169021 | NA | UQCRFS1 | ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 | 7386 | ENSG00000169021 |
| 114  | ENSG00000178449 | NA | COX14 | COX14 cytochrome c oxidase assembly homolog (S. cerevisiae) | 84987 | ENSG00000178449 |
| 115  | ENSG00000175193 | NA | PARL | presenilin associated, rhomboid-like | 55486 | ENSG00000175193 |
| 116  | ENSG00000078668 | NA | VDAC3 | voltage-dependent anion channel 3 | 7419 | ENSG00000078668 |
| 117  | ENSG00000111843 | NA | TMEM14C | transmembrane protein 14C | 51522 | ENSG00000111843 |
| 118  | ENSG00000108179 | NA | PPIF | peptidylprolyl isomerase F | 10105 | ENSG00000108179 |
| 119  | ENSG00000139180 | NA | NDUFA9 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa | 4704 | ENSG00000139180 |
| 120  | ENSG00000162600 | NA | OMA1 | OMA1 zinc metallopeptidase homolog (S. cerevisiae) | 115209 | ENSG00000162600 |
| 121  | ENSG00000127184 | NA | COX7C | cytochrome c oxidase subunit VIIc | 1350 | ENSG00000127184 |
| 122  | ENSG00000164405 | NA | UQCRQ | ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa | 27089 | ENSG00000164405 |
| 123  | ENSG00000165637 | NA | VDAC2 | voltage-dependent anion channel 2 | 7417 | ENSG00000165637 |
| 124  | ENSG00000173085 | NA | COQ2 | coenzyme Q2 homolog, prenyltransferase (yeast) | 27235 | ENSG00000173085 |
| 125  | ENSG00000124172 | NA | ATP5E | ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit | 514 | ENSG00000124172 |
| 126  | ENSG00000183648 | NA | NDUFB1 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa | 4707 | ENSG00000183648 |
| 127  | ENSG00000213585 | NA | VDAC1 | voltage-dependent anion channel 1 | 7416 | ENSG00000213585 |
| 128  | ENSG00000205981 | NA | DNAJC19 | DnaJ (Hsp40) homolog, subfamily C, member 19 | 131118 | ENSG00000205981 |
| 129  | ENSG00000132591 | NA | ERAL1 | Era G-protein-like 1 (E. coli) | 26284 | ENSG00000132591 |
| 130  | ENSG00000204370 | NA | SDHD | succinate dehydrogenase complex, subunit D, integral membrane protein | 6392 | ENSG00000204370 |
| 131  | ENSG00000099624 | NA | ATP5D | ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit | 513 | ENSG00000099624 |
| 132  | ENSG00000106554 | NA | CHCHD3 | coiled-coil-helix-coiled-coil-helix domain containing 3 | 54927 | ENSG00000106554 |
| 133  | ENSG00000125356 | NA | NDUFA1 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa | 4694 | ENSG00000125356 |
| 134  | ENSG00000108528 | NA | SLC25A11 | solute carrier family 25 (mitochondrial carrier; oxoglutarate carrier), member 11 | 8402 | ENSG00000108528 |
| 135  | ENSG00000099795 | NA | NDUFB7 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa | 4713 | ENSG00000099795 |
| 136  | ENSG00000174032 | NA | SLC25A30 | solute carrier family 25, member 30 | 253512 | ENSG00000174032 |
| 137  | ENSG00000023228 | NA | NDUFS1 | NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) | 4719 | ENSG00000023228 |
| 138  | ENSG00000143252 | NA | SDHC | succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa | 6391 | ENSG00000143252 |
| 139  | ENSG00000075336 | NA | TIMM21 | translocase of inner mitochondrial membrane 21 homolog (yeast) | 29090 | ENSG00000075336 |
| 140  | ENSG00000115840 | NA | SLC25A12 | solute carrier family 25 (aspartate/glutamate carrier), member 12 | 8604 | ENSG00000115840 |
| 141  | ENSG00000110955 | NA | ATP5B | ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide | 506 | ENSG00000110955 |
| 142  | ENSG00000197122 | NA | SRC | v-src sarcoma (Schmidt-Ruppin A-2) viral oncogene homolog (avian) | 6714 | ENSG00000197122 |
| 143  | ENSG00000112695 | NA | COX7A2 | cytochrome c oxidase subunit VIIa polypeptide 2 (liver) | 1347 | ENSG00000112695 |
| 144  | ENSG00000197448 | NA | GSTK1 | glutathione S-transferase kappa 1 | 373156 | ENSG00000197448 |
| 145  | ENSG00000167792 | NA | NDUFV1 | NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa | 4723 | ENSG00000167792 |
| 146  | ENSG00000131495 | NA | NDUFA2 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa | 4695 | ENSG00000131495 |
| 147  | ENSG00000065518 | NA | NDUFB4 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa | 4710 | ENSG00000065518 |
| 148  | ENSG00000095321 | NA | CRAT | carnitine O-acetyltransferase | 1384 | ENSG00000095321 |
| 149  | ENSG00000165688 | NA | PMPCA | peptidase (mitochondrial processing) alpha | 23203 | ENSG00000165688 |
| 150  | ENSG00000110717 | NA | NDUFS8 | NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) | 4728 | ENSG00000110717 |
| 151  | ENSG00000131174 | NA | COX7B | cytochrome c oxidase subunit VIIb | 1349 | ENSG00000131174 |
| 152  | ENSG00000170906 | NA | NDUFA3 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa | 4696 | ENSG00000170906 |
| 153  | ENSG00000128654 | NA | MTX2 | metaxin 2 | 10651 | ENSG00000128654 |
| 154  | ENSG00000204308 | NA | RNF5 | ring finger protein 5, E3 ubiquitin protein ligase | 6048 | ENSG00000204308 |
| 155  | ENSG00000167283 | NA | ATP5L | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G | 10632 | ENSG00000167283 |
| 156  | ENSG00000069509 | NA | FUNDC1 | FUN14 domain containing 1 | 139341 | ENSG00000069509 |
| 157  | ENSG00000183978 | NA | COA3 | cytochrome C oxidase assembly factor 3 | 28958 | ENSG00000183978 |
| 158  | ENSG00000124532 | NA | MRS2 | MRS2 magnesium homeostasis factor homolog (S. cerevisiae) | 57380 | ENSG00000124532 |
| 159  | ENSG00000131269 | NA | ABCB7 | ATP-binding cassette, sub-family B (MDR/TAP), member 7 | 22 | ENSG00000131269 |
| 160  | ENSG00000010256 | NA | UQCRC1 | ubiquinol-cytochrome c reductase core protein I | 7384 | ENSG00000010256 |
| 161  | ENSG00000137806 | NA | NDUFAF1 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 | 51103 | ENSG00000137806 |
| 162  | ENSG00000241468 | NA | ATP5J2 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 | 9551 | ENSG00000241468 |
| 163  | ENSG00000197912 | NA | SPG7 | spastic paraplegia 7 (pure and complicated autosomal recessive) | 6687 | ENSG00000197912 |
| 164  | ENSG00000171503 | NA | ETFDH | electron-transferring-flavoprotein dehydrogenase | 2110 | ENSG00000171503 |
| 165  | ENSG00000143158 | NA | MPC2 | mitochondrial pyruvate carrier 2 | 25874 | ENSG00000143158 |
| 166  | ENSG00000138796 | NA | HADH | hydroxyacyl-CoA dehydrogenase | 3033 | ENSG00000138796 |
| 167  | ENSG00000154518 | NA | ATP5G3 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C3 (subunit 9) | 518 | ENSG00000154518 |
| 168  | ENSG00000075303 | NA | SLC25A40 | solute carrier family 25, member 40 | 55972 | ENSG00000075303 |
| 169  | ENSG00000176340 | NA | COX8A | cytochrome c oxidase subunit VIIIA (ubiquitous) | 1351 | ENSG00000176340 |
| 170  | ENSG00000101247 | NA | NDUFAF5 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 5 | 79133 | ENSG00000101247 |
| 171  | ENSG00000168653 | NA | NDUFS5 | NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) | 4725 | ENSG00000168653 |
| 172  | ENSG00000126768 | NA | TIMM17B | translocase of inner mitochondrial membrane 17 homolog B (yeast) | 10245 | ENSG00000126768 |
| 173  | ENSG00000247077 | NA | PGAM5 | phosphoglycerate mutase family member 5 | 192111 | ENSG00000247077 |
| 174  | ENSG00000241837 | NA | ATP5O | ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit | 539 | ENSG00000241837 |
| Database:cellular component       Name:cytoplasmic part       ID:GO:0044444 | ||||||
|---|---|---|---|---|---|---|
| C=6772; O=698; E=411.01; R=1.70; rawP=3.35e-77; adjP=1.66e-75 | ||||||
| Index | UserID | Value | Gene Symbol | Gene Name | EntrezGene | Ensembl |
| 1  | ENSG00000143575 | NA | HAX1 | HCLS1 associated protein X-1 | 10456 | ENSG00000143575 |
| 2  | ENSG00000168803 | NA | ADAL | adenosine deaminase-like | 161823 | ENSG00000168803 |
| 3  | ENSG00000116898 | NA | MRPS15 | mitochondrial ribosomal protein S15 | 64960 | ENSG00000116898 |
| 4  | ENSG00000148672 | NA | GLUD1 | glutamate dehydrogenase 1 | 2746 | ENSG00000148672 |
| 5  | ENSG00000147592 | NA | LACTB2 | lactamase, beta 2 | 51110 | ENSG00000147592 |
| 6  | ENSG00000164172 | NA | MOCS2 | molybdenum cofactor synthesis 2 | 4338 | ENSG00000164172 |
| 7  | ENSG00000239264 | NA | TXNDC5 | thioredoxin domain containing 5 (endoplasmic reticulum) | 81567 | ENSG00000239264 |
| 8  | ENSG00000170296 | NA | GABARAP | GABA(A) receptor-associated protein | 11337 | ENSG00000170296 |
| 9  | ENSG00000135390 | NA | ATP5G2 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C2 (subunit 9) | 517 | ENSG00000135390 |
| 10  | ENSG00000134109 | NA | EDEM1 | ER degradation enhancer, mannosidase alpha-like 1 | 9695 | ENSG00000134109 |
| 11  | ENSG00000177370 | NA | TIMM22 | translocase of inner mitochondrial membrane 22 homolog (yeast) | 29928 | ENSG00000177370 |
| 12  | ENSG00000003509 | NA | C2orf56 | chromosome 2 open reading frame 56 | 55471 | ENSG00000003509 |
| 13  | ENSG00000116353 | NA | MECR | mitochondrial trans-2-enoyl-CoA reductase | 51102 | ENSG00000116353 |
| 14  | ENSG00000010282 | NA | HHATL | hedgehog acyltransferase-like | 57467 | ENSG00000010282 |
| 15  | ENSG00000205707 | NA | LYRM5 | LYR motif containing 5 | 144363 | ENSG00000205707 |
| 16  | ENSG00000165060 | NA | FXN | frataxin | 2395 | ENSG00000165060 |
| 17  | ENSG00000173141 | NA | MRP63 | mitochondrial ribosomal protein 63 | 78988 | ENSG00000173141 |
| 18  | ENSG00000109390 | NA | NDUFC1 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa | 4717 | ENSG00000109390 |
| 19  | ENSG00000125868 | NA | DSTN | destrin (actin depolymerizing factor) | 11034 | ENSG00000125868 |
| 20  | ENSG00000143314 | NA | MRPL24 | mitochondrial ribosomal protein L24 | 79590 | ENSG00000143314 |
| 21  | ENSG00000123384 | NA | LRP1 | low density lipoprotein receptor-related protein 1 | 4035 | ENSG00000123384 |
| 22  | ENSG00000103160 | NA | HSDL1 | hydroxysteroid dehydrogenase like 1 | 83693 | ENSG00000103160 |
| 23  | ENSG00000055950 | NA | MRPL43 | mitochondrial ribosomal protein L43 | 84545 | ENSG00000055950 |
| 24  | ENSG00000164054 | NA | SHISA5 | shisa homolog 5 (Xenopus laevis) | 51246 | ENSG00000164054 |
| 25  | ENSG00000135218 | NA | CD36 | CD36 molecule (thrombospondin receptor) | 948 | ENSG00000135218 |
| 26  | ENSG00000142082 | NA | SIRT3 | sirtuin 3 | 23410 | ENSG00000142082 |
| 27  | ENSG00000135070 | NA | ISCA1 | iron-sulfur cluster assembly 1 homolog (S. cerevisiae) | 81689 | ENSG00000135070 |
| 28  | ENSG00000127838 | NA | PNKD | paroxysmal nonkinesigenic dyskinesia | 25953 | ENSG00000127838 |
| 29  | ENSG00000204568 | NA | MRPS18B | mitochondrial ribosomal protein S18B | 28973 | ENSG00000204568 |
| 30  | ENSG00000148334 | NA | PTGES2 | prostaglandin E synthase 2 | 80142 | ENSG00000148334 |
| 31  | ENSG00000165283 | NA | STOML2 | stomatin (EPB72)-like 2 | 30968 | ENSG00000165283 |
| 32  | ENSG00000185627 | NA | PSMD13 | proteasome (prosome, macropain) 26S subunit, non-ATPase, 13 | 5719 | ENSG00000185627 |
| 33  | ENSG00000117697 | NA | NSL1 | NSL1, MIND kinetochore complex component, homolog (S. cerevisiae) | 25936 | ENSG00000117697 |
| 34  | ENSG00000149925 | NA | ALDOA | aldolase A, fructose-bisphosphate | 226 | ENSG00000149925 |
| 35  | ENSG00000126432 | NA | PRDX5 | peroxiredoxin 5 | 25824 | ENSG00000126432 |
| 36  | ENSG00000023330 | NA | ALAS1 | aminolevulinate, delta-, synthase 1 | 211 | ENSG00000023330 |
| 37  | ENSG00000213619 | NA | NDUFS3 | NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) | 4722 | ENSG00000213619 |
| 38  | ENSG00000178741 | NA | COX5A | cytochrome c oxidase subunit Va | 9377 | ENSG00000178741 |
| 39  | ENSG00000109180 | NA | OCIAD1 | OCIA domain containing 1 | 54940 | ENSG00000109180 |
| 40  | ENSG00000214253 | NA | FIS1 | fission 1 (mitochondrial outer membrane) homolog (S. cerevisiae) | 51024 | ENSG00000214253 |
| 41  | ENSG00000147586 | NA | MRPS28 | mitochondrial ribosomal protein S28 | 28957 | ENSG00000147586 |
| 42  | ENSG00000124570 | NA | SERPINB6 | serpin peptidase inhibitor, clade B (ovalbumin), member 6 | 5269 | ENSG00000124570 |
| 43  | ENSG00000169288 | NA | MRPL1 | mitochondrial ribosomal protein L1 | 65008 | ENSG00000169288 |
| 44  | ENSG00000160221 | NA | C21orf33 | chromosome 21 open reading frame 33 | 8209 | ENSG00000160221 |
| 45  | ENSG00000114854 | NA | TNNC1 | troponin C type 1 (slow) | 7134 | ENSG00000114854 |
| 46  | ENSG00000109919 | NA | MTCH2 | mitochondrial carrier 2 | 23788 | ENSG00000109919 |
| 47  | ENSG00000143436 | NA | MRPL9 | mitochondrial ribosomal protein L9 | 65005 | ENSG00000143436 |
| 48  | ENSG00000122140 | NA | MRPS2 | mitochondrial ribosomal protein S2 | 51116 | ENSG00000122140 |
| 49  | ENSG00000174175 | NA | SELP | selectin P (granule membrane protein 140kDa, antigen CD62) | 6403 | ENSG00000174175 |
| 50  | ENSG00000243279 | NA | PRAF2 | PRA1 domain family, member 2 | 11230 | ENSG00000243279 |
| 51  | ENSG00000156709 | NA | AIFM1 | apoptosis-inducing factor, mitochondrion-associated, 1 | 9131 | ENSG00000156709 |
| 52  | ENSG00000123739 | NA | PLA2G12A | phospholipase A2, group XIIA | 81579 | ENSG00000123739 |
| 53  | ENSG00000164919 | NA | COX6C | cytochrome c oxidase subunit VIc | 1345 | ENSG00000164919 |
| 54  | ENSG00000102871 | NA | TRADD | TNFRSF1A-associated via death domain | 8717 | ENSG00000102871 |
| 55  | ENSG00000196465 | NA | MYL6B | myosin, light chain 6B, alkali, smooth muscle and non-muscle | 140465 | ENSG00000196465 |
| 56  | ENSG00000139131 | NA | YARS2 | tyrosyl-tRNA synthetase 2, mitochondrial | 51067 | ENSG00000139131 |
| 57  | ENSG00000132570 | NA | PCBD2 | pterin-4 alpha-carbinolamine dehydratase/dimerization cofactor of hepatocyte nuclear factor 1 alpha (TCF1) 2 | 84105 | ENSG00000132570 |
| 58  | ENSG00000121766 | NA | ZCCHC17 | zinc finger, CCHC domain containing 17 | 51538 | ENSG00000121766 |
| 59  | ENSG00000167863 | NA | ATP5H | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d | 10476 | ENSG00000167863 |
| 60  | ENSG00000130203 | NA | APOE | apolipoprotein E | 348 | ENSG00000130203 |
| 61  | ENSG00000166165 | NA | CKB | creatine kinase, brain | 1152 | ENSG00000166165 |
| 62  | ENSG00000127540 | NA | UQCR11 | ubiquinol-cytochrome c reductase, complex III subunit XI | 10975 | ENSG00000127540 |
| 63  | ENSG00000197345 | NA | MRPL21 | mitochondrial ribosomal protein L21 | 219927 | ENSG00000197345 |
| 64  | ENSG00000184752 | NA | NDUFA12 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 | 55967 | ENSG00000184752 |
| 65  | ENSG00000132423 | NA | COQ3 | coenzyme Q3 homolog, methyltransferase (S. cerevisiae) | 51805 | ENSG00000132423 |
| 66  | ENSG00000156411 | NA | C14orf2 | chromosome 14 open reading frame 2 | 9556 | ENSG00000156411 |
| 67  | ENSG00000070756 | NA | PABPC1 | poly(A) binding protein, cytoplasmic 1 | 26986 | ENSG00000070756 |
| 68  | ENSG00000131844 | NA | MCCC2 | methylcrotonoyl-CoA carboxylase 2 (beta) | 64087 | ENSG00000131844 |
| 69  | ENSG00000173511 | NA | VEGFB | vascular endothelial growth factor B | 7423 | ENSG00000173511 |
| 70  | ENSG00000134905 | NA | CARS2 | cysteinyl-tRNA synthetase 2, mitochondrial (putative) | 79587 | ENSG00000134905 |
| 71  | ENSG00000150779 | NA | TIMM8B | translocase of inner mitochondrial membrane 8 homolog B (yeast) | 26521 | ENSG00000150779 |
| 72  | ENSG00000204228 | NA | HSD17B8 | hydroxysteroid (17-beta) dehydrogenase 8 | 7923 | ENSG00000204228 |
| 73  | ENSG00000179152 | NA | TCAIM | T cell activation inhibitor, mitochondrial | 285343 | ENSG00000179152 |
| 74  | ENSG00000067829 | NA | IDH3G | isocitrate dehydrogenase 3 (NAD+) gamma | 3421 | ENSG00000067829 |
| 75  | ENSG00000166902 | NA | MRPL16 | mitochondrial ribosomal protein L16 | 54948 | ENSG00000166902 |
| 76  | ENSG00000143742 | NA | SRP9 | signal recognition particle 9kDa | 6726 | ENSG00000143742 |
| 77  | ENSG00000198523 | NA | PLN | phospholamban | 5350 | ENSG00000198523 |
| 78  | ENSG00000247626 | NA | MARS2 | methionyl-tRNA synthetase 2, mitochondrial | 92935 | ENSG00000247626 |
| 79  | ENSG00000120662 | NA | MTRF1 | mitochondrial translational release factor 1 | 9617 | ENSG00000120662 |
| 80  | ENSG00000006530 | NA | AGK | acylglycerol kinase | 55750 | ENSG00000006530 |
| 81  | ENSG00000126602 | NA | TRAP1 | TNF receptor-associated protein 1 | 10131 | ENSG00000126602 |
| 82  | ENSG00000165629 | NA | ATP5C1 | ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 | 509 | ENSG00000165629 |
| 83  | ENSG00000224877 | NA | C17orf89 | chromosome 17 open reading frame 89 | 284184 | ENSG00000224877 |
| 84  | ENSG00000170860 | NA | LSM3 | LSM3 homolog, U6 small nuclear RNA associated (S. cerevisiae) | 27258 | ENSG00000170860 |
| 85  | ENSG00000148290 | NA | SURF1 | surfeit 1 | 6834 | ENSG00000148290 |
| 86  | ENSG00000014641 | NA | MDH1 | malate dehydrogenase 1, NAD (soluble) | 4190 | ENSG00000014641 |
| 87  | ENSG00000170634 | NA | ACYP2 | acylphosphatase 2, muscle type | 98 | ENSG00000170634 |
| 88  | ENSG00000154930 | NA | ACSS1 | acyl-CoA synthetase short-chain family member 1 | 84532 | ENSG00000154930 |
| 89  | ENSG00000054148 | NA | PHPT1 | phosphohistidine phosphatase 1 | 29085 | ENSG00000054148 |
| 90  | ENSG00000140319 | NA | SRP14 | signal recognition particle 14kDa (homologous Alu RNA binding protein) | 6727 | ENSG00000140319 |
| 91  | ENSG00000125652 | NA | ALKBH7 | alkB, alkylation repair homolog 7 (E. coli) | 84266 | ENSG00000125652 |
| 92  | ENSG00000196636 | NA | ACN9 | ACN9 homolog (S. cerevisiae) | 57001 | ENSG00000196636 |
| 93  | ENSG00000139410 | NA | SDSL | serine dehydratase-like | 113675 | ENSG00000139410 |
| 94  | ENSG00000059691 | NA | PET112 | PET112 homolog (yeast) | 5188 | ENSG00000059691 |
| 95  | ENSG00000187239 | NA | FNBP1 | formin binding protein 1 | 23048 | ENSG00000187239 |
| 96  | ENSG00000125995 | NA | ROMO1 | reactive oxygen species modulator 1 | 140823 | ENSG00000125995 |
| 97  | ENSG00000114021 | NA | NIT2 | nitrilase family, member 2 | 56954 | ENSG00000114021 |
| 98  | ENSG00000168958 | NA | MFF | mitochondrial fission factor | 56947 | ENSG00000168958 |
| 99  | ENSG00000120253 | NA | NUP43 | nucleoporin 43kDa | 348995 | ENSG00000120253 |
| 100  | ENSG00000085871 | NA | MGST2 | microsomal glutathione S-transferase 2 | 4258 | ENSG00000085871 |
| 101  | ENSG00000172954 | NA | LCLAT1 | lysocardiolipin acyltransferase 1 | 253558 | ENSG00000172954 |
| 102  | ENSG00000119013 | NA | NDUFB3 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa | 4709 | ENSG00000119013 |
| 103  | ENSG00000132463 | NA | GRSF1 | G-rich RNA sequence binding factor 1 | 2926 | ENSG00000132463 |
| 104  | ENSG00000259494 | NA | MRPL46 | mitochondrial ribosomal protein L46 | 26589 | ENSG00000259494 |
| 105  | ENSG00000116586 | NA | LAMTOR2 | late endosomal/lysosomal adaptor, MAPK and MTOR activator 2 | 28956 | ENSG00000116586 |
| 106  | ENSG00000165487 | NA | EFHA1 | EF-hand domain family, member A1 | 221154 | ENSG00000165487 |
| 107  | ENSG00000078668 | NA | VDAC3 | voltage-dependent anion channel 3 | 7419 | ENSG00000078668 |
| 108  | ENSG00000144827 | NA | ABHD10 | abhydrolase domain containing 10 | 55347 | ENSG00000144827 |
| 109  | ENSG00000173786 | NA | CNP | 2',3'-cyclic nucleotide 3' phosphodiesterase | 1267 | ENSG00000173786 |
| 110  | ENSG00000171130 | NA | ATP6V0E2 | ATPase, H+ transporting V0 subunit e2 | 155066 | ENSG00000171130 |
| 111  | ENSG00000143669 | NA | LYST | lysosomal trafficking regulator | 1130 | ENSG00000143669 |
| 112  | ENSG00000139180 | NA | NDUFA9 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa | 4704 | ENSG00000139180 |
| 113  | ENSG00000111640 | NA | GAPDH | glyceraldehyde-3-phosphate dehydrogenase | 2597 | ENSG00000111640 |
| 114  | ENSG00000135480 | NA | KRT7 | keratin 7 | 3855 | ENSG00000135480 |
| 115  | ENSG00000123836 | NA | PFKFB2 | 6-phosphofructo-2-kinase/fructose-2,6-biphosphatase 2 | 5208 | ENSG00000123836 |
| 116  | ENSG00000130208 | NA | APOC1 | apolipoprotein C-I | 341 | ENSG00000130208 |
| 117  | ENSG00000187118 | NA | CMC1 | COX assembly mitochondrial protein 1 homolog (S. cerevisiae) | 152100 | ENSG00000187118 |
| 118  | ENSG00000172878 | NA | METAP1D | methionyl aminopeptidase type 1D (mitochondrial) | 254042 | ENSG00000172878 |
| 119  | ENSG00000204370 | NA | SDHD | succinate dehydrogenase complex, subunit D, integral membrane protein | 6392 | ENSG00000204370 |
| 120  | ENSG00000106554 | NA | CHCHD3 | coiled-coil-helix-coiled-coil-helix domain containing 3 | 54927 | ENSG00000106554 |
| 121  | ENSG00000137106 | NA | GRHPR | glyoxylate reductase/hydroxypyruvate reductase | 9380 | ENSG00000137106 |
| 122  | ENSG00000107863 | NA | ARHGAP21 | Rho GTPase activating protein 21 | 57584 | ENSG00000107863 |
| 123  | ENSG00000027001 | NA | MIPEP | mitochondrial intermediate peptidase | 4285 | ENSG00000027001 |
| 124  | ENSG00000110048 | NA | OSBP | oxysterol binding protein | 5007 | ENSG00000110048 |
| 125  | ENSG00000182180 | NA | MRPS16 | mitochondrial ribosomal protein S16 | 51021 | ENSG00000182180 |
| 126  | ENSG00000174032 | NA | SLC25A30 | solute carrier family 25, member 30 | 253512 | ENSG00000174032 |
| 127  | ENSG00000066583 | NA | ISOC1 | isochorismatase domain containing 1 | 51015 | ENSG00000066583 |
| 128  | ENSG00000111669 | NA | TPI1 | triosephosphate isomerase 1 | 7167 | ENSG00000111669 |
| 129  | ENSG00000175756 | NA | AURKAIP1 | aurora kinase A interacting protein 1 | 54998 | ENSG00000175756 |
| 130  | ENSG00000138823 | NA | MTTP | microsomal triglyceride transfer protein | 4547 | ENSG00000138823 |
| 131  | ENSG00000143252 | NA | SDHC | succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa | 6391 | ENSG00000143252 |
| 132  | ENSG00000100116 | NA | GCAT | glycine C-acetyltransferase | 23464 | ENSG00000100116 |
| 133  | ENSG00000151376 | NA | ME3 | malic enzyme 3, NADP(+)-dependent, mitochondrial | 10873 | ENSG00000151376 |
| 134  | ENSG00000186318 | NA | BACE1 | beta-site APP-cleaving enzyme 1 | 23621 | ENSG00000265969 ENSG00000186318 |
| 135  | ENSG00000165775 | NA | FUNDC2 | FUN14 domain containing 2 | 65991 | ENSG00000165775 |
| 136  | ENSG00000182606 | NA | TRAK1 | trafficking protein, kinesin binding 1 | 22906 | ENSG00000182606 |
| 137  | ENSG00000110955 | NA | ATP5B | ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide | 506 | ENSG00000110955 |
| 138  | ENSG00000134248 | NA | LAMTOR5 | late endosomal/lysosomal adaptor, MAPK and MTOR activator 5 | 10542 | ENSG00000134248 |
| 139  | ENSG00000065518 | NA | NDUFB4 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa | 4710 | ENSG00000065518 |
| 140  | ENSG00000159445 | NA | THEM4 | thioesterase superfamily member 4 | 117145 | ENSG00000159445 |
| 141  | ENSG00000198721 | NA | ECI2 | enoyl-CoA delta isomerase 2 | 10455 | ENSG00000198721 |
| 142  | ENSG00000197580 | NA | BCO2 | beta-carotene oxygenase 2 | 83875 | ENSG00000197580 |
| 143  | ENSG00000147853 | NA | AK3 | adenylate kinase 3 | 50808 | ENSG00000147853 |
| 144  | ENSG00000131174 | NA | COX7B | cytochrome c oxidase subunit VIIb | 1349 | ENSG00000131174 |
| 145  | ENSG00000106305 | NA | AIMP2 | aminoacyl tRNA synthetase complex-interacting multifunctional protein 2 | 7965 | ENSG00000106305 |
| 146  | ENSG00000111716 | NA | LDHB | lactate dehydrogenase B | 3945 | ENSG00000111716 |
| 147  | ENSG00000142507 | NA | PSMB6 | proteasome (prosome, macropain) subunit, beta type, 6 | 5694 | ENSG00000142507 |
| 148  | ENSG00000069509 | NA | FUNDC1 | FUN14 domain containing 1 | 139341 | ENSG00000069509 |
| 149  | ENSG00000167799 | NA | NUDT8 | nudix (nucleoside diphosphate linked moiety X)-type motif 8 | 254552 | ENSG00000167799 |
| 150  | ENSG00000124532 | NA | MRS2 | MRS2 magnesium homeostasis factor homolog (S. cerevisiae) | 57380 | ENSG00000124532 |
| 151  | ENSG00000048544 | NA | MRPS10 | mitochondrial ribosomal protein S10 | 55173 | ENSG00000048544 |
| 152  | ENSG00000131269 | NA | ABCB7 | ATP-binding cassette, sub-family B (MDR/TAP), member 7 | 22 | ENSG00000131269 |
| 153  | ENSG00000051620 | NA | HEBP2 | heme binding protein 2 | 23593 | ENSG00000051620 |
| 154  | ENSG00000137806 | NA | NDUFAF1 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 | 51103 | ENSG00000137806 |
| 155  | ENSG00000171503 | NA | ETFDH | electron-transferring-flavoprotein dehydrogenase | 2110 | ENSG00000171503 |
| 156  | ENSG00000227345 | NA | PARG | poly (ADP-ribose) glycohydrolase | 8505 | ENSG00000227345 |
| 157  | ENSG00000161533 | NA | ACOX1 | acyl-CoA oxidase 1, palmitoyl | 51 | ENSG00000161533 |
| 158  | ENSG00000107317 | NA | PTGDS | prostaglandin D2 synthase 21kDa (brain) | 5730 | ENSG00000107317 |
| 159  | ENSG00000118473 | NA | SGIP1 | SH3-domain GRB2-like (endophilin) interacting protein 1 | 84251 | ENSG00000118473 |
| 160  | ENSG00000155368 | NA | DBI | diazepam binding inhibitor (GABA receptor modulator, acyl-CoA binding protein) | 1622 | ENSG00000155368 |
| 161  | ENSG00000126768 | NA | TIMM17B | translocase of inner mitochondrial membrane 17 homolog B (yeast) | 10245 | ENSG00000126768 |
| 162  | ENSG00000101019 | NA | UQCC | ubiquinol-cytochrome c reductase complex chaperone | 55245 | ENSG00000101019 |
| 163  | ENSG00000143553 | NA | SNAPIN | SNAP-associated protein | 23557 | ENSG00000143553 |
| 164  | ENSG00000163864 | NA | NMNAT3 | nicotinamide nucleotide adenylyltransferase 3 | 349565 | ENSG00000163864 |
| 165  | ENSG00000156467 | NA | UQCRB | ubiquinol-cytochrome c reductase binding protein | 7381 | ENSG00000156467 |
| 166  | ENSG00000123297 | NA | TSFM | Ts translation elongation factor, mitochondrial | 10102 | ENSG00000123297 |
| 167  | ENSG00000078070 | NA | MCCC1 | methylcrotonoyl-CoA carboxylase 1 (alpha) | 56922 | ENSG00000078070 |
| 168  | ENSG00000156885 | NA | COX6A2 | cytochrome c oxidase subunit VIa polypeptide 2 | 1339 | ENSG00000156885 |
| 169  | ENSG00000115884 | NA | SDC1 | syndecan 1 | 6382 | ENSG00000115884 |
| 170  | ENSG00000006695 | NA | COX10 | COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) | 1352 | ENSG00000006695 |
| 171  | ENSG00000123472 | NA | ATPAF1 | ATP synthase mitochondrial F1 complex assembly factor 1 | 64756 | ENSG00000123472 |
| 172  | ENSG00000139531 | NA | SUOX | sulfite oxidase | 6821 | ENSG00000139531 |
| 173  | ENSG00000198876 | NA | DCAF12 | DDB1 and CUL4 associated factor 12 | 25853 | ENSG00000198876 |
| 174  | ENSG00000114988 | NA | LMAN2L | lectin, mannose-binding 2-like | 81562 | ENSG00000114988 |
| 175  | ENSG00000161558 | NA | TMEM143 | transmembrane protein 143 | 55260 | ENSG00000161558 |
| 176  | ENSG00000140374 | NA | ETFA | electron-transfer-flavoprotein, alpha polypeptide | 2108 | ENSG00000140374 |
| 177  | ENSG00000102309 | NA | PIN4 | protein (peptidylprolyl cis/trans isomerase) NIMA-interacting, 4 (parvulin) | 5303 | ENSG00000102309 |
| 178  | ENSG00000173436 | NA | MINOS1 | mitochondrial inner membrane organizing system 1 | 440574 | ENSG00000173436 |
| 179  | ENSG00000135537 | NA | LACE1 | lactation elevated 1 | 246269 | ENSG00000135537 |
| 180  | ENSG00000116221 | NA | MRPL37 | mitochondrial ribosomal protein L37 | 51253 | ENSG00000116221 |
| 181  | ENSG00000262814 | NA | MRPL12 | mitochondrial ribosomal protein L12 | 6182 | ENSG00000262814 |
| 182  | ENSG00000181929 | NA | PRKAG1 | protein kinase, AMP-activated, gamma 1 non-catalytic subunit | 5571 | ENSG00000181929 |
| 183  | ENSG00000076043 | NA | REXO2 | REX2, RNA exonuclease 2 homolog (S. cerevisiae) | 25996 | ENSG00000076043 |
| 184  | ENSG00000069998 | NA | CECR5 | cat eye syndrome chromosome region, candidate 5 | 27440 | ENSG00000069998 |
| 185  | ENSG00000112715 | NA | VEGFA | vascular endothelial growth factor A | 7422 | ENSG00000112715 |
| 186  | ENSG00000147813 | NA | NAPRT1 | nicotinate phosphoribosyltransferase domain containing 1 | 93100 | ENSG00000147813 |
| 187  | ENSG00000119689 | NA | DLST | dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex) | 1743 | ENSG00000119689 |
| 188  | ENSG00000168291 | NA | PDHB | pyruvate dehydrogenase (lipoamide) beta | 5162 | ENSG00000168291 |
| 189  | ENSG00000156502 | NA | SUPV3L1 | suppressor of var1, 3-like 1 (S. cerevisiae) | 6832 | ENSG00000156502 |
| 190  | ENSG00000116459 | NA | ATP5F1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 | 515 | ENSG00000116459 |
| 191  | ENSG00000187145 | NA | MRPS21 | mitochondrial ribosomal protein S21 | 54460 | ENSG00000187145 |
| 192  | ENSG00000185499 | NA | MUC1 | mucin 1, cell surface associated | 4582 | ENSG00000185499 |
| 193  | ENSG00000099800 | NA | TIMM13 | translocase of inner mitochondrial membrane 13 homolog (yeast) | 26517 | ENSG00000099800 |
| 194  | ENSG00000119328 | NA | FAM206A | family with sequence similarity 206, member A | 54942 | ENSG00000119328 |
| 195  | ENSG00000107951 | NA | MTPAP | mitochondrial poly(A) polymerase | 55149 | ENSG00000107951 |
| 196  | ENSG00000130348 | NA | QRSL1 | glutaminyl-tRNA synthase (glutamine-hydrolyzing)-like 1 | 55278 | ENSG00000130348 |
| 197  | ENSG00000074319 | NA | TSG101 | tumor susceptibility gene 101 | 7251 | ENSG00000074319 |
| 198  | ENSG00000103335 | NA | PIEZO1 | piezo-type mechanosensitive ion channel component 1 | 9780 | ENSG00000103335 |
| 199  | ENSG00000148950 | NA | IMMP1L | IMP1 inner mitochondrial membrane peptidase-like (S. cerevisiae) | 196294 | ENSG00000148950 |
| 200  | ENSG00000087250 | NA | MT3 | metallothionein 3 | 4504 | ENSG00000087250 |
| 201  | ENSG00000170502 | NA | NUDT9 | nudix (nucleoside diphosphate linked moiety X)-type motif 9 | 53343 | ENSG00000170502 |
| 202  | ENSG00000137288 | NA | MNF1 | mitochondrial nucleoid factor 1 | 84300 | ENSG00000137288 |
| 203  | ENSG00000130347 | NA | RTN4IP1 | reticulon 4 interacting protein 1 | 84816 | ENSG00000130347 |
| 204  | ENSG00000133961 | NA | NUMB | numb homolog (Drosophila) | 8650 | ENSG00000133961 |
| 205  | ENSG00000154814 | NA | OXNAD1 | oxidoreductase NAD-binding domain containing 1 | 92106 | ENSG00000154814 |
| 206  | ENSG00000103121 | NA | CMC2 | COX assembly mitochondrial protein 2 homolog (S. cerevisiae) | 56942 | ENSG00000103121 |
| 207  | ENSG00000100804 | NA | PSMB5 | proteasome (prosome, macropain) subunit, beta type, 5 | 5693 | ENSG00000100804 |
| 208  | ENSG00000170791 | NA | CHCHD7 | coiled-coil-helix-coiled-coil-helix domain containing 7 | 79145 | ENSG00000170791 |
| 209  | ENSG00000215021 | NA | PHB2 | prohibitin 2 | 11331 | ENSG00000215021 |
| 210  | ENSG00000167085 | NA | PHB | prohibitin | 5245 | ENSG00000167085 |
| 211  | ENSG00000072506 | NA | HSD17B10 | hydroxysteroid (17-beta) dehydrogenase 10 | 3028 | ENSG00000072506 |
| 212  | ENSG00000106153 | NA | CHCHD2 | coiled-coil-helix-coiled-coil-helix domain containing 2 | 51142 | ENSG00000106153 |
| 213  | ENSG00000183036 | NA | PCP4 | Purkinje cell protein 4 | 5121 | ENSG00000183036 |
| 214  | ENSG00000131143 | NA | COX4I1 | cytochrome c oxidase subunit IV isoform 1 | 1327 | ENSG00000131143 |
| 215  | ENSG00000142546 | NA | NOSIP | nitric oxide synthase interacting protein | 51070 | ENSG00000142546 |
| 216  | ENSG00000136444 | NA | RSAD1 | radical S-adenosyl methionine domain containing 1 | 55316 | ENSG00000136444 |
| 217  | ENSG00000108561 | NA | C1QBP | complement component 1, q subcomponent binding protein | 708 | ENSG00000108561 |
| 218  | ENSG00000106355 | NA | LSM5 | LSM5 homolog, U6 small nuclear RNA associated (S. cerevisiae) | 23658 | ENSG00000106355 |
| 219  | ENSG00000102265 | NA | TIMP1 | TIMP metallopeptidase inhibitor 1 | 7076 | ENSG00000102265 |
| 220  | ENSG00000230055 | NA | CISD3 | CDGSH iron sulfur domain 3 | 284106 | ENSG00000230055 |
| 221  | ENSG00000175581 | NA | MRPL48 | mitochondrial ribosomal protein L48 | 51642 | ENSG00000175581 |
| 222  | ENSG00000047249 | NA | ATP6V1H | ATPase, H+ transporting, lysosomal 50/57kDa, V1 subunit H | 51606 | ENSG00000047249 |
| 223  | ENSG00000136143 | NA | SUCLA2 | succinate-CoA ligase, ADP-forming, beta subunit | 8803 | ENSG00000136143 |
| 224  | ENSG00000003137 | NA | CYP26B1 | cytochrome P450, family 26, subfamily B, polypeptide 1 | 56603 | ENSG00000003137 |
| 225  | ENSG00000168000 | NA | BSCL2 | Berardinelli-Seip congenital lipodystrophy 2 (seipin) | 26580 | ENSG00000168000 |
| 226  | ENSG00000166855 | NA | CLPX | ClpX caseinolytic peptidase X homolog (E. coli) | 10845 | ENSG00000166855 |
| 227  | ENSG00000090263 | NA | MRPS33 | mitochondrial ribosomal protein S33 | 51650 | ENSG00000090263 |
| 228  | ENSG00000166321 | NA | NUDT13 | nudix (nucleoside diphosphate linked moiety X)-type motif 13 | 25961 | ENSG00000166321 |
| 229  | ENSG00000074582 | NA | BCS1L | BCS1-like (S. cerevisiae) | 617 | ENSG00000074582 |
| 230  | ENSG00000122033 | NA | MTIF3 | mitochondrial translational initiation factor 3 | 219402 | ENSG00000122033 |
| 231  | ENSG00000116171 | NA | SCP2 | sterol carrier protein 2 | 6342 | ENSG00000116171 |
| 232  | ENSG00000082146 | NA | STRADB | STE20-related kinase adaptor beta | 55437 | ENSG00000082146 |
| 233  | ENSG00000104412 | NA | EMC2 | ER membrane protein complex subunit 2 | 9694 | ENSG00000104412 |
| 234  | ENSG00000172590 | NA | MRPL52 | mitochondrial ribosomal protein L52 | 122704 | ENSG00000172590 |
| 235  | ENSG00000140009 | NA | ESR2 | estrogen receptor 2 (ER beta) | 2100 | ENSG00000140009 |
| 236  | ENSG00000103018 | NA | CYB5B | cytochrome b5 type B (outer mitochondrial membrane) | 80777 | ENSG00000103018 |
| 237  | ENSG00000166816 | NA | LDHD | lactate dehydrogenase D | 197257 | ENSG00000166816 |
| 238  | ENSG00000143374 | NA | TARS2 | threonyl-tRNA synthetase 2, mitochondrial (putative) | 80222 | ENSG00000143374 |
| 239  | ENSG00000013275 | NA | PSMC4 | proteasome (prosome, macropain) 26S subunit, ATPase, 4 | 5704 | ENSG00000013275 |
| 240  | ENSG00000132313 | NA | MRPL35 | mitochondrial ribosomal protein L35 | 51318 | ENSG00000132313 |
| 241  | ENSG00000138495 | NA | COX17 | COX17 cytochrome c oxidase assembly homolog (S. cerevisiae) | 10063 | ENSG00000138495 |
| 242  | ENSG00000117118 | NA | SDHB | succinate dehydrogenase complex, subunit B, iron sulfur (Ip) | 6390 | ENSG00000117118 |
| 243  | ENSG00000171953 | NA | ATPAF2 | ATP synthase mitochondrial F1 complex assembly factor 2 | 91647 | ENSG00000171953 |
| 244  | ENSG00000168827 | NA | GFM1 | G elongation factor, mitochondrial 1 | 85476 | ENSG00000168827 |
| 245  | ENSG00000143641 | NA | GALNT2 | UDP-N-acetyl-alpha-D-galactosamine:polypeptide N-acetylgalactosaminyltransferase 2 (GalNAc-T2) | 2590 | ENSG00000143641 |
| 246  | ENSG00000135469 | NA | COQ10A | coenzyme Q10 homolog A (S. cerevisiae) | 93058 | ENSG00000135469 |
| 247  | ENSG00000177427 | NA | SMCR7 | Smith-Magenis syndrome chromosome region, candidate 7 | 125170 | ENSG00000177427 |
| 248  | ENSG00000149380 | NA | P4HA3 | prolyl 4-hydroxylase, alpha polypeptide III | 283208 | ENSG00000149380 |
| 249  | ENSG00000115944 | NA | COX7A2L | cytochrome c oxidase subunit VIIa polypeptide 2 like | 9167 | ENSG00000115944 |
| 250  | ENSG00000064652 | NA | SNX24 | sorting nexin 24 | 28966 | ENSG00000064652 |
| 251  | ENSG00000197150 | NA | ABCB8 | ATP-binding cassette, sub-family B (MDR/TAP), member 8 | 11194 | ENSG00000197150 |
| 252  | ENSG00000152234 | NA | ATP5A1 | ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle | 498 | ENSG00000152234 |
| 253  | ENSG00000164022 | NA | AIMP1 | aminoacyl tRNA synthetase complex-interacting multifunctional protein 1 | 9255 | ENSG00000164022 |
| 254  | ENSG00000105402 | NA | NAPA | N-ethylmaleimide-sensitive factor attachment protein, alpha | 8775 | ENSG00000105402 |
| 255  | ENSG00000198920 | NA | KIAA0753 | KIAA0753 | 9851 | ENSG00000198920 |
| 256  | ENSG00000128609 | NA | NDUFA5 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa | 4698 | ENSG00000128609 |
| 257  | ENSG00000178802 | NA | MPI | mannose phosphate isomerase | 4351 | ENSG00000178802 |
| 258  | ENSG00000163541 | NA | SUCLG1 | succinate-CoA ligase, alpha subunit | 8802 | ENSG00000163541 |
| 259  | ENSG00000165678 | NA | GHITM | growth hormone inducible transmembrane protein | 27069 | ENSG00000165678 |
| 260  | ENSG00000154719 | NA | MRPL39 | mitochondrial ribosomal protein L39 | 54148 | ENSG00000154719 |
| 261  | ENSG00000103489 | NA | XYLT1 | xylosyltransferase I | 64131 | ENSG00000103489 |
| 262  | ENSG00000173915 | NA | USMG5 | up-regulated during skeletal muscle growth 5 homolog (mouse) | 84833 | ENSG00000173915 |
| 263  | ENSG00000131730 | NA | CKMT2 | creatine kinase, mitochondrial 2 (sarcomeric) | 1160 | ENSG00000131730 |
| 264  | ENSG00000158882 | NA | TOMM40L | translocase of outer mitochondrial membrane 40 homolog (yeast)-like | 84134 | ENSG00000158882 |
| 265  | ENSG00000137714 | NA | FDX1 | ferredoxin 1 | 2230 | ENSG00000137714 |
| 266  | ENSG00000115652 | NA | UXS1 | UDP-glucuronate decarboxylase 1 | 80146 | ENSG00000115652 |
| 267  | ENSG00000136897 | NA | MRPL50 | mitochondrial ribosomal protein L50 | 54534 | ENSG00000136897 |
| 268  | ENSG00000132541 | NA | HRSP12 | heat-responsive protein 12 | 10247 | ENSG00000132541 |
| 269  | ENSG00000092096 | NA | SLC22A17 | solute carrier family 22, member 17 | 51310 | ENSG00000092096 |
| 270  | ENSG00000124523 | NA | SIRT5 | sirtuin 5 | 23408 | ENSG00000124523 |
| 271  | ENSG00000102738 | NA | MRPS31 | mitochondrial ribosomal protein S31 | 10240 | ENSG00000102738 |
| 272  | ENSG00000197943 | NA | PLCG2 | phospholipase C, gamma 2 (phosphatidylinositol-specific) | 5336 | ENSG00000197943 |
| 273  | ENSG00000130312 | NA | MRPL34 | mitochondrial ribosomal protein L34 | 64981 | ENSG00000130312 |
| 274  | ENSG00000132300 | NA | PTCD3 | pentatricopeptide repeat domain 3 | 55037 | ENSG00000132300 |
| 275  | ENSG00000139428 | NA | MMAB | methylmalonic aciduria (cobalamin deficiency) cblB type | 326625 | ENSG00000139428 |
| 276  | ENSG00000070808 | NA | CAMK2A | calcium/calmodulin-dependent protein kinase II alpha | 815 | ENSG00000070808 |
| 277  | ENSG00000196562 | NA | SULF2 | sulfatase 2 | 55959 | ENSG00000196562 |
| 278  | ENSG00000162600 | NA | OMA1 | OMA1 zinc metallopeptidase homolog (S. cerevisiae) | 115209 | ENSG00000162600 |
| 279  | ENSG00000108179 | NA | PPIF | peptidylprolyl isomerase F | 10105 | ENSG00000108179 |
| 280  | ENSG00000137133 | NA | HINT2 | histidine triad nucleotide binding protein 2 | 84681 | ENSG00000137133 |
| 281  | ENSG00000122729 | NA | ACO1 | aconitase 1, soluble | 48 | ENSG00000122729 |
| 282  | ENSG00000173085 | NA | COQ2 | coenzyme Q2 homolog, prenyltransferase (yeast) | 27235 | ENSG00000173085 |
| 283  | ENSG00000101096 | NA | NFATC2 | nuclear factor of activated T-cells, cytoplasmic, calcineurin-dependent 2 | 4773 | ENSG00000101096 |
| 284  | ENSG00000124172 | NA | ATP5E | ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit | 514 | ENSG00000124172 |
| 285  | ENSG00000213585 | NA | VDAC1 | voltage-dependent anion channel 1 | 7416 | ENSG00000213585 |
| 286  | ENSG00000205981 | NA | DNAJC19 | DnaJ (Hsp40) homolog, subfamily C, member 19 | 131118 | ENSG00000205981 |
| 287  | ENSG00000132591 | NA | ERAL1 | Era G-protein-like 1 (E. coli) | 26284 | ENSG00000132591 |
| 288  | ENSG00000120333 | NA | MRPS14 | mitochondrial ribosomal protein S14 | 63931 | ENSG00000120333 |
| 289  | ENSG00000184857 | NA | TMEM186 | transmembrane protein 186 | 25880 | ENSG00000184857 |
| 290  | ENSG00000099624 | NA | ATP5D | ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit | 513 | ENSG00000099624 |
| 291  | ENSG00000107954 | NA | NEURL | neuralized homolog (Drosophila) | 9148 | ENSG00000107954 |
| 292  | ENSG00000166949 | NA | SMAD3 | SMAD family member 3 | 4088 | ENSG00000166949 |
| 293  | ENSG00000138670 | NA | RASGEF1B | RasGEF domain family, member 1B | 153020 | ENSG00000138670 |
| 294  | ENSG00000100412 | NA | ACO2 | aconitase 2, mitochondrial | 50 | ENSG00000100412 |
| 295  | ENSG00000112651 | NA | MRPL2 | mitochondrial ribosomal protein L2 | 51069 | ENSG00000112651 |
| 296  | ENSG00000101311 | NA | FERMT1 | fermitin family member 1 | 55612 | ENSG00000101311 |
| 297  | ENSG00000164051 | NA | CCDC51 | coiled-coil domain containing 51 | 79714 | ENSG00000164051 |
| 298  | ENSG00000181610 | NA | MRPS23 | mitochondrial ribosomal protein S23 | 51649 | ENSG00000181610 |
| 299  | ENSG00000175792 | NA | RUVBL1 | RuvB-like 1 (E. coli) | 8607 | ENSG00000175792 |
| 300  | ENSG00000213563 | NA | C8orf82 | chromosome 8 open reading frame 82 | 414919 | ENSG00000213563 |
| 301  | ENSG00000164896 | NA | FASTK | Fas-activated serine/threonine kinase | 10922 | ENSG00000164896 |
| 302  | ENSG00000107020 | NA | PLGRKT | plasminogen receptor, C-terminal lysine transmembrane protein | 55848 | ENSG00000107020 |
| 303  | ENSG00000176422 | NA | SPRYD4 | SPRY domain containing 4 | 283377 | ENSG00000176422 |
| 304  | ENSG00000119673 | NA | ACOT2 | acyl-CoA thioesterase 2 | 10965 | ENSG00000119673 |
| 305  | ENSG00000070785 | NA | EIF2B3 | eukaryotic translation initiation factor 2B, subunit 3 gamma, 58kDa | 8891 | ENSG00000070785 |
| 306  | ENSG00000180185 | NA | FAHD1 | fumarylacetoacetate hydrolase domain containing 1 | 81889 | ENSG00000180185 |
| 307  | ENSG00000148090 | NA | AUH | AU RNA binding protein/enoyl-CoA hydratase | 549 | ENSG00000148090 |
| 308  | ENSG00000127989 | NA | MTERF | mitochondrial transcription termination factor | 7978 | ENSG00000127989 |
| 309  | ENSG00000090013 | NA | BLVRB | biliverdin reductase B (flavin reductase (NADPH)) | 645 | ENSG00000090013 |
| 310  | ENSG00000133943 | NA | C14orf159 | chromosome 14 open reading frame 159 | 80017 | ENSG00000133943 |
| 311  | ENSG00000172270 | NA | BSG | basigin (Ok blood group) | 682 | ENSG00000172270 |
| 312  | ENSG00000111817 | NA | DSE | dermatan sulfate epimerase | 29940 | ENSG00000111817 |
| 313  | ENSG00000119723 | NA | COQ6 | coenzyme Q6 homolog, monooxygenase (S. cerevisiae) | 51004 | ENSG00000119723 |
| 314  | ENSG00000197894 | NA | ADH5 | alcohol dehydrogenase 5 (class III), chi polypeptide | 128 | ENSG00000197894 |
| 315  | ENSG00000113312 | NA | TTC1 | tetratricopeptide repeat domain 1 | 7265 | ENSG00000113312 |
| 316  | ENSG00000197448 | NA | GSTK1 | glutathione S-transferase kappa 1 | 373156 | ENSG00000197448 |
| 317  | ENSG00000167792 | NA | NDUFV1 | NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa | 4723 | ENSG00000167792 |
| 318  | ENSG00000112335 | NA | SNX3 | sorting nexin 3 | 8724 | ENSG00000112335 |
| 319  | ENSG00000204308 | NA | RNF5 | ring finger protein 5, E3 ubiquitin protein ligase | 6048 | ENSG00000204308 |
| 320  | ENSG00000134020 | NA | PEBP4 | phosphatidylethanolamine-binding protein 4 | 157310 | ENSG00000134020 |
| 321  | ENSG00000162735 | NA | PEX19 | peroxisomal biogenesis factor 19 | 5824 | ENSG00000162735 |
| 322  | ENSG00000159377 | NA | PSMB4 | proteasome (prosome, macropain) subunit, beta type, 4 | 5692 | ENSG00000159377 |
| 323  | ENSG00000121361 | NA | KCNJ8 | potassium inwardly-rectifying channel, subfamily J, member 8 | 3764 | ENSG00000121361 |
| 324  | ENSG00000100034 | NA | PPM1F | protein phosphatase, Mg2+/Mn2+ dependent, 1F | 9647 | ENSG00000100034 |
| 325  | ENSG00000182809 | NA | CRIP2 | cysteine-rich protein 2 | 1397 | ENSG00000182809 |
| 326  | ENSG00000127884 | NA | ECHS1 | enoyl CoA hydratase, short chain, 1, mitochondrial | 1892 | ENSG00000127884 |
| 327  | ENSG00000178952 | NA | TUFM | Tu translation elongation factor, mitochondrial | 7284 | ENSG00000178952 |
| 328  | ENSG00000168273 | NA | C3orf78 | chromosome 3 open reading frame 78 | 440957 | ENSG00000168273 |
| 329  | ENSG00000125124 | NA | BBS2 | Bardet-Biedl syndrome 2 | 583 | ENSG00000125124 |
| 330  | ENSG00000125445 | NA | MRPS7 | mitochondrial ribosomal protein S7 | 51081 | ENSG00000125445 |
| 331  | ENSG00000105364 | NA | MRPL4 | mitochondrial ribosomal protein L4 | 51073 | ENSG00000105364 |
| 332  | ENSG00000142188 | NA | TMEM50B | transmembrane protein 50B | 757 | ENSG00000142188 |
| 333  | ENSG00000143158 | NA | MPC2 | mitochondrial pyruvate carrier 2 | 25874 | ENSG00000143158 |
| 334  | ENSG00000113013 | NA | HSPA9 | heat shock 70kDa protein 9 (mortalin) | 3313 | ENSG00000113013 |
| 335  | ENSG00000213420 | NA | GPC2 | glypican 2 | 221914 | ENSG00000213420 |
| 336  | ENSG00000110011 | NA | DNAJC4 | DnaJ (Hsp40) homolog, subfamily C, member 4 | 3338 | ENSG00000110011 |
| 337  | ENSG00000117151 | NA | CTBS | chitobiase, di-N-acetyl- | 1486 | ENSG00000117151 |
| 338  | ENSG00000101000 | NA | PROCR | protein C receptor, endothelial | 10544 | ENSG00000101000 |
| 339  | ENSG00000101247 | NA | NDUFAF5 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 5 | 79133 | ENSG00000101247 |
| 340  | ENSG00000241837 | NA | ATP5O | ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit | 539 | ENSG00000241837 |
| 341  | ENSG00000140905 | NA | GCSH | glycine cleavage system protein H (aminomethyl carrier) | 2653 | ENSG00000140905 |
| 342  | ENSG00000214026 | NA | MRPL23 | mitochondrial ribosomal protein L23 | 6150 | ENSG00000214026 |
| 343  | ENSG00000165264 | NA | NDUFB6 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa | 4712 | ENSG00000165264 |
| 344  | ENSG00000109846 | NA | CRYAB | crystallin, alpha B | 1410 | ENSG00000109846 |
| 345  | ENSG00000161281 | NA | COX7A1 | cytochrome c oxidase subunit VIIa polypeptide 1 (muscle) | 1346 | ENSG00000161281 |
| 346  | ENSG00000167862 | NA | ICT1 | immature colon carcinoma transcript 1 | 3396 | ENSG00000167862 |
| 347  | ENSG00000071246 | NA | VASH1 | vasohibin 1 | 22846 | ENSG00000071246 |
| 348  | ENSG00000116288 | NA | PARK7 | parkinson protein 7 | 11315 | ENSG00000116288 |
| 349  | ENSG00000198715 | NA | C1orf85 | chromosome 1 open reading frame 85 | 112770 | ENSG00000198715 |
| 350  | ENSG00000128203 | NA | ASPHD2 | aspartate beta-hydroxylase domain containing 2 | 57168 | ENSG00000128203 |
| 351  | ENSG00000166136 | NA | NDUFB8 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa | 4714 | ENSG00000166136 |
| 352  | ENSG00000172340 | NA | SUCLG2 | succinate-CoA ligase, GDP-forming, beta subunit | 8801 | ENSG00000172340 |
| 353  | ENSG00000151093 | NA | OXSM | 3-oxoacyl-ACP synthase, mitochondrial | 54995 | ENSG00000151093 |
| 354  | ENSG00000091140 | NA | DLD | dihydrolipoamide dehydrogenase | 1738 | ENSG00000091140 |
| 355  | ENSG00000130414 | NA | NDUFA10 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa | 4705 | ENSG00000130414 |
| 356  | ENSG00000007923 | NA | DNAJC11 | DnaJ (Hsp40) homolog, subfamily C, member 11 | 55735 | ENSG00000007923 |
| 357  | ENSG00000122971 | NA | ACADS | acyl-CoA dehydrogenase, C-2 to C-3 short chain | 35 | ENSG00000122971 |
| 358  | ENSG00000131828 | NA | PDHA1 | pyruvate dehydrogenase (lipoamide) alpha 1 | 5160 | ENSG00000131828 |
| 359  | ENSG00000103356 | NA | EARS2 | glutamyl-tRNA synthetase 2, mitochondrial (putative) | 124454 | ENSG00000103356 |
| 360  | ENSG00000182512 | NA | GLRX5 | glutaredoxin 5 | 51218 | ENSG00000182512 |
| 361  | ENSG00000168807 | NA | SNTB2 | syntrophin, beta 2 (dystrophin-associated protein A1, 59kDa, basic component 2) | 6645 | ENSG00000168807 |
| 362  | ENSG00000091483 | NA | FH | fumarate hydratase | 2271 | ENSG00000091483 |
| 363  | ENSG00000203797 | NA | DDO | D-aspartate oxidase | 8528 | ENSG00000203797 |
| 364  | ENSG00000103642 | NA | LACTB | lactamase, beta | 114294 | ENSG00000103642 |
| 365  | ENSG00000109586 | NA | GALNT7 | UDP-N-acetyl-alpha-D-galactosamine:polypeptide N-acetylgalactosaminyltransferase 7 (GalNAc-T7) | 51809 | ENSG00000109586 |
| 366  | ENSG00000136100 | NA | VPS36 | vacuolar protein sorting 36 homolog (S. cerevisiae) | 51028 | ENSG00000136100 |
| 367  | ENSG00000110074 | NA | FOXRED1 | FAD-dependent oxidoreductase domain containing 1 | 55572 | ENSG00000110074 |
| 368  | ENSG00000074201 | NA | CLNS1A | chloride channel, nucleotide-sensitive, 1A | 1207 | ENSG00000074201 |
| 369  | ENSG00000174374 | NA | WBSCR16 | Williams-Beuren syndrome chromosome region 16 | 81554 | ENSG00000174374 |
| 370  | ENSG00000164466 | NA | SFXN1 | sideroflexin 1 | 94081 | ENSG00000164466 |
| 371  | ENSG00000119537 | NA | KDSR | 3-ketodihydrosphingosine reductase | 2531 | ENSG00000119537 |
| 372  | ENSG00000111481 | NA | COPZ1 | coatomer protein complex, subunit zeta 1 | 22818 | ENSG00000111481 |
| 373  | ENSG00000151729 | NA | SLC25A4 | solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4 | 291 | ENSG00000151729 |
| 374  | ENSG00000178057 | NA | NDUFAF3 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 3 | 25915 | ENSG00000178057 |
| 375  | ENSG00000183172 | NA | C22orf32 | chromosome 22 open reading frame 32 | 91689 | ENSG00000183172 |
| 376  | ENSG00000173660 | NA | UQCRH | ubiquinol-cytochrome c reductase hinge protein | 7388 | ENSG00000173660 |
| 377  | ENSG00000133028 | NA | SCO1 | SCO cytochrome oxidase deficient homolog 1 (yeast) | 6341 | ENSG00000133028 |
| 378  | ENSG00000105696 | NA | TMEM59L | transmembrane protein 59-like | 25789 | ENSG00000105696 |
| 379  | ENSG00000100348 | NA | TXN2 | thioredoxin 2 | 25828 | ENSG00000100348 |
| 380  | ENSG00000140876 | NA | NUDT7 | nudix (nucleoside diphosphate linked moiety X)-type motif 7 | 283927 | ENSG00000140876 |
| 381  | ENSG00000101181 | NA | GTPBP5 | GTP binding protein 5 (putative) | 26164 | ENSG00000101181 |
| 382  | ENSG00000135940 | NA | COX5B | cytochrome c oxidase subunit Vb | 1329 | ENSG00000135940 |
| 383  | ENSG00000029639 | NA | TFB1M | transcription factor B1, mitochondrial | 51106 | ENSG00000029639 |
| 384  | ENSG00000129991 | NA | TNNI3 | troponin I type 3 (cardiac) | 7137 | ENSG00000129991 |
| 385  | ENSG00000135900 | NA | MRPL44 | mitochondrial ribosomal protein L44 | 65080 | ENSG00000135900 |
| 386  | ENSG00000239789 | NA | MRPS17 | mitochondrial ribosomal protein S17 | 51373 | ENSG00000239789 |
| 387  | ENSG00000113790 | NA | EHHADH | enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase | 1962 | ENSG00000113790 |
| 388  | ENSG00000162851 | NA | TFB2M | transcription factor B2, mitochondrial | 64216 | ENSG00000162851 |
| 389  | ENSG00000160293 | NA | VAV2 | vav 2 guanine nucleotide exchange factor | 7410 | ENSG00000160293 |
| 390  | ENSG00000159210 | NA | SNF8 | SNF8, ESCRT-II complex subunit, homolog (S. cerevisiae) | 11267 | ENSG00000159210 |
| 391  | ENSG00000082515 | NA | MRPL22 | mitochondrial ribosomal protein L22 | 29093 | ENSG00000082515 |
| 392  | ENSG00000189043 | NA | NDUFA4 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa | 4697 | ENSG00000189043 |
| 393  | ENSG00000179085 | NA | DPM3 | dolichyl-phosphate mannosyltransferase polypeptide 3 | 54344 | ENSG00000179085 |
| 394  | ENSG00000176894 | NA | PXMP2 | peroxisomal membrane protein 2, 22kDa | 5827 | ENSG00000176894 |
| 395  | ENSG00000172115 | NA | CYCS | cytochrome c, somatic | 54205 | ENSG00000172115 |
| 396  | ENSG00000160783 | NA | PMF1 | polyamine-modulated factor 1 | 11243 | ENSG00000160783 |
| 397  | ENSG00000035141 | NA | FAM136A | family with sequence similarity 136, member A | 84908 | ENSG00000035141 |
| 398  | ENSG00000185100 | NA | ADSSL1 | adenylosuccinate synthase like 1 | 122622 | ENSG00000185100 |
| 399  | ENSG00000115286 | NA | NDUFS7 | NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) | 374291 | ENSG00000115286 |
| 400  | ENSG00000164258 | NA | NDUFS4 | NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) | 4724 | ENSG00000164258 |
| 401  | ENSG00000156170 | NA | NDUFAF6 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 | 137682 | ENSG00000156170 |
| 402  | ENSG00000155463 | NA | OXA1L | oxidase (cytochrome c) assembly 1-like | 5018 | ENSG00000155463 |
| 403  | ENSG00000163319 | NA | MRPS18C | mitochondrial ribosomal protein S18C | 51023 | ENSG00000163319 |
| 404  | ENSG00000185608 | NA | MRPL40 | mitochondrial ribosomal protein L40 | 64976 | ENSG00000185608 |
| 405  | ENSG00000179091 | NA | CYC1 | cytochrome c-1 | 1537 | ENSG00000179091 |
| 406  | ENSG00000171861 | NA | RNMTL1 | RNA methyltransferase like 1 | 55178 | ENSG00000171861 |
| 407  | ENSG00000053501 | NA | USE1 | unconventional SNARE in the ER 1 homolog (S. cerevisiae) | 55850 | ENSG00000053501 |
| 408  | ENSG00000182810 | NA | DDX28 | DEAD (Asp-Glu-Ala-Asp) box polypeptide 28 | 55794 | ENSG00000182810 |
| 409  | ENSG00000105819 | NA | PMPCB | peptidase (mitochondrial processing) beta | 9512 | ENSG00000105819 |
| 410  | ENSG00000196683 | NA | TOMM7 | translocase of outer mitochondrial membrane 7 homolog (yeast) | 54543 | ENSG00000196683 |
| 411  | ENSG00000175198 | NA | PCCA | propionyl CoA carboxylase, alpha polypeptide | 5095 | ENSG00000175198 |
| 412  | ENSG00000129187 | NA | DCTD | dCMP deaminase | 1635 | ENSG00000129187 |
| 413  | ENSG00000067225 | NA | PKM | pyruvate kinase, muscle | 5315 | ENSG00000067225 |
| 414  | ENSG00000114023 | NA | FAM162A | family with sequence similarity 162, member A | 26355 | ENSG00000114023 |
| 415  | ENSG00000157326 | NA | DHRS4 | dehydrogenase/reductase (SDR family) member 4 | 10901 | ENSG00000157326 |
| 416  | ENSG00000140990 | NA | NDUFB10 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa | 4716 | ENSG00000140990 |
| 417  | ENSG00000135297 | NA | MTO1 | mitochondrial translation optimization 1 homolog (S. cerevisiae) | 25821 | ENSG00000135297 |
| 418  | ENSG00000144182 | NA | LIPT1 | lipoyltransferase 1 | 51601 | ENSG00000144182 |
| 419  | ENSG00000243147 | NA | MRPL33 | mitochondrial ribosomal protein L33 | 9553 | ENSG00000243147 |
| 420  | ENSG00000143653 | NA | SCCPDH | saccharopine dehydrogenase (putative) | 51097 | ENSG00000143653 |
| 421  | ENSG00000116906 | NA | GNPAT | glyceronephosphate O-acyltransferase | 8443 | ENSG00000116906 |
| 422  | ENSG00000123545 | NA | NDUFAF4 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 4 | 29078 | ENSG00000123545 |
| 423  | ENSG00000178913 | NA | TAF7 | TAF7 RNA polymerase II, TATA box binding protein (TBP)-associated factor, 55kDa | 6879 | ENSG00000178913 |
| 424  | ENSG00000105220 | NA | GPI | glucose-6-phosphate isomerase | 2821 | ENSG00000105220 |
| 425  | ENSG00000133315 | NA | MACROD1 | MACRO domain containing 1 | 28992 | ENSG00000133315 |
| 426  | ENSG00000072778 | NA | ACADVL | acyl-CoA dehydrogenase, very long chain | 37 | ENSG00000072778 |
| 427  | ENSG00000172893 | NA | DHCR7 | 7-dehydrocholesterol reductase | 1717 | ENSG00000172893 |
| 428  | ENSG00000108774 | NA | RAB5C | RAB5C, member RAS oncogene family | 5878 | ENSG00000108774 |
| 429  | ENSG00000150977 | NA | RILPL2 | Rab interacting lysosomal protein-like 2 | 196383 | ENSG00000150977 |
| 430  | ENSG00000049883 | NA | PTCD2 | pentatricopeptide repeat domain 2 | 79810 | ENSG00000049883 |
| 431  | ENSG00000084731 | NA | KIF3C | kinesin family member 3C | 3797 | ENSG00000084731 |
| 432  | ENSG00000160124 | NA | CCDC58 | coiled-coil domain containing 58 | 131076 | ENSG00000160124 |
| 433  | ENSG00000126088 | NA | UROD | uroporphyrinogen decarboxylase | 7389 | ENSG00000126088 |
| 434  | ENSG00000136521 | NA | NDUFB5 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa | 4711 | ENSG00000136521 |
| 435  | ENSG00000169020 | NA | ATP5I | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E | 521 | ENSG00000169020 |
| 436  | ENSG00000182054 | NA | IDH2 | isocitrate dehydrogenase 2 (NADP+), mitochondrial | 3418 | ENSG00000182054 |
| 437  | ENSG00000004779 | NA | NDUFAB1 | NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa | 4706 | ENSG00000004779 |
| 438  | ENSG00000165898 | NA | ISCA2 | iron-sulfur cluster assembly 2 homolog (S. cerevisiae) | 122961 | ENSG00000165898 |
| 439  | ENSG00000004961 | NA | HCCS | holocytochrome c synthase | 3052 | ENSG00000004961 |
| 440  | ENSG00000073578 | NA | SDHA | succinate dehydrogenase complex, subunit A, flavoprotein (Fp) | 6389 | ENSG00000073578 |
| 441  | ENSG00000167775 | NA | CD320 | CD320 molecule | 51293 | ENSG00000167775 |
| 442  | ENSG00000213965 | NA | NUDT19 | nudix (nucleoside diphosphate linked moiety X)-type motif 19 | 390916 | ENSG00000213965 |
| 443  | ENSG00000151413 | NA | NUBPL | nucleotide binding protein-like | 80224 | ENSG00000151413 |
| 444  | ENSG00000104325 | NA | DECR1 | 2,4-dienoyl CoA reductase 1, mitochondrial | 1666 | ENSG00000104325 |
| 445  | ENSG00000103245 | NA | NARFL | nuclear prelamin A recognition factor-like | 64428 | ENSG00000103245 |
| 446  | ENSG00000077348 | NA | EXOSC5 | exosome component 5 | 56915 | ENSG00000077348 |
| 447  | ENSG00000113048 | NA | MRPS27 | mitochondrial ribosomal protein S27 | 23107 | ENSG00000113048 |
| 448  | ENSG00000182154 | NA | MRPL41 | mitochondrial ribosomal protein L41 | 64975 | ENSG00000182154 |
| 449  | ENSG00000072401 | NA | UBE2D1 | ubiquitin-conjugating enzyme E2D 1 | 7321 | ENSG00000072401 |
| 450  | ENSG00000213988 | NA | ZNF90 | zinc finger protein 90 | 7643 | ENSG00000213988 |
| 451  | ENSG00000167468 | NA | GPX4 | glutathione peroxidase 4 | 2879 | ENSG00000167468 |
| 452  | ENSG00000127184 | NA | COX7C | cytochrome c oxidase subunit VIIc | 1350 | ENSG00000127184 |
| 453  | ENSG00000135775 | NA | COG2 | component of oligomeric golgi complex 2 | 22796 | ENSG00000135775 |
| 454  | ENSG00000085760 | NA | MTIF2 | mitochondrial translational initiation factor 2 | 4528 | ENSG00000085760 |
| 455  | ENSG00000165637 | NA | VDAC2 | voltage-dependent anion channel 2 | 7417 | ENSG00000165637 |
| 456  | ENSG00000120265 | NA | PCMT1 | protein-L-isoaspartate (D-aspartate) O-methyltransferase | 5110 | ENSG00000120265 |
| 457  | ENSG00000100211 | NA | CBY1 | chibby homolog 1 (Drosophila) | 25776 | ENSG00000100211 |
| 458  | ENSG00000149357 | NA | LAMTOR1 | late endosomal/lysosomal adaptor, MAPK and MTOR activator 1 | 55004 | ENSG00000149357 |
| 459  | ENSG00000178982 | NA | EIF3K | eukaryotic translation initiation factor 3, subunit K | 27335 | ENSG00000178982 |
| 460  | ENSG00000086504 | NA | MRPL28 | mitochondrial ribosomal protein L28 | 10573 | ENSG00000086504 |
| 461  | ENSG00000108384 | NA | RAD51C | RAD51 homolog C (S. cerevisiae) | 5889 | ENSG00000108384 |
| 462  | ENSG00000162910 | NA | MRPL55 | mitochondrial ribosomal protein L55 | 128308 | ENSG00000162910 |
| 463  | ENSG00000130733 | NA | YIPF2 | Yip1 domain family, member 2 | 78992 | ENSG00000130733 |
| 464  | ENSG00000130349 | NA | C6orf203 | chromosome 6 open reading frame 203 | 51250 | ENSG00000130349 |
| 465  | ENSG00000166681 | NA | NGFRAP1 | nerve growth factor receptor (TNFRSF16) associated protein 1 | 27018 | ENSG00000166681 |
| 466  | ENSG00000111271 | NA | ACAD10 | acyl-CoA dehydrogenase family, member 10 | 80724 | ENSG00000111271 |
| 467  | ENSG00000103423 | NA | DNAJA3 | DnaJ (Hsp40) homolog, subfamily A, member 3 | 9093 | ENSG00000103423 |
| 468  | ENSG00000160211 | NA | G6PD | glucose-6-phosphate dehydrogenase | 2539 | ENSG00000160211 |
| 469  | ENSG00000138777 | NA | PPA2 | pyrophosphatase (inorganic) 2 | 27068 | ENSG00000138777 |
| 470  | ENSG00000100601 | NA | ALKBH1 | alkB, alkylation repair homolog 1 (E. coli) | 8846 | ENSG00000100601 |
| 471  | ENSG00000102554 | NA | KLF5 | Kruppel-like factor 5 (intestinal) | 688 | ENSG00000102554 |
| 472  | ENSG00000188026 | NA | RILPL1 | Rab interacting lysosomal protein-like 1 | 353116 | ENSG00000188026 |
| 473  | ENSG00000136522 | NA | MRPL47 | mitochondrial ribosomal protein L47 | 57129 | ENSG00000136522 |
| 474  | ENSG00000135972 | NA | MRPS9 | mitochondrial ribosomal protein S9 | 64965 | ENSG00000135972 |
| 475  | ENSG00000144451 | NA | SPAG16 | sperm associated antigen 16 | 79582 | ENSG00000144451 |
| 476  | ENSG00000023228 | NA | NDUFS1 | NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) | 4719 | ENSG00000023228 |
| 477  | ENSG00000254470 | NA | AP5B1 | adaptor-related protein complex 5, beta 1 subunit | 91056 | ENSG00000254470 |
| 478  | ENSG00000115840 | NA | SLC25A12 | solute carrier family 25 (aspartate/glutamate carrier), member 12 | 8604 | ENSG00000115840 |
| 479  | ENSG00000145982 | NA | FARS2 | phenylalanyl-tRNA synthetase 2, mitochondrial | 10667 | ENSG00000145982 |
| 480  | ENSG00000121897 | NA | LIAS | lipoic acid synthetase | 11019 | ENSG00000121897 |
| 481  | ENSG00000197122 | NA | SRC | v-src sarcoma (Schmidt-Ruppin A-2) viral oncogene homolog (avian) | 6714 | ENSG00000197122 |
| 482  | ENSG00000112695 | NA | COX7A2 | cytochrome c oxidase subunit VIIa polypeptide 2 (liver) | 1347 | ENSG00000112695 |
| 483  | ENSG00000147155 | NA | EBP | emopamil binding protein (sterol isomerase) | 10682 | ENSG00000147155 |
| 484  | ENSG00000179958 | NA | DCTPP1 | dCTP pyrophosphatase 1 | 79077 | ENSG00000179958 |
| 485  | ENSG00000106571 | NA | GLI3 | GLI family zinc finger 3 | 2737 | ENSG00000106571 |
| 486  | ENSG00000083720 | NA | OXCT1 | 3-oxoacid CoA transferase 1 | 5019 | ENSG00000083720 |
| 487  | ENSG00000131495 | NA | NDUFA2 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa | 4695 | ENSG00000131495 |
| 488  | ENSG00000095321 | NA | CRAT | carnitine O-acetyltransferase | 1384 | ENSG00000095321 |
| 489  | ENSG00000185808 | NA | PIGP | phosphatidylinositol glycan anchor biosynthesis, class P | 51227 | ENSG00000185808 |
| 490  | ENSG00000165688 | NA | PMPCA | peptidase (mitochondrial processing) alpha | 23203 | ENSG00000165688 |
| 491  | ENSG00000120992 | NA | LYPLA1 | lysophospholipase I | 10434 | ENSG00000120992 |
| 492  | ENSG00000183617 | NA | MRPL54 | mitochondrial ribosomal protein L54 | 116541 | ENSG00000183617 |
| 493  | ENSG00000112855 | NA | HARS2 | histidyl-tRNA synthetase 2, mitochondrial | 23438 | ENSG00000112855 |
| 494  | ENSG00000108100 | NA | CCNY | cyclin Y | 219771 | ENSG00000108100 |
| 495  | ENSG00000119705 | NA | SLIRP | SRA stem-loop interacting RNA binding protein | 81892 | ENSG00000119705 |
| 496  | ENSG00000205309 | NA | NT5M | 5',3'-nucleotidase, mitochondrial | 56953 | ENSG00000205309 |
| 497  | ENSG00000170906 | NA | NDUFA3 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa | 4696 | ENSG00000170906 |
| 498  | ENSG00000138085 | NA | ATRAID | all-trans retinoic acid-induced differentiation factor | 51374 | ENSG00000138085 |
| 499  | ENSG00000128654 | NA | MTX2 | metaxin 2 | 10651 | ENSG00000128654 |
| 500  | ENSG00000160808 | NA | MYL3 | myosin, light chain 3, alkali; ventricular, skeletal, slow | 4634 | ENSG00000160808 |
| 501  | ENSG00000112304 | NA | ACOT13 | acyl-CoA thioesterase 13 | 55856 | ENSG00000112304 |
| 502  | ENSG00000108439 | NA | PNPO | pyridoxamine 5'-phosphate oxidase | 55163 | ENSG00000108439 |
| 503  | ENSG00000167283 | NA | ATP5L | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G | 10632 | ENSG00000167283 |
| 504  | ENSG00000114054 | NA | PCCB | propionyl CoA carboxylase, beta polypeptide | 5096 | ENSG00000114054 |
| 505  | ENSG00000111275 | NA | ALDH2 | aldehyde dehydrogenase 2 family (mitochondrial) | 217 | ENSG00000111275 |
| 506  | ENSG00000171202 | NA | TMEM126A | transmembrane protein 126A | 84233 | ENSG00000171202 |
| 507  | ENSG00000136270 | NA | TBRG4 | transforming growth factor beta regulator 4 | 9238 | ENSG00000136270 |
| 508  | ENSG00000010256 | NA | UQCRC1 | ubiquinol-cytochrome c reductase core protein I | 7384 | ENSG00000010256 |
| 509  | ENSG00000130560 | NA | UBAC1 | UBA domain containing 1 | 10422 | ENSG00000130560 |
| 510  | ENSG00000104823 | NA | ECH1 | enoyl CoA hydratase 1, peroxisomal | 1891 | ENSG00000104823 |
| 511  | ENSG00000167515 | NA | TRAPPC2L | trafficking protein particle complex 2-like | 51693 | ENSG00000167515 |
| 512  | ENSG00000197912 | NA | SPG7 | spastic paraplegia 7 (pure and complicated autosomal recessive) | 6687 | ENSG00000197912 |
| 513  | ENSG00000138796 | NA | HADH | hydroxyacyl-CoA dehydrogenase | 3033 | ENSG00000138796 |
| 514  | ENSG00000165672 | NA | PRDX3 | peroxiredoxin 3 | 10935 | ENSG00000165672 |
| 515  | ENSG00000154518 | NA | ATP5G3 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C3 (subunit 9) | 518 | ENSG00000154518 |
| 516  | ENSG00000101132 | NA | PFDN4 | prefoldin subunit 4 | 5203 | ENSG00000101132 |
| 517  | ENSG00000088682 | NA | COQ9 | coenzyme Q9 homolog (S. cerevisiae) | 57017 | ENSG00000088682 |
| 518  | ENSG00000075303 | NA | SLC25A40 | solute carrier family 25, member 40 | 55972 | ENSG00000075303 |
| 519  | ENSG00000163382 | NA | APOA1BP | apolipoprotein A-I binding protein | 128240 | ENSG00000163382 |
| 520  | ENSG00000177951 | NA | BET1L | blocked early in transport 1 homolog (S. cerevisiae)-like | 51272 | ENSG00000177951 |
| 521  | ENSG00000168653 | NA | NDUFS5 | NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) | 4725 | ENSG00000168653 |
| 522  | ENSG00000154237 | NA | LRRK1 | leucine-rich repeat kinase 1 | 79705 | ENSG00000154237 |
| 523  | ENSG00000247077 | NA | PGAM5 | phosphoglycerate mutase family member 5 | 192111 | ENSG00000247077 |
| 524  | ENSG00000156110 | NA | ADK | adenosine kinase | 132 | ENSG00000156110 |
| 525  | ENSG00000184903 | NA | IMMP2L | IMP2 inner mitochondrial membrane peptidase-like (S. cerevisiae) | 83943 | ENSG00000184903 |
| 526  | ENSG00000087299 | NA | L2HGDH | L-2-hydroxyglutarate dehydrogenase | 79944 | ENSG00000087299 |
| 527  | ENSG00000159335 | NA | PTMS | parathymosin | 5763 | ENSG00000159335 |
| 528  | ENSG00000136463 | NA | TACO1 | translational activator of mitochondrially encoded cytochrome c oxidase I | 51204 | ENSG00000136463 |
| 529  | ENSG00000197586 | NA | ENTPD6 | ectonucleoside triphosphate diphosphohydrolase 6 (putative) | 955 | ENSG00000197586 |
| 530  | ENSG00000103316 | NA | CRYM | crystallin, mu | 1428 | ENSG00000103316 |
| 531  | ENSG00000184076 | NA | UQCR10 | ubiquinol-cytochrome c reductase, complex III subunit X | 29796 | ENSG00000184076 |
| 532  | ENSG00000130300 | NA | PLVAP | plasmalemma vesicle associated protein | 83483 | ENSG00000130300 |
| 533  | ENSG00000075415 | NA | SLC25A3 | solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 3 | 5250 | ENSG00000075415 |
| 534  | ENSG00000184489 | NA | PTP4A3 | protein tyrosine phosphatase type IVA, member 3 | 11156 | ENSG00000184489 |
| 535  | ENSG00000100028 | NA | SNRPD3 | small nuclear ribonucleoprotein D3 polypeptide 18kDa | 6634 | ENSG00000100028 |
| 536  | ENSG00000186522 | NA | SEPT10 | septin 10 | 151011 | ENSG00000186522 |
| 537  | ENSG00000154723 | NA | ATP5J | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 | 522 | ENSG00000154723 |
| 538  | ENSG00000133983 | NA | COX16 | COX16 cytochrome c oxidase assembly homolog (S. cerevisiae) | 51241 | ENSG00000133983 |
| 539  | ENSG00000167969 | NA | ECI1 | enoyl-CoA delta isomerase 1 | 1632 | ENSG00000167969 |
| 540  | ENSG00000115364 | NA | MRPL19 | mitochondrial ribosomal protein L19 | 9801 | ENSG00000115364 |
| 541  | ENSG00000105552 | NA | BCAT2 | branched chain amino-acid transaminase 2, mitochondrial | 587 | ENSG00000105552 |
| 542  | ENSG00000112996 | NA | MRPS30 | mitochondrial ribosomal protein S30 | 10884 | ENSG00000112996 |
| 543  | ENSG00000100347 | NA | SAMM50 | sorting and assembly machinery component 50 homolog (S. cerevisiae) | 25813 | ENSG00000100347 |
| 544  | ENSG00000125166 | NA | GOT2 | glutamic-oxaloacetic transaminase 2, mitochondrial (aspartate aminotransferase 2) | 2806 | ENSG00000125166 |
| 545  | ENSG00000141552 | NA | ANAPC11 | anaphase promoting complex subunit 11 | 51529 | ENSG00000141552 |
| 546  | ENSG00000140740 | NA | UQCRC2 | ubiquinol-cytochrome c reductase core protein II | 7385 | ENSG00000140740 |
| 547  | ENSG00000114378 | NA | HYAL1 | hyaluronoglucosaminidase 1 | 3373 | ENSG00000114378 |
| 548  | ENSG00000160194 | NA | NDUFV3 | NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa | 4731 | ENSG00000160194 |
| 549  | ENSG00000147684 | NA | NDUFB9 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa | 4715 | ENSG00000147684 |
| 550  | ENSG00000169599 | NA | NFU1 | NFU1 iron-sulfur cluster scaffold homolog (S. cerevisiae) | 27247 | ENSG00000169599 |
| 551  | ENSG00000184983 | NA | NDUFA6 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa | 4700 | ENSG00000184983 |
| 552  | ENSG00000163626 | NA | COX18 | COX18 cytochrome c oxidase assembly homolog (S. cerevisiae) | 285521 | ENSG00000163626 |
| 553  | ENSG00000158864 | NA | NDUFS2 | NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) | 4720 | ENSG00000158864 |
| 554  | ENSG00000079691 | NA | LRRC16A | leucine rich repeat containing 16A | 55604 | ENSG00000079691 |
| 555  | ENSG00000105197 | NA | TIMM50 | translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae) | 92609 | ENSG00000105197 |
| 556  | ENSG00000142168 | NA | SOD1 | superoxide dismutase 1, soluble | 6647 | ENSG00000142168 |
| 557  | ENSG00000109519 | NA | GRPEL1 | GrpE-like 1, mitochondrial (E. coli) | 80273 | ENSG00000109519 |
| 558  | ENSG00000000419 | NA | DPM1 | dolichyl-phosphate mannosyltransferase polypeptide 1, catalytic subunit | 8813 | ENSG00000000419 |
| 559  | ENSG00000133393 | NA | FOPNL | FGFR1OP N-terminal like | 123811 | ENSG00000133393 |
| 560  | ENSG00000096080 | NA | MRPS18A | mitochondrial ribosomal protein S18A | 55168 | ENSG00000096080 |
| 561  | ENSG00000120254 | NA | MTHFD1L | methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 1-like | 25902 | ENSG00000120254 |
| 562  | ENSG00000134056 | NA | MRPS36 | mitochondrial ribosomal protein S36 | 92259 | ENSG00000134056 |
| 563  | ENSG00000139914 | NA | FITM1 | fat storage-inducing transmembrane protein 1 | 161247 | ENSG00000139914 |
| 564  | ENSG00000060762 | NA | MPC1 | mitochondrial pyruvate carrier 1 | 51660 | ENSG00000060762 |
| 565  | ENSG00000104980 | NA | TIMM44 | translocase of inner mitochondrial membrane 44 homolog (yeast) | 10469 | ENSG00000104980 |
| 566  | ENSG00000105499 | NA | PLA2G4C | phospholipase A2, group IVC (cytosolic, calcium-independent) | 8605 | ENSG00000105499 |
| 567  | ENSG00000138399 | NA | FASTKD1 | FAST kinase domains 1 | 79675 | ENSG00000138399 |
| 568  | ENSG00000112992 | NA | NNT | nicotinamide nucleotide transhydrogenase | 23530 | ENSG00000112992 |
| 569  | ENSG00000067704 | NA | IARS2 | isoleucyl-tRNA synthetase 2, mitochondrial | 55699 | ENSG00000067704 |
| 570  | ENSG00000215251 | NA | FASTKD5 | FAST kinase domains 5 | 60493 | ENSG00000215251 |
| 571  | ENSG00000119421 | NA | NDUFA8 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa | 4702 | ENSG00000119421 |
| 572  | ENSG00000172172 | NA | MRPL13 | mitochondrial ribosomal protein L13 | 28998 | ENSG00000172172 |
| 573  | ENSG00000244005 | NA | NFS1 | NFS1 nitrogen fixation 1 homolog (S. cerevisiae) | 9054 | ENSG00000244005 |
| 574  | ENSG00000104879 | NA | CKM | creatine kinase, muscle | 1158 | ENSG00000104879 |
| 575  | ENSG00000126267 | NA | COX6B1 | cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) | 1340 | ENSG00000126267 |
| 576  | ENSG00000121769 | NA | FABP3 | fatty acid binding protein 3, muscle and heart (mammary-derived growth inhibitor) | 2170 | ENSG00000121769 |
| 577  | ENSG00000148450 | NA | MSRB2 | methionine sulfoxide reductase B2 | 22921 | ENSG00000148450 |
| 578  | ENSG00000145494 | NA | NDUFS6 | NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) | 4726 | ENSG00000145494 |
| 579  | ENSG00000196236 | NA | XPNPEP3 | X-prolyl aminopeptidase (aminopeptidase P) 3, putative | 63929 | ENSG00000196236 |
| 580  | ENSG00000105379 | NA | ETFB | electron-transfer-flavoprotein, beta polypeptide | 2109 | ENSG00000105379 |
| 581  | ENSG00000165887 | NA | ANKRD2 | ankyrin repeat domain 2 (stretch responsive muscle) | 26287 | ENSG00000165887 |
| 582  | ENSG00000175334 | NA | BANF1 | barrier to autointegration factor 1 | 8815 | ENSG00000175334 |
| 583  | ENSG00000108515 | NA | ENO3 | enolase 3 (beta, muscle) | 2027 | ENSG00000108515 |
| 584  | ENSG00000213995 | NA | CARKD | carbohydrate kinase domain containing | 55739 | ENSG00000213995 |
| 585  | ENSG00000090266 | NA | NDUFB2 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa | 4708 | ENSG00000090266 |
| 586  | ENSG00000105649 | NA | RAB3A | RAB3A, member RAS oncogene family | 5864 | ENSG00000105649 |
| 587  | ENSG00000151498 | NA | ACAD8 | acyl-CoA dehydrogenase family, member 8 | 27034 | ENSG00000151498 |
| 588  | ENSG00000156928 | NA | MALSU1 | mitochondrial assembly of ribosomal large subunit 1 | 115416 | ENSG00000156928 |
| 589  | ENSG00000159199 | NA | ATP5G1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) | 516 | ENSG00000159199 |
| 590  | ENSG00000155906 | NA | RMND1 | required for meiotic nuclear division 1 homolog (S. cerevisiae) | 55005 | ENSG00000155906 |
| 591  | ENSG00000120509 | NA | PDZD11 | PDZ domain containing 11 | 51248 | ENSG00000120509 |
| 592  | ENSG00000130159 | NA | ECSIT | ECSIT homolog (Drosophila) | 51295 | ENSG00000130159 |
| 593  | ENSG00000129084 | NA | PSMA1 | proteasome (prosome, macropain) subunit, alpha type, 1 | 5682 | ENSG00000256206 ENSG00000129084 |
| 594  | ENSG00000114383 | NA | TUSC2 | tumor suppressor candidate 2 | 11334 | ENSG00000114383 |
| 595  | ENSG00000125863 | NA | MKKS | McKusick-Kaufman syndrome | 8195 | ENSG00000125863 |
| 596  | ENSG00000103274 | NA | NUBP1 | nucleotide binding protein 1 | 4682 | ENSG00000103274 |
| 597  | ENSG00000174917 | NA | C19orf70 | chromosome 19 open reading frame 70 | 125988 | ENSG00000174917 |
| 598  | ENSG00000181744 | NA | C3orf58 | chromosome 3 open reading frame 58 | 205428 | ENSG00000181744 |
| 599  | ENSG00000138190 | NA | EXOC6 | exocyst complex component 6 | 54536 | ENSG00000138190 |
| 600  | ENSG00000087460 | NA | GNAS | GNAS complex locus | 2778 | ENSG00000087460 |
| 601  | ENSG00000066926 | NA | FECH | ferrochelatase | 2235 | ENSG00000066926 |
| 602  | ENSG00000131779 | NA | PEX11B | peroxisomal biogenesis factor 11 beta | 8799 | ENSG00000131779 |
| 603  | ENSG00000039560 | NA | RAI14 | retinoic acid induced 14 | 26064 | ENSG00000039560 |
| 604  | ENSG00000166228 | NA | PCBD1 | pterin-4 alpha-carbinolamine dehydratase/dimerization cofactor of hepatocyte nuclear factor 1 alpha | 5092 | ENSG00000166228 |
| 605  | ENSG00000130147 | NA | SH3BP4 | SH3-domain binding protein 4 | 23677 | ENSG00000130147 |
| 606  | ENSG00000100294 | NA | MCAT | malonyl CoA:ACP acyltransferase (mitochondrial) | 27349 | ENSG00000100294 |
| 607  | ENSG00000137225 | NA | CAPN11 | calpain 11 | 11131 | ENSG00000137225 |
| 608  | ENSG00000146729 | NA | GBAS | glioblastoma amplified sequence | 2631 | ENSG00000146729 |
| 609  | ENSG00000164494 | NA | PDSS2 | prenyl (decaprenyl) diphosphate synthase, subunit 2 | 57107 | ENSG00000164494 |
| 610  | ENSG00000152082 | NA | MZT2B | mitotic spindle organizing protein 2B | 80097 | ENSG00000152082 |
| 611  | ENSG00000138463 | NA | DIRC2 | disrupted in renal carcinoma 2 | 84925 | ENSG00000138463 |
| 612  | ENSG00000132763 | NA | MMACHC | methylmalonic aciduria (cobalamin deficiency) cblC type, with homocystinuria | 25974 | ENSG00000132763 |
| 613  | ENSG00000151366 | NA | NDUFC2 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa | 4718 | ENSG00000151366 |
| 614  | ENSG00000130724 | NA | CHMP2A | charged multivesicular body protein 2A | 27243 | ENSG00000130724 |
| 615  | ENSG00000132305 | NA | IMMT | inner membrane protein, mitochondrial | 10989 | ENSG00000132305 |
| 616  | ENSG00000090432 | NA | MUL1 | mitochondrial E3 ubiquitin protein ligase 1 | 79594 | ENSG00000090432 |
| 617  | ENSG00000146701 | NA | MDH2 | malate dehydrogenase 2, NAD (mitochondrial) | 4191 | ENSG00000146701 |
| 618  | ENSG00000164038 | NA | SLC9B2 | solute carrier family 9, subfamily B (NHA2, cation proton antiporter 2), member 2 | 133308 | ENSG00000164038 |
| 619  | ENSG00000247596 | NA | TWF2 | twinfilin, actin-binding protein, homolog 2 (Drosophila) | 11344 | ENSG00000247596 |
| 620  | ENSG00000147123 | NA | NDUFB11 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa | 54539 | ENSG00000147123 |
| 621  | ENSG00000169021 | NA | UQCRFS1 | ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 | 7386 | ENSG00000169021 |
| 622  | ENSG00000104142 | NA | VPS18 | vacuolar protein sorting 18 homolog (S. cerevisiae) | 57617 | ENSG00000104142 |
| 623  | ENSG00000178449 | NA | COX14 | COX14 cytochrome c oxidase assembly homolog (S. cerevisiae) | 84987 | ENSG00000178449 |
| 624  | ENSG00000145439 | NA | CBR4 | carbonyl reductase 4 | 84869 | ENSG00000145439 |
| 625  | ENSG00000170231 | NA | FABP6 | fatty acid binding protein 6, ileal | 2172 | ENSG00000170231 |
| 626  | ENSG00000062485 | NA | CS | citrate synthase | 1431 | ENSG00000062485 |
| 627  | ENSG00000175193 | NA | PARL | presenilin associated, rhomboid-like | 55486 | ENSG00000175193 |
| 628  | ENSG00000120053 | NA | GOT1 | glutamic-oxaloacetic transaminase 1, soluble (aspartate aminotransferase 1) | 2805 | ENSG00000120053 |
| 629  | ENSG00000227500 | NA | SCAMP4 | secretory carrier membrane protein 4 | 113178 | ENSG00000227500 |
| 630  | ENSG00000189283 | NA | FHIT | fragile histidine triad | 2272 | ENSG00000189283 |
| 631  | ENSG00000111843 | NA | TMEM14C | transmembrane protein 14C | 51522 | ENSG00000111843 |
| 632  | ENSG00000185973 | NA | TMLHE | trimethyllysine hydroxylase, epsilon | 55217 | ENSG00000185973 |
| 633  | ENSG00000124370 | NA | MCEE | methylmalonyl CoA epimerase | 84693 | ENSG00000124370 |
| 634  | ENSG00000137513 | NA | NARS2 | asparaginyl-tRNA synthetase 2, mitochondrial (putative) | 79731 | ENSG00000137513 |
| 635  | ENSG00000111639 | NA | MRPL51 | mitochondrial ribosomal protein L51 | 51258 | ENSG00000111639 |
| 636  | ENSG00000164405 | NA | UQCRQ | ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa | 27089 | ENSG00000164405 |
| 637  | ENSG00000168569 | NA | TMEM223 | transmembrane protein 223 | 79064 | ENSG00000168569 |
| 638  | ENSG00000100321 | NA | SYNGR1 | synaptogyrin 1 | 9145 | ENSG00000100321 |
| 639  | ENSG00000136930 | NA | PSMB7 | proteasome (prosome, macropain) subunit, beta type, 7 | 5695 | ENSG00000136930 |
| 640  | ENSG00000115935 | NA | WIPF1 | WAS/WASL interacting protein family, member 1 | 7456 | ENSG00000115935 |
| 641  | ENSG00000148187 | NA | MRRF | mitochondrial ribosome recycling factor | 92399 | ENSG00000148187 |
| 642  | ENSG00000061794 | NA | MRPS35 | mitochondrial ribosomal protein S35 | 60488 | ENSG00000061794 |
| 643  | ENSG00000183648 | NA | NDUFB1 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa | 4707 | ENSG00000183648 |
| 644  | ENSG00000087302 | NA | C14orf166 | chromosome 14 open reading frame 166 | 51637 | ENSG00000087302 |
| 645  | ENSG00000110435 | NA | PDHX | pyruvate dehydrogenase complex, component X | 8050 | ENSG00000110435 |
| 646  | ENSG00000132676 | NA | DAP3 | death associated protein 3 | 7818 | ENSG00000132676 |
| 647  | ENSG00000172586 | NA | CHCHD1 | coiled-coil-helix-coiled-coil-helix domain containing 1 | 118487 | ENSG00000172586 |
| 648  | ENSG00000121022 | NA | COPS5 | COP9 constitutive photomorphogenic homolog subunit 5 (Arabidopsis) | 10987 | ENSG00000121022 |
| 649  | ENSG00000125356 | NA | NDUFA1 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa | 4694 | ENSG00000125356 |
| 650  | ENSG00000108528 | NA | SLC25A11 | solute carrier family 25 (mitochondrial carrier; oxoglutarate carrier), member 11 | 8402 | ENSG00000108528 |
| 651  | ENSG00000129282 | NA | MRM1 | mitochondrial rRNA methyltransferase 1 homolog (S. cerevisiae) | 79922 | ENSG00000129282 |
| 652  | ENSG00000163636 | NA | PSMD6 | proteasome (prosome, macropain) 26S subunit, non-ATPase, 6 | 9861 | ENSG00000163636 |
| 653  | ENSG00000099795 | NA | NDUFB7 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa | 4713 | ENSG00000099795 |
| 654  | ENSG00000137574 | NA | TGS1 | trimethylguanosine synthase 1 | 96764 | ENSG00000137574 |
| 655  | ENSG00000175470 | NA | PPP2R2D | protein phosphatase 2, regulatory subunit B, delta | 55844 | ENSG00000175470 |
| 656  | ENSG00000044459 | NA | CNTLN | centlein, centrosomal protein | 54875 | ENSG00000044459 |
| 657  | ENSG00000153574 | NA | RPIA | ribose 5-phosphate isomerase A | 22934 | ENSG00000153574 |
| 658  | ENSG00000101350 | NA | KIF3B | kinesin family member 3B | 9371 | ENSG00000101350 |
| 659  | ENSG00000138772 | NA | ANXA3 | annexin A3 | 306 | ENSG00000138772 |
| 660  | ENSG00000103507 | NA | BCKDK | branched chain ketoacid dehydrogenase kinase | 10295 | ENSG00000103507 |
| 661  | ENSG00000144021 | NA | CIAO1 | cytosolic iron-sulfur protein assembly 1 | 9391 | ENSG00000144021 |
| 662  | ENSG00000198015 | NA | MRPL42 | mitochondrial ribosomal protein L42 | 28977 | ENSG00000198015 |
| 663  | ENSG00000144567 | NA | FAM134A | family with sequence similarity 134, member A | 79137 | ENSG00000144567 |
| 664  | ENSG00000111785 | NA | RIC8B | resistance to inhibitors of cholinesterase 8 homolog B (C. elegans) | 55188 | ENSG00000111785 |
| 665  | ENSG00000125901 | NA | MRPS26 | mitochondrial ribosomal protein S26 | 64949 | ENSG00000125901 |
| 666  | ENSG00000167136 | NA | ENDOG | endonuclease G | 2021 | ENSG00000167136 |
| 667  | ENSG00000075336 | NA | TIMM21 | translocase of inner mitochondrial membrane 21 homolog (yeast) | 29090 | ENSG00000075336 |
| 668  | ENSG00000250479 | NA | CHCHD10 | coiled-coil-helix-coiled-coil-helix domain containing 10 | 400916 | ENSG00000250479 |
| 669  | ENSG00000074071 | NA | MRPS34 | mitochondrial ribosomal protein S34 | 65993 | ENSG00000074071 |
| 670  | ENSG00000060971 | NA | ACAA1 | acetyl-CoA acyltransferase 1 | 30 | ENSG00000060971 |
| 671  | ENSG00000164347 | NA | GFM2 | G elongation factor, mitochondrial 2 | 84340 | ENSG00000164347 |
| 672  | ENSG00000150867 | NA | PIP4K2A | phosphatidylinositol-5-phosphate 4-kinase, type II, alpha | 5305 | ENSG00000150867 |
| 673  | ENSG00000111906 | NA | HDDC2 | HD domain containing 2 | 51020 | ENSG00000111906 |
| 674  | ENSG00000181991 | NA | MRPS11 | mitochondrial ribosomal protein S11 | 64963 | ENSG00000181991 |
| 675  | ENSG00000138175 | NA | ARL3 | ADP-ribosylation factor-like 3 | 403 | ENSG00000138175 |
| 676  | ENSG00000175110 | NA | MRPS22 | mitochondrial ribosomal protein S22 | 56945 | ENSG00000175110 |
| 677  | ENSG00000112357 | NA | PEX7 | peroxisomal biogenesis factor 7 | 5191 | ENSG00000112357 |
| 678  | ENSG00000128463 | NA | EMC4 | ER membrane protein complex subunit 4 | 51234 | ENSG00000128463 |
| 679  | ENSG00000173272 | NA | MZT2A | mitotic spindle organizing protein 2A | 653784 | ENSG00000173272 |
| 680  | ENSG00000117594 | NA | HSD11B1 | hydroxysteroid (11-beta) dehydrogenase 1 | 3290 | ENSG00000117594 |
| 681  | ENSG00000110717 | NA | NDUFS8 | NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) | 4728 | ENSG00000110717 |
| 682  | ENSG00000174547 | NA | MRPL11 | mitochondrial ribosomal protein L11 | 65003 | ENSG00000174547 |
| 683  | ENSG00000137547 | NA | MRPL15 | mitochondrial ribosomal protein L15 | 29088 | ENSG00000137547 |
| 684  | ENSG00000197535 | NA | MYO5A | myosin VA (heavy chain 12, myoxin) | 4644 | ENSG00000197535 |
| 685  | ENSG00000162972 | NA | C2orf47 | chromosome 2 open reading frame 47 | 79568 | ENSG00000162972 |
| 686  | ENSG00000183978 | NA | COA3 | cytochrome C oxidase assembly factor 3 | 28958 | ENSG00000183978 |
| 687  | ENSG00000036672 | NA | USP2 | ubiquitin specific peptidase 2 | 9099 | ENSG00000036672 |
| 688  | ENSG00000198467 | NA | TPM2 | tropomyosin 2 (beta) | 7169 | ENSG00000198467 |
| 689  | ENSG00000153140 | NA | CETN3 | centrin, EF-hand protein, 3 | 1070 | ENSG00000153140 |
| 690  | ENSG00000113845 | NA | TIMMDC1 | translocase of inner mitochondrial membrane domain containing 1 | 51300 | ENSG00000113845 |
| 691  | ENSG00000241468 | NA | ATP5J2 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 | 9551 | ENSG00000241468 |
| 692  | ENSG00000013563 | NA | DNASE1L1 | deoxyribonuclease I-like 1 | 1774 | ENSG00000013563 |
| 693  | ENSG00000176340 | NA | COX8A | cytochrome c oxidase subunit VIIIA (ubiquitous) | 1351 | ENSG00000176340 |
| 694  | ENSG00000144029 | NA | MRPS5 | mitochondrial ribosomal protein S5 | 64969 | ENSG00000144029 |
| 695  | ENSG00000170266 | NA | GLB1 | galactosidase, beta 1 | 2720 | ENSG00000170266 |
| 696  | ENSG00000050393 | NA | CCDC90A | coiled-coil domain containing 90A | 63933 | ENSG00000050393 |
| 697  | ENSG00000101365 | NA | IDH3B | isocitrate dehydrogenase 3 (NAD+) beta | 3420 | ENSG00000101365 |
| 698  | ENSG00000158793 | NA | NIT1 | nitrilase 1 | 4817 | ENSG00000158793 |
| Database:cellular component       Name:mitochondrial membrane part       ID:GO:0044455 | ||||||
|---|---|---|---|---|---|---|
| C=147; O=87; E=8.92; R=9.75; rawP=1.33e-67; adjP=5.85e-66 | ||||||
| Index | UserID | Value | Gene Symbol | Gene Name | EntrezGene | Ensembl |
| 1  | ENSG00000087299 | NA | L2HGDH | L-2-hydroxyglutarate dehydrogenase | 79944 | ENSG00000087299 |
| 2  | ENSG00000184903 | NA | IMMP2L | IMP2 inner mitochondrial membrane peptidase-like (S. cerevisiae) | 83943 | ENSG00000184903 |
| 3  | ENSG00000128609 | NA | NDUFA5 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa | 4698 | ENSG00000128609 |
| 4  | ENSG00000151366 | NA | NDUFC2 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa | 4718 | ENSG00000151366 |
| 5  | ENSG00000132305 | NA | IMMT | inner membrane protein, mitochondrial | 10989 | ENSG00000132305 |
| 6  | ENSG00000165264 | NA | NDUFB6 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa | 4712 | ENSG00000165264 |
| 7  | ENSG00000156467 | NA | UQCRB | ubiquinol-cytochrome c reductase binding protein | 7381 | ENSG00000156467 |
| 8  | ENSG00000090432 | NA | MUL1 | mitochondrial E3 ubiquitin protein ligase 1 | 79594 | ENSG00000090432 |
| 9  | ENSG00000161281 | NA | COX7A1 | cytochrome c oxidase subunit VIIa polypeptide 1 (muscle) | 1346 | ENSG00000161281 |
| 10  | ENSG00000136521 | NA | NDUFB5 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa | 4711 | ENSG00000136521 |
| 11  | ENSG00000173915 | NA | USMG5 | up-regulated during skeletal muscle growth 5 homolog (mouse) | 84833 | ENSG00000173915 |
| 12  | ENSG00000169020 | NA | ATP5I | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E | 521 | ENSG00000169020 |
| 13  | ENSG00000004779 | NA | NDUFAB1 | NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa | 4706 | ENSG00000004779 |
| 14  | ENSG00000168958 | NA | MFF | mitochondrial fission factor | 56947 | ENSG00000168958 |
| 15  | ENSG00000156885 | NA | COX6A2 | cytochrome c oxidase subunit VIa polypeptide 2 | 1339 | ENSG00000156885 |
| 16  | ENSG00000147123 | NA | NDUFB11 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa | 54539 | ENSG00000147123 |
| 17  | ENSG00000154723 | NA | ATP5J | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 | 522 | ENSG00000154723 |
| 18  | ENSG00000073578 | NA | SDHA | succinate dehydrogenase complex, subunit A, flavoprotein (Fp) | 6389 | ENSG00000073578 |
| 19  | ENSG00000137714 | NA | FDX1 | ferredoxin 1 | 2230 | ENSG00000137714 |
| 20  | ENSG00000119013 | NA | NDUFB3 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa | 4709 | ENSG00000119013 |
| 21  | ENSG00000169021 | NA | UQCRFS1 | ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 | 7386 | ENSG00000169021 |
| 22  | ENSG00000100347 | NA | SAMM50 | sorting and assembly machinery component 50 homolog (S. cerevisiae) | 25813 | ENSG00000100347 |
| 23  | ENSG00000135390 | NA | ATP5G2 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C2 (subunit 9) | 517 | ENSG00000135390 |
| 24  | ENSG00000140740 | NA | UQCRC2 | ubiquinol-cytochrome c reductase core protein II | 7385 | ENSG00000140740 |
| 25  | ENSG00000166136 | NA | NDUFB8 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa | 4714 | ENSG00000166136 |
| 26  | ENSG00000160194 | NA | NDUFV3 | NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa | 4731 | ENSG00000160194 |
| 27  | ENSG00000147684 | NA | NDUFB9 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa | 4715 | ENSG00000147684 |
| 28  | ENSG00000184983 | NA | NDUFA6 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa | 4700 | ENSG00000184983 |
| 29  | ENSG00000130414 | NA | NDUFA10 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa | 4705 | ENSG00000130414 |
| 30  | ENSG00000163626 | NA | COX18 | COX18 cytochrome c oxidase assembly homolog (S. cerevisiae) | 285521 | ENSG00000163626 |
| 31  | ENSG00000158864 | NA | NDUFS2 | NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) | 4720 | ENSG00000158864 |
| 32  | ENSG00000105197 | NA | TIMM50 | translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae) | 92609 | ENSG00000105197 |
| 33  | ENSG00000139180 | NA | NDUFA9 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa | 4704 | ENSG00000139180 |
| 34  | ENSG00000109390 | NA | NDUFC1 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa | 4717 | ENSG00000109390 |
| 35  | ENSG00000124172 | NA | ATP5E | ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit | 514 | ENSG00000124172 |
| 36  | ENSG00000183648 | NA | NDUFB1 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa | 4707 | ENSG00000183648 |
| 37  | ENSG00000099624 | NA | ATP5D | ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit | 513 | ENSG00000099624 |
| 38  | ENSG00000204370 | NA | SDHD | succinate dehydrogenase complex, subunit D, integral membrane protein | 6392 | ENSG00000204370 |
| 39  | ENSG00000116459 | NA | ATP5F1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 | 515 | ENSG00000116459 |
| 40  | ENSG00000104980 | NA | TIMM44 | translocase of inner mitochondrial membrane 44 homolog (yeast) | 10469 | ENSG00000104980 |
| 41  | ENSG00000112992 | NA | NNT | nicotinamide nucleotide transhydrogenase | 23530 | ENSG00000112992 |
| 42  | ENSG00000125356 | NA | NDUFA1 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa | 4694 | ENSG00000125356 |
| 43  | ENSG00000213619 | NA | NDUFS3 | NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) | 4722 | ENSG00000213619 |
| 44  | ENSG00000173660 | NA | UQCRH | ubiquinol-cytochrome c reductase hinge protein | 7388 | ENSG00000173660 |
| 45  | ENSG00000214253 | NA | FIS1 | fission 1 (mitochondrial outer membrane) homolog (S. cerevisiae) | 51024 | ENSG00000214253 |
| 46  | ENSG00000099795 | NA | NDUFB7 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa | 4713 | ENSG00000099795 |
| 47  | ENSG00000119421 | NA | NDUFA8 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa | 4702 | ENSG00000119421 |
| 48  | ENSG00000023228 | NA | NDUFS1 | NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) | 4719 | ENSG00000023228 |
| 49  | ENSG00000143252 | NA | SDHC | succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa | 6391 | ENSG00000143252 |
| 50  | ENSG00000145494 | NA | NDUFS6 | NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) | 4726 | ENSG00000145494 |
| 51  | ENSG00000156709 | NA | AIFM1 | apoptosis-inducing factor, mitochondrion-associated, 1 | 9131 | ENSG00000156709 |
| 52  | ENSG00000189043 | NA | NDUFA4 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa | 4697 | ENSG00000189043 |
| 53  | ENSG00000110955 | NA | ATP5B | ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide | 506 | ENSG00000110955 |
| 54  | ENSG00000115286 | NA | NDUFS7 | NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) | 374291 | ENSG00000115286 |
| 55  | ENSG00000112695 | NA | COX7A2 | cytochrome c oxidase subunit VIIa polypeptide 2 (liver) | 1347 | ENSG00000112695 |
| 56  | ENSG00000164258 | NA | NDUFS4 | NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) | 4724 | ENSG00000164258 |
| 57  | ENSG00000167792 | NA | NDUFV1 | NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa | 4723 | ENSG00000167792 |
| 58  | ENSG00000131495 | NA | NDUFA2 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa | 4695 | ENSG00000131495 |
| 59  | ENSG00000155463 | NA | OXA1L | oxidase (cytochrome c) assembly 1-like | 5018 | ENSG00000155463 |
| 60  | ENSG00000065518 | NA | NDUFB4 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa | 4710 | ENSG00000065518 |
| 61  | ENSG00000167863 | NA | ATP5H | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d | 10476 | ENSG00000167863 |
| 62  | ENSG00000090266 | NA | NDUFB2 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa | 4708 | ENSG00000090266 |
| 63  | ENSG00000110717 | NA | NDUFS8 | NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) | 4728 | ENSG00000110717 |
| 64  | ENSG00000131174 | NA | COX7B | cytochrome c oxidase subunit VIIb | 1349 | ENSG00000131174 |
| 65  | ENSG00000170906 | NA | NDUFA3 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa | 4696 | ENSG00000170906 |
| 66  | ENSG00000184752 | NA | NDUFA12 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 | 55967 | ENSG00000184752 |
| 67  | ENSG00000156411 | NA | C14orf2 | chromosome 14 open reading frame 2 | 9556 | ENSG00000156411 |
| 68  | ENSG00000159199 | NA | ATP5G1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) | 516 | ENSG00000159199 |
| 69  | ENSG00000167283 | NA | ATP5L | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G | 10632 | ENSG00000167283 |
| 70  | ENSG00000069509 | NA | FUNDC1 | FUN14 domain containing 1 | 139341 | ENSG00000069509 |
| 71  | ENSG00000196683 | NA | TOMM7 | translocase of outer mitochondrial membrane 7 homolog (yeast) | 54543 | ENSG00000196683 |
| 72  | ENSG00000074582 | NA | BCS1L | BCS1-like (S. cerevisiae) | 617 | ENSG00000074582 |
| 73  | ENSG00000010256 | NA | UQCRC1 | ubiquinol-cytochrome c reductase core protein I | 7384 | ENSG00000010256 |
| 74  | ENSG00000137806 | NA | NDUFAF1 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 | 51103 | ENSG00000137806 |
| 75  | ENSG00000241468 | NA | ATP5J2 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 | 9551 | ENSG00000241468 |
| 76  | ENSG00000140990 | NA | NDUFB10 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa | 4716 | ENSG00000140990 |
| 77  | ENSG00000117118 | NA | SDHB | succinate dehydrogenase complex, subunit B, iron sulfur (Ip) | 6390 | ENSG00000117118 |
| 78  | ENSG00000171503 | NA | ETFDH | electron-transferring-flavoprotein dehydrogenase | 2110 | ENSG00000171503 |
| 79  | ENSG00000154518 | NA | ATP5G3 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C3 (subunit 9) | 518 | ENSG00000154518 |
| 80  | ENSG00000165629 | NA | ATP5C1 | ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 | 509 | ENSG00000165629 |
| 81  | ENSG00000115944 | NA | COX7A2L | cytochrome c oxidase subunit VIIa polypeptide 2 like | 9167 | ENSG00000115944 |
| 82  | ENSG00000148290 | NA | SURF1 | surfeit 1 | 6834 | ENSG00000148290 |
| 83  | ENSG00000101247 | NA | NDUFAF5 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 5 | 79133 | ENSG00000101247 |
| 84  | ENSG00000168653 | NA | NDUFS5 | NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) | 4725 | ENSG00000168653 |
| 85  | ENSG00000126768 | NA | TIMM17B | translocase of inner mitochondrial membrane 17 homolog B (yeast) | 10245 | ENSG00000126768 |
| 86  | ENSG00000152234 | NA | ATP5A1 | ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle | 498 | ENSG00000152234 |
| 87  | ENSG00000241837 | NA | ATP5O | ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit | 539 | ENSG00000241837 |
| Database:cellular component       Name:organelle envelope       ID:GO:0031967 | ||||||
|---|---|---|---|---|---|---|
| C=822; O=193; E=49.89; R=3.87; rawP=1.60e-64; adjP=6.34e-63 | ||||||
| Index | UserID | Value | Gene Symbol | Gene Name | EntrezGene | Ensembl |
| 1  | ENSG00000164828 | NA | SUN1 | Sad1 and UNC84 domain containing 1 | 23353 | ENSG00000164828 |
| 2  | ENSG00000087299 | NA | L2HGDH | L-2-hydroxyglutarate dehydrogenase | 79944 | ENSG00000087299 |
| 3  | ENSG00000184903 | NA | IMMP2L | IMP2 inner mitochondrial membrane peptidase-like (S. cerevisiae) | 83943 | ENSG00000184903 |
| 4  | ENSG00000143575 | NA | HAX1 | HCLS1 associated protein X-1 | 10456 | ENSG00000143575 |
| 5  | ENSG00000165264 | NA | NDUFB6 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa | 4712 | ENSG00000165264 |
| 6  | ENSG00000156467 | NA | UQCRB | ubiquinol-cytochrome c reductase binding protein | 7381 | ENSG00000156467 |
| 7  | ENSG00000116898 | NA | MRPS15 | mitochondrial ribosomal protein S15 | 64960 | ENSG00000116898 |
| 8  | ENSG00000161281 | NA | COX7A1 | cytochrome c oxidase subunit VIIa polypeptide 1 (muscle) | 1346 | ENSG00000161281 |
| 9  | ENSG00000184076 | NA | UQCR10 | ubiquinol-cytochrome c reductase, complex III subunit X | 29796 | ENSG00000184076 |
| 10  | ENSG00000078070 | NA | MCCC1 | methylcrotonoyl-CoA carboxylase 1 (alpha) | 56922 | ENSG00000078070 |
| 11  | ENSG00000075415 | NA | SLC25A3 | solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 3 | 5250 | ENSG00000075415 |
| 12  | ENSG00000156885 | NA | COX6A2 | cytochrome c oxidase subunit VIa polypeptide 2 | 1339 | ENSG00000156885 |
| 13  | ENSG00000006695 | NA | COX10 | COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) | 1352 | ENSG00000006695 |
| 14  | ENSG00000133983 | NA | COX16 | COX16 cytochrome c oxidase assembly homolog (S. cerevisiae) | 51241 | ENSG00000133983 |
| 15  | ENSG00000154723 | NA | ATP5J | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 | 522 | ENSG00000154723 |
| 16  | ENSG00000115364 | NA | MRPL19 | mitochondrial ribosomal protein L19 | 9801 | ENSG00000115364 |
| 17  | ENSG00000167969 | NA | ECI1 | enoyl-CoA delta isomerase 1 | 1632 | ENSG00000167969 |
| 18  | ENSG00000139531 | NA | SUOX | sulfite oxidase | 6821 | ENSG00000139531 |
| 19  | ENSG00000125166 | NA | GOT2 | glutamic-oxaloacetic transaminase 2, mitochondrial (aspartate aminotransferase 2) | 2806 | ENSG00000125166 |
| 20  | ENSG00000100347 | NA | SAMM50 | sorting and assembly machinery component 50 homolog (S. cerevisiae) | 25813 | ENSG00000100347 |
| 21  | ENSG00000135390 | NA | ATP5G2 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C2 (subunit 9) | 517 | ENSG00000135390 |
| 22  | ENSG00000177370 | NA | TIMM22 | translocase of inner mitochondrial membrane 22 homolog (yeast) | 29928 | ENSG00000177370 |
| 23  | ENSG00000140740 | NA | UQCRC2 | ubiquinol-cytochrome c reductase core protein II | 7385 | ENSG00000140740 |
| 24  | ENSG00000166136 | NA | NDUFB8 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa | 4714 | ENSG00000166136 |
| 25  | ENSG00000160194 | NA | NDUFV3 | NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa | 4731 | ENSG00000160194 |
| 26  | ENSG00000147684 | NA | NDUFB9 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa | 4715 | ENSG00000147684 |
| 27  | ENSG00000184983 | NA | NDUFA6 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa | 4700 | ENSG00000184983 |
| 28  | ENSG00000130414 | NA | NDUFA10 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa | 4705 | ENSG00000130414 |
| 29  | ENSG00000163626 | NA | COX18 | COX18 cytochrome c oxidase assembly homolog (S. cerevisiae) | 285521 | ENSG00000163626 |
| 30  | ENSG00000158864 | NA | NDUFS2 | NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) | 4720 | ENSG00000158864 |
| 31  | ENSG00000007923 | NA | DNAJC11 | DnaJ (Hsp40) homolog, subfamily C, member 11 | 55735 | ENSG00000007923 |
| 32  | ENSG00000173436 | NA | MINOS1 | mitochondrial inner membrane organizing system 1 | 440574 | ENSG00000173436 |
| 33  | ENSG00000105197 | NA | TIMM50 | translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae) | 92609 | ENSG00000105197 |
| 34  | ENSG00000109390 | NA | NDUFC1 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa | 4717 | ENSG00000109390 |
| 35  | ENSG00000164054 | NA | SHISA5 | shisa homolog 5 (Xenopus laevis) | 51246 | ENSG00000164054 |
| 36  | ENSG00000060762 | NA | MPC1 | mitochondrial pyruvate carrier 1 | 51660 | ENSG00000060762 |
| 37  | ENSG00000165283 | NA | STOML2 | stomatin (EPB72)-like 2 | 30968 | ENSG00000165283 |
| 38  | ENSG00000104980 | NA | TIMM44 | translocase of inner mitochondrial membrane 44 homolog (yeast) | 10469 | ENSG00000104980 |
| 39  | ENSG00000116459 | NA | ATP5F1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 | 515 | ENSG00000116459 |
| 40  | ENSG00000164466 | NA | SFXN1 | sideroflexin 1 | 94081 | ENSG00000164466 |
| 41  | ENSG00000099800 | NA | TIMM13 | translocase of inner mitochondrial membrane 13 homolog (yeast) | 26517 | ENSG00000099800 |
| 42  | ENSG00000151729 | NA | SLC25A4 | solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4 | 291 | ENSG00000151729 |
| 43  | ENSG00000178057 | NA | NDUFAF3 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 3 | 25915 | ENSG00000178057 |
| 44  | ENSG00000112992 | NA | NNT | nicotinamide nucleotide transhydrogenase | 23530 | ENSG00000112992 |
| 45  | ENSG00000213619 | NA | NDUFS3 | NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) | 4722 | ENSG00000213619 |
| 46  | ENSG00000178741 | NA | COX5A | cytochrome c oxidase subunit Va | 9377 | ENSG00000178741 |
| 47  | ENSG00000173660 | NA | UQCRH | ubiquinol-cytochrome c reductase hinge protein | 7388 | ENSG00000173660 |
| 48  | ENSG00000214253 | NA | FIS1 | fission 1 (mitochondrial outer membrane) homolog (S. cerevisiae) | 51024 | ENSG00000214253 |
| 49  | ENSG00000133028 | NA | SCO1 | SCO cytochrome oxidase deficient homolog 1 (yeast) | 6341 | ENSG00000133028 |
| 50  | ENSG00000148950 | NA | IMMP1L | IMP1 inner mitochondrial membrane peptidase-like (S. cerevisiae) | 196294 | ENSG00000148950 |
| 51  | ENSG00000119421 | NA | NDUFA8 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa | 4702 | ENSG00000119421 |
| 52  | ENSG00000126267 | NA | COX6B1 | cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) | 1340 | ENSG00000126267 |
| 53  | ENSG00000109919 | NA | MTCH2 | mitochondrial carrier 2 | 23788 | ENSG00000109919 |
| 54  | ENSG00000135940 | NA | COX5B | cytochrome c oxidase subunit Vb | 1329 | ENSG00000135940 |
| 55  | ENSG00000215021 | NA | PHB2 | prohibitin 2 | 11331 | ENSG00000215021 |
| 56  | ENSG00000145494 | NA | NDUFS6 | NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) | 4726 | ENSG00000145494 |
| 57  | ENSG00000167085 | NA | PHB | prohibitin | 5245 | ENSG00000167085 |
| 58  | ENSG00000072506 | NA | HSD17B10 | hydroxysteroid (17-beta) dehydrogenase 10 | 3028 | ENSG00000072506 |
| 59  | ENSG00000156709 | NA | AIFM1 | apoptosis-inducing factor, mitochondrion-associated, 1 | 9131 | ENSG00000156709 |
| 60  | ENSG00000189043 | NA | NDUFA4 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa | 4697 | ENSG00000189043 |
| 61  | ENSG00000131143 | NA | COX4I1 | cytochrome c oxidase subunit IV isoform 1 | 1327 | ENSG00000131143 |
| 62  | ENSG00000172115 | NA | CYCS | cytochrome c, somatic | 54205 | ENSG00000172115 |
| 63  | ENSG00000164919 | NA | COX6C | cytochrome c oxidase subunit VIc | 1345 | ENSG00000164919 |
| 64  | ENSG00000115286 | NA | NDUFS7 | NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) | 374291 | ENSG00000115286 |
| 65  | ENSG00000164258 | NA | NDUFS4 | NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) | 4724 | ENSG00000164258 |
| 66  | ENSG00000156170 | NA | NDUFAF6 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 | 137682 | ENSG00000156170 |
| 67  | ENSG00000155463 | NA | OXA1L | oxidase (cytochrome c) assembly 1-like | 5018 | ENSG00000155463 |
| 68  | ENSG00000167863 | NA | ATP5H | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d | 10476 | ENSG00000167863 |
| 69  | ENSG00000090266 | NA | NDUFB2 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa | 4708 | ENSG00000090266 |
| 70  | ENSG00000127540 | NA | UQCR11 | ubiquinol-cytochrome c reductase, complex III subunit XI | 10975 | ENSG00000127540 |
| 71  | ENSG00000179091 | NA | CYC1 | cytochrome c-1 | 1537 | ENSG00000179091 |
| 72  | ENSG00000184752 | NA | NDUFA12 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 | 55967 | ENSG00000184752 |
| 73  | ENSG00000156411 | NA | C14orf2 | chromosome 14 open reading frame 2 | 9556 | ENSG00000156411 |
| 74  | ENSG00000131844 | NA | MCCC2 | methylcrotonoyl-CoA carboxylase 2 (beta) | 64087 | ENSG00000131844 |
| 75  | ENSG00000159199 | NA | ATP5G1 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) | 516 | ENSG00000159199 |
| 76  | ENSG00000105819 | NA | PMPCB | peptidase (mitochondrial processing) beta | 9512 | ENSG00000105819 |
| 77  | ENSG00000150779 | NA | TIMM8B | translocase of inner mitochondrial membrane 8 homolog B (yeast) | 26521 | ENSG00000150779 |
| 78  | ENSG00000166855 | NA | CLPX | ClpX caseinolytic peptidase X homolog (E. coli) | 10845 | ENSG00000166855 |
| 79  | ENSG00000204228 | NA | HSD17B8 | hydroxysteroid (17-beta) dehydrogenase 8 | 7923 | ENSG00000204228 |
| 80  | ENSG00000196683 | NA | TOMM7 | translocase of outer mitochondrial membrane 7 homolog (yeast) | 54543 | ENSG00000196683 |
| 81  | ENSG00000074582 | NA | BCS1L | BCS1-like (S. cerevisiae) | 617 | ENSG00000074582 |
| 82  | ENSG00000103018 | NA | CYB5B | cytochrome b5 type B (outer mitochondrial membrane) | 80777 | ENSG00000103018 |
| 83  | ENSG00000166816 | NA | LDHD | lactate dehydrogenase D | 197257 | ENSG00000166816 |
| 84  | ENSG00000140990 | NA | NDUFB10 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa | 4716 | ENSG00000140990 |
| 85  | ENSG00000066926 | NA | FECH | ferrochelatase | 2235 | ENSG00000066926 |
| 86  | ENSG00000117118 | NA | SDHB | succinate dehydrogenase complex, subunit B, iron sulfur (Ip) | 6390 | ENSG00000117118 |
| 87  | ENSG00000138495 | NA | COX17 | COX17 cytochrome c oxidase assembly homolog (S. cerevisiae) | 10063 | ENSG00000138495 |
| 88  | ENSG00000198523 | NA | PLN | phospholamban | 5350 | ENSG00000198523 |
| 89  | ENSG00000006530 | NA | AGK | acylglycerol kinase | 55750 | ENSG00000006530 |
| 90  | ENSG00000135469 | NA | COQ10A | coenzyme Q10 homolog A (S. cerevisiae) | 93058 | ENSG00000135469 |
| 91  | ENSG00000180198 | NA | RCC1 | regulator of chromosome condensation 1 | 1104 | ENSG00000180198 |
| 92  | ENSG00000177427 | NA | SMCR7 | Smith-Magenis syndrome chromosome region, candidate 7 | 125170 | ENSG00000177427 |
| 93  | ENSG00000165629 | NA | ATP5C1 | ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 | 509 | ENSG00000165629 |
| 94  | ENSG00000115944 | NA | COX7A2L | cytochrome c oxidase subunit VIIa polypeptide 2 like | 9167 | ENSG00000115944 |
| 95  | ENSG00000123545 | NA | NDUFAF4 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 4 | 29078 | ENSG00000123545 |
| 96  | ENSG00000148290 | NA | SURF1 | surfeit 1 | 6834 | ENSG00000148290 |
| 97  | ENSG00000197150 | NA | ABCB8 | ATP-binding cassette, sub-family B (MDR/TAP), member 8 | 11194 | ENSG00000197150 |
| 98  | ENSG00000152234 | NA | ATP5A1 | ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle | 498 | ENSG00000152234 |
| 99  | ENSG00000072778 | NA | ACADVL | acyl-CoA dehydrogenase, very long chain | 37 | ENSG00000072778 |
| 100  | ENSG00000172893 | NA | DHCR7 | 7-dehydrocholesterol reductase | 1717 | ENSG00000172893 |
| 101  | ENSG00000151366 | NA | NDUFC2 | NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa | 4718 | ENSG00000151366 |
| 102  | ENSG00000196636 | NA | ACN9 | ACN9 homolog (S. cerevisiae) | 57001 | ENSG00000196636 |
| 103  | ENSG00000128609 | NA | NDUFA5 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa | 4698 | ENSG00000128609 |
| 104  | ENSG00000132305 | NA | IMMT | inner membrane protein, mitochondrial | 10989 | ENSG00000132305 |
| 105  | ENSG00000163541 | NA | SUCLG1 | succinate-CoA ligase, alpha subunit | 8802 | ENSG00000163541 |
| 106  | ENSG00000090432 | NA | MUL1 | mitochondrial E3 ubiquitin protein ligase 1 | 79594 | ENSG00000090432 |
| 107  | ENSG00000165678 | NA | GHITM | growth hormone inducible transmembrane protein | 27069 | ENSG00000165678 |
| 108  | ENSG00000146701 | NA | MDH2 | malate dehydrogenase 2, NAD (mitochondrial) | 4191 | ENSG00000146701 |
| 109  | ENSG00000125995 | NA | ROMO1 | reactive oxygen species modulator 1 | 140823 | ENSG00000125995 |
| 110  | ENSG00000136521 | NA | NDUFB5 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa | 4711 | ENSG00000136521 |
| 111  | ENSG00000173915 | NA | USMG5 | up-regulated during skeletal muscle growth 5 homolog (mouse) | 84833 | ENSG00000173915 |
| 112  | ENSG00000169020 | NA | ATP5I | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E | 521 | ENSG00000169020 |
| 113  | ENSG00000131730 | NA | CKMT2 | creatine kinase, mitochondrial 2 (sarcomeric) | 1160 | ENSG00000131730 |
| 114  | ENSG00000158882 | NA | TOMM40L | translocase of outer mitochondrial membrane 40 homolog (yeast)-like | 84134 | ENSG00000158882 |
| 115  | ENSG00000182054 | NA | IDH2 | isocitrate dehydrogenase 2 (NADP+), mitochondrial | 3418 | ENSG00000182054 |
| 116  | ENSG00000004779 | NA | NDUFAB1 | NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa | 4706 | ENSG00000004779 |
| 117  | ENSG00000120253 | NA | NUP43 | nucleoporin 43kDa | 348995 | ENSG00000120253 |
| 118  | ENSG00000168958 | NA | MFF | mitochondrial fission factor | 56947 | ENSG00000168958 |
| 119  | ENSG00000164038 | NA | SLC9B2 | solute carrier family 9, subfamily B (NHA2, cation proton antiporter 2), member 2 | 133308 | ENSG00000164038 |
| 120  | ENSG00000004961 | NA | HCCS | holocytochrome c synthase | 3052 | ENSG00000004961 |
| 121  | ENSG00000147123 | NA | NDUFB11 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa | 54539 | ENSG00000147123 |
| 122  | ENSG00000073578 | NA | SDHA | succinate dehydrogenase complex, subunit A, flavoprotein (Fp) | 6389 | ENSG00000073578 |
| 123  | ENSG00000137714 | NA | FDX1 | ferredoxin 1 | 2230 | ENSG00000137714 |
| 124  | ENSG00000119013 | NA | NDUFB3 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa | 4709 | ENSG00000119013 |
| 125  | ENSG00000169021 | NA | UQCRFS1 | ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 | 7386 | ENSG00000169021 |
| 126  | ENSG00000124523 | NA | SIRT5 | sirtuin 5 | 23408 | ENSG00000124523 |
| 127  | ENSG00000178449 | NA | COX14 | COX14 cytochrome c oxidase assembly homolog (S. cerevisiae) | 84987 | ENSG00000178449 |
| 128  | ENSG00000175193 | NA | PARL | presenilin associated, rhomboid-like | 55486 | ENSG00000175193 |
| 129  | ENSG00000078668 | NA | VDAC3 | voltage-dependent anion channel 3 | 7419 | ENSG00000078668 |
| 130  | ENSG00000111843 | NA | TMEM14C | transmembrane protein 14C | 51522 | ENSG00000111843 |
| 131  | ENSG00000162600 | NA | OMA1 | OMA1 zinc metallopeptidase homolog (S. cerevisiae) | 115209 | ENSG00000162600 |
| 132  | ENSG00000139180 | NA | NDUFA9 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa | 4704 | ENSG00000139180 |
| 133  | ENSG00000108179 | NA | PPIF | peptidylprolyl isomerase F | 10105 | ENSG00000108179 |
| 134  | ENSG00000127184 | NA | COX7C | cytochrome c oxidase subunit VIIc | 1350 | ENSG00000127184 |
| 135  | ENSG00000164405 | NA | UQCRQ | ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa | 27089 | ENSG00000164405 |
| 136  | ENSG00000165637 | NA | VDAC2 | voltage-dependent anion channel 2 | 7417 | ENSG00000165637 |
| 137  | ENSG00000173085 | NA | COQ2 | coenzyme Q2 homolog, prenyltransferase (yeast) | 27235 | ENSG00000173085 |
| 138  | ENSG00000124172 | NA | ATP5E | ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit | 514 | ENSG00000124172 |
| 139  | ENSG00000183648 | NA | NDUFB1 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa | 4707 | ENSG00000183648 |
| 140  | ENSG00000213585 | NA | VDAC1 | voltage-dependent anion channel 1 | 7416 | ENSG00000213585 |
| 141  | ENSG00000205981 | NA | DNAJC19 | DnaJ (Hsp40) homolog, subfamily C, member 19 | 131118 | ENSG00000205981 |
| 142  | ENSG00000132591 | NA | ERAL1 | Era G-protein-like 1 (E. coli) | 26284 | ENSG00000132591 |
| 143  | ENSG00000120333 | NA | MRPS14 | mitochondrial ribosomal protein S14 | 63931 | ENSG00000120333 |
| 144  | ENSG00000099624 | NA | ATP5D | ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit | 513 | ENSG00000099624 |
| 145  | ENSG00000204370 | NA | SDHD | succinate dehydrogenase complex, subunit D, integral membrane protein | 6392 | ENSG00000204370 |
| 146  | ENSG00000166949 | NA | SMAD3 | SMAD family member 3 | 4088 | ENSG00000166949 |
| 147  | ENSG00000106554 | NA | CHCHD3 | coiled-coil-helix-coiled-coil-helix domain containing 3 | 54927 | ENSG00000106554 |
| 148  | ENSG00000181610 | NA | MRPS23 | mitochondrial ribosomal protein S23 | 51649 | ENSG00000181610 |
| 149  | ENSG00000125356 | NA | NDUFA1 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa | 4694 | ENSG00000125356 |
| 150  | ENSG00000108528 | NA | SLC25A11 | solute carrier family 25 (mitochondrial carrier; oxoglutarate carrier), member 11 | 8402 | ENSG00000108528 |
| 151  | ENSG00000099795 | NA | NDUFB7 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa | 4713 | ENSG00000099795 |
| 152  | ENSG00000174032 | NA | SLC25A30 | solute carrier family 25, member 30 | 253512 | ENSG00000174032 |
| 153  | ENSG00000091732 | NA | ZC3HC1 | zinc finger, C3HC-type containing 1 | 51530 | ENSG00000091732 |
| 154  | ENSG00000023228 | NA | NDUFS1 | NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) | 4719 | ENSG00000023228 |
| 155  | ENSG00000143252 | NA | SDHC | succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa | 6391 | ENSG00000143252 |
| 156  | ENSG00000075336 | NA | TIMM21 | translocase of inner mitochondrial membrane 21 homolog (yeast) | 29090 | ENSG00000075336 |
| 157  | ENSG00000115840 | NA | SLC25A12 | solute carrier family 25 (aspartate/glutamate carrier), member 12 | 8604 | ENSG00000115840 |
| 158  | ENSG00000110955 | NA | ATP5B | ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide | 506 | ENSG00000110955 |
| 159  | ENSG00000197122 | NA | SRC | v-src sarcoma (Schmidt-Ruppin A-2) viral oncogene homolog (avian) | 6714 | ENSG00000197122 |
| 160  | ENSG00000112695 | NA | COX7A2 | cytochrome c oxidase subunit VIIa polypeptide 2 (liver) | 1347 | ENSG00000112695 |
| 161  | ENSG00000197448 | NA | GSTK1 | glutathione S-transferase kappa 1 | 373156 | ENSG00000197448 |
| 162  | ENSG00000167792 | NA | NDUFV1 | NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa | 4723 | ENSG00000167792 |
| 163  | ENSG00000131495 | NA | NDUFA2 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa | 4695 | ENSG00000131495 |
| 164  | ENSG00000065518 | NA | NDUFB4 | NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa | 4710 | ENSG00000065518 |
| 165  | ENSG00000095321 | NA | CRAT | carnitine O-acetyltransferase | 1384 | ENSG00000095321 |
| 166  | ENSG00000165688 | NA | PMPCA | peptidase (mitochondrial processing) alpha | 23203 | ENSG00000165688 |
| 167  | ENSG00000110717 | NA | NDUFS8 | NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) | 4728 | ENSG00000110717 |
| 168  | ENSG00000131174 | NA | COX7B | cytochrome c oxidase subunit VIIb | 1349 | ENSG00000131174 |
| 169  | ENSG00000170906 | NA | NDUFA3 | NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa | 4696 | ENSG00000170906 |
| 170  | ENSG00000138085 | NA | ATRAID | all-trans retinoic acid-induced differentiation factor | 51374 | ENSG00000138085 |
| 171  | ENSG00000128654 | NA | MTX2 | metaxin 2 | 10651 | ENSG00000128654 |
| 172  | ENSG00000204308 | NA | RNF5 | ring finger protein 5, E3 ubiquitin protein ligase | 6048 | ENSG00000204308 |
| 173  | ENSG00000167283 | NA | ATP5L | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G | 10632 | ENSG00000167283 |
| 174  | ENSG00000069509 | NA | FUNDC1 | FUN14 domain containing 1 | 139341 | ENSG00000069509 |
| 175  | ENSG00000183978 | NA | COA3 | cytochrome C oxidase assembly factor 3 | 28958 | ENSG00000183978 |
| 176  | ENSG00000124532 | NA | MRS2 | MRS2 magnesium homeostasis factor homolog (S. cerevisiae) | 57380 | ENSG00000124532 |
| 177  | ENSG00000131269 | NA | ABCB7 | ATP-binding cassette, sub-family B (MDR/TAP), member 7 | 22 | ENSG00000131269 |
| 178  | ENSG00000010256 | NA | UQCRC1 | ubiquinol-cytochrome c reductase core protein I | 7384 | ENSG00000010256 |
| 179  | ENSG00000137806 | NA | NDUFAF1 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 | 51103 | ENSG00000137806 |
| 180  | ENSG00000241468 | NA | ATP5J2 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 | 9551 | ENSG00000241468 |
| 181  | ENSG00000197912 | NA | SPG7 | spastic paraplegia 7 (pure and complicated autosomal recessive) | 6687 | ENSG00000197912 |
| 182  | ENSG00000171503 | NA | ETFDH | electron-transferring-flavoprotein dehydrogenase | 2110 | ENSG00000171503 |
| 183  | ENSG00000143158 | NA | MPC2 | mitochondrial pyruvate carrier 2 | 25874 | ENSG00000143158 |
| 184  | ENSG00000138796 | NA | HADH | hydroxyacyl-CoA dehydrogenase | 3033 | ENSG00000138796 |
| 185  | ENSG00000154518 | NA | ATP5G3 | ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C3 (subunit 9) | 518 | ENSG00000154518 |
| 186  | ENSG00000107317 | NA | PTGDS | prostaglandin D2 synthase 21kDa (brain) | 5730 | ENSG00000107317 |
| 187  | ENSG00000075303 | NA | SLC25A40 | solute carrier family 25, member 40 | 55972 | ENSG00000075303 |
| 188  | ENSG00000176340 | NA | COX8A | cytochrome c oxidase subunit VIIIA (ubiquitous) | 1351 | ENSG00000176340 |
| 189  | ENSG00000101247 | NA | NDUFAF5 | NADH dehydrogenase (ubiquinone) complex I, assembly factor 5 | 79133 | ENSG00000101247 |
| 190  | ENSG00000168653 | NA | NDUFS5 | NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) | 4725 | ENSG00000168653 |
| 191  | ENSG00000126768 | NA | TIMM17B | translocase of inner mitochondrial membrane 17 homolog B (yeast) | 10245 | ENSG00000126768 |
| 192  | ENSG00000247077 | NA | PGAM5 | phosphoglycerate mutase family member 5 | 192111 | ENSG00000247077 |
| 193  | ENSG00000241837 | NA | ATP5O | ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit | 539 | ENSG00000241837 |
WebGestalt is currently developed and maintained by Jing Wang and Bing Zhang at the Zhang Lab. Other people who have made significant contribution to the project include Dexter Duncan, Stefan Kirov, Zhiao Shi, and Jay Snoddy.
Funding credits: NIH/NIAAA (U01 AA016662, U01 AA013512); NIH/NIDA (P01 DA015027); NIH/NIMH (P50 MH078028, P50 MH096972); NIH/NCI (U24 CA159988); NIH/NIGMS (R01 GM088822).