WEB-based GEne SeT AnaLysis Toolkit
 
Translating gene lists into biological insights...
 



User data and parameters: User data: textAreaUpload.txt, Organism: hsapiens, Id Type: ensembl_gene_stable_id, Ref Set: entrezgene, Significance Level: Top10, Statistics Test: Hypergeometric, MTC: BH, Minimum: 2

The results for the enriched GO category are listed in this table. For each GO category, the first row lists its sub-root (biological process, molecular function, or cellular component), category name, and corresponding GO ID.
The second row lists the following statistics:
Finally, genes in the category are listed. For each gene, the table lists the user uploaded ID and value (optional), Entrez ID, Ensembl Gene Stable ID, Gene symbol, and description. Ensembl Gene Stable ID and Entrez Gene ID are linked to the Ensembl and Entrez Gene databases, respectively.

Database:biological process       Name:cellular respiration       ID:GO:0045333
C=159; O=100; E=9.74; R=10.27; rawP=1.93e-81; adjP=5.33e-78
Index UserID Value Gene Symbol Gene Name EntrezGene Ensembl
1  ENSG00000151366 NA NDUFC2 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa 4718 ENSG00000151366
2  ENSG00000128609 NA NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa 4698 ENSG00000128609
3  ENSG00000165264 NA NDUFB6 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa 4712 ENSG00000165264
4  ENSG00000163541 NA SUCLG1 succinate-CoA ligase, alpha subunit 8802 ENSG00000163541
5  ENSG00000156467 NA UQCRB ubiquinol-cytochrome c reductase binding protein 7381 ENSG00000156467
6  ENSG00000146701 NA MDH2 malate dehydrogenase 2, NAD (mitochondrial) 4191 ENSG00000146701
7  ENSG00000184076 NA UQCR10 ubiquinol-cytochrome c reductase, complex III subunit X 29796 ENSG00000184076
8  ENSG00000136521 NA NDUFB5 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa 4711 ENSG00000136521
9  ENSG00000004779 NA NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa 4706 ENSG00000004779
10  ENSG00000169020 NA ATP5I ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E 521 ENSG00000169020
11  ENSG00000182054 NA IDH2 isocitrate dehydrogenase 2 (NADP+), mitochondrial 3418 ENSG00000182054
12  ENSG00000147123 NA NDUFB11 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa 54539 ENSG00000147123
13  ENSG00000154723 NA ATP5J ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 522 ENSG00000154723
14  ENSG00000006695 NA COX10 COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) 1352 ENSG00000006695
15  ENSG00000073578 NA SDHA succinate dehydrogenase complex, subunit A, flavoprotein (Fp) 6389 ENSG00000073578
16  ENSG00000119013 NA NDUFB3 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa 4709 ENSG00000119013
17  ENSG00000169021 NA UQCRFS1 ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 7386 ENSG00000169021
18  ENSG00000062485 NA CS citrate synthase 1431 ENSG00000062485
19  ENSG00000140740 NA UQCRC2 ubiquinol-cytochrome c reductase core protein II 7385 ENSG00000140740
20  ENSG00000166136 NA NDUFB8 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa 4714 ENSG00000166136
21  ENSG00000140374 NA ETFA electron-transfer-flavoprotein, alpha polypeptide 2108 ENSG00000140374
22  ENSG00000172340 NA SUCLG2 succinate-CoA ligase, GDP-forming, beta subunit 8801 ENSG00000172340
23  ENSG00000147684 NA NDUFB9 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa 4715 ENSG00000147684
24  ENSG00000160194 NA NDUFV3 NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa 4731 ENSG00000160194
25  ENSG00000184983 NA NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa 4700 ENSG00000184983
26  ENSG00000130414 NA NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa 4705 ENSG00000130414
27  ENSG00000091140 NA DLD dihydrolipoamide dehydrogenase 1738 ENSG00000091140
28  ENSG00000165060 NA FXN frataxin 2395 ENSG00000165060
29  ENSG00000158864 NA NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) 4720 ENSG00000158864
30  ENSG00000139180 NA NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa 4704 ENSG00000139180
31  ENSG00000127184 NA COX7C cytochrome c oxidase subunit VIIc 1350 ENSG00000127184
32  ENSG00000109390 NA NDUFC1 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa 4717 ENSG00000109390
33  ENSG00000164405 NA UQCRQ ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa 27089 ENSG00000164405
34  ENSG00000091483 NA FH fumarate hydratase 2271 ENSG00000091483
35  ENSG00000122729 NA ACO1 aconitase 1, soluble 48 ENSG00000122729
36  ENSG00000124172 NA ATP5E ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit 514 ENSG00000124172
37  ENSG00000183648 NA NDUFB1 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa 4707 ENSG00000183648
38  ENSG00000142082 NA SIRT3 sirtuin 3 23410 ENSG00000142082
39  ENSG00000119689 NA DLST dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex) 1743 ENSG00000119689
40  ENSG00000168291 NA PDHB pyruvate dehydrogenase (lipoamide) beta 5162 ENSG00000168291
41  ENSG00000099624 NA ATP5D ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit 513 ENSG00000099624
42  ENSG00000204370 NA SDHD succinate dehydrogenase complex, subunit D, integral membrane protein 6392 ENSG00000204370
43  ENSG00000116459 NA ATP5F1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 515 ENSG00000116459
44  ENSG00000100412 NA ACO2 aconitase 2, mitochondrial 50 ENSG00000100412
45  ENSG00000138399 NA FASTKD1 FAST kinase domains 1 79675 ENSG00000138399
46  ENSG00000112992 NA NNT nicotinamide nucleotide transhydrogenase 23530 ENSG00000112992
47  ENSG00000125356 NA NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa 4694 ENSG00000125356
48  ENSG00000215251 NA FASTKD5 FAST kinase domains 5 60493 ENSG00000215251
49  ENSG00000213619 NA NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) 4722 ENSG00000213619
50  ENSG00000178741 NA COX5A cytochrome c oxidase subunit Va 9377 ENSG00000178741
51  ENSG00000173660 NA UQCRH ubiquinol-cytochrome c reductase hinge protein 7388 ENSG00000173660
52  ENSG00000099795 NA NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa 4713 ENSG00000099795
53  ENSG00000119421 NA NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa 4702 ENSG00000119421
54  ENSG00000126267 NA COX6B1 cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) 1340 ENSG00000126267
55  ENSG00000135940 NA COX5B cytochrome c oxidase subunit Vb 1329 ENSG00000135940
56  ENSG00000023228 NA NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) 4719 ENSG00000023228
57  ENSG00000143252 NA SDHC succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa 6391 ENSG00000143252
58  ENSG00000151376 NA ME3 malic enzyme 3, NADP(+)-dependent, mitochondrial 10873 ENSG00000151376
59  ENSG00000145494 NA NDUFS6 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) 4726 ENSG00000145494
60  ENSG00000115840 NA SLC25A12 solute carrier family 25 (aspartate/glutamate carrier), member 12 8604 ENSG00000115840
61  ENSG00000131143 NA COX4I1 cytochrome c oxidase subunit IV isoform 1 1327 ENSG00000131143
62  ENSG00000189043 NA NDUFA4 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa 4697 ENSG00000189043
63  ENSG00000172115 NA CYCS cytochrome c, somatic 54205 ENSG00000172115
64  ENSG00000110955 NA ATP5B ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide 506 ENSG00000110955
65  ENSG00000164919 NA COX6C cytochrome c oxidase subunit VIc 1345 ENSG00000164919
66  ENSG00000105379 NA ETFB electron-transfer-flavoprotein, beta polypeptide 2109 ENSG00000105379
67  ENSG00000115286 NA NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) 374291 ENSG00000115286
68  ENSG00000164258 NA NDUFS4 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) 4724 ENSG00000164258
69  ENSG00000167792 NA NDUFV1 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa 4723 ENSG00000167792
70  ENSG00000131495 NA NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa 4695 ENSG00000131495
71  ENSG00000065518 NA NDUFB4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa 4710 ENSG00000065518
72  ENSG00000155463 NA OXA1L oxidase (cytochrome c) assembly 1-like 5018 ENSG00000155463
73  ENSG00000167863 NA ATP5H ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d 10476 ENSG00000167863
74  ENSG00000090266 NA NDUFB2 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa 4708 ENSG00000090266
75  ENSG00000110717 NA NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) 4728 ENSG00000110717
76  ENSG00000127540 NA UQCR11 ubiquinol-cytochrome c reductase, complex III subunit XI 10975 ENSG00000127540
77  ENSG00000131174 NA COX7B cytochrome c oxidase subunit VIIb 1349 ENSG00000131174
78  ENSG00000179091 NA CYC1 cytochrome c-1 1537 ENSG00000179091
79  ENSG00000184752 NA NDUFA12 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 55967 ENSG00000184752
80  ENSG00000170906 NA NDUFA3 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa 4696 ENSG00000170906
81  ENSG00000159199 NA ATP5G1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) 516 ENSG00000159199
82  ENSG00000136143 NA SUCLA2 succinate-CoA ligase, ADP-forming, beta subunit 8803 ENSG00000136143
83  ENSG00000167283 NA ATP5L ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G 10632 ENSG00000167283
84  ENSG00000067829 NA IDH3G isocitrate dehydrogenase 3 (NAD+) gamma 3421 ENSG00000067829
85  ENSG00000136270 NA TBRG4 transforming growth factor beta regulator 4 9238 ENSG00000136270
86  ENSG00000010256 NA UQCRC1 ubiquinol-cytochrome c reductase core protein I 7384 ENSG00000010256
87  ENSG00000137806 NA NDUFAF1 NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 51103 ENSG00000137806
88  ENSG00000241468 NA ATP5J2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 9551 ENSG00000241468
89  ENSG00000140990 NA NDUFB10 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa 4716 ENSG00000140990
90  ENSG00000117118 NA SDHB succinate dehydrogenase complex, subunit B, iron sulfur (Ip) 6390 ENSG00000117118
91  ENSG00000171503 NA ETFDH electron-transferring-flavoprotein dehydrogenase 2110 ENSG00000171503
92  ENSG00000165629 NA ATP5C1 ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 509 ENSG00000165629
93  ENSG00000115944 NA COX7A2L cytochrome c oxidase subunit VIIa polypeptide 2 like 9167 ENSG00000115944
94  ENSG00000176340 NA COX8A cytochrome c oxidase subunit VIIIA (ubiquitous) 1351 ENSG00000176340
95  ENSG00000148290 NA SURF1 surfeit 1 6834 ENSG00000148290
96  ENSG00000014641 NA MDH1 malate dehydrogenase 1, NAD (soluble) 4190 ENSG00000014641
97  ENSG00000168653 NA NDUFS5 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) 4725 ENSG00000168653
98  ENSG00000152234 NA ATP5A1 ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle 498 ENSG00000152234
99  ENSG00000101365 NA IDH3B isocitrate dehydrogenase 3 (NAD+) beta 3420 ENSG00000101365
100  ENSG00000241837 NA ATP5O ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit 539 ENSG00000241837


Database:biological process       Name:respiratory electron transport chain       ID:GO:0022904
C=110; O=77; E=6.74; R=11.43; rawP=3.24e-68; adjP=4.47e-65
Index UserID Value Gene Symbol Gene Name EntrezGene Ensembl
1  ENSG00000151366 NA NDUFC2 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa 4718 ENSG00000151366
2  ENSG00000128609 NA NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa 4698 ENSG00000128609
3  ENSG00000165264 NA NDUFB6 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa 4712 ENSG00000165264
4  ENSG00000156467 NA UQCRB ubiquinol-cytochrome c reductase binding protein 7381 ENSG00000156467
5  ENSG00000184076 NA UQCR10 ubiquinol-cytochrome c reductase, complex III subunit X 29796 ENSG00000184076
6  ENSG00000136521 NA NDUFB5 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa 4711 ENSG00000136521
7  ENSG00000004779 NA NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa 4706 ENSG00000004779
8  ENSG00000169020 NA ATP5I ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E 521 ENSG00000169020
9  ENSG00000147123 NA NDUFB11 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa 54539 ENSG00000147123
10  ENSG00000154723 NA ATP5J ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 522 ENSG00000154723
11  ENSG00000006695 NA COX10 COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) 1352 ENSG00000006695
12  ENSG00000073578 NA SDHA succinate dehydrogenase complex, subunit A, flavoprotein (Fp) 6389 ENSG00000073578
13  ENSG00000119013 NA NDUFB3 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa 4709 ENSG00000119013
14  ENSG00000169021 NA UQCRFS1 ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 7386 ENSG00000169021
15  ENSG00000140740 NA UQCRC2 ubiquinol-cytochrome c reductase core protein II 7385 ENSG00000140740
16  ENSG00000166136 NA NDUFB8 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa 4714 ENSG00000166136
17  ENSG00000140374 NA ETFA electron-transfer-flavoprotein, alpha polypeptide 2108 ENSG00000140374
18  ENSG00000147684 NA NDUFB9 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa 4715 ENSG00000147684
19  ENSG00000160194 NA NDUFV3 NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa 4731 ENSG00000160194
20  ENSG00000184983 NA NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa 4700 ENSG00000184983
21  ENSG00000130414 NA NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa 4705 ENSG00000130414
22  ENSG00000091140 NA DLD dihydrolipoamide dehydrogenase 1738 ENSG00000091140
23  ENSG00000158864 NA NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) 4720 ENSG00000158864
24  ENSG00000139180 NA NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa 4704 ENSG00000139180
25  ENSG00000127184 NA COX7C cytochrome c oxidase subunit VIIc 1350 ENSG00000127184
26  ENSG00000109390 NA NDUFC1 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa 4717 ENSG00000109390
27  ENSG00000164405 NA UQCRQ ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa 27089 ENSG00000164405
28  ENSG00000124172 NA ATP5E ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit 514 ENSG00000124172
29  ENSG00000183648 NA NDUFB1 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa 4707 ENSG00000183648
30  ENSG00000204370 NA SDHD succinate dehydrogenase complex, subunit D, integral membrane protein 6392 ENSG00000204370
31  ENSG00000116459 NA ATP5F1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 515 ENSG00000116459
32  ENSG00000099624 NA ATP5D ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit 513 ENSG00000099624
33  ENSG00000125356 NA NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa 4694 ENSG00000125356
34  ENSG00000213619 NA NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) 4722 ENSG00000213619
35  ENSG00000178741 NA COX5A cytochrome c oxidase subunit Va 9377 ENSG00000178741
36  ENSG00000173660 NA UQCRH ubiquinol-cytochrome c reductase hinge protein 7388 ENSG00000173660
37  ENSG00000099795 NA NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa 4713 ENSG00000099795
38  ENSG00000119421 NA NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa 4702 ENSG00000119421
39  ENSG00000126267 NA COX6B1 cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) 1340 ENSG00000126267
40  ENSG00000135940 NA COX5B cytochrome c oxidase subunit Vb 1329 ENSG00000135940
41  ENSG00000023228 NA NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) 4719 ENSG00000023228
42  ENSG00000143252 NA SDHC succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa 6391 ENSG00000143252
43  ENSG00000145494 NA NDUFS6 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) 4726 ENSG00000145494
44  ENSG00000115840 NA SLC25A12 solute carrier family 25 (aspartate/glutamate carrier), member 12 8604 ENSG00000115840
45  ENSG00000131143 NA COX4I1 cytochrome c oxidase subunit IV isoform 1 1327 ENSG00000131143
46  ENSG00000189043 NA NDUFA4 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa 4697 ENSG00000189043
47  ENSG00000172115 NA CYCS cytochrome c, somatic 54205 ENSG00000172115
48  ENSG00000110955 NA ATP5B ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide 506 ENSG00000110955
49  ENSG00000164919 NA COX6C cytochrome c oxidase subunit VIc 1345 ENSG00000164919
50  ENSG00000115286 NA NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) 374291 ENSG00000115286
51  ENSG00000105379 NA ETFB electron-transfer-flavoprotein, beta polypeptide 2109 ENSG00000105379
52  ENSG00000164258 NA NDUFS4 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) 4724 ENSG00000164258
53  ENSG00000167792 NA NDUFV1 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa 4723 ENSG00000167792
54  ENSG00000131495 NA NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa 4695 ENSG00000131495
55  ENSG00000065518 NA NDUFB4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa 4710 ENSG00000065518
56  ENSG00000167863 NA ATP5H ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d 10476 ENSG00000167863
57  ENSG00000090266 NA NDUFB2 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa 4708 ENSG00000090266
58  ENSG00000110717 NA NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) 4728 ENSG00000110717
59  ENSG00000131174 NA COX7B cytochrome c oxidase subunit VIIb 1349 ENSG00000131174
60  ENSG00000127540 NA UQCR11 ubiquinol-cytochrome c reductase, complex III subunit XI 10975 ENSG00000127540
61  ENSG00000179091 NA CYC1 cytochrome c-1 1537 ENSG00000179091
62  ENSG00000184752 NA NDUFA12 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 55967 ENSG00000184752
63  ENSG00000170906 NA NDUFA3 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa 4696 ENSG00000170906
64  ENSG00000159199 NA ATP5G1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) 516 ENSG00000159199
65  ENSG00000167283 NA ATP5L ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G 10632 ENSG00000167283
66  ENSG00000010256 NA UQCRC1 ubiquinol-cytochrome c reductase core protein I 7384 ENSG00000010256
67  ENSG00000137806 NA NDUFAF1 NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 51103 ENSG00000137806
68  ENSG00000241468 NA ATP5J2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 9551 ENSG00000241468
69  ENSG00000140990 NA NDUFB10 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa 4716 ENSG00000140990
70  ENSG00000117118 NA SDHB succinate dehydrogenase complex, subunit B, iron sulfur (Ip) 6390 ENSG00000117118
71  ENSG00000171503 NA ETFDH electron-transferring-flavoprotein dehydrogenase 2110 ENSG00000171503
72  ENSG00000165629 NA ATP5C1 ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 509 ENSG00000165629
73  ENSG00000115944 NA COX7A2L cytochrome c oxidase subunit VIIa polypeptide 2 like 9167 ENSG00000115944
74  ENSG00000176340 NA COX8A cytochrome c oxidase subunit VIIIA (ubiquitous) 1351 ENSG00000176340
75  ENSG00000152234 NA ATP5A1 ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle 498 ENSG00000152234
76  ENSG00000168653 NA NDUFS5 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) 4725 ENSG00000168653
77  ENSG00000241837 NA ATP5O ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit 539 ENSG00000241837


Database:biological process       Name:electron transport chain       ID:GO:0022900
C=148; O=81; E=9.06; R=8.94; rawP=4.48e-59; adjP=4.12e-56
Index UserID Value Gene Symbol Gene Name EntrezGene Ensembl
1  ENSG00000151366 NA NDUFC2 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa 4718 ENSG00000151366
2  ENSG00000128609 NA NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa 4698 ENSG00000128609
3  ENSG00000165264 NA NDUFB6 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa 4712 ENSG00000165264
4  ENSG00000156467 NA UQCRB ubiquinol-cytochrome c reductase binding protein 7381 ENSG00000156467
5  ENSG00000184076 NA UQCR10 ubiquinol-cytochrome c reductase, complex III subunit X 29796 ENSG00000184076
6  ENSG00000136521 NA NDUFB5 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa 4711 ENSG00000136521
7  ENSG00000004779 NA NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa 4706 ENSG00000004779
8  ENSG00000169020 NA ATP5I ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E 521 ENSG00000169020
9  ENSG00000147123 NA NDUFB11 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa 54539 ENSG00000147123
10  ENSG00000154723 NA ATP5J ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 522 ENSG00000154723
11  ENSG00000006695 NA COX10 COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) 1352 ENSG00000006695
12  ENSG00000073578 NA SDHA succinate dehydrogenase complex, subunit A, flavoprotein (Fp) 6389 ENSG00000073578
13  ENSG00000137714 NA FDX1 ferredoxin 1 2230 ENSG00000137714
14  ENSG00000119013 NA NDUFB3 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa 4709 ENSG00000119013
15  ENSG00000169021 NA UQCRFS1 ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 7386 ENSG00000169021
16  ENSG00000140740 NA UQCRC2 ubiquinol-cytochrome c reductase core protein II 7385 ENSG00000140740
17  ENSG00000166136 NA NDUFB8 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa 4714 ENSG00000166136
18  ENSG00000140374 NA ETFA electron-transfer-flavoprotein, alpha polypeptide 2108 ENSG00000140374
19  ENSG00000147684 NA NDUFB9 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa 4715 ENSG00000147684
20  ENSG00000160194 NA NDUFV3 NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa 4731 ENSG00000160194
21  ENSG00000184983 NA NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa 4700 ENSG00000184983
22  ENSG00000130414 NA NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa 4705 ENSG00000130414
23  ENSG00000091140 NA DLD dihydrolipoamide dehydrogenase 1738 ENSG00000091140
24  ENSG00000158864 NA NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) 4720 ENSG00000158864
25  ENSG00000139180 NA NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa 4704 ENSG00000139180
26  ENSG00000127184 NA COX7C cytochrome c oxidase subunit VIIc 1350 ENSG00000127184
27  ENSG00000109390 NA NDUFC1 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa 4717 ENSG00000109390
28  ENSG00000164405 NA UQCRQ ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa 27089 ENSG00000164405
29  ENSG00000124172 NA ATP5E ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit 514 ENSG00000124172
30  ENSG00000183648 NA NDUFB1 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa 4707 ENSG00000183648
31  ENSG00000204370 NA SDHD succinate dehydrogenase complex, subunit D, integral membrane protein 6392 ENSG00000204370
32  ENSG00000116459 NA ATP5F1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 515 ENSG00000116459
33  ENSG00000099624 NA ATP5D ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit 513 ENSG00000099624
34  ENSG00000125356 NA NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa 4694 ENSG00000125356
35  ENSG00000213619 NA NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) 4722 ENSG00000213619
36  ENSG00000178741 NA COX5A cytochrome c oxidase subunit Va 9377 ENSG00000178741
37  ENSG00000173660 NA UQCRH ubiquinol-cytochrome c reductase hinge protein 7388 ENSG00000173660
38  ENSG00000099795 NA NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa 4713 ENSG00000099795
39  ENSG00000119421 NA NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa 4702 ENSG00000119421
40  ENSG00000100348 NA TXN2 thioredoxin 2 25828 ENSG00000100348
41  ENSG00000126267 NA COX6B1 cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) 1340 ENSG00000126267
42  ENSG00000135940 NA COX5B cytochrome c oxidase subunit Vb 1329 ENSG00000135940
43  ENSG00000023228 NA NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) 4719 ENSG00000023228
44  ENSG00000143252 NA SDHC succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa 6391 ENSG00000143252
45  ENSG00000145494 NA NDUFS6 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) 4726 ENSG00000145494
46  ENSG00000115840 NA SLC25A12 solute carrier family 25 (aspartate/glutamate carrier), member 12 8604 ENSG00000115840
47  ENSG00000131143 NA COX4I1 cytochrome c oxidase subunit IV isoform 1 1327 ENSG00000131143
48  ENSG00000189043 NA NDUFA4 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa 4697 ENSG00000189043
49  ENSG00000172115 NA CYCS cytochrome c, somatic 54205 ENSG00000172115
50  ENSG00000110955 NA ATP5B ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide 506 ENSG00000110955
51  ENSG00000164919 NA COX6C cytochrome c oxidase subunit VIc 1345 ENSG00000164919
52  ENSG00000105379 NA ETFB electron-transfer-flavoprotein, beta polypeptide 2109 ENSG00000105379
53  ENSG00000115286 NA NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) 374291 ENSG00000115286
54  ENSG00000164258 NA NDUFS4 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) 4724 ENSG00000164258
55  ENSG00000167792 NA NDUFV1 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa 4723 ENSG00000167792
56  ENSG00000131495 NA NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa 4695 ENSG00000131495
57  ENSG00000065518 NA NDUFB4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa 4710 ENSG00000065518
58  ENSG00000167863 NA ATP5H ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d 10476 ENSG00000167863
59  ENSG00000090266 NA NDUFB2 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa 4708 ENSG00000090266
60  ENSG00000110717 NA NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) 4728 ENSG00000110717
61  ENSG00000131174 NA COX7B cytochrome c oxidase subunit VIIb 1349 ENSG00000131174
62  ENSG00000127540 NA UQCR11 ubiquinol-cytochrome c reductase, complex III subunit XI 10975 ENSG00000127540
63  ENSG00000179091 NA CYC1 cytochrome c-1 1537 ENSG00000179091
64  ENSG00000184752 NA NDUFA12 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 55967 ENSG00000184752
65  ENSG00000170906 NA NDUFA3 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa 4696 ENSG00000170906
66  ENSG00000091164 NA TXNL1 thioredoxin-like 1 9352 ENSG00000091164
67  ENSG00000159199 NA ATP5G1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) 516 ENSG00000159199
68  ENSG00000167283 NA ATP5L ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G 10632 ENSG00000167283
69  ENSG00000010256 NA UQCRC1 ubiquinol-cytochrome c reductase core protein I 7384 ENSG00000010256
70  ENSG00000137806 NA NDUFAF1 NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 51103 ENSG00000137806
71  ENSG00000241468 NA ATP5J2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 9551 ENSG00000241468
72  ENSG00000103018 NA CYB5B cytochrome b5 type B (outer mitochondrial membrane) 80777 ENSG00000103018
73  ENSG00000140990 NA NDUFB10 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa 4716 ENSG00000140990
74  ENSG00000117118 NA SDHB succinate dehydrogenase complex, subunit B, iron sulfur (Ip) 6390 ENSG00000117118
75  ENSG00000171503 NA ETFDH electron-transferring-flavoprotein dehydrogenase 2110 ENSG00000171503
76  ENSG00000165629 NA ATP5C1 ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 509 ENSG00000165629
77  ENSG00000115944 NA COX7A2L cytochrome c oxidase subunit VIIa polypeptide 2 like 9167 ENSG00000115944
78  ENSG00000176340 NA COX8A cytochrome c oxidase subunit VIIIA (ubiquitous) 1351 ENSG00000176340
79  ENSG00000152234 NA ATP5A1 ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle 498 ENSG00000152234
80  ENSG00000168653 NA NDUFS5 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) 4725 ENSG00000168653
81  ENSG00000241837 NA ATP5O ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit 539 ENSG00000241837


Database:biological process       Name:generation of precursor metabolites and energy       ID:GO:0006091
C=451; O=134; E=27.62; R=4.85; rawP=3.19e-57; adjP=2.20e-54
Index UserID Value Gene Symbol Gene Name EntrezGene Ensembl
1  ENSG00000165264 NA NDUFB6 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa 4712 ENSG00000165264
2  ENSG00000156467 NA UQCRB ubiquinol-cytochrome c reductase binding protein 7381 ENSG00000156467
3  ENSG00000184076 NA UQCR10 ubiquinol-cytochrome c reductase, complex III subunit X 29796 ENSG00000184076
4  ENSG00000161281 NA COX7A1 cytochrome c oxidase subunit VIIa polypeptide 1 (muscle) 1346 ENSG00000161281
5  ENSG00000075415 NA SLC25A3 solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 3 5250 ENSG00000075415
6  ENSG00000156885 NA COX6A2 cytochrome c oxidase subunit VIa polypeptide 2 1339 ENSG00000156885
7  ENSG00000154723 NA ATP5J ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 522 ENSG00000154723
8  ENSG00000006695 NA COX10 COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) 1352 ENSG00000006695
9  ENSG00000140740 NA UQCRC2 ubiquinol-cytochrome c reductase core protein II 7385 ENSG00000140740
10  ENSG00000166136 NA NDUFB8 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa 4714 ENSG00000166136
11  ENSG00000140374 NA ETFA electron-transfer-flavoprotein, alpha polypeptide 2108 ENSG00000140374
12  ENSG00000172340 NA SUCLG2 succinate-CoA ligase, GDP-forming, beta subunit 8801 ENSG00000172340
13  ENSG00000147684 NA NDUFB9 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa 4715 ENSG00000147684
14  ENSG00000160194 NA NDUFV3 NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa 4731 ENSG00000160194
15  ENSG00000184983 NA NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa 4700 ENSG00000184983
16  ENSG00000130414 NA NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa 4705 ENSG00000130414
17  ENSG00000091140 NA DLD dihydrolipoamide dehydrogenase 1738 ENSG00000091140
18  ENSG00000165060 NA FXN frataxin 2395 ENSG00000165060
19  ENSG00000158864 NA NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) 4720 ENSG00000158864
20  ENSG00000131828 NA PDHA1 pyruvate dehydrogenase (lipoamide) alpha 1 5160 ENSG00000131828
21  ENSG00000109390 NA NDUFC1 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa 4717 ENSG00000109390
22  ENSG00000176533 NA GNG7 guanine nucleotide binding protein (G protein), gamma 7 2788 ENSG00000176533
23  ENSG00000091483 NA FH fumarate hydratase 2271 ENSG00000091483
24  ENSG00000181929 NA PRKAG1 protein kinase, AMP-activated, gamma 1 non-catalytic subunit 5571 ENSG00000181929
25  ENSG00000101440 NA ASIP agouti signaling protein 434 ENSG00000101440
26  ENSG00000119689 NA DLST dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex) 1743 ENSG00000119689
27  ENSG00000142082 NA SIRT3 sirtuin 3 23410 ENSG00000142082
28  ENSG00000168291 NA PDHB pyruvate dehydrogenase (lipoamide) beta 5162 ENSG00000168291
29  ENSG00000116459 NA ATP5F1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 515 ENSG00000116459
30  ENSG00000138399 NA FASTKD1 FAST kinase domains 1 79675 ENSG00000138399
31  ENSG00000151729 NA SLC25A4 solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4 291 ENSG00000151729
32  ENSG00000112992 NA NNT nicotinamide nucleotide transhydrogenase 23530 ENSG00000112992
33  ENSG00000149925 NA ALDOA aldolase A, fructose-bisphosphate 226 ENSG00000149925
34  ENSG00000215251 NA FASTKD5 FAST kinase domains 5 60493 ENSG00000215251
35  ENSG00000213619 NA NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) 4722 ENSG00000213619
36  ENSG00000178741 NA COX5A cytochrome c oxidase subunit Va 9377 ENSG00000178741
37  ENSG00000173660 NA UQCRH ubiquinol-cytochrome c reductase hinge protein 7388 ENSG00000173660
38  ENSG00000133028 NA SCO1 SCO cytochrome oxidase deficient homolog 1 (yeast) 6341 ENSG00000133028
39  ENSG00000087250 NA MT3 metallothionein 3 4504 ENSG00000087250
40  ENSG00000119421 NA NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa 4702 ENSG00000119421
41  ENSG00000100348 NA TXN2 thioredoxin 2 25828 ENSG00000100348
42  ENSG00000126267 NA COX6B1 cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) 1340 ENSG00000126267
43  ENSG00000135940 NA COX5B cytochrome c oxidase subunit Vb 1329 ENSG00000135940
44  ENSG00000145494 NA NDUFS6 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) 4726 ENSG00000145494
45  ENSG00000172115 NA CYCS cytochrome c, somatic 54205 ENSG00000172115
46  ENSG00000189043 NA NDUFA4 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa 4697 ENSG00000189043
47  ENSG00000131143 NA COX4I1 cytochrome c oxidase subunit IV isoform 1 1327 ENSG00000131143
48  ENSG00000164919 NA COX6C cytochrome c oxidase subunit VIc 1345 ENSG00000164919
49  ENSG00000105379 NA ETFB electron-transfer-flavoprotein, beta polypeptide 2109 ENSG00000105379
50  ENSG00000115286 NA NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) 374291 ENSG00000115286
51  ENSG00000164258 NA NDUFS4 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) 4724 ENSG00000164258
52  ENSG00000155463 NA OXA1L oxidase (cytochrome c) assembly 1-like 5018 ENSG00000155463
53  ENSG00000167863 NA ATP5H ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d 10476 ENSG00000167863
54  ENSG00000090266 NA NDUFB2 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa 4708 ENSG00000090266
55  ENSG00000108515 NA ENO3 enolase 3 (beta, muscle) 2027 ENSG00000108515
56  ENSG00000179091 NA CYC1 cytochrome c-1 1537 ENSG00000179091
57  ENSG00000127540 NA UQCR11 ubiquinol-cytochrome c reductase, complex III subunit XI 10975 ENSG00000127540
58  ENSG00000184752 NA NDUFA12 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 55967 ENSG00000184752
59  ENSG00000159199 NA ATP5G1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) 516 ENSG00000159199
60  ENSG00000136143 NA SUCLA2 succinate-CoA ligase, ADP-forming, beta subunit 8803 ENSG00000136143
61  ENSG00000172331 NA BPGM 2,3-bisphosphoglycerate mutase 669 ENSG00000172331
62  ENSG00000067829 NA IDH3G isocitrate dehydrogenase 3 (NAD+) gamma 3421 ENSG00000067829
63  ENSG00000067225 NA PKM pyruvate kinase, muscle 5315 ENSG00000067225
64  ENSG00000103018 NA CYB5B cytochrome b5 type B (outer mitochondrial membrane) 80777 ENSG00000103018
65  ENSG00000140990 NA NDUFB10 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa 4716 ENSG00000140990
66  ENSG00000066926 NA FECH ferrochelatase 2235 ENSG00000066926
67  ENSG00000087460 NA GNAS GNAS complex locus 2778 ENSG00000087460
68  ENSG00000138495 NA COX17 COX17 cytochrome c oxidase assembly homolog (S. cerevisiae) 10063 ENSG00000138495
69  ENSG00000117118 NA SDHB succinate dehydrogenase complex, subunit B, iron sulfur (Ip) 6390 ENSG00000117118
70  ENSG00000165629 NA ATP5C1 ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 509 ENSG00000165629
71  ENSG00000115944 NA COX7A2L cytochrome c oxidase subunit VIIa polypeptide 2 like 9167 ENSG00000115944
72  ENSG00000148290 NA SURF1 surfeit 1 6834 ENSG00000148290
73  ENSG00000014641 NA MDH1 malate dehydrogenase 1, NAD (soluble) 4190 ENSG00000014641
74  ENSG00000105220 NA GPI glucose-6-phosphate isomerase 2821 ENSG00000105220
75  ENSG00000152234 NA ATP5A1 ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle 498 ENSG00000152234
76  ENSG00000146729 NA GBAS glioblastoma amplified sequence 2631 ENSG00000146729
77  ENSG00000072778 NA ACADVL acyl-CoA dehydrogenase, very long chain 37 ENSG00000072778
78  ENSG00000128609 NA NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa 4698 ENSG00000128609
79  ENSG00000151366 NA NDUFC2 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa 4718 ENSG00000151366
80  ENSG00000163541 NA SUCLG1 succinate-CoA ligase, alpha subunit 8802 ENSG00000163541
81  ENSG00000146701 NA MDH2 malate dehydrogenase 2, NAD (mitochondrial) 4191 ENSG00000146701
82  ENSG00000136521 NA NDUFB5 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa 4711 ENSG00000136521
83  ENSG00000182054 NA IDH2 isocitrate dehydrogenase 2 (NADP+), mitochondrial 3418 ENSG00000182054
84  ENSG00000169020 NA ATP5I ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E 521 ENSG00000169020
85  ENSG00000004779 NA NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa 4706 ENSG00000004779
86  ENSG00000147123 NA NDUFB11 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa 54539 ENSG00000147123
87  ENSG00000073578 NA SDHA succinate dehydrogenase complex, subunit A, flavoprotein (Fp) 6389 ENSG00000073578
88  ENSG00000137714 NA FDX1 ferredoxin 1 2230 ENSG00000137714
89  ENSG00000119013 NA NDUFB3 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa 4709 ENSG00000119013
90  ENSG00000169021 NA UQCRFS1 ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 7386 ENSG00000169021
91  ENSG00000062485 NA CS citrate synthase 1431 ENSG00000062485
92  ENSG00000174021 NA GNG5 guanine nucleotide binding protein (G protein), gamma 5 2787 ENSG00000174021
93  ENSG00000139180 NA NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa 4704 ENSG00000139180
94  ENSG00000111640 NA GAPDH glyceraldehyde-3-phosphate dehydrogenase 2597 ENSG00000111640
95  ENSG00000127184 NA COX7C cytochrome c oxidase subunit VIIc 1350 ENSG00000127184
96  ENSG00000123836 NA PFKFB2 6-phosphofructo-2-kinase/fructose-2,6-biphosphatase 2 5208 ENSG00000123836
97  ENSG00000164405 NA UQCRQ ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa 27089 ENSG00000164405
98  ENSG00000122729 NA ACO1 aconitase 1, soluble 48 ENSG00000122729
99  ENSG00000124172 NA ATP5E ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit 514 ENSG00000124172
100  ENSG00000183648 NA NDUFB1 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa 4707 ENSG00000183648
101  ENSG00000204370 NA SDHD succinate dehydrogenase complex, subunit D, integral membrane protein 6392 ENSG00000204370
102  ENSG00000099624 NA ATP5D ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit 513 ENSG00000099624
103  ENSG00000100412 NA ACO2 aconitase 2, mitochondrial 50 ENSG00000100412
104  ENSG00000125356 NA NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa 4694 ENSG00000125356
105  ENSG00000099795 NA NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa 4713 ENSG00000099795
106  ENSG00000143437 NA ARNT aryl hydrocarbon receptor nuclear translocator 405 ENSG00000143437
107  ENSG00000111669 NA TPI1 triosephosphate isomerase 1 7167 ENSG00000111669
108  ENSG00000023228 NA NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) 4719 ENSG00000023228
109  ENSG00000143252 NA SDHC succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa 6391 ENSG00000143252
110  ENSG00000151376 NA ME3 malic enzyme 3, NADP(+)-dependent, mitochondrial 10873 ENSG00000151376
111  ENSG00000115840 NA SLC25A12 solute carrier family 25 (aspartate/glutamate carrier), member 12 8604 ENSG00000115840
112  ENSG00000250479 NA CHCHD10 coiled-coil-helix-coiled-coil-helix domain containing 10 400916 ENSG00000250479
113  ENSG00000110955 NA ATP5B ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide 506 ENSG00000110955
114  ENSG00000173281 NA PPP1R3B protein phosphatase 1, regulatory subunit 3B 79660 ENSG00000173281
115  ENSG00000167792 NA NDUFV1 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa 4723 ENSG00000167792
116  ENSG00000131495 NA NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa 4695 ENSG00000131495
117  ENSG00000065518 NA NDUFB4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa 4710 ENSG00000065518
118  ENSG00000110717 NA NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) 4728 ENSG00000110717
119  ENSG00000131174 NA COX7B cytochrome c oxidase subunit VIIb 1349 ENSG00000131174
120  ENSG00000170906 NA NDUFA3 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa 4696 ENSG00000170906
121  ENSG00000150594 NA ADRA2A adrenoceptor alpha 2A 150 ENSG00000150594
122  ENSG00000111716 NA LDHB lactate dehydrogenase B 3945 ENSG00000111716
123  ENSG00000091164 NA TXNL1 thioredoxin-like 1 9352 ENSG00000091164
124  ENSG00000167283 NA ATP5L ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G 10632 ENSG00000167283
125  ENSG00000136270 NA TBRG4 transforming growth factor beta regulator 4 9238 ENSG00000136270
126  ENSG00000010256 NA UQCRC1 ubiquinol-cytochrome c reductase core protein I 7384 ENSG00000010256
127  ENSG00000137806 NA NDUFAF1 NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 51103 ENSG00000137806
128  ENSG00000241468 NA ATP5J2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 9551 ENSG00000241468
129  ENSG00000171503 NA ETFDH electron-transferring-flavoprotein dehydrogenase 2110 ENSG00000171503
130  ENSG00000161533 NA ACOX1 acyl-CoA oxidase 1, palmitoyl 51 ENSG00000161533
131  ENSG00000176340 NA COX8A cytochrome c oxidase subunit VIIIA (ubiquitous) 1351 ENSG00000176340
132  ENSG00000168653 NA NDUFS5 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) 4725 ENSG00000168653
133  ENSG00000101365 NA IDH3B isocitrate dehydrogenase 3 (NAD+) beta 3420 ENSG00000101365
134  ENSG00000241837 NA ATP5O ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit 539 ENSG00000241837


Database:biological process       Name:oxidation-reduction process       ID:GO:0055114
C=558; O=147; E=34.17; R=4.30; rawP=1.92e-55; adjP=1.06e-52
Index UserID Value Gene Symbol Gene Name EntrezGene Ensembl
1  ENSG00000165264 NA NDUFB6 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa 4712 ENSG00000165264
2  ENSG00000156467 NA UQCRB ubiquinol-cytochrome c reductase binding protein 7381 ENSG00000156467
3  ENSG00000184076 NA UQCR10 ubiquinol-cytochrome c reductase, complex III subunit X 29796 ENSG00000184076
4  ENSG00000154723 NA ATP5J ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 522 ENSG00000154723
5  ENSG00000006695 NA COX10 COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) 1352 ENSG00000006695
6  ENSG00000167969 NA ECI1 enoyl-CoA delta isomerase 1 1632 ENSG00000167969
7  ENSG00000139531 NA SUOX sulfite oxidase 6821 ENSG00000139531
8  ENSG00000140740 NA UQCRC2 ubiquinol-cytochrome c reductase core protein II 7385 ENSG00000140740
9  ENSG00000166136 NA NDUFB8 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa 4714 ENSG00000166136
10  ENSG00000140374 NA ETFA electron-transfer-flavoprotein, alpha polypeptide 2108 ENSG00000140374
11  ENSG00000172340 NA SUCLG2 succinate-CoA ligase, GDP-forming, beta subunit 8801 ENSG00000172340
12  ENSG00000147684 NA NDUFB9 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa 4715 ENSG00000147684
13  ENSG00000160194 NA NDUFV3 NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa 4731 ENSG00000160194
14  ENSG00000184983 NA NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa 4700 ENSG00000184983
15  ENSG00000130414 NA NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa 4705 ENSG00000130414
16  ENSG00000091140 NA DLD dihydrolipoamide dehydrogenase 1738 ENSG00000091140
17  ENSG00000165060 NA FXN frataxin 2395 ENSG00000165060
18  ENSG00000158864 NA NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) 4720 ENSG00000158864
19  ENSG00000122971 NA ACADS acyl-CoA dehydrogenase, C-2 to C-3 short chain 35 ENSG00000122971
20  ENSG00000109390 NA NDUFC1 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa 4717 ENSG00000109390
21  ENSG00000176533 NA GNG7 guanine nucleotide binding protein (G protein), gamma 7 2788 ENSG00000176533
22  ENSG00000091483 NA FH fumarate hydratase 2271 ENSG00000091483
23  ENSG00000181929 NA PRKAG1 protein kinase, AMP-activated, gamma 1 non-catalytic subunit 5571 ENSG00000181929
24  ENSG00000119689 NA DLST dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex) 1743 ENSG00000119689
25  ENSG00000142082 NA SIRT3 sirtuin 3 23410 ENSG00000142082
26  ENSG00000168291 NA PDHB pyruvate dehydrogenase (lipoamide) beta 5162 ENSG00000168291
27  ENSG00000116459 NA ATP5F1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 515 ENSG00000116459
28  ENSG00000138399 NA FASTKD1 FAST kinase domains 1 79675 ENSG00000138399
29  ENSG00000151729 NA SLC25A4 solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4 291 ENSG00000151729
30  ENSG00000112992 NA NNT nicotinamide nucleotide transhydrogenase 23530 ENSG00000112992
31  ENSG00000126432 NA PRDX5 peroxiredoxin 5 25824 ENSG00000126432
32  ENSG00000215251 NA FASTKD5 FAST kinase domains 5 60493 ENSG00000215251
33  ENSG00000213619 NA NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) 4722 ENSG00000213619
34  ENSG00000178741 NA COX5A cytochrome c oxidase subunit Va 9377 ENSG00000178741
35  ENSG00000173660 NA UQCRH ubiquinol-cytochrome c reductase hinge protein 7388 ENSG00000173660
36  ENSG00000087250 NA MT3 metallothionein 3 4504 ENSG00000087250
37  ENSG00000119421 NA NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa 4702 ENSG00000119421
38  ENSG00000100348 NA TXN2 thioredoxin 2 25828 ENSG00000100348
39  ENSG00000126267 NA COX6B1 cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) 1340 ENSG00000126267
40  ENSG00000135940 NA COX5B cytochrome c oxidase subunit Vb 1329 ENSG00000135940
41  ENSG00000113790 NA EHHADH enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase 1962 ENSG00000113790
42  ENSG00000145494 NA NDUFS6 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) 4726 ENSG00000145494
43  ENSG00000172115 NA CYCS cytochrome c, somatic 54205 ENSG00000172115
44  ENSG00000189043 NA NDUFA4 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa 4697 ENSG00000189043
45  ENSG00000131143 NA COX4I1 cytochrome c oxidase subunit IV isoform 1 1327 ENSG00000131143
46  ENSG00000164919 NA COX6C cytochrome c oxidase subunit VIc 1345 ENSG00000164919
47  ENSG00000105379 NA ETFB electron-transfer-flavoprotein, beta polypeptide 2109 ENSG00000105379
48  ENSG00000115286 NA NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) 374291 ENSG00000115286
49  ENSG00000164258 NA NDUFS4 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) 4724 ENSG00000164258
50  ENSG00000155463 NA OXA1L oxidase (cytochrome c) assembly 1-like 5018 ENSG00000155463
51  ENSG00000167863 NA ATP5H ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d 10476 ENSG00000167863
52  ENSG00000090266 NA NDUFB2 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa 4708 ENSG00000090266
53  ENSG00000179091 NA CYC1 cytochrome c-1 1537 ENSG00000179091
54  ENSG00000127540 NA UQCR11 ubiquinol-cytochrome c reductase, complex III subunit XI 10975 ENSG00000127540
55  ENSG00000184752 NA NDUFA12 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 55967 ENSG00000184752
56  ENSG00000159199 NA ATP5G1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) 516 ENSG00000159199
57  ENSG00000136143 NA SUCLA2 succinate-CoA ligase, ADP-forming, beta subunit 8803 ENSG00000136143
58  ENSG00000003137 NA CYP26B1 cytochrome P450, family 26, subfamily B, polypeptide 1 56603 ENSG00000003137
59  ENSG00000175198 NA PCCA propionyl CoA carboxylase, alpha polypeptide 5095 ENSG00000175198
60  ENSG00000067829 NA IDH3G isocitrate dehydrogenase 3 (NAD+) gamma 3421 ENSG00000067829
61  ENSG00000082146 NA STRADB STE20-related kinase adaptor beta 55437 ENSG00000082146
62  ENSG00000116171 NA SCP2 sterol carrier protein 2 6342 ENSG00000116171
63  ENSG00000103018 NA CYB5B cytochrome b5 type B (outer mitochondrial membrane) 80777 ENSG00000103018
64  ENSG00000140990 NA NDUFB10 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa 4716 ENSG00000140990
65  ENSG00000157326 NA DHRS4 dehydrogenase/reductase (SDR family) member 4 10901 ENSG00000157326
66  ENSG00000135297 NA MTO1 mitochondrial translation optimization 1 homolog (S. cerevisiae) 25821 ENSG00000135297
67  ENSG00000087460 NA GNAS GNAS complex locus 2778 ENSG00000087460
68  ENSG00000117118 NA SDHB succinate dehydrogenase complex, subunit B, iron sulfur (Ip) 6390 ENSG00000117118
69  ENSG00000165629 NA ATP5C1 ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 509 ENSG00000165629
70  ENSG00000115944 NA COX7A2L cytochrome c oxidase subunit VIIa polypeptide 2 like 9167 ENSG00000115944
71  ENSG00000148290 NA SURF1 surfeit 1 6834 ENSG00000148290
72  ENSG00000014641 NA MDH1 malate dehydrogenase 1, NAD (soluble) 4190 ENSG00000014641
73  ENSG00000152234 NA ATP5A1 ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle 498 ENSG00000152234
74  ENSG00000072778 NA ACADVL acyl-CoA dehydrogenase, very long chain 37 ENSG00000072778
75  ENSG00000154930 NA ACSS1 acyl-CoA synthetase short-chain family member 1 84532 ENSG00000154930
76  ENSG00000128609 NA NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa 4698 ENSG00000128609
77  ENSG00000151366 NA NDUFC2 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa 4718 ENSG00000151366
78  ENSG00000163541 NA SUCLG1 succinate-CoA ligase, alpha subunit 8802 ENSG00000163541
79  ENSG00000146701 NA MDH2 malate dehydrogenase 2, NAD (mitochondrial) 4191 ENSG00000146701
80  ENSG00000136521 NA NDUFB5 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa 4711 ENSG00000136521
81  ENSG00000182054 NA IDH2 isocitrate dehydrogenase 2 (NADP+), mitochondrial 3418 ENSG00000182054
82  ENSG00000169020 NA ATP5I ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E 521 ENSG00000169020
83  ENSG00000004779 NA NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa 4706 ENSG00000004779
84  ENSG00000004961 NA HCCS holocytochrome c synthase 3052 ENSG00000004961
85  ENSG00000147123 NA NDUFB11 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa 54539 ENSG00000147123
86  ENSG00000073578 NA SDHA succinate dehydrogenase complex, subunit A, flavoprotein (Fp) 6389 ENSG00000073578
87  ENSG00000137714 NA FDX1 ferredoxin 1 2230 ENSG00000137714
88  ENSG00000119013 NA NDUFB3 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa 4709 ENSG00000119013
89  ENSG00000169021 NA UQCRFS1 ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 7386 ENSG00000169021
90  ENSG00000104325 NA DECR1 2,4-dienoyl CoA reductase 1, mitochondrial 1666 ENSG00000104325
91  ENSG00000062485 NA CS citrate synthase 1431 ENSG00000062485
92  ENSG00000122691 NA TWIST1 twist homolog 1 (Drosophila) 7291 ENSG00000122691
93  ENSG00000174021 NA GNG5 guanine nucleotide binding protein (G protein), gamma 5 2787 ENSG00000174021
94  ENSG00000167468 NA GPX4 glutathione peroxidase 4 2879 ENSG00000167468
95  ENSG00000124370 NA MCEE methylmalonyl CoA epimerase 84693 ENSG00000124370
96  ENSG00000139180 NA NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa 4704 ENSG00000139180
97  ENSG00000127184 NA COX7C cytochrome c oxidase subunit VIIc 1350 ENSG00000127184
98  ENSG00000164405 NA UQCRQ ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa 27089 ENSG00000164405
99  ENSG00000122729 NA ACO1 aconitase 1, soluble 48 ENSG00000122729
100  ENSG00000124172 NA ATP5E ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit 514 ENSG00000124172
101  ENSG00000183648 NA NDUFB1 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa 4707 ENSG00000183648
102  ENSG00000204370 NA SDHD succinate dehydrogenase complex, subunit D, integral membrane protein 6392 ENSG00000204370
103  ENSG00000099624 NA ATP5D ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit 513 ENSG00000099624
104  ENSG00000137106 NA GRHPR glyoxylate reductase/hydroxypyruvate reductase 9380 ENSG00000137106
105  ENSG00000100412 NA ACO2 aconitase 2, mitochondrial 50 ENSG00000100412
106  ENSG00000169738 NA DCXR dicarbonyl/L-xylulose reductase 51181 ENSG00000169738
107  ENSG00000160211 NA G6PD glucose-6-phosphate dehydrogenase 2539 ENSG00000160211
108  ENSG00000125356 NA NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa 4694 ENSG00000125356
109  ENSG00000100601 NA ALKBH1 alkB, alkylation repair homolog 1 (E. coli) 8846 ENSG00000100601
110  ENSG00000099795 NA NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa 4713 ENSG00000099795
111  ENSG00000111669 NA TPI1 triosephosphate isomerase 1 7167 ENSG00000111669
112  ENSG00000153574 NA RPIA ribose 5-phosphate isomerase A 22934 ENSG00000153574
113  ENSG00000023228 NA NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) 4719 ENSG00000023228
114  ENSG00000143252 NA SDHC succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa 6391 ENSG00000143252
115  ENSG00000151376 NA ME3 malic enzyme 3, NADP(+)-dependent, mitochondrial 10873 ENSG00000151376
116  ENSG00000115840 NA SLC25A12 solute carrier family 25 (aspartate/glutamate carrier), member 12 8604 ENSG00000115840
117  ENSG00000110955 NA ATP5B ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide 506 ENSG00000110955
118  ENSG00000060971 NA ACAA1 acetyl-CoA acyltransferase 1 30 ENSG00000060971
119  ENSG00000197894 NA ADH5 alcohol dehydrogenase 5 (class III), chi polypeptide 128 ENSG00000197894
120  ENSG00000173281 NA PPP1R3B protein phosphatase 1, regulatory subunit 3B 79660 ENSG00000173281
121  ENSG00000112357 NA PEX7 peroxisomal biogenesis factor 7 5191 ENSG00000112357
122  ENSG00000167792 NA NDUFV1 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa 4723 ENSG00000167792
123  ENSG00000131495 NA NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa 4695 ENSG00000131495
124  ENSG00000065518 NA NDUFB4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa 4710 ENSG00000065518
125  ENSG00000095321 NA CRAT carnitine O-acetyltransferase 1384 ENSG00000095321
126  ENSG00000110717 NA NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) 4728 ENSG00000110717
127  ENSG00000197580 NA BCO2 beta-carotene oxygenase 2 83875 ENSG00000197580
128  ENSG00000131174 NA COX7B cytochrome c oxidase subunit VIIb 1349 ENSG00000131174
129  ENSG00000170906 NA NDUFA3 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa 4696 ENSG00000170906
130  ENSG00000150594 NA ADRA2A adrenoceptor alpha 2A 150 ENSG00000150594
131  ENSG00000091164 NA TXNL1 thioredoxin-like 1 9352 ENSG00000091164
132  ENSG00000167283 NA ATP5L ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G 10632 ENSG00000167283
133  ENSG00000114054 NA PCCB propionyl CoA carboxylase, beta polypeptide 5096 ENSG00000114054
134  ENSG00000111275 NA ALDH2 aldehyde dehydrogenase 2 family (mitochondrial) 217 ENSG00000111275
135  ENSG00000127884 NA ECHS1 enoyl CoA hydratase, short chain, 1, mitochondrial 1892 ENSG00000127884
136  ENSG00000136270 NA TBRG4 transforming growth factor beta regulator 4 9238 ENSG00000136270
137  ENSG00000010256 NA UQCRC1 ubiquinol-cytochrome c reductase core protein I 7384 ENSG00000010256
138  ENSG00000137806 NA NDUFAF1 NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 51103 ENSG00000137806
139  ENSG00000241468 NA ATP5J2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 9551 ENSG00000241468
140  ENSG00000104823 NA ECH1 enoyl CoA hydratase 1, peroxisomal 1891 ENSG00000104823
141  ENSG00000171503 NA ETFDH electron-transferring-flavoprotein dehydrogenase 2110 ENSG00000171503
142  ENSG00000138796 NA HADH hydroxyacyl-CoA dehydrogenase 3033 ENSG00000138796
143  ENSG00000161533 NA ACOX1 acyl-CoA oxidase 1, palmitoyl 51 ENSG00000161533
144  ENSG00000176340 NA COX8A cytochrome c oxidase subunit VIIIA (ubiquitous) 1351 ENSG00000176340
145  ENSG00000168653 NA NDUFS5 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) 4725 ENSG00000168653
146  ENSG00000101365 NA IDH3B isocitrate dehydrogenase 3 (NAD+) beta 3420 ENSG00000101365
147  ENSG00000241837 NA ATP5O ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit 539 ENSG00000241837


Database:biological process       Name:energy derivation by oxidation of organic compounds       ID:GO:0015980
C=329; O=108; E=20.15; R=5.36; rawP=1.05e-50; adjP=4.83e-48
Index UserID Value Gene Symbol Gene Name EntrezGene Ensembl
1  ENSG00000151366 NA NDUFC2 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa 4718 ENSG00000151366
2  ENSG00000128609 NA NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa 4698 ENSG00000128609
3  ENSG00000165264 NA NDUFB6 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa 4712 ENSG00000165264
4  ENSG00000163541 NA SUCLG1 succinate-CoA ligase, alpha subunit 8802 ENSG00000163541
5  ENSG00000156467 NA UQCRB ubiquinol-cytochrome c reductase binding protein 7381 ENSG00000156467
6  ENSG00000146701 NA MDH2 malate dehydrogenase 2, NAD (mitochondrial) 4191 ENSG00000146701
7  ENSG00000184076 NA UQCR10 ubiquinol-cytochrome c reductase, complex III subunit X 29796 ENSG00000184076
8  ENSG00000136521 NA NDUFB5 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa 4711 ENSG00000136521
9  ENSG00000004779 NA NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa 4706 ENSG00000004779
10  ENSG00000169020 NA ATP5I ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E 521 ENSG00000169020
11  ENSG00000182054 NA IDH2 isocitrate dehydrogenase 2 (NADP+), mitochondrial 3418 ENSG00000182054
12  ENSG00000147123 NA NDUFB11 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa 54539 ENSG00000147123
13  ENSG00000154723 NA ATP5J ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 522 ENSG00000154723
14  ENSG00000006695 NA COX10 COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) 1352 ENSG00000006695
15  ENSG00000073578 NA SDHA succinate dehydrogenase complex, subunit A, flavoprotein (Fp) 6389 ENSG00000073578
16  ENSG00000119013 NA NDUFB3 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa 4709 ENSG00000119013
17  ENSG00000169021 NA UQCRFS1 ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 7386 ENSG00000169021
18  ENSG00000062485 NA CS citrate synthase 1431 ENSG00000062485
19  ENSG00000140740 NA UQCRC2 ubiquinol-cytochrome c reductase core protein II 7385 ENSG00000140740
20  ENSG00000166136 NA NDUFB8 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa 4714 ENSG00000166136
21  ENSG00000140374 NA ETFA electron-transfer-flavoprotein, alpha polypeptide 2108 ENSG00000140374
22  ENSG00000172340 NA SUCLG2 succinate-CoA ligase, GDP-forming, beta subunit 8801 ENSG00000172340
23  ENSG00000147684 NA NDUFB9 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa 4715 ENSG00000147684
24  ENSG00000160194 NA NDUFV3 NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa 4731 ENSG00000160194
25  ENSG00000184983 NA NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa 4700 ENSG00000184983
26  ENSG00000130414 NA NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa 4705 ENSG00000130414
27  ENSG00000091140 NA DLD dihydrolipoamide dehydrogenase 1738 ENSG00000091140
28  ENSG00000165060 NA FXN frataxin 2395 ENSG00000165060
29  ENSG00000174021 NA GNG5 guanine nucleotide binding protein (G protein), gamma 5 2787 ENSG00000174021
30  ENSG00000158864 NA NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) 4720 ENSG00000158864
31  ENSG00000139180 NA NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa 4704 ENSG00000139180
32  ENSG00000127184 NA COX7C cytochrome c oxidase subunit VIIc 1350 ENSG00000127184
33  ENSG00000109390 NA NDUFC1 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa 4717 ENSG00000109390
34  ENSG00000164405 NA UQCRQ ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa 27089 ENSG00000164405
35  ENSG00000176533 NA GNG7 guanine nucleotide binding protein (G protein), gamma 7 2788 ENSG00000176533
36  ENSG00000091483 NA FH fumarate hydratase 2271 ENSG00000091483
37  ENSG00000122729 NA ACO1 aconitase 1, soluble 48 ENSG00000122729
38  ENSG00000124172 NA ATP5E ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit 514 ENSG00000124172
39  ENSG00000183648 NA NDUFB1 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa 4707 ENSG00000183648
40  ENSG00000142082 NA SIRT3 sirtuin 3 23410 ENSG00000142082
41  ENSG00000119689 NA DLST dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex) 1743 ENSG00000119689
42  ENSG00000168291 NA PDHB pyruvate dehydrogenase (lipoamide) beta 5162 ENSG00000168291
43  ENSG00000099624 NA ATP5D ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit 513 ENSG00000099624
44  ENSG00000204370 NA SDHD succinate dehydrogenase complex, subunit D, integral membrane protein 6392 ENSG00000204370
45  ENSG00000116459 NA ATP5F1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 515 ENSG00000116459
46  ENSG00000100412 NA ACO2 aconitase 2, mitochondrial 50 ENSG00000100412
47  ENSG00000138399 NA FASTKD1 FAST kinase domains 1 79675 ENSG00000138399
48  ENSG00000151729 NA SLC25A4 solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4 291 ENSG00000151729
49  ENSG00000112992 NA NNT nicotinamide nucleotide transhydrogenase 23530 ENSG00000112992
50  ENSG00000125356 NA NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa 4694 ENSG00000125356
51  ENSG00000215251 NA FASTKD5 FAST kinase domains 5 60493 ENSG00000215251
52  ENSG00000213619 NA NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) 4722 ENSG00000213619
53  ENSG00000178741 NA COX5A cytochrome c oxidase subunit Va 9377 ENSG00000178741
54  ENSG00000173660 NA UQCRH ubiquinol-cytochrome c reductase hinge protein 7388 ENSG00000173660
55  ENSG00000087250 NA MT3 metallothionein 3 4504 ENSG00000087250
56  ENSG00000099795 NA NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa 4713 ENSG00000099795
57  ENSG00000119421 NA NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa 4702 ENSG00000119421
58  ENSG00000126267 NA COX6B1 cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) 1340 ENSG00000126267
59  ENSG00000135940 NA COX5B cytochrome c oxidase subunit Vb 1329 ENSG00000135940
60  ENSG00000023228 NA NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) 4719 ENSG00000023228
61  ENSG00000143252 NA SDHC succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa 6391 ENSG00000143252
62  ENSG00000151376 NA ME3 malic enzyme 3, NADP(+)-dependent, mitochondrial 10873 ENSG00000151376
63  ENSG00000145494 NA NDUFS6 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) 4726 ENSG00000145494
64  ENSG00000115840 NA SLC25A12 solute carrier family 25 (aspartate/glutamate carrier), member 12 8604 ENSG00000115840
65  ENSG00000131143 NA COX4I1 cytochrome c oxidase subunit IV isoform 1 1327 ENSG00000131143
66  ENSG00000189043 NA NDUFA4 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa 4697 ENSG00000189043
67  ENSG00000172115 NA CYCS cytochrome c, somatic 54205 ENSG00000172115
68  ENSG00000110955 NA ATP5B ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide 506 ENSG00000110955
69  ENSG00000164919 NA COX6C cytochrome c oxidase subunit VIc 1345 ENSG00000164919
70  ENSG00000105379 NA ETFB electron-transfer-flavoprotein, beta polypeptide 2109 ENSG00000105379
71  ENSG00000115286 NA NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) 374291 ENSG00000115286
72  ENSG00000164258 NA NDUFS4 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) 4724 ENSG00000164258
73  ENSG00000173281 NA PPP1R3B protein phosphatase 1, regulatory subunit 3B 79660 ENSG00000173281
74  ENSG00000167792 NA NDUFV1 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa 4723 ENSG00000167792
75  ENSG00000131495 NA NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa 4695 ENSG00000131495
76  ENSG00000065518 NA NDUFB4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa 4710 ENSG00000065518
77  ENSG00000155463 NA OXA1L oxidase (cytochrome c) assembly 1-like 5018 ENSG00000155463
78  ENSG00000167863 NA ATP5H ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d 10476 ENSG00000167863
79  ENSG00000090266 NA NDUFB2 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa 4708 ENSG00000090266
80  ENSG00000110717 NA NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) 4728 ENSG00000110717
81  ENSG00000127540 NA UQCR11 ubiquinol-cytochrome c reductase, complex III subunit XI 10975 ENSG00000127540
82  ENSG00000131174 NA COX7B cytochrome c oxidase subunit VIIb 1349 ENSG00000131174
83  ENSG00000179091 NA CYC1 cytochrome c-1 1537 ENSG00000179091
84  ENSG00000170906 NA NDUFA3 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa 4696 ENSG00000170906
85  ENSG00000184752 NA NDUFA12 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 55967 ENSG00000184752
86  ENSG00000150594 NA ADRA2A adrenoceptor alpha 2A 150 ENSG00000150594
87  ENSG00000159199 NA ATP5G1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) 516 ENSG00000159199
88  ENSG00000136143 NA SUCLA2 succinate-CoA ligase, ADP-forming, beta subunit 8803 ENSG00000136143
89  ENSG00000167283 NA ATP5L ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G 10632 ENSG00000167283
90  ENSG00000067829 NA IDH3G isocitrate dehydrogenase 3 (NAD+) gamma 3421 ENSG00000067829
91  ENSG00000136270 NA TBRG4 transforming growth factor beta regulator 4 9238 ENSG00000136270
92  ENSG00000010256 NA UQCRC1 ubiquinol-cytochrome c reductase core protein I 7384 ENSG00000010256
93  ENSG00000137806 NA NDUFAF1 NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 51103 ENSG00000137806
94  ENSG00000241468 NA ATP5J2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 9551 ENSG00000241468
95  ENSG00000140990 NA NDUFB10 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa 4716 ENSG00000140990
96  ENSG00000087460 NA GNAS GNAS complex locus 2778 ENSG00000087460
97  ENSG00000117118 NA SDHB succinate dehydrogenase complex, subunit B, iron sulfur (Ip) 6390 ENSG00000117118
98  ENSG00000171503 NA ETFDH electron-transferring-flavoprotein dehydrogenase 2110 ENSG00000171503
99  ENSG00000165629 NA ATP5C1 ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 509 ENSG00000165629
100  ENSG00000115944 NA COX7A2L cytochrome c oxidase subunit VIIa polypeptide 2 like 9167 ENSG00000115944
101  ENSG00000176340 NA COX8A cytochrome c oxidase subunit VIIIA (ubiquitous) 1351 ENSG00000176340
102  ENSG00000148290 NA SURF1 surfeit 1 6834 ENSG00000148290
103  ENSG00000014641 NA MDH1 malate dehydrogenase 1, NAD (soluble) 4190 ENSG00000014641
104  ENSG00000168653 NA NDUFS5 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) 4725 ENSG00000168653
105  ENSG00000152234 NA ATP5A1 ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle 498 ENSG00000152234
106  ENSG00000101365 NA IDH3B isocitrate dehydrogenase 3 (NAD+) beta 3420 ENSG00000101365
107  ENSG00000072778 NA ACADVL acyl-CoA dehydrogenase, very long chain 37 ENSG00000072778
108  ENSG00000241837 NA ATP5O ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit 539 ENSG00000241837


Database:biological process       Name:oxidative phosphorylation       ID:GO:0006119
C=69; O=47; E=4.23; R=11.12; rawP=5.01e-41; adjP=1.98e-38
Index UserID Value Gene Symbol Gene Name EntrezGene Ensembl
1  ENSG00000151366 NA NDUFC2 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa 4718 ENSG00000151366
2  ENSG00000128609 NA NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa 4698 ENSG00000128609
3  ENSG00000023228 NA NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) 4719 ENSG00000023228
4  ENSG00000165264 NA NDUFB6 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa 4712 ENSG00000165264
5  ENSG00000156467 NA UQCRB ubiquinol-cytochrome c reductase binding protein 7381 ENSG00000156467
6  ENSG00000184076 NA UQCR10 ubiquinol-cytochrome c reductase, complex III subunit X 29796 ENSG00000184076
7  ENSG00000145494 NA NDUFS6 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) 4726 ENSG00000145494
8  ENSG00000136521 NA NDUFB5 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa 4711 ENSG00000136521
9  ENSG00000250479 NA CHCHD10 coiled-coil-helix-coiled-coil-helix domain containing 10 400916 ENSG00000250479
10  ENSG00000004779 NA NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa 4706 ENSG00000004779
11  ENSG00000189043 NA NDUFA4 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa 4697 ENSG00000189043
12  ENSG00000006695 NA COX10 COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) 1352 ENSG00000006695
13  ENSG00000115286 NA NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) 374291 ENSG00000115286
14  ENSG00000164258 NA NDUFS4 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) 4724 ENSG00000164258
15  ENSG00000119013 NA NDUFB3 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa 4709 ENSG00000119013
16  ENSG00000167792 NA NDUFV1 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa 4723 ENSG00000167792
17  ENSG00000131495 NA NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa 4695 ENSG00000131495
18  ENSG00000065518 NA NDUFB4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa 4710 ENSG00000065518
19  ENSG00000090266 NA NDUFB2 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa 4708 ENSG00000090266
20  ENSG00000140740 NA UQCRC2 ubiquinol-cytochrome c reductase core protein II 7385 ENSG00000140740
21  ENSG00000166136 NA NDUFB8 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa 4714 ENSG00000166136
22  ENSG00000110717 NA NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) 4728 ENSG00000110717
23  ENSG00000147684 NA NDUFB9 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa 4715 ENSG00000147684
24  ENSG00000160194 NA NDUFV3 NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa 4731 ENSG00000160194
25  ENSG00000184983 NA NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa 4700 ENSG00000184983
26  ENSG00000170906 NA NDUFA3 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa 4696 ENSG00000170906
27  ENSG00000130414 NA NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa 4705 ENSG00000130414
28  ENSG00000091140 NA DLD dihydrolipoamide dehydrogenase 1738 ENSG00000091140
29  ENSG00000165060 NA FXN frataxin 2395 ENSG00000165060
30  ENSG00000158864 NA NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) 4720 ENSG00000158864
31  ENSG00000139180 NA NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa 4704 ENSG00000139180
32  ENSG00000109390 NA NDUFC1 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa 4717 ENSG00000109390
33  ENSG00000010256 NA UQCRC1 ubiquinol-cytochrome c reductase core protein I 7384 ENSG00000010256
34  ENSG00000137806 NA NDUFAF1 NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 51103 ENSG00000137806
35  ENSG00000183648 NA NDUFB1 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa 4707 ENSG00000183648
36  ENSG00000140990 NA NDUFB10 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa 4716 ENSG00000140990
37  ENSG00000204370 NA SDHD succinate dehydrogenase complex, subunit D, integral membrane protein 6392 ENSG00000204370
38  ENSG00000099624 NA ATP5D ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit 513 ENSG00000099624
39  ENSG00000165629 NA ATP5C1 ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 509 ENSG00000165629
40  ENSG00000125356 NA NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa 4694 ENSG00000125356
41  ENSG00000148290 NA SURF1 surfeit 1 6834 ENSG00000148290
42  ENSG00000213619 NA NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) 4722 ENSG00000213619
43  ENSG00000173660 NA UQCRH ubiquinol-cytochrome c reductase hinge protein 7388 ENSG00000173660
44  ENSG00000168653 NA NDUFS5 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) 4725 ENSG00000168653
45  ENSG00000099795 NA NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa 4713 ENSG00000099795
46  ENSG00000146729 NA GBAS glioblastoma amplified sequence 2631 ENSG00000146729
47  ENSG00000119421 NA NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa 4702 ENSG00000119421


Database:biological process       Name:mitochondrial ATP synthesis coupled electron transport       ID:GO:0042775
C=58; O=40; E=3.55; R=11.26; rawP=2.06e-35; adjP=5.69e-33
Index UserID Value Gene Symbol Gene Name EntrezGene Ensembl
1  ENSG00000151366 NA NDUFC2 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa 4718 ENSG00000151366
2  ENSG00000128609 NA NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa 4698 ENSG00000128609
3  ENSG00000023228 NA NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) 4719 ENSG00000023228
4  ENSG00000165264 NA NDUFB6 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa 4712 ENSG00000165264
5  ENSG00000156467 NA UQCRB ubiquinol-cytochrome c reductase binding protein 7381 ENSG00000156467
6  ENSG00000184076 NA UQCR10 ubiquinol-cytochrome c reductase, complex III subunit X 29796 ENSG00000184076
7  ENSG00000145494 NA NDUFS6 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) 4726 ENSG00000145494
8  ENSG00000136521 NA NDUFB5 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa 4711 ENSG00000136521
9  ENSG00000004779 NA NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa 4706 ENSG00000004779
10  ENSG00000189043 NA NDUFA4 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa 4697 ENSG00000189043
11  ENSG00000006695 NA COX10 COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) 1352 ENSG00000006695
12  ENSG00000115286 NA NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) 374291 ENSG00000115286
13  ENSG00000164258 NA NDUFS4 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) 4724 ENSG00000164258
14  ENSG00000119013 NA NDUFB3 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa 4709 ENSG00000119013
15  ENSG00000167792 NA NDUFV1 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa 4723 ENSG00000167792
16  ENSG00000131495 NA NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa 4695 ENSG00000131495
17  ENSG00000065518 NA NDUFB4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa 4710 ENSG00000065518
18  ENSG00000090266 NA NDUFB2 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa 4708 ENSG00000090266
19  ENSG00000166136 NA NDUFB8 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa 4714 ENSG00000166136
20  ENSG00000110717 NA NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) 4728 ENSG00000110717
21  ENSG00000147684 NA NDUFB9 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa 4715 ENSG00000147684
22  ENSG00000160194 NA NDUFV3 NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa 4731 ENSG00000160194
23  ENSG00000184983 NA NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa 4700 ENSG00000184983
24  ENSG00000170906 NA NDUFA3 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa 4696 ENSG00000170906
25  ENSG00000091140 NA DLD dihydrolipoamide dehydrogenase 1738 ENSG00000091140
26  ENSG00000130414 NA NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa 4705 ENSG00000130414
27  ENSG00000158864 NA NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) 4720 ENSG00000158864
28  ENSG00000139180 NA NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa 4704 ENSG00000139180
29  ENSG00000109390 NA NDUFC1 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa 4717 ENSG00000109390
30  ENSG00000010256 NA UQCRC1 ubiquinol-cytochrome c reductase core protein I 7384 ENSG00000010256
31  ENSG00000137806 NA NDUFAF1 NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 51103 ENSG00000137806
32  ENSG00000183648 NA NDUFB1 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa 4707 ENSG00000183648
33  ENSG00000140990 NA NDUFB10 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa 4716 ENSG00000140990
34  ENSG00000204370 NA SDHD succinate dehydrogenase complex, subunit D, integral membrane protein 6392 ENSG00000204370
35  ENSG00000125356 NA NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa 4694 ENSG00000125356
36  ENSG00000213619 NA NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) 4722 ENSG00000213619
37  ENSG00000173660 NA UQCRH ubiquinol-cytochrome c reductase hinge protein 7388 ENSG00000173660
38  ENSG00000168653 NA NDUFS5 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) 4725 ENSG00000168653
39  ENSG00000099795 NA NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa 4713 ENSG00000099795
40  ENSG00000119421 NA NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa 4702 ENSG00000119421


Database:biological process       Name:ATP synthesis coupled electron transport       ID:GO:0042773
C=58; O=40; E=3.55; R=11.26; rawP=2.06e-35; adjP=5.69e-33
Index UserID Value Gene Symbol Gene Name EntrezGene Ensembl
1  ENSG00000151366 NA NDUFC2 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa 4718 ENSG00000151366
2  ENSG00000128609 NA NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa 4698 ENSG00000128609
3  ENSG00000023228 NA NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) 4719 ENSG00000023228
4  ENSG00000165264 NA NDUFB6 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa 4712 ENSG00000165264
5  ENSG00000156467 NA UQCRB ubiquinol-cytochrome c reductase binding protein 7381 ENSG00000156467
6  ENSG00000184076 NA UQCR10 ubiquinol-cytochrome c reductase, complex III subunit X 29796 ENSG00000184076
7  ENSG00000145494 NA NDUFS6 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) 4726 ENSG00000145494
8  ENSG00000136521 NA NDUFB5 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa 4711 ENSG00000136521
9  ENSG00000004779 NA NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa 4706 ENSG00000004779
10  ENSG00000189043 NA NDUFA4 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa 4697 ENSG00000189043
11  ENSG00000006695 NA COX10 COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) 1352 ENSG00000006695
12  ENSG00000115286 NA NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) 374291 ENSG00000115286
13  ENSG00000164258 NA NDUFS4 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) 4724 ENSG00000164258
14  ENSG00000119013 NA NDUFB3 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa 4709 ENSG00000119013
15  ENSG00000167792 NA NDUFV1 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa 4723 ENSG00000167792
16  ENSG00000131495 NA NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa 4695 ENSG00000131495
17  ENSG00000065518 NA NDUFB4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa 4710 ENSG00000065518
18  ENSG00000090266 NA NDUFB2 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa 4708 ENSG00000090266
19  ENSG00000166136 NA NDUFB8 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa 4714 ENSG00000166136
20  ENSG00000110717 NA NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) 4728 ENSG00000110717
21  ENSG00000147684 NA NDUFB9 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa 4715 ENSG00000147684
22  ENSG00000160194 NA NDUFV3 NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa 4731 ENSG00000160194
23  ENSG00000184983 NA NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa 4700 ENSG00000184983
24  ENSG00000170906 NA NDUFA3 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa 4696 ENSG00000170906
25  ENSG00000091140 NA DLD dihydrolipoamide dehydrogenase 1738 ENSG00000091140
26  ENSG00000130414 NA NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa 4705 ENSG00000130414
27  ENSG00000158864 NA NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) 4720 ENSG00000158864
28  ENSG00000139180 NA NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa 4704 ENSG00000139180
29  ENSG00000109390 NA NDUFC1 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa 4717 ENSG00000109390
30  ENSG00000010256 NA UQCRC1 ubiquinol-cytochrome c reductase core protein I 7384 ENSG00000010256
31  ENSG00000137806 NA NDUFAF1 NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 51103 ENSG00000137806
32  ENSG00000183648 NA NDUFB1 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa 4707 ENSG00000183648
33  ENSG00000140990 NA NDUFB10 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa 4716 ENSG00000140990
34  ENSG00000204370 NA SDHD succinate dehydrogenase complex, subunit D, integral membrane protein 6392 ENSG00000204370
35  ENSG00000125356 NA NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa 4694 ENSG00000125356
36  ENSG00000213619 NA NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) 4722 ENSG00000213619
37  ENSG00000173660 NA UQCRH ubiquinol-cytochrome c reductase hinge protein 7388 ENSG00000173660
38  ENSG00000168653 NA NDUFS5 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) 4725 ENSG00000168653
39  ENSG00000099795 NA NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa 4713 ENSG00000099795
40  ENSG00000119421 NA NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa 4702 ENSG00000119421


Database:biological process       Name:small molecule metabolic process       ID:GO:0044281
C=2515; O=302; E=154.03; R=1.96; rawP=1.91e-35; adjP=5.69e-33
Index UserID Value Gene Symbol Gene Name EntrezGene Ensembl
1  ENSG00000168803 NA ADAL adenosine deaminase-like 161823 ENSG00000168803
2  ENSG00000165264 NA NDUFB6 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa 4712 ENSG00000165264
3  ENSG00000148672 NA GLUD1 glutamate dehydrogenase 1 2746 ENSG00000148672
4  ENSG00000169375 NA SIN3A SIN3 transcription regulator homolog A (yeast) 25942 ENSG00000169375
5  ENSG00000164172 NA MOCS2 molybdenum cofactor synthesis 2 4338 ENSG00000164172
6  ENSG00000239264 NA TXNDC5 thioredoxin domain containing 5 (endoplasmic reticulum) 81567 ENSG00000239264
7  ENSG00000135390 NA ATP5G2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C2 (subunit 9) 517 ENSG00000135390
8  ENSG00000166136 NA NDUFB8 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa 4714 ENSG00000166136
9  ENSG00000116353 NA MECR mitochondrial trans-2-enoyl-CoA reductase 51102 ENSG00000116353
10  ENSG00000172340 NA SUCLG2 succinate-CoA ligase, GDP-forming, beta subunit 8801 ENSG00000172340
11  ENSG00000151093 NA OXSM 3-oxoacyl-ACP synthase, mitochondrial 54995 ENSG00000151093
12  ENSG00000130414 NA NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa 4705 ENSG00000130414
13  ENSG00000091140 NA DLD dihydrolipoamide dehydrogenase 1738 ENSG00000091140
14  ENSG00000131828 NA PDHA1 pyruvate dehydrogenase (lipoamide) alpha 1 5160 ENSG00000131828
15  ENSG00000122971 NA ACADS acyl-CoA dehydrogenase, C-2 to C-3 short chain 35 ENSG00000122971
16  ENSG00000103356 NA EARS2 glutamyl-tRNA synthetase 2, mitochondrial (putative) 124454 ENSG00000103356
17  ENSG00000109390 NA NDUFC1 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa 4717 ENSG00000109390
18  ENSG00000176533 NA GNG7 guanine nucleotide binding protein (G protein), gamma 7 2788 ENSG00000176533
19  ENSG00000091483 NA FH fumarate hydratase 2271 ENSG00000091483
20  ENSG00000203797 NA DDO D-aspartate oxidase 8528 ENSG00000203797
21  ENSG00000123384 NA LRP1 low density lipoprotein receptor-related protein 1 4035 ENSG00000123384
22  ENSG00000135218 NA CD36 CD36 molecule (thrombospondin receptor) 948 ENSG00000135218
23  ENSG00000127838 NA PNKD paroxysmal nonkinesigenic dyskinesia 25953 ENSG00000127838
24  ENSG00000119537 NA KDSR 3-ketodihydrosphingosine reductase 2531 ENSG00000119537
25  ENSG00000151729 NA SLC25A4 solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4 291 ENSG00000151729
26  ENSG00000185627 NA PSMD13 proteasome (prosome, macropain) 26S subunit, non-ATPase, 13 5719 ENSG00000185627
27  ENSG00000119383 NA PPP2R4 protein phosphatase 2A activator, regulatory subunit 4 5524 ENSG00000119383
28  ENSG00000126432 NA PRDX5 peroxiredoxin 5 25824 ENSG00000126432
29  ENSG00000149925 NA ALDOA aldolase A, fructose-bisphosphate 226 ENSG00000149925
30  ENSG00000023330 NA ALAS1 aminolevulinate, delta-, synthase 1 211 ENSG00000023330
31  ENSG00000178741 NA COX5A cytochrome c oxidase subunit Va 9377 ENSG00000178741
32  ENSG00000213619 NA NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) 4722 ENSG00000213619
33  ENSG00000173660 NA UQCRH ubiquinol-cytochrome c reductase hinge protein 7388 ENSG00000173660
34  ENSG00000100348 NA TXN2 thioredoxin 2 25828 ENSG00000100348
35  ENSG00000140876 NA NUDT7 nudix (nucleoside diphosphate linked moiety X)-type motif 7 283927 ENSG00000140876
36  ENSG00000114854 NA TNNC1 troponin C type 1 (slow) 7134 ENSG00000114854
37  ENSG00000135940 NA COX5B cytochrome c oxidase subunit Vb 1329 ENSG00000135940
38  ENSG00000129991 NA TNNI3 troponin I type 3 (cardiac) 7137 ENSG00000129991
39  ENSG00000113790 NA EHHADH enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase 1962 ENSG00000113790
40  ENSG00000172115 NA CYCS cytochrome c, somatic 54205 ENSG00000172115
41  ENSG00000189043 NA NDUFA4 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa 4697 ENSG00000189043
42  ENSG00000123739 NA PLA2G12A phospholipase A2, group XIIA 81579 ENSG00000123739
43  ENSG00000164919 NA COX6C cytochrome c oxidase subunit VIc 1345 ENSG00000164919
44  ENSG00000185100 NA ADSSL1 adenylosuccinate synthase like 1 122622 ENSG00000185100
45  ENSG00000115286 NA NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) 374291 ENSG00000115286
46  ENSG00000139131 NA YARS2 tyrosyl-tRNA synthetase 2, mitochondrial 51067 ENSG00000139131
47  ENSG00000164258 NA NDUFS4 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) 4724 ENSG00000164258
48  ENSG00000155463 NA OXA1L oxidase (cytochrome c) assembly 1-like 5018 ENSG00000155463
49  ENSG00000167863 NA ATP5H ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d 10476 ENSG00000167863
50  ENSG00000137077 NA CCL21 chemokine (C-C motif) ligand 21 6366 ENSG00000137077
51  ENSG00000130203 NA APOE apolipoprotein E 348 ENSG00000130203
52  ENSG00000179091 NA CYC1 cytochrome c-1 1537 ENSG00000179091
53  ENSG00000166165 NA CKB creatine kinase, brain 1152 ENSG00000166165
54  ENSG00000127540 NA UQCR11 ubiquinol-cytochrome c reductase, complex III subunit XI 10975 ENSG00000127540
55  ENSG00000184752 NA NDUFA12 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 55967 ENSG00000184752
56  ENSG00000132423 NA COQ3 coenzyme Q3 homolog, methyltransferase (S. cerevisiae) 51805 ENSG00000132423
57  ENSG00000131844 NA MCCC2 methylcrotonoyl-CoA carboxylase 2 (beta) 64087 ENSG00000131844
58  ENSG00000134905 NA CARS2 cysteinyl-tRNA synthetase 2, mitochondrial (putative) 79587 ENSG00000134905
59  ENSG00000204228 NA HSD17B8 hydroxysteroid (17-beta) dehydrogenase 8 7923 ENSG00000204228
60  ENSG00000197283 NA SYNGAP1 synaptic Ras GTPase activating protein 1 8831 ENSG00000197283
61  ENSG00000175198 NA PCCA propionyl CoA carboxylase, alpha polypeptide 5095 ENSG00000175198
62  ENSG00000067829 NA IDH3G isocitrate dehydrogenase 3 (NAD+) gamma 3421 ENSG00000067829
63  ENSG00000129187 NA DCTD dCMP deaminase 1635 ENSG00000129187
64  ENSG00000067225 NA PKM pyruvate kinase, muscle 5315 ENSG00000067225
65  ENSG00000140990 NA NDUFB10 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa 4716 ENSG00000140990
66  ENSG00000157326 NA DHRS4 dehydrogenase/reductase (SDR family) member 4 10901 ENSG00000157326
67  ENSG00000135297 NA MTO1 mitochondrial translation optimization 1 homolog (S. cerevisiae) 25821 ENSG00000135297
68  ENSG00000247626 NA MARS2 methionyl-tRNA synthetase 2, mitochondrial 92935 ENSG00000247626
69  ENSG00000167363 NA FN3K fructosamine 3 kinase 64122 ENSG00000167363
70  ENSG00000165629 NA ATP5C1 ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 509 ENSG00000165629
71  ENSG00000116906 NA GNPAT glyceronephosphate O-acyltransferase 8443 ENSG00000116906
72  ENSG00000148290 NA SURF1 surfeit 1 6834 ENSG00000148290
73  ENSG00000014641 NA MDH1 malate dehydrogenase 1, NAD (soluble) 4190 ENSG00000014641
74  ENSG00000105220 NA GPI glucose-6-phosphate isomerase 2821 ENSG00000105220
75  ENSG00000133315 NA MACROD1 MACRO domain containing 1 28992 ENSG00000133315
76  ENSG00000072778 NA ACADVL acyl-CoA dehydrogenase, very long chain 37 ENSG00000072778
77  ENSG00000172893 NA DHCR7 7-dehydrocholesterol reductase 1717 ENSG00000172893
78  ENSG00000154930 NA ACSS1 acyl-CoA synthetase short-chain family member 1 84532 ENSG00000154930
79  ENSG00000108774 NA RAB5C RAB5C, member RAS oncogene family 5878 ENSG00000108774
80  ENSG00000196636 NA ACN9 ACN9 homolog (S. cerevisiae) 57001 ENSG00000196636
81  ENSG00000139410 NA SDSL serine dehydratase-like 113675 ENSG00000139410
82  ENSG00000059691 NA PET112 PET112 homolog (yeast) 5188 ENSG00000059691
83  ENSG00000112981 NA NME5 NME/NM23 family member 5 8382 ENSG00000112981
84  ENSG00000126088 NA UROD uroporphyrinogen decarboxylase 7389 ENSG00000126088
85  ENSG00000138430 NA OLA1 Obg-like ATPase 1 29789 ENSG00000138430
86  ENSG00000136521 NA NDUFB5 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa 4711 ENSG00000136521
87  ENSG00000004779 NA NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa 4706 ENSG00000004779
88  ENSG00000169020 NA ATP5I ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E 521 ENSG00000169020
89  ENSG00000182054 NA IDH2 isocitrate dehydrogenase 2 (NADP+), mitochondrial 3418 ENSG00000182054
90  ENSG00000120253 NA NUP43 nucleoporin 43kDa 348995 ENSG00000120253
91  ENSG00000085871 NA MGST2 microsomal glutathione S-transferase 2 4258 ENSG00000085871
92  ENSG00000172954 NA LCLAT1 lysocardiolipin acyltransferase 1 253558 ENSG00000172954
93  ENSG00000073578 NA SDHA succinate dehydrogenase complex, subunit A, flavoprotein (Fp) 6389 ENSG00000073578
94  ENSG00000119013 NA NDUFB3 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa 4709 ENSG00000119013
95  ENSG00000104325 NA DECR1 2,4-dienoyl CoA reductase 1, mitochondrial 1666 ENSG00000104325
96  ENSG00000144827 NA ABHD10 abhydrolase domain containing 10 55347 ENSG00000144827
97  ENSG00000173786 NA CNP 2',3'-cyclic nucleotide 3' phosphodiesterase 1267 ENSG00000173786
98  ENSG00000139180 NA NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa 4704 ENSG00000139180
99  ENSG00000127184 NA COX7C cytochrome c oxidase subunit VIIc 1350 ENSG00000127184
100  ENSG00000111640 NA GAPDH glyceraldehyde-3-phosphate dehydrogenase 2597 ENSG00000111640
101  ENSG00000123836 NA PFKFB2 6-phosphofructo-2-kinase/fructose-2,6-biphosphatase 2 5208 ENSG00000123836
102  ENSG00000130208 NA APOC1 apolipoprotein C-I 341 ENSG00000130208
103  ENSG00000120265 NA PCMT1 protein-L-isoaspartate (D-aspartate) O-methyltransferase 5110 ENSG00000120265
104  ENSG00000204370 NA SDHD succinate dehydrogenase complex, subunit D, integral membrane protein 6392 ENSG00000204370
105  ENSG00000137106 NA GRHPR glyoxylate reductase/hydroxypyruvate reductase 9380 ENSG00000137106
106  ENSG00000169738 NA DCXR dicarbonyl/L-xylulose reductase 51181 ENSG00000169738
107  ENSG00000160211 NA G6PD glucose-6-phosphate dehydrogenase 2539 ENSG00000160211
108  ENSG00000138777 NA PPA2 pyrophosphatase (inorganic) 2 27068 ENSG00000138777
109  ENSG00000117280 NA RAB7L1 RAB7, member RAS oncogene family-like 1 8934 ENSG00000117280
110  ENSG00000111669 NA TPI1 triosephosphate isomerase 1 7167 ENSG00000111669
111  ENSG00000138823 NA MTTP microsomal triglyceride transfer protein 4547 ENSG00000138823
112  ENSG00000023228 NA NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) 4719 ENSG00000023228
113  ENSG00000100116 NA GCAT glycine C-acetyltransferase 23464 ENSG00000100116
114  ENSG00000143252 NA SDHC succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa 6391 ENSG00000143252
115  ENSG00000151376 NA ME3 malic enzyme 3, NADP(+)-dependent, mitochondrial 10873 ENSG00000151376
116  ENSG00000145982 NA FARS2 phenylalanyl-tRNA synthetase 2, mitochondrial 10667 ENSG00000145982
117  ENSG00000115840 NA SLC25A12 solute carrier family 25 (aspartate/glutamate carrier), member 12 8604 ENSG00000115840
118  ENSG00000121897 NA LIAS lipoic acid synthetase 11019 ENSG00000121897
119  ENSG00000110955 NA ATP5B ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide 506 ENSG00000110955
120  ENSG00000147155 NA EBP emopamil binding protein (sterol isomerase) 10682 ENSG00000147155
121  ENSG00000179958 NA DCTPP1 dCTP pyrophosphatase 1 79077 ENSG00000179958
122  ENSG00000131495 NA NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa 4695 ENSG00000131495
123  ENSG00000083720 NA OXCT1 3-oxoacid CoA transferase 1 5019 ENSG00000083720
124  ENSG00000065518 NA NDUFB4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa 4710 ENSG00000065518
125  ENSG00000095321 NA CRAT carnitine O-acetyltransferase 1384 ENSG00000095321
126  ENSG00000159445 NA THEM4 thioesterase superfamily member 4 117145 ENSG00000159445
127  ENSG00000120992 NA LYPLA1 lysophospholipase I 10434 ENSG00000120992
128  ENSG00000198721 NA ECI2 enoyl-CoA delta isomerase 2 10455 ENSG00000198721
129  ENSG00000112855 NA HARS2 histidyl-tRNA synthetase 2, mitochondrial 23438 ENSG00000112855
130  ENSG00000197580 NA BCO2 beta-carotene oxygenase 2 83875 ENSG00000197580
131  ENSG00000131174 NA COX7B cytochrome c oxidase subunit VIIb 1349 ENSG00000131174
132  ENSG00000147853 NA AK3 adenylate kinase 3 50808 ENSG00000147853
133  ENSG00000170906 NA NDUFA3 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa 4696 ENSG00000170906
134  ENSG00000205309 NA NT5M 5',3'-nucleotidase, mitochondrial 56953 ENSG00000205309
135  ENSG00000106305 NA AIMP2 aminoacyl tRNA synthetase complex-interacting multifunctional protein 2 7965 ENSG00000106305
136  ENSG00000160808 NA MYL3 myosin, light chain 3, alkali; ventricular, skeletal, slow 4634 ENSG00000160808
137  ENSG00000142507 NA PSMB6 proteasome (prosome, macropain) subunit, beta type, 6 5694 ENSG00000142507
138  ENSG00000111716 NA LDHB lactate dehydrogenase B 3945 ENSG00000111716
139  ENSG00000108439 NA PNPO pyridoxamine 5'-phosphate oxidase 55163 ENSG00000108439
140  ENSG00000114054 NA PCCB propionyl CoA carboxylase, beta polypeptide 5096 ENSG00000114054
141  ENSG00000167283 NA ATP5L ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G 10632 ENSG00000167283
142  ENSG00000111275 NA ALDH2 aldehyde dehydrogenase 2 family (mitochondrial) 217 ENSG00000111275
143  ENSG00000136928 NA GABBR2 gamma-aminobutyric acid (GABA) B receptor, 2 9568 ENSG00000136928
144  ENSG00000078401 NA EDN1 endothelin 1 1906 ENSG00000078401
145  ENSG00000010256 NA UQCRC1 ubiquinol-cytochrome c reductase core protein I 7384 ENSG00000010256
146  ENSG00000104823 NA ECH1 enoyl CoA hydratase 1, peroxisomal 1891 ENSG00000104823
147  ENSG00000171503 NA ETFDH electron-transferring-flavoprotein dehydrogenase 2110 ENSG00000171503
148  ENSG00000138796 NA HADH hydroxyacyl-CoA dehydrogenase 3033 ENSG00000138796
149  ENSG00000154518 NA ATP5G3 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C3 (subunit 9) 518 ENSG00000154518
150  ENSG00000088682 NA COQ9 coenzyme Q9 homolog (S. cerevisiae) 57017 ENSG00000088682
151  ENSG00000161533 NA ACOX1 acyl-CoA oxidase 1, palmitoyl 51 ENSG00000161533
152  ENSG00000168653 NA NDUFS5 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) 4725 ENSG00000168653
153  ENSG00000156110 NA ADK adenosine kinase 132 ENSG00000156110
154  ENSG00000087299 NA L2HGDH L-2-hydroxyglutarate dehydrogenase 79944 ENSG00000087299
155  ENSG00000163864 NA NMNAT3 nicotinamide nucleotide adenylyltransferase 3 349565 ENSG00000163864
156  ENSG00000156467 NA UQCRB ubiquinol-cytochrome c reductase binding protein 7381 ENSG00000156467
157  ENSG00000103316 NA CRYM crystallin, mu 1428 ENSG00000103316
158  ENSG00000184076 NA UQCR10 ubiquinol-cytochrome c reductase, complex III subunit X 29796 ENSG00000184076
159  ENSG00000078070 NA MCCC1 methylcrotonoyl-CoA carboxylase 1 (alpha) 56922 ENSG00000078070
160  ENSG00000115884 NA SDC1 syndecan 1 6382 ENSG00000115884
161  ENSG00000154723 NA ATP5J ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 522 ENSG00000154723
162  ENSG00000167969 NA ECI1 enoyl-CoA delta isomerase 1 1632 ENSG00000167969
163  ENSG00000105552 NA BCAT2 branched chain amino-acid transaminase 2, mitochondrial 587 ENSG00000105552
164  ENSG00000006606 NA CCL26 chemokine (C-C motif) ligand 26 10344 ENSG00000006606
165  ENSG00000139531 NA SUOX sulfite oxidase 6821 ENSG00000139531
166  ENSG00000125166 NA GOT2 glutamic-oxaloacetic transaminase 2, mitochondrial (aspartate aminotransferase 2) 2806 ENSG00000125166
167  ENSG00000140374 NA ETFA electron-transfer-flavoprotein, alpha polypeptide 2108 ENSG00000140374
168  ENSG00000140740 NA UQCRC2 ubiquinol-cytochrome c reductase core protein II 7385 ENSG00000140740
169  ENSG00000114378 NA HYAL1 hyaluronoglucosaminidase 1 3373 ENSG00000114378
170  ENSG00000160194 NA NDUFV3 NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa 4731 ENSG00000160194
171  ENSG00000147684 NA NDUFB9 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa 4715 ENSG00000147684
172  ENSG00000184983 NA NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa 4700 ENSG00000184983
173  ENSG00000158864 NA NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) 4720 ENSG00000158864
174  ENSG00000079691 NA LRRC16A leucine rich repeat containing 16A 55604 ENSG00000079691
175  ENSG00000155749 NA ALS2CR12 amyotrophic lateral sclerosis 2 (juvenile) chromosome region, candidate 12 130540 ENSG00000155749
176  ENSG00000142168 NA SOD1 superoxide dismutase 1, soluble 6647 ENSG00000142168
177  ENSG00000000419 NA DPM1 dolichyl-phosphate mannosyltransferase polypeptide 1, catalytic subunit 8813 ENSG00000000419
178  ENSG00000181929 NA PRKAG1 protein kinase, AMP-activated, gamma 1 non-catalytic subunit 5571 ENSG00000181929
179  ENSG00000076043 NA REXO2 REX2, RNA exonuclease 2 homolog (S. cerevisiae) 25996 ENSG00000076043
180  ENSG00000120254 NA MTHFD1L methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 1-like 25902 ENSG00000120254
181  ENSG00000147813 NA NAPRT1 nicotinate phosphoribosyltransferase domain containing 1 93100 ENSG00000147813
182  ENSG00000119689 NA DLST dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex) 1743 ENSG00000119689
183  ENSG00000168291 NA PDHB pyruvate dehydrogenase (lipoamide) beta 5162 ENSG00000168291
184  ENSG00000156049 NA GNA14 guanine nucleotide binding protein (G protein), alpha 14 9630 ENSG00000156049
185  ENSG00000116459 NA ATP5F1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 515 ENSG00000116459
186  ENSG00000105499 NA PLA2G4C phospholipase A2, group IVC (cytosolic, calcium-independent) 8605 ENSG00000105499
187  ENSG00000119328 NA FAM206A family with sequence similarity 206, member A 54942 ENSG00000119328
188  ENSG00000112992 NA NNT nicotinamide nucleotide transhydrogenase 23530 ENSG00000112992
189  ENSG00000067704 NA IARS2 isoleucyl-tRNA synthetase 2, mitochondrial 55699 ENSG00000067704
190  ENSG00000130348 NA QRSL1 glutaminyl-tRNA synthase (glutamine-hydrolyzing)-like 1 55278 ENSG00000130348
191  ENSG00000087250 NA MT3 metallothionein 3 4504 ENSG00000087250
192  ENSG00000170502 NA NUDT9 nudix (nucleoside diphosphate linked moiety X)-type motif 9 53343 ENSG00000170502
193  ENSG00000119421 NA NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa 4702 ENSG00000119421
194  ENSG00000244005 NA NFS1 NFS1 nitrogen fixation 1 homolog (S. cerevisiae) 9054 ENSG00000244005
195  ENSG00000104879 NA CKM creatine kinase, muscle 1158 ENSG00000104879
196  ENSG00000126267 NA COX6B1 cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) 1340 ENSG00000126267
197  ENSG00000121769 NA FABP3 fatty acid binding protein 3, muscle and heart (mammary-derived growth inhibitor) 2170 ENSG00000121769
198  ENSG00000100804 NA PSMB5 proteasome (prosome, macropain) subunit, beta type, 5 5693 ENSG00000100804
199  ENSG00000145494 NA NDUFS6 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) 4726 ENSG00000145494
200  ENSG00000072506 NA HSD17B10 hydroxysteroid (17-beta) dehydrogenase 10 3028 ENSG00000072506
201  ENSG00000131143 NA COX4I1 cytochrome c oxidase subunit IV isoform 1 1327 ENSG00000131143
202  ENSG00000142546 NA NOSIP nitric oxide synthase interacting protein 51070 ENSG00000142546
203  ENSG00000105379 NA ETFB electron-transfer-flavoprotein, beta polypeptide 2109 ENSG00000105379
204  ENSG00000108515 NA ENO3 enolase 3 (beta, muscle) 2027 ENSG00000108515
205  ENSG00000090266 NA NDUFB2 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa 4708 ENSG00000090266
206  ENSG00000105649 NA RAB3A RAB3A, member RAS oncogene family 5864 ENSG00000105649
207  ENSG00000047249 NA ATP6V1H ATPase, H+ transporting, lysosomal 50/57kDa, V1 subunit H 51606 ENSG00000047249
208  ENSG00000151498 NA ACAD8 acyl-CoA dehydrogenase family, member 8 27034 ENSG00000151498
209  ENSG00000136143 NA SUCLA2 succinate-CoA ligase, ADP-forming, beta subunit 8803 ENSG00000136143
210  ENSG00000003137 NA CYP26B1 cytochrome P450, family 26, subfamily B, polypeptide 1 56603 ENSG00000003137
211  ENSG00000159199 NA ATP5G1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) 516 ENSG00000159199
212  ENSG00000173614 NA NMNAT1 nicotinamide nucleotide adenylyltransferase 1 64802 ENSG00000173614
213  ENSG00000082146 NA STRADB STE20-related kinase adaptor beta 55437 ENSG00000082146
214  ENSG00000116171 NA SCP2 sterol carrier protein 2 6342 ENSG00000116171
215  ENSG00000129084 NA PSMA1 proteasome (prosome, macropain) subunit, alpha type, 1 5682 ENSG00000256206 ENSG00000129084
216  ENSG00000143374 NA TARS2 threonyl-tRNA synthetase 2, mitochondrial (putative) 80222 ENSG00000143374
217  ENSG00000013275 NA PSMC4 proteasome (prosome, macropain) 26S subunit, ATPase, 4 5704 ENSG00000013275
218  ENSG00000117118 NA SDHB succinate dehydrogenase complex, subunit B, iron sulfur (Ip) 6390 ENSG00000117118
219  ENSG00000087460 NA GNAS GNAS complex locus 2778 ENSG00000087460
220  ENSG00000066926 NA FECH ferrochelatase 2235 ENSG00000066926
221  ENSG00000168827 NA GFM1 G elongation factor, mitochondrial 1 85476 ENSG00000168827
222  ENSG00000115944 NA COX7A2L cytochrome c oxidase subunit VIIa polypeptide 2 like 9167 ENSG00000115944
223  ENSG00000166228 NA PCBD1 pterin-4 alpha-carbinolamine dehydratase/dimerization cofactor of hepatocyte nuclear factor 1 alpha 5092 ENSG00000166228
224  ENSG00000100294 NA MCAT malonyl CoA:ACP acyltransferase (mitochondrial) 27349 ENSG00000100294
225  ENSG00000112667 NA C6orf108 chromosome 6 open reading frame 108 10591 ENSG00000112667
226  ENSG00000164022 NA AIMP1 aminoacyl tRNA synthetase complex-interacting multifunctional protein 1 9255 ENSG00000164022
227  ENSG00000152234 NA ATP5A1 ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle 498 ENSG00000152234
228  ENSG00000146729 NA GBAS glioblastoma amplified sequence 2631 ENSG00000146729
229  ENSG00000164494 NA PDSS2 prenyl (decaprenyl) diphosphate synthase, subunit 2 57107 ENSG00000164494
230  ENSG00000132763 NA MMACHC methylmalonic aciduria (cobalamin deficiency) cblC type, with homocystinuria 25974 ENSG00000132763
231  ENSG00000151366 NA NDUFC2 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa 4718 ENSG00000151366
232  ENSG00000128609 NA NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa 4698 ENSG00000128609
233  ENSG00000178802 NA MPI mannose phosphate isomerase 4351 ENSG00000178802
234  ENSG00000163541 NA SUCLG1 succinate-CoA ligase, alpha subunit 8802 ENSG00000163541
235  ENSG00000146701 NA MDH2 malate dehydrogenase 2, NAD (mitochondrial) 4191 ENSG00000146701
236  ENSG00000131730 NA CKMT2 creatine kinase, mitochondrial 2 (sarcomeric) 1160 ENSG00000131730
237  ENSG00000147123 NA NDUFB11 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa 54539 ENSG00000147123
238  ENSG00000137714 NA FDX1 ferredoxin 1 2230 ENSG00000137714
239  ENSG00000169021 NA UQCRFS1 ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 7386 ENSG00000169021
240  ENSG00000115652 NA UXS1 UDP-glucuronate decarboxylase 1 80146 ENSG00000115652
241  ENSG00000145439 NA CBR4 carbonyl reductase 4 84869 ENSG00000145439
242  ENSG00000157881 NA PANK4 pantothenate kinase 4 55229 ENSG00000157881
243  ENSG00000170231 NA FABP6 fatty acid binding protein 6, ileal 2172 ENSG00000170231
244  ENSG00000197943 NA PLCG2 phospholipase C, gamma 2 (phosphatidylinositol-specific) 5336 ENSG00000197943
245  ENSG00000062485 NA CS citrate synthase 1431 ENSG00000062485
246  ENSG00000122691 NA TWIST1 twist homolog 1 (Drosophila) 7291 ENSG00000122691
247  ENSG00000120053 NA GOT1 glutamic-oxaloacetic transaminase 1, soluble (aspartate aminotransferase 1) 2805 ENSG00000120053
248  ENSG00000189283 NA FHIT fragile histidine triad 2272 ENSG00000189283
249  ENSG00000174021 NA GNG5 guanine nucleotide binding protein (G protein), gamma 5 2787 ENSG00000174021
250  ENSG00000139428 NA MMAB methylmalonic aciduria (cobalamin deficiency) cblB type 326625 ENSG00000139428
251  ENSG00000185973 NA TMLHE trimethyllysine hydroxylase, epsilon 55217 ENSG00000185973
252  ENSG00000196562 NA SULF2 sulfatase 2 55959 ENSG00000196562
253  ENSG00000137513 NA NARS2 asparaginyl-tRNA synthetase 2, mitochondrial (putative) 79731 ENSG00000137513
254  ENSG00000124370 NA MCEE methylmalonyl CoA epimerase 84693 ENSG00000124370
255  ENSG00000164405 NA UQCRQ ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa 27089 ENSG00000164405
256  ENSG00000136930 NA PSMB7 proteasome (prosome, macropain) subunit, beta type, 7 5695 ENSG00000136930
257  ENSG00000122729 NA ACO1 aconitase 1, soluble 48 ENSG00000122729
258  ENSG00000173085 NA COQ2 coenzyme Q2 homolog, prenyltransferase (yeast) 27235 ENSG00000173085
259  ENSG00000124767 NA GLO1 glyoxalase I 2739 ENSG00000124767
260  ENSG00000124172 NA ATP5E ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit 514 ENSG00000124172
261  ENSG00000183648 NA NDUFB1 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa 4707 ENSG00000183648
262  ENSG00000110435 NA PDHX pyruvate dehydrogenase complex, component X 8050 ENSG00000110435
263  ENSG00000099624 NA ATP5D ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit 513 ENSG00000099624
264  ENSG00000100412 NA ACO2 aconitase 2, mitochondrial 50 ENSG00000100412
265  ENSG00000125356 NA NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa 4694 ENSG00000125356
266  ENSG00000108528 NA SLC25A11 solute carrier family 25 (mitochondrial carrier; oxoglutarate carrier), member 11 8402 ENSG00000108528
267  ENSG00000119673 NA ACOT2 acyl-CoA thioesterase 2 10965 ENSG00000119673
268  ENSG00000163636 NA PSMD6 proteasome (prosome, macropain) 26S subunit, non-ATPase, 6 9861 ENSG00000163636
269  ENSG00000137574 NA TGS1 trimethylguanosine synthase 1 96764 ENSG00000137574
270  ENSG00000099795 NA NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa 4713 ENSG00000099795
271  ENSG00000153574 NA RPIA ribose 5-phosphate isomerase A 22934 ENSG00000153574
272  ENSG00000103507 NA BCKDK branched chain ketoacid dehydrogenase kinase 10295 ENSG00000103507
273  ENSG00000148090 NA AUH AU RNA binding protein/enoyl-CoA hydratase 549 ENSG00000148090
274  ENSG00000090013 NA BLVRB biliverdin reductase B (flavin reductase (NADPH)) 645 ENSG00000090013
275  ENSG00000172270 NA BSG basigin (Ok blood group) 682 ENSG00000172270
276  ENSG00000250479 NA CHCHD10 coiled-coil-helix-coiled-coil-helix domain containing 10 400916 ENSG00000250479
277  ENSG00000111817 NA DSE dermatan sulfate epimerase 29940 ENSG00000111817
278  ENSG00000060971 NA ACAA1 acetyl-CoA acyltransferase 1 30 ENSG00000060971
279  ENSG00000150867 NA PIP4K2A phosphatidylinositol-5-phosphate 4-kinase, type II, alpha 5305 ENSG00000150867
280  ENSG00000164347 NA GFM2 G elongation factor, mitochondrial 2 84340 ENSG00000164347
281  ENSG00000119723 NA COQ6 coenzyme Q6 homolog, monooxygenase (S. cerevisiae) 51004 ENSG00000119723
282  ENSG00000197894 NA ADH5 alcohol dehydrogenase 5 (class III), chi polypeptide 128 ENSG00000197894
283  ENSG00000112357 NA PEX7 peroxisomal biogenesis factor 7 5191 ENSG00000112357
284  ENSG00000197448 NA GSTK1 glutathione S-transferase kappa 1 373156 ENSG00000197448
285  ENSG00000167792 NA NDUFV1 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa 4723 ENSG00000167792
286  ENSG00000117594 NA HSD11B1 hydroxysteroid (11-beta) dehydrogenase 1 3290 ENSG00000117594
287  ENSG00000110717 NA NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) 4728 ENSG00000110717
288  ENSG00000165609 NA NUDT5 nudix (nucleoside diphosphate linked moiety X)-type motif 5 11164 ENSG00000165609
289  ENSG00000197535 NA MYO5A myosin VA (heavy chain 12, myoxin) 4644 ENSG00000197535
290  ENSG00000150594 NA ADRA2A adrenoceptor alpha 2A 150 ENSG00000150594
291  ENSG00000091164 NA TXNL1 thioredoxin-like 1 9352 ENSG00000091164
292  ENSG00000198467 NA TPM2 tropomyosin 2 (beta) 7169 ENSG00000198467
293  ENSG00000159377 NA PSMB4 proteasome (prosome, macropain) subunit, beta type, 4 5692 ENSG00000159377
294  ENSG00000127884 NA ECHS1 enoyl CoA hydratase, short chain, 1, mitochondrial 1892 ENSG00000127884
295  ENSG00000241468 NA ATP5J2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 9551 ENSG00000241468
296  ENSG00000213420 NA GPC2 glypican 2 221914 ENSG00000213420
297  ENSG00000176340 NA COX8A cytochrome c oxidase subunit VIIIA (ubiquitous) 1351 ENSG00000176340
298  ENSG00000170266 NA GLB1 galactosidase, beta 1 2720 ENSG00000170266
299  ENSG00000101365 NA IDH3B isocitrate dehydrogenase 3 (NAD+) beta 3420 ENSG00000101365
300  ENSG00000173409 NA ARV1 ARV1 homolog (S. cerevisiae) 64801 ENSG00000173409
301  ENSG00000241837 NA ATP5O ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit 539 ENSG00000241837
302  ENSG00000140905 NA GCSH glycine cleavage system protein H (aminomethyl carrier) 2653 ENSG00000140905


Database:molecular function       Name:oxidoreductase activity       ID:GO:0016491
C=711; O=144; E=42.80; R=3.36; rawP=2.98e-40; adjP=1.75e-37
Index UserID Value Gene Symbol Gene Name EntrezGene Ensembl
1  ENSG00000087299 NA L2HGDH L-2-hydroxyglutarate dehydrogenase 79944 ENSG00000087299
2  ENSG00000187630 NA DHRS4L2 dehydrogenase/reductase (SDR family) member 4 like 2 317749 ENSG00000187630
3  ENSG00000165264 NA NDUFB6 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa 4712 ENSG00000165264
4  ENSG00000103316 NA CRYM crystallin, mu 1428 ENSG00000103316
5  ENSG00000156467 NA UQCRB ubiquinol-cytochrome c reductase binding protein 7381 ENSG00000156467
6  ENSG00000184076 NA UQCR10 ubiquinol-cytochrome c reductase, complex III subunit X 29796 ENSG00000184076
7  ENSG00000161281 NA COX7A1 cytochrome c oxidase subunit VIIa polypeptide 1 (muscle) 1346 ENSG00000161281
8  ENSG00000148672 NA GLUD1 glutamate dehydrogenase 1 2746 ENSG00000148672
9  ENSG00000156885 NA COX6A2 cytochrome c oxidase subunit VIa polypeptide 2 1339 ENSG00000156885
10  ENSG00000006695 NA COX10 COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) 1352 ENSG00000006695
11  ENSG00000169084 NA DHRSX dehydrogenase/reductase (SDR family) X-linked 207063 ENSG00000169084
12  ENSG00000116288 NA PARK7 parkinson protein 7 11315 ENSG00000116288
13  ENSG00000128203 NA ASPHD2 aspartate beta-hydroxylase domain containing 2 57168 ENSG00000128203
14  ENSG00000239264 NA TXNDC5 thioredoxin domain containing 5 (endoplasmic reticulum) 81567 ENSG00000239264
15  ENSG00000139531 NA SUOX sulfite oxidase 6821 ENSG00000139531
16  ENSG00000166136 NA NDUFB8 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa 4714 ENSG00000166136
17  ENSG00000140374 NA ETFA electron-transfer-flavoprotein, alpha polypeptide 2108 ENSG00000140374
18  ENSG00000116353 NA MECR mitochondrial trans-2-enoyl-CoA reductase 51102 ENSG00000116353
19  ENSG00000147684 NA NDUFB9 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa 4715 ENSG00000147684
20  ENSG00000160194 NA NDUFV3 NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa 4731 ENSG00000160194
21  ENSG00000184983 NA NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa 4700 ENSG00000184983
22  ENSG00000130414 NA NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa 4705 ENSG00000130414
23  ENSG00000091140 NA DLD dihydrolipoamide dehydrogenase 1738 ENSG00000091140
24  ENSG00000165060 NA FXN frataxin 2395 ENSG00000165060
25  ENSG00000158864 NA NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) 4720 ENSG00000158864
26  ENSG00000131828 NA PDHA1 pyruvate dehydrogenase (lipoamide) alpha 1 5160 ENSG00000131828
27  ENSG00000122971 NA ACADS acyl-CoA dehydrogenase, C-2 to C-3 short chain 35 ENSG00000122971
28  ENSG00000142168 NA SOD1 superoxide dismutase 1, soluble 6647 ENSG00000142168
29  ENSG00000109390 NA NDUFC1 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa 4717 ENSG00000109390
30  ENSG00000182512 NA GLRX5 glutaredoxin 5 51218 ENSG00000182512
31  ENSG00000203797 NA DDO D-aspartate oxidase 8528 ENSG00000203797
32  ENSG00000103160 NA HSDL1 hydroxysteroid dehydrogenase like 1 83693 ENSG00000103160
33  ENSG00000120254 NA MTHFD1L methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 1-like 25902 ENSG00000120254
34  ENSG00000110074 NA FOXRED1 FAD-dependent oxidoreductase domain containing 1 55572 ENSG00000110074
35  ENSG00000168291 NA PDHB pyruvate dehydrogenase (lipoamide) beta 5162 ENSG00000168291
36  ENSG00000148334 NA PTGES2 prostaglandin E synthase 2 80142 ENSG00000148334
37  ENSG00000119537 NA KDSR 3-ketodihydrosphingosine reductase 2531 ENSG00000119537
38  ENSG00000112992 NA NNT nicotinamide nucleotide transhydrogenase 23530 ENSG00000112992
39  ENSG00000126432 NA PRDX5 peroxiredoxin 5 25824 ENSG00000126432
40  ENSG00000178741 NA COX5A cytochrome c oxidase subunit Va 9377 ENSG00000178741
41  ENSG00000213619 NA NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) 4722 ENSG00000213619
42  ENSG00000173660 NA UQCRH ubiquinol-cytochrome c reductase hinge protein 7388 ENSG00000173660
43  ENSG00000119421 NA NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa 4702 ENSG00000119421
44  ENSG00000100348 NA TXN2 thioredoxin 2 25828 ENSG00000100348
45  ENSG00000130347 NA RTN4IP1 reticulon 4 interacting protein 1 84816 ENSG00000130347
46  ENSG00000126267 NA COX6B1 cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) 1340 ENSG00000126267
47  ENSG00000135940 NA COX5B cytochrome c oxidase subunit Vb 1329 ENSG00000135940
48  ENSG00000154814 NA OXNAD1 oxidoreductase NAD-binding domain containing 1 92106 ENSG00000154814
49  ENSG00000113790 NA EHHADH enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase 1962 ENSG00000113790
50  ENSG00000148450 NA MSRB2 methionine sulfoxide reductase B2 22921 ENSG00000148450
51  ENSG00000145494 NA NDUFS6 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) 4726 ENSG00000145494
52  ENSG00000156709 NA AIFM1 apoptosis-inducing factor, mitochondrion-associated, 1 9131 ENSG00000156709
53  ENSG00000072506 NA HSD17B10 hydroxysteroid (17-beta) dehydrogenase 10 3028 ENSG00000072506
54  ENSG00000189043 NA NDUFA4 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa 4697 ENSG00000189043
55  ENSG00000131143 NA COX4I1 cytochrome c oxidase subunit IV isoform 1 1327 ENSG00000131143
56  ENSG00000164919 NA COX6C cytochrome c oxidase subunit VIc 1345 ENSG00000164919
57  ENSG00000136444 NA RSAD1 radical S-adenosyl methionine domain containing 1 55316 ENSG00000136444
58  ENSG00000115286 NA NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) 374291 ENSG00000115286
59  ENSG00000164258 NA NDUFS4 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) 4724 ENSG00000164258
60  ENSG00000132570 NA PCBD2 pterin-4 alpha-carbinolamine dehydratase/dimerization cofactor of hepatocyte nuclear factor 1 alpha (TCF1) 2 84105 ENSG00000132570
61  ENSG00000090266 NA NDUFB2 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa 4708 ENSG00000090266
62  ENSG00000184860 NA SDR42E1 short chain dehydrogenase/reductase family 42E, member 1 93517 ENSG00000184860
63  ENSG00000127540 NA UQCR11 ubiquinol-cytochrome c reductase, complex III subunit XI 10975 ENSG00000127540
64  ENSG00000151498 NA ACAD8 acyl-CoA dehydrogenase family, member 8 27034 ENSG00000151498
65  ENSG00000184752 NA NDUFA12 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 55967 ENSG00000184752
66  ENSG00000003137 NA CYP26B1 cytochrome P450, family 26, subfamily B, polypeptide 1 56603 ENSG00000003137
67  ENSG00000204228 NA HSD17B8 hydroxysteroid (17-beta) dehydrogenase 8 7923 ENSG00000204228
68  ENSG00000067829 NA IDH3G isocitrate dehydrogenase 3 (NAD+) gamma 3421 ENSG00000067829
69  ENSG00000130159 NA ECSIT ECSIT homolog (Drosophila) 51295 ENSG00000130159
70  ENSG00000167815 NA PRDX2 peroxiredoxin 2 7001 ENSG00000167815
71  ENSG00000166816 NA LDHD lactate dehydrogenase D 197257 ENSG00000166816
72  ENSG00000140990 NA NDUFB10 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa 4716 ENSG00000140990
73  ENSG00000157326 NA DHRS4 dehydrogenase/reductase (SDR family) member 4 10901 ENSG00000157326
74  ENSG00000117118 NA SDHB succinate dehydrogenase complex, subunit B, iron sulfur (Ip) 6390 ENSG00000117118
75  ENSG00000143653 NA SCCPDH saccharopine dehydrogenase (putative) 51097 ENSG00000143653
76  ENSG00000149380 NA P4HA3 prolyl 4-hydroxylase, alpha polypeptide III 283208 ENSG00000149380
77  ENSG00000115944 NA COX7A2L cytochrome c oxidase subunit VIIa polypeptide 2 like 9167 ENSG00000115944
78  ENSG00000166228 NA PCBD1 pterin-4 alpha-carbinolamine dehydratase/dimerization cofactor of hepatocyte nuclear factor 1 alpha 5092 ENSG00000166228
79  ENSG00000148290 NA SURF1 surfeit 1 6834 ENSG00000148290
80  ENSG00000014641 NA MDH1 malate dehydrogenase 1, NAD (soluble) 4190 ENSG00000014641
81  ENSG00000072778 NA ACADVL acyl-CoA dehydrogenase, very long chain 37 ENSG00000072778
82  ENSG00000172893 NA DHCR7 7-dehydrocholesterol reductase 1717 ENSG00000172893
83  ENSG00000125652 NA ALKBH7 alkB, alkylation repair homolog 7 (E. coli) 84266 ENSG00000125652
84  ENSG00000128609 NA NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa 4698 ENSG00000128609
85  ENSG00000151366 NA NDUFC2 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa 4718 ENSG00000151366
86  ENSG00000146701 NA MDH2 malate dehydrogenase 2, NAD (mitochondrial) 4191 ENSG00000146701
87  ENSG00000136521 NA NDUFB5 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa 4711 ENSG00000136521
88  ENSG00000182054 NA IDH2 isocitrate dehydrogenase 2 (NADP+), mitochondrial 3418 ENSG00000182054
89  ENSG00000004779 NA NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa 4706 ENSG00000004779
90  ENSG00000085871 NA MGST2 microsomal glutathione S-transferase 2 4258 ENSG00000085871
91  ENSG00000073578 NA SDHA succinate dehydrogenase complex, subunit A, flavoprotein (Fp) 6389 ENSG00000073578
92  ENSG00000137714 NA FDX1 ferredoxin 1 2230 ENSG00000137714
93  ENSG00000119013 NA NDUFB3 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa 4709 ENSG00000119013
94  ENSG00000169021 NA UQCRFS1 ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 7386 ENSG00000169021
95  ENSG00000104325 NA DECR1 2,4-dienoyl CoA reductase 1, mitochondrial 1666 ENSG00000104325
96  ENSG00000145439 NA CBR4 carbonyl reductase 4 84869 ENSG00000145439
97  ENSG00000160439 NA RDH13 retinol dehydrogenase 13 (all-trans/9-cis) 112724 ENSG00000160439
98  ENSG00000185973 NA TMLHE trimethyllysine hydroxylase, epsilon 55217 ENSG00000185973
99  ENSG00000167468 NA GPX4 glutathione peroxidase 4 2879 ENSG00000167468
100  ENSG00000139180 NA NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa 4704 ENSG00000139180
101  ENSG00000111640 NA GAPDH glyceraldehyde-3-phosphate dehydrogenase 2597 ENSG00000111640
102  ENSG00000127184 NA COX7C cytochrome c oxidase subunit VIIc 1350 ENSG00000127184
103  ENSG00000164405 NA UQCRQ ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa 27089 ENSG00000164405
104  ENSG00000183648 NA NDUFB1 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa 4707 ENSG00000183648
105  ENSG00000204370 NA SDHD succinate dehydrogenase complex, subunit D, integral membrane protein 6392 ENSG00000204370
106  ENSG00000137106 NA GRHPR glyoxylate reductase/hydroxypyruvate reductase 9380 ENSG00000137106
107  ENSG00000169738 NA DCXR dicarbonyl/L-xylulose reductase 51181 ENSG00000169738
108  ENSG00000111271 NA ACAD10 acyl-CoA dehydrogenase family, member 10 80724 ENSG00000111271
109  ENSG00000160211 NA G6PD glucose-6-phosphate dehydrogenase 2539 ENSG00000160211
110  ENSG00000125356 NA NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa 4694 ENSG00000125356
111  ENSG00000100601 NA ALKBH1 alkB, alkylation repair homolog 1 (E. coli) 8846 ENSG00000100601
112  ENSG00000099795 NA NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa 4713 ENSG00000099795
113  ENSG00000023228 NA NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) 4719 ENSG00000023228
114  ENSG00000143252 NA SDHC succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa 6391 ENSG00000143252
115  ENSG00000151376 NA ME3 malic enzyme 3, NADP(+)-dependent, mitochondrial 10873 ENSG00000151376
116  ENSG00000090013 NA BLVRB biliverdin reductase B (flavin reductase (NADPH)) 645 ENSG00000090013
117  ENSG00000060971 NA ACAA1 acetyl-CoA acyltransferase 1 30 ENSG00000060971
118  ENSG00000119723 NA COQ6 coenzyme Q6 homolog, monooxygenase (S. cerevisiae) 51004 ENSG00000119723
119  ENSG00000112695 NA COX7A2 cytochrome c oxidase subunit VIIa polypeptide 2 (liver) 1347 ENSG00000112695
120  ENSG00000198736 NA MSRB1 methionine sulfoxide reductase B1 51734 ENSG00000198736
121  ENSG00000197894 NA ADH5 alcohol dehydrogenase 5 (class III), chi polypeptide 128 ENSG00000197894
122  ENSG00000197448 NA GSTK1 glutathione S-transferase kappa 1 373156 ENSG00000197448
123  ENSG00000167792 NA NDUFV1 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa 4723 ENSG00000167792
124  ENSG00000131495 NA NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa 4695 ENSG00000131495
125  ENSG00000065518 NA NDUFB4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa 4710 ENSG00000065518
126  ENSG00000117594 NA HSD11B1 hydroxysteroid (11-beta) dehydrogenase 1 3290 ENSG00000117594
127  ENSG00000110717 NA NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) 4728 ENSG00000110717
128  ENSG00000197580 NA BCO2 beta-carotene oxygenase 2 83875 ENSG00000197580
129  ENSG00000131174 NA COX7B cytochrome c oxidase subunit VIIb 1349 ENSG00000131174
130  ENSG00000170906 NA NDUFA3 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa 4696 ENSG00000170906
131  ENSG00000184719 NA RNLS renalase, FAD-dependent amine oxidase 55328 ENSG00000184719
132  ENSG00000111716 NA LDHB lactate dehydrogenase B 3945 ENSG00000111716
133  ENSG00000091164 NA TXNL1 thioredoxin-like 1 9352 ENSG00000091164
134  ENSG00000108439 NA PNPO pyridoxamine 5'-phosphate oxidase 55163 ENSG00000108439
135  ENSG00000111275 NA ALDH2 aldehyde dehydrogenase 2 family (mitochondrial) 217 ENSG00000111275
136  ENSG00000117139 NA KDM5B lysine (K)-specific demethylase 5B 10765 ENSG00000117139
137  ENSG00000010256 NA UQCRC1 ubiquinol-cytochrome c reductase core protein I 7384 ENSG00000010256
138  ENSG00000171503 NA ETFDH electron-transferring-flavoprotein dehydrogenase 2110 ENSG00000171503
139  ENSG00000138796 NA HADH hydroxyacyl-CoA dehydrogenase 3033 ENSG00000138796
140  ENSG00000165672 NA PRDX3 peroxiredoxin 3 10935 ENSG00000165672
141  ENSG00000161533 NA ACOX1 acyl-CoA oxidase 1, palmitoyl 51 ENSG00000161533
142  ENSG00000176340 NA COX8A cytochrome c oxidase subunit VIIIA (ubiquitous) 1351 ENSG00000176340
143  ENSG00000168653 NA NDUFS5 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) 4725 ENSG00000168653
144  ENSG00000101365 NA IDH3B isocitrate dehydrogenase 3 (NAD+) beta 3420 ENSG00000101365


Database:molecular function       Name:NADH dehydrogenase (ubiquinone) activity       ID:GO:0008137
C=44; O=33; E=2.65; R=12.46; rawP=1.24e-31; adjP=1.82e-29
Index UserID Value Gene Symbol Gene Name EntrezGene Ensembl
1  ENSG00000151366 NA NDUFC2 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa 4718 ENSG00000151366
2  ENSG00000128609 NA NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa 4698 ENSG00000128609
3  ENSG00000023228 NA NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) 4719 ENSG00000023228
4  ENSG00000165264 NA NDUFB6 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa 4712 ENSG00000165264
5  ENSG00000145494 NA NDUFS6 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) 4726 ENSG00000145494
6  ENSG00000136521 NA NDUFB5 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa 4711 ENSG00000136521
7  ENSG00000004779 NA NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa 4706 ENSG00000004779
8  ENSG00000189043 NA NDUFA4 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa 4697 ENSG00000189043
9  ENSG00000115286 NA NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) 374291 ENSG00000115286
10  ENSG00000164258 NA NDUFS4 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) 4724 ENSG00000164258
11  ENSG00000119013 NA NDUFB3 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa 4709 ENSG00000119013
12  ENSG00000167792 NA NDUFV1 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa 4723 ENSG00000167792
13  ENSG00000131495 NA NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa 4695 ENSG00000131495
14  ENSG00000065518 NA NDUFB4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa 4710 ENSG00000065518
15  ENSG00000090266 NA NDUFB2 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa 4708 ENSG00000090266
16  ENSG00000166136 NA NDUFB8 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa 4714 ENSG00000166136
17  ENSG00000110717 NA NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) 4728 ENSG00000110717
18  ENSG00000147684 NA NDUFB9 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa 4715 ENSG00000147684
19  ENSG00000160194 NA NDUFV3 NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa 4731 ENSG00000160194
20  ENSG00000184983 NA NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa 4700 ENSG00000184983
21  ENSG00000170906 NA NDUFA3 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa 4696 ENSG00000170906
22  ENSG00000184752 NA NDUFA12 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 55967 ENSG00000184752
23  ENSG00000130414 NA NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa 4705 ENSG00000130414
24  ENSG00000158864 NA NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) 4720 ENSG00000158864
25  ENSG00000139180 NA NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa 4704 ENSG00000139180
26  ENSG00000109390 NA NDUFC1 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa 4717 ENSG00000109390
27  ENSG00000183648 NA NDUFB1 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa 4707 ENSG00000183648
28  ENSG00000140990 NA NDUFB10 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa 4716 ENSG00000140990
29  ENSG00000125356 NA NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa 4694 ENSG00000125356
30  ENSG00000213619 NA NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) 4722 ENSG00000213619
31  ENSG00000168653 NA NDUFS5 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) 4725 ENSG00000168653
32  ENSG00000119421 NA NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa 4702 ENSG00000119421
33  ENSG00000099795 NA NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa 4713 ENSG00000099795


Database:molecular function       Name:NADH dehydrogenase activity       ID:GO:0003954
C=44; O=33; E=2.65; R=12.46; rawP=1.24e-31; adjP=1.82e-29
Index UserID Value Gene Symbol Gene Name EntrezGene Ensembl
1  ENSG00000151366 NA NDUFC2 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa 4718 ENSG00000151366
2  ENSG00000128609 NA NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa 4698 ENSG00000128609
3  ENSG00000023228 NA NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) 4719 ENSG00000023228
4  ENSG00000165264 NA NDUFB6 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa 4712 ENSG00000165264
5  ENSG00000145494 NA NDUFS6 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) 4726 ENSG00000145494
6  ENSG00000136521 NA NDUFB5 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa 4711 ENSG00000136521
7  ENSG00000004779 NA NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa 4706 ENSG00000004779
8  ENSG00000189043 NA NDUFA4 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa 4697 ENSG00000189043
9  ENSG00000115286 NA NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) 374291 ENSG00000115286
10  ENSG00000164258 NA NDUFS4 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) 4724 ENSG00000164258
11  ENSG00000119013 NA NDUFB3 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa 4709 ENSG00000119013
12  ENSG00000167792 NA NDUFV1 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa 4723 ENSG00000167792
13  ENSG00000131495 NA NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa 4695 ENSG00000131495
14  ENSG00000065518 NA NDUFB4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa 4710 ENSG00000065518
15  ENSG00000090266 NA NDUFB2 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa 4708 ENSG00000090266
16  ENSG00000166136 NA NDUFB8 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa 4714 ENSG00000166136
17  ENSG00000110717 NA NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) 4728 ENSG00000110717
18  ENSG00000147684 NA NDUFB9 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa 4715 ENSG00000147684
19  ENSG00000160194 NA NDUFV3 NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa 4731 ENSG00000160194
20  ENSG00000184983 NA NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa 4700 ENSG00000184983
21  ENSG00000170906 NA NDUFA3 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa 4696 ENSG00000170906
22  ENSG00000184752 NA NDUFA12 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 55967 ENSG00000184752
23  ENSG00000130414 NA NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa 4705 ENSG00000130414
24  ENSG00000158864 NA NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) 4720 ENSG00000158864
25  ENSG00000139180 NA NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa 4704 ENSG00000139180
26  ENSG00000109390 NA NDUFC1 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa 4717 ENSG00000109390
27  ENSG00000183648 NA NDUFB1 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa 4707 ENSG00000183648
28  ENSG00000140990 NA NDUFB10 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa 4716 ENSG00000140990
29  ENSG00000125356 NA NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa 4694 ENSG00000125356
30  ENSG00000213619 NA NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) 4722 ENSG00000213619
31  ENSG00000168653 NA NDUFS5 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) 4725 ENSG00000168653
32  ENSG00000119421 NA NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa 4702 ENSG00000119421
33  ENSG00000099795 NA NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa 4713 ENSG00000099795


Database:molecular function       Name:NADH dehydrogenase (quinone) activity       ID:GO:0050136
C=44; O=33; E=2.65; R=12.46; rawP=1.24e-31; adjP=1.82e-29
Index UserID Value Gene Symbol Gene Name EntrezGene Ensembl
1  ENSG00000151366 NA NDUFC2 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa 4718 ENSG00000151366
2  ENSG00000128609 NA NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa 4698 ENSG00000128609
3  ENSG00000023228 NA NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) 4719 ENSG00000023228
4  ENSG00000165264 NA NDUFB6 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa 4712 ENSG00000165264
5  ENSG00000145494 NA NDUFS6 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) 4726 ENSG00000145494
6  ENSG00000136521 NA NDUFB5 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa 4711 ENSG00000136521
7  ENSG00000004779 NA NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa 4706 ENSG00000004779
8  ENSG00000189043 NA NDUFA4 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa 4697 ENSG00000189043
9  ENSG00000115286 NA NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) 374291 ENSG00000115286
10  ENSG00000164258 NA NDUFS4 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) 4724 ENSG00000164258
11  ENSG00000119013 NA NDUFB3 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa 4709 ENSG00000119013
12  ENSG00000167792 NA NDUFV1 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa 4723 ENSG00000167792
13  ENSG00000131495 NA NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa 4695 ENSG00000131495
14  ENSG00000065518 NA NDUFB4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa 4710 ENSG00000065518
15  ENSG00000090266 NA NDUFB2 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa 4708 ENSG00000090266
16  ENSG00000166136 NA NDUFB8 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa 4714 ENSG00000166136
17  ENSG00000110717 NA NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) 4728 ENSG00000110717
18  ENSG00000147684 NA NDUFB9 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa 4715 ENSG00000147684
19  ENSG00000160194 NA NDUFV3 NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa 4731 ENSG00000160194
20  ENSG00000184983 NA NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa 4700 ENSG00000184983
21  ENSG00000170906 NA NDUFA3 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa 4696 ENSG00000170906
22  ENSG00000184752 NA NDUFA12 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 55967 ENSG00000184752
23  ENSG00000130414 NA NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa 4705 ENSG00000130414
24  ENSG00000158864 NA NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) 4720 ENSG00000158864
25  ENSG00000139180 NA NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa 4704 ENSG00000139180
26  ENSG00000109390 NA NDUFC1 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa 4717 ENSG00000109390
27  ENSG00000183648 NA NDUFB1 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa 4707 ENSG00000183648
28  ENSG00000140990 NA NDUFB10 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa 4716 ENSG00000140990
29  ENSG00000125356 NA NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa 4694 ENSG00000125356
30  ENSG00000213619 NA NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) 4722 ENSG00000213619
31  ENSG00000168653 NA NDUFS5 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) 4725 ENSG00000168653
32  ENSG00000119421 NA NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa 4702 ENSG00000119421
33  ENSG00000099795 NA NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa 4713 ENSG00000099795


Database:molecular function       Name:oxidoreductase activity, acting on NADH or NADPH, quinone or similar compound as acceptor       ID:GO:0016655
C=58; O=36; E=3.49; R=10.31; rawP=9.45e-30; adjP=1.11e-27
Index UserID Value Gene Symbol Gene Name EntrezGene Ensembl
1  ENSG00000151366 NA NDUFC2 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa 4718 ENSG00000151366
2  ENSG00000128609 NA NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa 4698 ENSG00000128609
3  ENSG00000023228 NA NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) 4719 ENSG00000023228
4  ENSG00000165264 NA NDUFB6 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa 4712 ENSG00000165264
5  ENSG00000145494 NA NDUFS6 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) 4726 ENSG00000145494
6  ENSG00000136521 NA NDUFB5 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa 4711 ENSG00000136521
7  ENSG00000004779 NA NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa 4706 ENSG00000004779
8  ENSG00000189043 NA NDUFA4 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa 4697 ENSG00000189043
9  ENSG00000115286 NA NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) 374291 ENSG00000115286
10  ENSG00000164258 NA NDUFS4 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) 4724 ENSG00000164258
11  ENSG00000119013 NA NDUFB3 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa 4709 ENSG00000119013
12  ENSG00000167792 NA NDUFV1 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa 4723 ENSG00000167792
13  ENSG00000131495 NA NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa 4695 ENSG00000131495
14  ENSG00000065518 NA NDUFB4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa 4710 ENSG00000065518
15  ENSG00000145439 NA CBR4 carbonyl reductase 4 84869 ENSG00000145439
16  ENSG00000090266 NA NDUFB2 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa 4708 ENSG00000090266
17  ENSG00000166136 NA NDUFB8 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa 4714 ENSG00000166136
18  ENSG00000110717 NA NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) 4728 ENSG00000110717
19  ENSG00000147684 NA NDUFB9 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa 4715 ENSG00000147684
20  ENSG00000160194 NA NDUFV3 NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa 4731 ENSG00000160194
21  ENSG00000184983 NA NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa 4700 ENSG00000184983
22  ENSG00000170906 NA NDUFA3 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa 4696 ENSG00000170906
23  ENSG00000184752 NA NDUFA12 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 55967 ENSG00000184752
24  ENSG00000130414 NA NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa 4705 ENSG00000130414
25  ENSG00000158864 NA NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) 4720 ENSG00000158864
26  ENSG00000139180 NA NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa 4704 ENSG00000139180
27  ENSG00000109390 NA NDUFC1 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa 4717 ENSG00000109390
28  ENSG00000183648 NA NDUFB1 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa 4707 ENSG00000183648
29  ENSG00000157326 NA DHRS4 dehydrogenase/reductase (SDR family) member 4 10901 ENSG00000157326
30  ENSG00000140990 NA NDUFB10 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa 4716 ENSG00000140990
31  ENSG00000169738 NA DCXR dicarbonyl/L-xylulose reductase 51181 ENSG00000169738
32  ENSG00000125356 NA NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa 4694 ENSG00000125356
33  ENSG00000213619 NA NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) 4722 ENSG00000213619
34  ENSG00000168653 NA NDUFS5 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) 4725 ENSG00000168653
35  ENSG00000099795 NA NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa 4713 ENSG00000099795
36  ENSG00000119421 NA NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa 4702 ENSG00000119421


Database:molecular function       Name:catalytic activity       ID:GO:0003824
C=5371; O=478; E=323.30; R=1.48; rawP=3.58e-27; adjP=3.50e-25
Index UserID Value Gene Symbol Gene Name EntrezGene Ensembl
1  ENSG00000070501 NA POLB polymerase (DNA directed), beta 5423 ENSG00000070501
2  ENSG00000187630 NA DHRS4L2 dehydrogenase/reductase (SDR family) member 4 like 2 317749 ENSG00000187630
3  ENSG00000038295 NA TLL1 tolloid-like 1 7092 ENSG00000038295
4  ENSG00000168803 NA ADAL adenosine deaminase-like 161823 ENSG00000168803
5  ENSG00000165264 NA NDUFB6 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa 4712 ENSG00000165264
6  ENSG00000161281 NA COX7A1 cytochrome c oxidase subunit VIIa polypeptide 1 (muscle) 1346 ENSG00000161281
7  ENSG00000167862 NA ICT1 immature colon carcinoma transcript 1 3396 ENSG00000167862
8  ENSG00000067596 NA DHX8 DEAH (Asp-Glu-Ala-His) box polypeptide 8 1659 ENSG00000067596
9  ENSG00000148672 NA GLUD1 glutamate dehydrogenase 1 2746 ENSG00000148672
10  ENSG00000147592 NA LACTB2 lactamase, beta 2 51110 ENSG00000147592
11  ENSG00000164172 NA MOCS2 molybdenum cofactor synthesis 2 4338 ENSG00000164172
12  ENSG00000116288 NA PARK7 parkinson protein 7 11315 ENSG00000116288
13  ENSG00000128203 NA ASPHD2 aspartate beta-hydroxylase domain containing 2 57168 ENSG00000128203
14  ENSG00000239264 NA TXNDC5 thioredoxin domain containing 5 (endoplasmic reticulum) 81567 ENSG00000239264
15  ENSG00000134109 NA EDEM1 ER degradation enhancer, mannosidase alpha-like 1 9695 ENSG00000134109
16  ENSG00000166136 NA NDUFB8 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa 4714 ENSG00000166136
17  ENSG00000116353 NA MECR mitochondrial trans-2-enoyl-CoA reductase 51102 ENSG00000116353
18  ENSG00000003509 NA C2orf56 chromosome 2 open reading frame 56 55471 ENSG00000003509
19  ENSG00000172340 NA SUCLG2 succinate-CoA ligase, GDP-forming, beta subunit 8801 ENSG00000172340
20  ENSG00000151093 NA OXSM 3-oxoacyl-ACP synthase, mitochondrial 54995 ENSG00000151093
21  ENSG00000130414 NA NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa 4705 ENSG00000130414
22  ENSG00000091140 NA DLD dihydrolipoamide dehydrogenase 1738 ENSG00000091140
23  ENSG00000165060 NA FXN frataxin 2395 ENSG00000165060
24  ENSG00000079387 NA SENP1 SUMO1/sentrin specific peptidase 1 29843 ENSG00000079387
25  ENSG00000131828 NA PDHA1 pyruvate dehydrogenase (lipoamide) alpha 1 5160 ENSG00000131828
26  ENSG00000122971 NA ACADS acyl-CoA dehydrogenase, C-2 to C-3 short chain 35 ENSG00000122971
27  ENSG00000012061 NA ERCC1 excision repair cross-complementing rodent repair deficiency, complementation group 1 (includes overlapping antisense sequence) 2067 ENSG00000012061
28  ENSG00000103356 NA EARS2 glutamyl-tRNA synthetase 2, mitochondrial (putative) 124454 ENSG00000103356
29  ENSG00000109390 NA NDUFC1 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa 4717 ENSG00000109390
30  ENSG00000182512 NA GLRX5 glutaredoxin 5 51218 ENSG00000182512
31  ENSG00000103642 NA LACTB lactamase, beta 114294 ENSG00000103642
32  ENSG00000091483 NA FH fumarate hydratase 2271 ENSG00000091483
33  ENSG00000203797 NA DDO D-aspartate oxidase 8528 ENSG00000203797
34  ENSG00000103160 NA HSDL1 hydroxysteroid dehydrogenase like 1 83693 ENSG00000103160
35  ENSG00000109586 NA GALNT7 UDP-N-acetyl-alpha-D-galactosamine:polypeptide N-acetylgalactosaminyltransferase 7 (GalNAc-T7) 51809 ENSG00000109586
36  ENSG00000110074 NA FOXRED1 FAD-dependent oxidoreductase domain containing 1 55572 ENSG00000110074
37  ENSG00000142082 NA SIRT3 sirtuin 3 23410 ENSG00000142082
38  ENSG00000127838 NA PNKD paroxysmal nonkinesigenic dyskinesia 25953 ENSG00000127838
39  ENSG00000168228 NA ZCCHC4 zinc finger, CCHC domain containing 4 29063 ENSG00000168228
40  ENSG00000148334 NA PTGES2 prostaglandin E synthase 2 80142 ENSG00000148334
41  ENSG00000119537 NA KDSR 3-ketodihydrosphingosine reductase 2531 ENSG00000119537
42  ENSG00000167112 NA TRUB2 TruB pseudouridine (psi) synthase homolog 2 (E. coli) 26995 ENSG00000167112
43  ENSG00000169189 NA NSMCE1 non-SMC element 1 homolog (S. cerevisiae) 197370 ENSG00000169189
44  ENSG00000119383 NA PPP2R4 protein phosphatase 2A activator, regulatory subunit 4 5524 ENSG00000119383
45  ENSG00000149925 NA ALDOA aldolase A, fructose-bisphosphate 226 ENSG00000149925
46  ENSG00000126432 NA PRDX5 peroxiredoxin 5 25824 ENSG00000126432
47  ENSG00000023330 NA ALAS1 aminolevulinate, delta-, synthase 1 211 ENSG00000023330
48  ENSG00000213619 NA NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) 4722 ENSG00000213619
49  ENSG00000178741 NA COX5A cytochrome c oxidase subunit Va 9377 ENSG00000178741
50  ENSG00000173660 NA UQCRH ubiquinol-cytochrome c reductase hinge protein 7388 ENSG00000173660
51  ENSG00000176490 NA DIRAS1 DIRAS family, GTP-binding RAS-like 1 148252 ENSG00000176490
52  ENSG00000105135 NA ILVBL ilvB (bacterial acetolactate synthase)-like 10994 ENSG00000105135
53  ENSG00000100348 NA TXN2 thioredoxin 2 25828 ENSG00000100348
54  ENSG00000140876 NA NUDT7 nudix (nucleoside diphosphate linked moiety X)-type motif 7 283927 ENSG00000140876
55  ENSG00000101181 NA GTPBP5 GTP binding protein 5 (putative) 26164 ENSG00000101181
56  ENSG00000135940 NA COX5B cytochrome c oxidase subunit Vb 1329 ENSG00000135940
57  ENSG00000135900 NA MRPL44 mitochondrial ribosomal protein L44 65080 ENSG00000135900
58  ENSG00000029639 NA TFB1M transcription factor B1, mitochondrial 51106 ENSG00000029639
59  ENSG00000113790 NA EHHADH enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase 1962 ENSG00000113790
60  ENSG00000162851 NA TFB2M transcription factor B2, mitochondrial 64216 ENSG00000162851
61  ENSG00000203705 NA TATDN3 TatD DNase domain containing 3 128387 ENSG00000203705
62  ENSG00000156709 NA AIFM1 apoptosis-inducing factor, mitochondrion-associated, 1 9131 ENSG00000156709
63  ENSG00000172115 NA CYCS cytochrome c, somatic 54205 ENSG00000172115
64  ENSG00000179085 NA DPM3 dolichyl-phosphate mannosyltransferase polypeptide 3 54344 ENSG00000179085
65  ENSG00000189043 NA NDUFA4 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa 4697 ENSG00000189043
66  ENSG00000123739 NA PLA2G12A phospholipase A2, group XIIA 81579 ENSG00000123739
67  ENSG00000164919 NA COX6C cytochrome c oxidase subunit VIc 1345 ENSG00000164919
68  ENSG00000185100 NA ADSSL1 adenylosuccinate synthase like 1 122622 ENSG00000185100
69  ENSG00000196465 NA MYL6B myosin, light chain 6B, alkali, smooth muscle and non-muscle 140465 ENSG00000196465
70  ENSG00000115286 NA NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) 374291 ENSG00000115286
71  ENSG00000139131 NA YARS2 tyrosyl-tRNA synthetase 2, mitochondrial 51067 ENSG00000139131
72  ENSG00000117543 NA DPH5 DPH5 homolog (S. cerevisiae) 51611 ENSG00000117543
73  ENSG00000164258 NA NDUFS4 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) 4724 ENSG00000164258
74  ENSG00000132570 NA PCBD2 pterin-4 alpha-carbinolamine dehydratase/dimerization cofactor of hepatocyte nuclear factor 1 alpha (TCF1) 2 84105 ENSG00000132570
75  ENSG00000156170 NA NDUFAF6 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 137682 ENSG00000156170
76  ENSG00000167863 NA ATP5H ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d 10476 ENSG00000167863
77  ENSG00000166165 NA CKB creatine kinase, brain 1152 ENSG00000166165
78  ENSG00000127540 NA UQCR11 ubiquinol-cytochrome c reductase, complex III subunit XI 10975 ENSG00000127540
79  ENSG00000184752 NA NDUFA12 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 55967 ENSG00000184752
80  ENSG00000132423 NA COQ3 coenzyme Q3 homolog, methyltransferase (S. cerevisiae) 51805 ENSG00000132423
81  ENSG00000148335 NA NTMT1 N-terminal Xaa-Pro-Lys N-methyltransferase 1 28989 ENSG00000148335
82  ENSG00000171861 NA RNMTL1 RNA methyltransferase like 1 55178 ENSG00000171861
83  ENSG00000131844 NA MCCC2 methylcrotonoyl-CoA carboxylase 2 (beta) 64087 ENSG00000131844
84  ENSG00000134905 NA CARS2 cysteinyl-tRNA synthetase 2, mitochondrial (putative) 79587 ENSG00000134905
85  ENSG00000006282 NA SPATA20 spermatogenesis associated 20 64847 ENSG00000006282
86  ENSG00000105819 NA PMPCB peptidase (mitochondrial processing) beta 9512 ENSG00000105819
87  ENSG00000182810 NA DDX28 DEAD (Asp-Glu-Ala-Asp) box polypeptide 28 55794 ENSG00000182810
88  ENSG00000204228 NA HSD17B8 hydroxysteroid (17-beta) dehydrogenase 8 7923 ENSG00000204228
89  ENSG00000149743 NA TRPT1 tRNA phosphotransferase 1 83707 ENSG00000149743
90  ENSG00000175198 NA PCCA propionyl CoA carboxylase, alpha polypeptide 5095 ENSG00000175198
91  ENSG00000067829 NA IDH3G isocitrate dehydrogenase 3 (NAD+) gamma 3421 ENSG00000067829
92  ENSG00000129187 NA DCTD dCMP deaminase 1635 ENSG00000129187
93  ENSG00000067225 NA PKM pyruvate kinase, muscle 5315 ENSG00000067225
94  ENSG00000140990 NA NDUFB10 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa 4716 ENSG00000140990
95  ENSG00000157326 NA DHRS4 dehydrogenase/reductase (SDR family) member 4 10901 ENSG00000157326
96  ENSG00000144182 NA LIPT1 lipoyltransferase 1 51601 ENSG00000144182
97  ENSG00000102996 NA MMP15 matrix metallopeptidase 15 (membrane-inserted) 4324 ENSG00000102996
98  ENSG00000247626 NA MARS2 methionyl-tRNA synthetase 2, mitochondrial 92935 ENSG00000247626
99  ENSG00000006530 NA AGK acylglycerol kinase 55750 ENSG00000006530
100  ENSG00000184207 NA PGP phosphoglycolate phosphatase 283871 ENSG00000184207
101  ENSG00000005075 NA POLR2J polymerase (RNA) II (DNA directed) polypeptide J, 13.3kDa 5439 ENSG00000005075
102  ENSG00000167363 NA FN3K fructosamine 3 kinase 64122 ENSG00000167363
103  ENSG00000165629 NA ATP5C1 ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 509 ENSG00000165629
104  ENSG00000143653 NA SCCPDH saccharopine dehydrogenase (putative) 51097 ENSG00000143653
105  ENSG00000116906 NA GNPAT glyceronephosphate O-acyltransferase 8443 ENSG00000116906
106  ENSG00000148290 NA SURF1 surfeit 1 6834 ENSG00000148290
107  ENSG00000198522 NA GPN1 GPN-loop GTPase 1 11321 ENSG00000198522
108  ENSG00000117266 NA CDK18 cyclin-dependent kinase 18 5129 ENSG00000117266
109  ENSG00000170634 NA ACYP2 acylphosphatase 2, muscle type 98 ENSG00000170634
110  ENSG00000014641 NA MDH1 malate dehydrogenase 1, NAD (soluble) 4190 ENSG00000014641
111  ENSG00000105220 NA GPI glucose-6-phosphate isomerase 2821 ENSG00000105220
112  ENSG00000133315 NA MACROD1 MACRO domain containing 1 28992 ENSG00000133315
113  ENSG00000072778 NA ACADVL acyl-CoA dehydrogenase, very long chain 37 ENSG00000072778
114  ENSG00000172893 NA DHCR7 7-dehydrocholesterol reductase 1717 ENSG00000172893
115  ENSG00000154930 NA ACSS1 acyl-CoA synthetase short-chain family member 1 84532 ENSG00000154930
116  ENSG00000108774 NA RAB5C RAB5C, member RAS oncogene family 5878 ENSG00000108774
117  ENSG00000125652 NA ALKBH7 alkB, alkylation repair homolog 7 (E. coli) 84266 ENSG00000125652
118  ENSG00000054148 NA PHPT1 phosphohistidine phosphatase 1 29085 ENSG00000054148
119  ENSG00000084731 NA KIF3C kinesin family member 3C 3797 ENSG00000084731
120  ENSG00000139410 NA SDSL serine dehydratase-like 113675 ENSG00000139410
121  ENSG00000059691 NA PET112 PET112 homolog (yeast) 5188 ENSG00000059691
122  ENSG00000112981 NA NME5 NME/NM23 family member 5 8382 ENSG00000112981
123  ENSG00000126088 NA UROD uroporphyrinogen decarboxylase 7389 ENSG00000126088
124  ENSG00000168060 NA NAALADL1 N-acetylated alpha-linked acidic dipeptidase-like 1 10004 ENSG00000168060
125  ENSG00000138430 NA OLA1 Obg-like ATPase 1 29789 ENSG00000138430
126  ENSG00000136521 NA NDUFB5 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa 4711 ENSG00000136521
127  ENSG00000004779 NA NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa 4706 ENSG00000004779
128  ENSG00000169020 NA ATP5I ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E 521 ENSG00000169020
129  ENSG00000182054 NA IDH2 isocitrate dehydrogenase 2 (NADP+), mitochondrial 3418 ENSG00000182054
130  ENSG00000114021 NA NIT2 nitrilase family, member 2 56954 ENSG00000114021
131  ENSG00000167272 NA POP5 processing of precursor 5, ribonuclease P/MRP subunit (S. cerevisiae) 51367 ENSG00000167272
132  ENSG00000085871 NA MGST2 microsomal glutathione S-transferase 2 4258 ENSG00000085871
133  ENSG00000004961 NA HCCS holocytochrome c synthase 3052 ENSG00000004961
134  ENSG00000172954 NA LCLAT1 lysocardiolipin acyltransferase 1 253558 ENSG00000172954
135  ENSG00000073578 NA SDHA succinate dehydrogenase complex, subunit A, flavoprotein (Fp) 6389 ENSG00000073578
136  ENSG00000119013 NA NDUFB3 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa 4709 ENSG00000119013
137  ENSG00000213965 NA NUDT19 nudix (nucleoside diphosphate linked moiety X)-type motif 19 390916 ENSG00000213965
138  ENSG00000104325 NA DECR1 2,4-dienoyl CoA reductase 1, mitochondrial 1666 ENSG00000104325
139  ENSG00000259494 NA MRPL46 mitochondrial ribosomal protein L46 26589 ENSG00000259494
140  ENSG00000077348 NA EXOSC5 exosome component 5 56915 ENSG00000077348
141  ENSG00000144827 NA ABHD10 abhydrolase domain containing 10 55347 ENSG00000144827
142  ENSG00000006757 NA PNPLA4 patatin-like phospholipase domain containing 4 8228 ENSG00000006757
143  ENSG00000072401 NA UBE2D1 ubiquitin-conjugating enzyme E2D 1 7321 ENSG00000072401
144  ENSG00000173786 NA CNP 2',3'-cyclic nucleotide 3' phosphodiesterase 1267 ENSG00000173786
145  ENSG00000171130 NA ATP6V0E2 ATPase, H+ transporting V0 subunit e2 155066 ENSG00000171130
146  ENSG00000159593 NA NAE1 NEDD8 activating enzyme E1 subunit 1 8883 ENSG00000159593
147  ENSG00000167468 NA GPX4 glutathione peroxidase 4 2879 ENSG00000167468
148  ENSG00000139180 NA NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa 4704 ENSG00000139180
149  ENSG00000127184 NA COX7C cytochrome c oxidase subunit VIIc 1350 ENSG00000127184
150  ENSG00000111640 NA GAPDH glyceraldehyde-3-phosphate dehydrogenase 2597 ENSG00000111640
151  ENSG00000177700 NA POLR2L polymerase (RNA) II (DNA directed) polypeptide L, 7.6kDa 5441 ENSG00000177700
152  ENSG00000123836 NA PFKFB2 6-phosphofructo-2-kinase/fructose-2,6-biphosphatase 2 5208 ENSG00000123836
153  ENSG00000085760 NA MTIF2 mitochondrial translational initiation factor 2 4528 ENSG00000085760
154  ENSG00000120265 NA PCMT1 protein-L-isoaspartate (D-aspartate) O-methyltransferase 5110 ENSG00000120265
155  ENSG00000109911 NA ELP4 elongator acetyltransferase complex subunit 4 26610 ENSG00000109911
156  ENSG00000156239 NA N6AMT1 N-6 adenine-specific DNA methyltransferase 1 (putative) 29104 ENSG00000156239
157  ENSG00000156958 NA GALK2 galactokinase 2 2585 ENSG00000156958
158  ENSG00000136159 NA NUDT15 nudix (nucleoside diphosphate linked moiety X)-type motif 15 55270 ENSG00000136159
159  ENSG00000100442 NA FKBP3 FK506 binding protein 3, 25kDa 2287 ENSG00000100442
160  ENSG00000172878 NA METAP1D methionyl aminopeptidase type 1D (mitochondrial) 254042 ENSG00000172878
161  ENSG00000204370 NA SDHD succinate dehydrogenase complex, subunit D, integral membrane protein 6392 ENSG00000204370
162  ENSG00000196704 NA AMZ2 archaelysin family metallopeptidase 2 51321 ENSG00000196704
163  ENSG00000108384 NA RAD51C RAD51 homolog C (S. cerevisiae) 5889 ENSG00000108384
164  ENSG00000137106 NA GRHPR glyoxylate reductase/hydroxypyruvate reductase 9380 ENSG00000137106
165  ENSG00000111271 NA ACAD10 acyl-CoA dehydrogenase family, member 10 80724 ENSG00000111271
166  ENSG00000169738 NA DCXR dicarbonyl/L-xylulose reductase 51181 ENSG00000169738
167  ENSG00000027001 NA MIPEP mitochondrial intermediate peptidase 4285 ENSG00000027001
168  ENSG00000160211 NA G6PD glucose-6-phosphate dehydrogenase 2539 ENSG00000160211
169  ENSG00000138777 NA PPA2 pyrophosphatase (inorganic) 2 27068 ENSG00000138777
170  ENSG00000143727 NA ACP1 acid phosphatase 1, soluble 52 ENSG00000143727
171  ENSG00000100601 NA ALKBH1 alkB, alkylation repair homolog 1 (E. coli) 8846 ENSG00000100601
172  ENSG00000117280 NA RAB7L1 RAB7, member RAS oncogene family-like 1 8934 ENSG00000117280
173  ENSG00000115042 NA FAHD2A fumarylacetoacetate hydrolase domain containing 2A 51011 ENSG00000115042
174  ENSG00000066583 NA ISOC1 isochorismatase domain containing 1 51015 ENSG00000066583
175  ENSG00000111669 NA TPI1 triosephosphate isomerase 1 7167 ENSG00000111669
176  ENSG00000023228 NA NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) 4719 ENSG00000023228
177  ENSG00000184788 NA SATL1 spermidine/spermine N1-acetyl transferase-like 1 340562 ENSG00000184788
178  ENSG00000139160 NA METTL20 methyltransferase like 20 254013 ENSG00000139160
179  ENSG00000143252 NA SDHC succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa 6391 ENSG00000143252
180  ENSG00000100116 NA GCAT glycine C-acetyltransferase 23464 ENSG00000100116
181  ENSG00000186318 NA BACE1 beta-site APP-cleaving enzyme 1 23621 ENSG00000265969 ENSG00000186318
182  ENSG00000151376 NA ME3 malic enzyme 3, NADP(+)-dependent, mitochondrial 10873 ENSG00000151376
183  ENSG00000145982 NA FARS2 phenylalanyl-tRNA synthetase 2, mitochondrial 10667 ENSG00000145982
184  ENSG00000121897 NA LIAS lipoic acid synthetase 11019 ENSG00000121897
185  ENSG00000110955 NA ATP5B ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide 506 ENSG00000110955
186  ENSG00000151883 NA PARP8 poly (ADP-ribose) polymerase family, member 8 79668 ENSG00000151883
187  ENSG00000197122 NA SRC v-src sarcoma (Schmidt-Ruppin A-2) viral oncogene homolog (avian) 6714 ENSG00000197122
188  ENSG00000112695 NA COX7A2 cytochrome c oxidase subunit VIIa polypeptide 2 (liver) 1347 ENSG00000112695
189  ENSG00000147155 NA EBP emopamil binding protein (sterol isomerase) 10682 ENSG00000147155
190  ENSG00000198373 NA WWP2 WW domain containing E3 ubiquitin protein ligase 2 11060 ENSG00000198373
191  ENSG00000198736 NA MSRB1 methionine sulfoxide reductase B1 51734 ENSG00000198736
192  ENSG00000179958 NA DCTPP1 dCTP pyrophosphatase 1 79077 ENSG00000179958
193  ENSG00000131495 NA NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa 4695 ENSG00000131495
194  ENSG00000083720 NA OXCT1 3-oxoacid CoA transferase 1 5019 ENSG00000083720
195  ENSG00000065518 NA NDUFB4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa 4710 ENSG00000065518
196  ENSG00000095321 NA CRAT carnitine O-acetyltransferase 1384 ENSG00000095321
197  ENSG00000185808 NA PIGP phosphatidylinositol glycan anchor biosynthesis, class P 51227 ENSG00000185808
198  ENSG00000159445 NA THEM4 thioesterase superfamily member 4 117145 ENSG00000159445
199  ENSG00000165688 NA PMPCA peptidase (mitochondrial processing) alpha 23203 ENSG00000165688
200  ENSG00000120992 NA LYPLA1 lysophospholipase I 10434 ENSG00000120992
201  ENSG00000198721 NA ECI2 enoyl-CoA delta isomerase 2 10455 ENSG00000198721
202  ENSG00000112855 NA HARS2 histidyl-tRNA synthetase 2, mitochondrial 23438 ENSG00000112855
203  ENSG00000197580 NA BCO2 beta-carotene oxygenase 2 83875 ENSG00000197580
204  ENSG00000147853 NA AK3 adenylate kinase 3 50808 ENSG00000147853
205  ENSG00000131174 NA COX7B cytochrome c oxidase subunit VIIb 1349 ENSG00000131174
206  ENSG00000147364 NA FBXO25 F-box protein 25 26260 ENSG00000147364
207  ENSG00000170906 NA NDUFA3 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa 4696 ENSG00000170906
208  ENSG00000205309 NA NT5M 5',3'-nucleotidase, mitochondrial 56953 ENSG00000205309
209  ENSG00000136247 NA ZDHHC4 zinc finger, DHHC-type containing 4 55146 ENSG00000136247
210  ENSG00000112304 NA ACOT13 acyl-CoA thioesterase 13 55856 ENSG00000112304
211  ENSG00000160808 NA MYL3 myosin, light chain 3, alkali; ventricular, skeletal, slow 4634 ENSG00000160808
212  ENSG00000142507 NA PSMB6 proteasome (prosome, macropain) subunit, beta type, 6 5694 ENSG00000142507
213  ENSG00000111716 NA LDHB lactate dehydrogenase B 3945 ENSG00000111716
214  ENSG00000108439 NA PNPO pyridoxamine 5'-phosphate oxidase 55163 ENSG00000108439
215  ENSG00000114054 NA PCCB propionyl CoA carboxylase, beta polypeptide 5096 ENSG00000114054
216  ENSG00000167283 NA ATP5L ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G 10632 ENSG00000167283
217  ENSG00000111275 NA ALDH2 aldehyde dehydrogenase 2 family (mitochondrial) 217 ENSG00000111275
218  ENSG00000167799 NA NUDT8 nudix (nucleoside diphosphate linked moiety X)-type motif 8 254552 ENSG00000167799
219  ENSG00000169071 NA ROR2 receptor tyrosine kinase-like orphan receptor 2 4920 ENSG00000169071
220  ENSG00000134452 NA FBXO18 F-box protein, helicase, 18 84893 ENSG00000134452
221  ENSG00000136270 NA TBRG4 transforming growth factor beta regulator 4 9238 ENSG00000136270
222  ENSG00000131269 NA ABCB7 ATP-binding cassette, sub-family B (MDR/TAP), member 7 22 ENSG00000131269
223  ENSG00000010256 NA UQCRC1 ubiquinol-cytochrome c reductase core protein I 7384 ENSG00000010256
224  ENSG00000104823 NA ECH1 enoyl CoA hydratase 1, peroxisomal 1891 ENSG00000104823
225  ENSG00000101391 NA CDK5RAP1 CDK5 regulatory subunit associated protein 1 51654 ENSG00000101391
226  ENSG00000197912 NA SPG7 spastic paraplegia 7 (pure and complicated autosomal recessive) 6687 ENSG00000197912
227  ENSG00000171503 NA ETFDH electron-transferring-flavoprotein dehydrogenase 2110 ENSG00000171503
228  ENSG00000167065 NA DUSP18 dual specificity phosphatase 18 150290 ENSG00000167065
229  ENSG00000138796 NA HADH hydroxyacyl-CoA dehydrogenase 3033 ENSG00000138796
230  ENSG00000099804 NA CDC34 cell division cycle 34 homolog (S. cerevisiae) 997 ENSG00000099804
231  ENSG00000141965 NA FEM1A fem-1 homolog a (C. elegans) 55527 ENSG00000141965
232  ENSG00000165672 NA PRDX3 peroxiredoxin 3 10935 ENSG00000165672
233  ENSG00000227345 NA PARG poly (ADP-ribose) glycohydrolase 8505 ENSG00000227345
234  ENSG00000163521 NA GLB1L galactosidase, beta 1-like 79411 ENSG00000163521
235  ENSG00000161533 NA ACOX1 acyl-CoA oxidase 1, palmitoyl 51 ENSG00000161533
236  ENSG00000107317 NA PTGDS prostaglandin D2 synthase 21kDa (brain) 5730 ENSG00000107317
237  ENSG00000163382 NA APOA1BP apolipoprotein A-I binding protein 128240 ENSG00000163382
238  ENSG00000154237 NA LRRK1 leucine-rich repeat kinase 1 79705 ENSG00000154237
239  ENSG00000168653 NA NDUFS5 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) 4725 ENSG00000168653
240  ENSG00000247077 NA PGAM5 phosphoglycerate mutase family member 5 192111 ENSG00000247077
241  ENSG00000156110 NA ADK adenosine kinase 132 ENSG00000156110
242  ENSG00000149761 NA NUDT22 nudix (nucleoside diphosphate linked moiety X)-type motif 22 84304 ENSG00000149761
243  ENSG00000087299 NA L2HGDH L-2-hydroxyglutarate dehydrogenase 79944 ENSG00000087299
244  ENSG00000184903 NA IMMP2L IMP2 inner mitochondrial membrane peptidase-like (S. cerevisiae) 83943 ENSG00000184903
245  ENSG00000163864 NA NMNAT3 nicotinamide nucleotide adenylyltransferase 3 349565 ENSG00000163864
246  ENSG00000103316 NA CRYM crystallin, mu 1428 ENSG00000103316
247  ENSG00000161204 NA ABCF3 ATP-binding cassette, sub-family F (GCN20), member 3 55324 ENSG00000161204
248  ENSG00000197586 NA ENTPD6 ectonucleoside triphosphate diphosphohydrolase 6 (putative) 955 ENSG00000197586
249  ENSG00000156467 NA UQCRB ubiquinol-cytochrome c reductase binding protein 7381 ENSG00000156467
250  ENSG00000100142 NA POLR2F polymerase (RNA) II (DNA directed) polypeptide F 5435 ENSG00000100142
251  ENSG00000184076 NA UQCR10 ubiquinol-cytochrome c reductase, complex III subunit X 29796 ENSG00000184076
252  ENSG00000078070 NA MCCC1 methylcrotonoyl-CoA carboxylase 1 (alpha) 56922 ENSG00000078070
253  ENSG00000184489 NA PTP4A3 protein tyrosine phosphatase type IVA, member 3 11156 ENSG00000184489
254  ENSG00000068903 NA SIRT2 sirtuin 2 22933 ENSG00000068903
255  ENSG00000166133 NA RPUSD2 RNA pseudouridylate synthase domain containing 2 27079 ENSG00000166133
256  ENSG00000156885 NA COX6A2 cytochrome c oxidase subunit VIa polypeptide 2 1339 ENSG00000156885
257  ENSG00000154723 NA ATP5J ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 522 ENSG00000154723
258  ENSG00000169084 NA DHRSX dehydrogenase/reductase (SDR family) X-linked 207063 ENSG00000169084
259  ENSG00000006695 NA COX10 COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) 1352 ENSG00000006695
260  ENSG00000167969 NA ECI1 enoyl-CoA delta isomerase 1 1632 ENSG00000167969
261  ENSG00000105552 NA BCAT2 branched chain amino-acid transaminase 2, mitochondrial 587 ENSG00000105552
262  ENSG00000153531 NA ADPRHL1 ADP-ribosylhydrolase like 1 113622 ENSG00000153531
263  ENSG00000139531 NA SUOX sulfite oxidase 6821 ENSG00000139531
264  ENSG00000106066 NA CPVL carboxypeptidase, vitellogenic-like 54504 ENSG00000106066
265  ENSG00000125166 NA GOT2 glutamic-oxaloacetic transaminase 2, mitochondrial (aspartate aminotransferase 2) 2806 ENSG00000125166
266  ENSG00000141552 NA ANAPC11 anaphase promoting complex subunit 11 51529 ENSG00000141552
267  ENSG00000172336 NA POP7 processing of precursor 7, ribonuclease P/MRP subunit (S. cerevisiae) 10248 ENSG00000172336
268  ENSG00000140740 NA UQCRC2 ubiquinol-cytochrome c reductase core protein II 7385 ENSG00000140740
269  ENSG00000140374 NA ETFA electron-transfer-flavoprotein, alpha polypeptide 2108 ENSG00000140374
270  ENSG00000114378 NA HYAL1 hyaluronoglucosaminidase 1 3373 ENSG00000114378
271  ENSG00000147684 NA NDUFB9 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa 4715 ENSG00000147684
272  ENSG00000160194 NA NDUFV3 NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa 4731 ENSG00000160194
273  ENSG00000184983 NA NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa 4700 ENSG00000184983
274  ENSG00000102309 NA PIN4 protein (peptidylprolyl cis/trans isomerase) NIMA-interacting, 4 (parvulin) 5303 ENSG00000102309
275  ENSG00000158864 NA NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) 4720 ENSG00000158864
276  ENSG00000105197 NA TIMM50 translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae) 92609 ENSG00000105197
277  ENSG00000142168 NA SOD1 superoxide dismutase 1, soluble 6647 ENSG00000142168
278  ENSG00000168101 NA NUDT16L1 nudix (nucleoside diphosphate linked moiety X)-type motif 16-like 1 84309 ENSG00000168101
279  ENSG00000000419 NA DPM1 dolichyl-phosphate mannosyltransferase polypeptide 1, catalytic subunit 8813 ENSG00000000419
280  ENSG00000181929 NA PRKAG1 protein kinase, AMP-activated, gamma 1 non-catalytic subunit 5571 ENSG00000181929
281  ENSG00000076043 NA REXO2 REX2, RNA exonuclease 2 homolog (S. cerevisiae) 25996 ENSG00000076043
282  ENSG00000120254 NA MTHFD1L methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 1-like 25902 ENSG00000120254
283  ENSG00000069998 NA CECR5 cat eye syndrome chromosome region, candidate 5 27440 ENSG00000069998
284  ENSG00000147813 NA NAPRT1 nicotinate phosphoribosyltransferase domain containing 1 93100 ENSG00000147813
285  ENSG00000119689 NA DLST dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex) 1743 ENSG00000119689
286  ENSG00000184924 NA PTRHD1 peptidyl-tRNA hydrolase domain containing 1 391356 ENSG00000184924
287  ENSG00000168291 NA PDHB pyruvate dehydrogenase (lipoamide) beta 5162 ENSG00000168291
288  ENSG00000156502 NA SUPV3L1 suppressor of var1, 3-like 1 (S. cerevisiae) 6832 ENSG00000156502
289  ENSG00000156049 NA GNA14 guanine nucleotide binding protein (G protein), alpha 14 9630 ENSG00000156049
290  ENSG00000162849 NA KIF26B kinesin family member 26B 55083 ENSG00000162849
291  ENSG00000116459 NA ATP5F1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 515 ENSG00000116459
292  ENSG00000105499 NA PLA2G4C phospholipase A2, group IVC (cytosolic, calcium-independent) 8605 ENSG00000105499
293  ENSG00000138399 NA FASTKD1 FAST kinase domains 1 79675 ENSG00000138399
294  ENSG00000112992 NA NNT nicotinamide nucleotide transhydrogenase 23530 ENSG00000112992
295  ENSG00000107951 NA MTPAP mitochondrial poly(A) polymerase 55149 ENSG00000107951
296  ENSG00000067704 NA IARS2 isoleucyl-tRNA synthetase 2, mitochondrial 55699 ENSG00000067704
297  ENSG00000215251 NA FASTKD5 FAST kinase domains 5 60493 ENSG00000215251
298  ENSG00000183785 NA TUBA8 tubulin, alpha 8 51807 ENSG00000183785
299  ENSG00000182185 NA RAD51B RAD51 homolog B (S. cerevisiae) 5890 ENSG00000182185
300  ENSG00000130348 NA QRSL1 glutaminyl-tRNA synthase (glutamine-hydrolyzing)-like 1 55278 ENSG00000130348
301  ENSG00000183765 NA CHEK2 checkpoint kinase 2 11200 ENSG00000183765
302  ENSG00000148950 NA IMMP1L IMP1 inner mitochondrial membrane peptidase-like (S. cerevisiae) 196294 ENSG00000148950
303  ENSG00000119421 NA NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa 4702 ENSG00000119421
304  ENSG00000170502 NA NUDT9 nudix (nucleoside diphosphate linked moiety X)-type motif 9 53343 ENSG00000170502
305  ENSG00000130347 NA RTN4IP1 reticulon 4 interacting protein 1 84816 ENSG00000130347
306  ENSG00000244005 NA NFS1 NFS1 nitrogen fixation 1 homolog (S. cerevisiae) 9054 ENSG00000244005
307  ENSG00000126267 NA COX6B1 cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) 1340 ENSG00000126267
308  ENSG00000104879 NA CKM creatine kinase, muscle 1158 ENSG00000104879
309  ENSG00000166192 NA SENP8 SUMO/sentrin specific peptidase family member 8 123228 ENSG00000166192
310  ENSG00000154814 NA OXNAD1 oxidoreductase NAD-binding domain containing 1 92106 ENSG00000154814
311  ENSG00000076003 NA MCM6 minichromosome maintenance complex component 6 4175 ENSG00000076003
312  ENSG00000100804 NA PSMB5 proteasome (prosome, macropain) subunit, beta type, 5 5693 ENSG00000100804
313  ENSG00000134330 NA IAH1 isoamyl acetate-hydrolyzing esterase 1 homolog (S. cerevisiae) 285148 ENSG00000134330
314  ENSG00000148450 NA MSRB2 methionine sulfoxide reductase B2 22921 ENSG00000148450
315  ENSG00000145494 NA NDUFS6 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) 4726 ENSG00000145494
316  ENSG00000163687 NA DNASE1L3 deoxyribonuclease I-like 3 1776 ENSG00000163687
317  ENSG00000072506 NA HSD17B10 hydroxysteroid (17-beta) dehydrogenase 10 3028 ENSG00000072506
318  ENSG00000131143 NA COX4I1 cytochrome c oxidase subunit IV isoform 1 1327 ENSG00000131143
319  ENSG00000196236 NA XPNPEP3 X-prolyl aminopeptidase (aminopeptidase P) 3, putative 63929 ENSG00000196236
320  ENSG00000136444 NA RSAD1 radical S-adenosyl methionine domain containing 1 55316 ENSG00000136444
321  ENSG00000197885 NA NKIRAS1 NFKB inhibitor interacting Ras-like 1 28512 ENSG00000197885
322  ENSG00000090266 NA NDUFB2 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa 4708 ENSG00000090266
323  ENSG00000108515 NA ENO3 enolase 3 (beta, muscle) 2027 ENSG00000108515
324  ENSG00000213995 NA CARKD carbohydrate kinase domain containing 55739 ENSG00000213995
325  ENSG00000105649 NA RAB3A RAB3A, member RAS oncogene family 5864 ENSG00000105649
326  ENSG00000184860 NA SDR42E1 short chain dehydrogenase/reductase family 42E, member 1 93517 ENSG00000184860
327  ENSG00000151498 NA ACAD8 acyl-CoA dehydrogenase family, member 8 27034 ENSG00000151498
328  ENSG00000047249 NA ATP6V1H ATPase, H+ transporting, lysosomal 50/57kDa, V1 subunit H 51606 ENSG00000047249
329  ENSG00000136143 NA SUCLA2 succinate-CoA ligase, ADP-forming, beta subunit 8803 ENSG00000136143
330  ENSG00000003137 NA CYP26B1 cytochrome P450, family 26, subfamily B, polypeptide 1 56603 ENSG00000003137
331  ENSG00000135778 NA NTPCR nucleoside-triphosphatase, cancer-related 84284 ENSG00000135778
332  ENSG00000105258 NA POLR2I polymerase (RNA) II (DNA directed) polypeptide I, 14.5kDa 5438 ENSG00000105258
333  ENSG00000166855 NA CLPX ClpX caseinolytic peptidase X homolog (E. coli) 10845 ENSG00000166855
334  ENSG00000110931 NA CAMKK2 calcium/calmodulin-dependent protein kinase kinase 2, beta 10645 ENSG00000110931
335  ENSG00000173614 NA NMNAT1 nicotinamide nucleotide adenylyltransferase 1 64802 ENSG00000173614
336  ENSG00000172331 NA BPGM 2,3-bisphosphoglycerate mutase 669 ENSG00000172331
337  ENSG00000166321 NA NUDT13 nudix (nucleoside diphosphate linked moiety X)-type motif 13 25961 ENSG00000166321
338  ENSG00000130159 NA ECSIT ECSIT homolog (Drosophila) 51295 ENSG00000130159
339  ENSG00000171763 NA SPATA5L1 spermatogenesis associated 5-like 1 79029 ENSG00000171763
340  ENSG00000074582 NA BCS1L BCS1-like (S. cerevisiae) 617 ENSG00000074582
341  ENSG00000129084 NA PSMA1 proteasome (prosome, macropain) subunit, alpha type, 1 5682 ENSG00000256206 ENSG00000129084
342  ENSG00000082146 NA STRADB STE20-related kinase adaptor beta 55437 ENSG00000082146
343  ENSG00000116171 NA SCP2 sterol carrier protein 2 6342 ENSG00000116171
344  ENSG00000103274 NA NUBP1 nucleotide binding protein 1 4682 ENSG00000103274
345  ENSG00000167815 NA PRDX2 peroxiredoxin 2 7001 ENSG00000167815
346  ENSG00000166816 NA LDHD lactate dehydrogenase D 197257 ENSG00000166816
347  ENSG00000143374 NA TARS2 threonyl-tRNA synthetase 2, mitochondrial (putative) 80222 ENSG00000143374
348  ENSG00000013275 NA PSMC4 proteasome (prosome, macropain) 26S subunit, ATPase, 4 5704 ENSG00000013275
349  ENSG00000066926 NA FECH ferrochelatase 2235 ENSG00000066926
350  ENSG00000087460 NA GNAS GNAS complex locus 2778 ENSG00000087460
351  ENSG00000117118 NA SDHB succinate dehydrogenase complex, subunit B, iron sulfur (Ip) 6390 ENSG00000117118
352  ENSG00000168827 NA GFM1 G elongation factor, mitochondrial 1 85476 ENSG00000168827
353  ENSG00000143641 NA GALNT2 UDP-N-acetyl-alpha-D-galactosamine:polypeptide N-acetylgalactosaminyltransferase 2 (GalNAc-T2) 2590 ENSG00000143641
354  ENSG00000142149 NA HUNK hormonally up-regulated Neu-associated kinase 30811 ENSG00000142149
355  ENSG00000149380 NA P4HA3 prolyl 4-hydroxylase, alpha polypeptide III 283208 ENSG00000149380
356  ENSG00000115944 NA COX7A2L cytochrome c oxidase subunit VIIa polypeptide 2 like 9167 ENSG00000115944
357  ENSG00000166228 NA PCBD1 pterin-4 alpha-carbinolamine dehydratase/dimerization cofactor of hepatocyte nuclear factor 1 alpha 5092 ENSG00000166228
358  ENSG00000137225 NA CAPN11 calpain 11 11131 ENSG00000137225
359  ENSG00000100294 NA MCAT malonyl CoA:ACP acyltransferase (mitochondrial) 27349 ENSG00000100294
360  ENSG00000112667 NA C6orf108 chromosome 6 open reading frame 108 10591 ENSG00000112667
361  ENSG00000197150 NA ABCB8 ATP-binding cassette, sub-family B (MDR/TAP), member 8 11194 ENSG00000197150
362  ENSG00000152234 NA ATP5A1 ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle 498 ENSG00000152234
363  ENSG00000164494 NA PDSS2 prenyl (decaprenyl) diphosphate synthase, subunit 2 57107 ENSG00000164494
364  ENSG00000151366 NA NDUFC2 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa 4718 ENSG00000151366
365  ENSG00000178802 NA MPI mannose phosphate isomerase 4351 ENSG00000178802
366  ENSG00000128609 NA NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa 4698 ENSG00000128609
367  ENSG00000163541 NA SUCLG1 succinate-CoA ligase, alpha subunit 8802 ENSG00000163541
368  ENSG00000090432 NA MUL1 mitochondrial E3 ubiquitin protein ligase 1 79594 ENSG00000090432
369  ENSG00000146701 NA MDH2 malate dehydrogenase 2, NAD (mitochondrial) 4191 ENSG00000146701
370  ENSG00000103489 NA XYLT1 xylosyltransferase I 64131 ENSG00000103489
371  ENSG00000172350 NA ABCG4 ATP-binding cassette, sub-family G (WHITE), member 4 64137 ENSG00000172350
372  ENSG00000131730 NA CKMT2 creatine kinase, mitochondrial 2 (sarcomeric) 1160 ENSG00000131730
373  ENSG00000137714 NA FDX1 ferredoxin 1 2230 ENSG00000137714
374  ENSG00000169021 NA UQCRFS1 ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 7386 ENSG00000169021
375  ENSG00000115652 NA UXS1 UDP-glucuronate decarboxylase 1 80146 ENSG00000115652
376  ENSG00000132541 NA HRSP12 heat-responsive protein 12 10247 ENSG00000132541
377  ENSG00000124523 NA SIRT5 sirtuin 5 23408 ENSG00000124523
378  ENSG00000145439 NA CBR4 carbonyl reductase 4 84869 ENSG00000145439
379  ENSG00000160446 NA ZDHHC12 zinc finger, DHHC-type containing 12 84885 ENSG00000160446
380  ENSG00000157881 NA PANK4 pantothenate kinase 4 55229 ENSG00000157881
381  ENSG00000197943 NA PLCG2 phospholipase C, gamma 2 (phosphatidylinositol-specific) 5336 ENSG00000197943
382  ENSG00000144199 NA FAHD2B fumarylacetoacetate hydrolase domain containing 2B 151313 ENSG00000144199
383  ENSG00000062485 NA CS citrate synthase 1431 ENSG00000062485
384  ENSG00000160439 NA RDH13 retinol dehydrogenase 13 (all-trans/9-cis) 112724 ENSG00000160439
385  ENSG00000175193 NA PARL presenilin associated, rhomboid-like 55486 ENSG00000175193
386  ENSG00000120053 NA GOT1 glutamic-oxaloacetic transaminase 1, soluble (aspartate aminotransferase 1) 2805 ENSG00000120053
387  ENSG00000149328 NA GLB1L2 galactosidase, beta 1-like 2 89944 ENSG00000149328
388  ENSG00000189283 NA FHIT fragile histidine triad 2272 ENSG00000189283
389  ENSG00000174021 NA GNG5 guanine nucleotide binding protein (G protein), gamma 5 2787 ENSG00000174021
390  ENSG00000139428 NA MMAB methylmalonic aciduria (cobalamin deficiency) cblB type 326625 ENSG00000139428
391  ENSG00000100246 NA DNAL4 dynein, axonemal, light chain 4 10126 ENSG00000100246
392  ENSG00000070808 NA CAMK2A calcium/calmodulin-dependent protein kinase II alpha 815 ENSG00000070808
393  ENSG00000185973 NA TMLHE trimethyllysine hydroxylase, epsilon 55217 ENSG00000185973
394  ENSG00000196562 NA SULF2 sulfatase 2 55959 ENSG00000196562
395  ENSG00000137513 NA NARS2 asparaginyl-tRNA synthetase 2, mitochondrial (putative) 79731 ENSG00000137513
396  ENSG00000124370 NA MCEE methylmalonyl CoA epimerase 84693 ENSG00000124370
397  ENSG00000162600 NA OMA1 OMA1 zinc metallopeptidase homolog (S. cerevisiae) 115209 ENSG00000162600
398  ENSG00000108179 NA PPIF peptidylprolyl isomerase F 10105 ENSG00000108179
399  ENSG00000137133 NA HINT2 histidine triad nucleotide binding protein 2 84681 ENSG00000137133
400  ENSG00000164405 NA UQCRQ ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa 27089 ENSG00000164405
401  ENSG00000136930 NA PSMB7 proteasome (prosome, macropain) subunit, beta type, 7 5695 ENSG00000136930
402  ENSG00000122729 NA ACO1 aconitase 1, soluble 48 ENSG00000122729
403  ENSG00000173085 NA COQ2 coenzyme Q2 homolog, prenyltransferase (yeast) 27235 ENSG00000173085
404  ENSG00000124767 NA GLO1 glyoxalase I 2739 ENSG00000124767
405  ENSG00000124172 NA ATP5E ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit 514 ENSG00000124172
406  ENSG00000183648 NA NDUFB1 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa 4707 ENSG00000183648
407  ENSG00000110435 NA PDHX pyruvate dehydrogenase complex, component X 8050 ENSG00000110435
408  ENSG00000099624 NA ATP5D ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit 513 ENSG00000099624
409  ENSG00000107954 NA NEURL neuralized homolog (Drosophila) 9148 ENSG00000107954
410  ENSG00000100412 NA ACO2 aconitase 2, mitochondrial 50 ENSG00000100412
411  ENSG00000185621 NA LMLN leishmanolysin-like (metallopeptidase M8 family) 89782 ENSG00000185621
412  ENSG00000175792 NA RUVBL1 RuvB-like 1 (E. coli) 8607 ENSG00000175792
413  ENSG00000121022 NA COPS5 COP9 constitutive photomorphogenic homolog subunit 5 (Arabidopsis) 10987 ENSG00000121022
414  ENSG00000164896 NA FASTK Fas-activated serine/threonine kinase 10922 ENSG00000164896
415  ENSG00000112655 NA PTK7 PTK7 protein tyrosine kinase 7 5754 ENSG00000112655
416  ENSG00000125356 NA NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa 4694 ENSG00000125356
417  ENSG00000129282 NA MRM1 mitochondrial rRNA methyltransferase 1 homolog (S. cerevisiae) 79922 ENSG00000129282
418  ENSG00000124641 NA MED20 mediator complex subunit 20 9477 ENSG00000124641
419  ENSG00000119673 NA ACOT2 acyl-CoA thioesterase 2 10965 ENSG00000119673
420  ENSG00000163636 NA PSMD6 proteasome (prosome, macropain) 26S subunit, non-ATPase, 6 9861 ENSG00000163636
421  ENSG00000070785 NA EIF2B3 eukaryotic translation initiation factor 2B, subunit 3 gamma, 58kDa 8891 ENSG00000070785
422  ENSG00000137574 NA TGS1 trimethylguanosine synthase 1 96764 ENSG00000137574
423  ENSG00000099795 NA NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa 4713 ENSG00000099795
424  ENSG00000180185 NA FAHD1 fumarylacetoacetate hydrolase domain containing 1 81889 ENSG00000180185
425  ENSG00000175470 NA PPP2R2D protein phosphatase 2, regulatory subunit B, delta 55844 ENSG00000175470
426  ENSG00000044459 NA CNTLN centlein, centrosomal protein 54875 ENSG00000044459
427  ENSG00000153574 NA RPIA ribose 5-phosphate isomerase A 22934 ENSG00000153574
428  ENSG00000101350 NA KIF3B kinesin family member 3B 9371 ENSG00000101350
429  ENSG00000103507 NA BCKDK branched chain ketoacid dehydrogenase kinase 10295 ENSG00000103507
430  ENSG00000148090 NA AUH AU RNA binding protein/enoyl-CoA hydratase 549 ENSG00000148090
431  ENSG00000137171 NA KLC4 kinesin light chain 4 89953 ENSG00000137171
432  ENSG00000090013 NA BLVRB biliverdin reductase B (flavin reductase (NADPH)) 645 ENSG00000090013
433  ENSG00000167136 NA ENDOG endonuclease G 2021 ENSG00000167136
434  ENSG00000123427 NA METTL21B methyltransferase like 21B 25895 ENSG00000123427
435  ENSG00000111817 NA DSE dermatan sulfate epimerase 29940 ENSG00000111817
436  ENSG00000060971 NA ACAA1 acetyl-CoA acyltransferase 1 30 ENSG00000060971
437  ENSG00000150867 NA PIP4K2A phosphatidylinositol-5-phosphate 4-kinase, type II, alpha 5305 ENSG00000150867
438  ENSG00000164347 NA GFM2 G elongation factor, mitochondrial 2 84340 ENSG00000164347
439  ENSG00000111906 NA HDDC2 HD domain containing 2 51020 ENSG00000111906
440  ENSG00000119723 NA COQ6 coenzyme Q6 homolog, monooxygenase (S. cerevisiae) 51004 ENSG00000119723
441  ENSG00000138175 NA ARL3 ADP-ribosylation factor-like 3 403 ENSG00000138175
442  ENSG00000197894 NA ADH5 alcohol dehydrogenase 5 (class III), chi polypeptide 128 ENSG00000197894
443  ENSG00000197448 NA GSTK1 glutathione S-transferase kappa 1 373156 ENSG00000197448
444  ENSG00000167792 NA NDUFV1 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa 4723 ENSG00000167792
445  ENSG00000117594 NA HSD11B1 hydroxysteroid (11-beta) dehydrogenase 1 3290 ENSG00000117594
446  ENSG00000188342 NA GTF2F2 general transcription factor IIF, polypeptide 2, 30kDa 2963 ENSG00000188342
447  ENSG00000110717 NA NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) 4728 ENSG00000110717
448  ENSG00000165609 NA NUDT5 nudix (nucleoside diphosphate linked moiety X)-type motif 5 11164 ENSG00000165609
449  ENSG00000197535 NA MYO5A myosin VA (heavy chain 12, myoxin) 4644 ENSG00000197535
450  ENSG00000204308 NA RNF5 ring finger protein 5, E3 ubiquitin protein ligase 6048 ENSG00000204308
451  ENSG00000184719 NA RNLS renalase, FAD-dependent amine oxidase 55328 ENSG00000184719
452  ENSG00000137996 NA RTCA RNA 3'-terminal phosphate cyclase 8634 ENSG00000137996
453  ENSG00000091164 NA TXNL1 thioredoxin-like 1 9352 ENSG00000091164
454  ENSG00000184508 NA HDDC3 HD domain containing 3 374659 ENSG00000184508
455  ENSG00000036672 NA USP2 ubiquitin specific peptidase 2 9099 ENSG00000036672
456  ENSG00000117139 NA KDM5B lysine (K)-specific demethylase 5B 10765 ENSG00000117139
457  ENSG00000159377 NA PSMB4 proteasome (prosome, macropain) subunit, beta type, 4 5692 ENSG00000159377
458  ENSG00000100034 NA PPM1F protein phosphatase, Mg2+/Mn2+ dependent, 1F 9647 ENSG00000100034
459  ENSG00000138382 NA METTL5 methyltransferase like 5 29081 ENSG00000138382
460  ENSG00000178952 NA TUFM Tu translation elongation factor, mitochondrial 7284 ENSG00000178952
461  ENSG00000177302 NA TOP3A topoisomerase (DNA) III alpha 7156 ENSG00000177302
462  ENSG00000127884 NA ECHS1 enoyl CoA hydratase, short chain, 1, mitochondrial 1892 ENSG00000127884
463  ENSG00000198796 NA ALPK2 alpha-kinase 2 115701 ENSG00000198796
464  ENSG00000126247 NA CAPNS1 calpain, small subunit 1 826 ENSG00000126247
465  ENSG00000241468 NA ATP5J2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 9551 ENSG00000241468
466  ENSG00000170430 NA MGMT O-6-methylguanine-DNA methyltransferase 4255 ENSG00000170430
467  ENSG00000140470 NA ADAMTS17 ADAM metallopeptidase with thrombospondin type 1 motif, 17 170691 ENSG00000140470
468  ENSG00000013563 NA DNASE1L1 deoxyribonuclease I-like 1 1774 ENSG00000013563
469  ENSG00000117151 NA CTBS chitobiase, di-N-acetyl- 1486 ENSG00000117151
470  ENSG00000176340 NA COX8A cytochrome c oxidase subunit VIIIA (ubiquitous) 1351 ENSG00000176340
471  ENSG00000170266 NA GLB1 galactosidase, beta 1 2720 ENSG00000170266
472  ENSG00000101247 NA NDUFAF5 NADH dehydrogenase (ubiquinone) complex I, assembly factor 5 79133 ENSG00000101247
473  ENSG00000101365 NA IDH3B isocitrate dehydrogenase 3 (NAD+) beta 3420 ENSG00000101365
474  ENSG00000241837 NA ATP5O ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit 539 ENSG00000241837
475  ENSG00000141504 NA SAT2 spermidine/spermine N1-acetyltransferase family member 2 112483 ENSG00000141504
476  ENSG00000140905 NA GCSH glycine cleavage system protein H (aminomethyl carrier) 2653 ENSG00000140905
477  ENSG00000158793 NA NIT1 nitrilase 1 4817 ENSG00000158793
478  ENSG00000182909 NA LENG9 leukocyte receptor cluster (LRC) member 9 94059 ENSG00000182909


Database:molecular function       Name:oxidoreductase activity, acting on NADH or NADPH       ID:GO:0016651
C=94; O=41; E=5.66; R=7.25; rawP=1.38e-25; adjP=1.16e-23
Index UserID Value Gene Symbol Gene Name EntrezGene Ensembl
1  ENSG00000151366 NA NDUFC2 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa 4718 ENSG00000151366
2  ENSG00000128609 NA NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa 4698 ENSG00000128609
3  ENSG00000023228 NA NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) 4719 ENSG00000023228
4  ENSG00000165264 NA NDUFB6 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa 4712 ENSG00000165264
5  ENSG00000145494 NA NDUFS6 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) 4726 ENSG00000145494
6  ENSG00000136521 NA NDUFB5 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa 4711 ENSG00000136521
7  ENSG00000004779 NA NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa 4706 ENSG00000004779
8  ENSG00000189043 NA NDUFA4 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa 4697 ENSG00000189043
9  ENSG00000115286 NA NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) 374291 ENSG00000115286
10  ENSG00000164258 NA NDUFS4 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) 4724 ENSG00000164258
11  ENSG00000119013 NA NDUFB3 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa 4709 ENSG00000119013
12  ENSG00000104325 NA DECR1 2,4-dienoyl CoA reductase 1, mitochondrial 1666 ENSG00000104325
13  ENSG00000167792 NA NDUFV1 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa 4723 ENSG00000167792
14  ENSG00000131495 NA NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa 4695 ENSG00000131495
15  ENSG00000065518 NA NDUFB4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa 4710 ENSG00000065518
16  ENSG00000145439 NA CBR4 carbonyl reductase 4 84869 ENSG00000145439
17  ENSG00000090266 NA NDUFB2 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa 4708 ENSG00000090266
18  ENSG00000166136 NA NDUFB8 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa 4714 ENSG00000166136
19  ENSG00000110717 NA NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) 4728 ENSG00000110717
20  ENSG00000147684 NA NDUFB9 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa 4715 ENSG00000147684
21  ENSG00000160194 NA NDUFV3 NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa 4731 ENSG00000160194
22  ENSG00000184983 NA NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa 4700 ENSG00000184983
23  ENSG00000170906 NA NDUFA3 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa 4696 ENSG00000170906
24  ENSG00000184752 NA NDUFA12 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 55967 ENSG00000184752
25  ENSG00000091140 NA DLD dihydrolipoamide dehydrogenase 1738 ENSG00000091140
26  ENSG00000130414 NA NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa 4705 ENSG00000130414
27  ENSG00000158864 NA NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) 4720 ENSG00000158864
28  ENSG00000139180 NA NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa 4704 ENSG00000139180
29  ENSG00000109390 NA NDUFC1 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa 4717 ENSG00000109390
30  ENSG00000130159 NA ECSIT ECSIT homolog (Drosophila) 51295 ENSG00000130159
31  ENSG00000183648 NA NDUFB1 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa 4707 ENSG00000183648
32  ENSG00000157326 NA DHRS4 dehydrogenase/reductase (SDR family) member 4 10901 ENSG00000157326
33  ENSG00000140990 NA NDUFB10 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa 4716 ENSG00000140990
34  ENSG00000169738 NA DCXR dicarbonyl/L-xylulose reductase 51181 ENSG00000169738
35  ENSG00000165672 NA PRDX3 peroxiredoxin 3 10935 ENSG00000165672
36  ENSG00000112992 NA NNT nicotinamide nucleotide transhydrogenase 23530 ENSG00000112992
37  ENSG00000125356 NA NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa 4694 ENSG00000125356
38  ENSG00000213619 NA NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) 4722 ENSG00000213619
39  ENSG00000168653 NA NDUFS5 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) 4725 ENSG00000168653
40  ENSG00000099795 NA NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa 4713 ENSG00000099795
41  ENSG00000119421 NA NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa 4702 ENSG00000119421


Database:molecular function       Name:hydrogen ion transmembrane transporter activity       ID:GO:0015078
C=101; O=40; E=6.08; R=6.58; rawP=4.48e-23; adjP=3.28e-21
Index UserID Value Gene Symbol Gene Name EntrezGene Ensembl
1  ENSG00000135940 NA COX5B cytochrome c oxidase subunit Vb 1329 ENSG00000135940
2  ENSG00000156467 NA UQCRB ubiquinol-cytochrome c reductase binding protein 7381 ENSG00000156467
3  ENSG00000184076 NA UQCR10 ubiquinol-cytochrome c reductase, complex III subunit X 29796 ENSG00000184076
4  ENSG00000161281 NA COX7A1 cytochrome c oxidase subunit VIIa polypeptide 1 (muscle) 1346 ENSG00000161281
5  ENSG00000169020 NA ATP5I ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E 521 ENSG00000169020
6  ENSG00000189043 NA NDUFA4 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa 4697 ENSG00000189043
7  ENSG00000131143 NA COX4I1 cytochrome c oxidase subunit IV isoform 1 1327 ENSG00000131143
8  ENSG00000110955 NA ATP5B ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide 506 ENSG00000110955
9  ENSG00000164038 NA SLC9B2 solute carrier family 9, subfamily B (NHA2, cation proton antiporter 2), member 2 133308 ENSG00000164038
10  ENSG00000156885 NA COX6A2 cytochrome c oxidase subunit VIa polypeptide 2 1339 ENSG00000156885
11  ENSG00000164919 NA COX6C cytochrome c oxidase subunit VIc 1345 ENSG00000164919
12  ENSG00000154723 NA ATP5J ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 522 ENSG00000154723
13  ENSG00000006695 NA COX10 COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) 1352 ENSG00000006695
14  ENSG00000112695 NA COX7A2 cytochrome c oxidase subunit VIIa polypeptide 2 (liver) 1347 ENSG00000112695
15  ENSG00000169021 NA UQCRFS1 ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 7386 ENSG00000169021
16  ENSG00000135390 NA ATP5G2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C2 (subunit 9) 517 ENSG00000135390
17  ENSG00000167863 NA ATP5H ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d 10476 ENSG00000167863
18  ENSG00000127540 NA UQCR11 ubiquinol-cytochrome c reductase, complex III subunit XI 10975 ENSG00000127540
19  ENSG00000131174 NA COX7B cytochrome c oxidase subunit VIIb 1349 ENSG00000131174
20  ENSG00000047249 NA ATP6V1H ATPase, H+ transporting, lysosomal 50/57kDa, V1 subunit H 51606 ENSG00000047249
21  ENSG00000171130 NA ATP6V0E2 ATPase, H+ transporting V0 subunit e2 155066 ENSG00000171130
22  ENSG00000159199 NA ATP5G1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) 516 ENSG00000159199
23  ENSG00000167283 NA ATP5L ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G 10632 ENSG00000167283
24  ENSG00000127184 NA COX7C cytochrome c oxidase subunit VIIc 1350 ENSG00000127184
25  ENSG00000164405 NA UQCRQ ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa 27089 ENSG00000164405
26  ENSG00000010256 NA UQCRC1 ubiquinol-cytochrome c reductase core protein I 7384 ENSG00000010256
27  ENSG00000124172 NA ATP5E ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit 514 ENSG00000124172
28  ENSG00000116459 NA ATP5F1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 515 ENSG00000116459
29  ENSG00000099624 NA ATP5D ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit 513 ENSG00000099624
30  ENSG00000154518 NA ATP5G3 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C3 (subunit 9) 518 ENSG00000154518
31  ENSG00000165629 NA ATP5C1 ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 509 ENSG00000165629
32  ENSG00000112992 NA NNT nicotinamide nucleotide transhydrogenase 23530 ENSG00000112992
33  ENSG00000115944 NA COX7A2L cytochrome c oxidase subunit VIIa polypeptide 2 like 9167 ENSG00000115944
34  ENSG00000176340 NA COX8A cytochrome c oxidase subunit VIIIA (ubiquitous) 1351 ENSG00000176340
35  ENSG00000148290 NA SURF1 surfeit 1 6834 ENSG00000148290
36  ENSG00000178741 NA COX5A cytochrome c oxidase subunit Va 9377 ENSG00000178741
37  ENSG00000173660 NA UQCRH ubiquinol-cytochrome c reductase hinge protein 7388 ENSG00000173660
38  ENSG00000152234 NA ATP5A1 ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle 498 ENSG00000152234
39  ENSG00000241837 NA ATP5O ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit 539 ENSG00000241837
40  ENSG00000126267 NA COX6B1 cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) 1340 ENSG00000126267


Database:molecular function       Name:structural constituent of ribosome       ID:GO:0003735
C=157; O=48; E=9.45; R=5.08; rawP=9.72e-22; adjP=6.33e-20
Index UserID Value Gene Symbol Gene Name EntrezGene Ensembl
1  ENSG00000135972 NA MRPS9 mitochondrial ribosomal protein S9 64965 ENSG00000135972
2  ENSG00000239789 NA MRPS17 mitochondrial ribosomal protein S17 51373 ENSG00000239789
3  ENSG00000143436 NA MRPL9 mitochondrial ribosomal protein L9 65005 ENSG00000143436
4  ENSG00000198015 NA MRPL42 mitochondrial ribosomal protein L42 28977 ENSG00000198015
5  ENSG00000122140 NA MRPS2 mitochondrial ribosomal protein S2 51116 ENSG00000122140
6  ENSG00000116898 NA MRPS15 mitochondrial ribosomal protein S15 64960 ENSG00000116898
7  ENSG00000082515 NA MRPL22 mitochondrial ribosomal protein L22 29093 ENSG00000082515
8  ENSG00000115364 NA MRPL19 mitochondrial ribosomal protein L19 9801 ENSG00000115364
9  ENSG00000181991 NA MRPS11 mitochondrial ribosomal protein S11 64963 ENSG00000181991
10  ENSG00000112996 NA MRPS30 mitochondrial ribosomal protein S30 10884 ENSG00000112996
11  ENSG00000175110 NA MRPS22 mitochondrial ribosomal protein S22 56945 ENSG00000175110
12  ENSG00000102738 NA MRPS31 mitochondrial ribosomal protein S31 10240 ENSG00000102738
13  ENSG00000130312 NA MRPL34 mitochondrial ribosomal protein L34 64981 ENSG00000130312
14  ENSG00000163319 NA MRPS18C mitochondrial ribosomal protein S18C 51023 ENSG00000163319
15  ENSG00000182154 NA MRPL41 mitochondrial ribosomal protein L41 64975 ENSG00000182154
16  ENSG00000175581 NA MRPL48 mitochondrial ribosomal protein L48 51642 ENSG00000175581
17  ENSG00000174547 NA MRPL11 mitochondrial ribosomal protein L11 65003 ENSG00000174547
18  ENSG00000197345 NA MRPL21 mitochondrial ribosomal protein L21 219927 ENSG00000197345
19  ENSG00000137547 NA MRPL15 mitochondrial ribosomal protein L15 29088 ENSG00000137547
20  ENSG00000173141 NA MRP63 mitochondrial ribosomal protein 63 78988 ENSG00000173141
21  ENSG00000116221 NA MRPL37 mitochondrial ribosomal protein L37 51253 ENSG00000116221
22  ENSG00000090263 NA MRPS33 mitochondrial ribosomal protein S33 51650 ENSG00000090263
23  ENSG00000111639 NA MRPL51 mitochondrial ribosomal protein L51 51258 ENSG00000111639
24  ENSG00000143314 NA MRPL24 mitochondrial ribosomal protein L24 79590 ENSG00000143314
25  ENSG00000055950 NA MRPL43 mitochondrial ribosomal protein L43 84545 ENSG00000055950
26  ENSG00000262814 NA MRPL12 mitochondrial ribosomal protein L12 6182 ENSG00000262814
27  ENSG00000048544 NA MRPS10 mitochondrial ribosomal protein S10 55173 ENSG00000048544
28  ENSG00000166902 NA MRPL16 mitochondrial ribosomal protein L16 54948 ENSG00000166902
29  ENSG00000096080 NA MRPS18A mitochondrial ribosomal protein S18A 55168 ENSG00000096080
30  ENSG00000172590 NA MRPL52 mitochondrial ribosomal protein L52 122704 ENSG00000172590
31  ENSG00000134056 NA MRPS36 mitochondrial ribosomal protein S36 92259 ENSG00000134056
32  ENSG00000120333 NA MRPS14 mitochondrial ribosomal protein S14 63931 ENSG00000120333
33  ENSG00000204568 NA MRPS18B mitochondrial ribosomal protein S18B 28973 ENSG00000204568
34  ENSG00000132313 NA MRPL35 mitochondrial ribosomal protein L35 51318 ENSG00000132313
35  ENSG00000125445 NA MRPS7 mitochondrial ribosomal protein S7 51081 ENSG00000125445
36  ENSG00000187145 NA MRPS21 mitochondrial ribosomal protein S21 54460 ENSG00000187145
37  ENSG00000105364 NA MRPL4 mitochondrial ribosomal protein L4 51073 ENSG00000105364
38  ENSG00000086504 NA MRPL28 mitochondrial ribosomal protein L28 10573 ENSG00000086504
39  ENSG00000112651 NA MRPL2 mitochondrial ribosomal protein L2 51069 ENSG00000112651
40  ENSG00000162910 NA MRPL55 mitochondrial ribosomal protein L55 128308 ENSG00000162910
41  ENSG00000181610 NA MRPS23 mitochondrial ribosomal protein S23 51649 ENSG00000181610
42  ENSG00000243147 NA MRPL33 mitochondrial ribosomal protein L33 9553 ENSG00000243147
43  ENSG00000144029 NA MRPS5 mitochondrial ribosomal protein S5 64969 ENSG00000144029
44  ENSG00000169288 NA MRPL1 mitochondrial ribosomal protein L1 65008 ENSG00000169288
45  ENSG00000172172 NA MRPL13 mitochondrial ribosomal protein L13 28998 ENSG00000172172
46  ENSG00000182180 NA MRPS16 mitochondrial ribosomal protein S16 51021 ENSG00000182180
47  ENSG00000136522 NA MRPL47 mitochondrial ribosomal protein L47 57129 ENSG00000136522
48  ENSG00000214026 NA MRPL23 mitochondrial ribosomal protein L23 6150 ENSG00000214026


Database:molecular function       Name:cofactor binding       ID:GO:0048037
C=262; O=54; E=15.77; R=3.42; rawP=8.09e-16; adjP=4.74e-14
Index UserID Value Gene Symbol Gene Name EntrezGene Ensembl
1  ENSG00000139410 NA SDSL serine dehydratase-like 113675 ENSG00000139410
2  ENSG00000113790 NA EHHADH enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase 1962 ENSG00000113790
3  ENSG00000163541 NA SUCLG1 succinate-CoA ligase, alpha subunit 8802 ENSG00000163541
4  ENSG00000103316 NA CRYM crystallin, mu 1428 ENSG00000103316
5  ENSG00000100116 NA GCAT glycine C-acetyltransferase 23464 ENSG00000100116
6  ENSG00000151376 NA ME3 malic enzyme 3, NADP(+)-dependent, mitochondrial 10873 ENSG00000151376
7  ENSG00000072506 NA HSD17B10 hydroxysteroid (17-beta) dehydrogenase 10 3028 ENSG00000072506
8  ENSG00000156709 NA AIFM1 apoptosis-inducing factor, mitochondrion-associated, 1 9131 ENSG00000156709
9  ENSG00000004779 NA NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa 4706 ENSG00000004779
10  ENSG00000182054 NA IDH2 isocitrate dehydrogenase 2 (NADP+), mitochondrial 3418 ENSG00000182054
11  ENSG00000148672 NA GLUD1 glutamate dehydrogenase 1 2746 ENSG00000148672
12  ENSG00000068903 NA SIRT2 sirtuin 2 22933 ENSG00000068903
13  ENSG00000073578 NA SDHA succinate dehydrogenase complex, subunit A, flavoprotein (Fp) 6389 ENSG00000073578
14  ENSG00000115286 NA NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) 374291 ENSG00000115286
15  ENSG00000119723 NA COQ6 coenzyme Q6 homolog, monooxygenase (S. cerevisiae) 51004 ENSG00000119723
16  ENSG00000115652 NA UXS1 UDP-glucuronate decarboxylase 1 80146 ENSG00000115652
17  ENSG00000104325 NA DECR1 2,4-dienoyl CoA reductase 1, mitochondrial 1666 ENSG00000104325
18  ENSG00000167792 NA NDUFV1 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa 4723 ENSG00000167792
19  ENSG00000139531 NA SUOX sulfite oxidase 6821 ENSG00000139531
20  ENSG00000125166 NA GOT2 glutamic-oxaloacetic transaminase 2, mitochondrial (aspartate aminotransferase 2) 2806 ENSG00000125166
21  ENSG00000124523 NA SIRT5 sirtuin 5 23408 ENSG00000124523
22  ENSG00000145439 NA CBR4 carbonyl reductase 4 84869 ENSG00000145439
23  ENSG00000140374 NA ETFA electron-transfer-flavoprotein, alpha polypeptide 2108 ENSG00000140374
24  ENSG00000198721 NA ECI2 enoyl-CoA delta isomerase 2 10455 ENSG00000198721
25  ENSG00000120053 NA GOT1 glutamic-oxaloacetic transaminase 1, soluble (aspartate aminotransferase 1) 2805 ENSG00000120053
26  ENSG00000151498 NA ACAD8 acyl-CoA dehydrogenase family, member 8 27034 ENSG00000151498
27  ENSG00000091140 NA DLD dihydrolipoamide dehydrogenase 1738 ENSG00000091140
28  ENSG00000158864 NA NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) 4720 ENSG00000158864
29  ENSG00000111716 NA LDHB lactate dehydrogenase B 3945 ENSG00000111716
30  ENSG00000108439 NA PNPO pyridoxamine 5'-phosphate oxidase 55163 ENSG00000108439
31  ENSG00000139180 NA NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa 4704 ENSG00000139180
32  ENSG00000122971 NA ACADS acyl-CoA dehydrogenase, C-2 to C-3 short chain 35 ENSG00000122971
33  ENSG00000111640 NA GAPDH glyceraldehyde-3-phosphate dehydrogenase 2597 ENSG00000111640
34  ENSG00000067829 NA IDH3G isocitrate dehydrogenase 3 (NAD+) gamma 3421 ENSG00000067829
35  ENSG00000203797 NA DDO D-aspartate oxidase 8528 ENSG00000203797
36  ENSG00000116171 NA SCP2 sterol carrier protein 2 6342 ENSG00000116171
37  ENSG00000142082 NA SIRT3 sirtuin 3 23410 ENSG00000142082
38  ENSG00000166816 NA LDHD lactate dehydrogenase D 197257 ENSG00000166816
39  ENSG00000135297 NA MTO1 mitochondrial translation optimization 1 homolog (S. cerevisiae) 25821 ENSG00000135297
40  ENSG00000204370 NA SDHD succinate dehydrogenase complex, subunit D, integral membrane protein 6392 ENSG00000204370
41  ENSG00000117118 NA SDHB succinate dehydrogenase complex, subunit B, iron sulfur (Ip) 6390 ENSG00000117118
42  ENSG00000171503 NA ETFDH electron-transferring-flavoprotein dehydrogenase 2110 ENSG00000171503
43  ENSG00000137106 NA GRHPR glyoxylate reductase/hydroxypyruvate reductase 9380 ENSG00000137106
44  ENSG00000138796 NA HADH hydroxyacyl-CoA dehydrogenase 3033 ENSG00000138796
45  ENSG00000111271 NA ACAD10 acyl-CoA dehydrogenase family, member 10 80724 ENSG00000111271
46  ENSG00000160211 NA G6PD glucose-6-phosphate dehydrogenase 2539 ENSG00000160211
47  ENSG00000161533 NA ACOX1 acyl-CoA oxidase 1, palmitoyl 51 ENSG00000161533
48  ENSG00000112992 NA NNT nicotinamide nucleotide transhydrogenase 23530 ENSG00000112992
49  ENSG00000155368 NA DBI diazepam binding inhibitor (GABA receptor modulator, acyl-CoA binding protein) 1622 ENSG00000155368
50  ENSG00000023330 NA ALAS1 aminolevulinate, delta-, synthase 1 211 ENSG00000023330
51  ENSG00000105135 NA ILVBL ilvB (bacterial acetolactate synthase)-like 10994 ENSG00000105135
52  ENSG00000101365 NA IDH3B isocitrate dehydrogenase 3 (NAD+) beta 3420 ENSG00000101365
53  ENSG00000072778 NA ACADVL acyl-CoA dehydrogenase, very long chain 37 ENSG00000072778
54  ENSG00000244005 NA NFS1 NFS1 nitrogen fixation 1 homolog (S. cerevisiae) 9054 ENSG00000244005


Database:cellular component       Name:mitochondrion       ID:GO:0005739
C=1525; O=468; E=92.56; R=5.06; rawP=4.24e-232; adjP=1.68e-229
Index UserID Value Gene Symbol Gene Name EntrezGene Ensembl
1  ENSG00000143575 NA HAX1 HCLS1 associated protein X-1 10456 ENSG00000143575
2  ENSG00000165264 NA NDUFB6 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa 4712 ENSG00000165264
3  ENSG00000109846 NA CRYAB crystallin, alpha B 1410 ENSG00000109846
4  ENSG00000116898 NA MRPS15 mitochondrial ribosomal protein S15 64960 ENSG00000116898
5  ENSG00000161281 NA COX7A1 cytochrome c oxidase subunit VIIa polypeptide 1 (muscle) 1346 ENSG00000161281
6  ENSG00000167862 NA ICT1 immature colon carcinoma transcript 1 3396 ENSG00000167862
7  ENSG00000148672 NA GLUD1 glutamate dehydrogenase 1 2746 ENSG00000148672
8  ENSG00000147592 NA LACTB2 lactamase, beta 2 51110 ENSG00000147592
9  ENSG00000116288 NA PARK7 parkinson protein 7 11315 ENSG00000116288
10  ENSG00000135390 NA ATP5G2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C2 (subunit 9) 517 ENSG00000135390
11  ENSG00000177370 NA TIMM22 translocase of inner mitochondrial membrane 22 homolog (yeast) 29928 ENSG00000177370
12  ENSG00000003509 NA C2orf56 chromosome 2 open reading frame 56 55471 ENSG00000003509
13  ENSG00000166136 NA NDUFB8 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa 4714 ENSG00000166136
14  ENSG00000116353 NA MECR mitochondrial trans-2-enoyl-CoA reductase 51102 ENSG00000116353
15  ENSG00000172340 NA SUCLG2 succinate-CoA ligase, GDP-forming, beta subunit 8801 ENSG00000172340
16  ENSG00000151093 NA OXSM 3-oxoacyl-ACP synthase, mitochondrial 54995 ENSG00000151093
17  ENSG00000205707 NA LYRM5 LYR motif containing 5 144363 ENSG00000205707
18  ENSG00000091140 NA DLD dihydrolipoamide dehydrogenase 1738 ENSG00000091140
19  ENSG00000130414 NA NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa 4705 ENSG00000130414
20  ENSG00000165060 NA FXN frataxin 2395 ENSG00000165060
21  ENSG00000007923 NA DNAJC11 DnaJ (Hsp40) homolog, subfamily C, member 11 55735 ENSG00000007923
22  ENSG00000173141 NA MRP63 mitochondrial ribosomal protein 63 78988 ENSG00000173141
23  ENSG00000131828 NA PDHA1 pyruvate dehydrogenase (lipoamide) alpha 1 5160 ENSG00000131828
24  ENSG00000122971 NA ACADS acyl-CoA dehydrogenase, C-2 to C-3 short chain 35 ENSG00000122971
25  ENSG00000103356 NA EARS2 glutamyl-tRNA synthetase 2, mitochondrial (putative) 124454 ENSG00000103356
26  ENSG00000109390 NA NDUFC1 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa 4717 ENSG00000109390
27  ENSG00000182512 NA GLRX5 glutaredoxin 5 51218 ENSG00000182512
28  ENSG00000091483 NA FH fumarate hydratase 2271 ENSG00000091483
29  ENSG00000143314 NA MRPL24 mitochondrial ribosomal protein L24 79590 ENSG00000143314
30  ENSG00000103160 NA HSDL1 hydroxysteroid dehydrogenase like 1 83693 ENSG00000103160
31  ENSG00000055950 NA MRPL43 mitochondrial ribosomal protein L43 84545 ENSG00000055950
32  ENSG00000103642 NA LACTB lactamase, beta 114294 ENSG00000103642
33  ENSG00000110074 NA FOXRED1 FAD-dependent oxidoreductase domain containing 1 55572 ENSG00000110074
34  ENSG00000135070 NA ISCA1 iron-sulfur cluster assembly 1 homolog (S. cerevisiae) 81689 ENSG00000135070
35  ENSG00000142082 NA SIRT3 sirtuin 3 23410 ENSG00000142082
36  ENSG00000127838 NA PNKD paroxysmal nonkinesigenic dyskinesia 25953 ENSG00000127838
37  ENSG00000204568 NA MRPS18B mitochondrial ribosomal protein S18B 28973 ENSG00000204568
38  ENSG00000148334 NA PTGES2 prostaglandin E synthase 2 80142 ENSG00000148334
39  ENSG00000174374 NA WBSCR16 Williams-Beuren syndrome chromosome region 16 81554 ENSG00000174374
40  ENSG00000165283 NA STOML2 stomatin (EPB72)-like 2 30968 ENSG00000165283
41  ENSG00000164466 NA SFXN1 sideroflexin 1 94081 ENSG00000164466
42  ENSG00000151729 NA SLC25A4 solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4 291 ENSG00000151729
43  ENSG00000178057 NA NDUFAF3 NADH dehydrogenase (ubiquinone) complex I, assembly factor 3 25915 ENSG00000178057
44  ENSG00000126432 NA PRDX5 peroxiredoxin 5 25824 ENSG00000126432
45  ENSG00000023330 NA ALAS1 aminolevulinate, delta-, synthase 1 211 ENSG00000023330
46  ENSG00000183172 NA C22orf32 chromosome 22 open reading frame 32 91689 ENSG00000183172
47  ENSG00000213619 NA NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) 4722 ENSG00000213619
48  ENSG00000109180 NA OCIAD1 OCIA domain containing 1 54940 ENSG00000109180
49  ENSG00000178741 NA COX5A cytochrome c oxidase subunit Va 9377 ENSG00000178741
50  ENSG00000173660 NA UQCRH ubiquinol-cytochrome c reductase hinge protein 7388 ENSG00000173660
51  ENSG00000214253 NA FIS1 fission 1 (mitochondrial outer membrane) homolog (S. cerevisiae) 51024 ENSG00000214253
52  ENSG00000147586 NA MRPS28 mitochondrial ribosomal protein S28 28957 ENSG00000147586
53  ENSG00000133028 NA SCO1 SCO cytochrome oxidase deficient homolog 1 (yeast) 6341 ENSG00000133028
54  ENSG00000169288 NA MRPL1 mitochondrial ribosomal protein L1 65008 ENSG00000169288
55  ENSG00000100348 NA TXN2 thioredoxin 2 25828 ENSG00000100348
56  ENSG00000160221 NA C21orf33 chromosome 21 open reading frame 33 8209 ENSG00000160221
57  ENSG00000101181 NA GTPBP5 GTP binding protein 5 (putative) 26164 ENSG00000101181
58  ENSG00000109919 NA MTCH2 mitochondrial carrier 2 23788 ENSG00000109919
59  ENSG00000135940 NA COX5B cytochrome c oxidase subunit Vb 1329 ENSG00000135940
60  ENSG00000029639 NA TFB1M transcription factor B1, mitochondrial 51106 ENSG00000029639
61  ENSG00000135900 NA MRPL44 mitochondrial ribosomal protein L44 65080 ENSG00000135900
62  ENSG00000143436 NA MRPL9 mitochondrial ribosomal protein L9 65005 ENSG00000143436
63  ENSG00000239789 NA MRPS17 mitochondrial ribosomal protein S17 51373 ENSG00000239789
64  ENSG00000113790 NA EHHADH enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase 1962 ENSG00000113790
65  ENSG00000162851 NA TFB2M transcription factor B2, mitochondrial 64216 ENSG00000162851
66  ENSG00000122140 NA MRPS2 mitochondrial ribosomal protein S2 51116 ENSG00000122140
67  ENSG00000156709 NA AIFM1 apoptosis-inducing factor, mitochondrion-associated, 1 9131 ENSG00000156709
68  ENSG00000082515 NA MRPL22 mitochondrial ribosomal protein L22 29093 ENSG00000082515
69  ENSG00000189043 NA NDUFA4 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa 4697 ENSG00000189043
70  ENSG00000172115 NA CYCS cytochrome c, somatic 54205 ENSG00000172115
71  ENSG00000176894 NA PXMP2 peroxisomal membrane protein 2, 22kDa 5827 ENSG00000176894
72  ENSG00000035141 NA FAM136A family with sequence similarity 136, member A 84908 ENSG00000035141
73  ENSG00000164919 NA COX6C cytochrome c oxidase subunit VIc 1345 ENSG00000164919
74  ENSG00000139131 NA YARS2 tyrosyl-tRNA synthetase 2, mitochondrial 51067 ENSG00000139131
75  ENSG00000115286 NA NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) 374291 ENSG00000115286
76  ENSG00000164258 NA NDUFS4 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) 4724 ENSG00000164258
77  ENSG00000132570 NA PCBD2 pterin-4 alpha-carbinolamine dehydratase/dimerization cofactor of hepatocyte nuclear factor 1 alpha (TCF1) 2 84105 ENSG00000132570
78  ENSG00000156170 NA NDUFAF6 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 137682 ENSG00000156170
79  ENSG00000155463 NA OXA1L oxidase (cytochrome c) assembly 1-like 5018 ENSG00000155463
80  ENSG00000167863 NA ATP5H ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d 10476 ENSG00000167863
81  ENSG00000163319 NA MRPS18C mitochondrial ribosomal protein S18C 51023 ENSG00000163319
82  ENSG00000166165 NA CKB creatine kinase, brain 1152 ENSG00000166165
83  ENSG00000179091 NA CYC1 cytochrome c-1 1537 ENSG00000179091
84  ENSG00000185608 NA MRPL40 mitochondrial ribosomal protein L40 64976 ENSG00000185608
85  ENSG00000127540 NA UQCR11 ubiquinol-cytochrome c reductase, complex III subunit XI 10975 ENSG00000127540
86  ENSG00000197345 NA MRPL21 mitochondrial ribosomal protein L21 219927 ENSG00000197345
87  ENSG00000184752 NA NDUFA12 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 55967 ENSG00000184752
88  ENSG00000132423 NA COQ3 coenzyme Q3 homolog, methyltransferase (S. cerevisiae) 51805 ENSG00000132423
89  ENSG00000171861 NA RNMTL1 RNA methyltransferase like 1 55178 ENSG00000171861
90  ENSG00000156411 NA C14orf2 chromosome 14 open reading frame 2 9556 ENSG00000156411
91  ENSG00000131844 NA MCCC2 methylcrotonoyl-CoA carboxylase 2 (beta) 64087 ENSG00000131844
92  ENSG00000134905 NA CARS2 cysteinyl-tRNA synthetase 2, mitochondrial (putative) 79587 ENSG00000134905
93  ENSG00000182810 NA DDX28 DEAD (Asp-Glu-Ala-Asp) box polypeptide 28 55794 ENSG00000182810
94  ENSG00000105819 NA PMPCB peptidase (mitochondrial processing) beta 9512 ENSG00000105819
95  ENSG00000150779 NA TIMM8B translocase of inner mitochondrial membrane 8 homolog B (yeast) 26521 ENSG00000150779
96  ENSG00000204228 NA HSD17B8 hydroxysteroid (17-beta) dehydrogenase 8 7923 ENSG00000204228
97  ENSG00000196683 NA TOMM7 translocase of outer mitochondrial membrane 7 homolog (yeast) 54543 ENSG00000196683
98  ENSG00000179152 NA TCAIM T cell activation inhibitor, mitochondrial 285343 ENSG00000179152
99  ENSG00000175198 NA PCCA propionyl CoA carboxylase, alpha polypeptide 5095 ENSG00000175198
100  ENSG00000067829 NA IDH3G isocitrate dehydrogenase 3 (NAD+) gamma 3421 ENSG00000067829
101  ENSG00000166902 NA MRPL16 mitochondrial ribosomal protein L16 54948 ENSG00000166902
102  ENSG00000067225 NA PKM pyruvate kinase, muscle 5315 ENSG00000067225
103  ENSG00000114023 NA FAM162A family with sequence similarity 162, member A 26355 ENSG00000114023
104  ENSG00000157326 NA DHRS4 dehydrogenase/reductase (SDR family) member 4 10901 ENSG00000157326
105  ENSG00000140990 NA NDUFB10 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa 4716 ENSG00000140990
106  ENSG00000135297 NA MTO1 mitochondrial translation optimization 1 homolog (S. cerevisiae) 25821 ENSG00000135297
107  ENSG00000144182 NA LIPT1 lipoyltransferase 1 51601 ENSG00000144182
108  ENSG00000198523 NA PLN phospholamban 5350 ENSG00000198523
109  ENSG00000006530 NA AGK acylglycerol kinase 55750 ENSG00000006530
110  ENSG00000120662 NA MTRF1 mitochondrial translational release factor 1 9617 ENSG00000120662
111  ENSG00000247626 NA MARS2 methionyl-tRNA synthetase 2, mitochondrial 92935 ENSG00000247626
112  ENSG00000126602 NA TRAP1 TNF receptor-associated protein 1 10131 ENSG00000126602
113  ENSG00000243147 NA MRPL33 mitochondrial ribosomal protein L33 9553 ENSG00000243147
114  ENSG00000165629 NA ATP5C1 ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 509 ENSG00000165629
115  ENSG00000224877 NA C17orf89 chromosome 17 open reading frame 89 284184 ENSG00000224877
116  ENSG00000143653 NA SCCPDH saccharopine dehydrogenase (putative) 51097 ENSG00000143653
117  ENSG00000116906 NA GNPAT glyceronephosphate O-acyltransferase 8443 ENSG00000116906
118  ENSG00000123545 NA NDUFAF4 NADH dehydrogenase (ubiquinone) complex I, assembly factor 4 29078 ENSG00000123545
119  ENSG00000148290 NA SURF1 surfeit 1 6834 ENSG00000148290
120  ENSG00000170634 NA ACYP2 acylphosphatase 2, muscle type 98 ENSG00000170634
121  ENSG00000133315 NA MACROD1 MACRO domain containing 1 28992 ENSG00000133315
122  ENSG00000072778 NA ACADVL acyl-CoA dehydrogenase, very long chain 37 ENSG00000072778
123  ENSG00000154930 NA ACSS1 acyl-CoA synthetase short-chain family member 1 84532 ENSG00000154930
124  ENSG00000125652 NA ALKBH7 alkB, alkylation repair homolog 7 (E. coli) 84266 ENSG00000125652
125  ENSG00000049883 NA PTCD2 pentatricopeptide repeat domain 2 79810 ENSG00000049883
126  ENSG00000196636 NA ACN9 ACN9 homolog (S. cerevisiae) 57001 ENSG00000196636
127  ENSG00000139410 NA SDSL serine dehydratase-like 113675 ENSG00000139410
128  ENSG00000059691 NA PET112 PET112 homolog (yeast) 5188 ENSG00000059691
129  ENSG00000160124 NA CCDC58 coiled-coil domain containing 58 131076 ENSG00000160124
130  ENSG00000125995 NA ROMO1 reactive oxygen species modulator 1 140823 ENSG00000125995
131  ENSG00000136521 NA NDUFB5 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa 4711 ENSG00000136521
132  ENSG00000169020 NA ATP5I ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E 521 ENSG00000169020
133  ENSG00000114021 NA NIT2 nitrilase family, member 2 56954 ENSG00000114021
134  ENSG00000004779 NA NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa 4706 ENSG00000004779
135  ENSG00000182054 NA IDH2 isocitrate dehydrogenase 2 (NADP+), mitochondrial 3418 ENSG00000182054
136  ENSG00000168958 NA MFF mitochondrial fission factor 56947 ENSG00000168958
137  ENSG00000004961 NA HCCS holocytochrome c synthase 3052 ENSG00000004961
138  ENSG00000165898 NA ISCA2 iron-sulfur cluster assembly 2 homolog (S. cerevisiae) 122961 ENSG00000165898
139  ENSG00000073578 NA SDHA succinate dehydrogenase complex, subunit A, flavoprotein (Fp) 6389 ENSG00000073578
140  ENSG00000119013 NA NDUFB3 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa 4709 ENSG00000119013
141  ENSG00000151413 NA NUBPL nucleotide binding protein-like 80224 ENSG00000151413
142  ENSG00000213965 NA NUDT19 nudix (nucleoside diphosphate linked moiety X)-type motif 19 390916 ENSG00000213965
143  ENSG00000104325 NA DECR1 2,4-dienoyl CoA reductase 1, mitochondrial 1666 ENSG00000104325
144  ENSG00000132463 NA GRSF1 G-rich RNA sequence binding factor 1 2926 ENSG00000132463
145  ENSG00000259494 NA MRPL46 mitochondrial ribosomal protein L46 26589 ENSG00000259494
146  ENSG00000113048 NA MRPS27 mitochondrial ribosomal protein S27 23107 ENSG00000113048
147  ENSG00000165487 NA EFHA1 EF-hand domain family, member A1 221154 ENSG00000165487
148  ENSG00000078668 NA VDAC3 voltage-dependent anion channel 3 7419 ENSG00000078668
149  ENSG00000182154 NA MRPL41 mitochondrial ribosomal protein L41 64975 ENSG00000182154
150  ENSG00000144827 NA ABHD10 abhydrolase domain containing 10 55347 ENSG00000144827
151  ENSG00000167468 NA GPX4 glutathione peroxidase 4 2879 ENSG00000167468
152  ENSG00000139180 NA NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa 4704 ENSG00000139180
153  ENSG00000127184 NA COX7C cytochrome c oxidase subunit VIIc 1350 ENSG00000127184
154  ENSG00000085760 NA MTIF2 mitochondrial translational initiation factor 2 4528 ENSG00000085760
155  ENSG00000165637 NA VDAC2 voltage-dependent anion channel 2 7417 ENSG00000165637
156  ENSG00000187118 NA CMC1 COX assembly mitochondrial protein 1 homolog (S. cerevisiae) 152100 ENSG00000187118
157  ENSG00000172878 NA METAP1D methionyl aminopeptidase type 1D (mitochondrial) 254042 ENSG00000172878
158  ENSG00000204370 NA SDHD succinate dehydrogenase complex, subunit D, integral membrane protein 6392 ENSG00000204370
159  ENSG00000106554 NA CHCHD3 coiled-coil-helix-coiled-coil-helix domain containing 3 54927 ENSG00000106554
160  ENSG00000086504 NA MRPL28 mitochondrial ribosomal protein L28 10573 ENSG00000086504
161  ENSG00000108384 NA RAD51C RAD51 homolog C (S. cerevisiae) 5889 ENSG00000108384
162  ENSG00000162910 NA MRPL55 mitochondrial ribosomal protein L55 128308 ENSG00000162910
163  ENSG00000130349 NA C6orf203 chromosome 6 open reading frame 203 51250 ENSG00000130349
164  ENSG00000027001 NA MIPEP mitochondrial intermediate peptidase 4285 ENSG00000027001
165  ENSG00000111271 NA ACAD10 acyl-CoA dehydrogenase family, member 10 80724 ENSG00000111271
166  ENSG00000103423 NA DNAJA3 DnaJ (Hsp40) homolog, subfamily A, member 3 9093 ENSG00000103423
167  ENSG00000138777 NA PPA2 pyrophosphatase (inorganic) 2 27068 ENSG00000138777
168  ENSG00000100601 NA ALKBH1 alkB, alkylation repair homolog 1 (E. coli) 8846 ENSG00000100601
169  ENSG00000182180 NA MRPS16 mitochondrial ribosomal protein S16 51021 ENSG00000182180
170  ENSG00000174032 NA SLC25A30 solute carrier family 25, member 30 253512 ENSG00000174032
171  ENSG00000136522 NA MRPL47 mitochondrial ribosomal protein L47 57129 ENSG00000136522
172  ENSG00000175756 NA AURKAIP1 aurora kinase A interacting protein 1 54998 ENSG00000175756
173  ENSG00000135972 NA MRPS9 mitochondrial ribosomal protein S9 64965 ENSG00000135972
174  ENSG00000023228 NA NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) 4719 ENSG00000023228
175  ENSG00000143252 NA SDHC succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa 6391 ENSG00000143252
176  ENSG00000100116 NA GCAT glycine C-acetyltransferase 23464 ENSG00000100116
177  ENSG00000151376 NA ME3 malic enzyme 3, NADP(+)-dependent, mitochondrial 10873 ENSG00000151376
178  ENSG00000165775 NA FUNDC2 FUN14 domain containing 2 65991 ENSG00000165775
179  ENSG00000182606 NA TRAK1 trafficking protein, kinesin binding 1 22906 ENSG00000182606
180  ENSG00000115840 NA SLC25A12 solute carrier family 25 (aspartate/glutamate carrier), member 12 8604 ENSG00000115840
181  ENSG00000145982 NA FARS2 phenylalanyl-tRNA synthetase 2, mitochondrial 10667 ENSG00000145982
182  ENSG00000121897 NA LIAS lipoic acid synthetase 11019 ENSG00000121897
183  ENSG00000110955 NA ATP5B ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide 506 ENSG00000110955
184  ENSG00000197122 NA SRC v-src sarcoma (Schmidt-Ruppin A-2) viral oncogene homolog (avian) 6714 ENSG00000197122
185  ENSG00000112695 NA COX7A2 cytochrome c oxidase subunit VIIa polypeptide 2 (liver) 1347 ENSG00000112695
186  ENSG00000083720 NA OXCT1 3-oxoacid CoA transferase 1 5019 ENSG00000083720
187  ENSG00000131495 NA NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa 4695 ENSG00000131495
188  ENSG00000065518 NA NDUFB4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa 4710 ENSG00000065518
189  ENSG00000095321 NA CRAT carnitine O-acetyltransferase 1384 ENSG00000095321
190  ENSG00000159445 NA THEM4 thioesterase superfamily member 4 117145 ENSG00000159445
191  ENSG00000165688 NA PMPCA peptidase (mitochondrial processing) alpha 23203 ENSG00000165688
192  ENSG00000120992 NA LYPLA1 lysophospholipase I 10434 ENSG00000120992
193  ENSG00000198721 NA ECI2 enoyl-CoA delta isomerase 2 10455 ENSG00000198721
194  ENSG00000183617 NA MRPL54 mitochondrial ribosomal protein L54 116541 ENSG00000183617
195  ENSG00000112855 NA HARS2 histidyl-tRNA synthetase 2, mitochondrial 23438 ENSG00000112855
196  ENSG00000197580 NA BCO2 beta-carotene oxygenase 2 83875 ENSG00000197580
197  ENSG00000147853 NA AK3 adenylate kinase 3 50808 ENSG00000147853
198  ENSG00000131174 NA COX7B cytochrome c oxidase subunit VIIb 1349 ENSG00000131174
199  ENSG00000119705 NA SLIRP SRA stem-loop interacting RNA binding protein 81892 ENSG00000119705
200  ENSG00000205309 NA NT5M 5',3'-nucleotidase, mitochondrial 56953 ENSG00000205309
201  ENSG00000170906 NA NDUFA3 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa 4696 ENSG00000170906
202  ENSG00000128654 NA MTX2 metaxin 2 10651 ENSG00000128654
203  ENSG00000111716 NA LDHB lactate dehydrogenase B 3945 ENSG00000111716
204  ENSG00000112304 NA ACOT13 acyl-CoA thioesterase 13 55856 ENSG00000112304
205  ENSG00000167283 NA ATP5L ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G 10632 ENSG00000167283
206  ENSG00000114054 NA PCCB propionyl CoA carboxylase, beta polypeptide 5096 ENSG00000114054
207  ENSG00000069509 NA FUNDC1 FUN14 domain containing 1 139341 ENSG00000069509
208  ENSG00000167799 NA NUDT8 nudix (nucleoside diphosphate linked moiety X)-type motif 8 254552 ENSG00000167799
209  ENSG00000111275 NA ALDH2 aldehyde dehydrogenase 2 family (mitochondrial) 217 ENSG00000111275
210  ENSG00000171202 NA TMEM126A transmembrane protein 126A 84233 ENSG00000171202
211  ENSG00000124532 NA MRS2 MRS2 magnesium homeostasis factor homolog (S. cerevisiae) 57380 ENSG00000124532
212  ENSG00000136270 NA TBRG4 transforming growth factor beta regulator 4 9238 ENSG00000136270
213  ENSG00000048544 NA MRPS10 mitochondrial ribosomal protein S10 55173 ENSG00000048544
214  ENSG00000051620 NA HEBP2 heme binding protein 2 23593 ENSG00000051620
215  ENSG00000131269 NA ABCB7 ATP-binding cassette, sub-family B (MDR/TAP), member 7 22 ENSG00000131269
216  ENSG00000010256 NA UQCRC1 ubiquinol-cytochrome c reductase core protein I 7384 ENSG00000010256
217  ENSG00000137806 NA NDUFAF1 NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 51103 ENSG00000137806
218  ENSG00000104823 NA ECH1 enoyl CoA hydratase 1, peroxisomal 1891 ENSG00000104823
219  ENSG00000197912 NA SPG7 spastic paraplegia 7 (pure and complicated autosomal recessive) 6687 ENSG00000197912
220  ENSG00000171503 NA ETFDH electron-transferring-flavoprotein dehydrogenase 2110 ENSG00000171503
221  ENSG00000138796 NA HADH hydroxyacyl-CoA dehydrogenase 3033 ENSG00000138796
222  ENSG00000165672 NA PRDX3 peroxiredoxin 3 10935 ENSG00000165672
223  ENSG00000154518 NA ATP5G3 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C3 (subunit 9) 518 ENSG00000154518
224  ENSG00000101132 NA PFDN4 prefoldin subunit 4 5203 ENSG00000101132
225  ENSG00000088682 NA COQ9 coenzyme Q9 homolog (S. cerevisiae) 57017 ENSG00000088682
226  ENSG00000161533 NA ACOX1 acyl-CoA oxidase 1, palmitoyl 51 ENSG00000161533
227  ENSG00000075303 NA SLC25A40 solute carrier family 25, member 40 55972 ENSG00000075303
228  ENSG00000155368 NA DBI diazepam binding inhibitor (GABA receptor modulator, acyl-CoA binding protein) 1622 ENSG00000155368
229  ENSG00000163382 NA APOA1BP apolipoprotein A-I binding protein 128240 ENSG00000163382
230  ENSG00000126768 NA TIMM17B translocase of inner mitochondrial membrane 17 homolog B (yeast) 10245 ENSG00000126768
231  ENSG00000154237 NA LRRK1 leucine-rich repeat kinase 1 79705 ENSG00000154237
232  ENSG00000168653 NA NDUFS5 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) 4725 ENSG00000168653
233  ENSG00000247077 NA PGAM5 phosphoglycerate mutase family member 5 192111 ENSG00000247077
234  ENSG00000101019 NA UQCC ubiquinol-cytochrome c reductase complex chaperone 55245 ENSG00000101019
235  ENSG00000184903 NA IMMP2L IMP2 inner mitochondrial membrane peptidase-like (S. cerevisiae) 83943 ENSG00000184903
236  ENSG00000087299 NA L2HGDH L-2-hydroxyglutarate dehydrogenase 79944 ENSG00000087299
237  ENSG00000163864 NA NMNAT3 nicotinamide nucleotide adenylyltransferase 3 349565 ENSG00000163864
238  ENSG00000136463 NA TACO1 translational activator of mitochondrially encoded cytochrome c oxidase I 51204 ENSG00000136463
239  ENSG00000156467 NA UQCRB ubiquinol-cytochrome c reductase binding protein 7381 ENSG00000156467
240  ENSG00000103316 NA CRYM crystallin, mu 1428 ENSG00000103316
241  ENSG00000184076 NA UQCR10 ubiquinol-cytochrome c reductase, complex III subunit X 29796 ENSG00000184076
242  ENSG00000123297 NA TSFM Ts translation elongation factor, mitochondrial 10102 ENSG00000123297
243  ENSG00000078070 NA MCCC1 methylcrotonoyl-CoA carboxylase 1 (alpha) 56922 ENSG00000078070
244  ENSG00000075415 NA SLC25A3 solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 3 5250 ENSG00000075415
245  ENSG00000156885 NA COX6A2 cytochrome c oxidase subunit VIa polypeptide 2 1339 ENSG00000156885
246  ENSG00000006695 NA COX10 COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) 1352 ENSG00000006695
247  ENSG00000154723 NA ATP5J ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 522 ENSG00000154723
248  ENSG00000133983 NA COX16 COX16 cytochrome c oxidase assembly homolog (S. cerevisiae) 51241 ENSG00000133983
249  ENSG00000167969 NA ECI1 enoyl-CoA delta isomerase 1 1632 ENSG00000167969
250  ENSG00000115364 NA MRPL19 mitochondrial ribosomal protein L19 9801 ENSG00000115364
251  ENSG00000123472 NA ATPAF1 ATP synthase mitochondrial F1 complex assembly factor 1 64756 ENSG00000123472
252  ENSG00000105552 NA BCAT2 branched chain amino-acid transaminase 2, mitochondrial 587 ENSG00000105552
253  ENSG00000112996 NA MRPS30 mitochondrial ribosomal protein S30 10884 ENSG00000112996
254  ENSG00000139531 NA SUOX sulfite oxidase 6821 ENSG00000139531
255  ENSG00000100347 NA SAMM50 sorting and assembly machinery component 50 homolog (S. cerevisiae) 25813 ENSG00000100347
256  ENSG00000125166 NA GOT2 glutamic-oxaloacetic transaminase 2, mitochondrial (aspartate aminotransferase 2) 2806 ENSG00000125166
257  ENSG00000161558 NA TMEM143 transmembrane protein 143 55260 ENSG00000161558
258  ENSG00000140374 NA ETFA electron-transfer-flavoprotein, alpha polypeptide 2108 ENSG00000140374
259  ENSG00000140740 NA UQCRC2 ubiquinol-cytochrome c reductase core protein II 7385 ENSG00000140740
260  ENSG00000160194 NA NDUFV3 NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa 4731 ENSG00000160194
261  ENSG00000147684 NA NDUFB9 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa 4715 ENSG00000147684
262  ENSG00000169599 NA NFU1 NFU1 iron-sulfur cluster scaffold homolog (S. cerevisiae) 27247 ENSG00000169599
263  ENSG00000184983 NA NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa 4700 ENSG00000184983
264  ENSG00000102309 NA PIN4 protein (peptidylprolyl cis/trans isomerase) NIMA-interacting, 4 (parvulin) 5303 ENSG00000102309
265  ENSG00000163626 NA COX18 COX18 cytochrome c oxidase assembly homolog (S. cerevisiae) 285521 ENSG00000163626
266  ENSG00000158864 NA NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) 4720 ENSG00000158864
267  ENSG00000173436 NA MINOS1 mitochondrial inner membrane organizing system 1 440574 ENSG00000173436
268  ENSG00000105197 NA TIMM50 translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae) 92609 ENSG00000105197
269  ENSG00000135537 NA LACE1 lactation elevated 1 246269 ENSG00000135537
270  ENSG00000116221 NA MRPL37 mitochondrial ribosomal protein L37 51253 ENSG00000116221
271  ENSG00000142168 NA SOD1 superoxide dismutase 1, soluble 6647 ENSG00000142168
272  ENSG00000109519 NA GRPEL1 GrpE-like 1, mitochondrial (E. coli) 80273 ENSG00000109519
273  ENSG00000262814 NA MRPL12 mitochondrial ribosomal protein L12 6182 ENSG00000262814
274  ENSG00000076043 NA REXO2 REX2, RNA exonuclease 2 homolog (S. cerevisiae) 25996 ENSG00000076043
275  ENSG00000096080 NA MRPS18A mitochondrial ribosomal protein S18A 55168 ENSG00000096080
276  ENSG00000069998 NA CECR5 cat eye syndrome chromosome region, candidate 5 27440 ENSG00000069998
277  ENSG00000120254 NA MTHFD1L methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 1-like 25902 ENSG00000120254
278  ENSG00000134056 NA MRPS36 mitochondrial ribosomal protein S36 92259 ENSG00000134056
279  ENSG00000119689 NA DLST dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex) 1743 ENSG00000119689
280  ENSG00000168291 NA PDHB pyruvate dehydrogenase (lipoamide) beta 5162 ENSG00000168291
281  ENSG00000156502 NA SUPV3L1 suppressor of var1, 3-like 1 (S. cerevisiae) 6832 ENSG00000156502
282  ENSG00000060762 NA MPC1 mitochondrial pyruvate carrier 1 51660 ENSG00000060762
283  ENSG00000116459 NA ATP5F1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 515 ENSG00000116459
284  ENSG00000104980 NA TIMM44 translocase of inner mitochondrial membrane 44 homolog (yeast) 10469 ENSG00000104980
285  ENSG00000187145 NA MRPS21 mitochondrial ribosomal protein S21 54460 ENSG00000187145
286  ENSG00000099800 NA TIMM13 translocase of inner mitochondrial membrane 13 homolog (yeast) 26517 ENSG00000099800
287  ENSG00000138399 NA FASTKD1 FAST kinase domains 1 79675 ENSG00000138399
288  ENSG00000107951 NA MTPAP mitochondrial poly(A) polymerase 55149 ENSG00000107951
289  ENSG00000112992 NA NNT nicotinamide nucleotide transhydrogenase 23530 ENSG00000112992
290  ENSG00000067704 NA IARS2 isoleucyl-tRNA synthetase 2, mitochondrial 55699 ENSG00000067704
291  ENSG00000215251 NA FASTKD5 FAST kinase domains 5 60493 ENSG00000215251
292  ENSG00000130348 NA QRSL1 glutaminyl-tRNA synthase (glutamine-hydrolyzing)-like 1 55278 ENSG00000130348
293  ENSG00000148950 NA IMMP1L IMP1 inner mitochondrial membrane peptidase-like (S. cerevisiae) 196294 ENSG00000148950
294  ENSG00000119421 NA NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa 4702 ENSG00000119421
295  ENSG00000170502 NA NUDT9 nudix (nucleoside diphosphate linked moiety X)-type motif 9 53343 ENSG00000170502
296  ENSG00000137288 NA MNF1 mitochondrial nucleoid factor 1 84300 ENSG00000137288
297  ENSG00000130347 NA RTN4IP1 reticulon 4 interacting protein 1 84816 ENSG00000130347
298  ENSG00000172172 NA MRPL13 mitochondrial ribosomal protein L13 28998 ENSG00000172172
299  ENSG00000244005 NA NFS1 NFS1 nitrogen fixation 1 homolog (S. cerevisiae) 9054 ENSG00000244005
300  ENSG00000126267 NA COX6B1 cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) 1340 ENSG00000126267
301  ENSG00000154814 NA OXNAD1 oxidoreductase NAD-binding domain containing 1 92106 ENSG00000154814
302  ENSG00000103121 NA CMC2 COX assembly mitochondrial protein 2 homolog (S. cerevisiae) 56942 ENSG00000103121
303  ENSG00000148450 NA MSRB2 methionine sulfoxide reductase B2 22921 ENSG00000148450
304  ENSG00000170791 NA CHCHD7 coiled-coil-helix-coiled-coil-helix domain containing 7 79145 ENSG00000170791
305  ENSG00000215021 NA PHB2 prohibitin 2 11331 ENSG00000215021
306  ENSG00000145494 NA NDUFS6 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) 4726 ENSG00000145494
307  ENSG00000167085 NA PHB prohibitin 5245 ENSG00000167085
308  ENSG00000072506 NA HSD17B10 hydroxysteroid (17-beta) dehydrogenase 10 3028 ENSG00000072506
309  ENSG00000106153 NA CHCHD2 coiled-coil-helix-coiled-coil-helix domain containing 2 51142 ENSG00000106153
310  ENSG00000131143 NA COX4I1 cytochrome c oxidase subunit IV isoform 1 1327 ENSG00000131143
311  ENSG00000196236 NA XPNPEP3 X-prolyl aminopeptidase (aminopeptidase P) 3, putative 63929 ENSG00000196236
312  ENSG00000136444 NA RSAD1 radical S-adenosyl methionine domain containing 1 55316 ENSG00000136444
313  ENSG00000108561 NA C1QBP complement component 1, q subcomponent binding protein 708 ENSG00000108561
314  ENSG00000105379 NA ETFB electron-transfer-flavoprotein, beta polypeptide 2109 ENSG00000105379
315  ENSG00000213995 NA CARKD carbohydrate kinase domain containing 55739 ENSG00000213995
316  ENSG00000090266 NA NDUFB2 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa 4708 ENSG00000090266
317  ENSG00000230055 NA CISD3 CDGSH iron sulfur domain 3 284106 ENSG00000230055
318  ENSG00000175581 NA MRPL48 mitochondrial ribosomal protein L48 51642 ENSG00000175581
319  ENSG00000151498 NA ACAD8 acyl-CoA dehydrogenase family, member 8 27034 ENSG00000151498
320  ENSG00000156928 NA MALSU1 mitochondrial assembly of ribosomal large subunit 1 115416 ENSG00000156928
321  ENSG00000136143 NA SUCLA2 succinate-CoA ligase, ADP-forming, beta subunit 8803 ENSG00000136143
322  ENSG00000159199 NA ATP5G1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) 516 ENSG00000159199
323  ENSG00000166855 NA CLPX ClpX caseinolytic peptidase X homolog (E. coli) 10845 ENSG00000166855
324  ENSG00000090263 NA MRPS33 mitochondrial ribosomal protein S33 51650 ENSG00000090263
325  ENSG00000155906 NA RMND1 required for meiotic nuclear division 1 homolog (S. cerevisiae) 55005 ENSG00000155906
326  ENSG00000166321 NA NUDT13 nudix (nucleoside diphosphate linked moiety X)-type motif 13 25961 ENSG00000166321
327  ENSG00000130159 NA ECSIT ECSIT homolog (Drosophila) 51295 ENSG00000130159
328  ENSG00000074582 NA BCS1L BCS1-like (S. cerevisiae) 617 ENSG00000074582
329  ENSG00000122033 NA MTIF3 mitochondrial translational initiation factor 3 219402 ENSG00000122033
330  ENSG00000116171 NA SCP2 sterol carrier protein 2 6342 ENSG00000116171
331  ENSG00000104412 NA EMC2 ER membrane protein complex subunit 2 9694 ENSG00000104412
332  ENSG00000114383 NA TUSC2 tumor suppressor candidate 2 11334 ENSG00000114383
333  ENSG00000172590 NA MRPL52 mitochondrial ribosomal protein L52 122704 ENSG00000172590
334  ENSG00000140009 NA ESR2 estrogen receptor 2 (ER beta) 2100 ENSG00000140009
335  ENSG00000103018 NA CYB5B cytochrome b5 type B (outer mitochondrial membrane) 80777 ENSG00000103018
336  ENSG00000174917 NA C19orf70 chromosome 19 open reading frame 70 125988 ENSG00000174917
337  ENSG00000166816 NA LDHD lactate dehydrogenase D 197257 ENSG00000166816
338  ENSG00000143374 NA TARS2 threonyl-tRNA synthetase 2, mitochondrial (putative) 80222 ENSG00000143374
339  ENSG00000013275 NA PSMC4 proteasome (prosome, macropain) 26S subunit, ATPase, 4 5704 ENSG00000013275
340  ENSG00000132313 NA MRPL35 mitochondrial ribosomal protein L35 51318 ENSG00000132313
341  ENSG00000066926 NA FECH ferrochelatase 2235 ENSG00000066926
342  ENSG00000131779 NA PEX11B peroxisomal biogenesis factor 11 beta 8799 ENSG00000131779
343  ENSG00000138495 NA COX17 COX17 cytochrome c oxidase assembly homolog (S. cerevisiae) 10063 ENSG00000138495
344  ENSG00000117118 NA SDHB succinate dehydrogenase complex, subunit B, iron sulfur (Ip) 6390 ENSG00000117118
345  ENSG00000171953 NA ATPAF2 ATP synthase mitochondrial F1 complex assembly factor 2 91647 ENSG00000171953
346  ENSG00000168827 NA GFM1 G elongation factor, mitochondrial 1 85476 ENSG00000168827
347  ENSG00000135469 NA COQ10A coenzyme Q10 homolog A (S. cerevisiae) 93058 ENSG00000135469
348  ENSG00000177427 NA SMCR7 Smith-Magenis syndrome chromosome region, candidate 7 125170 ENSG00000177427
349  ENSG00000115944 NA COX7A2L cytochrome c oxidase subunit VIIa polypeptide 2 like 9167 ENSG00000115944
350  ENSG00000039560 NA RAI14 retinoic acid induced 14 26064 ENSG00000039560
351  ENSG00000100294 NA MCAT malonyl CoA:ACP acyltransferase (mitochondrial) 27349 ENSG00000100294
352  ENSG00000197150 NA ABCB8 ATP-binding cassette, sub-family B (MDR/TAP), member 8 11194 ENSG00000197150
353  ENSG00000152234 NA ATP5A1 ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle 498 ENSG00000152234
354  ENSG00000146729 NA GBAS glioblastoma amplified sequence 2631 ENSG00000146729
355  ENSG00000164494 NA PDSS2 prenyl (decaprenyl) diphosphate synthase, subunit 2 57107 ENSG00000164494
356  ENSG00000132763 NA MMACHC methylmalonic aciduria (cobalamin deficiency) cblC type, with homocystinuria 25974 ENSG00000132763
357  ENSG00000128609 NA NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa 4698 ENSG00000128609
358  ENSG00000151366 NA NDUFC2 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa 4718 ENSG00000151366
359  ENSG00000132305 NA IMMT inner membrane protein, mitochondrial 10989 ENSG00000132305
360  ENSG00000163541 NA SUCLG1 succinate-CoA ligase, alpha subunit 8802 ENSG00000163541
361  ENSG00000090432 NA MUL1 mitochondrial E3 ubiquitin protein ligase 1 79594 ENSG00000090432
362  ENSG00000165678 NA GHITM growth hormone inducible transmembrane protein 27069 ENSG00000165678
363  ENSG00000154719 NA MRPL39 mitochondrial ribosomal protein L39 54148 ENSG00000154719
364  ENSG00000146701 NA MDH2 malate dehydrogenase 2, NAD (mitochondrial) 4191 ENSG00000146701
365  ENSG00000173915 NA USMG5 up-regulated during skeletal muscle growth 5 homolog (mouse) 84833 ENSG00000173915
366  ENSG00000131730 NA CKMT2 creatine kinase, mitochondrial 2 (sarcomeric) 1160 ENSG00000131730
367  ENSG00000158882 NA TOMM40L translocase of outer mitochondrial membrane 40 homolog (yeast)-like 84134 ENSG00000158882
368  ENSG00000164038 NA SLC9B2 solute carrier family 9, subfamily B (NHA2, cation proton antiporter 2), member 2 133308 ENSG00000164038
369  ENSG00000147123 NA NDUFB11 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa 54539 ENSG00000147123
370  ENSG00000137714 NA FDX1 ferredoxin 1 2230 ENSG00000137714
371  ENSG00000169021 NA UQCRFS1 ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 7386 ENSG00000169021
372  ENSG00000115652 NA UXS1 UDP-glucuronate decarboxylase 1 80146 ENSG00000115652
373  ENSG00000136897 NA MRPL50 mitochondrial ribosomal protein L50 54534 ENSG00000136897
374  ENSG00000132541 NA HRSP12 heat-responsive protein 12 10247 ENSG00000132541
375  ENSG00000124523 NA SIRT5 sirtuin 5 23408 ENSG00000124523
376  ENSG00000102738 NA MRPS31 mitochondrial ribosomal protein S31 10240 ENSG00000102738
377  ENSG00000178449 NA COX14 COX14 cytochrome c oxidase assembly homolog (S. cerevisiae) 84987 ENSG00000178449
378  ENSG00000145439 NA CBR4 carbonyl reductase 4 84869 ENSG00000145439
379  ENSG00000130312 NA MRPL34 mitochondrial ribosomal protein L34 64981 ENSG00000130312
380  ENSG00000132300 NA PTCD3 pentatricopeptide repeat domain 3 55037 ENSG00000132300
381  ENSG00000062485 NA CS citrate synthase 1431 ENSG00000062485
382  ENSG00000175193 NA PARL presenilin associated, rhomboid-like 55486 ENSG00000175193
383  ENSG00000111843 NA TMEM14C transmembrane protein 14C 51522 ENSG00000111843
384  ENSG00000139428 NA MMAB methylmalonic aciduria (cobalamin deficiency) cblB type 326625 ENSG00000139428
385  ENSG00000185973 NA TMLHE trimethyllysine hydroxylase, epsilon 55217 ENSG00000185973
386  ENSG00000124370 NA MCEE methylmalonyl CoA epimerase 84693 ENSG00000124370
387  ENSG00000162600 NA OMA1 OMA1 zinc metallopeptidase homolog (S. cerevisiae) 115209 ENSG00000162600
388  ENSG00000108179 NA PPIF peptidylprolyl isomerase F 10105 ENSG00000108179
389  ENSG00000137513 NA NARS2 asparaginyl-tRNA synthetase 2, mitochondrial (putative) 79731 ENSG00000137513
390  ENSG00000137133 NA HINT2 histidine triad nucleotide binding protein 2 84681 ENSG00000137133
391  ENSG00000111639 NA MRPL51 mitochondrial ribosomal protein L51 51258 ENSG00000111639
392  ENSG00000164405 NA UQCRQ ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa 27089 ENSG00000164405
393  ENSG00000168569 NA TMEM223 transmembrane protein 223 79064 ENSG00000168569
394  ENSG00000122729 NA ACO1 aconitase 1, soluble 48 ENSG00000122729
395  ENSG00000173085 NA COQ2 coenzyme Q2 homolog, prenyltransferase (yeast) 27235 ENSG00000173085
396  ENSG00000148187 NA MRRF mitochondrial ribosome recycling factor 92399 ENSG00000148187
397  ENSG00000061794 NA MRPS35 mitochondrial ribosomal protein S35 60488 ENSG00000061794
398  ENSG00000124172 NA ATP5E ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit 514 ENSG00000124172
399  ENSG00000183648 NA NDUFB1 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa 4707 ENSG00000183648
400  ENSG00000132591 NA ERAL1 Era G-protein-like 1 (E. coli) 26284 ENSG00000132591
401  ENSG00000205981 NA DNAJC19 DnaJ (Hsp40) homolog, subfamily C, member 19 131118 ENSG00000205981
402  ENSG00000213585 NA VDAC1 voltage-dependent anion channel 1 7416 ENSG00000213585
403  ENSG00000120333 NA MRPS14 mitochondrial ribosomal protein S14 63931 ENSG00000120333
404  ENSG00000110435 NA PDHX pyruvate dehydrogenase complex, component X 8050 ENSG00000110435
405  ENSG00000184857 NA TMEM186 transmembrane protein 186 25880 ENSG00000184857
406  ENSG00000099624 NA ATP5D ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit 513 ENSG00000099624
407  ENSG00000100412 NA ACO2 aconitase 2, mitochondrial 50 ENSG00000100412
408  ENSG00000112651 NA MRPL2 mitochondrial ribosomal protein L2 51069 ENSG00000112651
409  ENSG00000132676 NA DAP3 death associated protein 3 7818 ENSG00000132676
410  ENSG00000164051 NA CCDC51 coiled-coil domain containing 51 79714 ENSG00000164051
411  ENSG00000181610 NA MRPS23 mitochondrial ribosomal protein S23 51649 ENSG00000181610
412  ENSG00000213563 NA C8orf82 chromosome 8 open reading frame 82 414919 ENSG00000213563
413  ENSG00000172586 NA CHCHD1 coiled-coil-helix-coiled-coil-helix domain containing 1 118487 ENSG00000172586
414  ENSG00000164896 NA FASTK Fas-activated serine/threonine kinase 10922 ENSG00000164896
415  ENSG00000125356 NA NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa 4694 ENSG00000125356
416  ENSG00000107020 NA PLGRKT plasminogen receptor, C-terminal lysine transmembrane protein 55848 ENSG00000107020
417  ENSG00000108528 NA SLC25A11 solute carrier family 25 (mitochondrial carrier; oxoglutarate carrier), member 11 8402 ENSG00000108528
418  ENSG00000129282 NA MRM1 mitochondrial rRNA methyltransferase 1 homolog (S. cerevisiae) 79922 ENSG00000129282
419  ENSG00000119673 NA ACOT2 acyl-CoA thioesterase 2 10965 ENSG00000119673
420  ENSG00000176422 NA SPRYD4 SPRY domain containing 4 283377 ENSG00000176422
421  ENSG00000099795 NA NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa 4713 ENSG00000099795
422  ENSG00000180185 NA FAHD1 fumarylacetoacetate hydrolase domain containing 1 81889 ENSG00000180185
423  ENSG00000044459 NA CNTLN centlein, centrosomal protein 54875 ENSG00000044459
424  ENSG00000103507 NA BCKDK branched chain ketoacid dehydrogenase kinase 10295 ENSG00000103507
425  ENSG00000148090 NA AUH AU RNA binding protein/enoyl-CoA hydratase 549 ENSG00000148090
426  ENSG00000198015 NA MRPL42 mitochondrial ribosomal protein L42 28977 ENSG00000198015
427  ENSG00000127989 NA MTERF mitochondrial transcription termination factor 7978 ENSG00000127989
428  ENSG00000125901 NA MRPS26 mitochondrial ribosomal protein S26 64949 ENSG00000125901
429  ENSG00000167136 NA ENDOG endonuclease G 2021 ENSG00000167136
430  ENSG00000075336 NA TIMM21 translocase of inner mitochondrial membrane 21 homolog (yeast) 29090 ENSG00000075336
431  ENSG00000133943 NA C14orf159 chromosome 14 open reading frame 159 80017 ENSG00000133943
432  ENSG00000172270 NA BSG basigin (Ok blood group) 682 ENSG00000172270
433  ENSG00000250479 NA CHCHD10 coiled-coil-helix-coiled-coil-helix domain containing 10 400916 ENSG00000250479
434  ENSG00000074071 NA MRPS34 mitochondrial ribosomal protein S34 65993 ENSG00000074071
435  ENSG00000164347 NA GFM2 G elongation factor, mitochondrial 2 84340 ENSG00000164347
436  ENSG00000111906 NA HDDC2 HD domain containing 2 51020 ENSG00000111906
437  ENSG00000119723 NA COQ6 coenzyme Q6 homolog, monooxygenase (S. cerevisiae) 51004 ENSG00000119723
438  ENSG00000181991 NA MRPS11 mitochondrial ribosomal protein S11 64963 ENSG00000181991
439  ENSG00000197894 NA ADH5 alcohol dehydrogenase 5 (class III), chi polypeptide 128 ENSG00000197894
440  ENSG00000175110 NA MRPS22 mitochondrial ribosomal protein S22 56945 ENSG00000175110
441  ENSG00000197448 NA GSTK1 glutathione S-transferase kappa 1 373156 ENSG00000197448
442  ENSG00000167792 NA NDUFV1 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa 4723 ENSG00000167792
443  ENSG00000110717 NA NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) 4728 ENSG00000110717
444  ENSG00000174547 NA MRPL11 mitochondrial ribosomal protein L11 65003 ENSG00000174547
445  ENSG00000137547 NA MRPL15 mitochondrial ribosomal protein L15 29088 ENSG00000137547
446  ENSG00000204308 NA RNF5 ring finger protein 5, E3 ubiquitin protein ligase 6048 ENSG00000204308
447  ENSG00000162972 NA C2orf47 chromosome 2 open reading frame 47 79568 ENSG00000162972
448  ENSG00000183978 NA COA3 cytochrome C oxidase assembly factor 3 28958 ENSG00000183978
449  ENSG00000121361 NA KCNJ8 potassium inwardly-rectifying channel, subfamily J, member 8 3764 ENSG00000121361
450  ENSG00000113845 NA TIMMDC1 translocase of inner mitochondrial membrane domain containing 1 51300 ENSG00000113845
451  ENSG00000127884 NA ECHS1 enoyl CoA hydratase, short chain, 1, mitochondrial 1892 ENSG00000127884
452  ENSG00000178952 NA TUFM Tu translation elongation factor, mitochondrial 7284 ENSG00000178952
453  ENSG00000241468 NA ATP5J2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 9551 ENSG00000241468
454  ENSG00000168273 NA C3orf78 chromosome 3 open reading frame 78 440957 ENSG00000168273
455  ENSG00000125445 NA MRPS7 mitochondrial ribosomal protein S7 51081 ENSG00000125445
456  ENSG00000105364 NA MRPL4 mitochondrial ribosomal protein L4 51073 ENSG00000105364
457  ENSG00000143158 NA MPC2 mitochondrial pyruvate carrier 2 25874 ENSG00000143158
458  ENSG00000113013 NA HSPA9 heat shock 70kDa protein 9 (mortalin) 3313 ENSG00000113013
459  ENSG00000110011 NA DNAJC4 DnaJ (Hsp40) homolog, subfamily C, member 4 3338 ENSG00000110011
460  ENSG00000176340 NA COX8A cytochrome c oxidase subunit VIIIA (ubiquitous) 1351 ENSG00000176340
461  ENSG00000144029 NA MRPS5 mitochondrial ribosomal protein S5 64969 ENSG00000144029
462  ENSG00000101247 NA NDUFAF5 NADH dehydrogenase (ubiquinone) complex I, assembly factor 5 79133 ENSG00000101247
463  ENSG00000050393 NA CCDC90A coiled-coil domain containing 90A 63933 ENSG00000050393
464  ENSG00000101365 NA IDH3B isocitrate dehydrogenase 3 (NAD+) beta 3420 ENSG00000101365
465  ENSG00000241837 NA ATP5O ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit 539 ENSG00000241837
466  ENSG00000140905 NA GCSH glycine cleavage system protein H (aminomethyl carrier) 2653 ENSG00000140905
467  ENSG00000214026 NA MRPL23 mitochondrial ribosomal protein L23 6150 ENSG00000214026
468  ENSG00000158793 NA NIT1 nitrilase 1 4817 ENSG00000158793


Database:cellular component       Name:mitochondrial part       ID:GO:0044429
C=744; O=281; E=45.16; R=6.22; rawP=1.45e-156; adjP=2.87e-154
Index UserID Value Gene Symbol Gene Name EntrezGene Ensembl
1  ENSG00000165264 NA NDUFB6 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa 4712 ENSG00000165264
2  ENSG00000116898 NA MRPS15 mitochondrial ribosomal protein S15 64960 ENSG00000116898
3  ENSG00000161281 NA COX7A1 cytochrome c oxidase subunit VIIa polypeptide 1 (muscle) 1346 ENSG00000161281
4  ENSG00000167862 NA ICT1 immature colon carcinoma transcript 1 3396 ENSG00000167862
5  ENSG00000148672 NA GLUD1 glutamate dehydrogenase 1 2746 ENSG00000148672
6  ENSG00000135390 NA ATP5G2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C2 (subunit 9) 517 ENSG00000135390
7  ENSG00000177370 NA TIMM22 translocase of inner mitochondrial membrane 22 homolog (yeast) 29928 ENSG00000177370
8  ENSG00000166136 NA NDUFB8 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa 4714 ENSG00000166136
9  ENSG00000172340 NA SUCLG2 succinate-CoA ligase, GDP-forming, beta subunit 8801 ENSG00000172340
10  ENSG00000091140 NA DLD dihydrolipoamide dehydrogenase 1738 ENSG00000091140
11  ENSG00000130414 NA NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa 4705 ENSG00000130414
12  ENSG00000165060 NA FXN frataxin 2395 ENSG00000165060
13  ENSG00000007923 NA DNAJC11 DnaJ (Hsp40) homolog, subfamily C, member 11 55735 ENSG00000007923
14  ENSG00000173141 NA MRP63 mitochondrial ribosomal protein 63 78988 ENSG00000173141
15  ENSG00000131828 NA PDHA1 pyruvate dehydrogenase (lipoamide) alpha 1 5160 ENSG00000131828
16  ENSG00000122971 NA ACADS acyl-CoA dehydrogenase, C-2 to C-3 short chain 35 ENSG00000122971
17  ENSG00000103356 NA EARS2 glutamyl-tRNA synthetase 2, mitochondrial (putative) 124454 ENSG00000103356
18  ENSG00000109390 NA NDUFC1 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa 4717 ENSG00000109390
19  ENSG00000091483 NA FH fumarate hydratase 2271 ENSG00000091483
20  ENSG00000055950 NA MRPL43 mitochondrial ribosomal protein L43 84545 ENSG00000055950
21  ENSG00000142082 NA SIRT3 sirtuin 3 23410 ENSG00000142082
22  ENSG00000204568 NA MRPS18B mitochondrial ribosomal protein S18B 28973 ENSG00000204568
23  ENSG00000165283 NA STOML2 stomatin (EPB72)-like 2 30968 ENSG00000165283
24  ENSG00000164466 NA SFXN1 sideroflexin 1 94081 ENSG00000164466
25  ENSG00000151729 NA SLC25A4 solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4 291 ENSG00000151729
26  ENSG00000178057 NA NDUFAF3 NADH dehydrogenase (ubiquinone) complex I, assembly factor 3 25915 ENSG00000178057
27  ENSG00000023330 NA ALAS1 aminolevulinate, delta-, synthase 1 211 ENSG00000023330
28  ENSG00000213619 NA NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) 4722 ENSG00000213619
29  ENSG00000178741 NA COX5A cytochrome c oxidase subunit Va 9377 ENSG00000178741
30  ENSG00000173660 NA UQCRH ubiquinol-cytochrome c reductase hinge protein 7388 ENSG00000173660
31  ENSG00000214253 NA FIS1 fission 1 (mitochondrial outer membrane) homolog (S. cerevisiae) 51024 ENSG00000214253
32  ENSG00000147586 NA MRPS28 mitochondrial ribosomal protein S28 28957 ENSG00000147586
33  ENSG00000133028 NA SCO1 SCO cytochrome oxidase deficient homolog 1 (yeast) 6341 ENSG00000133028
34  ENSG00000109919 NA MTCH2 mitochondrial carrier 2 23788 ENSG00000109919
35  ENSG00000135940 NA COX5B cytochrome c oxidase subunit Vb 1329 ENSG00000135940
36  ENSG00000029639 NA TFB1M transcription factor B1, mitochondrial 51106 ENSG00000029639
37  ENSG00000143436 NA MRPL9 mitochondrial ribosomal protein L9 65005 ENSG00000143436
38  ENSG00000239789 NA MRPS17 mitochondrial ribosomal protein S17 51373 ENSG00000239789
39  ENSG00000162851 NA TFB2M transcription factor B2, mitochondrial 64216 ENSG00000162851
40  ENSG00000156709 NA AIFM1 apoptosis-inducing factor, mitochondrion-associated, 1 9131 ENSG00000156709
41  ENSG00000189043 NA NDUFA4 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa 4697 ENSG00000189043
42  ENSG00000172115 NA CYCS cytochrome c, somatic 54205 ENSG00000172115
43  ENSG00000164919 NA COX6C cytochrome c oxidase subunit VIc 1345 ENSG00000164919
44  ENSG00000139131 NA YARS2 tyrosyl-tRNA synthetase 2, mitochondrial 51067 ENSG00000139131
45  ENSG00000115286 NA NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) 374291 ENSG00000115286
46  ENSG00000164258 NA NDUFS4 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) 4724 ENSG00000164258
47  ENSG00000156170 NA NDUFAF6 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 137682 ENSG00000156170
48  ENSG00000155463 NA OXA1L oxidase (cytochrome c) assembly 1-like 5018 ENSG00000155463
49  ENSG00000167863 NA ATP5H ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d 10476 ENSG00000167863
50  ENSG00000163319 NA MRPS18C mitochondrial ribosomal protein S18C 51023 ENSG00000163319
51  ENSG00000179091 NA CYC1 cytochrome c-1 1537 ENSG00000179091
52  ENSG00000185608 NA MRPL40 mitochondrial ribosomal protein L40 64976 ENSG00000185608
53  ENSG00000127540 NA UQCR11 ubiquinol-cytochrome c reductase, complex III subunit XI 10975 ENSG00000127540
54  ENSG00000184752 NA NDUFA12 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 55967 ENSG00000184752
55  ENSG00000132423 NA COQ3 coenzyme Q3 homolog, methyltransferase (S. cerevisiae) 51805 ENSG00000132423
56  ENSG00000156411 NA C14orf2 chromosome 14 open reading frame 2 9556 ENSG00000156411
57  ENSG00000131844 NA MCCC2 methylcrotonoyl-CoA carboxylase 2 (beta) 64087 ENSG00000131844
58  ENSG00000134905 NA CARS2 cysteinyl-tRNA synthetase 2, mitochondrial (putative) 79587 ENSG00000134905
59  ENSG00000182810 NA DDX28 DEAD (Asp-Glu-Ala-Asp) box polypeptide 28 55794 ENSG00000182810
60  ENSG00000105819 NA PMPCB peptidase (mitochondrial processing) beta 9512 ENSG00000105819
61  ENSG00000150779 NA TIMM8B translocase of inner mitochondrial membrane 8 homolog B (yeast) 26521 ENSG00000150779
62  ENSG00000204228 NA HSD17B8 hydroxysteroid (17-beta) dehydrogenase 8 7923 ENSG00000204228
63  ENSG00000196683 NA TOMM7 translocase of outer mitochondrial membrane 7 homolog (yeast) 54543 ENSG00000196683
64  ENSG00000175198 NA PCCA propionyl CoA carboxylase, alpha polypeptide 5095 ENSG00000175198
65  ENSG00000067829 NA IDH3G isocitrate dehydrogenase 3 (NAD+) gamma 3421 ENSG00000067829
66  ENSG00000140990 NA NDUFB10 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa 4716 ENSG00000140990
67  ENSG00000198523 NA PLN phospholamban 5350 ENSG00000198523
68  ENSG00000006530 NA AGK acylglycerol kinase 55750 ENSG00000006530
69  ENSG00000247626 NA MARS2 methionyl-tRNA synthetase 2, mitochondrial 92935 ENSG00000247626
70  ENSG00000165629 NA ATP5C1 ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 509 ENSG00000165629
71  ENSG00000123545 NA NDUFAF4 NADH dehydrogenase (ubiquinone) complex I, assembly factor 4 29078 ENSG00000123545
72  ENSG00000148290 NA SURF1 surfeit 1 6834 ENSG00000148290
73  ENSG00000072778 NA ACADVL acyl-CoA dehydrogenase, very long chain 37 ENSG00000072778
74  ENSG00000154930 NA ACSS1 acyl-CoA synthetase short-chain family member 1 84532 ENSG00000154930
75  ENSG00000196636 NA ACN9 ACN9 homolog (S. cerevisiae) 57001 ENSG00000196636
76  ENSG00000125995 NA ROMO1 reactive oxygen species modulator 1 140823 ENSG00000125995
77  ENSG00000136521 NA NDUFB5 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa 4711 ENSG00000136521
78  ENSG00000169020 NA ATP5I ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E 521 ENSG00000169020
79  ENSG00000182054 NA IDH2 isocitrate dehydrogenase 2 (NADP+), mitochondrial 3418 ENSG00000182054
80  ENSG00000004779 NA NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa 4706 ENSG00000004779
81  ENSG00000168958 NA MFF mitochondrial fission factor 56947 ENSG00000168958
82  ENSG00000004961 NA HCCS holocytochrome c synthase 3052 ENSG00000004961
83  ENSG00000073578 NA SDHA succinate dehydrogenase complex, subunit A, flavoprotein (Fp) 6389 ENSG00000073578
84  ENSG00000119013 NA NDUFB3 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa 4709 ENSG00000119013
85  ENSG00000104325 NA DECR1 2,4-dienoyl CoA reductase 1, mitochondrial 1666 ENSG00000104325
86  ENSG00000078668 NA VDAC3 voltage-dependent anion channel 3 7419 ENSG00000078668
87  ENSG00000182154 NA MRPL41 mitochondrial ribosomal protein L41 64975 ENSG00000182154
88  ENSG00000139180 NA NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa 4704 ENSG00000139180
89  ENSG00000127184 NA COX7C cytochrome c oxidase subunit VIIc 1350 ENSG00000127184
90  ENSG00000165637 NA VDAC2 voltage-dependent anion channel 2 7417 ENSG00000165637
91  ENSG00000204370 NA SDHD succinate dehydrogenase complex, subunit D, integral membrane protein 6392 ENSG00000204370
92  ENSG00000106554 NA CHCHD3 coiled-coil-helix-coiled-coil-helix domain containing 3 54927 ENSG00000106554
93  ENSG00000086504 NA MRPL28 mitochondrial ribosomal protein L28 10573 ENSG00000086504
94  ENSG00000162910 NA MRPL55 mitochondrial ribosomal protein L55 128308 ENSG00000162910
95  ENSG00000027001 NA MIPEP mitochondrial intermediate peptidase 4285 ENSG00000027001
96  ENSG00000103423 NA DNAJA3 DnaJ (Hsp40) homolog, subfamily A, member 3 9093 ENSG00000103423
97  ENSG00000138777 NA PPA2 pyrophosphatase (inorganic) 2 27068 ENSG00000138777
98  ENSG00000182180 NA MRPS16 mitochondrial ribosomal protein S16 51021 ENSG00000182180
99  ENSG00000174032 NA SLC25A30 solute carrier family 25, member 30 253512 ENSG00000174032
100  ENSG00000136522 NA MRPL47 mitochondrial ribosomal protein L47 57129 ENSG00000136522
101  ENSG00000135972 NA MRPS9 mitochondrial ribosomal protein S9 64965 ENSG00000135972
102  ENSG00000023228 NA NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) 4719 ENSG00000023228
103  ENSG00000143252 NA SDHC succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa 6391 ENSG00000143252
104  ENSG00000151376 NA ME3 malic enzyme 3, NADP(+)-dependent, mitochondrial 10873 ENSG00000151376
105  ENSG00000115840 NA SLC25A12 solute carrier family 25 (aspartate/glutamate carrier), member 12 8604 ENSG00000115840
106  ENSG00000145982 NA FARS2 phenylalanyl-tRNA synthetase 2, mitochondrial 10667 ENSG00000145982
107  ENSG00000110955 NA ATP5B ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide 506 ENSG00000110955
108  ENSG00000197122 NA SRC v-src sarcoma (Schmidt-Ruppin A-2) viral oncogene homolog (avian) 6714 ENSG00000197122
109  ENSG00000112695 NA COX7A2 cytochrome c oxidase subunit VIIa polypeptide 2 (liver) 1347 ENSG00000112695
110  ENSG00000083720 NA OXCT1 3-oxoacid CoA transferase 1 5019 ENSG00000083720
111  ENSG00000131495 NA NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa 4695 ENSG00000131495
112  ENSG00000065518 NA NDUFB4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa 4710 ENSG00000065518
113  ENSG00000095321 NA CRAT carnitine O-acetyltransferase 1384 ENSG00000095321
114  ENSG00000165688 NA PMPCA peptidase (mitochondrial processing) alpha 23203 ENSG00000165688
115  ENSG00000112855 NA HARS2 histidyl-tRNA synthetase 2, mitochondrial 23438 ENSG00000112855
116  ENSG00000147853 NA AK3 adenylate kinase 3 50808 ENSG00000147853
117  ENSG00000131174 NA COX7B cytochrome c oxidase subunit VIIb 1349 ENSG00000131174
118  ENSG00000205309 NA NT5M 5',3'-nucleotidase, mitochondrial 56953 ENSG00000205309
119  ENSG00000170906 NA NDUFA3 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa 4696 ENSG00000170906
120  ENSG00000128654 NA MTX2 metaxin 2 10651 ENSG00000128654
121  ENSG00000167283 NA ATP5L ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G 10632 ENSG00000167283
122  ENSG00000114054 NA PCCB propionyl CoA carboxylase, beta polypeptide 5096 ENSG00000114054
123  ENSG00000069509 NA FUNDC1 FUN14 domain containing 1 139341 ENSG00000069509
124  ENSG00000111275 NA ALDH2 aldehyde dehydrogenase 2 family (mitochondrial) 217 ENSG00000111275
125  ENSG00000124532 NA MRS2 MRS2 magnesium homeostasis factor homolog (S. cerevisiae) 57380 ENSG00000124532
126  ENSG00000131269 NA ABCB7 ATP-binding cassette, sub-family B (MDR/TAP), member 7 22 ENSG00000131269
127  ENSG00000010256 NA UQCRC1 ubiquinol-cytochrome c reductase core protein I 7384 ENSG00000010256
128  ENSG00000137806 NA NDUFAF1 NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 51103 ENSG00000137806
129  ENSG00000197912 NA SPG7 spastic paraplegia 7 (pure and complicated autosomal recessive) 6687 ENSG00000197912
130  ENSG00000171503 NA ETFDH electron-transferring-flavoprotein dehydrogenase 2110 ENSG00000171503
131  ENSG00000138796 NA HADH hydroxyacyl-CoA dehydrogenase 3033 ENSG00000138796
132  ENSG00000154518 NA ATP5G3 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C3 (subunit 9) 518 ENSG00000154518
133  ENSG00000075303 NA SLC25A40 solute carrier family 25, member 40 55972 ENSG00000075303
134  ENSG00000126768 NA TIMM17B translocase of inner mitochondrial membrane 17 homolog B (yeast) 10245 ENSG00000126768
135  ENSG00000168653 NA NDUFS5 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) 4725 ENSG00000168653
136  ENSG00000247077 NA PGAM5 phosphoglycerate mutase family member 5 192111 ENSG00000247077
137  ENSG00000184903 NA IMMP2L IMP2 inner mitochondrial membrane peptidase-like (S. cerevisiae) 83943 ENSG00000184903
138  ENSG00000087299 NA L2HGDH L-2-hydroxyglutarate dehydrogenase 79944 ENSG00000087299
139  ENSG00000156467 NA UQCRB ubiquinol-cytochrome c reductase binding protein 7381 ENSG00000156467
140  ENSG00000184076 NA UQCR10 ubiquinol-cytochrome c reductase, complex III subunit X 29796 ENSG00000184076
141  ENSG00000078070 NA MCCC1 methylcrotonoyl-CoA carboxylase 1 (alpha) 56922 ENSG00000078070
142  ENSG00000075415 NA SLC25A3 solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 3 5250 ENSG00000075415
143  ENSG00000156885 NA COX6A2 cytochrome c oxidase subunit VIa polypeptide 2 1339 ENSG00000156885
144  ENSG00000154723 NA ATP5J ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 522 ENSG00000154723
145  ENSG00000133983 NA COX16 COX16 cytochrome c oxidase assembly homolog (S. cerevisiae) 51241 ENSG00000133983
146  ENSG00000006695 NA COX10 COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) 1352 ENSG00000006695
147  ENSG00000167969 NA ECI1 enoyl-CoA delta isomerase 1 1632 ENSG00000167969
148  ENSG00000105552 NA BCAT2 branched chain amino-acid transaminase 2, mitochondrial 587 ENSG00000105552
149  ENSG00000139531 NA SUOX sulfite oxidase 6821 ENSG00000139531
150  ENSG00000100347 NA SAMM50 sorting and assembly machinery component 50 homolog (S. cerevisiae) 25813 ENSG00000100347
151  ENSG00000125166 NA GOT2 glutamic-oxaloacetic transaminase 2, mitochondrial (aspartate aminotransferase 2) 2806 ENSG00000125166
152  ENSG00000140374 NA ETFA electron-transfer-flavoprotein, alpha polypeptide 2108 ENSG00000140374
153  ENSG00000140740 NA UQCRC2 ubiquinol-cytochrome c reductase core protein II 7385 ENSG00000140740
154  ENSG00000147684 NA NDUFB9 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa 4715 ENSG00000147684
155  ENSG00000160194 NA NDUFV3 NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa 4731 ENSG00000160194
156  ENSG00000184983 NA NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa 4700 ENSG00000184983
157  ENSG00000102309 NA PIN4 protein (peptidylprolyl cis/trans isomerase) NIMA-interacting, 4 (parvulin) 5303 ENSG00000102309
158  ENSG00000158864 NA NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) 4720 ENSG00000158864
159  ENSG00000163626 NA COX18 COX18 cytochrome c oxidase assembly homolog (S. cerevisiae) 285521 ENSG00000163626
160  ENSG00000173436 NA MINOS1 mitochondrial inner membrane organizing system 1 440574 ENSG00000173436
161  ENSG00000105197 NA TIMM50 translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae) 92609 ENSG00000105197
162  ENSG00000116221 NA MRPL37 mitochondrial ribosomal protein L37 51253 ENSG00000116221
163  ENSG00000142168 NA SOD1 superoxide dismutase 1, soluble 6647 ENSG00000142168
164  ENSG00000109519 NA GRPEL1 GrpE-like 1, mitochondrial (E. coli) 80273 ENSG00000109519
165  ENSG00000262814 NA MRPL12 mitochondrial ribosomal protein L12 6182 ENSG00000262814
166  ENSG00000096080 NA MRPS18A mitochondrial ribosomal protein S18A 55168 ENSG00000096080
167  ENSG00000119689 NA DLST dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex) 1743 ENSG00000119689
168  ENSG00000134056 NA MRPS36 mitochondrial ribosomal protein S36 92259 ENSG00000134056
169  ENSG00000156502 NA SUPV3L1 suppressor of var1, 3-like 1 (S. cerevisiae) 6832 ENSG00000156502
170  ENSG00000168291 NA PDHB pyruvate dehydrogenase (lipoamide) beta 5162 ENSG00000168291
171  ENSG00000060762 NA MPC1 mitochondrial pyruvate carrier 1 51660 ENSG00000060762
172  ENSG00000116459 NA ATP5F1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 515 ENSG00000116459
173  ENSG00000104980 NA TIMM44 translocase of inner mitochondrial membrane 44 homolog (yeast) 10469 ENSG00000104980
174  ENSG00000187145 NA MRPS21 mitochondrial ribosomal protein S21 54460 ENSG00000187145
175  ENSG00000099800 NA TIMM13 translocase of inner mitochondrial membrane 13 homolog (yeast) 26517 ENSG00000099800
176  ENSG00000112992 NA NNT nicotinamide nucleotide transhydrogenase 23530 ENSG00000112992
177  ENSG00000067704 NA IARS2 isoleucyl-tRNA synthetase 2, mitochondrial 55699 ENSG00000067704
178  ENSG00000148950 NA IMMP1L IMP1 inner mitochondrial membrane peptidase-like (S. cerevisiae) 196294 ENSG00000148950
179  ENSG00000137288 NA MNF1 mitochondrial nucleoid factor 1 84300 ENSG00000137288
180  ENSG00000172172 NA MRPL13 mitochondrial ribosomal protein L13 28998 ENSG00000172172
181  ENSG00000119421 NA NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa 4702 ENSG00000119421
182  ENSG00000244005 NA NFS1 NFS1 nitrogen fixation 1 homolog (S. cerevisiae) 9054 ENSG00000244005
183  ENSG00000126267 NA COX6B1 cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) 1340 ENSG00000126267
184  ENSG00000215021 NA PHB2 prohibitin 2 11331 ENSG00000215021
185  ENSG00000167085 NA PHB prohibitin 5245 ENSG00000167085
186  ENSG00000145494 NA NDUFS6 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) 4726 ENSG00000145494
187  ENSG00000072506 NA HSD17B10 hydroxysteroid (17-beta) dehydrogenase 10 3028 ENSG00000072506
188  ENSG00000131143 NA COX4I1 cytochrome c oxidase subunit IV isoform 1 1327 ENSG00000131143
189  ENSG00000108561 NA C1QBP complement component 1, q subcomponent binding protein 708 ENSG00000108561
190  ENSG00000105379 NA ETFB electron-transfer-flavoprotein, beta polypeptide 2109 ENSG00000105379
191  ENSG00000090266 NA NDUFB2 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa 4708 ENSG00000090266
192  ENSG00000175581 NA MRPL48 mitochondrial ribosomal protein L48 51642 ENSG00000175581
193  ENSG00000151498 NA ACAD8 acyl-CoA dehydrogenase family, member 8 27034 ENSG00000151498
194  ENSG00000156928 NA MALSU1 mitochondrial assembly of ribosomal large subunit 1 115416 ENSG00000156928
195  ENSG00000159199 NA ATP5G1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) 516 ENSG00000159199
196  ENSG00000136143 NA SUCLA2 succinate-CoA ligase, ADP-forming, beta subunit 8803 ENSG00000136143
197  ENSG00000090263 NA MRPS33 mitochondrial ribosomal protein S33 51650 ENSG00000090263
198  ENSG00000166855 NA CLPX ClpX caseinolytic peptidase X homolog (E. coli) 10845 ENSG00000166855
199  ENSG00000074582 NA BCS1L BCS1-like (S. cerevisiae) 617 ENSG00000074582
200  ENSG00000172590 NA MRPL52 mitochondrial ribosomal protein L52 122704 ENSG00000172590
201  ENSG00000103018 NA CYB5B cytochrome b5 type B (outer mitochondrial membrane) 80777 ENSG00000103018
202  ENSG00000143374 NA TARS2 threonyl-tRNA synthetase 2, mitochondrial (putative) 80222 ENSG00000143374
203  ENSG00000166816 NA LDHD lactate dehydrogenase D 197257 ENSG00000166816
204  ENSG00000132313 NA MRPL35 mitochondrial ribosomal protein L35 51318 ENSG00000132313
205  ENSG00000066926 NA FECH ferrochelatase 2235 ENSG00000066926
206  ENSG00000117118 NA SDHB succinate dehydrogenase complex, subunit B, iron sulfur (Ip) 6390 ENSG00000117118
207  ENSG00000138495 NA COX17 COX17 cytochrome c oxidase assembly homolog (S. cerevisiae) 10063 ENSG00000138495
208  ENSG00000135469 NA COQ10A coenzyme Q10 homolog A (S. cerevisiae) 93058 ENSG00000135469
209  ENSG00000177427 NA SMCR7 Smith-Magenis syndrome chromosome region, candidate 7 125170 ENSG00000177427
210  ENSG00000115944 NA COX7A2L cytochrome c oxidase subunit VIIa polypeptide 2 like 9167 ENSG00000115944
211  ENSG00000197150 NA ABCB8 ATP-binding cassette, sub-family B (MDR/TAP), member 8 11194 ENSG00000197150
212  ENSG00000152234 NA ATP5A1 ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle 498 ENSG00000152234
213  ENSG00000151366 NA NDUFC2 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa 4718 ENSG00000151366
214  ENSG00000128609 NA NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa 4698 ENSG00000128609
215  ENSG00000132305 NA IMMT inner membrane protein, mitochondrial 10989 ENSG00000132305
216  ENSG00000163541 NA SUCLG1 succinate-CoA ligase, alpha subunit 8802 ENSG00000163541
217  ENSG00000090432 NA MUL1 mitochondrial E3 ubiquitin protein ligase 1 79594 ENSG00000090432
218  ENSG00000146701 NA MDH2 malate dehydrogenase 2, NAD (mitochondrial) 4191 ENSG00000146701
219  ENSG00000154719 NA MRPL39 mitochondrial ribosomal protein L39 54148 ENSG00000154719
220  ENSG00000165678 NA GHITM growth hormone inducible transmembrane protein 27069 ENSG00000165678
221  ENSG00000173915 NA USMG5 up-regulated during skeletal muscle growth 5 homolog (mouse) 84833 ENSG00000173915
222  ENSG00000158882 NA TOMM40L translocase of outer mitochondrial membrane 40 homolog (yeast)-like 84134 ENSG00000158882
223  ENSG00000131730 NA CKMT2 creatine kinase, mitochondrial 2 (sarcomeric) 1160 ENSG00000131730
224  ENSG00000164038 NA SLC9B2 solute carrier family 9, subfamily B (NHA2, cation proton antiporter 2), member 2 133308 ENSG00000164038
225  ENSG00000147123 NA NDUFB11 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa 54539 ENSG00000147123
226  ENSG00000137714 NA FDX1 ferredoxin 1 2230 ENSG00000137714
227  ENSG00000169021 NA UQCRFS1 ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 7386 ENSG00000169021
228  ENSG00000178449 NA COX14 COX14 cytochrome c oxidase assembly homolog (S. cerevisiae) 84987 ENSG00000178449
229  ENSG00000102738 NA MRPS31 mitochondrial ribosomal protein S31 10240 ENSG00000102738
230  ENSG00000124523 NA SIRT5 sirtuin 5 23408 ENSG00000124523
231  ENSG00000145439 NA CBR4 carbonyl reductase 4 84869 ENSG00000145439
232  ENSG00000062485 NA CS citrate synthase 1431 ENSG00000062485
233  ENSG00000130312 NA MRPL34 mitochondrial ribosomal protein L34 64981 ENSG00000130312
234  ENSG00000175193 NA PARL presenilin associated, rhomboid-like 55486 ENSG00000175193
235  ENSG00000111843 NA TMEM14C transmembrane protein 14C 51522 ENSG00000111843
236  ENSG00000185973 NA TMLHE trimethyllysine hydroxylase, epsilon 55217 ENSG00000185973
237  ENSG00000124370 NA MCEE methylmalonyl CoA epimerase 84693 ENSG00000124370
238  ENSG00000137513 NA NARS2 asparaginyl-tRNA synthetase 2, mitochondrial (putative) 79731 ENSG00000137513
239  ENSG00000108179 NA PPIF peptidylprolyl isomerase F 10105 ENSG00000108179
240  ENSG00000162600 NA OMA1 OMA1 zinc metallopeptidase homolog (S. cerevisiae) 115209 ENSG00000162600
241  ENSG00000111639 NA MRPL51 mitochondrial ribosomal protein L51 51258 ENSG00000111639
242  ENSG00000164405 NA UQCRQ ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa 27089 ENSG00000164405
243  ENSG00000173085 NA COQ2 coenzyme Q2 homolog, prenyltransferase (yeast) 27235 ENSG00000173085
244  ENSG00000061794 NA MRPS35 mitochondrial ribosomal protein S35 60488 ENSG00000061794
245  ENSG00000124172 NA ATP5E ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit 514 ENSG00000124172
246  ENSG00000183648 NA NDUFB1 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa 4707 ENSG00000183648
247  ENSG00000132591 NA ERAL1 Era G-protein-like 1 (E. coli) 26284 ENSG00000132591
248  ENSG00000205981 NA DNAJC19 DnaJ (Hsp40) homolog, subfamily C, member 19 131118 ENSG00000205981
249  ENSG00000213585 NA VDAC1 voltage-dependent anion channel 1 7416 ENSG00000213585
250  ENSG00000120333 NA MRPS14 mitochondrial ribosomal protein S14 63931 ENSG00000120333
251  ENSG00000110435 NA PDHX pyruvate dehydrogenase complex, component X 8050 ENSG00000110435
252  ENSG00000099624 NA ATP5D ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit 513 ENSG00000099624
253  ENSG00000100412 NA ACO2 aconitase 2, mitochondrial 50 ENSG00000100412
254  ENSG00000132676 NA DAP3 death associated protein 3 7818 ENSG00000132676
255  ENSG00000125356 NA NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa 4694 ENSG00000125356
256  ENSG00000108528 NA SLC25A11 solute carrier family 25 (mitochondrial carrier; oxoglutarate carrier), member 11 8402 ENSG00000108528
257  ENSG00000099795 NA NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa 4713 ENSG00000099795
258  ENSG00000103507 NA BCKDK branched chain ketoacid dehydrogenase kinase 10295 ENSG00000103507
259  ENSG00000148090 NA AUH AU RNA binding protein/enoyl-CoA hydratase 549 ENSG00000148090
260  ENSG00000198015 NA MRPL42 mitochondrial ribosomal protein L42 28977 ENSG00000198015
261  ENSG00000127989 NA MTERF mitochondrial transcription termination factor 7978 ENSG00000127989
262  ENSG00000125901 NA MRPS26 mitochondrial ribosomal protein S26 64949 ENSG00000125901
263  ENSG00000075336 NA TIMM21 translocase of inner mitochondrial membrane 21 homolog (yeast) 29090 ENSG00000075336
264  ENSG00000181991 NA MRPS11 mitochondrial ribosomal protein S11 64963 ENSG00000181991
265  ENSG00000175110 NA MRPS22 mitochondrial ribosomal protein S22 56945 ENSG00000175110
266  ENSG00000197448 NA GSTK1 glutathione S-transferase kappa 1 373156 ENSG00000197448
267  ENSG00000167792 NA NDUFV1 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa 4723 ENSG00000167792
268  ENSG00000110717 NA NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) 4728 ENSG00000110717
269  ENSG00000174547 NA MRPL11 mitochondrial ribosomal protein L11 65003 ENSG00000174547
270  ENSG00000204308 NA RNF5 ring finger protein 5, E3 ubiquitin protein ligase 6048 ENSG00000204308
271  ENSG00000183978 NA COA3 cytochrome C oxidase assembly factor 3 28958 ENSG00000183978
272  ENSG00000178952 NA TUFM Tu translation elongation factor, mitochondrial 7284 ENSG00000178952
273  ENSG00000127884 NA ECHS1 enoyl CoA hydratase, short chain, 1, mitochondrial 1892 ENSG00000127884
274  ENSG00000241468 NA ATP5J2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 9551 ENSG00000241468
275  ENSG00000113013 NA HSPA9 heat shock 70kDa protein 9 (mortalin) 3313 ENSG00000113013
276  ENSG00000143158 NA MPC2 mitochondrial pyruvate carrier 2 25874 ENSG00000143158
277  ENSG00000176340 NA COX8A cytochrome c oxidase subunit VIIIA (ubiquitous) 1351 ENSG00000176340
278  ENSG00000101247 NA NDUFAF5 NADH dehydrogenase (ubiquinone) complex I, assembly factor 5 79133 ENSG00000101247
279  ENSG00000101365 NA IDH3B isocitrate dehydrogenase 3 (NAD+) beta 3420 ENSG00000101365
280  ENSG00000241837 NA ATP5O ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit 539 ENSG00000241837
281  ENSG00000214026 NA MRPL23 mitochondrial ribosomal protein L23 6150 ENSG00000214026


Database:cellular component       Name:mitochondrial inner membrane       ID:GO:0005743
C=354; O=151; E=21.49; R=7.03; rawP=2.20e-90; adjP=2.90e-88
Index UserID Value Gene Symbol Gene Name EntrezGene Ensembl
1  ENSG00000087299 NA L2HGDH L-2-hydroxyglutarate dehydrogenase 79944 ENSG00000087299
2  ENSG00000184903 NA IMMP2L IMP2 inner mitochondrial membrane peptidase-like (S. cerevisiae) 83943 ENSG00000184903
3  ENSG00000165264 NA NDUFB6 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa 4712 ENSG00000165264
4  ENSG00000156467 NA UQCRB ubiquinol-cytochrome c reductase binding protein 7381 ENSG00000156467
5  ENSG00000161281 NA COX7A1 cytochrome c oxidase subunit VIIa polypeptide 1 (muscle) 1346 ENSG00000161281
6  ENSG00000184076 NA UQCR10 ubiquinol-cytochrome c reductase, complex III subunit X 29796 ENSG00000184076
7  ENSG00000078070 NA MCCC1 methylcrotonoyl-CoA carboxylase 1 (alpha) 56922 ENSG00000078070
8  ENSG00000075415 NA SLC25A3 solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 3 5250 ENSG00000075415
9  ENSG00000156885 NA COX6A2 cytochrome c oxidase subunit VIa polypeptide 2 1339 ENSG00000156885
10  ENSG00000154723 NA ATP5J ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 522 ENSG00000154723
11  ENSG00000167969 NA ECI1 enoyl-CoA delta isomerase 1 1632 ENSG00000167969
12  ENSG00000125166 NA GOT2 glutamic-oxaloacetic transaminase 2, mitochondrial (aspartate aminotransferase 2) 2806 ENSG00000125166
13  ENSG00000100347 NA SAMM50 sorting and assembly machinery component 50 homolog (S. cerevisiae) 25813 ENSG00000100347
14  ENSG00000135390 NA ATP5G2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C2 (subunit 9) 517 ENSG00000135390
15  ENSG00000177370 NA TIMM22 translocase of inner mitochondrial membrane 22 homolog (yeast) 29928 ENSG00000177370
16  ENSG00000140740 NA UQCRC2 ubiquinol-cytochrome c reductase core protein II 7385 ENSG00000140740
17  ENSG00000166136 NA NDUFB8 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa 4714 ENSG00000166136
18  ENSG00000160194 NA NDUFV3 NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa 4731 ENSG00000160194
19  ENSG00000147684 NA NDUFB9 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa 4715 ENSG00000147684
20  ENSG00000184983 NA NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa 4700 ENSG00000184983
21  ENSG00000130414 NA NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa 4705 ENSG00000130414
22  ENSG00000163626 NA COX18 COX18 cytochrome c oxidase assembly homolog (S. cerevisiae) 285521 ENSG00000163626
23  ENSG00000158864 NA NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) 4720 ENSG00000158864
24  ENSG00000007923 NA DNAJC11 DnaJ (Hsp40) homolog, subfamily C, member 11 55735 ENSG00000007923
25  ENSG00000173436 NA MINOS1 mitochondrial inner membrane organizing system 1 440574 ENSG00000173436
26  ENSG00000105197 NA TIMM50 translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae) 92609 ENSG00000105197
27  ENSG00000109390 NA NDUFC1 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa 4717 ENSG00000109390
28  ENSG00000060762 NA MPC1 mitochondrial pyruvate carrier 1 51660 ENSG00000060762
29  ENSG00000165283 NA STOML2 stomatin (EPB72)-like 2 30968 ENSG00000165283
30  ENSG00000104980 NA TIMM44 translocase of inner mitochondrial membrane 44 homolog (yeast) 10469 ENSG00000104980
31  ENSG00000116459 NA ATP5F1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 515 ENSG00000116459
32  ENSG00000164466 NA SFXN1 sideroflexin 1 94081 ENSG00000164466
33  ENSG00000099800 NA TIMM13 translocase of inner mitochondrial membrane 13 homolog (yeast) 26517 ENSG00000099800
34  ENSG00000151729 NA SLC25A4 solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4 291 ENSG00000151729
35  ENSG00000178057 NA NDUFAF3 NADH dehydrogenase (ubiquinone) complex I, assembly factor 3 25915 ENSG00000178057
36  ENSG00000112992 NA NNT nicotinamide nucleotide transhydrogenase 23530 ENSG00000112992
37  ENSG00000213619 NA NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) 4722 ENSG00000213619
38  ENSG00000178741 NA COX5A cytochrome c oxidase subunit Va 9377 ENSG00000178741
39  ENSG00000173660 NA UQCRH ubiquinol-cytochrome c reductase hinge protein 7388 ENSG00000173660
40  ENSG00000133028 NA SCO1 SCO cytochrome oxidase deficient homolog 1 (yeast) 6341 ENSG00000133028
41  ENSG00000148950 NA IMMP1L IMP1 inner mitochondrial membrane peptidase-like (S. cerevisiae) 196294 ENSG00000148950
42  ENSG00000119421 NA NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa 4702 ENSG00000119421
43  ENSG00000126267 NA COX6B1 cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) 1340 ENSG00000126267
44  ENSG00000109919 NA MTCH2 mitochondrial carrier 2 23788 ENSG00000109919
45  ENSG00000135940 NA COX5B cytochrome c oxidase subunit Vb 1329 ENSG00000135940
46  ENSG00000215021 NA PHB2 prohibitin 2 11331 ENSG00000215021
47  ENSG00000145494 NA NDUFS6 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) 4726 ENSG00000145494
48  ENSG00000167085 NA PHB prohibitin 5245 ENSG00000167085
49  ENSG00000072506 NA HSD17B10 hydroxysteroid (17-beta) dehydrogenase 10 3028 ENSG00000072506
50  ENSG00000156709 NA AIFM1 apoptosis-inducing factor, mitochondrion-associated, 1 9131 ENSG00000156709
51  ENSG00000189043 NA NDUFA4 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa 4697 ENSG00000189043
52  ENSG00000131143 NA COX4I1 cytochrome c oxidase subunit IV isoform 1 1327 ENSG00000131143
53  ENSG00000172115 NA CYCS cytochrome c, somatic 54205 ENSG00000172115
54  ENSG00000164919 NA COX6C cytochrome c oxidase subunit VIc 1345 ENSG00000164919
55  ENSG00000115286 NA NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) 374291 ENSG00000115286
56  ENSG00000164258 NA NDUFS4 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) 4724 ENSG00000164258
57  ENSG00000156170 NA NDUFAF6 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 137682 ENSG00000156170
58  ENSG00000155463 NA OXA1L oxidase (cytochrome c) assembly 1-like 5018 ENSG00000155463
59  ENSG00000167863 NA ATP5H ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d 10476 ENSG00000167863
60  ENSG00000090266 NA NDUFB2 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa 4708 ENSG00000090266
61  ENSG00000127540 NA UQCR11 ubiquinol-cytochrome c reductase, complex III subunit XI 10975 ENSG00000127540
62  ENSG00000179091 NA CYC1 cytochrome c-1 1537 ENSG00000179091
63  ENSG00000184752 NA NDUFA12 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 55967 ENSG00000184752
64  ENSG00000156411 NA C14orf2 chromosome 14 open reading frame 2 9556 ENSG00000156411
65  ENSG00000131844 NA MCCC2 methylcrotonoyl-CoA carboxylase 2 (beta) 64087 ENSG00000131844
66  ENSG00000159199 NA ATP5G1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) 516 ENSG00000159199
67  ENSG00000105819 NA PMPCB peptidase (mitochondrial processing) beta 9512 ENSG00000105819
68  ENSG00000150779 NA TIMM8B translocase of inner mitochondrial membrane 8 homolog B (yeast) 26521 ENSG00000150779
69  ENSG00000166855 NA CLPX ClpX caseinolytic peptidase X homolog (E. coli) 10845 ENSG00000166855
70  ENSG00000074582 NA BCS1L BCS1-like (S. cerevisiae) 617 ENSG00000074582
71  ENSG00000103018 NA CYB5B cytochrome b5 type B (outer mitochondrial membrane) 80777 ENSG00000103018
72  ENSG00000166816 NA LDHD lactate dehydrogenase D 197257 ENSG00000166816
73  ENSG00000140990 NA NDUFB10 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa 4716 ENSG00000140990
74  ENSG00000066926 NA FECH ferrochelatase 2235 ENSG00000066926
75  ENSG00000117118 NA SDHB succinate dehydrogenase complex, subunit B, iron sulfur (Ip) 6390 ENSG00000117118
76  ENSG00000135469 NA COQ10A coenzyme Q10 homolog A (S. cerevisiae) 93058 ENSG00000135469
77  ENSG00000165629 NA ATP5C1 ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 509 ENSG00000165629
78  ENSG00000115944 NA COX7A2L cytochrome c oxidase subunit VIIa polypeptide 2 like 9167 ENSG00000115944
79  ENSG00000148290 NA SURF1 surfeit 1 6834 ENSG00000148290
80  ENSG00000197150 NA ABCB8 ATP-binding cassette, sub-family B (MDR/TAP), member 8 11194 ENSG00000197150
81  ENSG00000152234 NA ATP5A1 ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle 498 ENSG00000152234
82  ENSG00000072778 NA ACADVL acyl-CoA dehydrogenase, very long chain 37 ENSG00000072778
83  ENSG00000151366 NA NDUFC2 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa 4718 ENSG00000151366
84  ENSG00000128609 NA NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa 4698 ENSG00000128609
85  ENSG00000132305 NA IMMT inner membrane protein, mitochondrial 10989 ENSG00000132305
86  ENSG00000163541 NA SUCLG1 succinate-CoA ligase, alpha subunit 8802 ENSG00000163541
87  ENSG00000146701 NA MDH2 malate dehydrogenase 2, NAD (mitochondrial) 4191 ENSG00000146701
88  ENSG00000165678 NA GHITM growth hormone inducible transmembrane protein 27069 ENSG00000165678
89  ENSG00000125995 NA ROMO1 reactive oxygen species modulator 1 140823 ENSG00000125995
90  ENSG00000136521 NA NDUFB5 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa 4711 ENSG00000136521
91  ENSG00000173915 NA USMG5 up-regulated during skeletal muscle growth 5 homolog (mouse) 84833 ENSG00000173915
92  ENSG00000182054 NA IDH2 isocitrate dehydrogenase 2 (NADP+), mitochondrial 3418 ENSG00000182054
93  ENSG00000004779 NA NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa 4706 ENSG00000004779
94  ENSG00000131730 NA CKMT2 creatine kinase, mitochondrial 2 (sarcomeric) 1160 ENSG00000131730
95  ENSG00000169020 NA ATP5I ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E 521 ENSG00000169020
96  ENSG00000004961 NA HCCS holocytochrome c synthase 3052 ENSG00000004961
97  ENSG00000147123 NA NDUFB11 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa 54539 ENSG00000147123
98  ENSG00000073578 NA SDHA succinate dehydrogenase complex, subunit A, flavoprotein (Fp) 6389 ENSG00000073578
99  ENSG00000137714 NA FDX1 ferredoxin 1 2230 ENSG00000137714
100  ENSG00000119013 NA NDUFB3 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa 4709 ENSG00000119013
101  ENSG00000169021 NA UQCRFS1 ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 7386 ENSG00000169021
102  ENSG00000175193 NA PARL presenilin associated, rhomboid-like 55486 ENSG00000175193
103  ENSG00000108179 NA PPIF peptidylprolyl isomerase F 10105 ENSG00000108179
104  ENSG00000139180 NA NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa 4704 ENSG00000139180
105  ENSG00000162600 NA OMA1 OMA1 zinc metallopeptidase homolog (S. cerevisiae) 115209 ENSG00000162600
106  ENSG00000127184 NA COX7C cytochrome c oxidase subunit VIIc 1350 ENSG00000127184
107  ENSG00000164405 NA UQCRQ ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa 27089 ENSG00000164405
108  ENSG00000165637 NA VDAC2 voltage-dependent anion channel 2 7417 ENSG00000165637
109  ENSG00000124172 NA ATP5E ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit 514 ENSG00000124172
110  ENSG00000183648 NA NDUFB1 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa 4707 ENSG00000183648
111  ENSG00000132591 NA ERAL1 Era G-protein-like 1 (E. coli) 26284 ENSG00000132591
112  ENSG00000205981 NA DNAJC19 DnaJ (Hsp40) homolog, subfamily C, member 19 131118 ENSG00000205981
113  ENSG00000213585 NA VDAC1 voltage-dependent anion channel 1 7416 ENSG00000213585
114  ENSG00000204370 NA SDHD succinate dehydrogenase complex, subunit D, integral membrane protein 6392 ENSG00000204370
115  ENSG00000099624 NA ATP5D ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit 513 ENSG00000099624
116  ENSG00000106554 NA CHCHD3 coiled-coil-helix-coiled-coil-helix domain containing 3 54927 ENSG00000106554
117  ENSG00000125356 NA NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa 4694 ENSG00000125356
118  ENSG00000108528 NA SLC25A11 solute carrier family 25 (mitochondrial carrier; oxoglutarate carrier), member 11 8402 ENSG00000108528
119  ENSG00000099795 NA NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa 4713 ENSG00000099795
120  ENSG00000174032 NA SLC25A30 solute carrier family 25, member 30 253512 ENSG00000174032
121  ENSG00000023228 NA NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) 4719 ENSG00000023228
122  ENSG00000143252 NA SDHC succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa 6391 ENSG00000143252
123  ENSG00000115840 NA SLC25A12 solute carrier family 25 (aspartate/glutamate carrier), member 12 8604 ENSG00000115840
124  ENSG00000110955 NA ATP5B ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide 506 ENSG00000110955
125  ENSG00000197122 NA SRC v-src sarcoma (Schmidt-Ruppin A-2) viral oncogene homolog (avian) 6714 ENSG00000197122
126  ENSG00000112695 NA COX7A2 cytochrome c oxidase subunit VIIa polypeptide 2 (liver) 1347 ENSG00000112695
127  ENSG00000197448 NA GSTK1 glutathione S-transferase kappa 1 373156 ENSG00000197448
128  ENSG00000167792 NA NDUFV1 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa 4723 ENSG00000167792
129  ENSG00000131495 NA NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa 4695 ENSG00000131495
130  ENSG00000065518 NA NDUFB4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa 4710 ENSG00000065518
131  ENSG00000095321 NA CRAT carnitine O-acetyltransferase 1384 ENSG00000095321
132  ENSG00000165688 NA PMPCA peptidase (mitochondrial processing) alpha 23203 ENSG00000165688
133  ENSG00000110717 NA NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) 4728 ENSG00000110717
134  ENSG00000131174 NA COX7B cytochrome c oxidase subunit VIIb 1349 ENSG00000131174
135  ENSG00000170906 NA NDUFA3 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa 4696 ENSG00000170906
136  ENSG00000167283 NA ATP5L ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G 10632 ENSG00000167283
137  ENSG00000124532 NA MRS2 MRS2 magnesium homeostasis factor homolog (S. cerevisiae) 57380 ENSG00000124532
138  ENSG00000131269 NA ABCB7 ATP-binding cassette, sub-family B (MDR/TAP), member 7 22 ENSG00000131269
139  ENSG00000010256 NA UQCRC1 ubiquinol-cytochrome c reductase core protein I 7384 ENSG00000010256
140  ENSG00000137806 NA NDUFAF1 NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 51103 ENSG00000137806
141  ENSG00000241468 NA ATP5J2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 9551 ENSG00000241468
142  ENSG00000171503 NA ETFDH electron-transferring-flavoprotein dehydrogenase 2110 ENSG00000171503
143  ENSG00000143158 NA MPC2 mitochondrial pyruvate carrier 2 25874 ENSG00000143158
144  ENSG00000138796 NA HADH hydroxyacyl-CoA dehydrogenase 3033 ENSG00000138796
145  ENSG00000154518 NA ATP5G3 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C3 (subunit 9) 518 ENSG00000154518
146  ENSG00000075303 NA SLC25A40 solute carrier family 25, member 40 55972 ENSG00000075303
147  ENSG00000176340 NA COX8A cytochrome c oxidase subunit VIIIA (ubiquitous) 1351 ENSG00000176340
148  ENSG00000101247 NA NDUFAF5 NADH dehydrogenase (ubiquinone) complex I, assembly factor 5 79133 ENSG00000101247
149  ENSG00000168653 NA NDUFS5 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) 4725 ENSG00000168653
150  ENSG00000126768 NA TIMM17B translocase of inner mitochondrial membrane 17 homolog B (yeast) 10245 ENSG00000126768
151  ENSG00000241837 NA ATP5O ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit 539 ENSG00000241837


Database:cellular component       Name:mitochondrial matrix       ID:GO:0005759
C=278; O=135; E=16.87; R=8.00; rawP=8.25e-90; adjP=8.17e-88
Index UserID Value Gene Symbol Gene Name EntrezGene Ensembl
1  ENSG00000116898 NA MRPS15 mitochondrial ribosomal protein S15 64960 ENSG00000116898
2  ENSG00000167862 NA ICT1 immature colon carcinoma transcript 1 3396 ENSG00000167862
3  ENSG00000078070 NA MCCC1 methylcrotonoyl-CoA carboxylase 1 (alpha) 56922 ENSG00000078070
4  ENSG00000148672 NA GLUD1 glutamate dehydrogenase 1 2746 ENSG00000148672
5  ENSG00000167969 NA ECI1 enoyl-CoA delta isomerase 1 1632 ENSG00000167969
6  ENSG00000105552 NA BCAT2 branched chain amino-acid transaminase 2, mitochondrial 587 ENSG00000105552
7  ENSG00000139531 NA SUOX sulfite oxidase 6821 ENSG00000139531
8  ENSG00000125166 NA GOT2 glutamic-oxaloacetic transaminase 2, mitochondrial (aspartate aminotransferase 2) 2806 ENSG00000125166
9  ENSG00000140374 NA ETFA electron-transfer-flavoprotein, alpha polypeptide 2108 ENSG00000140374
10  ENSG00000172340 NA SUCLG2 succinate-CoA ligase, GDP-forming, beta subunit 8801 ENSG00000172340
11  ENSG00000091140 NA DLD dihydrolipoamide dehydrogenase 1738 ENSG00000091140
12  ENSG00000130414 NA NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa 4705 ENSG00000130414
13  ENSG00000102309 NA PIN4 protein (peptidylprolyl cis/trans isomerase) NIMA-interacting, 4 (parvulin) 5303 ENSG00000102309
14  ENSG00000165060 NA FXN frataxin 2395 ENSG00000165060
15  ENSG00000173141 NA MRP63 mitochondrial ribosomal protein 63 78988 ENSG00000173141
16  ENSG00000116221 NA MRPL37 mitochondrial ribosomal protein L37 51253 ENSG00000116221
17  ENSG00000131828 NA PDHA1 pyruvate dehydrogenase (lipoamide) alpha 1 5160 ENSG00000131828
18  ENSG00000122971 NA ACADS acyl-CoA dehydrogenase, C-2 to C-3 short chain 35 ENSG00000122971
19  ENSG00000142168 NA SOD1 superoxide dismutase 1, soluble 6647 ENSG00000142168
20  ENSG00000103356 NA EARS2 glutamyl-tRNA synthetase 2, mitochondrial (putative) 124454 ENSG00000103356
21  ENSG00000109519 NA GRPEL1 GrpE-like 1, mitochondrial (E. coli) 80273 ENSG00000109519
22  ENSG00000091483 NA FH fumarate hydratase 2271 ENSG00000091483
23  ENSG00000262814 NA MRPL12 mitochondrial ribosomal protein L12 6182 ENSG00000262814
24  ENSG00000055950 NA MRPL43 mitochondrial ribosomal protein L43 84545 ENSG00000055950
25  ENSG00000096080 NA MRPS18A mitochondrial ribosomal protein S18A 55168 ENSG00000096080
26  ENSG00000134056 NA MRPS36 mitochondrial ribosomal protein S36 92259 ENSG00000134056
27  ENSG00000142082 NA SIRT3 sirtuin 3 23410 ENSG00000142082
28  ENSG00000119689 NA DLST dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex) 1743 ENSG00000119689
29  ENSG00000204568 NA MRPS18B mitochondrial ribosomal protein S18B 28973 ENSG00000204568
30  ENSG00000168291 NA PDHB pyruvate dehydrogenase (lipoamide) beta 5162 ENSG00000168291
31  ENSG00000156502 NA SUPV3L1 suppressor of var1, 3-like 1 (S. cerevisiae) 6832 ENSG00000156502
32  ENSG00000104980 NA TIMM44 translocase of inner mitochondrial membrane 44 homolog (yeast) 10469 ENSG00000104980
33  ENSG00000116459 NA ATP5F1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 515 ENSG00000116459
34  ENSG00000187145 NA MRPS21 mitochondrial ribosomal protein S21 54460 ENSG00000187145
35  ENSG00000067704 NA IARS2 isoleucyl-tRNA synthetase 2, mitochondrial 55699 ENSG00000067704
36  ENSG00000023330 NA ALAS1 aminolevulinate, delta-, synthase 1 211 ENSG00000023330
37  ENSG00000147586 NA MRPS28 mitochondrial ribosomal protein S28 28957 ENSG00000147586
38  ENSG00000172172 NA MRPL13 mitochondrial ribosomal protein L13 28998 ENSG00000172172
39  ENSG00000137288 NA MNF1 mitochondrial nucleoid factor 1 84300 ENSG00000137288
40  ENSG00000244005 NA NFS1 NFS1 nitrogen fixation 1 homolog (S. cerevisiae) 9054 ENSG00000244005
41  ENSG00000029639 NA TFB1M transcription factor B1, mitochondrial 51106 ENSG00000029639
42  ENSG00000143436 NA MRPL9 mitochondrial ribosomal protein L9 65005 ENSG00000143436
43  ENSG00000239789 NA MRPS17 mitochondrial ribosomal protein S17 51373 ENSG00000239789
44  ENSG00000162851 NA TFB2M transcription factor B2, mitochondrial 64216 ENSG00000162851
45  ENSG00000072506 NA HSD17B10 hydroxysteroid (17-beta) dehydrogenase 10 3028 ENSG00000072506
46  ENSG00000108561 NA C1QBP complement component 1, q subcomponent binding protein 708 ENSG00000108561
47  ENSG00000105379 NA ETFB electron-transfer-flavoprotein, beta polypeptide 2109 ENSG00000105379
48  ENSG00000139131 NA YARS2 tyrosyl-tRNA synthetase 2, mitochondrial 51067 ENSG00000139131
49  ENSG00000163319 NA MRPS18C mitochondrial ribosomal protein S18C 51023 ENSG00000163319
50  ENSG00000175581 NA MRPL48 mitochondrial ribosomal protein L48 51642 ENSG00000175581
51  ENSG00000185608 NA MRPL40 mitochondrial ribosomal protein L40 64976 ENSG00000185608
52  ENSG00000151498 NA ACAD8 acyl-CoA dehydrogenase family, member 8 27034 ENSG00000151498
53  ENSG00000132423 NA COQ3 coenzyme Q3 homolog, methyltransferase (S. cerevisiae) 51805 ENSG00000132423
54  ENSG00000131844 NA MCCC2 methylcrotonoyl-CoA carboxylase 2 (beta) 64087 ENSG00000131844
55  ENSG00000134905 NA CARS2 cysteinyl-tRNA synthetase 2, mitochondrial (putative) 79587 ENSG00000134905
56  ENSG00000156928 NA MALSU1 mitochondrial assembly of ribosomal large subunit 1 115416 ENSG00000156928
57  ENSG00000136143 NA SUCLA2 succinate-CoA ligase, ADP-forming, beta subunit 8803 ENSG00000136143
58  ENSG00000182810 NA DDX28 DEAD (Asp-Glu-Ala-Asp) box polypeptide 28 55794 ENSG00000182810
59  ENSG00000105819 NA PMPCB peptidase (mitochondrial processing) beta 9512 ENSG00000105819
60  ENSG00000166855 NA CLPX ClpX caseinolytic peptidase X homolog (E. coli) 10845 ENSG00000166855
61  ENSG00000090263 NA MRPS33 mitochondrial ribosomal protein S33 51650 ENSG00000090263
62  ENSG00000204228 NA HSD17B8 hydroxysteroid (17-beta) dehydrogenase 8 7923 ENSG00000204228
63  ENSG00000175198 NA PCCA propionyl CoA carboxylase, alpha polypeptide 5095 ENSG00000175198
64  ENSG00000067829 NA IDH3G isocitrate dehydrogenase 3 (NAD+) gamma 3421 ENSG00000067829
65  ENSG00000172590 NA MRPL52 mitochondrial ribosomal protein L52 122704 ENSG00000172590
66  ENSG00000143374 NA TARS2 threonyl-tRNA synthetase 2, mitochondrial (putative) 80222 ENSG00000143374
67  ENSG00000132313 NA MRPL35 mitochondrial ribosomal protein L35 51318 ENSG00000132313
68  ENSG00000066926 NA FECH ferrochelatase 2235 ENSG00000066926
69  ENSG00000247626 NA MARS2 methionyl-tRNA synthetase 2, mitochondrial 92935 ENSG00000247626
70  ENSG00000165629 NA ATP5C1 ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 509 ENSG00000165629
71  ENSG00000152234 NA ATP5A1 ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle 498 ENSG00000152234
72  ENSG00000072778 NA ACADVL acyl-CoA dehydrogenase, very long chain 37 ENSG00000072778
73  ENSG00000154930 NA ACSS1 acyl-CoA synthetase short-chain family member 1 84532 ENSG00000154930
74  ENSG00000163541 NA SUCLG1 succinate-CoA ligase, alpha subunit 8802 ENSG00000163541
75  ENSG00000146701 NA MDH2 malate dehydrogenase 2, NAD (mitochondrial) 4191 ENSG00000146701
76  ENSG00000154719 NA MRPL39 mitochondrial ribosomal protein L39 54148 ENSG00000154719
77  ENSG00000182054 NA IDH2 isocitrate dehydrogenase 2 (NADP+), mitochondrial 3418 ENSG00000182054
78  ENSG00000004779 NA NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa 4706 ENSG00000004779
79  ENSG00000137714 NA FDX1 ferredoxin 1 2230 ENSG00000137714
80  ENSG00000104325 NA DECR1 2,4-dienoyl CoA reductase 1, mitochondrial 1666 ENSG00000104325
81  ENSG00000102738 NA MRPS31 mitochondrial ribosomal protein S31 10240 ENSG00000102738
82  ENSG00000124523 NA SIRT5 sirtuin 5 23408 ENSG00000124523
83  ENSG00000145439 NA CBR4 carbonyl reductase 4 84869 ENSG00000145439
84  ENSG00000062485 NA CS citrate synthase 1431 ENSG00000062485
85  ENSG00000130312 NA MRPL34 mitochondrial ribosomal protein L34 64981 ENSG00000130312
86  ENSG00000182154 NA MRPL41 mitochondrial ribosomal protein L41 64975 ENSG00000182154
87  ENSG00000185973 NA TMLHE trimethyllysine hydroxylase, epsilon 55217 ENSG00000185973
88  ENSG00000108179 NA PPIF peptidylprolyl isomerase F 10105 ENSG00000108179
89  ENSG00000139180 NA NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa 4704 ENSG00000139180
90  ENSG00000137513 NA NARS2 asparaginyl-tRNA synthetase 2, mitochondrial (putative) 79731 ENSG00000137513
91  ENSG00000124370 NA MCEE methylmalonyl CoA epimerase 84693 ENSG00000124370
92  ENSG00000111639 NA MRPL51 mitochondrial ribosomal protein L51 51258 ENSG00000111639
93  ENSG00000165637 NA VDAC2 voltage-dependent anion channel 2 7417 ENSG00000165637
94  ENSG00000061794 NA MRPS35 mitochondrial ribosomal protein S35 60488 ENSG00000061794
95  ENSG00000124172 NA ATP5E ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit 514 ENSG00000124172
96  ENSG00000132591 NA ERAL1 Era G-protein-like 1 (E. coli) 26284 ENSG00000132591
97  ENSG00000213585 NA VDAC1 voltage-dependent anion channel 1 7416 ENSG00000213585
98  ENSG00000120333 NA MRPS14 mitochondrial ribosomal protein S14 63931 ENSG00000120333
99  ENSG00000110435 NA PDHX pyruvate dehydrogenase complex, component X 8050 ENSG00000110435
100  ENSG00000099624 NA ATP5D ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit 513 ENSG00000099624
101  ENSG00000100412 NA ACO2 aconitase 2, mitochondrial 50 ENSG00000100412
102  ENSG00000086504 NA MRPL28 mitochondrial ribosomal protein L28 10573 ENSG00000086504
103  ENSG00000132676 NA DAP3 death associated protein 3 7818 ENSG00000132676
104  ENSG00000162910 NA MRPL55 mitochondrial ribosomal protein L55 128308 ENSG00000162910
105  ENSG00000027001 NA MIPEP mitochondrial intermediate peptidase 4285 ENSG00000027001
106  ENSG00000103423 NA DNAJA3 DnaJ (Hsp40) homolog, subfamily A, member 3 9093 ENSG00000103423
107  ENSG00000138777 NA PPA2 pyrophosphatase (inorganic) 2 27068 ENSG00000138777
108  ENSG00000182180 NA MRPS16 mitochondrial ribosomal protein S16 51021 ENSG00000182180
109  ENSG00000136522 NA MRPL47 mitochondrial ribosomal protein L47 57129 ENSG00000136522
110  ENSG00000135972 NA MRPS9 mitochondrial ribosomal protein S9 64965 ENSG00000135972
111  ENSG00000103507 NA BCKDK branched chain ketoacid dehydrogenase kinase 10295 ENSG00000103507
112  ENSG00000148090 NA AUH AU RNA binding protein/enoyl-CoA hydratase 549 ENSG00000148090
113  ENSG00000198015 NA MRPL42 mitochondrial ribosomal protein L42 28977 ENSG00000198015
114  ENSG00000127989 NA MTERF mitochondrial transcription termination factor 7978 ENSG00000127989
115  ENSG00000151376 NA ME3 malic enzyme 3, NADP(+)-dependent, mitochondrial 10873 ENSG00000151376
116  ENSG00000125901 NA MRPS26 mitochondrial ribosomal protein S26 64949 ENSG00000125901
117  ENSG00000145982 NA FARS2 phenylalanyl-tRNA synthetase 2, mitochondrial 10667 ENSG00000145982
118  ENSG00000110955 NA ATP5B ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide 506 ENSG00000110955
119  ENSG00000181991 NA MRPS11 mitochondrial ribosomal protein S11 64963 ENSG00000181991
120  ENSG00000175110 NA MRPS22 mitochondrial ribosomal protein S22 56945 ENSG00000175110
121  ENSG00000083720 NA OXCT1 3-oxoacid CoA transferase 1 5019 ENSG00000083720
122  ENSG00000165688 NA PMPCA peptidase (mitochondrial processing) alpha 23203 ENSG00000165688
123  ENSG00000112855 NA HARS2 histidyl-tRNA synthetase 2, mitochondrial 23438 ENSG00000112855
124  ENSG00000147853 NA AK3 adenylate kinase 3 50808 ENSG00000147853
125  ENSG00000174547 NA MRPL11 mitochondrial ribosomal protein L11 65003 ENSG00000174547
126  ENSG00000205309 NA NT5M 5',3'-nucleotidase, mitochondrial 56953 ENSG00000205309
127  ENSG00000114054 NA PCCB propionyl CoA carboxylase, beta polypeptide 5096 ENSG00000114054
128  ENSG00000111275 NA ALDH2 aldehyde dehydrogenase 2 family (mitochondrial) 217 ENSG00000111275
129  ENSG00000178952 NA TUFM Tu translation elongation factor, mitochondrial 7284 ENSG00000178952
130  ENSG00000127884 NA ECHS1 enoyl CoA hydratase, short chain, 1, mitochondrial 1892 ENSG00000127884
131  ENSG00000171503 NA ETFDH electron-transferring-flavoprotein dehydrogenase 2110 ENSG00000171503
132  ENSG00000113013 NA HSPA9 heat shock 70kDa protein 9 (mortalin) 3313 ENSG00000113013
133  ENSG00000138796 NA HADH hydroxyacyl-CoA dehydrogenase 3033 ENSG00000138796
134  ENSG00000101365 NA IDH3B isocitrate dehydrogenase 3 (NAD+) beta 3420 ENSG00000101365
135  ENSG00000214026 NA MRPL23 mitochondrial ribosomal protein L23 6150 ENSG00000214026


Database:cellular component       Name:mitochondrial envelope       ID:GO:0005740
C=530; O=179; E=32.17; R=5.56; rawP=1.89e-87; adjP=1.50e-85
Index UserID Value Gene Symbol Gene Name EntrezGene Ensembl
1  ENSG00000087299 NA L2HGDH L-2-hydroxyglutarate dehydrogenase 79944 ENSG00000087299
2  ENSG00000184903 NA IMMP2L IMP2 inner mitochondrial membrane peptidase-like (S. cerevisiae) 83943 ENSG00000184903
3  ENSG00000165264 NA NDUFB6 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa 4712 ENSG00000165264
4  ENSG00000156467 NA UQCRB ubiquinol-cytochrome c reductase binding protein 7381 ENSG00000156467
5  ENSG00000161281 NA COX7A1 cytochrome c oxidase subunit VIIa polypeptide 1 (muscle) 1346 ENSG00000161281
6  ENSG00000184076 NA UQCR10 ubiquinol-cytochrome c reductase, complex III subunit X 29796 ENSG00000184076
7  ENSG00000078070 NA MCCC1 methylcrotonoyl-CoA carboxylase 1 (alpha) 56922 ENSG00000078070
8  ENSG00000075415 NA SLC25A3 solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 3 5250 ENSG00000075415
9  ENSG00000156885 NA COX6A2 cytochrome c oxidase subunit VIa polypeptide 2 1339 ENSG00000156885
10  ENSG00000006695 NA COX10 COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) 1352 ENSG00000006695
11  ENSG00000133983 NA COX16 COX16 cytochrome c oxidase assembly homolog (S. cerevisiae) 51241 ENSG00000133983
12  ENSG00000154723 NA ATP5J ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 522 ENSG00000154723
13  ENSG00000167969 NA ECI1 enoyl-CoA delta isomerase 1 1632 ENSG00000167969
14  ENSG00000139531 NA SUOX sulfite oxidase 6821 ENSG00000139531
15  ENSG00000125166 NA GOT2 glutamic-oxaloacetic transaminase 2, mitochondrial (aspartate aminotransferase 2) 2806 ENSG00000125166
16  ENSG00000100347 NA SAMM50 sorting and assembly machinery component 50 homolog (S. cerevisiae) 25813 ENSG00000100347
17  ENSG00000135390 NA ATP5G2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C2 (subunit 9) 517 ENSG00000135390
18  ENSG00000177370 NA TIMM22 translocase of inner mitochondrial membrane 22 homolog (yeast) 29928 ENSG00000177370
19  ENSG00000140740 NA UQCRC2 ubiquinol-cytochrome c reductase core protein II 7385 ENSG00000140740
20  ENSG00000166136 NA NDUFB8 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa 4714 ENSG00000166136
21  ENSG00000160194 NA NDUFV3 NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa 4731 ENSG00000160194
22  ENSG00000147684 NA NDUFB9 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa 4715 ENSG00000147684
23  ENSG00000184983 NA NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa 4700 ENSG00000184983
24  ENSG00000130414 NA NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa 4705 ENSG00000130414
25  ENSG00000163626 NA COX18 COX18 cytochrome c oxidase assembly homolog (S. cerevisiae) 285521 ENSG00000163626
26  ENSG00000158864 NA NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) 4720 ENSG00000158864
27  ENSG00000007923 NA DNAJC11 DnaJ (Hsp40) homolog, subfamily C, member 11 55735 ENSG00000007923
28  ENSG00000173436 NA MINOS1 mitochondrial inner membrane organizing system 1 440574 ENSG00000173436
29  ENSG00000105197 NA TIMM50 translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae) 92609 ENSG00000105197
30  ENSG00000109390 NA NDUFC1 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa 4717 ENSG00000109390
31  ENSG00000060762 NA MPC1 mitochondrial pyruvate carrier 1 51660 ENSG00000060762
32  ENSG00000165283 NA STOML2 stomatin (EPB72)-like 2 30968 ENSG00000165283
33  ENSG00000104980 NA TIMM44 translocase of inner mitochondrial membrane 44 homolog (yeast) 10469 ENSG00000104980
34  ENSG00000116459 NA ATP5F1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 515 ENSG00000116459
35  ENSG00000164466 NA SFXN1 sideroflexin 1 94081 ENSG00000164466
36  ENSG00000099800 NA TIMM13 translocase of inner mitochondrial membrane 13 homolog (yeast) 26517 ENSG00000099800
37  ENSG00000151729 NA SLC25A4 solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4 291 ENSG00000151729
38  ENSG00000178057 NA NDUFAF3 NADH dehydrogenase (ubiquinone) complex I, assembly factor 3 25915 ENSG00000178057
39  ENSG00000112992 NA NNT nicotinamide nucleotide transhydrogenase 23530 ENSG00000112992
40  ENSG00000213619 NA NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) 4722 ENSG00000213619
41  ENSG00000178741 NA COX5A cytochrome c oxidase subunit Va 9377 ENSG00000178741
42  ENSG00000173660 NA UQCRH ubiquinol-cytochrome c reductase hinge protein 7388 ENSG00000173660
43  ENSG00000214253 NA FIS1 fission 1 (mitochondrial outer membrane) homolog (S. cerevisiae) 51024 ENSG00000214253
44  ENSG00000133028 NA SCO1 SCO cytochrome oxidase deficient homolog 1 (yeast) 6341 ENSG00000133028
45  ENSG00000148950 NA IMMP1L IMP1 inner mitochondrial membrane peptidase-like (S. cerevisiae) 196294 ENSG00000148950
46  ENSG00000119421 NA NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa 4702 ENSG00000119421
47  ENSG00000126267 NA COX6B1 cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) 1340 ENSG00000126267
48  ENSG00000109919 NA MTCH2 mitochondrial carrier 2 23788 ENSG00000109919
49  ENSG00000135940 NA COX5B cytochrome c oxidase subunit Vb 1329 ENSG00000135940
50  ENSG00000215021 NA PHB2 prohibitin 2 11331 ENSG00000215021
51  ENSG00000145494 NA NDUFS6 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) 4726 ENSG00000145494
52  ENSG00000167085 NA PHB prohibitin 5245 ENSG00000167085
53  ENSG00000072506 NA HSD17B10 hydroxysteroid (17-beta) dehydrogenase 10 3028 ENSG00000072506
54  ENSG00000156709 NA AIFM1 apoptosis-inducing factor, mitochondrion-associated, 1 9131 ENSG00000156709
55  ENSG00000189043 NA NDUFA4 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa 4697 ENSG00000189043
56  ENSG00000131143 NA COX4I1 cytochrome c oxidase subunit IV isoform 1 1327 ENSG00000131143
57  ENSG00000172115 NA CYCS cytochrome c, somatic 54205 ENSG00000172115
58  ENSG00000164919 NA COX6C cytochrome c oxidase subunit VIc 1345 ENSG00000164919
59  ENSG00000115286 NA NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) 374291 ENSG00000115286
60  ENSG00000164258 NA NDUFS4 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) 4724 ENSG00000164258
61  ENSG00000156170 NA NDUFAF6 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 137682 ENSG00000156170
62  ENSG00000155463 NA OXA1L oxidase (cytochrome c) assembly 1-like 5018 ENSG00000155463
63  ENSG00000167863 NA ATP5H ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d 10476 ENSG00000167863
64  ENSG00000090266 NA NDUFB2 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa 4708 ENSG00000090266
65  ENSG00000127540 NA UQCR11 ubiquinol-cytochrome c reductase, complex III subunit XI 10975 ENSG00000127540
66  ENSG00000179091 NA CYC1 cytochrome c-1 1537 ENSG00000179091
67  ENSG00000184752 NA NDUFA12 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 55967 ENSG00000184752
68  ENSG00000156411 NA C14orf2 chromosome 14 open reading frame 2 9556 ENSG00000156411
69  ENSG00000131844 NA MCCC2 methylcrotonoyl-CoA carboxylase 2 (beta) 64087 ENSG00000131844
70  ENSG00000159199 NA ATP5G1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) 516 ENSG00000159199
71  ENSG00000105819 NA PMPCB peptidase (mitochondrial processing) beta 9512 ENSG00000105819
72  ENSG00000150779 NA TIMM8B translocase of inner mitochondrial membrane 8 homolog B (yeast) 26521 ENSG00000150779
73  ENSG00000166855 NA CLPX ClpX caseinolytic peptidase X homolog (E. coli) 10845 ENSG00000166855
74  ENSG00000204228 NA HSD17B8 hydroxysteroid (17-beta) dehydrogenase 8 7923 ENSG00000204228
75  ENSG00000196683 NA TOMM7 translocase of outer mitochondrial membrane 7 homolog (yeast) 54543 ENSG00000196683
76  ENSG00000074582 NA BCS1L BCS1-like (S. cerevisiae) 617 ENSG00000074582
77  ENSG00000103018 NA CYB5B cytochrome b5 type B (outer mitochondrial membrane) 80777 ENSG00000103018
78  ENSG00000166816 NA LDHD lactate dehydrogenase D 197257 ENSG00000166816
79  ENSG00000140990 NA NDUFB10 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa 4716 ENSG00000140990
80  ENSG00000066926 NA FECH ferrochelatase 2235 ENSG00000066926
81  ENSG00000117118 NA SDHB succinate dehydrogenase complex, subunit B, iron sulfur (Ip) 6390 ENSG00000117118
82  ENSG00000138495 NA COX17 COX17 cytochrome c oxidase assembly homolog (S. cerevisiae) 10063 ENSG00000138495
83  ENSG00000198523 NA PLN phospholamban 5350 ENSG00000198523
84  ENSG00000006530 NA AGK acylglycerol kinase 55750 ENSG00000006530
85  ENSG00000135469 NA COQ10A coenzyme Q10 homolog A (S. cerevisiae) 93058 ENSG00000135469
86  ENSG00000177427 NA SMCR7 Smith-Magenis syndrome chromosome region, candidate 7 125170 ENSG00000177427
87  ENSG00000165629 NA ATP5C1 ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 509 ENSG00000165629
88  ENSG00000115944 NA COX7A2L cytochrome c oxidase subunit VIIa polypeptide 2 like 9167 ENSG00000115944
89  ENSG00000123545 NA NDUFAF4 NADH dehydrogenase (ubiquinone) complex I, assembly factor 4 29078 ENSG00000123545
90  ENSG00000148290 NA SURF1 surfeit 1 6834 ENSG00000148290
91  ENSG00000197150 NA ABCB8 ATP-binding cassette, sub-family B (MDR/TAP), member 8 11194 ENSG00000197150
92  ENSG00000152234 NA ATP5A1 ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle 498 ENSG00000152234
93  ENSG00000072778 NA ACADVL acyl-CoA dehydrogenase, very long chain 37 ENSG00000072778
94  ENSG00000151366 NA NDUFC2 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa 4718 ENSG00000151366
95  ENSG00000196636 NA ACN9 ACN9 homolog (S. cerevisiae) 57001 ENSG00000196636
96  ENSG00000128609 NA NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa 4698 ENSG00000128609
97  ENSG00000132305 NA IMMT inner membrane protein, mitochondrial 10989 ENSG00000132305
98  ENSG00000163541 NA SUCLG1 succinate-CoA ligase, alpha subunit 8802 ENSG00000163541
99  ENSG00000090432 NA MUL1 mitochondrial E3 ubiquitin protein ligase 1 79594 ENSG00000090432
100  ENSG00000146701 NA MDH2 malate dehydrogenase 2, NAD (mitochondrial) 4191 ENSG00000146701
101  ENSG00000165678 NA GHITM growth hormone inducible transmembrane protein 27069 ENSG00000165678
102  ENSG00000125995 NA ROMO1 reactive oxygen species modulator 1 140823 ENSG00000125995
103  ENSG00000136521 NA NDUFB5 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa 4711 ENSG00000136521
104  ENSG00000173915 NA USMG5 up-regulated during skeletal muscle growth 5 homolog (mouse) 84833 ENSG00000173915
105  ENSG00000169020 NA ATP5I ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E 521 ENSG00000169020
106  ENSG00000158882 NA TOMM40L translocase of outer mitochondrial membrane 40 homolog (yeast)-like 84134 ENSG00000158882
107  ENSG00000182054 NA IDH2 isocitrate dehydrogenase 2 (NADP+), mitochondrial 3418 ENSG00000182054
108  ENSG00000004779 NA NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa 4706 ENSG00000004779
109  ENSG00000131730 NA CKMT2 creatine kinase, mitochondrial 2 (sarcomeric) 1160 ENSG00000131730
110  ENSG00000168958 NA MFF mitochondrial fission factor 56947 ENSG00000168958
111  ENSG00000164038 NA SLC9B2 solute carrier family 9, subfamily B (NHA2, cation proton antiporter 2), member 2 133308 ENSG00000164038
112  ENSG00000004961 NA HCCS holocytochrome c synthase 3052 ENSG00000004961
113  ENSG00000147123 NA NDUFB11 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa 54539 ENSG00000147123
114  ENSG00000073578 NA SDHA succinate dehydrogenase complex, subunit A, flavoprotein (Fp) 6389 ENSG00000073578
115  ENSG00000137714 NA FDX1 ferredoxin 1 2230 ENSG00000137714
116  ENSG00000119013 NA NDUFB3 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa 4709 ENSG00000119013
117  ENSG00000169021 NA UQCRFS1 ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 7386 ENSG00000169021
118  ENSG00000178449 NA COX14 COX14 cytochrome c oxidase assembly homolog (S. cerevisiae) 84987 ENSG00000178449
119  ENSG00000124523 NA SIRT5 sirtuin 5 23408 ENSG00000124523
120  ENSG00000175193 NA PARL presenilin associated, rhomboid-like 55486 ENSG00000175193
121  ENSG00000078668 NA VDAC3 voltage-dependent anion channel 3 7419 ENSG00000078668
122  ENSG00000111843 NA TMEM14C transmembrane protein 14C 51522 ENSG00000111843
123  ENSG00000139180 NA NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa 4704 ENSG00000139180
124  ENSG00000108179 NA PPIF peptidylprolyl isomerase F 10105 ENSG00000108179
125  ENSG00000162600 NA OMA1 OMA1 zinc metallopeptidase homolog (S. cerevisiae) 115209 ENSG00000162600
126  ENSG00000127184 NA COX7C cytochrome c oxidase subunit VIIc 1350 ENSG00000127184
127  ENSG00000164405 NA UQCRQ ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa 27089 ENSG00000164405
128  ENSG00000165637 NA VDAC2 voltage-dependent anion channel 2 7417 ENSG00000165637
129  ENSG00000173085 NA COQ2 coenzyme Q2 homolog, prenyltransferase (yeast) 27235 ENSG00000173085
130  ENSG00000124172 NA ATP5E ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit 514 ENSG00000124172
131  ENSG00000183648 NA NDUFB1 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa 4707 ENSG00000183648
132  ENSG00000213585 NA VDAC1 voltage-dependent anion channel 1 7416 ENSG00000213585
133  ENSG00000205981 NA DNAJC19 DnaJ (Hsp40) homolog, subfamily C, member 19 131118 ENSG00000205981
134  ENSG00000132591 NA ERAL1 Era G-protein-like 1 (E. coli) 26284 ENSG00000132591
135  ENSG00000204370 NA SDHD succinate dehydrogenase complex, subunit D, integral membrane protein 6392 ENSG00000204370
136  ENSG00000099624 NA ATP5D ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit 513 ENSG00000099624
137  ENSG00000106554 NA CHCHD3 coiled-coil-helix-coiled-coil-helix domain containing 3 54927 ENSG00000106554
138  ENSG00000125356 NA NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa 4694 ENSG00000125356
139  ENSG00000108528 NA SLC25A11 solute carrier family 25 (mitochondrial carrier; oxoglutarate carrier), member 11 8402 ENSG00000108528
140  ENSG00000099795 NA NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa 4713 ENSG00000099795
141  ENSG00000174032 NA SLC25A30 solute carrier family 25, member 30 253512 ENSG00000174032
142  ENSG00000023228 NA NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) 4719 ENSG00000023228
143  ENSG00000143252 NA SDHC succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa 6391 ENSG00000143252
144  ENSG00000075336 NA TIMM21 translocase of inner mitochondrial membrane 21 homolog (yeast) 29090 ENSG00000075336
145  ENSG00000115840 NA SLC25A12 solute carrier family 25 (aspartate/glutamate carrier), member 12 8604 ENSG00000115840
146  ENSG00000110955 NA ATP5B ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide 506 ENSG00000110955
147  ENSG00000197122 NA SRC v-src sarcoma (Schmidt-Ruppin A-2) viral oncogene homolog (avian) 6714 ENSG00000197122
148  ENSG00000112695 NA COX7A2 cytochrome c oxidase subunit VIIa polypeptide 2 (liver) 1347 ENSG00000112695
149  ENSG00000197448 NA GSTK1 glutathione S-transferase kappa 1 373156 ENSG00000197448
150  ENSG00000167792 NA NDUFV1 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa 4723 ENSG00000167792
151  ENSG00000131495 NA NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa 4695 ENSG00000131495
152  ENSG00000065518 NA NDUFB4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa 4710 ENSG00000065518
153  ENSG00000095321 NA CRAT carnitine O-acetyltransferase 1384 ENSG00000095321
154  ENSG00000165688 NA PMPCA peptidase (mitochondrial processing) alpha 23203 ENSG00000165688
155  ENSG00000110717 NA NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) 4728 ENSG00000110717
156  ENSG00000131174 NA COX7B cytochrome c oxidase subunit VIIb 1349 ENSG00000131174
157  ENSG00000170906 NA NDUFA3 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa 4696 ENSG00000170906
158  ENSG00000128654 NA MTX2 metaxin 2 10651 ENSG00000128654
159  ENSG00000204308 NA RNF5 ring finger protein 5, E3 ubiquitin protein ligase 6048 ENSG00000204308
160  ENSG00000167283 NA ATP5L ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G 10632 ENSG00000167283
161  ENSG00000069509 NA FUNDC1 FUN14 domain containing 1 139341 ENSG00000069509
162  ENSG00000183978 NA COA3 cytochrome C oxidase assembly factor 3 28958 ENSG00000183978
163  ENSG00000124532 NA MRS2 MRS2 magnesium homeostasis factor homolog (S. cerevisiae) 57380 ENSG00000124532
164  ENSG00000131269 NA ABCB7 ATP-binding cassette, sub-family B (MDR/TAP), member 7 22 ENSG00000131269
165  ENSG00000010256 NA UQCRC1 ubiquinol-cytochrome c reductase core protein I 7384 ENSG00000010256
166  ENSG00000137806 NA NDUFAF1 NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 51103 ENSG00000137806
167  ENSG00000241468 NA ATP5J2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 9551 ENSG00000241468
168  ENSG00000197912 NA SPG7 spastic paraplegia 7 (pure and complicated autosomal recessive) 6687 ENSG00000197912
169  ENSG00000171503 NA ETFDH electron-transferring-flavoprotein dehydrogenase 2110 ENSG00000171503
170  ENSG00000143158 NA MPC2 mitochondrial pyruvate carrier 2 25874 ENSG00000143158
171  ENSG00000138796 NA HADH hydroxyacyl-CoA dehydrogenase 3033 ENSG00000138796
172  ENSG00000154518 NA ATP5G3 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C3 (subunit 9) 518 ENSG00000154518
173  ENSG00000075303 NA SLC25A40 solute carrier family 25, member 40 55972 ENSG00000075303
174  ENSG00000176340 NA COX8A cytochrome c oxidase subunit VIIIA (ubiquitous) 1351 ENSG00000176340
175  ENSG00000101247 NA NDUFAF5 NADH dehydrogenase (ubiquinone) complex I, assembly factor 5 79133 ENSG00000101247
176  ENSG00000168653 NA NDUFS5 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) 4725 ENSG00000168653
177  ENSG00000126768 NA TIMM17B translocase of inner mitochondrial membrane 17 homolog B (yeast) 10245 ENSG00000126768
178  ENSG00000247077 NA PGAM5 phosphoglycerate mutase family member 5 192111 ENSG00000247077
179  ENSG00000241837 NA ATP5O ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit 539 ENSG00000241837


Database:cellular component       Name:organelle inner membrane       ID:GO:0019866
C=384; O=153; E=23.31; R=6.56; rawP=2.25e-86; adjP=1.48e-84
Index UserID Value Gene Symbol Gene Name EntrezGene Ensembl
1  ENSG00000164828 NA SUN1 Sad1 and UNC84 domain containing 1 23353 ENSG00000164828
2  ENSG00000087299 NA L2HGDH L-2-hydroxyglutarate dehydrogenase 79944 ENSG00000087299
3  ENSG00000184903 NA IMMP2L IMP2 inner mitochondrial membrane peptidase-like (S. cerevisiae) 83943 ENSG00000184903
4  ENSG00000165264 NA NDUFB6 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa 4712 ENSG00000165264
5  ENSG00000156467 NA UQCRB ubiquinol-cytochrome c reductase binding protein 7381 ENSG00000156467
6  ENSG00000161281 NA COX7A1 cytochrome c oxidase subunit VIIa polypeptide 1 (muscle) 1346 ENSG00000161281
7  ENSG00000184076 NA UQCR10 ubiquinol-cytochrome c reductase, complex III subunit X 29796 ENSG00000184076
8  ENSG00000078070 NA MCCC1 methylcrotonoyl-CoA carboxylase 1 (alpha) 56922 ENSG00000078070
9  ENSG00000075415 NA SLC25A3 solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 3 5250 ENSG00000075415
10  ENSG00000156885 NA COX6A2 cytochrome c oxidase subunit VIa polypeptide 2 1339 ENSG00000156885
11  ENSG00000154723 NA ATP5J ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 522 ENSG00000154723
12  ENSG00000167969 NA ECI1 enoyl-CoA delta isomerase 1 1632 ENSG00000167969
13  ENSG00000125166 NA GOT2 glutamic-oxaloacetic transaminase 2, mitochondrial (aspartate aminotransferase 2) 2806 ENSG00000125166
14  ENSG00000100347 NA SAMM50 sorting and assembly machinery component 50 homolog (S. cerevisiae) 25813 ENSG00000100347
15  ENSG00000135390 NA ATP5G2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C2 (subunit 9) 517 ENSG00000135390
16  ENSG00000177370 NA TIMM22 translocase of inner mitochondrial membrane 22 homolog (yeast) 29928 ENSG00000177370
17  ENSG00000140740 NA UQCRC2 ubiquinol-cytochrome c reductase core protein II 7385 ENSG00000140740
18  ENSG00000166136 NA NDUFB8 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa 4714 ENSG00000166136
19  ENSG00000160194 NA NDUFV3 NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa 4731 ENSG00000160194
20  ENSG00000147684 NA NDUFB9 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa 4715 ENSG00000147684
21  ENSG00000184983 NA NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa 4700 ENSG00000184983
22  ENSG00000130414 NA NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa 4705 ENSG00000130414
23  ENSG00000163626 NA COX18 COX18 cytochrome c oxidase assembly homolog (S. cerevisiae) 285521 ENSG00000163626
24  ENSG00000158864 NA NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) 4720 ENSG00000158864
25  ENSG00000007923 NA DNAJC11 DnaJ (Hsp40) homolog, subfamily C, member 11 55735 ENSG00000007923
26  ENSG00000173436 NA MINOS1 mitochondrial inner membrane organizing system 1 440574 ENSG00000173436
27  ENSG00000105197 NA TIMM50 translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae) 92609 ENSG00000105197
28  ENSG00000109390 NA NDUFC1 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa 4717 ENSG00000109390
29  ENSG00000060762 NA MPC1 mitochondrial pyruvate carrier 1 51660 ENSG00000060762
30  ENSG00000165283 NA STOML2 stomatin (EPB72)-like 2 30968 ENSG00000165283
31  ENSG00000104980 NA TIMM44 translocase of inner mitochondrial membrane 44 homolog (yeast) 10469 ENSG00000104980
32  ENSG00000116459 NA ATP5F1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 515 ENSG00000116459
33  ENSG00000164466 NA SFXN1 sideroflexin 1 94081 ENSG00000164466
34  ENSG00000099800 NA TIMM13 translocase of inner mitochondrial membrane 13 homolog (yeast) 26517 ENSG00000099800
35  ENSG00000151729 NA SLC25A4 solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4 291 ENSG00000151729
36  ENSG00000178057 NA NDUFAF3 NADH dehydrogenase (ubiquinone) complex I, assembly factor 3 25915 ENSG00000178057
37  ENSG00000112992 NA NNT nicotinamide nucleotide transhydrogenase 23530 ENSG00000112992
38  ENSG00000213619 NA NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) 4722 ENSG00000213619
39  ENSG00000178741 NA COX5A cytochrome c oxidase subunit Va 9377 ENSG00000178741
40  ENSG00000173660 NA UQCRH ubiquinol-cytochrome c reductase hinge protein 7388 ENSG00000173660
41  ENSG00000133028 NA SCO1 SCO cytochrome oxidase deficient homolog 1 (yeast) 6341 ENSG00000133028
42  ENSG00000148950 NA IMMP1L IMP1 inner mitochondrial membrane peptidase-like (S. cerevisiae) 196294 ENSG00000148950
43  ENSG00000119421 NA NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa 4702 ENSG00000119421
44  ENSG00000126267 NA COX6B1 cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) 1340 ENSG00000126267
45  ENSG00000109919 NA MTCH2 mitochondrial carrier 2 23788 ENSG00000109919
46  ENSG00000135940 NA COX5B cytochrome c oxidase subunit Vb 1329 ENSG00000135940
47  ENSG00000215021 NA PHB2 prohibitin 2 11331 ENSG00000215021
48  ENSG00000145494 NA NDUFS6 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) 4726 ENSG00000145494
49  ENSG00000167085 NA PHB prohibitin 5245 ENSG00000167085
50  ENSG00000072506 NA HSD17B10 hydroxysteroid (17-beta) dehydrogenase 10 3028 ENSG00000072506
51  ENSG00000156709 NA AIFM1 apoptosis-inducing factor, mitochondrion-associated, 1 9131 ENSG00000156709
52  ENSG00000189043 NA NDUFA4 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa 4697 ENSG00000189043
53  ENSG00000131143 NA COX4I1 cytochrome c oxidase subunit IV isoform 1 1327 ENSG00000131143
54  ENSG00000172115 NA CYCS cytochrome c, somatic 54205 ENSG00000172115
55  ENSG00000164919 NA COX6C cytochrome c oxidase subunit VIc 1345 ENSG00000164919
56  ENSG00000115286 NA NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) 374291 ENSG00000115286
57  ENSG00000164258 NA NDUFS4 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) 4724 ENSG00000164258
58  ENSG00000156170 NA NDUFAF6 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 137682 ENSG00000156170
59  ENSG00000155463 NA OXA1L oxidase (cytochrome c) assembly 1-like 5018 ENSG00000155463
60  ENSG00000167863 NA ATP5H ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d 10476 ENSG00000167863
61  ENSG00000090266 NA NDUFB2 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa 4708 ENSG00000090266
62  ENSG00000127540 NA UQCR11 ubiquinol-cytochrome c reductase, complex III subunit XI 10975 ENSG00000127540
63  ENSG00000179091 NA CYC1 cytochrome c-1 1537 ENSG00000179091
64  ENSG00000184752 NA NDUFA12 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 55967 ENSG00000184752
65  ENSG00000156411 NA C14orf2 chromosome 14 open reading frame 2 9556 ENSG00000156411
66  ENSG00000131844 NA MCCC2 methylcrotonoyl-CoA carboxylase 2 (beta) 64087 ENSG00000131844
67  ENSG00000159199 NA ATP5G1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) 516 ENSG00000159199
68  ENSG00000105819 NA PMPCB peptidase (mitochondrial processing) beta 9512 ENSG00000105819
69  ENSG00000150779 NA TIMM8B translocase of inner mitochondrial membrane 8 homolog B (yeast) 26521 ENSG00000150779
70  ENSG00000166855 NA CLPX ClpX caseinolytic peptidase X homolog (E. coli) 10845 ENSG00000166855
71  ENSG00000074582 NA BCS1L BCS1-like (S. cerevisiae) 617 ENSG00000074582
72  ENSG00000103018 NA CYB5B cytochrome b5 type B (outer mitochondrial membrane) 80777 ENSG00000103018
73  ENSG00000166816 NA LDHD lactate dehydrogenase D 197257 ENSG00000166816
74  ENSG00000140990 NA NDUFB10 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa 4716 ENSG00000140990
75  ENSG00000066926 NA FECH ferrochelatase 2235 ENSG00000066926
76  ENSG00000117118 NA SDHB succinate dehydrogenase complex, subunit B, iron sulfur (Ip) 6390 ENSG00000117118
77  ENSG00000135469 NA COQ10A coenzyme Q10 homolog A (S. cerevisiae) 93058 ENSG00000135469
78  ENSG00000165629 NA ATP5C1 ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 509 ENSG00000165629
79  ENSG00000115944 NA COX7A2L cytochrome c oxidase subunit VIIa polypeptide 2 like 9167 ENSG00000115944
80  ENSG00000148290 NA SURF1 surfeit 1 6834 ENSG00000148290
81  ENSG00000197150 NA ABCB8 ATP-binding cassette, sub-family B (MDR/TAP), member 8 11194 ENSG00000197150
82  ENSG00000152234 NA ATP5A1 ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle 498 ENSG00000152234
83  ENSG00000072778 NA ACADVL acyl-CoA dehydrogenase, very long chain 37 ENSG00000072778
84  ENSG00000151366 NA NDUFC2 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa 4718 ENSG00000151366
85  ENSG00000128609 NA NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa 4698 ENSG00000128609
86  ENSG00000132305 NA IMMT inner membrane protein, mitochondrial 10989 ENSG00000132305
87  ENSG00000163541 NA SUCLG1 succinate-CoA ligase, alpha subunit 8802 ENSG00000163541
88  ENSG00000146701 NA MDH2 malate dehydrogenase 2, NAD (mitochondrial) 4191 ENSG00000146701
89  ENSG00000165678 NA GHITM growth hormone inducible transmembrane protein 27069 ENSG00000165678
90  ENSG00000125995 NA ROMO1 reactive oxygen species modulator 1 140823 ENSG00000125995
91  ENSG00000136521 NA NDUFB5 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa 4711 ENSG00000136521
92  ENSG00000173915 NA USMG5 up-regulated during skeletal muscle growth 5 homolog (mouse) 84833 ENSG00000173915
93  ENSG00000182054 NA IDH2 isocitrate dehydrogenase 2 (NADP+), mitochondrial 3418 ENSG00000182054
94  ENSG00000004779 NA NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa 4706 ENSG00000004779
95  ENSG00000131730 NA CKMT2 creatine kinase, mitochondrial 2 (sarcomeric) 1160 ENSG00000131730
96  ENSG00000169020 NA ATP5I ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E 521 ENSG00000169020
97  ENSG00000004961 NA HCCS holocytochrome c synthase 3052 ENSG00000004961
98  ENSG00000147123 NA NDUFB11 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa 54539 ENSG00000147123
99  ENSG00000073578 NA SDHA succinate dehydrogenase complex, subunit A, flavoprotein (Fp) 6389 ENSG00000073578
100  ENSG00000137714 NA FDX1 ferredoxin 1 2230 ENSG00000137714
101  ENSG00000119013 NA NDUFB3 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa 4709 ENSG00000119013
102  ENSG00000169021 NA UQCRFS1 ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 7386 ENSG00000169021
103  ENSG00000175193 NA PARL presenilin associated, rhomboid-like 55486 ENSG00000175193
104  ENSG00000108179 NA PPIF peptidylprolyl isomerase F 10105 ENSG00000108179
105  ENSG00000139180 NA NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa 4704 ENSG00000139180
106  ENSG00000162600 NA OMA1 OMA1 zinc metallopeptidase homolog (S. cerevisiae) 115209 ENSG00000162600
107  ENSG00000127184 NA COX7C cytochrome c oxidase subunit VIIc 1350 ENSG00000127184
108  ENSG00000164405 NA UQCRQ ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa 27089 ENSG00000164405
109  ENSG00000165637 NA VDAC2 voltage-dependent anion channel 2 7417 ENSG00000165637
110  ENSG00000124172 NA ATP5E ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit 514 ENSG00000124172
111  ENSG00000183648 NA NDUFB1 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa 4707 ENSG00000183648
112  ENSG00000132591 NA ERAL1 Era G-protein-like 1 (E. coli) 26284 ENSG00000132591
113  ENSG00000205981 NA DNAJC19 DnaJ (Hsp40) homolog, subfamily C, member 19 131118 ENSG00000205981
114  ENSG00000213585 NA VDAC1 voltage-dependent anion channel 1 7416 ENSG00000213585
115  ENSG00000204370 NA SDHD succinate dehydrogenase complex, subunit D, integral membrane protein 6392 ENSG00000204370
116  ENSG00000099624 NA ATP5D ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit 513 ENSG00000099624
117  ENSG00000106554 NA CHCHD3 coiled-coil-helix-coiled-coil-helix domain containing 3 54927 ENSG00000106554
118  ENSG00000166949 NA SMAD3 SMAD family member 3 4088 ENSG00000166949
119  ENSG00000125356 NA NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa 4694 ENSG00000125356
120  ENSG00000108528 NA SLC25A11 solute carrier family 25 (mitochondrial carrier; oxoglutarate carrier), member 11 8402 ENSG00000108528
121  ENSG00000099795 NA NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa 4713 ENSG00000099795
122  ENSG00000174032 NA SLC25A30 solute carrier family 25, member 30 253512 ENSG00000174032
123  ENSG00000023228 NA NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) 4719 ENSG00000023228
124  ENSG00000143252 NA SDHC succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa 6391 ENSG00000143252
125  ENSG00000115840 NA SLC25A12 solute carrier family 25 (aspartate/glutamate carrier), member 12 8604 ENSG00000115840
126  ENSG00000110955 NA ATP5B ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide 506 ENSG00000110955
127  ENSG00000197122 NA SRC v-src sarcoma (Schmidt-Ruppin A-2) viral oncogene homolog (avian) 6714 ENSG00000197122
128  ENSG00000112695 NA COX7A2 cytochrome c oxidase subunit VIIa polypeptide 2 (liver) 1347 ENSG00000112695
129  ENSG00000197448 NA GSTK1 glutathione S-transferase kappa 1 373156 ENSG00000197448
130  ENSG00000167792 NA NDUFV1 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa 4723 ENSG00000167792
131  ENSG00000131495 NA NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa 4695 ENSG00000131495
132  ENSG00000065518 NA NDUFB4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa 4710 ENSG00000065518
133  ENSG00000095321 NA CRAT carnitine O-acetyltransferase 1384 ENSG00000095321
134  ENSG00000165688 NA PMPCA peptidase (mitochondrial processing) alpha 23203 ENSG00000165688
135  ENSG00000110717 NA NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) 4728 ENSG00000110717
136  ENSG00000131174 NA COX7B cytochrome c oxidase subunit VIIb 1349 ENSG00000131174
137  ENSG00000170906 NA NDUFA3 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa 4696 ENSG00000170906
138  ENSG00000167283 NA ATP5L ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G 10632 ENSG00000167283
139  ENSG00000124532 NA MRS2 MRS2 magnesium homeostasis factor homolog (S. cerevisiae) 57380 ENSG00000124532
140  ENSG00000131269 NA ABCB7 ATP-binding cassette, sub-family B (MDR/TAP), member 7 22 ENSG00000131269
141  ENSG00000010256 NA UQCRC1 ubiquinol-cytochrome c reductase core protein I 7384 ENSG00000010256
142  ENSG00000137806 NA NDUFAF1 NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 51103 ENSG00000137806
143  ENSG00000241468 NA ATP5J2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 9551 ENSG00000241468
144  ENSG00000171503 NA ETFDH electron-transferring-flavoprotein dehydrogenase 2110 ENSG00000171503
145  ENSG00000143158 NA MPC2 mitochondrial pyruvate carrier 2 25874 ENSG00000143158
146  ENSG00000138796 NA HADH hydroxyacyl-CoA dehydrogenase 3033 ENSG00000138796
147  ENSG00000154518 NA ATP5G3 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C3 (subunit 9) 518 ENSG00000154518
148  ENSG00000075303 NA SLC25A40 solute carrier family 25, member 40 55972 ENSG00000075303
149  ENSG00000176340 NA COX8A cytochrome c oxidase subunit VIIIA (ubiquitous) 1351 ENSG00000176340
150  ENSG00000101247 NA NDUFAF5 NADH dehydrogenase (ubiquinone) complex I, assembly factor 5 79133 ENSG00000101247
151  ENSG00000168653 NA NDUFS5 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) 4725 ENSG00000168653
152  ENSG00000126768 NA TIMM17B translocase of inner mitochondrial membrane 17 homolog B (yeast) 10245 ENSG00000126768
153  ENSG00000241837 NA ATP5O ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit 539 ENSG00000241837


Database:cellular component       Name:mitochondrial membrane       ID:GO:0031966
C=508; O=174; E=30.83; R=5.64; rawP=4.88e-86; adjP=2.76e-84
Index UserID Value Gene Symbol Gene Name EntrezGene Ensembl
1  ENSG00000087299 NA L2HGDH L-2-hydroxyglutarate dehydrogenase 79944 ENSG00000087299
2  ENSG00000184903 NA IMMP2L IMP2 inner mitochondrial membrane peptidase-like (S. cerevisiae) 83943 ENSG00000184903
3  ENSG00000165264 NA NDUFB6 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa 4712 ENSG00000165264
4  ENSG00000156467 NA UQCRB ubiquinol-cytochrome c reductase binding protein 7381 ENSG00000156467
5  ENSG00000161281 NA COX7A1 cytochrome c oxidase subunit VIIa polypeptide 1 (muscle) 1346 ENSG00000161281
6  ENSG00000184076 NA UQCR10 ubiquinol-cytochrome c reductase, complex III subunit X 29796 ENSG00000184076
7  ENSG00000078070 NA MCCC1 methylcrotonoyl-CoA carboxylase 1 (alpha) 56922 ENSG00000078070
8  ENSG00000075415 NA SLC25A3 solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 3 5250 ENSG00000075415
9  ENSG00000156885 NA COX6A2 cytochrome c oxidase subunit VIa polypeptide 2 1339 ENSG00000156885
10  ENSG00000006695 NA COX10 COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) 1352 ENSG00000006695
11  ENSG00000133983 NA COX16 COX16 cytochrome c oxidase assembly homolog (S. cerevisiae) 51241 ENSG00000133983
12  ENSG00000154723 NA ATP5J ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 522 ENSG00000154723
13  ENSG00000167969 NA ECI1 enoyl-CoA delta isomerase 1 1632 ENSG00000167969
14  ENSG00000125166 NA GOT2 glutamic-oxaloacetic transaminase 2, mitochondrial (aspartate aminotransferase 2) 2806 ENSG00000125166
15  ENSG00000100347 NA SAMM50 sorting and assembly machinery component 50 homolog (S. cerevisiae) 25813 ENSG00000100347
16  ENSG00000135390 NA ATP5G2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C2 (subunit 9) 517 ENSG00000135390
17  ENSG00000177370 NA TIMM22 translocase of inner mitochondrial membrane 22 homolog (yeast) 29928 ENSG00000177370
18  ENSG00000140740 NA UQCRC2 ubiquinol-cytochrome c reductase core protein II 7385 ENSG00000140740
19  ENSG00000166136 NA NDUFB8 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa 4714 ENSG00000166136
20  ENSG00000160194 NA NDUFV3 NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa 4731 ENSG00000160194
21  ENSG00000147684 NA NDUFB9 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa 4715 ENSG00000147684
22  ENSG00000184983 NA NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa 4700 ENSG00000184983
23  ENSG00000130414 NA NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa 4705 ENSG00000130414
24  ENSG00000163626 NA COX18 COX18 cytochrome c oxidase assembly homolog (S. cerevisiae) 285521 ENSG00000163626
25  ENSG00000158864 NA NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) 4720 ENSG00000158864
26  ENSG00000007923 NA DNAJC11 DnaJ (Hsp40) homolog, subfamily C, member 11 55735 ENSG00000007923
27  ENSG00000173436 NA MINOS1 mitochondrial inner membrane organizing system 1 440574 ENSG00000173436
28  ENSG00000105197 NA TIMM50 translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae) 92609 ENSG00000105197
29  ENSG00000109390 NA NDUFC1 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa 4717 ENSG00000109390
30  ENSG00000060762 NA MPC1 mitochondrial pyruvate carrier 1 51660 ENSG00000060762
31  ENSG00000165283 NA STOML2 stomatin (EPB72)-like 2 30968 ENSG00000165283
32  ENSG00000104980 NA TIMM44 translocase of inner mitochondrial membrane 44 homolog (yeast) 10469 ENSG00000104980
33  ENSG00000116459 NA ATP5F1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 515 ENSG00000116459
34  ENSG00000164466 NA SFXN1 sideroflexin 1 94081 ENSG00000164466
35  ENSG00000099800 NA TIMM13 translocase of inner mitochondrial membrane 13 homolog (yeast) 26517 ENSG00000099800
36  ENSG00000151729 NA SLC25A4 solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4 291 ENSG00000151729
37  ENSG00000178057 NA NDUFAF3 NADH dehydrogenase (ubiquinone) complex I, assembly factor 3 25915 ENSG00000178057
38  ENSG00000112992 NA NNT nicotinamide nucleotide transhydrogenase 23530 ENSG00000112992
39  ENSG00000213619 NA NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) 4722 ENSG00000213619
40  ENSG00000178741 NA COX5A cytochrome c oxidase subunit Va 9377 ENSG00000178741
41  ENSG00000173660 NA UQCRH ubiquinol-cytochrome c reductase hinge protein 7388 ENSG00000173660
42  ENSG00000214253 NA FIS1 fission 1 (mitochondrial outer membrane) homolog (S. cerevisiae) 51024 ENSG00000214253
43  ENSG00000133028 NA SCO1 SCO cytochrome oxidase deficient homolog 1 (yeast) 6341 ENSG00000133028
44  ENSG00000148950 NA IMMP1L IMP1 inner mitochondrial membrane peptidase-like (S. cerevisiae) 196294 ENSG00000148950
45  ENSG00000119421 NA NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa 4702 ENSG00000119421
46  ENSG00000126267 NA COX6B1 cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) 1340 ENSG00000126267
47  ENSG00000109919 NA MTCH2 mitochondrial carrier 2 23788 ENSG00000109919
48  ENSG00000135940 NA COX5B cytochrome c oxidase subunit Vb 1329 ENSG00000135940
49  ENSG00000215021 NA PHB2 prohibitin 2 11331 ENSG00000215021
50  ENSG00000145494 NA NDUFS6 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) 4726 ENSG00000145494
51  ENSG00000167085 NA PHB prohibitin 5245 ENSG00000167085
52  ENSG00000072506 NA HSD17B10 hydroxysteroid (17-beta) dehydrogenase 10 3028 ENSG00000072506
53  ENSG00000156709 NA AIFM1 apoptosis-inducing factor, mitochondrion-associated, 1 9131 ENSG00000156709
54  ENSG00000189043 NA NDUFA4 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa 4697 ENSG00000189043
55  ENSG00000131143 NA COX4I1 cytochrome c oxidase subunit IV isoform 1 1327 ENSG00000131143
56  ENSG00000172115 NA CYCS cytochrome c, somatic 54205 ENSG00000172115
57  ENSG00000164919 NA COX6C cytochrome c oxidase subunit VIc 1345 ENSG00000164919
58  ENSG00000115286 NA NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) 374291 ENSG00000115286
59  ENSG00000164258 NA NDUFS4 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) 4724 ENSG00000164258
60  ENSG00000156170 NA NDUFAF6 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 137682 ENSG00000156170
61  ENSG00000155463 NA OXA1L oxidase (cytochrome c) assembly 1-like 5018 ENSG00000155463
62  ENSG00000167863 NA ATP5H ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d 10476 ENSG00000167863
63  ENSG00000090266 NA NDUFB2 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa 4708 ENSG00000090266
64  ENSG00000127540 NA UQCR11 ubiquinol-cytochrome c reductase, complex III subunit XI 10975 ENSG00000127540
65  ENSG00000179091 NA CYC1 cytochrome c-1 1537 ENSG00000179091
66  ENSG00000184752 NA NDUFA12 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 55967 ENSG00000184752
67  ENSG00000156411 NA C14orf2 chromosome 14 open reading frame 2 9556 ENSG00000156411
68  ENSG00000131844 NA MCCC2 methylcrotonoyl-CoA carboxylase 2 (beta) 64087 ENSG00000131844
69  ENSG00000159199 NA ATP5G1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) 516 ENSG00000159199
70  ENSG00000105819 NA PMPCB peptidase (mitochondrial processing) beta 9512 ENSG00000105819
71  ENSG00000150779 NA TIMM8B translocase of inner mitochondrial membrane 8 homolog B (yeast) 26521 ENSG00000150779
72  ENSG00000166855 NA CLPX ClpX caseinolytic peptidase X homolog (E. coli) 10845 ENSG00000166855
73  ENSG00000196683 NA TOMM7 translocase of outer mitochondrial membrane 7 homolog (yeast) 54543 ENSG00000196683
74  ENSG00000074582 NA BCS1L BCS1-like (S. cerevisiae) 617 ENSG00000074582
75  ENSG00000103018 NA CYB5B cytochrome b5 type B (outer mitochondrial membrane) 80777 ENSG00000103018
76  ENSG00000166816 NA LDHD lactate dehydrogenase D 197257 ENSG00000166816
77  ENSG00000140990 NA NDUFB10 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa 4716 ENSG00000140990
78  ENSG00000066926 NA FECH ferrochelatase 2235 ENSG00000066926
79  ENSG00000117118 NA SDHB succinate dehydrogenase complex, subunit B, iron sulfur (Ip) 6390 ENSG00000117118
80  ENSG00000198523 NA PLN phospholamban 5350 ENSG00000198523
81  ENSG00000006530 NA AGK acylglycerol kinase 55750 ENSG00000006530
82  ENSG00000135469 NA COQ10A coenzyme Q10 homolog A (S. cerevisiae) 93058 ENSG00000135469
83  ENSG00000177427 NA SMCR7 Smith-Magenis syndrome chromosome region, candidate 7 125170 ENSG00000177427
84  ENSG00000165629 NA ATP5C1 ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 509 ENSG00000165629
85  ENSG00000115944 NA COX7A2L cytochrome c oxidase subunit VIIa polypeptide 2 like 9167 ENSG00000115944
86  ENSG00000123545 NA NDUFAF4 NADH dehydrogenase (ubiquinone) complex I, assembly factor 4 29078 ENSG00000123545
87  ENSG00000148290 NA SURF1 surfeit 1 6834 ENSG00000148290
88  ENSG00000197150 NA ABCB8 ATP-binding cassette, sub-family B (MDR/TAP), member 8 11194 ENSG00000197150
89  ENSG00000152234 NA ATP5A1 ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle 498 ENSG00000152234
90  ENSG00000072778 NA ACADVL acyl-CoA dehydrogenase, very long chain 37 ENSG00000072778
91  ENSG00000151366 NA NDUFC2 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa 4718 ENSG00000151366
92  ENSG00000128609 NA NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa 4698 ENSG00000128609
93  ENSG00000132305 NA IMMT inner membrane protein, mitochondrial 10989 ENSG00000132305
94  ENSG00000163541 NA SUCLG1 succinate-CoA ligase, alpha subunit 8802 ENSG00000163541
95  ENSG00000090432 NA MUL1 mitochondrial E3 ubiquitin protein ligase 1 79594 ENSG00000090432
96  ENSG00000146701 NA MDH2 malate dehydrogenase 2, NAD (mitochondrial) 4191 ENSG00000146701
97  ENSG00000165678 NA GHITM growth hormone inducible transmembrane protein 27069 ENSG00000165678
98  ENSG00000125995 NA ROMO1 reactive oxygen species modulator 1 140823 ENSG00000125995
99  ENSG00000136521 NA NDUFB5 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa 4711 ENSG00000136521
100  ENSG00000173915 NA USMG5 up-regulated during skeletal muscle growth 5 homolog (mouse) 84833 ENSG00000173915
101  ENSG00000169020 NA ATP5I ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E 521 ENSG00000169020
102  ENSG00000158882 NA TOMM40L translocase of outer mitochondrial membrane 40 homolog (yeast)-like 84134 ENSG00000158882
103  ENSG00000182054 NA IDH2 isocitrate dehydrogenase 2 (NADP+), mitochondrial 3418 ENSG00000182054
104  ENSG00000004779 NA NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa 4706 ENSG00000004779
105  ENSG00000131730 NA CKMT2 creatine kinase, mitochondrial 2 (sarcomeric) 1160 ENSG00000131730
106  ENSG00000168958 NA MFF mitochondrial fission factor 56947 ENSG00000168958
107  ENSG00000164038 NA SLC9B2 solute carrier family 9, subfamily B (NHA2, cation proton antiporter 2), member 2 133308 ENSG00000164038
108  ENSG00000004961 NA HCCS holocytochrome c synthase 3052 ENSG00000004961
109  ENSG00000147123 NA NDUFB11 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa 54539 ENSG00000147123
110  ENSG00000073578 NA SDHA succinate dehydrogenase complex, subunit A, flavoprotein (Fp) 6389 ENSG00000073578
111  ENSG00000137714 NA FDX1 ferredoxin 1 2230 ENSG00000137714
112  ENSG00000119013 NA NDUFB3 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa 4709 ENSG00000119013
113  ENSG00000169021 NA UQCRFS1 ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 7386 ENSG00000169021
114  ENSG00000178449 NA COX14 COX14 cytochrome c oxidase assembly homolog (S. cerevisiae) 84987 ENSG00000178449
115  ENSG00000175193 NA PARL presenilin associated, rhomboid-like 55486 ENSG00000175193
116  ENSG00000078668 NA VDAC3 voltage-dependent anion channel 3 7419 ENSG00000078668
117  ENSG00000111843 NA TMEM14C transmembrane protein 14C 51522 ENSG00000111843
118  ENSG00000108179 NA PPIF peptidylprolyl isomerase F 10105 ENSG00000108179
119  ENSG00000139180 NA NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa 4704 ENSG00000139180
120  ENSG00000162600 NA OMA1 OMA1 zinc metallopeptidase homolog (S. cerevisiae) 115209 ENSG00000162600
121  ENSG00000127184 NA COX7C cytochrome c oxidase subunit VIIc 1350 ENSG00000127184
122  ENSG00000164405 NA UQCRQ ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa 27089 ENSG00000164405
123  ENSG00000165637 NA VDAC2 voltage-dependent anion channel 2 7417 ENSG00000165637
124  ENSG00000173085 NA COQ2 coenzyme Q2 homolog, prenyltransferase (yeast) 27235 ENSG00000173085
125  ENSG00000124172 NA ATP5E ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit 514 ENSG00000124172
126  ENSG00000183648 NA NDUFB1 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa 4707 ENSG00000183648
127  ENSG00000213585 NA VDAC1 voltage-dependent anion channel 1 7416 ENSG00000213585
128  ENSG00000205981 NA DNAJC19 DnaJ (Hsp40) homolog, subfamily C, member 19 131118 ENSG00000205981
129  ENSG00000132591 NA ERAL1 Era G-protein-like 1 (E. coli) 26284 ENSG00000132591
130  ENSG00000204370 NA SDHD succinate dehydrogenase complex, subunit D, integral membrane protein 6392 ENSG00000204370
131  ENSG00000099624 NA ATP5D ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit 513 ENSG00000099624
132  ENSG00000106554 NA CHCHD3 coiled-coil-helix-coiled-coil-helix domain containing 3 54927 ENSG00000106554
133  ENSG00000125356 NA NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa 4694 ENSG00000125356
134  ENSG00000108528 NA SLC25A11 solute carrier family 25 (mitochondrial carrier; oxoglutarate carrier), member 11 8402 ENSG00000108528
135  ENSG00000099795 NA NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa 4713 ENSG00000099795
136  ENSG00000174032 NA SLC25A30 solute carrier family 25, member 30 253512 ENSG00000174032
137  ENSG00000023228 NA NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) 4719 ENSG00000023228
138  ENSG00000143252 NA SDHC succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa 6391 ENSG00000143252
139  ENSG00000075336 NA TIMM21 translocase of inner mitochondrial membrane 21 homolog (yeast) 29090 ENSG00000075336
140  ENSG00000115840 NA SLC25A12 solute carrier family 25 (aspartate/glutamate carrier), member 12 8604 ENSG00000115840
141  ENSG00000110955 NA ATP5B ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide 506 ENSG00000110955
142  ENSG00000197122 NA SRC v-src sarcoma (Schmidt-Ruppin A-2) viral oncogene homolog (avian) 6714 ENSG00000197122
143  ENSG00000112695 NA COX7A2 cytochrome c oxidase subunit VIIa polypeptide 2 (liver) 1347 ENSG00000112695
144  ENSG00000197448 NA GSTK1 glutathione S-transferase kappa 1 373156 ENSG00000197448
145  ENSG00000167792 NA NDUFV1 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa 4723 ENSG00000167792
146  ENSG00000131495 NA NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa 4695 ENSG00000131495
147  ENSG00000065518 NA NDUFB4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa 4710 ENSG00000065518
148  ENSG00000095321 NA CRAT carnitine O-acetyltransferase 1384 ENSG00000095321
149  ENSG00000165688 NA PMPCA peptidase (mitochondrial processing) alpha 23203 ENSG00000165688
150  ENSG00000110717 NA NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) 4728 ENSG00000110717
151  ENSG00000131174 NA COX7B cytochrome c oxidase subunit VIIb 1349 ENSG00000131174
152  ENSG00000170906 NA NDUFA3 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa 4696 ENSG00000170906
153  ENSG00000128654 NA MTX2 metaxin 2 10651 ENSG00000128654
154  ENSG00000204308 NA RNF5 ring finger protein 5, E3 ubiquitin protein ligase 6048 ENSG00000204308
155  ENSG00000167283 NA ATP5L ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G 10632 ENSG00000167283
156  ENSG00000069509 NA FUNDC1 FUN14 domain containing 1 139341 ENSG00000069509
157  ENSG00000183978 NA COA3 cytochrome C oxidase assembly factor 3 28958 ENSG00000183978
158  ENSG00000124532 NA MRS2 MRS2 magnesium homeostasis factor homolog (S. cerevisiae) 57380 ENSG00000124532
159  ENSG00000131269 NA ABCB7 ATP-binding cassette, sub-family B (MDR/TAP), member 7 22 ENSG00000131269
160  ENSG00000010256 NA UQCRC1 ubiquinol-cytochrome c reductase core protein I 7384 ENSG00000010256
161  ENSG00000137806 NA NDUFAF1 NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 51103 ENSG00000137806
162  ENSG00000241468 NA ATP5J2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 9551 ENSG00000241468
163  ENSG00000197912 NA SPG7 spastic paraplegia 7 (pure and complicated autosomal recessive) 6687 ENSG00000197912
164  ENSG00000171503 NA ETFDH electron-transferring-flavoprotein dehydrogenase 2110 ENSG00000171503
165  ENSG00000143158 NA MPC2 mitochondrial pyruvate carrier 2 25874 ENSG00000143158
166  ENSG00000138796 NA HADH hydroxyacyl-CoA dehydrogenase 3033 ENSG00000138796
167  ENSG00000154518 NA ATP5G3 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C3 (subunit 9) 518 ENSG00000154518
168  ENSG00000075303 NA SLC25A40 solute carrier family 25, member 40 55972 ENSG00000075303
169  ENSG00000176340 NA COX8A cytochrome c oxidase subunit VIIIA (ubiquitous) 1351 ENSG00000176340
170  ENSG00000101247 NA NDUFAF5 NADH dehydrogenase (ubiquinone) complex I, assembly factor 5 79133 ENSG00000101247
171  ENSG00000168653 NA NDUFS5 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) 4725 ENSG00000168653
172  ENSG00000126768 NA TIMM17B translocase of inner mitochondrial membrane 17 homolog B (yeast) 10245 ENSG00000126768
173  ENSG00000247077 NA PGAM5 phosphoglycerate mutase family member 5 192111 ENSG00000247077
174  ENSG00000241837 NA ATP5O ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit 539 ENSG00000241837


Database:cellular component       Name:cytoplasmic part       ID:GO:0044444
C=6772; O=698; E=411.01; R=1.70; rawP=3.35e-77; adjP=1.66e-75
Index UserID Value Gene Symbol Gene Name EntrezGene Ensembl
1  ENSG00000143575 NA HAX1 HCLS1 associated protein X-1 10456 ENSG00000143575
2  ENSG00000168803 NA ADAL adenosine deaminase-like 161823 ENSG00000168803
3  ENSG00000116898 NA MRPS15 mitochondrial ribosomal protein S15 64960 ENSG00000116898
4  ENSG00000148672 NA GLUD1 glutamate dehydrogenase 1 2746 ENSG00000148672
5  ENSG00000147592 NA LACTB2 lactamase, beta 2 51110 ENSG00000147592
6  ENSG00000164172 NA MOCS2 molybdenum cofactor synthesis 2 4338 ENSG00000164172
7  ENSG00000239264 NA TXNDC5 thioredoxin domain containing 5 (endoplasmic reticulum) 81567 ENSG00000239264
8  ENSG00000170296 NA GABARAP GABA(A) receptor-associated protein 11337 ENSG00000170296
9  ENSG00000135390 NA ATP5G2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C2 (subunit 9) 517 ENSG00000135390
10  ENSG00000134109 NA EDEM1 ER degradation enhancer, mannosidase alpha-like 1 9695 ENSG00000134109
11  ENSG00000177370 NA TIMM22 translocase of inner mitochondrial membrane 22 homolog (yeast) 29928 ENSG00000177370
12  ENSG00000003509 NA C2orf56 chromosome 2 open reading frame 56 55471 ENSG00000003509
13  ENSG00000116353 NA MECR mitochondrial trans-2-enoyl-CoA reductase 51102 ENSG00000116353
14  ENSG00000010282 NA HHATL hedgehog acyltransferase-like 57467 ENSG00000010282
15  ENSG00000205707 NA LYRM5 LYR motif containing 5 144363 ENSG00000205707
16  ENSG00000165060 NA FXN frataxin 2395 ENSG00000165060
17  ENSG00000173141 NA MRP63 mitochondrial ribosomal protein 63 78988 ENSG00000173141
18  ENSG00000109390 NA NDUFC1 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa 4717 ENSG00000109390
19  ENSG00000125868 NA DSTN destrin (actin depolymerizing factor) 11034 ENSG00000125868
20  ENSG00000143314 NA MRPL24 mitochondrial ribosomal protein L24 79590 ENSG00000143314
21  ENSG00000123384 NA LRP1 low density lipoprotein receptor-related protein 1 4035 ENSG00000123384
22  ENSG00000103160 NA HSDL1 hydroxysteroid dehydrogenase like 1 83693 ENSG00000103160
23  ENSG00000055950 NA MRPL43 mitochondrial ribosomal protein L43 84545 ENSG00000055950
24  ENSG00000164054 NA SHISA5 shisa homolog 5 (Xenopus laevis) 51246 ENSG00000164054
25  ENSG00000135218 NA CD36 CD36 molecule (thrombospondin receptor) 948 ENSG00000135218
26  ENSG00000142082 NA SIRT3 sirtuin 3 23410 ENSG00000142082
27  ENSG00000135070 NA ISCA1 iron-sulfur cluster assembly 1 homolog (S. cerevisiae) 81689 ENSG00000135070
28  ENSG00000127838 NA PNKD paroxysmal nonkinesigenic dyskinesia 25953 ENSG00000127838
29  ENSG00000204568 NA MRPS18B mitochondrial ribosomal protein S18B 28973 ENSG00000204568
30  ENSG00000148334 NA PTGES2 prostaglandin E synthase 2 80142 ENSG00000148334
31  ENSG00000165283 NA STOML2 stomatin (EPB72)-like 2 30968 ENSG00000165283
32  ENSG00000185627 NA PSMD13 proteasome (prosome, macropain) 26S subunit, non-ATPase, 13 5719 ENSG00000185627
33  ENSG00000117697 NA NSL1 NSL1, MIND kinetochore complex component, homolog (S. cerevisiae) 25936 ENSG00000117697
34  ENSG00000149925 NA ALDOA aldolase A, fructose-bisphosphate 226 ENSG00000149925
35  ENSG00000126432 NA PRDX5 peroxiredoxin 5 25824 ENSG00000126432
36  ENSG00000023330 NA ALAS1 aminolevulinate, delta-, synthase 1 211 ENSG00000023330
37  ENSG00000213619 NA NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) 4722 ENSG00000213619
38  ENSG00000178741 NA COX5A cytochrome c oxidase subunit Va 9377 ENSG00000178741
39  ENSG00000109180 NA OCIAD1 OCIA domain containing 1 54940 ENSG00000109180
40  ENSG00000214253 NA FIS1 fission 1 (mitochondrial outer membrane) homolog (S. cerevisiae) 51024 ENSG00000214253
41  ENSG00000147586 NA MRPS28 mitochondrial ribosomal protein S28 28957 ENSG00000147586
42  ENSG00000124570 NA SERPINB6 serpin peptidase inhibitor, clade B (ovalbumin), member 6 5269 ENSG00000124570
43  ENSG00000169288 NA MRPL1 mitochondrial ribosomal protein L1 65008 ENSG00000169288
44  ENSG00000160221 NA C21orf33 chromosome 21 open reading frame 33 8209 ENSG00000160221
45  ENSG00000114854 NA TNNC1 troponin C type 1 (slow) 7134 ENSG00000114854
46  ENSG00000109919 NA MTCH2 mitochondrial carrier 2 23788 ENSG00000109919
47  ENSG00000143436 NA MRPL9 mitochondrial ribosomal protein L9 65005 ENSG00000143436
48  ENSG00000122140 NA MRPS2 mitochondrial ribosomal protein S2 51116 ENSG00000122140
49  ENSG00000174175 NA SELP selectin P (granule membrane protein 140kDa, antigen CD62) 6403 ENSG00000174175
50  ENSG00000243279 NA PRAF2 PRA1 domain family, member 2 11230 ENSG00000243279
51  ENSG00000156709 NA AIFM1 apoptosis-inducing factor, mitochondrion-associated, 1 9131 ENSG00000156709
52  ENSG00000123739 NA PLA2G12A phospholipase A2, group XIIA 81579 ENSG00000123739
53  ENSG00000164919 NA COX6C cytochrome c oxidase subunit VIc 1345 ENSG00000164919
54  ENSG00000102871 NA TRADD TNFRSF1A-associated via death domain 8717 ENSG00000102871
55  ENSG00000196465 NA MYL6B myosin, light chain 6B, alkali, smooth muscle and non-muscle 140465 ENSG00000196465
56  ENSG00000139131 NA YARS2 tyrosyl-tRNA synthetase 2, mitochondrial 51067 ENSG00000139131
57  ENSG00000132570 NA PCBD2 pterin-4 alpha-carbinolamine dehydratase/dimerization cofactor of hepatocyte nuclear factor 1 alpha (TCF1) 2 84105 ENSG00000132570
58  ENSG00000121766 NA ZCCHC17 zinc finger, CCHC domain containing 17 51538 ENSG00000121766
59  ENSG00000167863 NA ATP5H ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d 10476 ENSG00000167863
60  ENSG00000130203 NA APOE apolipoprotein E 348 ENSG00000130203
61  ENSG00000166165 NA CKB creatine kinase, brain 1152 ENSG00000166165
62  ENSG00000127540 NA UQCR11 ubiquinol-cytochrome c reductase, complex III subunit XI 10975 ENSG00000127540
63  ENSG00000197345 NA MRPL21 mitochondrial ribosomal protein L21 219927 ENSG00000197345
64  ENSG00000184752 NA NDUFA12 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 55967 ENSG00000184752
65  ENSG00000132423 NA COQ3 coenzyme Q3 homolog, methyltransferase (S. cerevisiae) 51805 ENSG00000132423
66  ENSG00000156411 NA C14orf2 chromosome 14 open reading frame 2 9556 ENSG00000156411
67  ENSG00000070756 NA PABPC1 poly(A) binding protein, cytoplasmic 1 26986 ENSG00000070756
68  ENSG00000131844 NA MCCC2 methylcrotonoyl-CoA carboxylase 2 (beta) 64087 ENSG00000131844
69  ENSG00000173511 NA VEGFB vascular endothelial growth factor B 7423 ENSG00000173511
70  ENSG00000134905 NA CARS2 cysteinyl-tRNA synthetase 2, mitochondrial (putative) 79587 ENSG00000134905
71  ENSG00000150779 NA TIMM8B translocase of inner mitochondrial membrane 8 homolog B (yeast) 26521 ENSG00000150779
72  ENSG00000204228 NA HSD17B8 hydroxysteroid (17-beta) dehydrogenase 8 7923 ENSG00000204228
73  ENSG00000179152 NA TCAIM T cell activation inhibitor, mitochondrial 285343 ENSG00000179152
74  ENSG00000067829 NA IDH3G isocitrate dehydrogenase 3 (NAD+) gamma 3421 ENSG00000067829
75  ENSG00000166902 NA MRPL16 mitochondrial ribosomal protein L16 54948 ENSG00000166902
76  ENSG00000143742 NA SRP9 signal recognition particle 9kDa 6726 ENSG00000143742
77  ENSG00000198523 NA PLN phospholamban 5350 ENSG00000198523
78  ENSG00000247626 NA MARS2 methionyl-tRNA synthetase 2, mitochondrial 92935 ENSG00000247626
79  ENSG00000120662 NA MTRF1 mitochondrial translational release factor 1 9617 ENSG00000120662
80  ENSG00000006530 NA AGK acylglycerol kinase 55750 ENSG00000006530
81  ENSG00000126602 NA TRAP1 TNF receptor-associated protein 1 10131 ENSG00000126602
82  ENSG00000165629 NA ATP5C1 ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 509 ENSG00000165629
83  ENSG00000224877 NA C17orf89 chromosome 17 open reading frame 89 284184 ENSG00000224877
84  ENSG00000170860 NA LSM3 LSM3 homolog, U6 small nuclear RNA associated (S. cerevisiae) 27258 ENSG00000170860
85  ENSG00000148290 NA SURF1 surfeit 1 6834 ENSG00000148290
86  ENSG00000014641 NA MDH1 malate dehydrogenase 1, NAD (soluble) 4190 ENSG00000014641
87  ENSG00000170634 NA ACYP2 acylphosphatase 2, muscle type 98 ENSG00000170634
88  ENSG00000154930 NA ACSS1 acyl-CoA synthetase short-chain family member 1 84532 ENSG00000154930
89  ENSG00000054148 NA PHPT1 phosphohistidine phosphatase 1 29085 ENSG00000054148
90  ENSG00000140319 NA SRP14 signal recognition particle 14kDa (homologous Alu RNA binding protein) 6727 ENSG00000140319
91  ENSG00000125652 NA ALKBH7 alkB, alkylation repair homolog 7 (E. coli) 84266 ENSG00000125652
92  ENSG00000196636 NA ACN9 ACN9 homolog (S. cerevisiae) 57001 ENSG00000196636
93  ENSG00000139410 NA SDSL serine dehydratase-like 113675 ENSG00000139410
94  ENSG00000059691 NA PET112 PET112 homolog (yeast) 5188 ENSG00000059691
95  ENSG00000187239 NA FNBP1 formin binding protein 1 23048 ENSG00000187239
96  ENSG00000125995 NA ROMO1 reactive oxygen species modulator 1 140823 ENSG00000125995
97  ENSG00000114021 NA NIT2 nitrilase family, member 2 56954 ENSG00000114021
98  ENSG00000168958 NA MFF mitochondrial fission factor 56947 ENSG00000168958
99  ENSG00000120253 NA NUP43 nucleoporin 43kDa 348995 ENSG00000120253
100  ENSG00000085871 NA MGST2 microsomal glutathione S-transferase 2 4258 ENSG00000085871
101  ENSG00000172954 NA LCLAT1 lysocardiolipin acyltransferase 1 253558 ENSG00000172954
102  ENSG00000119013 NA NDUFB3 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa 4709 ENSG00000119013
103  ENSG00000132463 NA GRSF1 G-rich RNA sequence binding factor 1 2926 ENSG00000132463
104  ENSG00000259494 NA MRPL46 mitochondrial ribosomal protein L46 26589 ENSG00000259494
105  ENSG00000116586 NA LAMTOR2 late endosomal/lysosomal adaptor, MAPK and MTOR activator 2 28956 ENSG00000116586
106  ENSG00000165487 NA EFHA1 EF-hand domain family, member A1 221154 ENSG00000165487
107  ENSG00000078668 NA VDAC3 voltage-dependent anion channel 3 7419 ENSG00000078668
108  ENSG00000144827 NA ABHD10 abhydrolase domain containing 10 55347 ENSG00000144827
109  ENSG00000173786 NA CNP 2',3'-cyclic nucleotide 3' phosphodiesterase 1267 ENSG00000173786
110  ENSG00000171130 NA ATP6V0E2 ATPase, H+ transporting V0 subunit e2 155066 ENSG00000171130
111  ENSG00000143669 NA LYST lysosomal trafficking regulator 1130 ENSG00000143669
112  ENSG00000139180 NA NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa 4704 ENSG00000139180
113  ENSG00000111640 NA GAPDH glyceraldehyde-3-phosphate dehydrogenase 2597 ENSG00000111640
114  ENSG00000135480 NA KRT7 keratin 7 3855 ENSG00000135480
115  ENSG00000123836 NA PFKFB2 6-phosphofructo-2-kinase/fructose-2,6-biphosphatase 2 5208 ENSG00000123836
116  ENSG00000130208 NA APOC1 apolipoprotein C-I 341 ENSG00000130208
117  ENSG00000187118 NA CMC1 COX assembly mitochondrial protein 1 homolog (S. cerevisiae) 152100 ENSG00000187118
118  ENSG00000172878 NA METAP1D methionyl aminopeptidase type 1D (mitochondrial) 254042 ENSG00000172878
119  ENSG00000204370 NA SDHD succinate dehydrogenase complex, subunit D, integral membrane protein 6392 ENSG00000204370
120  ENSG00000106554 NA CHCHD3 coiled-coil-helix-coiled-coil-helix domain containing 3 54927 ENSG00000106554
121  ENSG00000137106 NA GRHPR glyoxylate reductase/hydroxypyruvate reductase 9380 ENSG00000137106
122  ENSG00000107863 NA ARHGAP21 Rho GTPase activating protein 21 57584 ENSG00000107863
123  ENSG00000027001 NA MIPEP mitochondrial intermediate peptidase 4285 ENSG00000027001
124  ENSG00000110048 NA OSBP oxysterol binding protein 5007 ENSG00000110048
125  ENSG00000182180 NA MRPS16 mitochondrial ribosomal protein S16 51021 ENSG00000182180
126  ENSG00000174032 NA SLC25A30 solute carrier family 25, member 30 253512 ENSG00000174032
127  ENSG00000066583 NA ISOC1 isochorismatase domain containing 1 51015 ENSG00000066583
128  ENSG00000111669 NA TPI1 triosephosphate isomerase 1 7167 ENSG00000111669
129  ENSG00000175756 NA AURKAIP1 aurora kinase A interacting protein 1 54998 ENSG00000175756
130  ENSG00000138823 NA MTTP microsomal triglyceride transfer protein 4547 ENSG00000138823
131  ENSG00000143252 NA SDHC succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa 6391 ENSG00000143252
132  ENSG00000100116 NA GCAT glycine C-acetyltransferase 23464 ENSG00000100116
133  ENSG00000151376 NA ME3 malic enzyme 3, NADP(+)-dependent, mitochondrial 10873 ENSG00000151376
134  ENSG00000186318 NA BACE1 beta-site APP-cleaving enzyme 1 23621 ENSG00000265969 ENSG00000186318
135  ENSG00000165775 NA FUNDC2 FUN14 domain containing 2 65991 ENSG00000165775
136  ENSG00000182606 NA TRAK1 trafficking protein, kinesin binding 1 22906 ENSG00000182606
137  ENSG00000110955 NA ATP5B ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide 506 ENSG00000110955
138  ENSG00000134248 NA LAMTOR5 late endosomal/lysosomal adaptor, MAPK and MTOR activator 5 10542 ENSG00000134248
139  ENSG00000065518 NA NDUFB4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa 4710 ENSG00000065518
140  ENSG00000159445 NA THEM4 thioesterase superfamily member 4 117145 ENSG00000159445
141  ENSG00000198721 NA ECI2 enoyl-CoA delta isomerase 2 10455 ENSG00000198721
142  ENSG00000197580 NA BCO2 beta-carotene oxygenase 2 83875 ENSG00000197580
143  ENSG00000147853 NA AK3 adenylate kinase 3 50808 ENSG00000147853
144  ENSG00000131174 NA COX7B cytochrome c oxidase subunit VIIb 1349 ENSG00000131174
145  ENSG00000106305 NA AIMP2 aminoacyl tRNA synthetase complex-interacting multifunctional protein 2 7965 ENSG00000106305
146  ENSG00000111716 NA LDHB lactate dehydrogenase B 3945 ENSG00000111716
147  ENSG00000142507 NA PSMB6 proteasome (prosome, macropain) subunit, beta type, 6 5694 ENSG00000142507
148  ENSG00000069509 NA FUNDC1 FUN14 domain containing 1 139341 ENSG00000069509
149  ENSG00000167799 NA NUDT8 nudix (nucleoside diphosphate linked moiety X)-type motif 8 254552 ENSG00000167799
150  ENSG00000124532 NA MRS2 MRS2 magnesium homeostasis factor homolog (S. cerevisiae) 57380 ENSG00000124532
151  ENSG00000048544 NA MRPS10 mitochondrial ribosomal protein S10 55173 ENSG00000048544
152  ENSG00000131269 NA ABCB7 ATP-binding cassette, sub-family B (MDR/TAP), member 7 22 ENSG00000131269
153  ENSG00000051620 NA HEBP2 heme binding protein 2 23593 ENSG00000051620
154  ENSG00000137806 NA NDUFAF1 NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 51103 ENSG00000137806
155  ENSG00000171503 NA ETFDH electron-transferring-flavoprotein dehydrogenase 2110 ENSG00000171503
156  ENSG00000227345 NA PARG poly (ADP-ribose) glycohydrolase 8505 ENSG00000227345
157  ENSG00000161533 NA ACOX1 acyl-CoA oxidase 1, palmitoyl 51 ENSG00000161533
158  ENSG00000107317 NA PTGDS prostaglandin D2 synthase 21kDa (brain) 5730 ENSG00000107317
159  ENSG00000118473 NA SGIP1 SH3-domain GRB2-like (endophilin) interacting protein 1 84251 ENSG00000118473
160  ENSG00000155368 NA DBI diazepam binding inhibitor (GABA receptor modulator, acyl-CoA binding protein) 1622 ENSG00000155368
161  ENSG00000126768 NA TIMM17B translocase of inner mitochondrial membrane 17 homolog B (yeast) 10245 ENSG00000126768
162  ENSG00000101019 NA UQCC ubiquinol-cytochrome c reductase complex chaperone 55245 ENSG00000101019
163  ENSG00000143553 NA SNAPIN SNAP-associated protein 23557 ENSG00000143553
164  ENSG00000163864 NA NMNAT3 nicotinamide nucleotide adenylyltransferase 3 349565 ENSG00000163864
165  ENSG00000156467 NA UQCRB ubiquinol-cytochrome c reductase binding protein 7381 ENSG00000156467
166  ENSG00000123297 NA TSFM Ts translation elongation factor, mitochondrial 10102 ENSG00000123297
167  ENSG00000078070 NA MCCC1 methylcrotonoyl-CoA carboxylase 1 (alpha) 56922 ENSG00000078070
168  ENSG00000156885 NA COX6A2 cytochrome c oxidase subunit VIa polypeptide 2 1339 ENSG00000156885
169  ENSG00000115884 NA SDC1 syndecan 1 6382 ENSG00000115884
170  ENSG00000006695 NA COX10 COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) 1352 ENSG00000006695
171  ENSG00000123472 NA ATPAF1 ATP synthase mitochondrial F1 complex assembly factor 1 64756 ENSG00000123472
172  ENSG00000139531 NA SUOX sulfite oxidase 6821 ENSG00000139531
173  ENSG00000198876 NA DCAF12 DDB1 and CUL4 associated factor 12 25853 ENSG00000198876
174  ENSG00000114988 NA LMAN2L lectin, mannose-binding 2-like 81562 ENSG00000114988
175  ENSG00000161558 NA TMEM143 transmembrane protein 143 55260 ENSG00000161558
176  ENSG00000140374 NA ETFA electron-transfer-flavoprotein, alpha polypeptide 2108 ENSG00000140374
177  ENSG00000102309 NA PIN4 protein (peptidylprolyl cis/trans isomerase) NIMA-interacting, 4 (parvulin) 5303 ENSG00000102309
178  ENSG00000173436 NA MINOS1 mitochondrial inner membrane organizing system 1 440574 ENSG00000173436
179  ENSG00000135537 NA LACE1 lactation elevated 1 246269 ENSG00000135537
180  ENSG00000116221 NA MRPL37 mitochondrial ribosomal protein L37 51253 ENSG00000116221
181  ENSG00000262814 NA MRPL12 mitochondrial ribosomal protein L12 6182 ENSG00000262814
182  ENSG00000181929 NA PRKAG1 protein kinase, AMP-activated, gamma 1 non-catalytic subunit 5571 ENSG00000181929
183  ENSG00000076043 NA REXO2 REX2, RNA exonuclease 2 homolog (S. cerevisiae) 25996 ENSG00000076043
184  ENSG00000069998 NA CECR5 cat eye syndrome chromosome region, candidate 5 27440 ENSG00000069998
185  ENSG00000112715 NA VEGFA vascular endothelial growth factor A 7422 ENSG00000112715
186  ENSG00000147813 NA NAPRT1 nicotinate phosphoribosyltransferase domain containing 1 93100 ENSG00000147813
187  ENSG00000119689 NA DLST dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex) 1743 ENSG00000119689
188  ENSG00000168291 NA PDHB pyruvate dehydrogenase (lipoamide) beta 5162 ENSG00000168291
189  ENSG00000156502 NA SUPV3L1 suppressor of var1, 3-like 1 (S. cerevisiae) 6832 ENSG00000156502
190  ENSG00000116459 NA ATP5F1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 515 ENSG00000116459
191  ENSG00000187145 NA MRPS21 mitochondrial ribosomal protein S21 54460 ENSG00000187145
192  ENSG00000185499 NA MUC1 mucin 1, cell surface associated 4582 ENSG00000185499
193  ENSG00000099800 NA TIMM13 translocase of inner mitochondrial membrane 13 homolog (yeast) 26517 ENSG00000099800
194  ENSG00000119328 NA FAM206A family with sequence similarity 206, member A 54942 ENSG00000119328
195  ENSG00000107951 NA MTPAP mitochondrial poly(A) polymerase 55149 ENSG00000107951
196  ENSG00000130348 NA QRSL1 glutaminyl-tRNA synthase (glutamine-hydrolyzing)-like 1 55278 ENSG00000130348
197  ENSG00000074319 NA TSG101 tumor susceptibility gene 101 7251 ENSG00000074319
198  ENSG00000103335 NA PIEZO1 piezo-type mechanosensitive ion channel component 1 9780 ENSG00000103335
199  ENSG00000148950 NA IMMP1L IMP1 inner mitochondrial membrane peptidase-like (S. cerevisiae) 196294 ENSG00000148950
200  ENSG00000087250 NA MT3 metallothionein 3 4504 ENSG00000087250
201  ENSG00000170502 NA NUDT9 nudix (nucleoside diphosphate linked moiety X)-type motif 9 53343 ENSG00000170502
202  ENSG00000137288 NA MNF1 mitochondrial nucleoid factor 1 84300 ENSG00000137288
203  ENSG00000130347 NA RTN4IP1 reticulon 4 interacting protein 1 84816 ENSG00000130347
204  ENSG00000133961 NA NUMB numb homolog (Drosophila) 8650 ENSG00000133961
205  ENSG00000154814 NA OXNAD1 oxidoreductase NAD-binding domain containing 1 92106 ENSG00000154814
206  ENSG00000103121 NA CMC2 COX assembly mitochondrial protein 2 homolog (S. cerevisiae) 56942 ENSG00000103121
207  ENSG00000100804 NA PSMB5 proteasome (prosome, macropain) subunit, beta type, 5 5693 ENSG00000100804
208  ENSG00000170791 NA CHCHD7 coiled-coil-helix-coiled-coil-helix domain containing 7 79145 ENSG00000170791
209  ENSG00000215021 NA PHB2 prohibitin 2 11331 ENSG00000215021
210  ENSG00000167085 NA PHB prohibitin 5245 ENSG00000167085
211  ENSG00000072506 NA HSD17B10 hydroxysteroid (17-beta) dehydrogenase 10 3028 ENSG00000072506
212  ENSG00000106153 NA CHCHD2 coiled-coil-helix-coiled-coil-helix domain containing 2 51142 ENSG00000106153
213  ENSG00000183036 NA PCP4 Purkinje cell protein 4 5121 ENSG00000183036
214  ENSG00000131143 NA COX4I1 cytochrome c oxidase subunit IV isoform 1 1327 ENSG00000131143
215  ENSG00000142546 NA NOSIP nitric oxide synthase interacting protein 51070 ENSG00000142546
216  ENSG00000136444 NA RSAD1 radical S-adenosyl methionine domain containing 1 55316 ENSG00000136444
217  ENSG00000108561 NA C1QBP complement component 1, q subcomponent binding protein 708 ENSG00000108561
218  ENSG00000106355 NA LSM5 LSM5 homolog, U6 small nuclear RNA associated (S. cerevisiae) 23658 ENSG00000106355
219  ENSG00000102265 NA TIMP1 TIMP metallopeptidase inhibitor 1 7076 ENSG00000102265
220  ENSG00000230055 NA CISD3 CDGSH iron sulfur domain 3 284106 ENSG00000230055
221  ENSG00000175581 NA MRPL48 mitochondrial ribosomal protein L48 51642 ENSG00000175581
222  ENSG00000047249 NA ATP6V1H ATPase, H+ transporting, lysosomal 50/57kDa, V1 subunit H 51606 ENSG00000047249
223  ENSG00000136143 NA SUCLA2 succinate-CoA ligase, ADP-forming, beta subunit 8803 ENSG00000136143
224  ENSG00000003137 NA CYP26B1 cytochrome P450, family 26, subfamily B, polypeptide 1 56603 ENSG00000003137
225  ENSG00000168000 NA BSCL2 Berardinelli-Seip congenital lipodystrophy 2 (seipin) 26580 ENSG00000168000
226  ENSG00000166855 NA CLPX ClpX caseinolytic peptidase X homolog (E. coli) 10845 ENSG00000166855
227  ENSG00000090263 NA MRPS33 mitochondrial ribosomal protein S33 51650 ENSG00000090263
228  ENSG00000166321 NA NUDT13 nudix (nucleoside diphosphate linked moiety X)-type motif 13 25961 ENSG00000166321
229  ENSG00000074582 NA BCS1L BCS1-like (S. cerevisiae) 617 ENSG00000074582
230  ENSG00000122033 NA MTIF3 mitochondrial translational initiation factor 3 219402 ENSG00000122033
231  ENSG00000116171 NA SCP2 sterol carrier protein 2 6342 ENSG00000116171
232  ENSG00000082146 NA STRADB STE20-related kinase adaptor beta 55437 ENSG00000082146
233  ENSG00000104412 NA EMC2 ER membrane protein complex subunit 2 9694 ENSG00000104412
234  ENSG00000172590 NA MRPL52 mitochondrial ribosomal protein L52 122704 ENSG00000172590
235  ENSG00000140009 NA ESR2 estrogen receptor 2 (ER beta) 2100 ENSG00000140009
236  ENSG00000103018 NA CYB5B cytochrome b5 type B (outer mitochondrial membrane) 80777 ENSG00000103018
237  ENSG00000166816 NA LDHD lactate dehydrogenase D 197257 ENSG00000166816
238  ENSG00000143374 NA TARS2 threonyl-tRNA synthetase 2, mitochondrial (putative) 80222 ENSG00000143374
239  ENSG00000013275 NA PSMC4 proteasome (prosome, macropain) 26S subunit, ATPase, 4 5704 ENSG00000013275
240  ENSG00000132313 NA MRPL35 mitochondrial ribosomal protein L35 51318 ENSG00000132313
241  ENSG00000138495 NA COX17 COX17 cytochrome c oxidase assembly homolog (S. cerevisiae) 10063 ENSG00000138495
242  ENSG00000117118 NA SDHB succinate dehydrogenase complex, subunit B, iron sulfur (Ip) 6390 ENSG00000117118
243  ENSG00000171953 NA ATPAF2 ATP synthase mitochondrial F1 complex assembly factor 2 91647 ENSG00000171953
244  ENSG00000168827 NA GFM1 G elongation factor, mitochondrial 1 85476 ENSG00000168827
245  ENSG00000143641 NA GALNT2 UDP-N-acetyl-alpha-D-galactosamine:polypeptide N-acetylgalactosaminyltransferase 2 (GalNAc-T2) 2590 ENSG00000143641
246  ENSG00000135469 NA COQ10A coenzyme Q10 homolog A (S. cerevisiae) 93058 ENSG00000135469
247  ENSG00000177427 NA SMCR7 Smith-Magenis syndrome chromosome region, candidate 7 125170 ENSG00000177427
248  ENSG00000149380 NA P4HA3 prolyl 4-hydroxylase, alpha polypeptide III 283208 ENSG00000149380
249  ENSG00000115944 NA COX7A2L cytochrome c oxidase subunit VIIa polypeptide 2 like 9167 ENSG00000115944
250  ENSG00000064652 NA SNX24 sorting nexin 24 28966 ENSG00000064652
251  ENSG00000197150 NA ABCB8 ATP-binding cassette, sub-family B (MDR/TAP), member 8 11194 ENSG00000197150
252  ENSG00000152234 NA ATP5A1 ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle 498 ENSG00000152234
253  ENSG00000164022 NA AIMP1 aminoacyl tRNA synthetase complex-interacting multifunctional protein 1 9255 ENSG00000164022
254  ENSG00000105402 NA NAPA N-ethylmaleimide-sensitive factor attachment protein, alpha 8775 ENSG00000105402
255  ENSG00000198920 NA KIAA0753 KIAA0753 9851 ENSG00000198920
256  ENSG00000128609 NA NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa 4698 ENSG00000128609
257  ENSG00000178802 NA MPI mannose phosphate isomerase 4351 ENSG00000178802
258  ENSG00000163541 NA SUCLG1 succinate-CoA ligase, alpha subunit 8802 ENSG00000163541
259  ENSG00000165678 NA GHITM growth hormone inducible transmembrane protein 27069 ENSG00000165678
260  ENSG00000154719 NA MRPL39 mitochondrial ribosomal protein L39 54148 ENSG00000154719
261  ENSG00000103489 NA XYLT1 xylosyltransferase I 64131 ENSG00000103489
262  ENSG00000173915 NA USMG5 up-regulated during skeletal muscle growth 5 homolog (mouse) 84833 ENSG00000173915
263  ENSG00000131730 NA CKMT2 creatine kinase, mitochondrial 2 (sarcomeric) 1160 ENSG00000131730
264  ENSG00000158882 NA TOMM40L translocase of outer mitochondrial membrane 40 homolog (yeast)-like 84134 ENSG00000158882
265  ENSG00000137714 NA FDX1 ferredoxin 1 2230 ENSG00000137714
266  ENSG00000115652 NA UXS1 UDP-glucuronate decarboxylase 1 80146 ENSG00000115652
267  ENSG00000136897 NA MRPL50 mitochondrial ribosomal protein L50 54534 ENSG00000136897
268  ENSG00000132541 NA HRSP12 heat-responsive protein 12 10247 ENSG00000132541
269  ENSG00000092096 NA SLC22A17 solute carrier family 22, member 17 51310 ENSG00000092096
270  ENSG00000124523 NA SIRT5 sirtuin 5 23408 ENSG00000124523
271  ENSG00000102738 NA MRPS31 mitochondrial ribosomal protein S31 10240 ENSG00000102738
272  ENSG00000197943 NA PLCG2 phospholipase C, gamma 2 (phosphatidylinositol-specific) 5336 ENSG00000197943
273  ENSG00000130312 NA MRPL34 mitochondrial ribosomal protein L34 64981 ENSG00000130312
274  ENSG00000132300 NA PTCD3 pentatricopeptide repeat domain 3 55037 ENSG00000132300
275  ENSG00000139428 NA MMAB methylmalonic aciduria (cobalamin deficiency) cblB type 326625 ENSG00000139428
276  ENSG00000070808 NA CAMK2A calcium/calmodulin-dependent protein kinase II alpha 815 ENSG00000070808
277  ENSG00000196562 NA SULF2 sulfatase 2 55959 ENSG00000196562
278  ENSG00000162600 NA OMA1 OMA1 zinc metallopeptidase homolog (S. cerevisiae) 115209 ENSG00000162600
279  ENSG00000108179 NA PPIF peptidylprolyl isomerase F 10105 ENSG00000108179
280  ENSG00000137133 NA HINT2 histidine triad nucleotide binding protein 2 84681 ENSG00000137133
281  ENSG00000122729 NA ACO1 aconitase 1, soluble 48 ENSG00000122729
282  ENSG00000173085 NA COQ2 coenzyme Q2 homolog, prenyltransferase (yeast) 27235 ENSG00000173085
283  ENSG00000101096 NA NFATC2 nuclear factor of activated T-cells, cytoplasmic, calcineurin-dependent 2 4773 ENSG00000101096
284  ENSG00000124172 NA ATP5E ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit 514 ENSG00000124172
285  ENSG00000213585 NA VDAC1 voltage-dependent anion channel 1 7416 ENSG00000213585
286  ENSG00000205981 NA DNAJC19 DnaJ (Hsp40) homolog, subfamily C, member 19 131118 ENSG00000205981
287  ENSG00000132591 NA ERAL1 Era G-protein-like 1 (E. coli) 26284 ENSG00000132591
288  ENSG00000120333 NA MRPS14 mitochondrial ribosomal protein S14 63931 ENSG00000120333
289  ENSG00000184857 NA TMEM186 transmembrane protein 186 25880 ENSG00000184857
290  ENSG00000099624 NA ATP5D ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit 513 ENSG00000099624
291  ENSG00000107954 NA NEURL neuralized homolog (Drosophila) 9148 ENSG00000107954
292  ENSG00000166949 NA SMAD3 SMAD family member 3 4088 ENSG00000166949
293  ENSG00000138670 NA RASGEF1B RasGEF domain family, member 1B 153020 ENSG00000138670
294  ENSG00000100412 NA ACO2 aconitase 2, mitochondrial 50 ENSG00000100412
295  ENSG00000112651 NA MRPL2 mitochondrial ribosomal protein L2 51069 ENSG00000112651
296  ENSG00000101311 NA FERMT1 fermitin family member 1 55612 ENSG00000101311
297  ENSG00000164051 NA CCDC51 coiled-coil domain containing 51 79714 ENSG00000164051
298  ENSG00000181610 NA MRPS23 mitochondrial ribosomal protein S23 51649 ENSG00000181610
299  ENSG00000175792 NA RUVBL1 RuvB-like 1 (E. coli) 8607 ENSG00000175792
300  ENSG00000213563 NA C8orf82 chromosome 8 open reading frame 82 414919 ENSG00000213563
301  ENSG00000164896 NA FASTK Fas-activated serine/threonine kinase 10922 ENSG00000164896
302  ENSG00000107020 NA PLGRKT plasminogen receptor, C-terminal lysine transmembrane protein 55848 ENSG00000107020
303  ENSG00000176422 NA SPRYD4 SPRY domain containing 4 283377 ENSG00000176422
304  ENSG00000119673 NA ACOT2 acyl-CoA thioesterase 2 10965 ENSG00000119673
305  ENSG00000070785 NA EIF2B3 eukaryotic translation initiation factor 2B, subunit 3 gamma, 58kDa 8891 ENSG00000070785
306  ENSG00000180185 NA FAHD1 fumarylacetoacetate hydrolase domain containing 1 81889 ENSG00000180185
307  ENSG00000148090 NA AUH AU RNA binding protein/enoyl-CoA hydratase 549 ENSG00000148090
308  ENSG00000127989 NA MTERF mitochondrial transcription termination factor 7978 ENSG00000127989
309  ENSG00000090013 NA BLVRB biliverdin reductase B (flavin reductase (NADPH)) 645 ENSG00000090013
310  ENSG00000133943 NA C14orf159 chromosome 14 open reading frame 159 80017 ENSG00000133943
311  ENSG00000172270 NA BSG basigin (Ok blood group) 682 ENSG00000172270
312  ENSG00000111817 NA DSE dermatan sulfate epimerase 29940 ENSG00000111817
313  ENSG00000119723 NA COQ6 coenzyme Q6 homolog, monooxygenase (S. cerevisiae) 51004 ENSG00000119723
314  ENSG00000197894 NA ADH5 alcohol dehydrogenase 5 (class III), chi polypeptide 128 ENSG00000197894
315  ENSG00000113312 NA TTC1 tetratricopeptide repeat domain 1 7265 ENSG00000113312
316  ENSG00000197448 NA GSTK1 glutathione S-transferase kappa 1 373156 ENSG00000197448
317  ENSG00000167792 NA NDUFV1 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa 4723 ENSG00000167792
318  ENSG00000112335 NA SNX3 sorting nexin 3 8724 ENSG00000112335
319  ENSG00000204308 NA RNF5 ring finger protein 5, E3 ubiquitin protein ligase 6048 ENSG00000204308
320  ENSG00000134020 NA PEBP4 phosphatidylethanolamine-binding protein 4 157310 ENSG00000134020
321  ENSG00000162735 NA PEX19 peroxisomal biogenesis factor 19 5824 ENSG00000162735
322  ENSG00000159377 NA PSMB4 proteasome (prosome, macropain) subunit, beta type, 4 5692 ENSG00000159377
323  ENSG00000121361 NA KCNJ8 potassium inwardly-rectifying channel, subfamily J, member 8 3764 ENSG00000121361
324  ENSG00000100034 NA PPM1F protein phosphatase, Mg2+/Mn2+ dependent, 1F 9647 ENSG00000100034
325  ENSG00000182809 NA CRIP2 cysteine-rich protein 2 1397 ENSG00000182809
326  ENSG00000127884 NA ECHS1 enoyl CoA hydratase, short chain, 1, mitochondrial 1892 ENSG00000127884
327  ENSG00000178952 NA TUFM Tu translation elongation factor, mitochondrial 7284 ENSG00000178952
328  ENSG00000168273 NA C3orf78 chromosome 3 open reading frame 78 440957 ENSG00000168273
329  ENSG00000125124 NA BBS2 Bardet-Biedl syndrome 2 583 ENSG00000125124
330  ENSG00000125445 NA MRPS7 mitochondrial ribosomal protein S7 51081 ENSG00000125445
331  ENSG00000105364 NA MRPL4 mitochondrial ribosomal protein L4 51073 ENSG00000105364
332  ENSG00000142188 NA TMEM50B transmembrane protein 50B 757 ENSG00000142188
333  ENSG00000143158 NA MPC2 mitochondrial pyruvate carrier 2 25874 ENSG00000143158
334  ENSG00000113013 NA HSPA9 heat shock 70kDa protein 9 (mortalin) 3313 ENSG00000113013
335  ENSG00000213420 NA GPC2 glypican 2 221914 ENSG00000213420
336  ENSG00000110011 NA DNAJC4 DnaJ (Hsp40) homolog, subfamily C, member 4 3338 ENSG00000110011
337  ENSG00000117151 NA CTBS chitobiase, di-N-acetyl- 1486 ENSG00000117151
338  ENSG00000101000 NA PROCR protein C receptor, endothelial 10544 ENSG00000101000
339  ENSG00000101247 NA NDUFAF5 NADH dehydrogenase (ubiquinone) complex I, assembly factor 5 79133 ENSG00000101247
340  ENSG00000241837 NA ATP5O ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit 539 ENSG00000241837
341  ENSG00000140905 NA GCSH glycine cleavage system protein H (aminomethyl carrier) 2653 ENSG00000140905
342  ENSG00000214026 NA MRPL23 mitochondrial ribosomal protein L23 6150 ENSG00000214026
343  ENSG00000165264 NA NDUFB6 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa 4712 ENSG00000165264
344  ENSG00000109846 NA CRYAB crystallin, alpha B 1410 ENSG00000109846
345  ENSG00000161281 NA COX7A1 cytochrome c oxidase subunit VIIa polypeptide 1 (muscle) 1346 ENSG00000161281
346  ENSG00000167862 NA ICT1 immature colon carcinoma transcript 1 3396 ENSG00000167862
347  ENSG00000071246 NA VASH1 vasohibin 1 22846 ENSG00000071246
348  ENSG00000116288 NA PARK7 parkinson protein 7 11315 ENSG00000116288
349  ENSG00000198715 NA C1orf85 chromosome 1 open reading frame 85 112770 ENSG00000198715
350  ENSG00000128203 NA ASPHD2 aspartate beta-hydroxylase domain containing 2 57168 ENSG00000128203
351  ENSG00000166136 NA NDUFB8 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa 4714 ENSG00000166136
352  ENSG00000172340 NA SUCLG2 succinate-CoA ligase, GDP-forming, beta subunit 8801 ENSG00000172340
353  ENSG00000151093 NA OXSM 3-oxoacyl-ACP synthase, mitochondrial 54995 ENSG00000151093
354  ENSG00000091140 NA DLD dihydrolipoamide dehydrogenase 1738 ENSG00000091140
355  ENSG00000130414 NA NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa 4705 ENSG00000130414
356  ENSG00000007923 NA DNAJC11 DnaJ (Hsp40) homolog, subfamily C, member 11 55735 ENSG00000007923
357  ENSG00000122971 NA ACADS acyl-CoA dehydrogenase, C-2 to C-3 short chain 35 ENSG00000122971
358  ENSG00000131828 NA PDHA1 pyruvate dehydrogenase (lipoamide) alpha 1 5160 ENSG00000131828
359  ENSG00000103356 NA EARS2 glutamyl-tRNA synthetase 2, mitochondrial (putative) 124454 ENSG00000103356
360  ENSG00000182512 NA GLRX5 glutaredoxin 5 51218 ENSG00000182512
361  ENSG00000168807 NA SNTB2 syntrophin, beta 2 (dystrophin-associated protein A1, 59kDa, basic component 2) 6645 ENSG00000168807
362  ENSG00000091483 NA FH fumarate hydratase 2271 ENSG00000091483
363  ENSG00000203797 NA DDO D-aspartate oxidase 8528 ENSG00000203797
364  ENSG00000103642 NA LACTB lactamase, beta 114294 ENSG00000103642
365  ENSG00000109586 NA GALNT7 UDP-N-acetyl-alpha-D-galactosamine:polypeptide N-acetylgalactosaminyltransferase 7 (GalNAc-T7) 51809 ENSG00000109586
366  ENSG00000136100 NA VPS36 vacuolar protein sorting 36 homolog (S. cerevisiae) 51028 ENSG00000136100
367  ENSG00000110074 NA FOXRED1 FAD-dependent oxidoreductase domain containing 1 55572 ENSG00000110074
368  ENSG00000074201 NA CLNS1A chloride channel, nucleotide-sensitive, 1A 1207 ENSG00000074201
369  ENSG00000174374 NA WBSCR16 Williams-Beuren syndrome chromosome region 16 81554 ENSG00000174374
370  ENSG00000164466 NA SFXN1 sideroflexin 1 94081 ENSG00000164466
371  ENSG00000119537 NA KDSR 3-ketodihydrosphingosine reductase 2531 ENSG00000119537
372  ENSG00000111481 NA COPZ1 coatomer protein complex, subunit zeta 1 22818 ENSG00000111481
373  ENSG00000151729 NA SLC25A4 solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4 291 ENSG00000151729
374  ENSG00000178057 NA NDUFAF3 NADH dehydrogenase (ubiquinone) complex I, assembly factor 3 25915 ENSG00000178057
375  ENSG00000183172 NA C22orf32 chromosome 22 open reading frame 32 91689 ENSG00000183172
376  ENSG00000173660 NA UQCRH ubiquinol-cytochrome c reductase hinge protein 7388 ENSG00000173660
377  ENSG00000133028 NA SCO1 SCO cytochrome oxidase deficient homolog 1 (yeast) 6341 ENSG00000133028
378  ENSG00000105696 NA TMEM59L transmembrane protein 59-like 25789 ENSG00000105696
379  ENSG00000100348 NA TXN2 thioredoxin 2 25828 ENSG00000100348
380  ENSG00000140876 NA NUDT7 nudix (nucleoside diphosphate linked moiety X)-type motif 7 283927 ENSG00000140876
381  ENSG00000101181 NA GTPBP5 GTP binding protein 5 (putative) 26164 ENSG00000101181
382  ENSG00000135940 NA COX5B cytochrome c oxidase subunit Vb 1329 ENSG00000135940
383  ENSG00000029639 NA TFB1M transcription factor B1, mitochondrial 51106 ENSG00000029639
384  ENSG00000129991 NA TNNI3 troponin I type 3 (cardiac) 7137 ENSG00000129991
385  ENSG00000135900 NA MRPL44 mitochondrial ribosomal protein L44 65080 ENSG00000135900
386  ENSG00000239789 NA MRPS17 mitochondrial ribosomal protein S17 51373 ENSG00000239789
387  ENSG00000113790 NA EHHADH enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase 1962 ENSG00000113790
388  ENSG00000162851 NA TFB2M transcription factor B2, mitochondrial 64216 ENSG00000162851
389  ENSG00000160293 NA VAV2 vav 2 guanine nucleotide exchange factor 7410 ENSG00000160293
390  ENSG00000159210 NA SNF8 SNF8, ESCRT-II complex subunit, homolog (S. cerevisiae) 11267 ENSG00000159210
391  ENSG00000082515 NA MRPL22 mitochondrial ribosomal protein L22 29093 ENSG00000082515
392  ENSG00000189043 NA NDUFA4 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa 4697 ENSG00000189043
393  ENSG00000179085 NA DPM3 dolichyl-phosphate mannosyltransferase polypeptide 3 54344 ENSG00000179085
394  ENSG00000176894 NA PXMP2 peroxisomal membrane protein 2, 22kDa 5827 ENSG00000176894
395  ENSG00000172115 NA CYCS cytochrome c, somatic 54205 ENSG00000172115
396  ENSG00000160783 NA PMF1 polyamine-modulated factor 1 11243 ENSG00000160783
397  ENSG00000035141 NA FAM136A family with sequence similarity 136, member A 84908 ENSG00000035141
398  ENSG00000185100 NA ADSSL1 adenylosuccinate synthase like 1 122622 ENSG00000185100
399  ENSG00000115286 NA NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) 374291 ENSG00000115286
400  ENSG00000164258 NA NDUFS4 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) 4724 ENSG00000164258
401  ENSG00000156170 NA NDUFAF6 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 137682 ENSG00000156170
402  ENSG00000155463 NA OXA1L oxidase (cytochrome c) assembly 1-like 5018 ENSG00000155463
403  ENSG00000163319 NA MRPS18C mitochondrial ribosomal protein S18C 51023 ENSG00000163319
404  ENSG00000185608 NA MRPL40 mitochondrial ribosomal protein L40 64976 ENSG00000185608
405  ENSG00000179091 NA CYC1 cytochrome c-1 1537 ENSG00000179091
406  ENSG00000171861 NA RNMTL1 RNA methyltransferase like 1 55178 ENSG00000171861
407  ENSG00000053501 NA USE1 unconventional SNARE in the ER 1 homolog (S. cerevisiae) 55850 ENSG00000053501
408  ENSG00000182810 NA DDX28 DEAD (Asp-Glu-Ala-Asp) box polypeptide 28 55794 ENSG00000182810
409  ENSG00000105819 NA PMPCB peptidase (mitochondrial processing) beta 9512 ENSG00000105819
410  ENSG00000196683 NA TOMM7 translocase of outer mitochondrial membrane 7 homolog (yeast) 54543 ENSG00000196683
411  ENSG00000175198 NA PCCA propionyl CoA carboxylase, alpha polypeptide 5095 ENSG00000175198
412  ENSG00000129187 NA DCTD dCMP deaminase 1635 ENSG00000129187
413  ENSG00000067225 NA PKM pyruvate kinase, muscle 5315 ENSG00000067225
414  ENSG00000114023 NA FAM162A family with sequence similarity 162, member A 26355 ENSG00000114023
415  ENSG00000157326 NA DHRS4 dehydrogenase/reductase (SDR family) member 4 10901 ENSG00000157326
416  ENSG00000140990 NA NDUFB10 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa 4716 ENSG00000140990
417  ENSG00000135297 NA MTO1 mitochondrial translation optimization 1 homolog (S. cerevisiae) 25821 ENSG00000135297
418  ENSG00000144182 NA LIPT1 lipoyltransferase 1 51601 ENSG00000144182
419  ENSG00000243147 NA MRPL33 mitochondrial ribosomal protein L33 9553 ENSG00000243147
420  ENSG00000143653 NA SCCPDH saccharopine dehydrogenase (putative) 51097 ENSG00000143653
421  ENSG00000116906 NA GNPAT glyceronephosphate O-acyltransferase 8443 ENSG00000116906
422  ENSG00000123545 NA NDUFAF4 NADH dehydrogenase (ubiquinone) complex I, assembly factor 4 29078 ENSG00000123545
423  ENSG00000178913 NA TAF7 TAF7 RNA polymerase II, TATA box binding protein (TBP)-associated factor, 55kDa 6879 ENSG00000178913
424  ENSG00000105220 NA GPI glucose-6-phosphate isomerase 2821 ENSG00000105220
425  ENSG00000133315 NA MACROD1 MACRO domain containing 1 28992 ENSG00000133315
426  ENSG00000072778 NA ACADVL acyl-CoA dehydrogenase, very long chain 37 ENSG00000072778
427  ENSG00000172893 NA DHCR7 7-dehydrocholesterol reductase 1717 ENSG00000172893
428  ENSG00000108774 NA RAB5C RAB5C, member RAS oncogene family 5878 ENSG00000108774
429  ENSG00000150977 NA RILPL2 Rab interacting lysosomal protein-like 2 196383 ENSG00000150977
430  ENSG00000049883 NA PTCD2 pentatricopeptide repeat domain 2 79810 ENSG00000049883
431  ENSG00000084731 NA KIF3C kinesin family member 3C 3797 ENSG00000084731
432  ENSG00000160124 NA CCDC58 coiled-coil domain containing 58 131076 ENSG00000160124
433  ENSG00000126088 NA UROD uroporphyrinogen decarboxylase 7389 ENSG00000126088
434  ENSG00000136521 NA NDUFB5 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa 4711 ENSG00000136521
435  ENSG00000169020 NA ATP5I ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E 521 ENSG00000169020
436  ENSG00000182054 NA IDH2 isocitrate dehydrogenase 2 (NADP+), mitochondrial 3418 ENSG00000182054
437  ENSG00000004779 NA NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa 4706 ENSG00000004779
438  ENSG00000165898 NA ISCA2 iron-sulfur cluster assembly 2 homolog (S. cerevisiae) 122961 ENSG00000165898
439  ENSG00000004961 NA HCCS holocytochrome c synthase 3052 ENSG00000004961
440  ENSG00000073578 NA SDHA succinate dehydrogenase complex, subunit A, flavoprotein (Fp) 6389 ENSG00000073578
441  ENSG00000167775 NA CD320 CD320 molecule 51293 ENSG00000167775
442  ENSG00000213965 NA NUDT19 nudix (nucleoside diphosphate linked moiety X)-type motif 19 390916 ENSG00000213965
443  ENSG00000151413 NA NUBPL nucleotide binding protein-like 80224 ENSG00000151413
444  ENSG00000104325 NA DECR1 2,4-dienoyl CoA reductase 1, mitochondrial 1666 ENSG00000104325
445  ENSG00000103245 NA NARFL nuclear prelamin A recognition factor-like 64428 ENSG00000103245
446  ENSG00000077348 NA EXOSC5 exosome component 5 56915 ENSG00000077348
447  ENSG00000113048 NA MRPS27 mitochondrial ribosomal protein S27 23107 ENSG00000113048
448  ENSG00000182154 NA MRPL41 mitochondrial ribosomal protein L41 64975 ENSG00000182154
449  ENSG00000072401 NA UBE2D1 ubiquitin-conjugating enzyme E2D 1 7321 ENSG00000072401
450  ENSG00000213988 NA ZNF90 zinc finger protein 90 7643 ENSG00000213988
451  ENSG00000167468 NA GPX4 glutathione peroxidase 4 2879 ENSG00000167468
452  ENSG00000127184 NA COX7C cytochrome c oxidase subunit VIIc 1350 ENSG00000127184
453  ENSG00000135775 NA COG2 component of oligomeric golgi complex 2 22796 ENSG00000135775
454  ENSG00000085760 NA MTIF2 mitochondrial translational initiation factor 2 4528 ENSG00000085760
455  ENSG00000165637 NA VDAC2 voltage-dependent anion channel 2 7417 ENSG00000165637
456  ENSG00000120265 NA PCMT1 protein-L-isoaspartate (D-aspartate) O-methyltransferase 5110 ENSG00000120265
457  ENSG00000100211 NA CBY1 chibby homolog 1 (Drosophila) 25776 ENSG00000100211
458  ENSG00000149357 NA LAMTOR1 late endosomal/lysosomal adaptor, MAPK and MTOR activator 1 55004 ENSG00000149357
459  ENSG00000178982 NA EIF3K eukaryotic translation initiation factor 3, subunit K 27335 ENSG00000178982
460  ENSG00000086504 NA MRPL28 mitochondrial ribosomal protein L28 10573 ENSG00000086504
461  ENSG00000108384 NA RAD51C RAD51 homolog C (S. cerevisiae) 5889 ENSG00000108384
462  ENSG00000162910 NA MRPL55 mitochondrial ribosomal protein L55 128308 ENSG00000162910
463  ENSG00000130733 NA YIPF2 Yip1 domain family, member 2 78992 ENSG00000130733
464  ENSG00000130349 NA C6orf203 chromosome 6 open reading frame 203 51250 ENSG00000130349
465  ENSG00000166681 NA NGFRAP1 nerve growth factor receptor (TNFRSF16) associated protein 1 27018 ENSG00000166681
466  ENSG00000111271 NA ACAD10 acyl-CoA dehydrogenase family, member 10 80724 ENSG00000111271
467  ENSG00000103423 NA DNAJA3 DnaJ (Hsp40) homolog, subfamily A, member 3 9093 ENSG00000103423
468  ENSG00000160211 NA G6PD glucose-6-phosphate dehydrogenase 2539 ENSG00000160211
469  ENSG00000138777 NA PPA2 pyrophosphatase (inorganic) 2 27068 ENSG00000138777
470  ENSG00000100601 NA ALKBH1 alkB, alkylation repair homolog 1 (E. coli) 8846 ENSG00000100601
471  ENSG00000102554 NA KLF5 Kruppel-like factor 5 (intestinal) 688 ENSG00000102554
472  ENSG00000188026 NA RILPL1 Rab interacting lysosomal protein-like 1 353116 ENSG00000188026
473  ENSG00000136522 NA MRPL47 mitochondrial ribosomal protein L47 57129 ENSG00000136522
474  ENSG00000135972 NA MRPS9 mitochondrial ribosomal protein S9 64965 ENSG00000135972
475  ENSG00000144451 NA SPAG16 sperm associated antigen 16 79582 ENSG00000144451
476  ENSG00000023228 NA NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) 4719 ENSG00000023228
477  ENSG00000254470 NA AP5B1 adaptor-related protein complex 5, beta 1 subunit 91056 ENSG00000254470
478  ENSG00000115840 NA SLC25A12 solute carrier family 25 (aspartate/glutamate carrier), member 12 8604 ENSG00000115840
479  ENSG00000145982 NA FARS2 phenylalanyl-tRNA synthetase 2, mitochondrial 10667 ENSG00000145982
480  ENSG00000121897 NA LIAS lipoic acid synthetase 11019 ENSG00000121897
481  ENSG00000197122 NA SRC v-src sarcoma (Schmidt-Ruppin A-2) viral oncogene homolog (avian) 6714 ENSG00000197122
482  ENSG00000112695 NA COX7A2 cytochrome c oxidase subunit VIIa polypeptide 2 (liver) 1347 ENSG00000112695
483  ENSG00000147155 NA EBP emopamil binding protein (sterol isomerase) 10682 ENSG00000147155
484  ENSG00000179958 NA DCTPP1 dCTP pyrophosphatase 1 79077 ENSG00000179958
485  ENSG00000106571 NA GLI3 GLI family zinc finger 3 2737 ENSG00000106571
486  ENSG00000083720 NA OXCT1 3-oxoacid CoA transferase 1 5019 ENSG00000083720
487  ENSG00000131495 NA NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa 4695 ENSG00000131495
488  ENSG00000095321 NA CRAT carnitine O-acetyltransferase 1384 ENSG00000095321
489  ENSG00000185808 NA PIGP phosphatidylinositol glycan anchor biosynthesis, class P 51227 ENSG00000185808
490  ENSG00000165688 NA PMPCA peptidase (mitochondrial processing) alpha 23203 ENSG00000165688
491  ENSG00000120992 NA LYPLA1 lysophospholipase I 10434 ENSG00000120992
492  ENSG00000183617 NA MRPL54 mitochondrial ribosomal protein L54 116541 ENSG00000183617
493  ENSG00000112855 NA HARS2 histidyl-tRNA synthetase 2, mitochondrial 23438 ENSG00000112855
494  ENSG00000108100 NA CCNY cyclin Y 219771 ENSG00000108100
495  ENSG00000119705 NA SLIRP SRA stem-loop interacting RNA binding protein 81892 ENSG00000119705
496  ENSG00000205309 NA NT5M 5',3'-nucleotidase, mitochondrial 56953 ENSG00000205309
497  ENSG00000170906 NA NDUFA3 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa 4696 ENSG00000170906
498  ENSG00000138085 NA ATRAID all-trans retinoic acid-induced differentiation factor 51374 ENSG00000138085
499  ENSG00000128654 NA MTX2 metaxin 2 10651 ENSG00000128654
500  ENSG00000160808 NA MYL3 myosin, light chain 3, alkali; ventricular, skeletal, slow 4634 ENSG00000160808
501  ENSG00000112304 NA ACOT13 acyl-CoA thioesterase 13 55856 ENSG00000112304
502  ENSG00000108439 NA PNPO pyridoxamine 5'-phosphate oxidase 55163 ENSG00000108439
503  ENSG00000167283 NA ATP5L ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G 10632 ENSG00000167283
504  ENSG00000114054 NA PCCB propionyl CoA carboxylase, beta polypeptide 5096 ENSG00000114054
505  ENSG00000111275 NA ALDH2 aldehyde dehydrogenase 2 family (mitochondrial) 217 ENSG00000111275
506  ENSG00000171202 NA TMEM126A transmembrane protein 126A 84233 ENSG00000171202
507  ENSG00000136270 NA TBRG4 transforming growth factor beta regulator 4 9238 ENSG00000136270
508  ENSG00000010256 NA UQCRC1 ubiquinol-cytochrome c reductase core protein I 7384 ENSG00000010256
509  ENSG00000130560 NA UBAC1 UBA domain containing 1 10422 ENSG00000130560
510  ENSG00000104823 NA ECH1 enoyl CoA hydratase 1, peroxisomal 1891 ENSG00000104823
511  ENSG00000167515 NA TRAPPC2L trafficking protein particle complex 2-like 51693 ENSG00000167515
512  ENSG00000197912 NA SPG7 spastic paraplegia 7 (pure and complicated autosomal recessive) 6687 ENSG00000197912
513  ENSG00000138796 NA HADH hydroxyacyl-CoA dehydrogenase 3033 ENSG00000138796
514  ENSG00000165672 NA PRDX3 peroxiredoxin 3 10935 ENSG00000165672
515  ENSG00000154518 NA ATP5G3 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C3 (subunit 9) 518 ENSG00000154518
516  ENSG00000101132 NA PFDN4 prefoldin subunit 4 5203 ENSG00000101132
517  ENSG00000088682 NA COQ9 coenzyme Q9 homolog (S. cerevisiae) 57017 ENSG00000088682
518  ENSG00000075303 NA SLC25A40 solute carrier family 25, member 40 55972 ENSG00000075303
519  ENSG00000163382 NA APOA1BP apolipoprotein A-I binding protein 128240 ENSG00000163382
520  ENSG00000177951 NA BET1L blocked early in transport 1 homolog (S. cerevisiae)-like 51272 ENSG00000177951
521  ENSG00000168653 NA NDUFS5 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) 4725 ENSG00000168653
522  ENSG00000154237 NA LRRK1 leucine-rich repeat kinase 1 79705 ENSG00000154237
523  ENSG00000247077 NA PGAM5 phosphoglycerate mutase family member 5 192111 ENSG00000247077
524  ENSG00000156110 NA ADK adenosine kinase 132 ENSG00000156110
525  ENSG00000184903 NA IMMP2L IMP2 inner mitochondrial membrane peptidase-like (S. cerevisiae) 83943 ENSG00000184903
526  ENSG00000087299 NA L2HGDH L-2-hydroxyglutarate dehydrogenase 79944 ENSG00000087299
527  ENSG00000159335 NA PTMS parathymosin 5763 ENSG00000159335
528  ENSG00000136463 NA TACO1 translational activator of mitochondrially encoded cytochrome c oxidase I 51204 ENSG00000136463
529  ENSG00000197586 NA ENTPD6 ectonucleoside triphosphate diphosphohydrolase 6 (putative) 955 ENSG00000197586
530  ENSG00000103316 NA CRYM crystallin, mu 1428 ENSG00000103316
531  ENSG00000184076 NA UQCR10 ubiquinol-cytochrome c reductase, complex III subunit X 29796 ENSG00000184076
532  ENSG00000130300 NA PLVAP plasmalemma vesicle associated protein 83483 ENSG00000130300
533  ENSG00000075415 NA SLC25A3 solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 3 5250 ENSG00000075415
534  ENSG00000184489 NA PTP4A3 protein tyrosine phosphatase type IVA, member 3 11156 ENSG00000184489
535  ENSG00000100028 NA SNRPD3 small nuclear ribonucleoprotein D3 polypeptide 18kDa 6634 ENSG00000100028
536  ENSG00000186522 NA SEPT10 septin 10 151011 ENSG00000186522
537  ENSG00000154723 NA ATP5J ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 522 ENSG00000154723
538  ENSG00000133983 NA COX16 COX16 cytochrome c oxidase assembly homolog (S. cerevisiae) 51241 ENSG00000133983
539  ENSG00000167969 NA ECI1 enoyl-CoA delta isomerase 1 1632 ENSG00000167969
540  ENSG00000115364 NA MRPL19 mitochondrial ribosomal protein L19 9801 ENSG00000115364
541  ENSG00000105552 NA BCAT2 branched chain amino-acid transaminase 2, mitochondrial 587 ENSG00000105552
542  ENSG00000112996 NA MRPS30 mitochondrial ribosomal protein S30 10884 ENSG00000112996
543  ENSG00000100347 NA SAMM50 sorting and assembly machinery component 50 homolog (S. cerevisiae) 25813 ENSG00000100347
544  ENSG00000125166 NA GOT2 glutamic-oxaloacetic transaminase 2, mitochondrial (aspartate aminotransferase 2) 2806 ENSG00000125166
545  ENSG00000141552 NA ANAPC11 anaphase promoting complex subunit 11 51529 ENSG00000141552
546  ENSG00000140740 NA UQCRC2 ubiquinol-cytochrome c reductase core protein II 7385 ENSG00000140740
547  ENSG00000114378 NA HYAL1 hyaluronoglucosaminidase 1 3373 ENSG00000114378
548  ENSG00000160194 NA NDUFV3 NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa 4731 ENSG00000160194
549  ENSG00000147684 NA NDUFB9 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa 4715 ENSG00000147684
550  ENSG00000169599 NA NFU1 NFU1 iron-sulfur cluster scaffold homolog (S. cerevisiae) 27247 ENSG00000169599
551  ENSG00000184983 NA NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa 4700 ENSG00000184983
552  ENSG00000163626 NA COX18 COX18 cytochrome c oxidase assembly homolog (S. cerevisiae) 285521 ENSG00000163626
553  ENSG00000158864 NA NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) 4720 ENSG00000158864
554  ENSG00000079691 NA LRRC16A leucine rich repeat containing 16A 55604 ENSG00000079691
555  ENSG00000105197 NA TIMM50 translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae) 92609 ENSG00000105197
556  ENSG00000142168 NA SOD1 superoxide dismutase 1, soluble 6647 ENSG00000142168
557  ENSG00000109519 NA GRPEL1 GrpE-like 1, mitochondrial (E. coli) 80273 ENSG00000109519
558  ENSG00000000419 NA DPM1 dolichyl-phosphate mannosyltransferase polypeptide 1, catalytic subunit 8813 ENSG00000000419
559  ENSG00000133393 NA FOPNL FGFR1OP N-terminal like 123811 ENSG00000133393
560  ENSG00000096080 NA MRPS18A mitochondrial ribosomal protein S18A 55168 ENSG00000096080
561  ENSG00000120254 NA MTHFD1L methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 1-like 25902 ENSG00000120254
562  ENSG00000134056 NA MRPS36 mitochondrial ribosomal protein S36 92259 ENSG00000134056
563  ENSG00000139914 NA FITM1 fat storage-inducing transmembrane protein 1 161247 ENSG00000139914
564  ENSG00000060762 NA MPC1 mitochondrial pyruvate carrier 1 51660 ENSG00000060762
565  ENSG00000104980 NA TIMM44 translocase of inner mitochondrial membrane 44 homolog (yeast) 10469 ENSG00000104980
566  ENSG00000105499 NA PLA2G4C phospholipase A2, group IVC (cytosolic, calcium-independent) 8605 ENSG00000105499
567  ENSG00000138399 NA FASTKD1 FAST kinase domains 1 79675 ENSG00000138399
568  ENSG00000112992 NA NNT nicotinamide nucleotide transhydrogenase 23530 ENSG00000112992
569  ENSG00000067704 NA IARS2 isoleucyl-tRNA synthetase 2, mitochondrial 55699 ENSG00000067704
570  ENSG00000215251 NA FASTKD5 FAST kinase domains 5 60493 ENSG00000215251
571  ENSG00000119421 NA NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa 4702 ENSG00000119421
572  ENSG00000172172 NA MRPL13 mitochondrial ribosomal protein L13 28998 ENSG00000172172
573  ENSG00000244005 NA NFS1 NFS1 nitrogen fixation 1 homolog (S. cerevisiae) 9054 ENSG00000244005
574  ENSG00000104879 NA CKM creatine kinase, muscle 1158 ENSG00000104879
575  ENSG00000126267 NA COX6B1 cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) 1340 ENSG00000126267
576  ENSG00000121769 NA FABP3 fatty acid binding protein 3, muscle and heart (mammary-derived growth inhibitor) 2170 ENSG00000121769
577  ENSG00000148450 NA MSRB2 methionine sulfoxide reductase B2 22921 ENSG00000148450
578  ENSG00000145494 NA NDUFS6 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) 4726 ENSG00000145494
579  ENSG00000196236 NA XPNPEP3 X-prolyl aminopeptidase (aminopeptidase P) 3, putative 63929 ENSG00000196236
580  ENSG00000105379 NA ETFB electron-transfer-flavoprotein, beta polypeptide 2109 ENSG00000105379
581  ENSG00000165887 NA ANKRD2 ankyrin repeat domain 2 (stretch responsive muscle) 26287 ENSG00000165887
582  ENSG00000175334 NA BANF1 barrier to autointegration factor 1 8815 ENSG00000175334
583  ENSG00000108515 NA ENO3 enolase 3 (beta, muscle) 2027 ENSG00000108515
584  ENSG00000213995 NA CARKD carbohydrate kinase domain containing 55739 ENSG00000213995
585  ENSG00000090266 NA NDUFB2 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa 4708 ENSG00000090266
586  ENSG00000105649 NA RAB3A RAB3A, member RAS oncogene family 5864 ENSG00000105649
587  ENSG00000151498 NA ACAD8 acyl-CoA dehydrogenase family, member 8 27034 ENSG00000151498
588  ENSG00000156928 NA MALSU1 mitochondrial assembly of ribosomal large subunit 1 115416 ENSG00000156928
589  ENSG00000159199 NA ATP5G1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) 516 ENSG00000159199
590  ENSG00000155906 NA RMND1 required for meiotic nuclear division 1 homolog (S. cerevisiae) 55005 ENSG00000155906
591  ENSG00000120509 NA PDZD11 PDZ domain containing 11 51248 ENSG00000120509
592  ENSG00000130159 NA ECSIT ECSIT homolog (Drosophila) 51295 ENSG00000130159
593  ENSG00000129084 NA PSMA1 proteasome (prosome, macropain) subunit, alpha type, 1 5682 ENSG00000256206 ENSG00000129084
594  ENSG00000114383 NA TUSC2 tumor suppressor candidate 2 11334 ENSG00000114383
595  ENSG00000125863 NA MKKS McKusick-Kaufman syndrome 8195 ENSG00000125863
596  ENSG00000103274 NA NUBP1 nucleotide binding protein 1 4682 ENSG00000103274
597  ENSG00000174917 NA C19orf70 chromosome 19 open reading frame 70 125988 ENSG00000174917
598  ENSG00000181744 NA C3orf58 chromosome 3 open reading frame 58 205428 ENSG00000181744
599  ENSG00000138190 NA EXOC6 exocyst complex component 6 54536 ENSG00000138190
600  ENSG00000087460 NA GNAS GNAS complex locus 2778 ENSG00000087460
601  ENSG00000066926 NA FECH ferrochelatase 2235 ENSG00000066926
602  ENSG00000131779 NA PEX11B peroxisomal biogenesis factor 11 beta 8799 ENSG00000131779
603  ENSG00000039560 NA RAI14 retinoic acid induced 14 26064 ENSG00000039560
604  ENSG00000166228 NA PCBD1 pterin-4 alpha-carbinolamine dehydratase/dimerization cofactor of hepatocyte nuclear factor 1 alpha 5092 ENSG00000166228
605  ENSG00000130147 NA SH3BP4 SH3-domain binding protein 4 23677 ENSG00000130147
606  ENSG00000100294 NA MCAT malonyl CoA:ACP acyltransferase (mitochondrial) 27349 ENSG00000100294
607  ENSG00000137225 NA CAPN11 calpain 11 11131 ENSG00000137225
608  ENSG00000146729 NA GBAS glioblastoma amplified sequence 2631 ENSG00000146729
609  ENSG00000164494 NA PDSS2 prenyl (decaprenyl) diphosphate synthase, subunit 2 57107 ENSG00000164494
610  ENSG00000152082 NA MZT2B mitotic spindle organizing protein 2B 80097 ENSG00000152082
611  ENSG00000138463 NA DIRC2 disrupted in renal carcinoma 2 84925 ENSG00000138463
612  ENSG00000132763 NA MMACHC methylmalonic aciduria (cobalamin deficiency) cblC type, with homocystinuria 25974 ENSG00000132763
613  ENSG00000151366 NA NDUFC2 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa 4718 ENSG00000151366
614  ENSG00000130724 NA CHMP2A charged multivesicular body protein 2A 27243 ENSG00000130724
615  ENSG00000132305 NA IMMT inner membrane protein, mitochondrial 10989 ENSG00000132305
616  ENSG00000090432 NA MUL1 mitochondrial E3 ubiquitin protein ligase 1 79594 ENSG00000090432
617  ENSG00000146701 NA MDH2 malate dehydrogenase 2, NAD (mitochondrial) 4191 ENSG00000146701
618  ENSG00000164038 NA SLC9B2 solute carrier family 9, subfamily B (NHA2, cation proton antiporter 2), member 2 133308 ENSG00000164038
619  ENSG00000247596 NA TWF2 twinfilin, actin-binding protein, homolog 2 (Drosophila) 11344 ENSG00000247596
620  ENSG00000147123 NA NDUFB11 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa 54539 ENSG00000147123
621  ENSG00000169021 NA UQCRFS1 ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 7386 ENSG00000169021
622  ENSG00000104142 NA VPS18 vacuolar protein sorting 18 homolog (S. cerevisiae) 57617 ENSG00000104142
623  ENSG00000178449 NA COX14 COX14 cytochrome c oxidase assembly homolog (S. cerevisiae) 84987 ENSG00000178449
624  ENSG00000145439 NA CBR4 carbonyl reductase 4 84869 ENSG00000145439
625  ENSG00000170231 NA FABP6 fatty acid binding protein 6, ileal 2172 ENSG00000170231
626  ENSG00000062485 NA CS citrate synthase 1431 ENSG00000062485
627  ENSG00000175193 NA PARL presenilin associated, rhomboid-like 55486 ENSG00000175193
628  ENSG00000120053 NA GOT1 glutamic-oxaloacetic transaminase 1, soluble (aspartate aminotransferase 1) 2805 ENSG00000120053
629  ENSG00000227500 NA SCAMP4 secretory carrier membrane protein 4 113178 ENSG00000227500
630  ENSG00000189283 NA FHIT fragile histidine triad 2272 ENSG00000189283
631  ENSG00000111843 NA TMEM14C transmembrane protein 14C 51522 ENSG00000111843
632  ENSG00000185973 NA TMLHE trimethyllysine hydroxylase, epsilon 55217 ENSG00000185973
633  ENSG00000124370 NA MCEE methylmalonyl CoA epimerase 84693 ENSG00000124370
634  ENSG00000137513 NA NARS2 asparaginyl-tRNA synthetase 2, mitochondrial (putative) 79731 ENSG00000137513
635  ENSG00000111639 NA MRPL51 mitochondrial ribosomal protein L51 51258 ENSG00000111639
636  ENSG00000164405 NA UQCRQ ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa 27089 ENSG00000164405
637  ENSG00000168569 NA TMEM223 transmembrane protein 223 79064 ENSG00000168569
638  ENSG00000100321 NA SYNGR1 synaptogyrin 1 9145 ENSG00000100321
639  ENSG00000136930 NA PSMB7 proteasome (prosome, macropain) subunit, beta type, 7 5695 ENSG00000136930
640  ENSG00000115935 NA WIPF1 WAS/WASL interacting protein family, member 1 7456 ENSG00000115935
641  ENSG00000148187 NA MRRF mitochondrial ribosome recycling factor 92399 ENSG00000148187
642  ENSG00000061794 NA MRPS35 mitochondrial ribosomal protein S35 60488 ENSG00000061794
643  ENSG00000183648 NA NDUFB1 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa 4707 ENSG00000183648
644  ENSG00000087302 NA C14orf166 chromosome 14 open reading frame 166 51637 ENSG00000087302
645  ENSG00000110435 NA PDHX pyruvate dehydrogenase complex, component X 8050 ENSG00000110435
646  ENSG00000132676 NA DAP3 death associated protein 3 7818 ENSG00000132676
647  ENSG00000172586 NA CHCHD1 coiled-coil-helix-coiled-coil-helix domain containing 1 118487 ENSG00000172586
648  ENSG00000121022 NA COPS5 COP9 constitutive photomorphogenic homolog subunit 5 (Arabidopsis) 10987 ENSG00000121022
649  ENSG00000125356 NA NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa 4694 ENSG00000125356
650  ENSG00000108528 NA SLC25A11 solute carrier family 25 (mitochondrial carrier; oxoglutarate carrier), member 11 8402 ENSG00000108528
651  ENSG00000129282 NA MRM1 mitochondrial rRNA methyltransferase 1 homolog (S. cerevisiae) 79922 ENSG00000129282
652  ENSG00000163636 NA PSMD6 proteasome (prosome, macropain) 26S subunit, non-ATPase, 6 9861 ENSG00000163636
653  ENSG00000099795 NA NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa 4713 ENSG00000099795
654  ENSG00000137574 NA TGS1 trimethylguanosine synthase 1 96764 ENSG00000137574
655  ENSG00000175470 NA PPP2R2D protein phosphatase 2, regulatory subunit B, delta 55844 ENSG00000175470
656  ENSG00000044459 NA CNTLN centlein, centrosomal protein 54875 ENSG00000044459
657  ENSG00000153574 NA RPIA ribose 5-phosphate isomerase A 22934 ENSG00000153574
658  ENSG00000101350 NA KIF3B kinesin family member 3B 9371 ENSG00000101350
659  ENSG00000138772 NA ANXA3 annexin A3 306 ENSG00000138772
660  ENSG00000103507 NA BCKDK branched chain ketoacid dehydrogenase kinase 10295 ENSG00000103507
661  ENSG00000144021 NA CIAO1 cytosolic iron-sulfur protein assembly 1 9391 ENSG00000144021
662  ENSG00000198015 NA MRPL42 mitochondrial ribosomal protein L42 28977 ENSG00000198015
663  ENSG00000144567 NA FAM134A family with sequence similarity 134, member A 79137 ENSG00000144567
664  ENSG00000111785 NA RIC8B resistance to inhibitors of cholinesterase 8 homolog B (C. elegans) 55188 ENSG00000111785
665  ENSG00000125901 NA MRPS26 mitochondrial ribosomal protein S26 64949 ENSG00000125901
666  ENSG00000167136 NA ENDOG endonuclease G 2021 ENSG00000167136
667  ENSG00000075336 NA TIMM21 translocase of inner mitochondrial membrane 21 homolog (yeast) 29090 ENSG00000075336
668  ENSG00000250479 NA CHCHD10 coiled-coil-helix-coiled-coil-helix domain containing 10 400916 ENSG00000250479
669  ENSG00000074071 NA MRPS34 mitochondrial ribosomal protein S34 65993 ENSG00000074071
670  ENSG00000060971 NA ACAA1 acetyl-CoA acyltransferase 1 30 ENSG00000060971
671  ENSG00000164347 NA GFM2 G elongation factor, mitochondrial 2 84340 ENSG00000164347
672  ENSG00000150867 NA PIP4K2A phosphatidylinositol-5-phosphate 4-kinase, type II, alpha 5305 ENSG00000150867
673  ENSG00000111906 NA HDDC2 HD domain containing 2 51020 ENSG00000111906
674  ENSG00000181991 NA MRPS11 mitochondrial ribosomal protein S11 64963 ENSG00000181991
675  ENSG00000138175 NA ARL3 ADP-ribosylation factor-like 3 403 ENSG00000138175
676  ENSG00000175110 NA MRPS22 mitochondrial ribosomal protein S22 56945 ENSG00000175110
677  ENSG00000112357 NA PEX7 peroxisomal biogenesis factor 7 5191 ENSG00000112357
678  ENSG00000128463 NA EMC4 ER membrane protein complex subunit 4 51234 ENSG00000128463
679  ENSG00000173272 NA MZT2A mitotic spindle organizing protein 2A 653784 ENSG00000173272
680  ENSG00000117594 NA HSD11B1 hydroxysteroid (11-beta) dehydrogenase 1 3290 ENSG00000117594
681  ENSG00000110717 NA NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) 4728 ENSG00000110717
682  ENSG00000174547 NA MRPL11 mitochondrial ribosomal protein L11 65003 ENSG00000174547
683  ENSG00000137547 NA MRPL15 mitochondrial ribosomal protein L15 29088 ENSG00000137547
684  ENSG00000197535 NA MYO5A myosin VA (heavy chain 12, myoxin) 4644 ENSG00000197535
685  ENSG00000162972 NA C2orf47 chromosome 2 open reading frame 47 79568 ENSG00000162972
686  ENSG00000183978 NA COA3 cytochrome C oxidase assembly factor 3 28958 ENSG00000183978
687  ENSG00000036672 NA USP2 ubiquitin specific peptidase 2 9099 ENSG00000036672
688  ENSG00000198467 NA TPM2 tropomyosin 2 (beta) 7169 ENSG00000198467
689  ENSG00000153140 NA CETN3 centrin, EF-hand protein, 3 1070 ENSG00000153140
690  ENSG00000113845 NA TIMMDC1 translocase of inner mitochondrial membrane domain containing 1 51300 ENSG00000113845
691  ENSG00000241468 NA ATP5J2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 9551 ENSG00000241468
692  ENSG00000013563 NA DNASE1L1 deoxyribonuclease I-like 1 1774 ENSG00000013563
693  ENSG00000176340 NA COX8A cytochrome c oxidase subunit VIIIA (ubiquitous) 1351 ENSG00000176340
694  ENSG00000144029 NA MRPS5 mitochondrial ribosomal protein S5 64969 ENSG00000144029
695  ENSG00000170266 NA GLB1 galactosidase, beta 1 2720 ENSG00000170266
696  ENSG00000050393 NA CCDC90A coiled-coil domain containing 90A 63933 ENSG00000050393
697  ENSG00000101365 NA IDH3B isocitrate dehydrogenase 3 (NAD+) beta 3420 ENSG00000101365
698  ENSG00000158793 NA NIT1 nitrilase 1 4817 ENSG00000158793


Database:cellular component       Name:mitochondrial membrane part       ID:GO:0044455
C=147; O=87; E=8.92; R=9.75; rawP=1.33e-67; adjP=5.85e-66
Index UserID Value Gene Symbol Gene Name EntrezGene Ensembl
1  ENSG00000087299 NA L2HGDH L-2-hydroxyglutarate dehydrogenase 79944 ENSG00000087299
2  ENSG00000184903 NA IMMP2L IMP2 inner mitochondrial membrane peptidase-like (S. cerevisiae) 83943 ENSG00000184903
3  ENSG00000128609 NA NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa 4698 ENSG00000128609
4  ENSG00000151366 NA NDUFC2 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa 4718 ENSG00000151366
5  ENSG00000132305 NA IMMT inner membrane protein, mitochondrial 10989 ENSG00000132305
6  ENSG00000165264 NA NDUFB6 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa 4712 ENSG00000165264
7  ENSG00000156467 NA UQCRB ubiquinol-cytochrome c reductase binding protein 7381 ENSG00000156467
8  ENSG00000090432 NA MUL1 mitochondrial E3 ubiquitin protein ligase 1 79594 ENSG00000090432
9  ENSG00000161281 NA COX7A1 cytochrome c oxidase subunit VIIa polypeptide 1 (muscle) 1346 ENSG00000161281
10  ENSG00000136521 NA NDUFB5 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa 4711 ENSG00000136521
11  ENSG00000173915 NA USMG5 up-regulated during skeletal muscle growth 5 homolog (mouse) 84833 ENSG00000173915
12  ENSG00000169020 NA ATP5I ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E 521 ENSG00000169020
13  ENSG00000004779 NA NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa 4706 ENSG00000004779
14  ENSG00000168958 NA MFF mitochondrial fission factor 56947 ENSG00000168958
15  ENSG00000156885 NA COX6A2 cytochrome c oxidase subunit VIa polypeptide 2 1339 ENSG00000156885
16  ENSG00000147123 NA NDUFB11 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa 54539 ENSG00000147123
17  ENSG00000154723 NA ATP5J ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 522 ENSG00000154723
18  ENSG00000073578 NA SDHA succinate dehydrogenase complex, subunit A, flavoprotein (Fp) 6389 ENSG00000073578
19  ENSG00000137714 NA FDX1 ferredoxin 1 2230 ENSG00000137714
20  ENSG00000119013 NA NDUFB3 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa 4709 ENSG00000119013
21  ENSG00000169021 NA UQCRFS1 ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 7386 ENSG00000169021
22  ENSG00000100347 NA SAMM50 sorting and assembly machinery component 50 homolog (S. cerevisiae) 25813 ENSG00000100347
23  ENSG00000135390 NA ATP5G2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C2 (subunit 9) 517 ENSG00000135390
24  ENSG00000140740 NA UQCRC2 ubiquinol-cytochrome c reductase core protein II 7385 ENSG00000140740
25  ENSG00000166136 NA NDUFB8 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa 4714 ENSG00000166136
26  ENSG00000160194 NA NDUFV3 NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa 4731 ENSG00000160194
27  ENSG00000147684 NA NDUFB9 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa 4715 ENSG00000147684
28  ENSG00000184983 NA NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa 4700 ENSG00000184983
29  ENSG00000130414 NA NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa 4705 ENSG00000130414
30  ENSG00000163626 NA COX18 COX18 cytochrome c oxidase assembly homolog (S. cerevisiae) 285521 ENSG00000163626
31  ENSG00000158864 NA NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) 4720 ENSG00000158864
32  ENSG00000105197 NA TIMM50 translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae) 92609 ENSG00000105197
33  ENSG00000139180 NA NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa 4704 ENSG00000139180
34  ENSG00000109390 NA NDUFC1 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa 4717 ENSG00000109390
35  ENSG00000124172 NA ATP5E ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit 514 ENSG00000124172
36  ENSG00000183648 NA NDUFB1 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa 4707 ENSG00000183648
37  ENSG00000099624 NA ATP5D ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit 513 ENSG00000099624
38  ENSG00000204370 NA SDHD succinate dehydrogenase complex, subunit D, integral membrane protein 6392 ENSG00000204370
39  ENSG00000116459 NA ATP5F1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 515 ENSG00000116459
40  ENSG00000104980 NA TIMM44 translocase of inner mitochondrial membrane 44 homolog (yeast) 10469 ENSG00000104980
41  ENSG00000112992 NA NNT nicotinamide nucleotide transhydrogenase 23530 ENSG00000112992
42  ENSG00000125356 NA NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa 4694 ENSG00000125356
43  ENSG00000213619 NA NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) 4722 ENSG00000213619
44  ENSG00000173660 NA UQCRH ubiquinol-cytochrome c reductase hinge protein 7388 ENSG00000173660
45  ENSG00000214253 NA FIS1 fission 1 (mitochondrial outer membrane) homolog (S. cerevisiae) 51024 ENSG00000214253
46  ENSG00000099795 NA NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa 4713 ENSG00000099795
47  ENSG00000119421 NA NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa 4702 ENSG00000119421
48  ENSG00000023228 NA NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) 4719 ENSG00000023228
49  ENSG00000143252 NA SDHC succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa 6391 ENSG00000143252
50  ENSG00000145494 NA NDUFS6 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) 4726 ENSG00000145494
51  ENSG00000156709 NA AIFM1 apoptosis-inducing factor, mitochondrion-associated, 1 9131 ENSG00000156709
52  ENSG00000189043 NA NDUFA4 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa 4697 ENSG00000189043
53  ENSG00000110955 NA ATP5B ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide 506 ENSG00000110955
54  ENSG00000115286 NA NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) 374291 ENSG00000115286
55  ENSG00000112695 NA COX7A2 cytochrome c oxidase subunit VIIa polypeptide 2 (liver) 1347 ENSG00000112695
56  ENSG00000164258 NA NDUFS4 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) 4724 ENSG00000164258
57  ENSG00000167792 NA NDUFV1 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa 4723 ENSG00000167792
58  ENSG00000131495 NA NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa 4695 ENSG00000131495
59  ENSG00000155463 NA OXA1L oxidase (cytochrome c) assembly 1-like 5018 ENSG00000155463
60  ENSG00000065518 NA NDUFB4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa 4710 ENSG00000065518
61  ENSG00000167863 NA ATP5H ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d 10476 ENSG00000167863
62  ENSG00000090266 NA NDUFB2 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa 4708 ENSG00000090266
63  ENSG00000110717 NA NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) 4728 ENSG00000110717
64  ENSG00000131174 NA COX7B cytochrome c oxidase subunit VIIb 1349 ENSG00000131174
65  ENSG00000170906 NA NDUFA3 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa 4696 ENSG00000170906
66  ENSG00000184752 NA NDUFA12 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 55967 ENSG00000184752
67  ENSG00000156411 NA C14orf2 chromosome 14 open reading frame 2 9556 ENSG00000156411
68  ENSG00000159199 NA ATP5G1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) 516 ENSG00000159199
69  ENSG00000167283 NA ATP5L ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G 10632 ENSG00000167283
70  ENSG00000069509 NA FUNDC1 FUN14 domain containing 1 139341 ENSG00000069509
71  ENSG00000196683 NA TOMM7 translocase of outer mitochondrial membrane 7 homolog (yeast) 54543 ENSG00000196683
72  ENSG00000074582 NA BCS1L BCS1-like (S. cerevisiae) 617 ENSG00000074582
73  ENSG00000010256 NA UQCRC1 ubiquinol-cytochrome c reductase core protein I 7384 ENSG00000010256
74  ENSG00000137806 NA NDUFAF1 NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 51103 ENSG00000137806
75  ENSG00000241468 NA ATP5J2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 9551 ENSG00000241468
76  ENSG00000140990 NA NDUFB10 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa 4716 ENSG00000140990
77  ENSG00000117118 NA SDHB succinate dehydrogenase complex, subunit B, iron sulfur (Ip) 6390 ENSG00000117118
78  ENSG00000171503 NA ETFDH electron-transferring-flavoprotein dehydrogenase 2110 ENSG00000171503
79  ENSG00000154518 NA ATP5G3 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C3 (subunit 9) 518 ENSG00000154518
80  ENSG00000165629 NA ATP5C1 ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 509 ENSG00000165629
81  ENSG00000115944 NA COX7A2L cytochrome c oxidase subunit VIIa polypeptide 2 like 9167 ENSG00000115944
82  ENSG00000148290 NA SURF1 surfeit 1 6834 ENSG00000148290
83  ENSG00000101247 NA NDUFAF5 NADH dehydrogenase (ubiquinone) complex I, assembly factor 5 79133 ENSG00000101247
84  ENSG00000168653 NA NDUFS5 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) 4725 ENSG00000168653
85  ENSG00000126768 NA TIMM17B translocase of inner mitochondrial membrane 17 homolog B (yeast) 10245 ENSG00000126768
86  ENSG00000152234 NA ATP5A1 ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle 498 ENSG00000152234
87  ENSG00000241837 NA ATP5O ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit 539 ENSG00000241837


Database:cellular component       Name:organelle envelope       ID:GO:0031967
C=822; O=193; E=49.89; R=3.87; rawP=1.60e-64; adjP=6.34e-63
Index UserID Value Gene Symbol Gene Name EntrezGene Ensembl
1  ENSG00000164828 NA SUN1 Sad1 and UNC84 domain containing 1 23353 ENSG00000164828
2  ENSG00000087299 NA L2HGDH L-2-hydroxyglutarate dehydrogenase 79944 ENSG00000087299
3  ENSG00000184903 NA IMMP2L IMP2 inner mitochondrial membrane peptidase-like (S. cerevisiae) 83943 ENSG00000184903
4  ENSG00000143575 NA HAX1 HCLS1 associated protein X-1 10456 ENSG00000143575
5  ENSG00000165264 NA NDUFB6 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa 4712 ENSG00000165264
6  ENSG00000156467 NA UQCRB ubiquinol-cytochrome c reductase binding protein 7381 ENSG00000156467
7  ENSG00000116898 NA MRPS15 mitochondrial ribosomal protein S15 64960 ENSG00000116898
8  ENSG00000161281 NA COX7A1 cytochrome c oxidase subunit VIIa polypeptide 1 (muscle) 1346 ENSG00000161281
9  ENSG00000184076 NA UQCR10 ubiquinol-cytochrome c reductase, complex III subunit X 29796 ENSG00000184076
10  ENSG00000078070 NA MCCC1 methylcrotonoyl-CoA carboxylase 1 (alpha) 56922 ENSG00000078070
11  ENSG00000075415 NA SLC25A3 solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 3 5250 ENSG00000075415
12  ENSG00000156885 NA COX6A2 cytochrome c oxidase subunit VIa polypeptide 2 1339 ENSG00000156885
13  ENSG00000006695 NA COX10 COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast) 1352 ENSG00000006695
14  ENSG00000133983 NA COX16 COX16 cytochrome c oxidase assembly homolog (S. cerevisiae) 51241 ENSG00000133983
15  ENSG00000154723 NA ATP5J ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 522 ENSG00000154723
16  ENSG00000115364 NA MRPL19 mitochondrial ribosomal protein L19 9801 ENSG00000115364
17  ENSG00000167969 NA ECI1 enoyl-CoA delta isomerase 1 1632 ENSG00000167969
18  ENSG00000139531 NA SUOX sulfite oxidase 6821 ENSG00000139531
19  ENSG00000125166 NA GOT2 glutamic-oxaloacetic transaminase 2, mitochondrial (aspartate aminotransferase 2) 2806 ENSG00000125166
20  ENSG00000100347 NA SAMM50 sorting and assembly machinery component 50 homolog (S. cerevisiae) 25813 ENSG00000100347
21  ENSG00000135390 NA ATP5G2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C2 (subunit 9) 517 ENSG00000135390
22  ENSG00000177370 NA TIMM22 translocase of inner mitochondrial membrane 22 homolog (yeast) 29928 ENSG00000177370
23  ENSG00000140740 NA UQCRC2 ubiquinol-cytochrome c reductase core protein II 7385 ENSG00000140740
24  ENSG00000166136 NA NDUFB8 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa 4714 ENSG00000166136
25  ENSG00000160194 NA NDUFV3 NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa 4731 ENSG00000160194
26  ENSG00000147684 NA NDUFB9 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa 4715 ENSG00000147684
27  ENSG00000184983 NA NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa 4700 ENSG00000184983
28  ENSG00000130414 NA NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa 4705 ENSG00000130414
29  ENSG00000163626 NA COX18 COX18 cytochrome c oxidase assembly homolog (S. cerevisiae) 285521 ENSG00000163626
30  ENSG00000158864 NA NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) 4720 ENSG00000158864
31  ENSG00000007923 NA DNAJC11 DnaJ (Hsp40) homolog, subfamily C, member 11 55735 ENSG00000007923
32  ENSG00000173436 NA MINOS1 mitochondrial inner membrane organizing system 1 440574 ENSG00000173436
33  ENSG00000105197 NA TIMM50 translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae) 92609 ENSG00000105197
34  ENSG00000109390 NA NDUFC1 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa 4717 ENSG00000109390
35  ENSG00000164054 NA SHISA5 shisa homolog 5 (Xenopus laevis) 51246 ENSG00000164054
36  ENSG00000060762 NA MPC1 mitochondrial pyruvate carrier 1 51660 ENSG00000060762
37  ENSG00000165283 NA STOML2 stomatin (EPB72)-like 2 30968 ENSG00000165283
38  ENSG00000104980 NA TIMM44 translocase of inner mitochondrial membrane 44 homolog (yeast) 10469 ENSG00000104980
39  ENSG00000116459 NA ATP5F1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 515 ENSG00000116459
40  ENSG00000164466 NA SFXN1 sideroflexin 1 94081 ENSG00000164466
41  ENSG00000099800 NA TIMM13 translocase of inner mitochondrial membrane 13 homolog (yeast) 26517 ENSG00000099800
42  ENSG00000151729 NA SLC25A4 solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4 291 ENSG00000151729
43  ENSG00000178057 NA NDUFAF3 NADH dehydrogenase (ubiquinone) complex I, assembly factor 3 25915 ENSG00000178057
44  ENSG00000112992 NA NNT nicotinamide nucleotide transhydrogenase 23530 ENSG00000112992
45  ENSG00000213619 NA NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) 4722 ENSG00000213619
46  ENSG00000178741 NA COX5A cytochrome c oxidase subunit Va 9377 ENSG00000178741
47  ENSG00000173660 NA UQCRH ubiquinol-cytochrome c reductase hinge protein 7388 ENSG00000173660
48  ENSG00000214253 NA FIS1 fission 1 (mitochondrial outer membrane) homolog (S. cerevisiae) 51024 ENSG00000214253
49  ENSG00000133028 NA SCO1 SCO cytochrome oxidase deficient homolog 1 (yeast) 6341 ENSG00000133028
50  ENSG00000148950 NA IMMP1L IMP1 inner mitochondrial membrane peptidase-like (S. cerevisiae) 196294 ENSG00000148950
51  ENSG00000119421 NA NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa 4702 ENSG00000119421
52  ENSG00000126267 NA COX6B1 cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) 1340 ENSG00000126267
53  ENSG00000109919 NA MTCH2 mitochondrial carrier 2 23788 ENSG00000109919
54  ENSG00000135940 NA COX5B cytochrome c oxidase subunit Vb 1329 ENSG00000135940
55  ENSG00000215021 NA PHB2 prohibitin 2 11331 ENSG00000215021
56  ENSG00000145494 NA NDUFS6 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) 4726 ENSG00000145494
57  ENSG00000167085 NA PHB prohibitin 5245 ENSG00000167085
58  ENSG00000072506 NA HSD17B10 hydroxysteroid (17-beta) dehydrogenase 10 3028 ENSG00000072506
59  ENSG00000156709 NA AIFM1 apoptosis-inducing factor, mitochondrion-associated, 1 9131 ENSG00000156709
60  ENSG00000189043 NA NDUFA4 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa 4697 ENSG00000189043
61  ENSG00000131143 NA COX4I1 cytochrome c oxidase subunit IV isoform 1 1327 ENSG00000131143
62  ENSG00000172115 NA CYCS cytochrome c, somatic 54205 ENSG00000172115
63  ENSG00000164919 NA COX6C cytochrome c oxidase subunit VIc 1345 ENSG00000164919
64  ENSG00000115286 NA NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) 374291 ENSG00000115286
65  ENSG00000164258 NA NDUFS4 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) 4724 ENSG00000164258
66  ENSG00000156170 NA NDUFAF6 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 137682 ENSG00000156170
67  ENSG00000155463 NA OXA1L oxidase (cytochrome c) assembly 1-like 5018 ENSG00000155463
68  ENSG00000167863 NA ATP5H ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d 10476 ENSG00000167863
69  ENSG00000090266 NA NDUFB2 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa 4708 ENSG00000090266
70  ENSG00000127540 NA UQCR11 ubiquinol-cytochrome c reductase, complex III subunit XI 10975 ENSG00000127540
71  ENSG00000179091 NA CYC1 cytochrome c-1 1537 ENSG00000179091
72  ENSG00000184752 NA NDUFA12 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 55967 ENSG00000184752
73  ENSG00000156411 NA C14orf2 chromosome 14 open reading frame 2 9556 ENSG00000156411
74  ENSG00000131844 NA MCCC2 methylcrotonoyl-CoA carboxylase 2 (beta) 64087 ENSG00000131844
75  ENSG00000159199 NA ATP5G1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) 516 ENSG00000159199
76  ENSG00000105819 NA PMPCB peptidase (mitochondrial processing) beta 9512 ENSG00000105819
77  ENSG00000150779 NA TIMM8B translocase of inner mitochondrial membrane 8 homolog B (yeast) 26521 ENSG00000150779
78  ENSG00000166855 NA CLPX ClpX caseinolytic peptidase X homolog (E. coli) 10845 ENSG00000166855
79  ENSG00000204228 NA HSD17B8 hydroxysteroid (17-beta) dehydrogenase 8 7923 ENSG00000204228
80  ENSG00000196683 NA TOMM7 translocase of outer mitochondrial membrane 7 homolog (yeast) 54543 ENSG00000196683
81  ENSG00000074582 NA BCS1L BCS1-like (S. cerevisiae) 617 ENSG00000074582
82  ENSG00000103018 NA CYB5B cytochrome b5 type B (outer mitochondrial membrane) 80777 ENSG00000103018
83  ENSG00000166816 NA LDHD lactate dehydrogenase D 197257 ENSG00000166816
84  ENSG00000140990 NA NDUFB10 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa 4716 ENSG00000140990
85  ENSG00000066926 NA FECH ferrochelatase 2235 ENSG00000066926
86  ENSG00000117118 NA SDHB succinate dehydrogenase complex, subunit B, iron sulfur (Ip) 6390 ENSG00000117118
87  ENSG00000138495 NA COX17 COX17 cytochrome c oxidase assembly homolog (S. cerevisiae) 10063 ENSG00000138495
88  ENSG00000198523 NA PLN phospholamban 5350 ENSG00000198523
89  ENSG00000006530 NA AGK acylglycerol kinase 55750 ENSG00000006530
90  ENSG00000135469 NA COQ10A coenzyme Q10 homolog A (S. cerevisiae) 93058 ENSG00000135469
91  ENSG00000180198 NA RCC1 regulator of chromosome condensation 1 1104 ENSG00000180198
92  ENSG00000177427 NA SMCR7 Smith-Magenis syndrome chromosome region, candidate 7 125170 ENSG00000177427
93  ENSG00000165629 NA ATP5C1 ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 509 ENSG00000165629
94  ENSG00000115944 NA COX7A2L cytochrome c oxidase subunit VIIa polypeptide 2 like 9167 ENSG00000115944
95  ENSG00000123545 NA NDUFAF4 NADH dehydrogenase (ubiquinone) complex I, assembly factor 4 29078 ENSG00000123545
96  ENSG00000148290 NA SURF1 surfeit 1 6834 ENSG00000148290
97  ENSG00000197150 NA ABCB8 ATP-binding cassette, sub-family B (MDR/TAP), member 8 11194 ENSG00000197150
98  ENSG00000152234 NA ATP5A1 ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle 498 ENSG00000152234
99  ENSG00000072778 NA ACADVL acyl-CoA dehydrogenase, very long chain 37 ENSG00000072778
100  ENSG00000172893 NA DHCR7 7-dehydrocholesterol reductase 1717 ENSG00000172893
101  ENSG00000151366 NA NDUFC2 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa 4718 ENSG00000151366
102  ENSG00000196636 NA ACN9 ACN9 homolog (S. cerevisiae) 57001 ENSG00000196636
103  ENSG00000128609 NA NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDa 4698 ENSG00000128609
104  ENSG00000132305 NA IMMT inner membrane protein, mitochondrial 10989 ENSG00000132305
105  ENSG00000163541 NA SUCLG1 succinate-CoA ligase, alpha subunit 8802 ENSG00000163541
106  ENSG00000090432 NA MUL1 mitochondrial E3 ubiquitin protein ligase 1 79594 ENSG00000090432
107  ENSG00000165678 NA GHITM growth hormone inducible transmembrane protein 27069 ENSG00000165678
108  ENSG00000146701 NA MDH2 malate dehydrogenase 2, NAD (mitochondrial) 4191 ENSG00000146701
109  ENSG00000125995 NA ROMO1 reactive oxygen species modulator 1 140823 ENSG00000125995
110  ENSG00000136521 NA NDUFB5 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa 4711 ENSG00000136521
111  ENSG00000173915 NA USMG5 up-regulated during skeletal muscle growth 5 homolog (mouse) 84833 ENSG00000173915
112  ENSG00000169020 NA ATP5I ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E 521 ENSG00000169020
113  ENSG00000131730 NA CKMT2 creatine kinase, mitochondrial 2 (sarcomeric) 1160 ENSG00000131730
114  ENSG00000158882 NA TOMM40L translocase of outer mitochondrial membrane 40 homolog (yeast)-like 84134 ENSG00000158882
115  ENSG00000182054 NA IDH2 isocitrate dehydrogenase 2 (NADP+), mitochondrial 3418 ENSG00000182054
116  ENSG00000004779 NA NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa 4706 ENSG00000004779
117  ENSG00000120253 NA NUP43 nucleoporin 43kDa 348995 ENSG00000120253
118  ENSG00000168958 NA MFF mitochondrial fission factor 56947 ENSG00000168958
119  ENSG00000164038 NA SLC9B2 solute carrier family 9, subfamily B (NHA2, cation proton antiporter 2), member 2 133308 ENSG00000164038
120  ENSG00000004961 NA HCCS holocytochrome c synthase 3052 ENSG00000004961
121  ENSG00000147123 NA NDUFB11 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa 54539 ENSG00000147123
122  ENSG00000073578 NA SDHA succinate dehydrogenase complex, subunit A, flavoprotein (Fp) 6389 ENSG00000073578
123  ENSG00000137714 NA FDX1 ferredoxin 1 2230 ENSG00000137714
124  ENSG00000119013 NA NDUFB3 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa 4709 ENSG00000119013
125  ENSG00000169021 NA UQCRFS1 ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 7386 ENSG00000169021
126  ENSG00000124523 NA SIRT5 sirtuin 5 23408 ENSG00000124523
127  ENSG00000178449 NA COX14 COX14 cytochrome c oxidase assembly homolog (S. cerevisiae) 84987 ENSG00000178449
128  ENSG00000175193 NA PARL presenilin associated, rhomboid-like 55486 ENSG00000175193
129  ENSG00000078668 NA VDAC3 voltage-dependent anion channel 3 7419 ENSG00000078668
130  ENSG00000111843 NA TMEM14C transmembrane protein 14C 51522 ENSG00000111843
131  ENSG00000162600 NA OMA1 OMA1 zinc metallopeptidase homolog (S. cerevisiae) 115209 ENSG00000162600
132  ENSG00000139180 NA NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa 4704 ENSG00000139180
133  ENSG00000108179 NA PPIF peptidylprolyl isomerase F 10105 ENSG00000108179
134  ENSG00000127184 NA COX7C cytochrome c oxidase subunit VIIc 1350 ENSG00000127184
135  ENSG00000164405 NA UQCRQ ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa 27089 ENSG00000164405
136  ENSG00000165637 NA VDAC2 voltage-dependent anion channel 2 7417 ENSG00000165637
137  ENSG00000173085 NA COQ2 coenzyme Q2 homolog, prenyltransferase (yeast) 27235 ENSG00000173085
138  ENSG00000124172 NA ATP5E ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit 514 ENSG00000124172
139  ENSG00000183648 NA NDUFB1 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa 4707 ENSG00000183648
140  ENSG00000213585 NA VDAC1 voltage-dependent anion channel 1 7416 ENSG00000213585
141  ENSG00000205981 NA DNAJC19 DnaJ (Hsp40) homolog, subfamily C, member 19 131118 ENSG00000205981
142  ENSG00000132591 NA ERAL1 Era G-protein-like 1 (E. coli) 26284 ENSG00000132591
143  ENSG00000120333 NA MRPS14 mitochondrial ribosomal protein S14 63931 ENSG00000120333
144  ENSG00000099624 NA ATP5D ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit 513 ENSG00000099624
145  ENSG00000204370 NA SDHD succinate dehydrogenase complex, subunit D, integral membrane protein 6392 ENSG00000204370
146  ENSG00000166949 NA SMAD3 SMAD family member 3 4088 ENSG00000166949
147  ENSG00000106554 NA CHCHD3 coiled-coil-helix-coiled-coil-helix domain containing 3 54927 ENSG00000106554
148  ENSG00000181610 NA MRPS23 mitochondrial ribosomal protein S23 51649 ENSG00000181610
149  ENSG00000125356 NA NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa 4694 ENSG00000125356
150  ENSG00000108528 NA SLC25A11 solute carrier family 25 (mitochondrial carrier; oxoglutarate carrier), member 11 8402 ENSG00000108528
151  ENSG00000099795 NA NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa 4713 ENSG00000099795
152  ENSG00000174032 NA SLC25A30 solute carrier family 25, member 30 253512 ENSG00000174032
153  ENSG00000091732 NA ZC3HC1 zinc finger, C3HC-type containing 1 51530 ENSG00000091732
154  ENSG00000023228 NA NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) 4719 ENSG00000023228
155  ENSG00000143252 NA SDHC succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa 6391 ENSG00000143252
156  ENSG00000075336 NA TIMM21 translocase of inner mitochondrial membrane 21 homolog (yeast) 29090 ENSG00000075336
157  ENSG00000115840 NA SLC25A12 solute carrier family 25 (aspartate/glutamate carrier), member 12 8604 ENSG00000115840
158  ENSG00000110955 NA ATP5B ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide 506 ENSG00000110955
159  ENSG00000197122 NA SRC v-src sarcoma (Schmidt-Ruppin A-2) viral oncogene homolog (avian) 6714 ENSG00000197122
160  ENSG00000112695 NA COX7A2 cytochrome c oxidase subunit VIIa polypeptide 2 (liver) 1347 ENSG00000112695
161  ENSG00000197448 NA GSTK1 glutathione S-transferase kappa 1 373156 ENSG00000197448
162  ENSG00000167792 NA NDUFV1 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa 4723 ENSG00000167792
163  ENSG00000131495 NA NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa 4695 ENSG00000131495
164  ENSG00000065518 NA NDUFB4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa 4710 ENSG00000065518
165  ENSG00000095321 NA CRAT carnitine O-acetyltransferase 1384 ENSG00000095321
166  ENSG00000165688 NA PMPCA peptidase (mitochondrial processing) alpha 23203 ENSG00000165688
167  ENSG00000110717 NA NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) 4728 ENSG00000110717
168  ENSG00000131174 NA COX7B cytochrome c oxidase subunit VIIb 1349 ENSG00000131174
169  ENSG00000170906 NA NDUFA3 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa 4696 ENSG00000170906
170  ENSG00000138085 NA ATRAID all-trans retinoic acid-induced differentiation factor 51374 ENSG00000138085
171  ENSG00000128654 NA MTX2 metaxin 2 10651 ENSG00000128654
172  ENSG00000204308 NA RNF5 ring finger protein 5, E3 ubiquitin protein ligase 6048 ENSG00000204308
173  ENSG00000167283 NA ATP5L ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G 10632 ENSG00000167283
174  ENSG00000069509 NA FUNDC1 FUN14 domain containing 1 139341 ENSG00000069509
175  ENSG00000183978 NA COA3 cytochrome C oxidase assembly factor 3 28958 ENSG00000183978
176  ENSG00000124532 NA MRS2 MRS2 magnesium homeostasis factor homolog (S. cerevisiae) 57380 ENSG00000124532
177  ENSG00000131269 NA ABCB7 ATP-binding cassette, sub-family B (MDR/TAP), member 7 22 ENSG00000131269
178  ENSG00000010256 NA UQCRC1 ubiquinol-cytochrome c reductase core protein I 7384 ENSG00000010256
179  ENSG00000137806 NA NDUFAF1 NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 51103 ENSG00000137806
180  ENSG00000241468 NA ATP5J2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 9551 ENSG00000241468
181  ENSG00000197912 NA SPG7 spastic paraplegia 7 (pure and complicated autosomal recessive) 6687 ENSG00000197912
182  ENSG00000171503 NA ETFDH electron-transferring-flavoprotein dehydrogenase 2110 ENSG00000171503
183  ENSG00000143158 NA MPC2 mitochondrial pyruvate carrier 2 25874 ENSG00000143158
184  ENSG00000138796 NA HADH hydroxyacyl-CoA dehydrogenase 3033 ENSG00000138796
185  ENSG00000154518 NA ATP5G3 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C3 (subunit 9) 518 ENSG00000154518
186  ENSG00000107317 NA PTGDS prostaglandin D2 synthase 21kDa (brain) 5730 ENSG00000107317
187  ENSG00000075303 NA SLC25A40 solute carrier family 25, member 40 55972 ENSG00000075303
188  ENSG00000176340 NA COX8A cytochrome c oxidase subunit VIIIA (ubiquitous) 1351 ENSG00000176340
189  ENSG00000101247 NA NDUFAF5 NADH dehydrogenase (ubiquinone) complex I, assembly factor 5 79133 ENSG00000101247
190  ENSG00000168653 NA NDUFS5 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) 4725 ENSG00000168653
191  ENSG00000126768 NA TIMM17B translocase of inner mitochondrial membrane 17 homolog B (yeast) 10245 ENSG00000126768
192  ENSG00000247077 NA PGAM5 phosphoglycerate mutase family member 5 192111 ENSG00000247077
193  ENSG00000241837 NA ATP5O ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit 539 ENSG00000241837





WebGestalt is currently developed and maintained by Jing Wang and Bing Zhang at the Zhang Lab. Other people who have made significant contribution to the project include Dexter Duncan, Stefan Kirov, Zhiao Shi, and Jay Snoddy.

Funding credits: NIH/NIAAA (U01 AA016662, U01 AA013512); NIH/NIDA (P01 DA015027); NIH/NIMH (P50 MH078028, P50 MH096972); NIH/NCI (U24 CA159988); NIH/NIGMS (R01 GM088822).